acetyl-CoA carboxylase alpha (ACACA) - coding DNA reference sequence

(used for variant description)

(last modified January 16, 2014)


This file was created to facilitate the description of sequence variants on transcript NM_198834.1 in the ACACA gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_023295.1, covering ACACA transcript NM_198834.1.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                               .         .         .                g.5033
                            ggcccccgccgggtgctgagcgcccgccaccgc       c.-481

 .         .         .         .         .         .                g.5093
 cctcttggccttttcccggtccccgccgcgcgcctgctgctgtccccgtgcccgaggact       c.-421

 .         .         .         .         .         .                g.5153
 gggaggatggggctgagccgcttgcctgacttttgatccgaccagtaatcactttgcccg       c.-361

 .         .         .         .         .         .                g.5213
 tgtggcgcgtggcccgttgcctgaggcttcctggcgcgtggggctgtttggtcccctccg       c.-301

 .         .         .         .         .         .                g.5273
 gagtgcggtgaggcgggccgagccgggactgcctgggtttggggataacgttcccatctc       c.-241

 .         .         .         .         .         .                g.5333
 cacccctgttgcagcaagggaaattgaggctgagggaactgggcccagggacggcgagcc       c.-181

 .         .         .         .         .         .                g.5393
 gtggctgcctctccagtccgggccccgaagggctgctcgtggatgaaccagactgatttt       c.-121

 .         .         .         .         .         .                g.5453
 aaggggtgaagagggtgcgtttcaatcagatgcttctggaacgtcgaaattgtcttcttt       c.-61

 .         .         .         .         .         .                g.5513
 ggaaagaaccatcccctctttgggcttcagaggcccaaattgaggcgcaatgatgagagg       c.-1

          .         .         .         | 02         .         .    g.75114
 ATGTGGTGGTCTACTCTGATGTCAATCTTGAGGGCTAG | GTCTTTCTGGAAGTGGATATCT    c.60
 M  W  W  S  T  L  M  S  I  L  R  A  R  |  S  F  W  K  W  I  S      p.20

          .         .      | 03  .         .         .         .    g.84572
 ACTCAGACAGTAAGAATTATAAGAG | CTGTAAGAGCTCATTTTGGAGGAATAATGGATGAA    c.120
 T  Q  T  V  R  I  I  R  A |   V  R  A  H  F  G  G  I  M  D  E      p.40

          .         .         .         .         .         .       g.84632
 CCATCTCCCTTGGCCCAACCTCTGGAGCTGAACCAGCACTCTCGATTCATAATAGGTTCT       c.180
 P  S  P  L  A  Q  P  L  E  L  N  Q  H  S  R  F  I  I  G  S         p.60

          .         .         .         .         .         .       g.84692
 GTGTCTGAAGATAACTCAGAGGATGAGATCAGCAACCTGGTGAAGTTGGACCTACTGGAG       c.240
 V  S  E  D  N  S  E  D  E  I  S  N  L  V  K  L  D  L  L  E         p.80

          .         .         .         .         .         .       g.84752
 GAGAAGGAGGGCTCCTTGTCACCTGCTTCTGTTGGCTCAGATACACTCTCTGATTTGGGG       c.300
 E  K  E  G  S  L  S  P  A  S  V  G  S  D  T  L  S  D  L  G         p.100

          .         .         .         | 04         .         .    g.130053
 ATCTCTAGCCTACAGGATGGCTTGGCCTTGCACATAAG | GTCCAGCATGTCTGGCTTGCAC    c.360
 I  S  S  L  Q  D  G  L  A  L  H  I  R  |  S  S  M  S  G  L  H      p.120

          .         .         .         .         .         .       g.130113
 CTAGTAAAGCAGGGCCGAGACAGAAAGAAAATAGATTCTCAACGAGATTTCACTGTGGCT       c.420
 L  V  K  Q  G  R  D  R  K  K  I  D  S  Q  R  D  F  T  V  A         p.140

          .         .         .         .         .  | 05      .    g.131605
 TCTCCAGCAGAATTTGTTACTCGCTTTGGGGGAAATAAAGTGATTGAGAAG | GTTCTTATT    c.480
 S  P  A  E  F  V  T  R  F  G  G  N  K  V  I  E  K   | V  L  I      p.160

          .         .         .         .         .         .       g.131665
 GCTAACAATGGCATTGCAGCAGTGAAATGCATGCGGTCTATCCGTAGGTGGTCTTATGAA       c.540
 A  N  N  G  I  A  A  V  K  C  M  R  S  I  R  R  W  S  Y  E         p.180

          .         .         .         .         .         .       g.131725
 ATGTTTCGAAATGAACGTGCAATTAGATTCGTTGTCATGGTCACACCTGAAGACCTTAAA       c.600
 M  F  R  N  E  R  A  I  R  F  V  V  M  V  T  P  E  D  L  K         p.200

          . | 06       .         .         .         .         .    g.137054
 GCCAATGCAG | AATACATTAAGATGGCAGATCACTATGTGCCAGTGCCTGGAGGACCAAAC    c.660
 A  N  A  E |   Y  I  K  M  A  D  H  Y  V  P  V  P  G  G  P  N      p.220

          .         .         .         .         .         .       g.137114
 AACAACAACTATGCAAATGTGGAATTAATTCTTGATATTGCTAAAAGGATCCCAGTACAA       c.720
 N  N  N  Y  A  N  V  E  L  I  L  D  I  A  K  R  I  P  V  Q         p.240

  | 07       .         .         .         .         .         .    g.137955
  | GCAGTGTGGGCTGGCTGGGGTCATGCTTCTGAGAATCCCAAACTACCGGAACTTCTCTTG    c.780
  | A  V  W  A  G  W  G  H  A  S  E  N  P  K  L  P  E  L  L  L      p.260

