amyloid beta (A4) precursor protein (APP) - coding DNA reference sequence

(used for variant description)

(last modified October 23, 2014)


This file was created to facilitate the description of sequence variants on transcript NM_000484.3 in the APP gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_007376.1, covering APP transcript NM_000484.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                         .         .                g.5014
                                         ggatcagctgactcgcctgg       c.-181

 .         .         .         .         .         .                g.5074
 ctctgagccccgccgccgcgctcgggctccgtcagtttcctcggcagcggtaggcgagag       c.-121

 .         .         .         .         .         .                g.5134
 cacgcggaggagcgtgcgcgggggccccgggagacggcggcggtggcggcgcgggcagag       c.-61

 .         .         .         .         .         .                g.5194
 caaggacgcggcggatcccactcgcacagcagcgcactcggtgccccgcgcagggtcgcg       c.-1

          .         .         .         .         .        | 02.    g.63672
 ATGCTGCCCGGTTTGGCACTGCTCCTGCTGGCCGCCTGGACGGCTCGGGCGCTGGAG | GTA    c.60
 M  L  P  G  L  A  L  L  L  L  A  A  W  T  A  R  A  L  E   | V      p.20

          .         .         .         .         .         .       g.63732
 CCCACTGATGGTAATGCTGGCCTGCTGGCTGAACCCCAGATTGCCATGTTCTGTGGCAGA       c.120
 P  T  D  G  N  A  G  L  L  A  E  P  Q  I  A  M  F  C  G  R         p.40

          .         .         .         .         .         .       g.63792
 CTGAACATGCACATGAATGTCCAGAATGGGAAGTGGGATTCAGATCCATCAGGGACCAAA       c.180
 L  N  M  H  M  N  V  Q  N  G  K  W  D  S  D  P  S  G  T  K         p.60

          .         .         .         .      | 03  .         .    g.85759
 ACCTGCATTGATACCAAGGAAGGCATCCTGCAGTATTGCCAAGAA | GTCTACCCTGAACTG    c.240
 T  C  I  D  T  K  E  G  I  L  Q  Y  C  Q  E   | V  Y  P  E  L      p.80

          .         .         .         .         .         .       g.85819
 CAGATCACCAATGTGGTAGAAGCCAACCAACCAGTGACCATCCAGAACTGGTGCAAGCGG       c.300
 Q  I  T  N  V  V  E  A  N  Q  P  V  T  I  Q  N  W  C  K  R         p.100

          .         .         .         .         .      | 04  .    g.122473
 GGCCGCAAGCAGTGCAAGACCCATCCCCACTTTGTGATTCCCTACCGCTGCTTAG | TTGGT    c.360
 G  R  K  Q  C  K  T  H  P  H  F  V  I  P  Y  R  C  L  V |   G      p.120

          .         .         .         .         .         .       g.122533
 GAGTTTGTAAGTGATGCCCTTCTCGTTCCTGACAAGTGCAAATTCTTACACCAGGAGAGG       c.420
 E  F  V  S  D  A  L  L  V  P  D  K  C  K  F  L  H  Q  E  R         p.140

          .         .         .         .         | 05         .    g.124635
 ATGGATGTTTGCGAAACTCATCTTCACTGGCACACCGTCGCCAAAGAG | ACATGCAGTGAG    c.480
 M  D  V  C  E  T  H  L  H  W  H  T  V  A  K  E   | T  C  S  E      p.160

          .         .         .         .         .         .       g.124695
 AAGAGTACCAACTTGCATGACTACGGCATGTTGCTGCCCTGCGGAATTGACAAGTTCCGA       c.540
 K  S  T  N  L  H  D  Y  G  M  L  L  P  C  G  I  D  K  F  R         p.180

          .         .         .         .         .         .       g.124755
 GGGGTAGAGTTTGTGTGTTGCCCACTGGCTGAAGAAAGTGACAATGTGGATTCTGCTGAT       c.600
 G  V  E  F  V  C  C  P  L  A  E  E  S  D  N  V  D  S  A  D         p.200

