acetyl-CoA carboxylase alpha (ACACA) - coding DNA reference sequence

(used for variant description)

(last modified January 16, 2014)


This file was created to facilitate the description of sequence variants on transcript NM_198836.1 in the ACACA gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000017.10, covering ACACA transcript NM_198836.1.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                   .                g.55854
                                                  cggcctggtgc       c.-181

 .         .         .         .         .         .                g.55914
 tgcacgcctgtcagccatcgcccgagccgccggcgtctcctcccgcccagcagttcctcc       c.-121

 .         .         .         .         .       | 02 .             g.75105
 acgcaggggctccggaatcgcccgaccgcacacgttgccaccctgag | gtctttctggaag    c.-61

 .         .         .         .    | 03    .         .             g.84563
 tggatatctactcagacagtaagaattataagag | ctgtaagagctcattttggaggaata    c.-1

          .         .         .         .         .         .       g.84623
 ATGGATGAACCATCTCCCTTGGCCCAACCTCTGGAGCTGAACCAGCACTCTCGATTCATA       c.60
 M  D  E  P  S  P  L  A  Q  P  L  E  L  N  Q  H  S  R  F  I         p.20

          .         .         .         .         .         .       g.84683
 ATAGGTTCTGTGTCTGAAGATAACTCAGAGGATGAGATCAGCAACCTGGTGAAGTTGGAC       c.120
 I  G  S  V  S  E  D  N  S  E  D  E  I  S  N  L  V  K  L  D         p.40

          .         .         .         .         .         .       g.84743
 CTACTGGAGGAGAAGGAGGGCTCCTTGTCACCTGCTTCTGTTGGCTCAGATACACTCTCT       c.180
 L  L  E  E  K  E  G  S  L  S  P  A  S  V  G  S  D  T  L  S         p.60

          .         .         .         .        | 04.         .    g.130044
 GATTTGGGGATCTCTAGCCTACAGGATGGCTTGGCCTTGCACATAAG | GTCCAGCATGTCT    c.240
 D  L  G  I  S  S  L  Q  D  G  L  A  L  H  I  R  |  S  S  M  S      p.80

          .         .         .         .         .         .       g.130104
 GGCTTGCACCTAGTAAAGCAGGGCCGAGACAGAAAGAAAATAGATTCTCAACGAGATTTC       c.300
 G  L  H  L  V  K  Q  G  R  D  R  K  K  I  D  S  Q  R  D  F         p.100

          .         .         .         .         .         .       g.130164
 ACTGTGGCTTCTCCAGCAGAATTTGTTACTCGCTTTGGGGGAAATAAAGTGATTGAGAAG       c.360
 T  V  A  S  P  A  E  F  V  T  R  F  G  G  N  K  V  I  E  K         p.120

  | 05       .         .         .         .         .         .    g.131656
  | GTTCTTATTGCTAACAATGGCATTGCAGCAGTGAAATGCATGCGGTCTATCCGTAGGTGG    c.420
  | V  L  I  A  N  N  G  I  A  A  V  K  C  M  R  S  I  R  R  W      p.140

          .         .         .         .         .         .       g.131716
 TCTTATGAAATGTTTCGAAATGAACGTGCAATTAGATTCGTTGTCATGGTCACACCTGAA       c.480
 S  Y  E  M  F  R  N  E  R  A  I  R  F  V  V  M  V  T  P  E         p.160

          .          | 06        .         .         .         .    g.137045
 GACCTTAAAGCCAATGCAG | AATACATTAAGATGGCAGATCACTATGTGCCAGTGCCTGGA    c.540
 D  L  K  A  N  A  E |   Y  I  K  M  A  D  H  Y  V  P  V  P  G      p.180

          .         .         .         .         .         .       g.137105
 GGACCAAACAACAACAACTATGCAAATGTGGAATTAATTCTTGATATTGCTAAAAGGATC       c.600
 G  P  N  N  N  N  Y  A  N  V  E  L  I  L  D  I  A  K  R  I         p.200

           | 07        .         .         .         .         .    g.137946
 CCAGTACAA | GCAGTGTGGGCTGGCTGGGGTCATGCTTCTGAGAATCCCAAACTACCGGAA    c.660
 P  V  Q   | A  V  W  A  G  W  G  H  A  S  E  N  P  K  L  P  E      p.220

          .         .         .  | 08      .         .         .    g.138989
 CTTCTCTTGAAAAATGGCATTGCCTTCATGG | GTCCTCCAAGCCAGGCCATGTGGGCTTTA    c.720
 L  L  L  K  N  G  I  A  F  M  G |   P  P  S  Q  A  M  W  A  L      p.240

          .         .         .         .         .         .       g.139049
 GGGGATAAGATTGCATCTTCCATAGTGGCTCAAACTGCAGGTATCCCAACTCTTCCCTGG       c.780
 G  D  K  I  A  S  S  I  V  A  Q  T  A  G  I  P  T  L  P  W         p.260

          . | 09       .         .         .         .         .    g.140762
 AGCGGCAGTG | GTCTTCGTGTGGACTGGCAGGAAAATGATTTTTCAAAACGTATCTTAAAT    c.840
 S  G  S  G |   L  R  V  D  W  Q  E  N  D  F  S  K  R  I  L  N      p.280

          .         .         .         .         .        | 10.    g.144153
 GTTCCCCAGGAGCTATATGAAAAAGGTTATGTGAAAGATGTGGATGATGGGCTACAG | GCA    c.900
 V  P  Q  E  L  Y  E  K  G  Y  V  K  D  V  D  D  G  L  Q   | A      p.300

