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Phenotypes for disease #00469 (HPS (Hermansky-Pudlak syndrome))
Legend
Please note that a short description of a certain column can be displayed when you move your mouse cursor over the column's header and hold it still. Below, a more detailed description is shown per column.
Phenotype details
: additional information on the phenotype of the individual, preferably use HPO terms only (http://www.human-phenotype-ontology.org/)
Diagnosis/Initial
: initial diagnosis, before molecular testing
Diagnosis/Definite
: phenotype individual after molecular testing (OMIM abbreviation)
Inheritance
: Indicates the inheritance of the phenotype in the family; unknown, familial (autosomal/X-linked, dominant/ recessive), paternal (Y-linked), maternal (mitochondrial), isolated (sporadic) or complex
All options:
Unknown
Familial
Familial, autosomal dominant
Familial, autosomal recessive
Familial, X-linked
Familial, X-linked dominant
Familial, X-linked dominant, male sparing
Familial, X-linked recessive
Paternal, Y-linked
Maternal, mitochondrial
Isolated (sporadic)
Di-genic
Complex
- = Not applicable
Age/Examination
: age at which the individual was examined.
35y = 35 years
04y08m = 4 years and 8 months
00y00m01d12h = 1 day and 12 hours
18y? = around 18 years
30y-40y = between 30 and 40 years
>54y = older than 54
? = unknown
Age/Diagnosis
: age diagnosis was confirmed
35y = 35 years
04y08m = 4 years and 8 months
00y00m01d12h = 1 day and 12 hours
18y? = around 18 years
30y-40y = between 30 and 40 years
>54y = older than 54
? = unknown
Age/Onset
: Age first symptoms disease appeared in individual:
35y = 35 years
04y08m = 4 years and 8 months
00y00m01d12h = 1 day and 12 hours
18y? = around 18 years
30y-40y = between 30 and 40 years
>54y = older than 54
? = unknown
Phenotype/Onset
: individual's phenotype at Age/Onset described using HPO
Protein
: result from protein staining
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Text
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all entries containing 'Arg'
space
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Text
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!
Text
!fs
all entries not containing 'fs'
^
Text
^p.(Arg
all entries beginning with 'p.(Arg'
$
Text
Ser)$
all entries ending with 'Ser)'
=""
Text
=""
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Text
="p.0"
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combination
Text
*|Ter !fs
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Date
2020
all entries matching the year 2020
|
Date
2020-03|2020-04
all entries matching March or April, 2020
!
Date
!2020-03
all entries not matching March, 2020
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Date
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all entries before the year 2020
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Date
<=2020-06
all entries in or before June, 2020
>
Date
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all entries after June, 2020
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Date
>=2020-06-15
all entries on or after June 15th, 2020
combination
Date
2019|2020 <2020-03
all entries in 2019 or 2020, and before March, 2020
Numeric
23
all entries exactly matching 23
|
Numeric
23|24
all entries exactly matching 23 or 24
!
Numeric
!23
all entries not exactly matching 23
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Numeric
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all entries lower than 23
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Numeric
<=23
all entries lower than, or equal to, 23
>
Numeric
>23
all entries higher than 23
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Numeric
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all entries higher than, or equal to, 23
combination
Numeric
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all entries with values from 20 to 29, but not equal to 23
Some more advanced examples:
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all entries containing 'Asian', 'asian', including 'Caucasian', 'caucasian', etc.
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all entries containing 'Asian' but not containing 'Caucasian'
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all entries containing 'Asian' or 'African', but not containing 'Caucasian'
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all entries containing 'South Asian', but not containing 'South East Asian'
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50 entries on 1 page. Showing entries 1 - 50.
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Legend
How to query
Phenotype ID
Phenotype details
Diagnosis/Initial
Diagnosis/Definite
Inheritance
Age/Examination
Age/Diagnosis
Age/Onset
Phenotype/Onset
Protein
Owner
Individual ID
0000017255
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019454
0000017258
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019457
0000017259
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019458
0000017260
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019459
0000017261
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019460
0000017262
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019461
0000017263
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019462
0000017264
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019463
0000017265
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019464
0000017266
see paper; ...
Hermansky-Pudlak syndrome
HPS6
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019465
0000017267
see paper; ..., oculocutaneous albinism, frequent prolonged nosebleeds, prolonged bleeding after dental extractions and surgery, no pulmonary or gastrointestinal symptoms, platelet count normal
Hermansky-Pudlak syndrome
HPS6
Familial, autosomal recessive
39y
-
-
-
-
William (Bill) Oetting
00019466
0000017268
see paper; ...
Hermansky-Pudlak syndrome
HPS6
Familial, autosomal recessive
36y
-
-
-
-
William (Bill) Oetting
00019467
0000017269
see paper; ...
Hermansky-Pudlak syndrome
HPS6
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019468
0000017270
see paper; ...
Hermansky-Pudlak syndrome
HPS6
Familial, autosomal recessive
22y
-
-
-
-
William (Bill) Oetting
00019469
0000017271
see paper; ...
Hermansky-Pudlak syndrome
HPS6
Familial, autosomal recessive
56y
-
-
-
-
William (Bill) Oetting
00019470
0000017272
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019471
0000017273
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019472
0000017274
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019473
0000017275
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019474
0000017276
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019475
0000017277
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019476
0000017278
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019477
0000017279
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019478
0000017280
see paper; ...
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019479
0000017281
see paper; ...
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019480
0000017282
see paper; ...
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019481
0000017283
see paper; ...
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019482
0000017284
see paper; ...
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019483
0000017285
see paper; ...
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019484
0000017286
see paper; ...
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00019485
0000017287
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019486
0000017288
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019487
0000017289
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019488
0000017290
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019489
0000017291
lethal hemophagocytic lymphohistiocytosis
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019490
0000017292
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019491
0000017293
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019492
0000017294
-
-
-
Unknown
-
-
-
-
-
William (Bill) Oetting
00019493
0000069492
see paper; …
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00090119
0000069493
see paper; …
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00090120
0000069494
see paper; …
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00090121
0000069495
see paper; …
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00090122
0000069496
see paper; …
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00090123
0000069498
see paper; …
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00090124
0000069499
see paper; …
-
-
Familial, autosomal recessive
-
-
-
-
-
William (Bill) Oetting
00090125
0000167088
HPS
-
-
Unknown
-
-
-
-
-
Karl Heinimann
00218606
0000167089
HPS
-
-
Unknown
-
-
-
-
-
Karl Heinimann
00218607
0000167289
HPS
-
-
Unknown
-
-
-
-
-
Karl Heinimann
00218753
0000273528
HP:0032122, HP:0000613, HP:0001123, HP:0000639, HP:0000007, HP:0007443, HP:0007750, HP:0000978
Hermansky-Pudlak syndrome (HPS)
-
Familial, autosomal recessive
-
-
-
-
-
Jinu Han
00379684
0000325304
2 sisters also affected with Hermansky-Pudlak syndrome
Hermansky-Pudlak syndrome
HPS1
Familial, autosomal recessive
-
-
-
-
-
Johan den Dunnen
00410806
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