acyl-CoA dehydrogenase family, member 9 (ACAD9) - coding DNA reference sequence

(used for variant description)

(last modified September 23, 2024)


This file was created to facilitate the description of sequence variants on transcript NM_014049.4 in the ACAD9 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000003.11, covering ACAD9 transcript NM_014049.4.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                         .         .                g.5022
                                       aggtgcacgtgactaaggcctt       c.-181

 .         .         .         .         .         .                g.5082
 gggcgcggcaggtggtagccttcccgcccttctggcctctccatcccctgctgcggggga       c.-121

 .         .         .         .         .         .                g.5142
 ccgcgcaagcgcagtgagtactgcacgttgtcgcgggccagtaacgtcatcagacgtgtg       c.-61

 .         .         .         .         .         .                g.5202
 tgtgtccctgcggcgctaagaaggggagactgaggctgaggctggggaacatcgggcagc       c.-1

          .         .         .         .         .         .       g.5262
 ATGAGCGGCTGCGGGCTCTTCCTGCGCACCACGGCTGCGGCTCGTGCCTGCCGGGGTCTG       c.60
 M  S  G  C  G  L  F  L  R  T  T  A  A  A  R  A  C  R  G  L         p.20

          .         .         .         .         .         .       g.5322
 GTGGTCTCTACCGCGAACCGGCGGCTACTGCGCACCAGCCCGCCTGTACGAGCTTTCGCC       c.120
 V  V  S  T  A  N  R  R  L  L  R  T  S  P  P  V  R  A  F  A         p.40

          .         .         . | 02       .         .         .    g.10193
 AAAGAGCTTTTCCTAGGCAAAATCAAGAAG | AAAGAAGTTTTCCCATTTCCAGAAGTTAGC    c.180
 K  E  L  F  L  G  K  I  K  K   | K  E  V  F  P  F  P  E  V  S      p.60

          .         .         .         .         .         .       g.10253
 CAAGATGAACTTAATGAAATCAATCAGTTCTTGGGACCCGTGGAAAAATTCTTCACTGAA       c.240
 Q  D  E  L  N  E  I  N  Q  F  L  G  P  V  E  K  F  F  T  E         p.80

      | 03   .         .         .         .         .         .    g.19121
 GAGG | TGGACTCCCGAAAAATTGACCAGGAAGGGAAAATCCCAGATGAAACTTTGGAGAAA    c.300
 E  V |   D  S  R  K  I  D  Q  E  G  K  I  P  D  E  T  L  E  K      p.100

          .         .         .         .       | 04 .         .    g.20834
 TTGAAGAGCCTAGGGCTTTTTGGGCTGCAAGTCCCAGAAGAATATG | GTGGCCTGGGCTTC    c.360
 L  K  S  L  G  L  F  G  L  Q  V  P  E  E  Y  G |   G  L  G  F      p.120

          .         .         .         .         .         .       g.20894
 TCCAACACCATGTACTCAAGACTAGGGGAGATCATCAGCATGGATGGGTCCATCACTGTG       c.420
 S  N  T  M  Y  S  R  L  G  E  I  I  S  M  D  G  S  I  T  V         p.140

          .         .         .    | 05    .         .         .    g.21973
 ACCCTGGCAGCGCACCAGGCTATTGGCCTCAAG | GGGATCATCTTGGCTGGCACTGAGGAG    c.480
 T  L  A  A  H  Q  A  I  G  L  K   | G  I  I  L  A  G  T  E  E      p.160

          .         .         .         .         .         .       g.22033
 CAGAAAGCCAAATACTTGCCTAAACTGGCGTCCGGGGAGCACATTGCAGCCTTCTGCCTC       c.540
 Q  K  A  K  Y  L  P  K  L  A  S  G  E  H  I  A  A  F  C  L         p.180

          .     | 06   .         .         .         .         .    g.23188
 ACGGAGCCAGCCAG | TGGGAGCGATGCAGCCTCAATCCGGAGCAGAGCCACACTAAGTGAA    c.600
 T  E  P  A  S  |  G  S  D  A  A  S  I  R  S  R  A  T  L  S  E      p.200