          .         .         .         .         .         .       g.144213
 GCTGAGGAAGTTGGATATCCAGTAATGATCAAGGCCTCAGAGGGAGGAGGAGGGAAGGGA       c.960
 A  E  E  V  G  Y  P  V  M  I  K  A  S  E  G  G  G  G  K  G         p.320

          .         .         .         .         | 11         .    g.151117
 ATTAGAAAAGTCAACAATGCAGATGACTTCCCTAATCTCTTCAGACAG | GTTCAAGCTGAA    c.1020
 I  R  K  V  N  N  A  D  D  F  P  N  L  F  R  Q   | V  Q  A  E      p.340

          .         .         .         .         .         .       g.151177
 GTTCCTGGATCTCCCATATTTGTGATGAGACTAGCCAAACAATCTCGTCATCTGGAGGTG       c.1080
 V  P  G  S  P  I  F  V  M  R  L  A  K  Q  S  R  H  L  E  V         p.360

          .         .         .         .         .         .       g.151237
 CAGATCTTAGCGGACCAATATGGCAATGCTATCTCTTTGTTTGGTCGTGATTGCTCTGTA       c.1140
 Q  I  L  A  D  Q  Y  G  N  A  I  S  L  F  G  R  D  C  S  V         p.380

          .         .         .         .         .         .       g.151297
 CAACGCAGGCATCAGAAGATTATTGAAGAAGCACCTGCTACTATTGCTACTCCAGCAGTA       c.1200
 Q  R  R  H  Q  K  I  I  E  E  A  P  A  T  I  A  T  P  A  V         p.400

          .         | 12         .         .         .         .    g.155492
 TTTGAACACATGGAACAG | TGTGCGGTGAAACTTGCCAAAATGGTGGGTTATGTGAGTGCT    c.1260
 F  E  H  M  E  Q   | C  A  V  K  L  A  K  M  V  G  Y  V  S  A      p.420

          .         .         .         .         .         .       g.155552
 GGGACTGTGGAATACCTGTACAGCCAGGATGGCAGCTTCTACTTTCTGGAATTGAATCCT       c.1320
 G  T  V  E  Y  L  Y  S  Q  D  G  S  F  Y  F  L  E  L  N  P         p.440

          .         .         .         .         .         .       g.155612
 CGGCTGCAGGTAGAGCACCCTTGTACAGAGATGGTGGCTGATGTCAATCTCCCTGCAGCA       c.1380
 R  L  Q  V  E  H  P  C  T  E  M  V  A  D  V  N  L  P  A  A         p.460

           | 13        .         .         .         .         .    g.156658
 CAGCTCCAG | ATTGCCATGGGGATTCCTCTATATAGAATCAAGGATATCCGTATGATGTAT    c.1440
 Q  L  Q   | I  A  M  G  I  P  L  Y  R  I  K  D  I  R  M  M  Y      p.480

          .         .         .         .         .         .       g.156718
 GGGGTATCTCCCTGGGGTGATTCTCCCATTGATTTTGAAGATTCTGCACACGTTCCTTGT       c.1500
 G  V  S  P  W  G  D  S  P  I  D  F  E  D  S  A  H  V  P  C         p.500

          .         .         .         .         .  | 14      .    g.157123
 CCAAGGGGCCATGTTATTGCTGCTCGGATCACTAGTGAAAATCCAGATGAG | GGTTTTAAG    c.1560
 P  R  G  H  V  I  A  A  R  I  T  S  E  N  P  D  E   | G  F  K      p.520

          .         .         .         .         .         .       g.157183
 CCCAGCTCAGGAACAGTTCAGGAGCTAAATTTCCGCAGCAATAAGAATGTTTGGGGATAT       c.1620
 P  S  S  G  T  V  Q  E  L  N  F  R  S  N  K  N  V  W  G  Y         p.540

          .         .         .         .         .         .       g.157243
 TTCAGTGTTGCTGCTGCAGGGGGACTTCATGAATTTGCTGATTCTCAGTTTGGTCACTGC       c.1680
 F  S  V  A  A  A  G  G  L  H  E  F  A  D  S  Q  F  G  H  C         p.560

          .         .         .      | 15  .         .         .    g.161965
 TTTTCTTGGGGAGAAAACAGAGAAGAGGCAATTTC | AAACATGGTGGTGGCTTTGAAGGAG    c.1740
 F  S  W  G  E  N  R  E  E  A  I  S  |  N  M  V  V  A  L  K  E      p.580

          .         .         .         .         .         .       g.162025
 CTGTCTATTCGGGGTGACTTTCGAACTACAGTTGAATACCTGATCAAATTGTTAGAGACT       c.1800
 L  S  I  R  G  D  F  R  T  T  V  E  Y  L  I  K  L  L  E  T         p.600

          .         .         .         .         .         .       g.162085
 GAAAGCTTTCAGATGAACAGAATTGATACTGGCTGGCTGGACAGACTGATAGCAGAAAAA       c.1860
 E  S  F  Q  M  N  R  I  D  T  G  W  L  D  R  L  I  A  E  K         p.620

        | 16 .         .         .         .         .         .    g.162922
 GTACAG | GCTGAGCGACCTGACACCATGTTGGGGGTTGTGTGTGGTGCCCTCCACGTGGCA    c.1920
 V  Q   | A  E  R  P  D  T  M  L  G  V  V  C  G  A  L  H  V  A      p.640

