acyl-CoA dehydrogenase family, member 8 (ACAD8) - coding DNA reference sequence

(used for mutation description)

(last modified July 20, 2012)


This file was created to facilitate the description of sequence variants on transcript NM_014384.2 in the ACAD8 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000011.9, covering ACAD8 transcript NM_014384.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                                    g.5001
                                                            g       c.-61

 .         .         .         .         .         .                g.5061
 cgagcgcaacggaggtcgaaggcgttcagactcttagctgaacgcggagctgcggcggct       c.-1

          .         .         .         .         .         .       g.5121
 ATGCTGTGGAGCGGCTGCCGGCGTTTCGGGGCGCGCCTCGGCTGCCTGCCCGGCGGTCTC       c.60
 M  L  W  S  G  C  R  R  F  G  A  R  L  G  C  L  P  G  G  L         p.20

          .         .         .         .          | 02        .    g.8019
 CGGGTCCTCGTCCAGACCGGCCACCGGAGCTTGACCTCCTGCATCGACC | CTTCCATGGGA    c.120
 R  V  L  V  Q  T  G  H  R  S  L  T  S  C  I  D  P |   S  M  G      p.40

          .         .         .         .         .         .       g.8079
 CTTAATGAAGAGCAGAAAGAATTTCAAAAAGTGGCCTTTGACTTTGCTGCCCGAGAGATG       c.180
 L  N  E  E  Q  K  E  F  Q  K  V  A  F  D  F  A  A  R  E  M         p.60

          .         .         . | 03       .         .         .    g.8578
 GCTCCAAATATGGCAGAGTGGGACCAGAAG | GAGCTGTTCCCAGTGGATGTGATGCGGAAG    c.240
 A  P  N  M  A  E  W  D  Q  K   | E  L  F  P  V  D  V  M  R  K      p.80

          .         .         .         .         .         .       g.8638
 GCAGCCCAGCTAGGCTTCGGAGGGGTCTACATACAAACAGATGTGGGCGGGTCTGGGCTG       c.300
 A  A  Q  L  G  F  G  G  V  Y  I  Q  T  D  V  G  G  S  G  L         p.100

          .         .         .         .         .         .       g.8698
 TCACGTCTTGATACCTCTGTCATTTTTGAAGCCTTGGCTACAGGCTGCACCAGCACCACA       c.360
 S  R  L  D  T  S  V  I  F  E  A  L  A  T  G  C  T  S  T  T         p.120

          .         . | 04       .         .         .         .    g.10015
 GCCTATATAAGCATCCACAA | CATGTGTGCCTGGATGATTGATAGCTTCGGAAATGAGGAA    c.420
 A  Y  I  S  I  H  N  |  M  C  A  W  M  I  D  S  F  G  N  E  E      p.140

          .         .         .         .         .         .       g.10075
 CAGAGGCACAAATTTTGCCCACCGCTCTGTACCATGGAGAAGTTTGCTTCCTACTGCCTC       c.480
 Q  R  H  K  F  C  P  P  L  C  T  M  E  K  F  A  S  Y  C  L         p.160

          . | 05       .         .         .         .         .    g.10518
 ACTGAACCAG | GAAGTGGGAGTGATGCTGCCTCTCTTCTGACCTCCGCTAAGAAACAGGGA    c.540
 T  E  P  G |   S  G  S  D  A  A  S  L  L  T  S  A  K  K  Q  G      p.180

          .         .        | 06.         .         .         .    g.11101
 GATCATTACATCCTCAATGGCTCCAAG | GCCTTCATCAGTGGTGCTGGTGAGTCAGACATC    c.600
 D  H  Y  I  L  N  G  S  K   | A  F  I  S  G  A  G  E  S  D  I      p.200

          .         .         .         .         .         .       g.11161
 TATGTGGTCATGTGCCGAACAGGAGGACCAGGCCCCAAGGGCATCTCATGCATAGTTGTT       c.660
 Y  V  V  M  C  R  T  G  G  P  G  P  K  G  I  S  C  I  V  V         p.220

          .         .         .         .      | 07  .         .    g.12519
 GAGAAGGGGACCCCTGGCCTCAGCTTTGGCAAGAAGGAGAAAAAG | GTGGGGTGGAACTCC    c.720
 E  K  G  T  P  G  L  S  F  G  K  K  E  K  K   | V  G  W  N  S      p.240

          .         .         .         .         .         .       g.12579
 CAGCCAACACGAGCTGTGATCTTCGAAGACTGTGCTGTCCCTGTGGCCAACAGAATTGGG       c.780
 Q  P  T  R  A  V  I  F  E  D  C  A  V  P  V  A  N  R  I  G         p.260

