ATP-binding cassette, sub-family A (ABC1), member 4 (ABCA4) - coding DNA reference sequence

(used for variant description)

(last modified February 27, 2015)


This file was created to facilitate the description of sequence variants on transcript NM_000350.2 in the ABCA4 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_009073.1, covering ABCA4 transcript NM_000350.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5044
                 aggacacagcgtccggagccagaggcgctcttaacggcgtttat       c.-61

 .         .         .         .         .         .                g.5104
 gtcctttgctgtctgaggggcctcagctctgaccaatctggtcttcgtgtggtcattagc       c.-1

          .         .         .         .         .         .       g.5164
 ATGGGCTTCGTGAGACAGATACAGCTTTTGCTCTGGAAGAACTGGACCCTGCGGAAAAGG       c.60
 M  G  F  V  R  Q  I  Q  L  L  L  W  K  N  W  T  L  R  K  R         p.20

        | 02 .         .         .         .         .         .    g.13137
 CAAAAG | ATTCGCTTTGTGGTGGAACTCGTGTGGCCTTTATCTTTATTTCTGGTCTTGATC    c.120
 Q  K   | I  R  F  V  V  E  L  V  W  P  L  S  L  F  L  V  L  I      p.40

          .         .         .         . | 03       .         .    g.14590
 TGGTTAAGGAATGCCAACCCGCTCTACAGCCATCATGAAT | GCCATTTCCCCAACAAGGCG    c.180
 W  L  R  N  A  N  P  L  Y  S  H  H  E  C |   H  F  P  N  K  A      p.60

          .         .         .         .         .         .       g.14650
 ATGCCCTCAGCAGGAATGCTGCCGTGGCTCCAGGGGATCTTCTGCAATGTGAACAATCCC       c.240
 M  P  S  A  G  M  L  P  W  L  Q  G  I  F  C  N  V  N  N  P         p.80

          .         .         .         .         .         .       g.14710
 TGTTTTCAAAGCCCCACCCCAGGAGAATCTCCTGGAATTGTGTCAAACTATAACAACTCC       c.300
 C  F  Q  S  P  T  P  G  E  S  P  G  I  V  S  N  Y  N  N  S         p.100

    | 04     .         .         .         .         .         .    g.17491
 AT | CTTGGCAAGGGTATATCGAGATTTTCAAGAACTCCTCATGAATGCACCAGAGAGCCAG    c.360
 I  |  L  A  R  V  Y  R  D  F  Q  E  L  L  M  N  A  P  E  S  Q      p.120

          .         .         .         .         .         .       g.17551
 CACCTTGGCCGTATTTGGACAGAGCTACACATCTTGTCCCAATTCATGGACACCCTCCGG       c.420
 H  L  G  R  I  W  T  E  L  H  I  L  S  Q  F  M  D  T  L  R         p.140

          .         .   | 05     .         .         .         .    g.23045
 ACTCACCCGGAGAGAATTGCAG | GAAGAGGAATACGAATAAGGGATATCTTGAAAGATGAA    c.480
 T  H  P  E  R  I  A  G |   R  G  I  R  I  R  D  I  L  K  D  E      p.160

          .         .         .         .         .         .       g.23105
 GAAACACTGACACTATTTCTCATTAAAAACATCGGCCTGTCTGACTCAGTGGTCTACCTT       c.540
 E  T  L  T  L  F  L  I  K  N  I  G  L  S  D  S  V  V  Y  L         p.180

          .         .         . | 06       .         .         .    g.27188
 CTGATCAACTCTCAAGTCCGTCCAGAGCAG | TTCGCTCATGGAGTCCCGGACCTGGCGCTG    c.600
 L  I  N  S  Q  V  R  P  E  Q   | F  A  H  G  V  P  D  L  A  L      p.200

          .         .         .         .         .         .       g.27248
 AAGGACATCGCCTGCAGCGAGGCCCTCCTGGAGCGCTTCATCATCTTCAGCCAGAGACGC       c.660
 K  D  I  A  C  S  E  A  L  L  E  R  F  I  I  F  S  Q  R  R         p.220

          .         .         .         .         .         .       g.27308
 GGGGCAAAGACGGTGCGCTATGCCCTGTGCTCCCTCTCCCAGGGCACCCTACAGTGGATA       c.720
 G  A  K  T  V  R  Y  A  L  C  S  L  S  Q  G  T  L  Q  W  I         p.240

          .         .         .         .         | 07         .    g.42720
 GAAGACACTCTGTATGCCAACGTGGACTTCTTCAAGCTCTTCCGTGTG | CTTCCCACACTC    c.780
 E  D  T  L  Y  A  N  V  D  F  F  K  L  F  R  V   | L  P  T  L      p.260