          .         .   | 08     .         .         .         .    g.138998
 AAAAATGGCATTGCCTTCATGG | GTCCTCCAAGCCAGGCCATGTGGGCTTTAGGGGATAAG    c.840
 K  N  G  I  A  F  M  G |   P  P  S  Q  A  M  W  A  L  G  D  K      p.280

          .         .         .         .         .         .       g.139058
 ATTGCATCTTCCATAGTGGCTCAAACTGCAGGTATCCCAACTCTTCCCTGGAGCGGCAGT       c.900
 I  A  S  S  I  V  A  Q  T  A  G  I  P  T  L  P  W  S  G  S         p.300

   | 09      .         .         .         .         .         .    g.140771
 G | GTCTTCGTGTGGACTGGCAGGAAAATGATTTTTCAAAACGTATCTTAAATGTTCCCCAG    c.960
 G |   L  R  V  D  W  Q  E  N  D  F  S  K  R  I  L  N  V  P  Q      p.320

          .         .         .         .         | 10         .    g.144162
 GAGCTATATGAAAAAGGTTATGTGAAAGATGTGGATGATGGGCTACAG | GCAGCTGAGGAA    c.1020
 E  L  Y  E  K  G  Y  V  K  D  V  D  D  G  L  Q   | A  A  E  E      p.340

          .         .         .         .         .         .       g.144222
 GTTGGATATCCAGTAATGATCAAGGCCTCAGAGGGAGGAGGAGGGAAGGGAATTAGAAAA       c.1080
 V  G  Y  P  V  M  I  K  A  S  E  G  G  G  G  K  G  I  R  K         p.360

          .         .         .          | 11        .         .    g.151126
 GTCAACAATGCAGATGACTTCCCTAATCTCTTCAGACAG | GTTCAAGCTGAAGTTCCTGGA    c.1140
 V  N  N  A  D  D  F  P  N  L  F  R  Q   | V  Q  A  E  V  P  G      p.380

          .         .         .         .         .         .       g.151186
 TCTCCCATATTTGTGATGAGACTAGCCAAACAATCTCGTCATCTGGAGGTGCAGATCTTA       c.1200
 S  P  I  F  V  M  R  L  A  K  Q  S  R  H  L  E  V  Q  I  L         p.400

          .         .         .         .         .         .       g.151246
 GCGGACCAATATGGCAATGCTATCTCTTTGTTTGGTCGTGATTGCTCTGTACAACGCAGG       c.1260
 A  D  Q  Y  G  N  A  I  S  L  F  G  R  D  C  S  V  Q  R  R         p.420

          .         .         .         .         .         .       g.151306
 CATCAGAAGATTATTGAAGAAGCACCTGCTACTATTGCTACTCCAGCAGTATTTGAACAC       c.1320
 H  Q  K  I  I  E  E  A  P  A  T  I  A  T  P  A  V  F  E  H         p.440

           | 12        .         .         .         .         .    g.155501
 ATGGAACAG | TGTGCGGTGAAACTTGCCAAAATGGTGGGTTATGTGAGTGCTGGGACTGTG    c.1380
 M  E  Q   | C  A  V  K  L  A  K  M  V  G  Y  V  S  A  G  T  V      p.460

          .         .         .         .         .         .       g.155561
 GAATACCTGTACAGCCAGGATGGCAGCTTCTACTTTCTGGAATTGAATCCTCGGCTGCAG       c.1440
 E  Y  L  Y  S  Q  D  G  S  F  Y  F  L  E  L  N  P  R  L  Q         p.480

          .         .         .         .         .         .       g.155621
 GTAGAGCACCCTTGTACAGAGATGGTGGCTGATGTCAATCTCCCTGCAGCACAGCTCCAG       c.1500
 V  E  H  P  C  T  E  M  V  A  D  V  N  L  P  A  A  Q  L  Q         p.500

  | 13       .         .         .         .         .         .    g.156667
  | ATTGCCATGGGGATTCCTCTATATAGAATCAAGGATATCCGTATGATGTATGGGGTATCT    c.1560
  | I  A  M  G  I  P  L  Y  R  I  K  D  I  R  M  M  Y  G  V  S      p.520

          .         .         .         .         .         .       g.156727
 CCCTGGGGTGATTCTCCCATTGATTTTGAAGATTCTGCACACGTTCCTTGTCCAAGGGGC       c.1620
 P  W  G  D  S  P  I  D  F  E  D  S  A  H  V  P  C  P  R  G         p.540

          .         .         .         .   | 14     .         .    g.157132
 CATGTTATTGCTGCTCGGATCACTAGTGAAAATCCAGATGAG | GGTTTTAAGCCCAGCTCA    c.1680
 H  V  I  A  A  R  I  T  S  E  N  P  D  E   | G  F  K  P  S  S      p.560

          .         .         .         .         .         .       g.157192
 GGAACAGTTCAGGAGCTAAATTTCCGCAGCAATAAGAATGTTTGGGGATATTTCAGTGTT       c.1740
 G  T  V  Q  E  L  N  F  R  S  N  K  N  V  W  G  Y  F  S  V         p.580

          .         .         .         .         .         .       g.157252
 GCTGCTGCAGGGGGACTTCATGAATTTGCTGATTCTCAGTTTGGTCACTGCTTTTCTTGG       c.1800
 A  A  A  G  G  L  H  E  F  A  D  S  Q  F  G  H  C  F  S  W         p.600

          .         .       | 15 .         .         .         .    g.161974
 GGAGAAAACAGAGAAGAGGCAATTTC | AAACATGGTGGTGGCTTTGAAGGAGCTGTCTATT    c.1860
 G  E  N  R  E  E  A  I  S  |  N  M  V  V  A  L  K  E  L  S  I      p.620

