ATP-binding cassette, sub-family A (ABC1), member 2 (ABCA2) - coding DNA reference sequence

(used for variant description)

(last modified May 22, 2020)


This file was created to facilitate the description of sequence variants on transcript NM_212533.2 in the ABCA2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_011789.1, covering ABCA2 transcript NM_212533.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
           .         .         .         .         .                g.5050
           agaaccgcctgatcccgaactccctgtgcagagaccagactcgcccgaat       c.-1

          .         .         .         .         .         .       g.5110
 ATGGGGAGAAAAACGAGCCGCGTGCAGCAGGGGCCGCCTCGGTCCCCTGCCTGCTCCGCT       c.60
 M  G  R  K  T  S  R  V  Q  Q  G  P  P  R  S  P  A  C  S  A         p.20

          .         .         .         .         .         .       g.5170
 CACGGCGAGCGTTCCTGGGGCCTCGAGTTTCCCCCCTTCCGCTGGCTGCTCGGAATCGCG       c.120
 H  G  E  R  S  W  G  L  E  F  P  P  F  R  W  L  L  G  I  A         p.40

          .         .         .       | 02 .         .         .    g.9710
 GGACGGACCCACCTGGCCGCCCTGCCTCCCTTCCAG | TGGGTCCTGGCCTTCGAGATCTTC    c.180
 G  R  T  H  L  A  A  L  P  P  F  Q   | W  V  L  A  F  E  I  F      p.60

          .         .         .         .         .         .       g.9770
 ATCCCCCTGGTGCTGTTCTTTATCCTGCTGGGGCTGCGACAGAAGAAGCCCACCATCTCC       c.240
 I  P  L  V  L  F  F  I  L  L  G  L  R  Q  K  K  P  T  I  S         p.80

          . | 03  | 04    .         .         .         .         . g.10917
 GTGAAGGAAG | TCT | CCTTCTACACAGCGGCGCCCCTGACGTCTGCCGGCATCCTGCCTGTC c.300
 V  K  E  V |   S |   F  Y  T  A  A  P  L  T  S  A  G  I  L  P  V   p.100

          .         .         .         .         .         .       g.10977
 ATGCAATCGCTGTGCCCGGACGGCCAGCGAGACGAGTTCGGCTTCCTGCAGTACGCCAAC       c.360
 M  Q  S  L  C  P  D  G  Q  R  D  E  F  G  F  L  Q  Y  A  N         p.120

       | 05  .         .         .         .         .         .    g.11112
 TCCAC | GGTCACGCAGCTGCTTGAGCGCCTGGACCGCGTGGTGGAGGAAGGCAACCTGTTT    c.420
 S  T  |  V  T  Q  L  L  E  R  L  D  R  V  V  E  E  G  N  L  F      p.140

          .         .         .         .         .         .       g.11172
 GACCCAGCGCGGCCCAGCCTGGGCTCAGAGCTCGAGGCCCTACGCCAGCATCTGGAGGCC       c.480
 D  P  A  R  P  S  L  G  S  E  L  E  A  L  R  Q  H  L  E  A         p.160

          .         .         .         .          | 06        .    g.11455
 CTCAGTGCGGGCCCGGGCACCTCGGGGAGCCACCTGGACAGATCCACAG | TGTCTTCCTTC    c.540
 L  S  A  G  P  G  T  S  G  S  H  L  D  R  S  T  V |   S  S  F      p.180

          .         .         .         .         .         .       g.11515
 TCTCTGGACTCGGTGGCCAGAAACCCGCAGGAGCTCTGGCGTTTCCTGACGCAAAACTTG       c.600
 S  L  D  S  V  A  R  N  P  Q  E  L  W  R  F  L  T  Q  N  L         p.200

          .         .         .         .         .        | 07.    g.11924
 TCGCTGCCCAATAGCACGGCCCAAGCACTCTTGGCCGCCCGTGTGGACCCGCCCGAG | GTC    c.660
 S  L  P  N  S  T  A  Q  A  L  L  A  A  R  V  D  P  P  E   | V      p.220

          .         .         .         .         .         .       g.11984
 TACCACCTGCTCTTTGGTCCCTCATCTGCCCTGGATTCACAGTCTGGCCTCCACAAGGGT       c.720
 Y  H  L  L  F  G  P  S  S  A  L  D  S  Q  S  G  L  H  K  G         p.240

          .         .         .         .         | 08         .    g.12324
 CAGGAGCCCTGGAGCCGCCTAGGGGGCAATCCCCTGTTCCGGATGGAG | GAGCTGCTGCTG    c.780
 Q  E  P  W  S  R  L  G  G  N  P  L  F  R  M  E   | E  L  L  L      p.260

          .         .         .         .         .         .       g.12384
 GCTCCTGCCCTCCTGGAGCAGCTCACCTGCACGCCGGGCTCGGGGGAGCTGGGCCGGATC       c.840
 A  P  A  L  L  E  Q  L  T  C  T  P  G  S  G  E  L  G  R  I         p.280

          .         .         .         .         .         .       g.12444
 CTCACTGTGCCTGAGAGTCAGAAGGGAGCCCTGCAGGGCTACCGGGATGCTGTCTGCAGT       c.900
 L  T  V  P  E  S  Q  K  G  A  L  Q  G  Y  R  D  A  V  C  S         p.300