          .         .         .         .         .         .       g.42780
 CTAGACAGCCGTTCTCAAGGTATCAATCTGAGATCTTGGGGAGGAATATTATCTGATATG       c.840
 L  D  S  R  S  Q  G  I  N  L  R  S  W  G  G  I  L  S  D  M         p.280

          .         | 08         .         .         .         .    g.45473
 TCACCAAGAATTCAAGAG | TTTATCCATCGGCCGAGTATGCAGGACTTGCTGTGGGTGACC    c.900
 S  P  R  I  Q  E   | F  I  H  R  P  S  M  Q  D  L  L  W  V  T      p.300

          .         .         .         .         .         .       g.45533
 AGGCCCCTCATGCAGAATGGTGGTCCAGAGACCTTTACAAAGCTGATGGGCATCCTGTCT       c.960
 R  P  L  M  Q  N  G  G  P  E  T  F  T  K  L  M  G  I  L  S         p.320

          .         .         .         .         .         .       g.45593
 GACCTCCTGTGTGGCTACCCCGAGGGAGGTGGCTCTCGGGTGCTCTCCTTCAACTGGTAT       c.1020
 D  L  L  C  G  Y  P  E  G  G  G  S  R  V  L  S  F  N  W  Y         p.340

          .         .         .         .         .         .       g.45653
 GAAGACAATAACTATAAGGCCTTTCTGGGGATTGACTCCACAAGGAAGGATCCTATCTAT       c.1080
 E  D  N  N  Y  K  A  F  L  G  I  D  S  T  R  K  D  P  I  Y         p.360

          .          | 09        .         .         .         .    g.46729
 TCTTATGACAGAAGAACAA | CATCCTTTTGTAATGCATTGATCCAGAGCCTGGAGTCAAAT    c.1140
 S  Y  D  R  R  T  T |   S  F  C  N  A  L  I  Q  S  L  E  S  N      p.380

          .         .         .         .         .         .       g.46789
 CCTTTAACCAAAATCGCTTGGAGGGCGGCAAAGCCTTTGCTGATGGGAAAAATCCTGTAC       c.1200
 P  L  T  K  I  A  W  R  A  A  K  P  L  L  M  G  K  I  L  Y         p.400

          .         .         .          | 10        .         .    g.47464
 ACTCCTGATTCACCTGCAGCACGAAGGATACTGAAGAAT | GCCAACTCAACTTTTGAAGAA    c.1260
 T  P  D  S  P  A  A  R  R  I  L  K  N   | A  N  S  T  F  E  E      p.420

          .         .         .         .         .         .       g.47524
 CTGGAACACGTTAGGAAGTTGGTCAAAGCCTGGGAAGAAGTAGGGCCCCAGATCTGGTAC       c.1320
 L  E  H  V  R  K  L  V  K  A  W  E  E  V  G  P  Q  I  W  Y         p.440

          .         .         .       | 11 .         .         .    g.48286
 TTCTTTGACAACAGCACACAGATGAACATGATCAGA | GATACCCTGGGGAACCCAACAGTA    c.1380
 F  F  D  N  S  T  Q  M  N  M  I  R   | D  T  L  G  N  P  T  V      p.460

          .         .         .         .         .         .       g.48346
 AAAGACTTTTTGAATAGGCAGCTTGGTGAAGAAGGTATTACTGCTGAAGCCATCCTAAAC       c.1440
 K  D  F  L  N  R  Q  L  G  E  E  G  I  T  A  E  A  I  L  N         p.480

          .         .         .         .         .         .       g.48406
 TTCCTCTACAAGGGCCCTCGGGAAAGCCAGGCTGACGACATGGCCAACTTCGACTGGAGG       c.1500
 F  L  Y  K  G  P  R  E  S  Q  A  D  D  M  A  N  F  D  W  R         p.500

          .         .         .         .         .     | 12   .    g.62838
 GACATATTTAACATCACTGATCGCACCCTCCGCCTGGTCAATCAATACCTGGAG | TGCTTG    c.1560
 D  I  F  N  I  T  D  R  T  L  R  L  V  N  Q  Y  L  E   | C  L      p.520

          .         .         .         .         .         .       g.62898
 GTCCTGGATAAGTTTGAAAGCTACAATGATGAAACTCAGCTCACCCAACGTGCCCTCTCT       c.1620
 V  L  D  K  F  E  S  Y  N  D  E  T  Q  L  T  Q  R  A  L  S         p.540

          .         .         .         .         .         .       g.62958
 CTACTGGAGGAAAACATGTTCTGGGCCGGAGTGGTATTCCCTGACATGTATCCCTGGACC       c.1680
 L  L  E  E  N  M  F  W  A  G  V  V  F  P  D  M  Y  P  W  T         p.560