          .         .         .         .         . | 17       .    g.166314
 GATGTGAGCCTGCGGAATAGCGTCTCTAACTTCCTTCACTCCTTAGAAAG | GGGTCAAGTC    c.1980
 D  V  S  L  R  N  S  V  S  N  F  L  H  S  L  E  R  |  G  Q  V      p.660

          .         .         .         .         .         .       g.166374
 CTTCCTGCTCATACACTTCTGAATACAGTAGATGTTGAACTTATCTATGAGGGAGTCAAG       c.2040
 L  P  A  H  T  L  L  N  T  V  D  V  E  L  I  Y  E  G  V  K         p.680

          .   | 18     .         .         .         .         .    g.166870
 TATGTACTTAAG | GTGACTCGACAGTCCCCCAACTCCTATGTGGTGATCATGAATGGCTCA    c.2100
 Y  V  L  K   | V  T  R  Q  S  P  N  S  Y  V  V  I  M  N  G  S      p.700

          .         .         .         .         .         .       g.166930
 TGTGTAGAAGTAGATGTACATCGGCTGAGTGACGGTGGACTGCTCTTGTCCTATGATGGC       c.2160
 C  V  E  V  D  V  H  R  L  S  D  G  G  L  L  L  S  Y  D  G         p.720

          .         .         .         | 19         .         .    g.168032
 AGCAGTTATACTACGTATATGAAAGAGGAAGTGGATAG | ATATCGCATCACAATTGGCAAT    c.2220
 S  S  Y  T  T  Y  M  K  E  E  V  D  R  |  Y  R  I  T  I  G  N      p.740

          .         .         .         .         .         .       g.168092
 AAAACCTGTGTGTTTGAGAAGGAAAATGACCCATCGGTGATGCGCTCACCTTCTGCTGGG       c.2280
 K  T  C  V  F  E  K  E  N  D  P  S  V  M  R  S  P  S  A  G         p.760

          .         .         .         .         .         .       g.168152
 AAGTTAATCCAGTACATTGTAGAAGATGGAGGTCATGTGTTTGCCGGCCAGTGCTATGCT       c.2340
 K  L  I  Q  Y  I  V  E  D  G  G  H  V  F  A  G  Q  C  Y  A         p.780

           | 20        .         .         .         .         .    g.169823
 GAGATTGAG | GTAATGAAGATGGTAATGACCTTAACAGCTGTGGAGTCTGGCTGTATCCAT    c.2400
 E  I  E   | V  M  K  M  V  M  T  L  T  A  V  E  S  G  C  I  H      p.800

          .         .         .         .         .         .       g.169883
 TACGTCAAGCGACCTGGAGCAGCTCTTGACCCTGGCTGTGTACTAGCCAAAATGCAACTG       c.2460
 Y  V  K  R  P  G  A  A  L  D  P  G  C  V  L  A  K  M  Q  L         p.820

          .         .     | 21   .         .         .         .    g.170288
 GACAACCCCAGCAAGGTTCAGCAG | GCTGAACTTCACACAGGTAGTCTGCCACGGATCCAG    c.2520
 D  N  P  S  K  V  Q  Q   | A  E  L  H  T  G  S  L  P  R  I  Q      p.840

          .         .         .         .         .         .       g.170348
 AGCACGGCACTCAGAGGCGAGAAACTCCATCGAGTGTTCCATTATGTCCTGGATAATCTG       c.2580
 S  T  A  L  R  G  E  K  L  H  R  V  F  H  Y  V  L  D  N  L         p.860

          .         .         .         .         .  | 22      .    g.171436
 GTCAATGTAATGAATGGATACTGCCTTCCAGATCCTTTCTTTAGCAGCAAG | GTAAAAGAC    c.2640
 V  N  V  M  N  G  Y  C  L  P  D  P  F  F  S  S  K   | V  K  D      p.880

          .         .         .         .         .         .       g.171496
 TGGGTAGAGCGATTGATGAAAACCCTCAGAGATCCCTCCCTGCCTCTCCTAGAATTGCAA       c.2700
 W  V  E  R  L  M  K  T  L  R  D  P  S  L  P  L  L  E  L  Q         p.900

          .         .         .         .         .         .       g.171556
 GATATTATGACCAGTGTGTCTGGCCGCATTCCCCCCAATGTGGAGAAGTCTATCAAGAAG       c.2760
 D  I  M  T  S  V  S  G  R  I  P  P  N  V  E  K  S  I  K  K         p.920

          .         .         .         .         .         .       g.171616
 GAAATGGCTCAGTATGCTAGCAACATCACATCAGTCCTCTGTCAGTTTCCCAGCCAGCAG       c.2820
 E  M  A  Q  Y  A  S  N  I  T  S  V  L  C  Q  F  P  S  Q  Q         p.940

  | 23       .         .         .         .         .         .    g.172993
  | ATTGCAAACATCCTAGATAGCCATGCAGCTACATTGAACCGGAAATCTGAACGGGAAGTC    c.2880
  | I  A  N  I  L  D  S  H  A  A  T  L  N  R  K  S  E  R  E  V      p.960

          .         .         .         .  | 24      .         .    g.174441
 TTCTTTATGAATACTCAGAGCATTGTTCAGCTGGTACAGAG | GTACCGAAGTGGCATCCGA    c.2940
 F  F  M  N  T  Q  S  I  V  Q  L  V  Q  R  |  Y  R  S  G  I  R      p.980

          .         .         .         .         .         .       g.174501
 GGCCACATGAAGGCTGTGGTGATGGATCTGCTCCGGCAGTACCTGCGAGTAGAGACACAA       c.3000
 G  H  M  K  A  V  V  M  D  L  L  R  Q  Y  L  R  V  E  T  Q         p.1000