          .         .         .         .         .         .       g.12504
 GGGCAGGCTGCTGCGCGTGCCAGGCGCTTCTCTGGGCTGTCTGCTGAGCTCCGGAACCAG       c.960
 G  Q  A  A  A  R  A  R  R  F  S  G  L  S  A  E  L  R  N  Q         p.320

          .         .        | 09.         .         .         .    g.12894
 CTGGACGTGGCCAAGGTCTCCCAGCAG | CTGGGCCTGGATGCCCCCAACGGCTCGGACTCC    c.1020
 L  D  V  A  K  V  S  Q  Q   | L  G  L  D  A  P  N  G  S  D  S      p.340

          .         .         .         .         .         .       g.12954
 TCGCCACAGGCGCCACCCCCACGGAGGCTGCAGGCGCTTCTGGGGGACCTGCTGGATGCC       c.1080
 S  P  Q  A  P  P  P  R  R  L  Q  A  L  L  G  D  L  L  D  A         p.360

          .         .         .         .         .         .       g.13014
 CAGAAGGTTCTGCAGGATGTGGATGTCCTGTCGGCCCTGGCCCTGCTACTGCCCCAGGGT       c.1140
 Q  K  V  L  Q  D  V  D  V  L  S  A  L  A  L  L  L  P  Q  G         p.380

          .         .         .         .         .         .       g.13074
 GCCTGCACTGGCCGGACCCCCGGACCCCCAGCCAGTGGTGCGGGTGGGGCGGCCAATGGC       c.1200
 A  C  T  G  R  T  P  G  P  P  A  S  G  A  G  G  A  A  N  G         p.400

          .         .         .         .         .         .       g.13134
 ACTGGGGCAGGGGCAGTCATGGGCCCCAACGCCACCGCTGAGGAGGGCGCACCCTCTGCT       c.1260
 T  G  A  G  A  V  M  G  P  N  A  T  A  E  E  G  A  P  S  A         p.420

          .         .         .         .         .         .       g.13194
 GCAGCACTGGCCACCCCGGACACGCTGCAGGGCCAGTGCTCAGCCTTCGTACAGCTCTGG       c.1320
 A  A  L  A  T  P  D  T  L  Q  G  Q  C  S  A  F  V  Q  L  W         p.440

          .         .         .      | 10  .         .         .    g.13452
 GCCGGCCTGCAGCCCATCTTGTGTGGCAACAACCG | CACCATTGAACCCGAGGCGCTGCGG    c.1380
 A  G  L  Q  P  I  L  C  G  N  N  R  |  T  I  E  P  E  A  L  R      p.460

          .         .         .         .         .         .       g.13512
 CGGGGCAACATGAGCTCCCTGGGCTTCACGAGCAAGGAGCAGCGGAACCTGGGCCTCCTC       c.1440
 R  G  N  M  S  S  L  G  F  T  S  K  E  Q  R  N  L  G  L  L         p.480

          .         .         .         .         .         .       g.13572
 GTGCACCTCATGACCAGCAACCCCAAAATCCTGTACGCGCCTGCGGGCTCTGAGGTCGAC       c.1500
 V  H  L  M  T  S  N  P  K  I  L  Y  A  P  A  G  S  E  V  D         p.500

          .      | 11  .         .         .         .         .    g.14661
 CGCGTCATCCTCAAG | GCCAACGAGACTTTTGCTTTTGTGGGCAACGTGACTCACTATGCC    c.1560
 R  V  I  L  K   | A  N  E  T  F  A  F  V  G  N  V  T  H  Y  A      p.520

          .         .         .         .         .         .       g.14721
 CAGGTCTGGCTCAACATCTCGGCGGAGATCCGCAGCTTCCTGGAGCAGGGCAGGCTGCAG       c.1620
 Q  V  W  L  N  I  S  A  E  I  R  S  F  L  E  Q  G  R  L  Q         p.540

          .         .     | 12   .         .         .         .    g.14888
 CAACACCTGCGCTGGCTGCAGCAG | TATGTAGCAGAGCTGCGGCTGCACCCCGAGGCACTG    c.1680
 Q  H  L  R  W  L  Q  Q   | Y  V  A  E  L  R  L  H  P  E  A  L      p.560

          .         .         .         .         .         .       g.14948
 AACCTGTCACTGGATGAGCTGCCGCCGGCCCTGAGACAGGACAACTTCTCGCTGCCCAGT       c.1740
 N  L  S  L  D  E  L  P  P  A  L  R  Q  D  N  F  S  L  P  S         p.580

          .         .         .         .         .         .       g.15008
 GGCATGGCCCTCCTGCAGCAGCTGGATACCATTGACAACGCGGCCTGCGGCTGGATCCAG       c.1800
 G  M  A  L  L  Q  Q  L  D  T  I  D  N  A  A  C  G  W  I  Q         p.600

          .   | 13     .         .         .         .         .    g.15155
 TTCATGTCCAAG | GTGAGCGTGGACATCTTCAAGGGCTTCCACGACGAGGAGAGCATTGTC    c.1860
 F  M  S  K   | V  S  V  D  I  F  K  G  F  H  D  E  E  S  I  V      p.620