          .         .         .    | 07    .         .         .    g.24824
 GACAAGAAGCACTACATCCTCAATGGCTCCAAG | GTCTGGATTACTAATGGAGGACTGGCC    c.660
 D  K  K  H  Y  I  L  N  G  S  K   | V  W  I  T  N  G  G  L  A      p.220

          .         .         .         .         .         .       g.24884
 AATATTTTTACTGTGTTTGCAAAGACTGAGGTCGTTGATTCTGATGGATCAGTGAAAGAC       c.720
 N  I  F  T  V  F  A  K  T  E  V  V  D  S  D  G  S  V  K  D         p.240

          .         .         .         .         .         .       g.24944
 AAAATCACAGCATTCATAGTAGAAAGAGACTTTGGTGGAGTCACTAATGGGAAACCCGAA       c.780
 K  I  T  A  F  I  V  E  R  D  F  G  G  V  T  N  G  K  P  E         p.260

          .         .         | 08         .         .         .    g.26818
 GATAAATTAGGCATTCGGGGCTCCAACA | CTTGTGAAGTCCATTTTGAAAACACCAAGATA    c.840
 D  K  L  G  I  R  G  S  N  T |   C  E  V  H  F  E  N  T  K  I      p.280

          .         .         .         .   | 09     .         .    g.28081
 CCTGTGGAAAACATCCTTGGAGAGGTCGGAGATGGGTTTAAG | GTGGCCATGAACATCCTC    c.900
 P  V  E  N  I  L  G  E  V  G  D  G  F  K   | V  A  M  N  I  L      p.300

          .         .         .         .         .         | 10    g.29574
 AACAGCGGCCGGTTCAGCATGGGCAGCGTCGTGGCTGGGCTGCTCAAGAGATTGATTG | AA    c.960
 N  S  G  R  F  S  M  G  S  V  V  A  G  L  L  K  R  L  I  E |       p.320

          .         .         .         .         .         .       g.29634
 ATGACTGCTGAGTACGCCTGCACAAGGAAACAGTTTAACAAGAGGCTCAGTGAATTTGGA       c.1020
 M  T  A  E  Y  A  C  T  R  K  Q  F  N  K  R  L  S  E  F  G         p.340

           | 11        .         .         .         .         .    g.29947
 TTGATTCAG | GAGAAATTTGCACTGATGGCTCAGAAGGCTTACGTCATGGAGAGTATGACC    c.1080
 L  I  Q   | E  K  F  A  L  M  A  Q  K  A  Y  V  M  E  S  M  T      p.360

          .         .         .         .         .         .       g.30007
 TACCTCACAGCAGGGATGCTGGACCAACCTGGCTTTCCCGACTGCTCCATCGAGGCAGCC       c.1140
 Y  L  T  A  G  M  L  D  Q  P  G  F  P  D  C  S  I  E  A  A         p.380

           | 12        .         .         .         .         .    g.31682
 ATGGTGAAG | GTGTTCAGCTCCGAGGCCGCCTGGCAGTGTGTGAGTGAGGCGCTGCAGATC    c.1200
 M  V  K   | V  F  S  S  E  A  A  W  Q  C  V  S  E  A  L  Q  I      p.400

          .         .         .         .         .         .       g.31742
 CTCGGGGGCTTGGGCTACACAAGGGACTATCCGTACGAGCGCATACTGCGTGACACCCGC       c.1260
 L  G  G  L  G  Y  T  R  D  Y  P  Y  E  R  I  L  R  D  T  R         p.420

          .         | 13         .         .         .         .    g.33737
 ATCCTCCTCATCTTCGAG | GGAACCAATGAGATTCTCCGGATGTACATCGCCCTGACGGGT    c.1320
 I  L  L  I  F  E   | G  T  N  E  I  L  R  M  Y  I  A  L  T  G      p.440

          .         .         .         | 14         .         .    g.34505
 CTGCAGCATGCCGGCCGCATCCTGACTACCAGGATCCA | TGAGCTTAAACAGGCCAAAGTG    c.1380
 L  Q  H  A  G  R  I  L  T  T  R  I  H  |  E  L  K  Q  A  K  V      p.460

