Global Variome shared LOVD
G6PC3 (glucose 6 phosphatase, catalytic, 3)
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Phenotypes for disease #02784 (MCPH5 (microcephaly, type 5, autosomal recessive (MCPH-5)), OMIM:608716)
Legend
Please note that a short description of a certain column can be displayed when you move your mouse cursor over the column's header and hold it still. Below, a more detailed description is shown per column.
Phenotype details
: additional information on the phenotype of the individual, preferably use HPO terms only (http://www.human-phenotype-ontology.org/)
Diagnosis/Initial
: initial diagnosis, before molecular testing
Diagnosis/Definite
: phenotype individual after molecular testing (OMIM abbreviation)
Inheritance
: Indicates the inheritance of the phenotype in the family; unknown, familial (autosomal/X-linked, dominant/ recessive), paternal (Y-linked), maternal (mitochondrial), isolated (sporadic) or complex
All options:
Unknown
Familial
Familial, autosomal dominant
Familial, autosomal recessive
Familial, X-linked
Familial, X-linked dominant
Familial, X-linked dominant, male sparing
Familial, X-linked recessive
Paternal, Y-linked
Maternal, mitochondrial
Isolated (sporadic)
Di-genic
Complex
- = Not applicable
Age/Examination
: age at which the individual was examined.
35y = 35 years
04y08m = 4 years and 8 months
00y00m01d12h = 1 day and 12 hours
18y? = around 18 years
30y-40y = between 30 and 40 years
>54y = older than 54
? = unknown
Age/Diagnosis
: age diagnosis was confirmed
35y = 35 years
04y08m = 4 years and 8 months
00y00m01d12h = 1 day and 12 hours
18y? = around 18 years
30y-40y = between 30 and 40 years
>54y = older than 54
? = unknown
Age/Onset
: Age first symptoms disease appeared in individual:
35y = 35 years
04y08m = 4 years and 8 months
00y00m01d12h = 1 day and 12 hours
18y? = around 18 years
30y-40y = between 30 and 40 years
>54y = older than 54
? = unknown
Phenotype/Onset
: individual's phenotype at Age/Onset described using HPO
Protein
: result from protein staining
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25 entries on 1 page. Showing entries 1 - 25.
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How to query
Phenotype ID
Phenotype details
Diagnosis/Initial
Diagnosis/Definite
Inheritance
Age/Examination
Age/Diagnosis
Age/Onset
Phenotype/Onset
Protein
Owner
Individual ID
0000044549
brain magnetic resonance imaging: not available; additional clinical featuresmild intellectual disability, seizures, behavioural problems (brother with intellectual disability and microcephaly)
microcephaly
MCPH5
Familial, autosomal recessive
31y
-
-
-
-
Birgit Sikkema-Raddatz
00057250
0000044554
microcephaly; brain magnetic resonance imaging: simplified gyral pattern; additional clinical featuresseizures, behavioural problems, short stature, obesity, severe intellectual disability
microcephaly
MCPH5
Familial, autosomal recessive
14y
-
-
-
-
Birgit Sikkema-Raddatz
00057267
0000060512
Microcephaly 5, primary, autosomal recessive (OMIM:608716)
-
-
Familial, autosomal recessive
-
-
-
-
-
Daniel Trujillano
00080943
0000060570
Microcephaly 5, primary, autosomal recessive (OMIM:608716)
-
-
Familial, autosomal recessive
-
-
-
-
-
Daniel Trujillano
00081001
0000104277
ultrasound microcephaly second trimester pregnancy; birth OFC (SD-7.5), length (SD-1), weight (SD-1.6); OFC (SD-10), length (SD-5.8), weight (SD-1.3); <18m-no walk; speech <3y no first senteence; no epilepsy; MRI brain -slight cortical atrophy; hyperactivity