          .         .         .         .          | 14        .    g.15582
 AACTACACCCTCAACCAGGCCTACCAGGACAACGTCACTGTTTTTGCCA | GTGTGATCTTC    c.1920
 N  Y  T  L  N  Q  A  Y  Q  D  N  V  T  V  F  A  S |   V  I  F      p.640

          .         .         .         .         .         .       g.15642
 CAGACCCGGAAGGACGGCTCGCTCCCGCCTCACGTGCACTACAAGATCCGCCAGAACTCC       c.1980
 Q  T  R  K  D  G  S  L  P  P  H  V  H  Y  K  I  R  Q  N  S         p.660

          .         .         .         .         .         .       g.15702
 AGCTTCACCGAGAAAACCAACGAGATCCGCCGCGCCTACTGGCGGCCTGGGCCCAATACT       c.2040
 S  F  T  E  K  T  N  E  I  R  R  A  Y  W  R  P  G  P  N  T         p.680

          .         .         .         .    | 15    .         .    g.15864
 GGCGGCCGCTTCTACTTCCTCTACGGCTTCGTCTGGATCCAGG | ACATGATGGAGCGCGCC    c.2100
 G  G  R  F  Y  F  L  Y  G  F  V  W  I  Q  D |   M  M  E  R  A      p.700

          .         .         .         .         .         .       g.15924
 ATCATCGACACTTTTGTGGGGCACGATGTGGTGGAGCCAGGCAGCTACGTGCAGATGTTC       c.2160
 I  I  D  T  F  V  G  H  D  V  V  E  P  G  S  Y  V  Q  M  F         p.720

          .         .       | 16 .         .         .         .    g.16055
 CCCTACCCCTGCTACACACGCGATGA | CTTCCTGTTTGTCATTGAGCACATGATGCCGCTG    c.2220
 P  Y  P  C  Y  T  R  D  D  |  F  L  F  V  I  E  H  M  M  P  L      p.740

          .         .         .         .         .         .       g.16115
 TGCATGGTGATCTCCTGGGTCTACTCCGTGGCCATGACCATCCAGCACATCGTGGCGGAG       c.2280
 C  M  V  I  S  W  V  Y  S  V  A  M  T  I  Q  H  I  V  A  E         p.760

          .         .  | 17      .         .         .         .    g.16269
 AAGGAGCACCGGCTCAAGGAG | GTGATGAAGACCATGGGCCTGAACAACGCGGTGCACTGG    c.2340
 K  E  H  R  L  K  E   | V  M  K  T  M  G  L  N  N  A  V  H  W      p.780

          .         .         .         .         .         .       g.16329
 GTGGCCTGGTTCATCACCGGCTTTGTGCAGCTGTCCATCTCCGTGACAGCACTCACCGCC       c.2400
 V  A  W  F  I  T  G  F  V  Q  L  S  I  S  V  T  A  L  T  A         p.800

          .         .         .         .         .         .       g.16389
 ATCCTGAAGTACGGCCAGGTGCTTATGCACAGCCACGTGGTCATCATCTGGCTCTTCCTG       c.2460
 I  L  K  Y  G  Q  V  L  M  H  S  H  V  V  I  I  W  L  F  L         p.820

          .         .         .   | 18     .         .         .    g.16604
 GCAGTCTACGCGGTGGCCACCATCATGTTCTG | CTTCCTGGTGTCTGTGCTGTACTCCAAG    c.2520
 A  V  Y  A  V  A  T  I  M  F  C  |  F  L  V  S  V  L  Y  S  K      p.840

          .         .         .         .         .         .       g.16664
 GCCAAGCTGGCCTCGGCCTGCGGTGGCATCATCTACTTCCTGAGCTACGTGCCCTACATG       c.2580
 A  K  L  A  S  A  C  G  G  I  I  Y  F  L  S  Y  V  P  Y  M         p.860

          .         .         .         .         .         .       g.16724
 TACGTGGCGATCCGAGAGGAGGTGGCGCATGATAAGATCACGGCCTTCGAGAAGTGCATC       c.2640
 Y  V  A  I  R  E  E  V  A  H  D  K  I  T  A  F  E  K  C  I         p.880

     | 19    .         .         .         .         .         .    g.16855
 GCG | TCCCTCATGTCCACGACGGCCTTTGGTCTGGGCTCTAAGTACTTCGCGCTGTATGAG    c.2700
 A   | S  L  M  S  T  T  A  F  G  L  G  S  K  Y  F  A  L  Y  E      p.900

          .         .         .         .         .         .       g.16915
 GTGGCCGGCGTGGGCATCCAGTGGCACACCTTCAGCCAGTCCCCGGTGGAGGGGGACGAC       c.2760
 V  A  G  V  G  I  Q  W  H  T  F  S  Q  S  P  V  E  G  D  D         p.920

          .         .         .         .         .         .       g.16975
 TTCAACTTGCTCCTGGCTGTCACCATGCTGATGGTGGACGCCGTGGTCTATGGCATCCTC       c.2820
 F  N  L  L  L  A  V  T  M  L  M  V  D  A  V  V  Y  G  I  L         p.940

          .         .         | 20         .         .         .    g.17216
 ACGTGGTACATTGAGGCTGTGCACCCAG | GCATGTACGGGCTGCCCCGGCCCTGGTACTTC    c.2880
 T  W  Y  I  E  A  V  H  P  G |   M  Y  G  L  P  R  P  W  Y  F      p.960