          .         .         .         .         .         .       g.162034
 CGGGGTGACTTTCGAACTACAGTTGAATACCTGATCAAATTGTTAGAGACTGAAAGCTTT       c.1920
 R  G  D  F  R  T  T  V  E  Y  L  I  K  L  L  E  T  E  S  F         p.640

          .         .         .         .         .        | 16.    g.162871
 CAGATGAACAGAATTGATACTGGCTGGCTGGACAGACTGATAGCAGAAAAAGTACAG | GCT    c.1980
 Q  M  N  R  I  D  T  G  W  L  D  R  L  I  A  E  K  V  Q   | A      p.660

          .         .         .         .         .         .       g.162931
 GAGCGACCTGACACCATGTTGGGGGTTGTGTGTGGTGCCCTCCACGTGGCAGATGTGAGC       c.2040
 E  R  P  D  T  M  L  G  V  V  C  G  A  L  H  V  A  D  V  S         p.680

          .         .         .         .  | 17      .         .    g.166323
 CTGCGGAATAGCGTCTCTAACTTCCTTCACTCCTTAGAAAG | GGGTCAAGTCCTTCCTGCT    c.2100
 L  R  N  S  V  S  N  F  L  H  S  L  E  R  |  G  Q  V  L  P  A      p.700

          .         .         .         .         .         .       g.166383
 CATACACTTCTGAATACAGTAGATGTTGAACTTATCTATGAGGGAGTCAAGTATGTACTT       c.2160
 H  T  L  L  N  T  V  D  V  E  L  I  Y  E  G  V  K  Y  V  L         p.720

     | 18    .         .         .         .         .         .    g.166879
 AAG | GTGACTCGACAGTCCCCCAACTCCTATGTGGTGATCATGAATGGCTCATGTGTAGAA    c.2220
 K   | V  T  R  Q  S  P  N  S  Y  V  V  I  M  N  G  S  C  V  E      p.740

          .         .         .         .         .         .       g.166939
 GTAGATGTACATCGGCTGAGTGACGGTGGACTGCTCTTGTCCTATGATGGCAGCAGTTAT       c.2280
 V  D  V  H  R  L  S  D  G  G  L  L  L  S  Y  D  G  S  S  Y         p.760

          .         .          | 19        .         .         .    g.168041
 ACTACGTATATGAAAGAGGAAGTGGATAG | ATATCGCATCACAATTGGCAATAAAACCTGT    c.2340
 T  T  Y  M  K  E  E  V  D  R  |  Y  R  I  T  I  G  N  K  T  C      p.780

          .         .         .         .         .         .       g.168101
 GTGTTTGAGAAGGAAAATGACCCATCGGTGATGCGCTCACCTTCTGCTGGGAAGTTAATC       c.2400
 V  F  E  K  E  N  D  P  S  V  M  R  S  P  S  A  G  K  L  I         p.800

          .         .         .         .         .         .       g.168161
 CAGTACATTGTAGAAGATGGAGGTCATGTGTTTGCCGGCCAGTGCTATGCTGAGATTGAG       c.2460
 Q  Y  I  V  E  D  G  G  H  V  F  A  G  Q  C  Y  A  E  I  E         p.820

  | 20       .         .         .         .         .         .    g.169832
  | GTAATGAAGATGGTAATGACCTTAACAGCTGTGGAGTCTGGCTGTATCCATTACGTCAAG    c.2520
  | V  M  K  M  V  M  T  L  T  A  V  E  S  G  C  I  H  Y  V  K      p.840

          .         .         .         .         .         .       g.169892
 CGACCTGGAGCAGCTCTTGACCCTGGCTGTGTACTAGCCAAAATGCAACTGGACAACCCC       c.2580
 R  P  G  A  A  L  D  P  G  C  V  L  A  K  M  Q  L  D  N  P         p.860

          .      | 21  .         .         .         .         .    g.170297
 AGCAAGGTTCAGCAG | GCTGAACTTCACACAGGTAGTCTGCCACGGATCCAGAGCACGGCA    c.2640
 S  K  V  Q  Q   | A  E  L  H  T  G  S  L  P  R  I  Q  S  T  A      p.880

          .         .         .         .         .         .       g.170357
 CTCAGAGGCGAGAAACTCCATCGAGTGTTCCATTATGTCCTGGATAATCTGGTCAATGTA       c.2700
 L  R  G  E  K  L  H  R  V  F  H  Y  V  L  D  N  L  V  N  V         p.900

          .         .         .         .   | 22     .         .    g.171445
 ATGAATGGATACTGCCTTCCAGATCCTTTCTTTAGCAGCAAG | GTAAAAGACTGGGTAGAG    c.2760
 M  N  G  Y  C  L  P  D  P  F  F  S  S  K   | V  K  D  W  V  E      p.920

          .         .         .         .         .         .       g.171505
 CGATTGATGAAAACCCTCAGAGATCCCTCCCTGCCTCTCCTAGAATTGCAAGATATTATG       c.2820
 R  L  M  K  T  L  R  D  P  S  L  P  L  L  E  L  Q  D  I  M         p.940

          .         .         .         .         .         .       g.171565
 ACCAGTGTGTCTGGCCGCATTCCCCCCAATGTGGAGAAGTCTATCAAGAAGGAAATGGCT       c.2880
 T  S  V  S  G  R  I  P  P  N  V  E  K  S  I  K  K  E  M  A         p.960

          .         .         .         .         .  | 23      .    g.172942
 CAGTATGCTAGCAACATCACATCAGTCCTCTGTCAGTTTCCCAGCCAGCAG | ATTGCAAAC    c.2940
 Q  Y  A  S  N  I  T  S  V  L  C  Q  F  P  S  Q  Q   | I  A  N      p.980