microcephaly
MCPH5
Familial, autosomal recessive
11.7y
-
-
-
-
Nathalie Pouvreau
00132087
0000104278
birth OFC (SD-6.7), length (SD-5.2), weight (SD-3.2); OFC (SD-5.8), length (SD-1), weight (SD-1.4); no epilepsy; MRI brain 0.6y-gyral simplification; thin corpus callosum; subcortical hypersignal on T2-weighted images; hyperpigmentation spot
microcephaly
MCPH5
Familial, autosomal recessive
0.6y
-
-
-
-
Nathalie Pouvreau
00132088
0000104280
birth OFC (SD-3.8), length (SD-1.5), weight (SD-0.9); OFC (SD-7.5), length (SD-2.5), weight (SD-2.8); <18m-no walk; no epilepsy; MRI brain 0.5y-gyral simplification; behavioral disorders
microcephaly
MCPH5
Familial, autosomal recessive
1.7y
-
-
-
-
Nathalie Pouvreau
00132089
0000104281
ultrasound no microcephaly; birth OFC (SD-3.4), length (SD0), weight (SD+1.1); OFC (SD-4.1), length (SD-0.8), weight (SD+0.9); <18m-no walk; speech <3y no first senteence; no epilepsy
microcephaly
MCPH5
Familial, autosomal recessive
20y
-
-
-
-
Nathalie Pouvreau
00132090
0000104282
birth weight (SD-1.5); OFC (SD-10.6), length (SD-2.2), weight (SD-2.5); <18m-no walk; speech <3y no first senteence; no epilepsy; MRI brain gyral simplification; corpus callosum hypoplasia; congenital hip dislocation
microcephaly
MCPH5
Familial, autosomal recessive
07y
-
-
-
-
Nathalie Pouvreau
00132091
0000104314
birth OFC (SD-6.6), length (SD-2.5), weight (SD-2.2); OFC (SD-9.5), length (SD-0.8), weight (SD-0.8); <4y-epilepsy
microcephaly
MCPH5
Familial, autosomal recessive
07y
-
-
-
-
Nathalie Pouvreau
00132121
0000104316
ultrasound microcephaly third trimester pregnancy; birth OFC (SD-4.5), length (SD-0.2), weight (SD-0.7); OFC (SD-8.5), length (SD-0.2), weight (SD-0.4); <18m-walk; speech <3y no first senteence; 14y-epilepsy; MRI brain 0.8y-gyral simplification, mild ventricular enlargement; scaphocephaly; behavioral disorders
microcephaly
MCPH5
Familial, autosomal recessive
19y
-
-
-
-
Nathalie Pouvreau
00132122
0000104336
birth OFC (SD-2.7), length (SD-0.5), weight (SD-1); OFC (SD-3.4); <18m-walk; no epilepsy; 3y6m-Bayley III DQ95; MRI brain 1.7y-gyral simplification; arachnoid cyst in the posterior fossa; enlarged Virchow-Robin spaces
microcephaly
MCPH5
Familial, autosomal recessive
03y
-
-
-
-
Nathalie Pouvreau
00132123
0000104337
OFC (SD-7.2), length (SD-3.7), weight (SD-1.9); no epilepsy; 7y-Stanford Binet DQ56; MRI brain 7y-gyral simplification, mild ventricular enlargement, thin corpus callosum and brainstem
microcephaly
MCPH5
Familial, autosomal recessive
07y
-
-
-
-
Nathalie Pouvreau
00132143
0000104338
ultrasound microcephaly third trimester pregnancy; birth OFC (SD-4.7), length (SD-2.5), weight (SD-2); OFC (SD-6.4), length (SD-0.6), weight (SD-0.4); <18m-walk; speech <3y no first senteence; no epilepsy; WPPSI-III (5.5): FSIQ = 82*/ VIQ = 75/ PIQ = 90/ GCL = 77; MRI brain 5.5y-white matter hypersignal in T2-weighted images, ventricular enlargement
microcephaly
MCPH5
Familial, autosomal recessive
5.5y
-
-
-
-
Nathalie Pouvreau
00132144
0000104339
ultrasound microcephaly third trimester pregnancy; OFC (SD-8.5), length (SD+0.5); <18m-walk; speech <3y first senteence; 6m-epilepsy; hyperactivity, enuresis
microcephaly
MCPH5
Familial, autosomal recessive
09y
-
-
-
-
Nathalie Pouvreau
00132145
0000104340
ultrasound no microcephaly; birth OFC (SD-4), length (SD-1.3), weight (SD-1.5); OFC (SD-5.5), length (SD+0.7), weight (SD+1.1); <18m-no walk; speech <3y no first senteence; no epilepsy; MRI brain 0.5y-gyral simplification, enlarged subarachnoid spaces, mega cisterna magna