          .         .         .         .         .         .       g.17276
 CCACTGCAGAAGTCCTACTGGCTGGGCAGTGGGCGGACAGAAGCCTGGGAGTGGAGCTGG       c.2940
 P  L  Q  K  S  Y  W  L  G  S  G  R  T  E  A  W  E  W  S  W         p.980

          .         .         .         .         .         .       g.17336
 CCGTGGGCACGCACCCCCCGCCTCAGTGTCATGGAGGAGGACCAGGCCTGTGCCATGGAG       c.3000
 P  W  A  R  T  P  R  L  S  V  M  E  E  D  Q  A  C  A  M  E         p.1000

          .    | 21    .         .         .         .         .    g.17498
 AGCCGGCGCTTTG | AGGAGACCCGTGGCATGGAGGAGGAGCCCACCCACCTGCCTCTGGTT    c.3060
 S  R  R  F  E |   E  T  R  G  M  E  E  E  P  T  H  L  P  L  V      p.1020

          .         .         .         .         .         .       g.17558
 GTCTGCGTGGACAAACTCACCAAGGTCTACAAGGACGACAAGAAGCTGGCCCTGAACAAG       c.3120
 V  C  V  D  K  L  T  K  V  Y  K  D  D  K  K  L  A  L  N  K         p.1040

          .         .         .         .         .         .       g.17618
 CTGAGCCTGAACCTCTACGAGAACCAGGTGGTCTCCTTCTTGGGCCACAACGGGGCGGGC       c.3180
 L  S  L  N  L  Y  E  N  Q  V  V  S  F  L  G  H  N  G  A  G         p.1060

          .     | 22   .         .         .         .         .    g.17794
 AAGACCACCACCAT | GTCCATCCTGACCGGCCTGTTCCCTCCAACGTCGGGTTCCGCCACC    c.3240
 K  T  T  T  M  |  S  I  L  T  G  L  F  P  P  T  S  G  S  A  T      p.1080

          .         .         .         .         .         .       g.17854
 ATCTACGGGCACGACATCCGCACGGAGATGGATGAGATCCGCAAGAACCTGGGCATGTGC       c.3300
 I  Y  G  H  D  I  R  T  E  M  D  E  I  R  K  N  L  G  M  C         p.1100

          .         .         .         .         .         .       g.17914
 CCGCAGCACAATGTGCTCTTTGACCGGCTCACGGTGGAGGAACACCTCTGGTTCTACTCA       c.3360
 P  Q  H  N  V  L  F  D  R  L  T  V  E  E  H  L  W  F  Y  S         p.1120

          .         .         .         .        | 23.         .    g.18064
 CGGCTCAAGAGCATGGCTCAGGAGGAGATCCGCAGAGAGATGGACAA | GATGATCGAGGAC    c.3420
 R  L  K  S  M  A  Q  E  E  I  R  R  E  M  D  K  |  M  I  E  D      p.1140

          .         .         .         .         .         .       g.18124
 CTGGAGCTCTCCAACAAACGGCACTCACTGGTGCAGACATTGTCGGGTGGCATGAAGCGC       c.3480
 L  E  L  S  N  K  R  H  S  L  V  Q  T  L  S  G  G  M  K  R         p.1160

          .         .         .         .         .         .       g.18184
 AAGCTGTCCGTGGCCATCGCCTTCGTGGGCGGCTCTCGCGCCATCATCCTGGACGAGCCC       c.3540
 K  L  S  V  A  I  A  F  V  G  G  S  R  A  I  I  L  D  E  P         p.1180

          .         .         .         .         .         .       g.18244
 ACGGCGGGCGTGGACCCCTACGCGCGCCGCGCCATCTGGGACCTCATCCTGAAGTACAAG       c.3600
 T  A  G  V  D  P  Y  A  R  R  A  I  W  D  L  I  L  K  Y  K         p.1200

      | 24   .         .         .         .         .         .    g.18382
 CCAG | GCCGCACCATCCTTCTGTCCACCCACCACATGGATGAGGCTGACCTGCTTGGGGAC    c.3660
 P  G |   R  T  I  L  L  S  T  H  H  M  D  E  A  D  L  L  G  D      p.1220

          .         .         .         .         .         .       g.18442
 CGCATTGCCATCATCTCCCATGGGAAGCTCAAGTGCTGCGGCTCCCCGCTCTTCCTCAAG       c.3720
 R  I  A  I  I  S  H  G  K  L  K  C  C  G  S  P  L  F  L  K         p.1240

          .         .         .         .         .         .       g.18502
 GGCACCTATGGCGACGGGTACCGCCTCACGCTGGTCAAGCGGCCCGCCGAGCCGGGGGGC       c.3780
 G  T  Y  G  D  G  Y  R  L  T  L  V  K  R  P  A  E  P  G  G         p.1260

         | 25.         .         .         .         .         .    g.18878
 CCCCAAG | AGCCAGGGCTGGCATCCAGCCCCCCAGGTCGGGCCCCGCTGAGCAGCTGCTCC    c.3840
 P  Q  E |   P  G  L  A  S  S  P  P  G  R  A  P  L  S  S  C  S      p.1280