          .         .         .         .         .         .       g.63018
 AGCTCTCTACCACCCCACGTGAAGTATAAGATCCGAATGGACATAGACGTGGTGGAGAAA       c.1740
 S  S  L  P  P  H  V  K  Y  K  I  R  M  D  I  D  V  V  E  K         p.580

          .         . | 13       .         .         .         .    g.63436
 ACCAATAAGATTAAAGACAG | GTATTGGGATTCTGGTCCCAGAGCTGATCCCGTGGAAGAT    c.1800
 T  N  K  I  K  D  R  |  Y  W  D  S  G  P  R  A  D  P  V  E  D      p.600

          .         .         .         .         .         .       g.63496
 TTCCGGTACATCTGGGGCGGGTTTGCCTATCTGCAGGACATGGTTGAACAGGGGATCACA       c.1860
 F  R  Y  I  W  G  G  F  A  Y  L  Q  D  M  V  E  Q  G  I  T         p.620

          .         .         .         .         .         .       g.63556
 AGGAGCCAGGTGCAGGCGGAGGCTCCAGTTGGAATCTACCTCCAGCAGATGCCCTACCCC       c.1920
 R  S  Q  V  Q  A  E  A  P  V  G  I  Y  L  Q  Q  M  P  Y  P         p.640

          .        | 14.         .         .         .         .    g.65433
 TGCTTCGTGGACGATTC | TTTCATGATCATCCTGAACCGCTGTTTCCCTATCTTCATGGTG    c.1980
 C  F  V  D  D  S  |  F  M  I  I  L  N  R  C  F  P  I  F  M  V      p.660

          .         .         .         .         .         .       g.65493
 CTGGCATGGATCTACTCTGTCTCCATGACTGTGAAGAGCATCGTCTTGGAGAAGGAGTTG       c.2040
 L  A  W  I  Y  S  V  S  M  T  V  K  S  I  V  L  E  K  E  L         p.680

          .         .         .         .         .         .       g.65553
 CGACTGAAGGAGACCTTGAAAAATCAGGGTGTCTCCAATGCAGTGATTTGGTGTACCTGG       c.2100
 R  L  K  E  T  L  K  N  Q  G  V  S  N  A  V  I  W  C  T  W         p.700

          .         .         .         .         .         .       g.65613
 TTCCTGGACAGCTTCTCCATCATGTCGATGAGCATCTTCCTCCTGACGATATTCATCATG       c.2160
 F  L  D  S  F  S  I  M  S  M  S  I  F  L  L  T  I  F  I  M         p.720

  | 15       .         .         .         .         .         .    g.69387
  | CATGGAAGAATCCTACATTACAGCGACCCATTCATCCTCTTCCTGTTCTTGTTGGCTTTC    c.2220
  | H  G  R  I  L  H  Y  S  D  P  F  I  L  F  L  F  L  L  A  F      p.740

          .         .         .         .         .         .       g.69447
 TCCACTGCCACCATCATGCTGTGCTTTCTGCTCAGCACCTTCTTCTCCAAGGCCAGTCTG       c.2280
 S  T  A  T  I  M  L  C  F  L  L  S  T  F  F  S  K  A  S  L         p.760

          .         .         .         .         .         .       g.69507
 GCAGCAGCCTGTAGTGGTGTCATCTATTTCACCCTCTACCTGCCACACATCCTGTGCTTC       c.2340
 A  A  A  C  S  G  V  I  Y  F  T  L  Y  L  P  H  I  L  C  F         p.780

          .         .         .         .   | 16     .         .    g.70852
 GCCTGGCAGGACCGCATGACCGCTGAGCTGAAGAAGGCTGTG | AGCTTACTGTCTCCGGTG    c.2400
 A  W  Q  D  R  M  T  A  E  L  K  K  A  V   | S  L  L  S  P  V      p.800

          .         .         .         .         .         .       g.70912
 GCATTTGGATTTGGCACTGAGTACCTGGTTCGCTTTGAAGAGCAAGGCCTGGGGCTGCAG       c.2460
 A  F  G  F  G  T  E  Y  L  V  R  F  E  E  Q  G  L  G  L  Q         p.820

          .         .         .         .         .         .       g.70972
 TGGAGCAACATCGGGAACAGTCCCACGGAAGGGGACGAATTCAGCTTCCTGCTGTCCATG       c.2520
 W  S  N  I  G  N  S  P  T  E  G  D  E  F  S  F  L  L  S  M         p.840

          .         .         .         .         .         .       g.71032
 CAGATGATGCTCCTTGATGCTGCTGTCTATGGCTTACTCGCTTGGTACCTTGATCAGGTG       c.2580
 Q  M  M  L  L  D  A  A  V  Y  G  L  L  A  W  Y  L  D  Q  V         p.860

         | 17.         .         .         .         .         .    g.74504
 TTTCCAG | GAGACTATGGAACCCCACTTCCTTGGTACTTTCTTCTACAAGAGTCGTATTGG    c.2640
 F  P  G |   D  Y  G  T  P  L  P  W  Y  F  L  L  Q  E  S  Y  W      p.880