microcephaly
MCPH5
Familial, autosomal recessive
5.5y
-
-
-
-
Nathalie Pouvreau
00132146
0000104461
ultrasound microcephaly second and third trimester pregnancy; birth OFC (SD-3.8), length (SD-1), weight (SD+0.2); OFC (SD-6), length (SD2), weight (SD+1); <18m-walk; no epilepsy; behavioral disorders
microcephaly
MCPH5
Familial, autosomal recessive
01y
-
-
-
-
Nathalie Pouvreau
00132271
0000104462
ultrasound microcephaly third trimester pregnancy; birth OFC (SD-8.4), length (SD-2.6), weight (SD-4); OFC (SD-6.9), length (SD-1.5), weight (SD-1.6); <18m-no walk; speech <3y no first senteence; 7y-epilepsy; 4y6m-Borel-Maisonny DQ56; MRI brain 9y-slight left cerebral atrophy; cervicothoracic syringomyelia; spastic hemiplegic cerebral palsy, severe behavioral disorders
microcephaly
MCPH5
Familial, autosomal recessive
17.5y
-
-
-
-
Nathalie Pouvreau
00132272
0000105060
ultrasound no microcephaly; birth OFC (SD-7.2), length (SD-1.1), weight (SD-0.3); OFC (SD-7), length (SD-3), weight (SD-2.2); <18m-no walk; speech <3y no first senteence; 1y6m-epilepsy; MRI brain 0.3y-gyral simplification, thin corpus callosum, pineal cyst, large arachnoid cyst in the posterior fossa; left middle ear hypoplasia, behavioral disorders
microcephaly
MCPH5
Familial, autosomal recessive
3.3y
-
-
-
-
Nathalie Pouvreau
00132276
0000105061
ultrasound microcephaly second and third trimester pregnancy; birth OFC (SD-4.3), length (SD-0.5), weight (SD0); OFC (SD-5.6), length (SD-1.4), weight (SD-1.7); <18m-walk; speech <3y no first senteence; 6y-epilepsy; 9y3m-DQ34; MRI brain 7y-gyral simplification, polymicrogyria in fronto-insular region
microcephaly
MCPH5
Familial, autosomal recessive
07y
-
-
-
-
Nathalie Pouvreau
00132277
0000105063
OFC (SD-6.3); <18m-no walk; 7y-epilepsy; MRI brain 45y-gyral simplification; mild ventricular enlargement; mega cisterna magna; hypersignal of the temporal poles in T2-weighted images; thin brainstem; major vermis and cerebellar atrophy; ceroid lipofuscinosis with identified CLN3 mutations (retinitis pigmentosa)
microcephaly
MCPH5
Familial, autosomal recessive
45y
-
-
-
-
Nathalie Pouvreau
00132279
0000105065
OFC (SD-10.8), length (SD-3.9), weight (SD-3.1); <18m-no walk; no epilepsy; MRI brain 4.3y-thick frontal gyri, gyral simplification; thick corpus callosum; extensive bilateral posterior polymicrogyria; spastic tetraplegia
microcephaly
MCPH5
Familial, autosomal recessive
04y
-
-
-
-
Nathalie Pouvreau
00132281
0000105066
ultrasound no microcephaly; OFC (SD-4.3), length (SD-2), weight (SD-1.2); <18m-walk; speech <3y no first senteence; no epilepsy
microcephaly
MCPH5
Familial, autosomal recessive
17y
-
-
-
-
Nathalie Pouvreau
00132282
0000105068
ultrasound microcephaly third trimester pregnancy; birth OFC (SD-3.8), length (SD-1), weight (SD-0.8); OFC (SD-5.6), length (SD+1.5), weight (SD+0.6); <18m-no walk; speech <3y no first senteence; no epilepsy; WPPSI-III (3.7): FSIQ = 60*/ VIQ = 74/ PIQ = 54/ GCL = 85; MRI brain 3.7y-ventricular enlargement, cerebellar hypoplasia, subcortical hypersignal on T2-weighted images, elongated superior cerebellar peduncles
microcephaly
MCPH5
Familial, autosomal recessive
3.7y
-
-
-
-
Nathalie Pouvreau
00132284
0000350783
Moderate to late preterm birth, Short chin, Small for gestational age, Microcephaly, Inguinal hernia, Abnormality of temperature regulation
-
-
Familial, autosomal recessive
00y02m
-
-
-
-
Andreas Laner
00465248
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