          .         .         .         .         .         .       g.18938
 GAGCTCCAGGTGTCCCAGTTCATCCGCAAGCATGTGGCCTCCTGCCTGCTGGTCTCAGAC       c.3900
 E  L  Q  V  S  Q  F  I  R  K  H  V  A  S  C  L  L  V  S  D         p.1300

          .         .         .         .         .         .       g.18998
 ACAAGCACGGAGCTCTCCTACATCCTGCCCAGCGAGGCCGCCAAGAAGGGGGCTTTCGAG       c.3960
 T  S  T  E  L  S  Y  I  L  P  S  E  A  A  K  K  G  A  F  E         p.1320

          .   | 26     .         .         .         .         .    g.19160
 CGCCTCTTCCAG | CACCTGGAGCGCAGCCTGGATGCACTGCACCTCAGCAGCTTCGGGCTG    c.4020
 R  L  F  Q   | H  L  E  R  S  L  D  A  L  H  L  S  S  F  G  L      p.1340

          .         .         .         .         .         .       g.19220
 ATGGACACGACCCTGGAGGAAGTGTTCCTCAAGGTGTCGGAGGAGGATCAGTCGCTGGAG       c.4080
 M  D  T  T  L  E  E  V  F  L  K  V  S  E  E  D  Q  S  L  E         p.1360

          .    | 27    .         .         .         .         .    g.19565
 AACAGTGAGGCCG | ATGTGAAGGAGTCCAGGAAGGATGTGCTCCCTGGGGCGGAGGGCCCG    c.4140
 N  S  E  A  D |   V  K  E  S  R  K  D  V  L  P  G  A  E  G  P      p.1380

          .         .         .         .         .         .       g.19625
 GCGTCTGGGGAGGGTCACGCTGGCAATCTGGCCCGGTGCTCGGAGCTGACCCAGTCGCAG       c.4200
 A  S  G  E  G  H  A  G  N  L  A  R  C  S  E  L  T  Q  S  Q         p.1400

          .         .         .         .         .         .       g.19685
 GCATCGCTGCAGTCGGCGTCATCTGTGGGCTCTGCCCGTGGCGACGAGGGAGCTGGCTAC       c.4260
 A  S  L  Q  S  A  S  S  V  G  S  A  R  G  D  E  G  A  G  Y         p.1420

          .         .         .         .         .         .       g.19745
 ACCGACGTCTATGGCGACTACCGCCCCCTCTTTGATAACCCACAGGACCCAGACAATGTC       c.4320
 T  D  V  Y  G  D  Y  R  P  L  F  D  N  P  Q  D  P  D  N  V         p.1440

          . | 28       .         .         .         .         .    g.19934
 AGCCTGCAAG | AGGTGGAGGCAGAGGCCCTGTCGAGGGTCGGCCAGGGCAGCCGCAAGCTG    c.4380
 S  L  Q  E |   V  E  A  E  A  L  S  R  V  G  Q  G  S  R  K  L      p.1460

          .         .         .         .         .         .       g.19994
 GACGGCGGGTGGCTGAAGGTGCGCCAGTTCCACGGGCTGCTGGTCAAACGCTTCCACTGC       c.4440
 D  G  G  W  L  K  V  R  Q  F  H  G  L  L  V  K  R  F  H  C         p.1480

          .         .         .         .         .         .       g.20054
 GCCCGCCGCAACTCCAAGGCACTCTTCTCCCAGATCTTGCTGCCAGCCTTCTTCGTCTGC       c.4500
 A  R  R  N  S  K  A  L  F  S  Q  I  L  L  P  A  F  F  V  C         p.1500

          .         .         .        | 29.         .         .    g.20382
 GTGGCCATGACCGTGGCCCTGTCCGTCCCGGAGATTG | GTGATCTGCCCCCGCTGGTCCTG    c.4560
 V  A  M  T  V  A  L  S  V  P  E  I  G |   D  L  P  P  L  V  L      p.1520

          .         .         .         .         .         .       g.20442
 TCACCTTCCCAGTACCACAACTACACCCAGCCCCGTGGCAATTTCATCCCCTACGCCAAC       c.4620
 S  P  S  Q  Y  H  N  Y  T  Q  P  R  G  N  F  I  P  Y  A  N         p.1540

          .         . | 30       .         .         .         .    g.20644
 GAGGAGCGCCGCGAGTACCG | GCTGCGGCTATCGCCCGACGCCAGCCCCCAGCAGCTCGTG    c.4680
 E  E  R  R  E  Y  R  |  L  R  L  S  P  D  A  S  P  Q  Q  L  V      p.1560

          .         .         .         .         .         .       g.20704
 AGCACGTTCCGGCTGCCGTCGGGGGTGGGTGCCACCTGCGTGCTCAAGTCTCCCGCCAAC       c.4740
 S  T  F  R  L  P  S  G  V  G  A  T  C  V  L  K  S  P  A  N         p.1580

          .         .         .         .         .         .       g.20764
 GGCTCGCTGGGGCCCACGTTGAACCTGAGCAGCGGGGAGTCGCGCCTGCTGGCGGCTCGG       c.4800
 G  S  L  G  P  T  L  N  L  S  S  G  E  S  R  L  L  A  A  R         p.1600