          .    | 18    .         .         .         .         .    g.77239
 CTTGGCGGTGAAG | GGTGTTCAACCAGAGAAGAAAGAGCCCTGGAAAAGACCGAGCCCCTA    c.2700
 L  G  G  E  G |   C  S  T  R  E  E  R  A  L  E  K  T  E  P  L      p.900

          .         .         .         .    | 19    .         .    g.79073
 ACAGAGGAAACGGAGGATCCAGAGCACCCAGAAGGAATACACG | ACTCCTTCTTTGAACGT    c.2760
 T  E  E  T  E  D  P  E  H  P  E  G  I  H  D |   S  F  F  E  R      p.920

          .         .         .         .         .         .       g.79133
 GAGCATCCAGGGTGGGTTCCTGGGGTATGCGTGAAGAATCTGGTAAAGATTTTTGAGCCC       c.2820
 E  H  P  G  W  V  P  G  V  C  V  K  N  L  V  K  I  F  E  P         p.940

          .         .         .         .         .         .       g.79193
 TGTGGCCGGCCAGCTGTGGACCGTCTGAACATCACCTTCTACGAGAACCAGATCACCGCA       c.2880
 C  G  R  P  A  V  D  R  L  N  I  T  F  Y  E  N  Q  I  T  A         p.960

          .         .         .         | 20         .         .    g.81427
 TTCCTGGGCCACAATGGAGCTGGGAAAACCACCACCTT | GTCCATCCTGACGGGTCTGTTG    c.2940
 F  L  G  H  N  G  A  G  K  T  T  T  L  |  S  I  L  T  G  L  L      p.980

          .         .         .         .         .         .       g.81487
 CCACCAACCTCTGGGACTGTGCTCGTTGGGGGAAGGGACATTGAAACCAGCCTGGATGCA       c.3000
 P  P  T  S  G  T  V  L  V  G  G  R  D  I  E  T  S  L  D  A         p.1000

          .         .         .         .         . | 21       .    g.82684
 GTCCGGCAGAGCCTTGGCATGTGTCCACAGCACAACATCCTGTTCCACCA | CCTCACGGTG    c.3060
 V  R  Q  S  L  G  M  C  P  Q  H  N  I  L  F  H  H  |  L  T  V      p.1020

          .         .         .         .         .         .       g.82744
 GCTGAGCACATGCTGTTCTATGCCCAGCTGAAAGGAAAGTCCCAGGAGGAGGCCCAGCTG       c.3120
 A  E  H  M  L  F  Y  A  Q  L  K  G  K  S  Q  E  E  A  Q  L         p.1040

          .         .         .         .         .         .       g.82804
 GAGATGGAAGCCATGTTGGAGGACACAGGCCTCCACCACAAGCGGAATGAAGAGGCTCAG       c.3180
 E  M  E  A  M  L  E  D  T  G  L  H  H  K  R  N  E  E  A  Q         p.1060

          . | 22       .         .         .         .         .    g.83301
 GACCTATCAG | GTGGCATGCAGAGAAAGCTGTCGGTTGCCATTGCCTTTGTGGGAGATGCC    c.3240
 D  L  S  G |   G  M  Q  R  K  L  S  V  A  I  A  F  V  G  D  A      p.1080

          .         .         .         .         .         .       g.83361
 AAGGTGGTGATTCTGGACGAACCCACCTCTGGGGTGGACCCTTACTCGAGACGCTCAATC       c.3300
 K  V  V  I  L  D  E  P  T  S  G  V  D  P  Y  S  R  R  S  I         p.1100

          .         .         | 23         .         .         .    g.84779
 TGGGATCTGCTCCTGAAGTATCGCTCAG | GCAGAACCATCATCATGTCCACTCACCACATG    c.3360
 W  D  L  L  L  K  Y  R  S  G |   R  T  I  I  M  S  T  H  H  M      p.1120

          .         .         .         .         .         .       g.84839
 GACGAGGCCGACCTCCTTGGGGACCGCATTGCCATCATTGCCCAGGGAAGGCTCTACTGC       c.3420
 D  E  A  D  L  L  G  D  R  I  A  I  I  A  Q  G  R  L  Y  C         p.1140

          .         .         .         .         .         .       g.84899
 TCAGGCACCCCACTCTTCCTGAAGAACTGCTTTGGCACAGGCTTGTACTTAACCTTGGTG       c.3480
 S  G  T  P  L  F  L  K  N  C  F  G  T  G  L  Y  L  T  L  V         p.1160