          .         .         .         .         .         .       g.173002
 ATCCTAGATAGCCATGCAGCTACATTGAACCGGAAATCTGAACGGGAAGTCTTCTTTATG       c.3000
 I  L  D  S  H  A  A  T  L  N  R  K  S  E  R  E  V  F  F  M         p.1000

          .         .         .   | 24     .         .         .    g.174450
 AATACTCAGAGCATTGTTCAGCTGGTACAGAG | GTACCGAAGTGGCATCCGAGGCCACATG    c.3060
 N  T  Q  S  I  V  Q  L  V  Q  R  |  Y  R  S  G  I  R  G  H  M      p.1020

          .         .         .         .         .         .       g.174510
 AAGGCTGTGGTGATGGATCTGCTCCGGCAGTACCTGCGAGTAGAGACACAATTCCAGAAT       c.3120
 K  A  V  V  M  D  L  L  R  Q  Y  L  R  V  E  T  Q  F  Q  N         p.1040

   | 25      .         .         .         .         .         .    g.179947
 G | GTCACTATGACAAATGTGTATTCGCCCTCCGAGAAGAGAATAAAAGTGACATGAACACT    c.3180
 G |   H  Y  D  K  C  V  F  A  L  R  E  E  N  K  S  D  M  N  T      p.1060

          .         .         .         .         .         .       g.180007
 GTACTGAACTACATCTTCTCTCACGCTCAAGTCACCAAGAAGAATCTTCTGGTCACAATG       c.3240
 V  L  N  Y  I  F  S  H  A  Q  V  T  K  K  N  L  L  V  T  M         p.1080

        | 26 .         .         .         .         .         .    g.188583
 CTTATT | GATCAGTTGTGTGGCCGGGACCCTACTCTCACTGATGAGCTGCTGAATATTCTC    c.3300
 L  I   | D  Q  L  C  G  R  D  P  T  L  T  D  E  L  L  N  I  L      p.1100

          .         .         .         .         .         .       g.188643
 ACAGAGCTAACTCAACTCAGTAAGACCACCAATGCCAAAGTAGCACTTCGAGCACGCCAG       c.3360
 T  E  L  T  Q  L  S  K  T  T  N  A  K  V  A  L  R  A  R  Q         p.1120

  | 27       .         .         .         .         .         .    g.189936
  | GTTCTTATTGCCTCCCATTTGCCATCATATGAGCTTCGCCATAACCAAGTAGAGTCTATC    c.3420
  | V  L  I  A  S  H  L  P  S  Y  E  L  R  H  N  Q  V  E  S  I      p.1140

          .         .         .         .         .     | 28   .    g.191386
 TTCCTATCAGCTATTGACATGTATGGACATCAATTTTGCATTGAGAACCTGCAG | AAACTC    c.3480
 F  L  S  A  I  D  M  Y  G  H  Q  F  C  I  E  N  L  Q   | K  L      p.1160

          .         .         .         .         .         .       g.191446
 ATCCTATCAGAAACATCTATTTTTGATGTCCTACCAAACTTCTTCTATCACAGCAACCAA       c.3540
 I  L  S  E  T  S  I  F  D  V  L  P  N  F  F  Y  H  S  N  Q         p.1180

          .         .     | 29   .         .         .         .    g.193175
 GTAGTGAGGATGGCAGCTCTGGAG | GTGTATGTTCGAAGGGCTTATATTGCCTATGAACTT    c.3600
 V  V  R  M  A  A  L  E   | V  Y  V  R  R  A  Y  I  A  Y  E  L      p.1200

          .         .         .         .         .         .       g.193235
 AACAGCGTACAACACCGCCAGCTTAAGGACAACACCTGTGTGGTGGAATTCCAGTTCATG       c.3660
 N  S  V  Q  H  R  Q  L  K  D  N  T  C  V  V  E  F  Q  F  M         p.1220

          .         .    | 30    .         .        | 31.         . g.207201
 CTGCCCACATCTCATCCAAACAG | AGGGAACATCCCTACGCTAAACAG | AATGTCCTTCTCC c.3720
 L  P  T  S  H  P  N  R  |  G  N  I  P  T  L  N  R  |  M  S  F  S   p.1240

          .         .         .         .         .         .       g.207261
 TCCAACCTCAACCACTATGGCATGACCCATGTAGCTAGTGTCAGCGATGTACTGTTGGAC       c.3780
 S  N  L  N  H  Y  G  M  T  H  V  A  S  V  S  D  V  L  L  D         p.1260

          .         .         .         .         .         .       g.207321
 AACTCATTCACTCCACCTTGTCAGCGGATGGGCGGAATGGTCTCTTTTCGGACTTTTGAA       c.3840
 N  S  F  T  P  P  C  Q  R  M  G  G  M  V  S  F  R  T  F  E         p.1280

          .  | 32      .         .         .         .         .    g.208158
 GATTTTGTCAG | GATCTTTGATGAAGTGATGGGCTGCTTCTCTGACTCCCCACCCCAGAGT    c.3900
 D  F  V  R  |  I  F  D  E  V  M  G  C  F  S  D  S  P  P  Q  S      p.1300

          .         .         .         .         | 33         .    g.209128
 CCCACATTCCCTGAGGCAGGTCACACGTCTCTTTATGATGAGGATAAG | GTTCCCAGGGAT    c.3960
 P  T  F  P  E  A  G  H  T  S  L  Y  D  E  D  K   | V  P  R  D      p.1320

          .         .         .         .         .         .       g.209188
 GAACCAATTCACATTCTCAATGTGGCTATCAAGACTGACTGTGATATTGAGGATGACAGG       c.4020
 E  P  I  H  I  L  N  V  A  I  K  T  D  C  D  I  E  D  D  R         p.1340