          .         .         .         .         .         .       g.12639
 AGCGAGGGGCAGGGCTTCCTCATTGCCGTGAGAGGACTGAACGGAGGGAGGATCAATATT       c.840
 S  E  G  Q  G  F  L  I  A  V  R  G  L  N  G  G  R  I  N  I         p.280

   | 08      .         .         .         .         .         .    g.12794
 G | CTTCCTGCTCCCTGGGGGCTGCCCACGCCTCTGTCATCCTCACCCGAGACCACCTCAAT    c.900
 A |   S  C  S  L  G  A  A  H  A  S  V  I  L  T  R  D  H  L  N      p.300

          .         .         .          | 09        .         .    g.13219
 GTCCGGAAGCAGTTTGGAGAGCCTCTGGCCAGTAACCAG | TACTTGCAATTCACACTGGCT    c.960
 V  R  K  Q  F  G  E  P  L  A  S  N  Q   | Y  L  Q  F  T  L  A      p.320

          .         .         .         .         .         .       g.13279
 GATATGGCAACAAGGCTGGTGGCCGCGCGGCTGATGGTCCGCAATGCAGCAGTGGCTCTG       c.1020
 D  M  A  T  R  L  V  A  A  R  L  M  V  R  N  A  A  V  A  L         p.340

          .         .         .         .         .         .       g.13339
 CAGGAGGAGAGGAAGGATGCAGTGGCCTTGTGCTCCATGGCCAAGCTCTTTGCTACAGAT       c.1080
 Q  E  E  R  K  D  A  V  A  L  C  S  M  A  K  L  F  A  T  D         p.360

          .   | 10     .         .         .         .         .    g.14028
 GAATGCTTTGCC | ATCTGCAACCAGGCCTTGCAGATGCACGGGGGCTACGGCTACCTGAAG    c.1140
 E  C  F  A   | I  C  N  Q  A  L  Q  M  H  G  G  Y  G  Y  L  K      p.380

          .         .         .         .         .      | 11  .    g.16373
 GATTACGCTGTTCAGCAGTACGTGCGGGACTCCAGGGTCCACCAGATTCTAGAAG | GTAGC    c.1200
 D  Y  A  V  Q  Q  Y  V  R  D  S  R  V  H  Q  I  L  E  G |   S      p.400

          .         .         .         .                           g.16421
 AATGAAGTGATGAGGATACTGATCTCTAGAAGCCTGCTTCAGGAGTAG                   c.1248
 N  E  V  M  R  I  L  I  S  R  S  L  L  Q  E  X                     p.415

          .         .         .         .         .         .       g.16481
 aacccacacttgttctggcctggtgttcagtgcgactgcagtcagtgttgagtggtgcca       c.*60

          .         .         .         .         .         .       g.16541
 tgtgggccgctctattccaaaggaatcatggattagacccaagggctgagctcctctagg       c.*120

          .         .         .         .         .         .       g.16601
 gcaggacctgcaccctgtgtgttggcaccagcatcgggtcttggactggggcagaatccc       c.*180

          .         .         .         .         .         .       g.16661
 cagtggaaccggaagagctggactgatgagaaacatcagaagaacacatactaccttgtt       c.*240

          .         .         .         .         .         .       g.16721
 ttcctaatgccagaagggtgaccagtgaagattcaccgtcaaaccatgaaagtcctttct       c.*300

          .         .         .         .         .         .       g.16781
 tggatccactttatcttgattagtctgcattttactagttcactggatccctcctctagg       c.*360

          .         .         .         .         .         .       g.16841
 ggcctggggactttcactgatgctcttcctgattctagagcaaaggtgtgggaaggggaa       c.*420

          .         .         .         .         .         .       g.16901
 atggaggaatgccctcctgtctgtgtcgttctctgtgccacagctacagatgcagaaggt       c.*480

          .         .         .         .         .         .       g.16961
 ttctctggatagcacacctctgaatgtaaatcatgataaaatggatatttggaaacttac       c.*540

          .         .         .         .         .         .       g.17021
 tcctaagctgtgatttagggtgtatttctacttctggactgcctcaatatcaagggctga       c.*600

          .         .         .         .         .         .       g.17081
 gacttttgaattttgaatattcgttgggtttcatgttaagaagcctgtggtctaggagtg       c.*660

          .         .         .         .         .         .       g.17141
 ctattcagtgtttcttttcctgataaacactttgaatattttttttgtgtttttgtttcc       c.*720

          .         .         .         .         .         .       g.17201
 ttttctgaagctgttcctccttttaaatatttttaatcacattgataaaatctatccttc       c.*780

          .         .         .         .         .         .       g.17261
 accacctctggttctactatagttgatttttattttaaatgtttaattgtatttgattaa       c.*840

          .         .         .         .         .                 g.17316
 acacttaactggattttggaataataaaactctcgtccaatttggcttttaaaaa            c.*895

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Acyl-CoA dehydrogenase family, member 8 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift mutations, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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