          .         .         .         .   | 24     .         .    g.86040
 CGCAAGATGAAAAACATCCAGAGCCAAAGGAAAGGCAGTGAG | GGGACCTGCAGCTGCTCG    c.3540
 R  K  M  K  N  I  Q  S  Q  R  K  G  S  E   | G  T  C  S  C  S      p.1180

          .         .         .         .         .         .       g.86100
 TCTAAGGGTTTCTCCACCACGTGTCCAGCCCACGTCGATGACCTAACTCCAGAACAAGTC       c.3600
 S  K  G  F  S  T  T  C  P  A  H  V  D  D  L  T  P  E  Q  V         p.1200

         | 25.         .         .         .         .         .    g.88852
 CTGGATG | GGGATGTAAATGAGCTGATGGATGTAGTTCTCCACCATGTTCCAGAGGCAAAG    c.3660
 L  D  G |   D  V  N  E  L  M  D  V  V  L  H  H  V  P  E  A  K      p.1220

          .         .         .         .         .         .       g.88912
 CTGGTGGAGTGCATTGGTCAAGAACTTATCTTCCTTCTTCCAAATAAGAACTTCAAGCAC       c.3720
 L  V  E  C  I  G  Q  E  L  I  F  L  L  P  N  K  N  F  K  H         p.1240

          .         .         .         .         .         .       g.88972
 AGAGCATATGCCAGCCTTTTCAGAGAGCTGGAGGAGACGCTGGCTGACCTTGGTCTCAGC       c.3780
 R  A  Y  A  S  L  F  R  E  L  E  E  T  L  A  D  L  G  L  S         p.1260

          .         .         .    | 26    .         .         .    g.89388
 AGTTTTGGAATTTCTGACACTCCCCTGGAAGAG | ATTTTTCTGAAGGTCACGGAGGATTCT    c.3840
 S  F  G  I  S  D  T  P  L  E  E   | I  F  L  K  V  T  E  D  S      p.1280

          .         .   | 27     .         .         .         .    g.94144
 GATTCAGGACCTCTGTTTGCGG | GTGGCGCTCAGCAGAAAAGAGAAAACGTCAACCCCCGA    c.3900
 D  S  G  P  L  F  A  G |   G  A  Q  Q  K  R  E  N  V  N  P  R      p.1300

          .         .         .         .         .         .       g.94204
 CACCCCTGCTTGGGTCCCAGAGAGAAGGCTGGACAGACACCCCAGGACTCCAATGTCTGC       c.3960
 H  P  C  L  G  P  R  E  K  A  G  Q  T  P  Q  D  S  N  V  C         p.1320

          .         .         .         .         .         .       g.94264
 TCCCCAGGGGCGCCGGCTGCTCACCCAGAGGGCCAGCCTCCCCCAGAGCCAGAGTGCCCA       c.4020
 S  P  G  A  P  A  A  H  P  E  G  Q  P  P  P  E  P  E  C  P         p.1340

          .         .         .         .         .         .       g.94324
 GGCCCGCAGCTCAACACGGGGACACAGCTGGTCCTCCAGCATGTGCAGGCGCTGCTGGTC       c.4080
 G  P  Q  L  N  T  G  T  Q  L  V  L  Q  H  V  Q  A  L  L  V         p.1360

          .         .         .         .         | 28         .    g.95041
 AAGAGATTCCAACACACCATCCGCAGCCACAAGGACTTCCTGGCGCAG | ATCGTGCTCCCG    c.4140
 K  R  F  Q  H  T  I  R  S  H  K  D  F  L  A  Q   | I  V  L  P      p.1380

          .         .         .         .         .         .       g.95101
 GCTACCTTTGTGTTTTTGGCTCTGATGCTTTCTATTGTTATCCCTCCTTTTGGCGAATAC       c.4200
 A  T  F  V  F  L  A  L  M  L  S  I  V  I  P  P  F  G  E  Y         p.1400

          .         .         .         .         .    | 29    .    g.95630
 CCCGCTTTGACCCTTCACCCCTGGATATATGGGCAGCAGTACACCTTCTTCAG | CATGGAT    c.4260
 P  A  L  T  L  H  P  W  I  Y  G  Q  Q  Y  T  F  F  S  |  M  D      p.1420

          .         .         .         .         .         .       g.95690
 GAACCAGGCAGTGAGCAGTTCACGGTACTTGCAGACGTCCTCCTGAATAAGCCAGGCTTT       c.4320
 E  P  G  S  E  Q  F  T  V  L  A  D  V  L  L  N  K  P  G  F         p.1440

          .         .         .   | 30     .         .         .    g.96546
 GGCAACCGCTGCCTGAAGGAAGGGTGGCTTCC | GGAGTACCCCTGTGGCAACTCAACACCC    c.4380
 G  N  R  C  L  K  E  G  W  L  P  |  E  Y  P  C  G  N  S  T  P      p.1460