          .         .         .       | 34 .         .         .    g.214500
 CTGGCAGCTATGTTCAGAGAATTTACCCAGCAAAAT | AAAGCTACCCTGGTTGACCATGGG    c.4080
 L  A  A  M  F  R  E  F  T  Q  Q  N   | K  A  T  L  V  D  H  G      p.1360

          .         .         .    | 35    .         .         .    g.214803
 ATCCGGCGCCTTACTTTCCTGGTTGCACAAAAG | GATTTCAGAAAGCAGGTCAACTATGAG    c.4140
 I  R  R  L  T  F  L  V  A  Q  K   | D  F  R  K  Q  V  N  Y  E      p.1380

          .         | 36         .         .         .         .    g.221588
 GTGGATCGGAGATTTCAT | AGAGAATTCCCTAAATTTTTTACATTCCGAGCAAGGGATAAG    c.4200
 V  D  R  R  F  H   | R  E  F  P  K  F  F  T  F  R  A  R  D  K      p.1400

  | 37       .         .         .         .         .         .    g.222716
  | TTTGAGGAGGATCGTATCTATCGTCATCTGGAGCCTGCTCTGGCTTTCCAGTTAGAGCTG    c.4260
  | F  E  E  D  R  I  Y  R  H  L  E  P  A  L  A  F  Q  L  E  L      p.1420

          .         .         .         .         .         .       g.222776
 AACCGGATGAGAAATTTTGACCTCACTGCCATTCCATGTGCTAATCACAAGATGCACCTG       c.4320
 N  R  M  R  N  F  D  L  T  A  I  P  C  A  N  H  K  M  H  L         p.1440

          .         .         .         .         .         .       g.222836
 TATCTCGGGGCAGCCAAGGTGGAAGTGGGCACAGAAGTGACAGACTACAGGTTCTTTGTT       c.4380
 Y  L  G  A  A  K  V  E  V  G  T  E  V  T  D  Y  R  F  F  V         p.1460

          .         .         .       | 38 .         .         .    g.223710
 CGTGCAATCATCAGGCATTCTGATCTGGTCACCAAG | GAAGCTTCTTTTGAATATCTGCAA    c.4440
 R  A  I  I  R  H  S  D  L  V  T  K   | E  A  S  F  E  Y  L  Q      p.1480

          .         .         .         .         .         .       g.223770
 AATGAAGGGGAGCGGCTACTCCTGGAAGCCATGGATGAGTTGGAAGTTGCTTTTAACAAT       c.4500
 N  E  G  E  R  L  L  L  E  A  M  D  E  L  E  V  A  F  N  N         p.1500

          .         .         .         .         .         .       g.223830
 ACAAATGTCCGCACTGACTGTAACCACATCTTCCTCAACTTTGTGCCCACGGTTATCATG       c.4560
 T  N  V  R  T  D  C  N  H  I  F  L  N  F  V  P  T  V  I  M         p.1520

          .   | 39     .         .         .         .         .    g.226530
 GACCCATCAAAG | ATTGAGGAATCCGTGCGGAGCATGGTAATGCGGTATGGAAGTCGCCTG    c.4620
 D  P  S  K   | I  E  E  S  V  R  S  M  V  M  R  Y  G  S  R  L      p.1540

          .         .         .         .         .         .       g.226590
 TGGAAATTGCGCGTCCTCCAGGCAGAACTGAAAATCAACATTCGCCTGACGCCAACTGGA       c.4680
 W  K  L  R  V  L  Q  A  E  L  K  I  N  I  R  L  T  P  T  G         p.1560

          .         .         .         .         .         .       g.226650
 AAAGCAATTCCCATCCGCCTCTTCCTGACAAACGAGTCTGGCTATTACTTGGATATCAGC       c.4740
 K  A  I  P  I  R  L  F  L  T  N  E  S  G  Y  Y  L  D  I  S         p.1580

          .         .         .       | 40 .         .         .    g.233629
 CTATACAAGGAAGTGACTGACTCCAGGACAGCACAG | ATCATGTTTCAGGCATATGGAGAC    c.4800
 L  Y  K  E  V  T  D  S  R  T  A  Q   | I  M  F  Q  A  Y  G  D      p.1600

          .         .         .         .         .         .       g.233689
 AAACAGGGACCACTGCATGGAATGTTAATCAATACTCCATATGTGACCAAAGACCTGCTG       c.4860
 K  Q  G  P  L  H  G  M  L  I  N  T  P  Y  V  T  K  D  L  L         p.1620

          .         .         .         .         .         .       g.233749
 CAATCAAAGAGGTTCCAGGCACAATCCTTAGGGACAACATACATATATGATATCCCAGAG       c.4920
 Q  S  K  R  F  Q  A  Q  S  L  G  T  T  Y  I  Y  D  I  P  E         p.1640

          .   | 41     .         .         .         .         .    g.235603
 ATGTTTCGGCAG | TCCCTGATCAAACTCTGGGAGTCTATGTCCACTCAAGCATTTCTTCCA    c.4980
 M  F  R  Q   | S  L  I  K  L  W  E  S  M  S  T  Q  A  F  L  P      p.1660

          .         .         .         .         .         .       g.235663
 TCTCCCCCTCTGCCTTCTGACATGCTGACTTACACTGAACTGGTACTGGATGATCAAGGT       c.5040
 S  P  P  L  P  S  D  M  L  T  Y  T  E  L  V  L  D  D  Q  G         p.1680

          .         .         .          | 42        .         .    g.252959
 CAGCTGGTCCACATGAACAGGCTTCCAGGAGGAAATGAG | ATTGGCATGGTAGCTTGGAAA    c.5100
 Q  L  V  H  M  N  R  L  P  G  G  N  E   | I  G  M  V  A  W  K      p.1700