          . | 25       .         .         .         .         .    g.179938
 TTCCAGAATG | GTCACTATGACAAATGTGTATTCGCCCTCCGAGAAGAGAATAAAAGTGAC    c.3060
 F  Q  N  G |   H  Y  D  K  C  V  F  A  L  R  E  E  N  K  S  D      p.1020

          .         .         .         .         .         .       g.179998
 ATGAACACTGTACTGAACTACATCTTCTCTCACGCTCAAGTCACCAAGAAGAATCTTCTG       c.3120
 M  N  T  V  L  N  Y  I  F  S  H  A  Q  V  T  K  K  N  L  L         p.1040

          .      | 26  .         .         .         .         .    g.188574
 GTCACAATGCTTATT | GATCAGTTGTGTGGCCGGGACCCTACTCTCACTGATGAGCTGCTG    c.3180
 V  T  M  L  I   | D  Q  L  C  G  R  D  P  T  L  T  D  E  L  L      p.1060

          .         .         .         .         .         .       g.188634
 AATATTCTCACAGAGCTAACTCAACTCAGTAAGACCACCAATGCCAAAGTAGCACTTCGA       c.3240
 N  I  L  T  E  L  T  Q  L  S  K  T  T  N  A  K  V  A  L  R         p.1080

           | 27        .         .         .         .         .    g.189927
 GCACGCCAG | GTTCTTATTGCCTCCCATTTGCCATCATATGAGCTTCGCCATAACCAAGTA    c.3300
 A  R  Q   | V  L  I  A  S  H  L  P  S  Y  E  L  R  H  N  Q  V      p.1100

          .         .         .         .         .         .       g.189987
 GAGTCTATCTTCCTATCAGCTATTGACATGTATGGACATCAATTTTGCATTGAGAACCTG       c.3360
 E  S  I  F  L  S  A  I  D  M  Y  G  H  Q  F  C  I  E  N  L         p.1120

     | 28    .         .         .         .         .         .    g.191437
 CAG | AAACTCATCCTATCAGAAACATCTATTTTTGATGTCCTACCAAACTTCTTCTATCAC    c.3420
 Q   | K  L  I  L  S  E  T  S  I  F  D  V  L  P  N  F  F  Y  H      p.1140

          .         .         .    | 29    .         .         .    g.193166
 AGCAACCAAGTAGTGAGGATGGCAGCTCTGGAG | GTGTATGTTCGAAGGGCTTATATTGCC    c.3480
 S  N  Q  V  V  R  M  A  A  L  E   | V  Y  V  R  R  A  Y  I  A      p.1160

          .         .         .         .         .         .       g.193226
 TATGAACTTAACAGCGTACAACACCGCCAGCTTAAGGACAACACCTGTGTGGTGGAATTC       c.3540
 Y  E  L  N  S  V  Q  H  R  Q  L  K  D  N  T  C  V  V  E  F         p.1180

          .         .         .   | 30     .         .       | 31 . g.207192
 CAGTTCATGCTGCCCACATCTCATCCAAACAG | AGGGAACATCCCTACGCTAAACAG | AATG c.3600
 Q  F  M  L  P  T  S  H  P  N  R  |  G  N  I  P  T  L  N  R  |  M   p.1200

          .         .         .         .         .         .       g.207252
 TCCTTCTCCTCCAACCTCAACCACTATGGCATGACCCATGTAGCTAGTGTCAGCGATGTA       c.3660
 S  F  S  S  N  L  N  H  Y  G  M  T  H  V  A  S  V  S  D  V         p.1220

          .         .         .         .         .         .       g.207312
 CTGTTGGACAACTCATTCACTCCACCTTGTCAGCGGATGGGCGGAATGGTCTCTTTTCGG       c.3720
 L  L  D  N  S  F  T  P  P  C  Q  R  M  G  G  M  V  S  F  R         p.1240

          .         . | 32       .         .         .         .    g.208149
 ACTTTTGAAGATTTTGTCAG | GATCTTTGATGAAGTGATGGGCTGCTTCTCTGACTCCCCA    c.3780
 T  F  E  D  F  V  R  |  I  F  D  E  V  M  G  C  F  S  D  S  P      p.1260

          .         .         .         .         .        | 33.    g.209119
 CCCCAGAGTCCCACATTCCCTGAGGCAGGTCACACGTCTCTTTATGATGAGGATAAG | GTT    c.3840
 P  Q  S  P  T  F  P  E  A  G  H  T  S  L  Y  D  E  D  K   | V      p.1280

          .         .         .         .         .         .       g.209179
 CCCAGGGATGAACCAATTCACATTCTCAATGTGGCTATCAAGACTGACTGTGATATTGAG       c.3900
 P  R  D  E  P  I  H  I  L  N  V  A  I  K  T  D  C  D  I  E         p.1300

          .         .         .         .      | 34  .         .    g.214491
 GATGACAGGCTGGCAGCTATGTTCAGAGAATTTACCCAGCAAAAT | AAAGCTACCCTGGTT    c.3960
 D  D  R  L  A  A  M  F  R  E  F  T  Q  Q  N   | K  A  T  L  V      p.1320

          .         .         .         .   | 35     .         .    g.214794
 GACCATGGGATCCGGCGCCTTACTTTCCTGGTTGCACAAAAG | GATTTCAGAAAGCAGGTC    c.4020
 D  H  G  I  R  R  L  T  F  L  V  A  Q  K   | D  F  R  K  Q  V      p.1340