          .         .         .         .         .         .       g.96606
 TGGAAGACTCCTTCTGTGTCCCCAAACATCACCCAGCTGTTCCAGAAGCAGAAATGGACA       c.4440
 W  K  T  P  S  V  S  P  N  I  T  Q  L  F  Q  K  Q  K  W  T         p.1480

          .         .         .         .         .         .       g.96666
 CAGGTCAACCCTTCACCATCCTGCAGGTGCAGCACCAGGGAGAAGCTCACCATGCTGCCA       c.4500
 Q  V  N  P  S  P  S  C  R  C  S  T  R  E  K  L  T  M  L  P         p.1500

          .         .         .          | 31        .         .    g.101122
 GAGTGCCCCGAGGGTGCCGGGGGCCTCCCGCCCCCCCAG | AGAACACAGCGCAGCACGGAA    c.4560
 E  C  P  E  G  A  G  G  L  P  P  P  Q   | R  T  Q  R  S  T  E      p.1520

          .         .         .         .         .         .       g.101182
 ATTCTACAAGACCTGACGGACAGGAACATCTCCGACTTCTTGGTAAAAACGTATCCTGCT       c.4620
 I  L  Q  D  L  T  D  R  N  I  S  D  F  L  V  K  T  Y  P  A         p.1540

          .     | 32   .         .         .        | 33.         . g.104211
 CTTATAAGAAGCAG | CTTAAAGAGCAAATTCTGGGTCAATGAACAGAG | GTATGGAGGAATT c.4680
 L  I  R  S  S  |  L  K  S  K  F  W  V  N  E  Q  R  |  Y  G  G  I   p.1560

          .         .         .         .         .         .       g.104271
 TCCATTGGAGGAAAGCTCCCAGTCGTCCCCATCACGGGGGAAGCACTTGTTGGGTTTTTA       c.4740
 S  I  G  G  K  L  P  V  V  P  I  T  G  E  A  L  V  G  F  L         p.1580

          .         .         .    | 34    .         .         .    g.104462
 AGCGACCTTGGCCGGATCATGAATGTGAGCGGG | GGCCCTATCACTAGAGAGGCCTCTAAA    c.4800
 S  D  L  G  R  I  M  N  V  S  G   | G  P  I  T  R  E  A  S  K      p.1600

          .         .         .         .         | 35         .    g.104752
 GAAATACCTGATTTCCTTAAACATCTAGAAACTGAAGACAACATTAAG | GTGTGGTTTAAT    c.4860
 E  I  P  D  F  L  K  H  L  E  T  E  D  N  I  K   | V  W  F  N      p.1620

          .         .         .         .         .         .       g.104812
 AACAAAGGCTGGCATGCCCTGGTCAGCTTTCTCAATGTGGCCCACAACGCCATCTTACGG       c.4920
 N  K  G  W  H  A  L  V  S  F  L  N  V  A  H  N  A  I  L  R         p.1640

          .         .         .         .         .         .       g.104872
 GCCAGCCTGCCTAAGGACAGGAGCCCCGAGGAGTATGGAATCACCGTCATTAGCCAACCC       c.4980
 A  S  L  P  K  D  R  S  P  E  E  Y  G  I  T  V  I  S  Q  P         p.1660

          .         .         .         | 36         .         .    g.106412
 CTGAACCTGACCAAGGAGCAGCTCTCAGAGATTACAGT | GCTGACCACTTCAGTGGATGCT    c.5040
 L  N  L  T  K  E  Q  L  S  E  I  T  V  |  L  T  T  S  V  D  A      p.1680

          .         .         .         .         .         .       g.106472
 GTGGTTGCCATCTGCGTGATTTTCTCCATGTCCTTCGTCCCAGCCAGCTTTGTCCTTTAT       c.5100
 V  V  A  I  C  V  I  F  S  M  S  F  V  P  A  S  F  V  L  Y         p.1700

          .         .         .         .         .         .       g.106532
 TTGATCCAGGAGCGGGTGAACAAATCCAAGCACCTCCAGTTTATCAGTGGAGTGAGCCCC       c.5160
 L  I  Q  E  R  V  N  K  S  K  H  L  Q  F  I  S  G  V  S  P         p.1720

          .         .         .       | 37 .         .         .    g.110319
 ACCACCTACTGGGTGACCAACTTCCTCTGGGACATC | ATGAATTATTCCGTGAGTGCTGGG    c.5220
 T  T  Y  W  V  T  N  F  L  W  D  I   | M  N  Y  S  V  S  A  G      p.1740

          .         .         .         .         .         .       g.110379
 CTGGTGGTGGGCATCTTCATCGGGTTTCAGAAGAAAGCCTACACTTCTCCAGAAAACCTT       c.5280
 L  V  V  G  I  F  I  G  F  Q  K  K  A  Y  T  S  P  E  N  L         p.1760