          .         .         .         .         .         .       g.20824
 TTCTTCGACAGCATGTGTCTGGAGTCCTTCACACAGGGGCTGCCACTGTCCAATTTCGTG       c.4860
 F  F  D  S  M  C  L  E  S  F  T  Q  G  L  P  L  S  N  F  V         p.1620

          .         .         .         .         .         .       g.20884
 CCACCCCCACCCTCGCCCGCCCCATCTGACTCGCCAGCGTCCCCGGATGAGGACCTGCAG       c.4920
 P  P  P  P  S  P  A  P  S  D  S  P  A  S  P  D  E  D  L  Q         p.1640

          .         .         .        | 31.         .         .    g.21020
 GCCTGGAACGTCTCCCTGCCGCCCACCGCTGGGCCAG | AAATGTGGACGTCGGCACCCTCC    c.4980
 A  W  N  V  S  L  P  P  T  A  G  P  E |   M  W  T  S  A  P  S      p.1660

          .         .         .         .         .         .       g.21080
 CTGCCGCGCCTGGTACGGGAGCCCGTCCGCTGCACCTGCTCTGCGCAGGGCACCGGCTTC       c.5040
 L  P  R  L  V  R  E  P  V  R  C  T  C  S  A  Q  G  T  G  F         p.1680

          .         .         .         .         .         .       g.21140
 TCCTGCCCCAGCAGTGTGGGCGGGCACCCGCCCCAGATGCGGGTGGTCACAGGCGACATC       c.5100
 S  C  P  S  S  V  G  G  H  P  P  Q  M  R  V  V  T  G  D  I         p.1700

          .         .         .         .         .         .       g.21200
 CTGACCGACATCACCGGCCACAATGTCTCTGAGTACCTGCTCTTCACCTCCGACCGCTTC       c.5160
 L  T  D  I  T  G  H  N  V  S  E  Y  L  L  F  T  S  D  R  F         p.1720

          .  | 32      .         .         .         .         .    g.21381
 CGACTGCACCG | GTATGGGGCCATCACCTTTGGAAACGTCCTGAAGTCCATCCCAGCCTCA    c.5220
 R  L  H  R  |  Y  G  A  I  T  F  G  N  V  L  K  S  I  P  A  S      p.1740

          .         .         .         .         .        | 33.    g.21549
 TTTGGCACCAGGGCCCCACCCATGGTGCGGAAGATCGCGGTGCGCAGGGCTGCCCAG | GTT    c.5280
 F  G  T  R  A  P  P  M  V  R  K  I  A  V  R  R  A  A  Q   | V      p.1760

          .         .         .         .         .         .       g.21609
 TTCTACAACAACAAGGGCTATCACAGCATGCCCACCTACCTCAACAGCCTCAACAACGCC       c.5340
 F  Y  N  N  K  G  Y  H  S  M  P  T  Y  L  N  S  L  N  N  A         p.1780

          .         .         .         .          | 34        .    g.21771
 ATCCTGCGTGCCAACCTGCCCAAGAGCAAGGGCAACCCGGCGGCTTACG | GCATCACCGTC    c.5400
 I  L  R  A  N  L  P  K  S  K  G  N  P  A  A  Y  G |   I  T  V      p.1800

          .         .         .         .         . | 35       .    g.21914
 ACCAACCACCCCATGAATAAGACCAGCGCCAGCCTCTCCCTGGATTACCT | GCTGCAGGGC    c.5460
 T  N  H  P  M  N  K  T  S  A  S  L  S  L  D  Y  L  |  L  Q  G      p.1820

          .         .         .         .         .         .       g.21974
 ACGGATGTCGTCATCGCCATCTTCATCATCGTGGCCATGTCCTTCGTGCCGGCCAGCTTC       c.5520
 T  D  V  V  I  A  I  F  I  I  V  A  M  S  F  V  P  A  S  F         p.1840

          .         .         .         .         .         .       g.22034
 GTTGTCTTCCTCGTGGCCGAGAAGTCCACCAAGGCCAAGCACCTGCAGTTTGTCAGCGGC       c.5580
 V  V  F  L  V  A  E  K  S  T  K  A  K  H  L  Q  F  V  S  G         p.1860

          .         .         .         .      | 36  .         .    g.22188
 TGCAACCCCATCATCTACTGGCTGGCGAACTACGTGTGGGACATG | CTCAACTACCTGGTC    c.5640
 C  N  P  I  I  Y  W  L  A  N  Y  V  W  D  M   | L  N  Y  L  V      p.1880

          .         .         .         .         .         .       g.22248
 CCCGCTACCTGCTGTGTCATCATCCTGTTTGTGTTCGACCTGCCGGCCTACACGTCGCCC       c.5700
 P  A  T  C  C  V  I  I  L  F  V  F  D  L  P  A  Y  T  S  P         p.1900

          .         .         .         .  | 37      .         .    g.22387
 ACCAACTTCCCTGCCGTCCTCTCCCTCTTCCTGCTCTATGG | GTGGTCCATCACGCCCATC    c.5760
 T  N  F  P  A  V  L  S  L  F  L  L  Y  G  |  W  S  I  T  P  I      p.1920

          .         .         .         .         .         .       g.22447
 ATGTACCCGGCCTCCTTCTGGTTCGAGGTCCCCAGCTCCGCCTACGTGTTCCTCATTGTC       c.5820
 M  Y  P  A  S  F  W  F  E  V  P  S  S  A  Y  V  F  L  I  V         p.1940