          .         .         .         .         .         .       g.253019
 ATGACCTTTAAAAGTCCTGAATATCCAGAAGGCCGAGATATCATTGTTATTGGCAATGAC       c.5160
 M  T  F  K  S  P  E  Y  P  E  G  R  D  I  I  V  I  G  N  D         p.1720

          .         .         .         .         .         .       g.253079
 ATCACATACCGAATTGGGTCCTTTGGGCCTCAAGAGGATTTGTTATTTCTCAGAGCTTCC       c.5220
 I  T  Y  R  I  G  S  F  G  P  Q  E  D  L  L  F  L  R  A  S         p.1740

          .         .         .         .         .         .       g.253139
 GAACTTGCTAGGGCAGAAGGTATTCCACGCATCTATGTATCAGCCAACAGTGGAGCAAGA       c.5280
 E  L  A  R  A  E  G  I  P  R  I  Y  V  S  A  N  S  G  A  R         p.1760

          .         .         .         .         .         .       g.253199
 ATCGGACTGGCAGAAGAAATTCGCCATATGTTTCATGTGGCCTGGGTAGATCCTGAGGAT       c.5340
 I  G  L  A  E  E  I  R  H  M  F  H  V  A  W  V  D  P  E  D         p.1780

           | 43        .         .         .         .         .    g.259251
 CCTTACAAG | GGATACAGGTATTTATATCTGACTCCTCAAGATTATAAGAGAGTCAGTGCT    c.5400
 P  Y  K   | G  Y  R  Y  L  Y  L  T  P  Q  D  Y  K  R  V  S  A      p.1800

          .         .         .         .        | 44.         .    g.263569
 CTCAACTCTGTCCATTGTGAACACGTGGAAGATGAAGGAGAATCCAG | GTACAAGATAACA    c.5460
 L  N  S  V  H  C  E  H  V  E  D  E  G  E  S  R  |  Y  K  I  T      p.1820

          .         .         .         .         .         .       g.263629
 GATATTATTGGGAAAGAAGAGGGAATTGGACCCGAGAACCTTCGAGGTTCTGGAATGATT       c.5520
 D  I  I  G  K  E  E  G  I  G  P  E  N  L  R  G  S  G  M  I         p.1840

          .         .         .         .         | 45         .    g.265016
 GCTGGAGAATCCTCATTGGCCTATAATGAGATCATTACCATCAGCCTG | GTGACGTGCCGG    c.5580
 A  G  E  S  S  L  A  Y  N  E  I  I  T  I  S  L   | V  T  C  R      p.1860

          .         .         .         .         .         .       g.265076
 GCCATTGGGATTGGGGCTTACCTTGTCCGGCTGGGACAGAGAACCATCCAGGTTGAGAAT       c.5640
 A  I  G  I  G  A  Y  L  V  R  L  G  Q  R  T  I  Q  V  E  N         p.1880

          .         .         .          | 46        .         .    g.284779
 TCTCACTTAATTCTAACAGGAGCTGGAGCCCTCAACAAA | GTCCTCGGGCGGGAAGTGTAC    c.5700
 S  H  L  I  L  T  G  A  G  A  L  N  K   | V  L  G  R  E  V  Y      p.1900

          .         .         .         .         .         .       g.284839
 ACCTCCAATAACCAGCTGGGGGGCATCCAGATTATGCACAACAATGGGGTGACCCACTGC       c.5760
 T  S  N  N  Q  L  G  G  I  Q  I  M  H  N  N  G  V  T  H  C         p.1920

          .         .         .         .         .         .       g.284899
 ACTGTGTGTGATGACTTTGAAGGGGTTTTCACTGTCCTGCACTGGCTGTCTTACATGCCC       c.5820
 T  V  C  D  D  F  E  G  V  F  T  V  L  H  W  L  S  Y  M  P         p.1940

     | 47    .         .         .         .         .         .    g.285548
 AAG | AGCGTGCACAGTTCAGTTCCTCTTCTGAACTCAAAGGATCCTATAGACAGAATCATC    c.5880
 K   | S  V  H  S  S  V  P  L  L  N  S  K  D  P  I  D  R  I  I      p.1960

          .         .         .         .         .         .       g.285608
 GAGTTTGTTCCCACAAAGACCCCATACGATCCTCGATGGATGCTAGCAGGCCGTCCTCAC       c.5940
 E  F  V  P  T  K  T  P  Y  D  P  R  W  M  L  A  G  R  P  H         p.1980

      | 48   .         .         .         .         .         .    g.289243
 CCAA | CCCAAAAAGGTCAGTGGTTGAGTGGCTTTTTTGACTATGGATCTTTCTCAGAGATT    c.6000
 P  T |   Q  K  G  Q  W  L  S  G  F  F  D  Y  G  S  F  S  E  I      p.2000

          .         .         .         .  | 49      .         .    g.292372
 ATGCAGCCCTGGGCACAGACTGTGGTGGTTGGTAGAGCCAG | GCTAGGAGGAATACCTGTG    c.6060
 M  Q  P  W  A  Q  T  V  V  V  G  R  A  R  |  L  G  G  I  P  V      p.2020

          .         .         .         .         .         .       g.292432
 GGAGTTGTTGCTGTAGAAACCCGAACAGTAGAACTAAGTATCCCAGCTGATCCAGCAAAC       c.6120
 G  V  V  A  V  E  T  R  T  V  E  L  S  I  P  A  D  P  A  N         p.2040

          .         | 50         .         .         .         .    g.293532
 CTGGATTCTGAAGCCAAG | ATAATCCAGCAGGCTGGCCAGGTTTGGTTCCCAGATTCTGCG    c.6180
 L  D  S  E  A  K   | I  I  Q  Q  A  G  Q  V  W  F  P  D  S  A      p.2060