          .         .         .   | 38     .         .         .    g.111487
 CCTGCCCTTGTGGCACTGCTCCTGCTGTATGG | ATGGGCGGTCATTCCCATGATGTACCCA    c.5340
 P  A  L  V  A  L  L  L  L  Y  G  |  W  A  V  I  P  M  M  Y  P      p.1780

          .         .         .         .         .         .       g.111547
 GCATCCTTCCTGTTTGATGTCCCCAGCACAGCCTATGTGGCTTTATCTTGTGCTAATCTG       c.5400
 A  S  F  L  F  D  V  P  S  T  A  Y  V  A  L  S  C  A  N  L         p.1800

          .         .         .         .         .         .       g.111607
 TTCATCGGCATCAACAGCAGTGCTATTACCTTCATCTTGGAATTATTTGAGAATAACCGG       c.5460
 F  I  G  I  N  S  S  A  I  T  F  I  L  E  L  F  E  N  N  R         p.1820

  | 39       .         .         .         .         .         .    g.114824
  | ACGCTGCTCAGGTTCAACGCCGTGCTGAGGAAGCTGCTCATTGTCTTCCCCCACTTCTGC    c.5520
  | T  L  L  R  F  N  A  V  L  R  K  L  L  I  V  F  P  H  F  C      p.1840

          .         .         .         .         .         .       g.114884
 CTGGGCCGGGGCCTCATTGACCTTGCACTGAGCCAGGCTGTGACAGATGTCTATGCCCGG       c.5580
 L  G  R  G  L  I  D  L  A  L  S  Q  A  V  T  D  V  Y  A  R         p.1860

      | 40   .         .         .         .         .         .    g.115276
 TTTG | GTGAGGAGCACTCTGCAAATCCGTTCCACTGGGACCTGATTGGGAAGAACCTGTTT    c.5640
 F  G |   E  E  H  S  A  N  P  F  H  W  D  L  I  G  K  N  L  F      p.1880

          .         .         .         .         .         .       g.115336
 GCCATGGTGGTGGAAGGGGTGGTGTACTTCCTCCTGACCCTGCTGGTCCAGCGCCACTTC       c.5700
 A  M  V  V  E  G  V  V  Y  F  L  L  T  L  L  V  Q  R  H  F         p.1900

          .     | 41   .         .         .         .         .    g.117324
 TTCCTCTCCCAATG | GATTGCCGAGCCCACTAAGGAGCCCATTGTTGATGAAGATGATGAT    c.5760
 F  L  S  Q  W  |  I  A  E  P  T  K  E  P  I  V  D  E  D  D  D      p.1920

          .         .         .         .         .         .       g.117384
 GTGGCTGAAGAAAGACAAAGAATTATTACTGGTGGAAATAAAACTGACATCTTAAGGCTA       c.5820
 V  A  E  E  R  Q  R  I  I  T  G  G  N  K  T  D  I  L  R  L         p.1940

          .      | 42  .         .         .         .         .    g.117897
 CATGAACTAACCAAG | ATTTATCCAGGCACCTCCAGCCCAGCAGTGGACAGGCTGTGTGTC    c.5880
 H  E  L  T  K   | I  Y  P  G  T  S  S  P  A  V  D  R  L  C  V      p.1960

          .         | 43         .         .         .         .    g.118451
 GGAGTTCGCCCTGGAGAG | TGCTTTGGCCTCCTGGGAGTGAATGGTGCCGGCAAAACAACC    c.5940
 G  V  R  P  G  E   | C  F  G  L  L  G  V  N  G  A  G  K  T  T      p.1980

          .         .         .         .         .         .       g.118511
 ACATTCAAGATGCTCACTGGGGACACCACAGTGACCTCAGGGGATGCCACCGTAGCAGGC       c.6000
 T  F  K  M  L  T  G  D  T  T  V  T  S  G  D  A  T  V  A  G         p.2000

       | 44  .         .         .         .         .         .    g.120622
 AAGAG | TATTTTAACCAATATTTCTGAAGTCCATCAAAATATGGGCTACTGTCCTCAGTTT    c.6060
 K  S  |  I  L  T  N  I  S  E  V  H  Q  N  M  G  Y  C  P  Q  F      p.2020

          .         .         .         .         .         .       g.120682
 GATGCAATTGATGAGCTGCTCACAGGACGAGAACATCTTTACCTTTATGCCCGGCTTCGA       c.6120
 D  A  I  D  E  L  L  T  G  R  E  H  L  Y  L  Y  A  R  L  R         p.2040

          .         .        | 45.         .         .         .    g.124190
 GGTGTACCAGCAGAAGAAATCGAAAAG | GTTGCAAACTGGAGTATTAAGAGCCTGGGCCTG    c.6180
 G  V  P  A  E  E  I  E  K   | V  A  N  W  S  I  K  S  L  G  L      p.2060