          .         .        | 36.         .         .         .    g.221579
 AACTATGAGGTGGATCGGAGATTTCAT | AGAGAATTCCCTAAATTTTTTACATTCCGAGCA    c.4080
 N  Y  E  V  D  R  R  F  H   | R  E  F  P  K  F  F  T  F  R  A      p.1360

           | 37        .         .         .         .         .    g.222707
 AGGGATAAG | TTTGAGGAGGATCGTATCTATCGTCATCTGGAGCCTGCTCTGGCTTTCCAG    c.4140
 R  D  K   | F  E  E  D  R  I  Y  R  H  L  E  P  A  L  A  F  Q      p.1380

          .         .         .         .         .         .       g.222767
 TTAGAGCTGAACCGGATGAGAAATTTTGACCTCACTGCCATTCCATGTGCTAATCACAAG       c.4200
 L  E  L  N  R  M  R  N  F  D  L  T  A  I  P  C  A  N  H  K         p.1400

          .         .         .         .         .         .       g.222827
 ATGCACCTGTATCTCGGGGCAGCCAAGGTGGAAGTGGGCACAGAAGTGACAGACTACAGG       c.4260
 M  H  L  Y  L  G  A  A  K  V  E  V  G  T  E  V  T  D  Y  R         p.1420

          .         .         .         .      | 38  .         .    g.223701
 TTCTTTGTTCGTGCAATCATCAGGCATTCTGATCTGGTCACCAAG | GAAGCTTCTTTTGAA    c.4320
 F  F  V  R  A  I  I  R  H  S  D  L  V  T  K   | E  A  S  F  E      p.1440

          .         .         .         .         .         .       g.223761
 TATCTGCAAAATGAAGGGGAGCGGCTACTCCTGGAAGCCATGGATGAGTTGGAAGTTGCT       c.4380
 Y  L  Q  N  E  G  E  R  L  L  L  E  A  M  D  E  L  E  V  A         p.1460

          .         .         .         .         .         .       g.223821
 TTTAACAATACAAATGTCCGCACTGACTGTAACCACATCTTCCTCAACTTTGTGCCCACG       c.4440
 F  N  N  T  N  V  R  T  D  C  N  H  I  F  L  N  F  V  P  T         p.1480

          .         .  | 39      .         .         .         .    g.226521
 GTTATCATGGACCCATCAAAG | ATTGAGGAATCCGTGCGGAGCATGGTAATGCGGTATGGA    c.4500
 V  I  M  D  P  S  K   | I  E  E  S  V  R  S  M  V  M  R  Y  G      p.1500

          .         .         .         .         .         .       g.226581
 AGTCGCCTGTGGAAATTGCGCGTCCTCCAGGCAGAACTGAAAATCAACATTCGCCTGACG       c.4560
 S  R  L  W  K  L  R  V  L  Q  A  E  L  K  I  N  I  R  L  T         p.1520

          .         .         .         .         .         .       g.226641
 CCAACTGGAAAAGCAATTCCCATCCGCCTCTTCCTGACAAACGAGTCTGGCTATTACTTG       c.4620
 P  T  G  K  A  I  P  I  R  L  F  L  T  N  E  S  G  Y  Y  L         p.1540

          .         .         .         .      | 40  .         .    g.233620
 GATATCAGCCTATACAAGGAAGTGACTGACTCCAGGACAGCACAG | ATCATGTTTCAGGCA    c.4680
 D  I  S  L  Y  K  E  V  T  D  S  R  T  A  Q   | I  M  F  Q  A      p.1560

          .         .         .         .         .         .       g.233680
 TATGGAGACAAACAGGGACCACTGCATGGAATGTTAATCAATACTCCATATGTGACCAAA       c.4740
 Y  G  D  K  Q  G  P  L  H  G  M  L  I  N  T  P  Y  V  T  K         p.1580

          .         .         .         .         .         .       g.233740
 GACCTGCTGCAATCAAAGAGGTTCCAGGCACAATCCTTAGGGACAACATACATATATGAT       c.4800
 D  L  L  Q  S  K  R  F  Q  A  Q  S  L  G  T  T  Y  I  Y  D         p.1600

          .         .  | 41      .         .         .         .    g.235594
 ATCCCAGAGATGTTTCGGCAG | TCCCTGATCAAACTCTGGGAGTCTATGTCCACTCAAGCA    c.4860
 I  P  E  M  F  R  Q   | S  L  I  K  L  W  E  S  M  S  T  Q  A      p.1620

          .         .         .         .         .         .       g.235654
 TTTCTTCCATCTCCCCCTCTGCCTTCTGACATGCTGACTTACACTGAACTGGTACTGGAT       c.4920
 F  L  P  S  P  P  L  P  S  D  M  L  T  Y  T  E  L  V  L  D         p.1640

          .         .         .         .         | 42         .    g.252950
 GATCAAGGTCAGCTGGTCCACATGAACAGGCTTCCAGGAGGAAATGAG | ATTGGCATGGTA    c.4980
 D  Q  G  Q  L  V  H  M  N  R  L  P  G  G  N  E   | I  G  M  V      p.1660

          .         .         .         .         .         .       g.253010
 GCTTGGAAAATGACCTTTAAAAGTCCTGAATATCCAGAAGGCCGAGATATCATTGTTATT       c.5040
 A  W  K  M  T  F  K  S  P  E  Y  P  E  G  R  D  I  I  V  I         p.1680

          .         .         .         .         .         .       g.253070
 GGCAATGACATCACATACCGAATTGGGTCCTTTGGGCCTCAAGAGGATTTGTTATTTCTC       c.5100
 G  N  D  I  T  Y  R  I  G  S  F  G  P  Q  E  D  L  L  F  L         p.1700