          .         .         .         .         .         .       g.34565
 AGCACAGTCATGGATACCGTTGGCCGGAGGCTTCGGGACTCCCTGGGCCGAACTGTGGAC       c.1440
 S  T  V  M  D  T  V  G  R  R  L  R  D  S  L  G  R  T  V  D         p.480

          .         .         .         .      | 15  .         .    g.34869
 CTGGGGCTGACAGGCAACCATGGAGTTGTGCACCCCAGTCTTGCG | GACAGTGCCAACAAG    c.1500
 L  G  L  T  G  N  H  G  V  V  H  P  S  L  A   | D  S  A  N  K      p.500

          .         .         .         .         .         .       g.34929
 TTTGAGGAGAACACCTACTGCTTCGGCCGGACCGTGGAGACACTGCTGCTCCGCTTTGGC       c.1560
 F  E  E  N  T  Y  C  F  G  R  T  V  E  T  L  L  L  R  F  G         p.520

     | 16    .         .         .         .         .         .    g.35588
 AAG | ACCATCATGGAGGAGCAGCTGGTACTGAAGCGGGTGGCCAACATCCTCATCAACCTG    c.1620
 K   | T  I  M  E  E  Q  L  V  L  K  R  V  A  N  I  L  I  N  L      p.540

          .         .         .         .         .         .       g.35648
 TATGGCATGACGGCCGTGCTGTCGCGGGCCAGCCGCTCCATCCGCATTGGGCTCCGCAAC       c.1680
 Y  G  M  T  A  V  L  S  R  A  S  R  S  I  R  I  G  L  R  N         p.560

          .   | 17     .         .         .         .         .    g.36299
 CACGACCACGAG | GTTCTCTTGGCCAACACCTTCTGCGTGGAAGCTTACTTGCAGAATCTC    c.1740
 H  D  H  E   | V  L  L  A  N  T  F  C  V  E  A  Y  L  Q  N  L      p.580

          .         .      | 18  .         .         .         .    g.38052
 TTCAGCCTCTCTCAGCTGGACAAGT | ATGCTCCAGAAAACCTAGATGAGCAGATTAAGAAA    c.1800
 F  S  L  S  Q  L  D  K  Y |   A  P  E  N  L  D  E  Q  I  K  K      p.600

          .         .         .         .         .         .       g.38112
 GTGTCCCAGCAGATCCTTGAGAAGCGAGCCTATATCTGTGCCCACCCTCTGGACAGGACA       c.1860
 V  S  Q  Q  I  L  E  K  R  A  Y  I  C  A  H  P  L  D  R  T         p.620

                                                                    g.38118
 TGCTGA                                                             c.1866
 C  X                                                               p.621

          .         .         .         .         .         .       g.38178
 ggcaggggacagtgtcccctgctaccgcccgcccctacccatggcccgttgctggatgac       c.*60

          .         .         .         .         .         .       g.38238
 tgttactcttttttcagaaggtgttgggattatcacaggttaagccttttgttccccgtc       c.*120

          .         .         .         .         .         .       g.38298
 tgcacctgaagggttgtcgcctggcctgggagagcctcttccaggttttgacctgcaggc       c.*180

          .         .         .         .         .         .       g.38358
 agtgctctctaacaggaccatcacagcttctgaactgagccggagagagagaatggaatt       c.*240

          .         .         .         .         .         .       g.38418
 gctgacccctggaactggcgggtattctggtcattgaggagacaccatagtggaaactgg       c.*300

          .         .         .         .         .         .       g.38478
 ggcttatgctgctgcctccagggtgtgaggtgggtggggacctgtgtcaggtgtggatag       c.*360

          .         .         .         .         .         .       g.38538
 ccatttctgctcaaccacacattctctaagaaacagcttgaaagctctgtctgggtcatt       c.*420

          .         .         .         .         .         .       g.38598
 catttaaactagaagcagaggcacttaaaacatgtaccaggaaccatttaacaaagaata       c.*480

          .         .                                               g.38625
 taaaatgtcacaatctgtgtactgtta                                        c.*507

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Acyl-CoA dehydrogenase family, member 9 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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