          .         .         .         .         .         .       g.124250
 ACTGTCTACGCCGACTGCCTGGCTGGCACGTACAGTGGGGGCAACAAGCGGAAACTCTCC       c.6240
 T  V  Y  A  D  C  L  A  G  T  Y  S  G  G  N  K  R  K  L  S         p.2080

          .         .         .         .   | 46     .         .    g.125062
 ACAGCCATCGCACTCATTGGCTGCCCACCGCTGGTGCTGCTG | GATGAGCCCACCACAGGG    c.6300
 T  A  I  A  L  I  G  C  P  P  L  V  L  L   | D  E  P  T  T  G      p.2100

          .         .         .         .         .         .       g.125122
 ATGGACCCCCAGGCACGCCGCATGCTGTGGAACGTCATCGTGAGCATCATCAGAGAAGGG       c.6360
 M  D  P  Q  A  R  R  M  L  W  N  V  I  V  S  I  I  R  E  G         p.2120

          .         .       | 47 .         .         .         .    g.125255
 AGGGCTGTGGTCCTCACATCCCACAG | CATGGAAGAATGTGAGGCACTGTGTACCCGGCTG    c.6420
 R  A  V  V  L  T  S  H  S  |  M  E  E  C  E  A  L  C  T  R  L      p.2140

          .         .         .         .         .          | 48    g.128040
 GCCATCATGGTAAAGGGCGCCTTTCGATGTATGGGCACCATTCAGCATCTCAAGTCCAA | A    c.6480
 A  I  M  V  K  G  A  F  R  C  M  G  T  I  Q  H  L  K  S  K  |      p.2160

          .         .         .         .         .         .       g.128100
 TTTGGAGATGGCTATATCGTCACAATGAAGATCAAATCCCCGAAGGACGACCTGCTTCCT       c.6540
 F  G  D  G  Y  I  V  T  M  K  I  K  S  P  K  D  D  L  L  P         p.2180

          .         .         .         .         .         .       g.128160
 GACCTGAACCCTGTGGAGCAGTTCTTCCAGGGGAACTTCCCAGGCAGTGTGCAGAGGGAG       c.6600
 D  L  N  P  V  E  Q  F  F  Q  G  N  F  P  G  S  V  Q  R  E         p.2200

          .         .         .         .         .         .       g.128220
 AGGCACTACAACATGCTCCAGTTCCAGGTCTCCTCCTCCTCCCTGGCGAGGATCTTCCAG       c.6660
 R  H  Y  N  M  L  Q  F  Q  V  S  S  S  S  L  A  R  I  F  Q         p.2220

          .         .         .         .         .         .       g.128280
 CTCCTCCTCTCCCACAAGGACAGCCTGCTCATCGAGGAGTACTCAGTCACACAGACCACA       c.6720
 L  L  L  S  H  K  D  S  L  L  I  E  E  Y  S  V  T  Q  T  T         p.2240

           | 49        .         .         .         .         .    g.130005
 CTGGACCAG | GTGTTTGTAAATTTTGCTAAACAGCAGACTGAAAGTCATGACCTCCCTCTG    c.6780
 L  D  Q   | V  F  V  N  F  A  K  Q  Q  T  E  S  H  D  L  P  L      p.2260

          .         .         .       | 50 .                        g.132931
 CACCCTCGAGCTGCTGGAGCCAGTCGACAAGCCCAG | GACTGA                      c.6822
 H  P  R  A  A  G  A  S  R  Q  A  Q   | D  X                        p.2273

          .         .         .         .         .         .       g.132991
 tctttcacaccgctcgttcctgcagccagaaaggaactctgggcagctggaggcgcagga       c.*60

          .         .         .         .         .         .       g.133051
 gcctgtgcccatatggtcatccaaatggactggccagcgtaaatgaccccactgcagcag       c.*120

          .         .         .         .         .         .       g.133111
 aaaacaaacacacgaggagcatgcagcgaattcagaaagaggtctttcagaaggaaaccg       c.*180

          .         .         .         .         .         .       g.133171
 aaactgacttgctcacctggaacacctgatggtgaaaccaaacaaatacaaaatccttct       c.*240

          .         .         .         .         .         .       g.133231
 ccagaccccagaactagaaaccccgggccatcccactagcagctttggcctccatattgc       c.*300

          .         .         .         .         .         .       g.133291
 tctcatttcaagcagatctgcttttctgcatgtttgtctgtgtgtctgcgttgtgtgtga       c.*360

          .         .         .         .                           g.133331
 ttttcatggaaaaataaaatgcaaatgcactcatcacaaa                           c.*400

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The ATP-binding cassette, sub-family A (ABC1), member 4 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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