          .         .         .         .         .         .       g.253130
 AGAGCTTCCGAACTTGCTAGGGCAGAAGGTATTCCACGCATCTATGTATCAGCCAACAGT       c.5160
 R  A  S  E  L  A  R  A  E  G  I  P  R  I  Y  V  S  A  N  S         p.1720

          .         .         .         .         .         .       g.253190
 GGAGCAAGAATCGGACTGGCAGAAGAAATTCGCCATATGTTTCATGTGGCCTGGGTAGAT       c.5220
 G  A  R  I  G  L  A  E  E  I  R  H  M  F  H  V  A  W  V  D         p.1740

          .         | 43         .         .         .         .    g.259242
 CCTGAGGATCCTTACAAG | GGATACAGGTATTTATATCTGACTCCTCAAGATTATAAGAGA    c.5280
 P  E  D  P  Y  K   | G  Y  R  Y  L  Y  L  T  P  Q  D  Y  K  R      p.1760

          .         .         .         .         .       | 44 .    g.263560
 GTCAGTGCTCTCAACTCTGTCCATTGTGAACACGTGGAAGATGAAGGAGAATCCAG | GTAC    c.5340
 V  S  A  L  N  S  V  H  C  E  H  V  E  D  E  G  E  S  R  |  Y      p.1780

          .         .         .         .         .         .       g.263620
 AAGATAACAGATATTATTGGGAAAGAAGAGGGAATTGGACCCGAGAACCTTCGAGGTTCT       c.5400
 K  I  T  D  I  I  G  K  E  E  G  I  G  P  E  N  L  R  G  S         p.1800

          .         .         .         .         .        | 45.    g.265007
 GGAATGATTGCTGGAGAATCCTCATTGGCCTATAATGAGATCATTACCATCAGCCTG | GTG    c.5460
 G  M  I  A  G  E  S  S  L  A  Y  N  E  I  I  T  I  S  L   | V      p.1820

          .         .         .         .         .         .       g.265067
 ACGTGCCGGGCCATTGGGATTGGGGCTTACCTTGTCCGGCTGGGACAGAGAACCATCCAG       c.5520
 T  C  R  A  I  G  I  G  A  Y  L  V  R  L  G  Q  R  T  I  Q         p.1840

          .         .         .         .         | 46         .    g.284770
 GTTGAGAATTCTCACTTAATTCTAACAGGAGCTGGAGCCCTCAACAAA | GTCCTCGGGCGG    c.5580
 V  E  N  S  H  L  I  L  T  G  A  G  A  L  N  K   | V  L  G  R      p.1860

          .         .         .         .         .         .       g.284830
 GAAGTGTACACCTCCAATAACCAGCTGGGGGGCATCCAGATTATGCACAACAATGGGGTG       c.5640
 E  V  Y  T  S  N  N  Q  L  G  G  I  Q  I  M  H  N  N  G  V         p.1880

          .         .         .         .         .         .       g.284890
 ACCCACTGCACTGTGTGTGATGACTTTGAAGGGGTTTTCACTGTCCTGCACTGGCTGTCT       c.5700
 T  H  C  T  V  C  D  D  F  E  G  V  F  T  V  L  H  W  L  S         p.1900

          .   | 47     .         .         .         .         .    g.285539
 TACATGCCCAAG | AGCGTGCACAGTTCAGTTCCTCTTCTGAACTCAAAGGATCCTATAGAC    c.5760
 Y  M  P  K   | S  V  H  S  S  V  P  L  L  N  S  K  D  P  I  D      p.1920

          .         .         .         .         .         .       g.285599
 AGAATCATCGAGTTTGTTCCCACAAAGACCCCATACGATCCTCGATGGATGCTAGCAGGC       c.5820
 R  I  I  E  F  V  P  T  K  T  P  Y  D  P  R  W  M  L  A  G         p.1940

          .    | 48    .         .         .         .         .    g.289234
 CGTCCTCACCCAA | CCCAAAAAGGTCAGTGGTTGAGTGGCTTTTTTGACTATGGATCTTTC    c.5880
 R  P  H  P  T |   Q  K  G  Q  W  L  S  G  F  F  D  Y  G  S  F      p.1960

          .         .         .         .         . | 49       .    g.292363
 TCAGAGATTATGCAGCCCTGGGCACAGACTGTGGTGGTTGGTAGAGCCAG | GCTAGGAGGA    c.5940
 S  E  I  M  Q  P  W  A  Q  T  V  V  V  G  R  A  R  |  L  G  G      p.1980

          .         .         .         .         .         .       g.292423
 ATACCTGTGGGAGTTGTTGCTGTAGAAACCCGAACAGTAGAACTAAGTATCCCAGCTGAT       c.6000
 I  P  V  G  V  V  A  V  E  T  R  T  V  E  L  S  I  P  A  D         p.2000

          .         .        | 50.         .         .         .    g.293523
 CCAGCAAACCTGGATTCTGAAGCCAAG | ATAATCCAGCAGGCTGGCCAGGTTTGGTTCCCA    c.6060
 P  A  N  L  D  S  E  A  K   | I  I  Q  Q  A  G  Q  V  W  F  P      p.2020

          .         .         .         .         .         .       g.293583
 GATTCTGCGTTTAAGACATATCAGGCCATCAAGGACTTCAACCGGGAAGGGCTGCCTCTG       c.6120
 D  S  A  F  K  T  Y  Q  A  I  K  D  F  N  R  E  G  L  P  L         p.2040