          .         .         .         .         .         .       g.22507
 ATCAATCTCTTCATCGGCATCACCGCCACCGTGGCCACCTTCCTGCTACAGCTCTTCGAG       c.5880
 I  N  L  F  I  G  I  T  A  T  V  A  T  F  L  L  Q  L  F  E         p.1960

           | 38        .         .         .         .         .    g.22664
 CACGACAAG | GACCTGAAGGTTGTCAACAGTTACCTGAAAAGCTGCTTCCTCATTTTCCCC    c.5940
 H  D  K   | D  L  K  V  V  N  S  Y  L  K  S  C  F  L  I  F  P      p.1980

          .         .         .         .         .         .       g.22724
 AACTACAACCTGGGCCACGGGCTCATGGAGATGGCCTACAACGAGTACATCAACGAGTAC       c.6000
 N  Y  N  L  G  H  G  L  M  E  M  A  Y  N  E  Y  I  N  E  Y         p.2000

          .    | 39    .         .         .         .         .    g.22864
 TACGCCAAGATTG | GCCAGTTTGACAAGATGAAGTCCCCGTTCGAGTGGGACATTGTCACC    c.6060
 Y  A  K  I  G |   Q  F  D  K  M  K  S  P  F  E  W  D  I  V  T      p.2020

          .         .         .         .         .         .       g.22924
 CGCGGACTGGTGGCCATGGCGGTTGAGGGCGTCGTGGGCTTCCTCCTGACCATCATGTGC       c.6120
 R  G  L  V  A  M  A  V  E  G  V  V  G  F  L  L  T  I  M  C         p.2040

          .         .       | 40 .         .         .         .    g.23219
 CAGTACAACTTCCTGCGGCGGCCACA | GCGCATGCCTGTGTCTACCAAGCCTGTGGAGGAT    c.6180
 Q  Y  N  F  L  R  R  P  Q  |  R  M  P  V  S  T  K  P  V  E  D      p.2060

          .         .         .         .         .         .       g.23279
 GATGTGGACGTGGCCAGTGAGCGGCAGCGAGTGCTCCGGGGAGACGCCGACAATGACATG       c.6240
 D  V  D  V  A  S  E  R  Q  R  V  L  R  G  D  A  D  N  D  M         p.2080

          .         .     | 41   .         .         .         .    g.23587
 GTCAAGATTGAGAACCTGACCAAG | GTCTACAAGTCCCGGAAGATTGGCCGTATCCTGGCC    c.6300
 V  K  I  E  N  L  T  K   | V  Y  K  S  R  K  I  G  R  I  L  A      p.2100

          .         .         .         .         .         .       g.23647
 GTTGACCGCCTGTGCCTGGGTGTGCGTCCTGGCGAGTGCTTCGGGCTCCTGGGCGTCAAC       c.6360
 V  D  R  L  C  L  G  V  R  P  G  E  C  F  G  L  L  G  V  N         p.2120

          .         .         .         .         .         .       g.23707
 GGTGCGGGCAAGACCAGCACCTTCAAGATGCTGACCGGCGACGAGAGCACGACGGGGGGC       c.6420
 G  A  G  K  T  S  T  F  K  M  L  T  G  D  E  S  T  T  G  G         p.2140

          .         .    | 42    .         .         .         .    g.23835
 GAGGCCTTCGTCAATGGACACAG | CGTGCTGAAGGAGCTGCTCCAGGTGCAGCAGAGCCTC    c.6480
 E  A  F  V  N  G  H  S  |  V  L  K  E  L  L  Q  V  Q  Q  S  L      p.2160

          .         .         .         .         .         .       g.23895
 GGCTACTGCCCGCAGTGTGACGCGCTGTTCGACGAGCTCACGGCCCGGGAGCACCTGCAG       c.6540
 G  Y  C  P  Q  C  D  A  L  F  D  E  L  T  A  R  E  H  L  Q         p.2180

          .         .         .         .      | 43  .         .    g.24034
 CTGTACACGCGGCTGCGTGGGATCTCCTGGAAGGACGAGGCCCGG | GTGGTGAAGTGGGCT    c.6600
 L  Y  T  R  L  R  G  I  S  W  K  D  E  A  R   | V  V  K  W  A      p.2200

          .         .         .         .         .         .       g.24094
 CTGGAGAAGCTGGAGCTGACCAAGTACGCAGACAAGCCGGCTGGCACCTACAGCGGCGGC       c.6660
 L  E  K  L  E  L  T  K  Y  A  D  K  P  A  G  T  Y  S  G  G         p.2220

          .         .         .         .         .         .       g.24154
 AACAAGCGGAAGCTCTCCACGGCCATCGCCCTCATTGGGTACCCAGCCTTCATCTTCCTG       c.6720
 N  K  R  K  L  S  T  A  I  A  L  I  G  Y  P  A  F  I  F  L         p.2240

  | 44       .         .         .         .         .         .    g.24338
  | GACGAGCCCACCACAGGCATGGACCCCAAGGCCCGGCGCTTCCTCTGGAACCTCATCCTT    c.6780
  | D  E  P  T  T  G  M  D  P  K  A  R  R  F  L  W  N  L  I  L      p.2260