          .         .         .         .         .         .       g.293592
 TTTAAGACATATCAGGCCATCAAGGACTTCAACCGGGAAGGGCTGCCTCTGATGGTCTTT       c.6240
 F  K  T  Y  Q  A  I  K  D  F  N  R  E  G  L  P  L  M  V  F         p.2080

          .         .         .     | 51   .         .         .    g.301728
 GCCAACTGGAGAGGCTTCTCTGGTGGAATGAAAG | ATATGTACGACCAAGTGCTGAAGTTT    c.6300
 A  N  W  R  G  F  S  G  G  M  K  D |   M  Y  D  Q  V  L  K  F      p.2100

          .         .         .         .         .         .       g.301788
 GGTGCTTACATTGTGGATGGCTTGAGGGAGTGCTGCCAGCCTGTGCTGGTTTACATTCCT       c.6360
 G  A  Y  I  V  D  G  L  R  E  C  C  Q  P  V  L  V  Y  I  P         p.2120

          .         .         .         .         .         .       g.301848
 CCCCAGGCTGAGCTGCGGGGTGGCTCCTGGGTGGTGATTGACTCCTCCATCAACCCCCGG       c.6420
 P  Q  A  E  L  R  G  G  S  W  V  V  I  D  S  S  I  N  P  R         p.2140

          .         .         .   | 52     .         .         .    g.303352
 CACATGGAGATGTATGCTGACCGAGAAAGCAG | GGGATCTGTTCTGGAGCCAGAAGGGACA    c.6480
 H  M  E  M  Y  A  D  R  E  S  R  |  G  S  V  L  E  P  E  G  T      p.2160

          .         .         .         .         .         .       g.303412
 GTAGAAATCAAATTCCGCAGAAAGGATCTGGTGAAAACCATGCGTCGGGTGGACCCAGTC       c.6540
 V  E  I  K  F  R  R  K  D  L  V  K  T  M  R  R  V  D  P  V         p.2180

          .         .      | 53  .         .         .         .    g.317018
 TACATCCACTTGGCTGAGCGATTGG | GGACCCCAGAGCTAAGCACAGCTGAGCGGAAGGAG    c.6600
 Y  I  H  L  A  E  R  L  G |   T  P  E  L  S  T  A  E  R  K  E      p.2200

          .         .         .         .         .         .       g.317078
 TTGGAGAACAAGTTGAAGGAGCGGGAGGAATTCCTAATTCCCATTTACCATCAGGTAGCC       c.6660
 L  E  N  K  L  K  E  R  E  E  F  L  I  P  I  Y  H  Q  V  A         p.2220

          .         .         .         .         .         .       g.317138
 GTGCAGTTTGCTGACTTGCACGACACACCAGGCCGGATGCAGGAGAAGGGTGTTATTAGC       c.6720
 V  Q  F  A  D  L  H  D  T  P  G  R  M  Q  E  K  G  V  I  S         p.2240

  | 54       .         .         .         .         .         .    g.317861
  | GATATCCTGGATTGGAAAACATCCCGTACCTTCTTCTACTGGCGGCTGAGGCGTCTTCTG    c.6780
  | D  I  L  D  W  K  T  S  R  T  F  F  Y  W  R  L  R  R  L  L      p.2260

          .         .         .         .         .         .       g.317921
 CTGGAGGACCTGGTCAAGAAGAAAATCCACAATGCCAACCCTGAGCTGACTGATGGCCAG       c.6840
 L  E  D  L  V  K  K  K  I  H  N  A  N  P  E  L  T  D  G  Q         p.2280

          .         .         .         .         .  | 55      .    g.325902
 ATTCAAGCCATGTTAAGGCGCTGGTTTGTGGAAGTGGAAGGAACAGTGAAG | GCTTATGTT    c.6900
 I  Q  A  M  L  R  R  W  F  V  E  V  E  G  T  V  K   | A  Y  V      p.2300

          .         .         .         .         .         .       g.325962
 TGGGACAATAATAAGGATCTGGCGGAGTGGCTAGAGAAACAGCTGACAGAGGAGGATGGT       c.6960
 W  D  N  N  K  D  L  A  E  W  L  E  K  Q  L  T  E  E  D  G         p.2320

          .         .         .         .         .         .       g.326022
 GTTCACTCGGTAATAGAGGAAAACATCAAATGCATCAGCAGAGACTACGTCCTCAAGCAA       c.7020
 V  H  S  V  I  E  E  N  I  K  C  I  S  R  D  Y  V  L  K  Q         p.2340

          | 56         .         .         .         .         .    g.327580
 ATCCGCAG | CTTGGTCCAGGCCAATCCAGAGGTTGCCATGGATTCCATCATCCATATGACG    c.7080
 I  R  S  |  L  V  Q  A  N  P  E  V  A  M  D  S  I  I  H  M  T      p.2360

          .         .         .         .         .         .       g.327640
 CAGCACATATCACCCACTCAGCGAGCAGAAGTCATACGGATCCTCTCCACAATGGATTCC       c.7140
 Q  H  I  S  P  T  Q  R  A  E  V  I  R  I  L  S  T  M  D  S         p.2380

          .                                                         g.327652
 CCTTCCACGTAG                                                       c.7152
 P  S  T  X                                                         p.2383

          .         .         .         .         .         .       g.327712
 gaagagcttcctgcctgtccctgccctgtctctggagaaaagggctagagctgcctttta       c.*60

          .         .         .         .         .         .       g.327772
 caactgtaaccactgtaatgagaaggcacaggagacccagcactggagtcaaatggcatt       c.*120

          .         .         .         .         .         .       g.327832
 ttacttcctctcgtttcaggttatgcatgacatcctgggatgtaagatcacagaatcccc       c.*180