          .         .         .         .    | 51    .         .    g.301719
 ATGGTCTTTGCCAACTGGAGAGGCTTCTCTGGTGGAATGAAAG | ATATGTACGACCAAGTG    c.6180
 M  V  F  A  N  W  R  G  F  S  G  G  M  K  D |   M  Y  D  Q  V      p.2060

          .         .         .         .         .         .       g.301779
 CTGAAGTTTGGTGCTTACATTGTGGATGGCTTGAGGGAGTGCTGCCAGCCTGTGCTGGTT       c.6240
 L  K  F  G  A  Y  I  V  D  G  L  R  E  C  C  Q  P  V  L  V         p.2080

          .         .         .         .         .         .       g.301839
 TACATTCCTCCCCAGGCTGAGCTGCGGGGTGGCTCCTGGGTGGTGATTGACTCCTCCATC       c.6300
 Y  I  P  P  Q  A  E  L  R  G  G  S  W  V  V  I  D  S  S  I         p.2100

          .         .         .         .  | 52      .         .    g.303343
 AACCCCCGGCACATGGAGATGTATGCTGACCGAGAAAGCAG | GGGATCTGTTCTGGAGCCA    c.6360
 N  P  R  H  M  E  M  Y  A  D  R  E  S  R  |  G  S  V  L  E  P      p.2120

          .         .         .         .         .         .       g.303403
 GAAGGGACAGTAGAAATCAAATTCCGCAGAAAGGATCTGGTGAAAACCATGCGTCGGGTG       c.6420
 E  G  T  V  E  I  K  F  R  R  K  D  L  V  K  T  M  R  R  V         p.2140

          .         .         .     | 53   .         .         .    g.317009
 GACCCAGTCTACATCCACTTGGCTGAGCGATTGG | GGACCCCAGAGCTAAGCACAGCTGAG    c.6480
 D  P  V  Y  I  H  L  A  E  R  L  G |   T  P  E  L  S  T  A  E      p.2160

          .         .         .         .         .         .       g.317069
 CGGAAGGAGTTGGAGAACAAGTTGAAGGAGCGGGAGGAATTCCTAATTCCCATTTACCAT       c.6540
 R  K  E  L  E  N  K  L  K  E  R  E  E  F  L  I  P  I  Y  H         p.2180

          .         .         .         .         .         .       g.317129
 CAGGTAGCCGTGCAGTTTGCTGACTTGCACGACACACCAGGCCGGATGCAGGAGAAGGGT       c.6600
 Q  V  A  V  Q  F  A  D  L  H  D  T  P  G  R  M  Q  E  K  G         p.2200

           | 54        .         .         .         .         .    g.317852
 GTTATTAGC | GATATCCTGGATTGGAAAACATCCCGTACCTTCTTCTACTGGCGGCTGAGG    c.6660
 V  I  S   | D  I  L  D  W  K  T  S  R  T  F  F  Y  W  R  L  R      p.2220

          .         .         .         .         .         .       g.317912
 CGTCTTCTGCTGGAGGACCTGGTCAAGAAGAAAATCCACAATGCCAACCCTGAGCTGACT       c.6720
 R  L  L  L  E  D  L  V  K  K  K  I  H  N  A  N  P  E  L  T         p.2240

          .         .         .         .         .         .       g.317972
 GATGGCCAGATTCAAGCCATGTTAAGGCGCTGGTTTGTGGAAGTGGAAGGAACAGTGAAG       c.6780
 D  G  Q  I  Q  A  M  L  R  R  W  F  V  E  V  E  G  T  V  K         p.2260

  | 55       .         .         .         .         .         .    g.325953
  | GCTTATGTTTGGGACAATAATAAGGATCTGGCGGAGTGGCTAGAGAAACAGCTGACAGAG    c.6840
  | A  Y  V  W  D  N  N  K  D  L  A  E  W  L  E  K  Q  L  T  E      p.2280

          .         .         .         .         .         .       g.326013
 GAGGATGGTGTTCACTCGGTAATAGAGGAAAACATCAAATGCATCAGCAGAGACTACGTC       c.6900
 E  D  G  V  H  S  V  I  E  E  N  I  K  C  I  S  R  D  Y  V         p.2300

          .        | 56.         .         .         .         .    g.327571
 CTCAAGCAAATCCGCAG | CTTGGTCCAGGCCAATCCAGAGGTTGCCATGGATTCCATCATC    c.6960
 L  K  Q  I  R  S  |  L  V  Q  A  N  P  E  V  A  M  D  S  I  I      p.2320

          .         .         .         .         .         .       g.327631
 CATATGACGCAGCACATATCACCCACTCAGCGAGCAGAAGTCATACGGATCCTCTCCACA       c.7020
 H  M  T  Q  H  I  S  P  T  Q  R  A  E  V  I  R  I  L  S  T         p.2340

          .         .                                               g.327652
 ATGGATTCCCCTTCCACGTAG                                              c.7041
 M  D  S  P  S  T  X                                                p.2346

          .         .         .         .         .         .       g.327712
 gaagagcttcctgcctgtccctgccctgtctctggagaaaagggctagagctgcctttta       c.*60

          .         .         .         .         .         .       g.327772
 caactgtaaccactgtaatgagaaggcacaggagacccagcactggagtcaaatggcatt       c.*120

          .         .         .         .         .         .       g.327832
 ttacttcctctcgtttcaggttatgcatgacatcctgggatgtaagatcacagaatcccc       c.*180

          .         .         .         .         .         .       g.327892
 ctccagcccaccagtcacacctaccccattcagtatttattaccctggccaggcctagtc       c.*240