          .         .         .         .     | 45   .         .    g.24476
 GACCTCATCAAGACAGGGCGTTCAGTGGTGCTGACATCACACAG | CATGGAGGAGTGCGAG    c.6840
 D  L  I  K  T  G  R  S  V  V  L  T  S  H  S  |  M  E  E  C  E      p.2280

          .         .         .         .         .         .       g.24536
 GCGCTGTGCACGCGGCTGGCCATCATGGTGAACGGTCGCCTGCGGTGCCTGGGCAGCATC       c.6900
 A  L  C  T  R  L  A  I  M  V  N  G  R  L  R  C  L  G  S  I         p.2300

          .        | 46.         .         .         .         .    g.24912
 CAGCACCTGAAGAACCG | GTTTGGAGATGGCTACATGATCACGGTGCGGACCAAGAGCAGC    c.6960
 Q  H  L  K  N  R  |  F  G  D  G  Y  M  I  T  V  R  T  K  S  S      p.2320

          .         .         .         .         .         .       g.24972
 CAGAGTGTGAAGGACGTGGTGCGGTTCTTCAACCGCAACTTCCCGGAAGCCATGCTCAAG       c.7020
 Q  S  V  K  D  V  V  R  F  F  N  R  N  F  P  E  A  M  L  K         p.2340

  | 47       .         .         .         .         .         .    g.25114
  | GAGCGGCACCACACAAAGGTGCAGTACCAGCTCAAGTCGGAGCACATCTCGCTGGCCCAG    c.7080
  | E  R  H  H  T  K  V  Q  Y  Q  L  K  S  E  H  I  S  L  A  Q      p.2360

          .         .         .         .         .         .       g.25174
 GTGTTCAGCAAGATGGAGCAGGTGTCTGGCGTGCTGGGCATCGAGGACTACTCGGTCAGC       c.7140
 V  F  S  K  M  E  Q  V  S  G  V  L  G  I  E  D  Y  S  V  S         p.2380

          .         | 48         .         .         .         .    g.25342
 CAGACCACACTGGACAAT | GTGTTCGTGAACTTTGCCAAGAAGCAGAGTGACAACCTGGAG    c.7200
 Q  T  T  L  D  N   | V  F  V  N  F  A  K  K  Q  S  D  N  L  E      p.2400

          .         .         .         .         .         .       g.25402
 CAGCAGGAGACGGAGCCGCCATCCGCACTGCAGTCCCCTCTCGGCTGCTTGCTCAGCCTG       c.7260
 Q  Q  E  T  E  P  P  S  A  L  Q  S  P  L  G  C  L  L  S  L         p.2420

          .         .         .         .         .         .       g.25462
 CTCCGGCCCCGGTCTGCCCCCACGGAGCTCCGGGCACTTGTGGCAGACGAGCCCGAGGAC       c.7320
 L  R  P  R  S  A  P  T  E  L  R  A  L  V  A  D  E  P  E  D         p.2440

          .         .         .         .      | 49  .         .    g.25973
 CTGGACACGGAGGACGAGGGCCTCATCAGCTTCGAGGAGGAGCGG | GCCCAGCTGTCCTTC    c.7380
 L  D  T  E  D  E  G  L  I  S  F  E  E  E  R   | A  Q  L  S  F      p.2460

          .         .                                               g.25994
 AACACGGACACGCTCTGCTGA                                              c.7401
 N  T  D  T  L  C  X                                                p.2466

          .         .         .         .         .         .       g.26054
 ccacccagagctgggccagggaggacacgctccactgaccacccagagctgggccaggga       c.*60

          .         .         .         .         .         .       g.26114
 ctcaacaatggggacagaagtcccccagtgcctgccagggcctggagtggaggttcagga       c.*120

          .         .         .         .         .         .       g.26174
 ccaaggggcttctggtcctccagcccctgtactcggccatgccctgtggtcactgcggtt       c.*180

          .         .         .         .         .         .       g.26234
 gccgcccctaattgtgccaaaggctgacccggcccgggctgcgtacacccttgccctgct       c.*240

          .         .         .         .         .         .       g.26294
 ttgccttaaagcctcggggtctgcccggcccctcgcccctgcctggcactgctcaccgcc       c.*300

          .         .         .         .         .         .       g.26354
 caaggcgacgccggctggaccaggcactgctggcctttctcctgcccggcctcggaacca       c.*360

          .         .         .         .         .         .       g.26414
 gcttttctctcttacgatgaaggctgatgccgagagcgggctgtgggcggagctgggtca       c.*420

          .         .         .         .         .         .       g.26474
 gtcccgtatttattttgctttgagaagaggctcctctggccctgctctcctgcagggagg       c.*480

          .         .         .         .         .         .       g.26534
 tggctgtcctgcgggaagccatcagcttgggccagctggcaggtggcaggaatggagaag       c.*540

          .         .         .         .         .         .       g.26594
 ctgaccctgctggccaggcaaggggccagaccccccccaacccccagctgccatcgctct       c.*600

          .         .         .         .         .         .       g.26654
 cccacccagcttggccccctgcccgcccacctccctgggagccgggcctgtacatagcgc       c.*660

          .         .         .                                     g.26689
 acagatgtttgttttaaataaataaacaaaatgtc                                c.*695

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The ATP-binding cassette, sub-family A (ABC1), member 2 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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