          .         .         .         .         .         .       g.327892
 ctccagcccaccagtcacacctaccccattcagtatttattaccctggccaggcctagtc       c.*240

          .         .         .         .         .         .       g.327952
 ctccactccctgcacaggactgagaaggcaatgaaaggtacaaacatgtaccatgaggtc       c.*300

          .         .         .         .         .         .       g.328012
 ttactaaccaaagtagggctgcccctcctgtcctgacagccccttggcctcccagcatgg       c.*360

          .         .         .         .         .         .       g.328072
 ggaagcgtgaggagttgcccagcagtgagcagcccccctcactcctggccccatgagccg       c.*420

          .         .         .         .         .         .       g.328132
 cagccacaggcagcagaggagggctaaggagaggaggaagcctcaagtccattgtttatt       c.*480

          .         .         .         .         .         .       g.328192
 accccgactcttagcccagcacacagtaggcactggagaggaatgattcccagtttaacc       c.*540

          .         .         .         .         .         .       g.328252
 acactacggtaccttttatgaagaaaaattagagcataaaatctactacaagctccatag       c.*600

          .         .         .         .         .         .       g.328312
 gaactcaaagatgagggcaaaactgtgagccaagaagcagagaaagaaaatagaaccagt       c.*660

          .         .         .         .         .         .       g.328372
 tattcttgatttaggggacctcaaccttgggttcagtctctgaggacaaagggaaaggta       c.*720

          .         .         .         .         .         .       g.328432
 gttgttggcctgcctctcgcctgcacgtcactgctggactagctgtcgcatgtggctggg       c.*780

          .         .         .         .         .         .       g.328492
 agctgcaaggccagtgcttgaggggccccagcagttccacaggtggtgaagcctgagttg       c.*840

          .         .         .         .         .         .       g.328552
 gcagaggaggagccagaagagaactgccctttctgcactggtggaaactagttatttatg       c.*900

          .         .         .         .         .         .       g.328612
 ccatgtggagagccagtgagatagatagatagtctgtttgttttgaggacttggaaagtt       c.*960

          .         .         .         .         .         .       g.328672
 gttcctatgaagcctggagcttggatggttttgagaggttaatggtgcctccacactcac       c.*1020

          .         .         .         .         .         .       g.328732
 tcttccctagttccaggattactgtcctagcagctaacggttctactctcttccccagag       c.*1080

          .         .         .         .         .         .       g.328792
 tgtagacaggcagcaggtctccccacagctctgaaaggaccctggtgacagctacaccct       c.*1140

          .         .         .         .         .         .       g.328852
 cagcaccaggagctggccttcctgatgagggaggcttccaggaaacacagaatccacatg       c.*1200

          .         .         .         .         .         .       g.328912
 accttaagattatttacaactcagtcatggtgctgctgtcctccaggcttactggcccct       c.*1260

          .         .         .         .         .         .       g.328972
 cctgactggcatcaggggcttcctcaggtggtggagagagtttactttcaacaactagtt       c.*1320

          .         .         .         .         .         .       g.329032
 tattcaagaaaagaacttactgattcctctgttcctaaagcaagagtggcaggtgatcag       c.*1380

          .         .         .         .         .         .       g.329092
 ggctggtgtagcatccggttcctttagtgcagctaactgcatttgtcactgatgaccaag       c.*1440

          .         .         .         .         .         .       g.329152
 gaggaaatcactaagacatttgagaagcagtggtatgaacgttcttggacaagccacagt       c.*1500

          .         .         .         .         .         .       g.329212
 tctgagccttaaccctgtagtttgcacacaagaacgagctccacctccccttcttcagga       c.*1560

          .         .         .         .         .         .       g.329272
 ggaatctgtgcggatagattggctggacttttcaatggttctgggttgcaggtgggcact       c.*1620

          .         .         .         .         .         .       g.329332
 gtatggctgggtatggagcggacagcccccaggagtcagagcctcagcccggctgccctg       c.*1680

          .         .         .         .         .         .       g.329392
 gtggaaggtacaggtgttcagcaccttcagaaaagggcataaagtggtgggggacaattc       c.*1740

          .         .         .         .         .         .       g.329452
 tcagtccaggaaaatgcattgaccattgctggctatttgcttacctagtaagaattggat       c.*1800

          .         .         .         .         .         .       g.329512
 tcatttttgaccagattattcttctatgcttttttgcaataaatcaaatcccacatatct       c.*1860

          .         .         .         .         .         .       g.329572
 acaagtggtatgaagtcctgcaccccccaggaggcctgtccaggcatgtcttcagaggca       c.*1920

          .         .         .         .         .         .       g.329632
 gggtgggttacactcatttacctcccctctccccaccaaattatgacacaaacgagtatg       c.*1980

          .         .         .         .         .         .       g.329692
 tttcctctctagaaccctgtaatgcctcctcccccatccccagagctccttactgtaggt       c.*2040

          .         .         .         .         .         .       g.329752
 cttaccctggacaaggattttttcaagttggaggcacagaacatgagcaatctgacattc       c.*2100

          .         .         .         .         .         .       g.329812
 ccacagcccctcaaacatgcaaggctactaaggcaggaggagtataaatgatggatattg       c.*2160

          .         .         .         .         .         .       g.329872
 accaagacctgcttggacggagaccgccatattatctgttctcttcgttcacaaaacagc       c.*2220

          .         .         .         .         .         .       g.329932
 cttcacttgtctcagaatttgatggacacatactgtgatgagcaggagcttcagatgcac       c.*2280

          .         .         .         .                           g.329976
 tctttacacattttgttgaaataaacctctacatttgtagaaga                       c.*2324

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Acetyl-CoA carboxylase alpha protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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