          .         .         .         .         .         .       g.327952
 ctccactccctgcacaggactgagaaggcaatgaaaggtacaaacatgtaccatgaggtc       c.*300

          .         .         .         .         .         .       g.328012
 ttactaaccaaagtagggctgcccctcctgtcctgacagccccttggcctcccagcatgg       c.*360

          .         .         .         .         .         .       g.328072
 ggaagcgtgaggagttgcccagcagtgagcagcccccctcactcctggccccatgagccg       c.*420

          .         .         .         .         .         .       g.328132
 cagccacaggcagcagaggagggctaaggagaggaggaagcctcaagtccattgtttatt       c.*480

          .         .         .         .         .         .       g.328192
 accccgactcttagcccagcacacagtaggcactggagaggaatgattcccagtttaacc       c.*540

          .         .         .         .         .         .       g.328252
 acactacggtaccttttatgaagaaaaattagagcataaaatctactacaagctccatag       c.*600

          .         .         .         .         .         .       g.328312
 gaactcaaagatgagggcaaaactgtgagccaagaagcagagaaagaaaatagaaccagt       c.*660

          .         .         .         .         .         .       g.328372
 tattcttgatttaggggacctcaaccttgggttcagtctctgaggacaaagggaaaggta       c.*720

          .         .         .         .         .         .       g.328432
 gttgttggcctgcctctcgcctgcacgtcactgctggactagctgtcgcatgtggctggg       c.*780

          .         .         .         .         .         .       g.328492
 agctgcaaggccagtgcttgaggggccccagcagttccacaggtggtgaagcctgagttg       c.*840

          .         .         .         .         .         .       g.328552
 gcagaggaggagccagaagagaactgccctttctgcactggtggaaactagttatttatg       c.*900

          .         .         .         .         .         .       g.328612
 ccatgtggagagccagtgagatagatagatagtctgtttgttttgaggacttggaaagtt       c.*960

          .         .         .         .         .         .       g.328672
 gttcctatgaagcctggagcttggatggttttgagaggttaatggtgcctccacactcac       c.*1020

          .         .         .         .         .         .       g.328732
 tcttccctagttccaggattactgtcctagcagctaacggttctactctcttccccagag       c.*1080

          .         .         .         .         .         .       g.328792
 tgtagacaggcagcaggtctccccacagctctgaaaggaccctggtgacagctacaccct       c.*1140

          .         .         .         .         .         .       g.328852
 cagcaccaggagctggccttcctgatgagggaggcttccaggaaacacagaatccacatg       c.*1200

          .         .         .         .         .         .       g.328912
 accttaagattatttacaactcagtcatggtgctgctgtcctccaggcttactggcccct       c.*1260

          .         .         .         .         .         .       g.328972
 cctgactggcatcaggggcttcctcaggtggtggagagagtttactttcaacaactagtt       c.*1320

          .         .         .         .         .         .       g.329032
 tattcaagaaaagaacttactgattcctctgttcctaaagcaagagtggcaggtgatcag       c.*1380

          .         .         .         .         .         .       g.329092
 ggctggtgtagcatccggttcctttagtgcagctaactgcatttgtcactgatgaccaag       c.*1440

          .         .         .         .         .         .       g.329152
 gaggaaatcactaagacatttgagaagcagtggtatgaacgttcttggacaagccacagt       c.*1500

          .         .         .         .         .         .       g.329212
 tctgagccttaaccctgtagtttgcacacaagaacgagctccacctccccttcttcagga       c.*1560

          .         .         .         .         .         .       g.329272
 ggaatctgtgcggatagattggctggacttttcaatggttctgggttgcaggtgggcact       c.*1620

          .         .         .         .         .         .       g.329332
 gtatggctgggtatggagcggacagcccccaggagtcagagcctcagcccggctgccctg       c.*1680

          .         .         .         .         .         .       g.329392
 gtggaaggtacaggtgttcagcaccttcagaaaagggcataaagtggtgggggacaattc       c.*1740

          .         .         .         .         .         .       g.329452
 tcagtccaggaaaatgcattgaccattgctggctatttgcttacctagtaagaattggat       c.*1800

          .         .         .         .         .         .       g.329512
 tcatttttgaccagattattcttctatgcttttttgcaataaatcaaatcccacatatct       c.*1860

          .         .         .         .         .         .       g.329572
 acaagtggtatgaagtcctgcaccccccaggaggcctgtccaggcatgtcttcagaggca       c.*1920

          .         .         .         .         .         .       g.329632
 gggtgggttacactcatttacctcccctctccccaccaaattatgacacaaacgagtatg       c.*1980

          .         .         .         .         .         .       g.329692
 tttcctctctagaaccctgtaatgcctcctcccccatccccagagctccttactgtaggt       c.*2040

          .         .         .         .         .         .       g.329752
 cttaccctggacaaggattttttcaagttggaggcacagaacatgagcaatctgacattc       c.*2100

          .         .         .         .         .         .       g.329812
 ccacagcccctcaaacatgcaaggctactaaggcaggaggagtataaatgatggatattg       c.*2160

          .         .         .         .         .         .       g.329872
 accaagacctgcttggacggagaccgccatattatctgttctcttcgttcacaaaacagc       c.*2220

          .         .         .         .         .         .       g.329932
 cttcacttgtctcagaatttgatggacacatactgtgatgagcaggagcttcagatgcac       c.*2280

          .         .         .         .                           g.329976
 tctttacacattttgttgaaataaacctctacatttgtagaaga                       c.*2324

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Acetyl-CoA carboxylase alpha protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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