          .         .         .         .         .         .       g.124815
 GCGGAGGAGGATGACTCGGATGTCTGGTGGGGCGGAGCAGACACAGACTATGCAGATGGG       c.660
 A  E  E  D  D  S  D  V  W  W  G  G  A  D  T  D  Y  A  D  G         p.220

    | 06     .         .         .         .         .         .    g.153832
 AG | TGAAGACAAAGTAGTAGAAGTAGCAGAGGAGGAAGAAGTGGCTGAGGTGGAAGAAGAA    c.720
 S  |  E  D  K  V  V  E  V  A  E  E  E  E  V  A  E  V  E  E  E      p.240

          .         .         .         .         .         .       g.153892
 GAAGCCGATGATGACGAGGACGATGAGGATGGTGATGAGGTAGAGGAAGAGGCTGAGGAA       c.780
 E  A  D  D  D  E  D  D  E  D  G  D  E  V  E  E  E  A  E  E         p.260

          .         .         .         .         .         .       g.153952
 CCCTACGAAGAAGCCACAGAGAGAACCACCAGCATTGCCACCACCACCACCACCACCACA       c.840
 P  Y  E  E  A  T  E  R  T  T  S  I  A  T  T  T  T  T  T  T         p.280

          .         .      | 07  .         .         .         .    g.175670
 GAGTCTGTGGAAGAGGTGGTTCGAG | AGGTGTGCTCTGAACAAGCCGAGACGGGGCCGTGC    c.900
 E  S  V  E  E  V  V  R  E |   V  C  S  E  Q  A  E  T  G  P  C      p.300

          .         .         .         .         .         .       g.175730
 CGAGCAATGATCTCCCGCTGGTACTTTGATGTGACTGAAGGGAAGTGTGCCCCATTCTTT       c.960
 R  A  M  I  S  R  W  Y  F  D  V  T  E  G  K  C  A  P  F  F         p.320

          .         .         .         .         .         .       g.175790
 TACGGCGGATGTGGCGGCAACCGGAACAACTTTGACACAGAAGAGTACTGCATGGCCGTG       c.1020
 Y  G  G  C  G  G  N  R  N  N  F  D  T  E  E  Y  C  M  A  V         p.340

          .    | 08    .         .         .         .         .    g.178448
 TGTGGCAGCGCCA | TGTCCCAAAGTTTACTCAAGACTACCCAGGAACCTCTTGCCCGAGAT    c.1080
 C  G  S  A  M |   S  Q  S  L  L  K  T  T  Q  E  P  L  A  R  D      p.360

          . | 09       .         .         .         .         .    g.193392
 CCTGTTAAAC | TTCCTACAACAGCAGCCAGTACCCCTGATGCCGTTGACAAGTATCTCGAG    c.1140
 P  V  K  L |   P  T  T  A  A  S  T  P  D  A  V  D  K  Y  L  E      p.380

          .         .         .         .         .         .       g.193452
 ACACCTGGGGATGAGAATGAACATGCCCATTTCCAGAAAGCCAAAGAGAGGCTTGAGGCC       c.1200
 T  P  G  D  E  N  E  H  A  H  F  Q  K  A  K  E  R  L  E  A         p.400

          .         .     | 10   .         .         .         .    g.199827
 AAGCACCGAGAGAGAATGTCCCAG | GTCATGAGAGAATGGGAAGAGGCAGAACGTCAAGCA    c.1260
 K  H  R  E  R  M  S  Q   | V  M  R  E  W  E  E  A  E  R  Q  A      p.420

          .         .         .          | 11        .         .    g.200612
 AAGAACTTGCCTAAAGCTGATAAGAAGGCAGTTATCCAG | CATTTCCAGGAGAAAGTGGAA    c.1320
 K  N  L  P  K  A  D  K  K  A  V  I  Q   | H  F  Q  E  K  V  E      p.440

          .         .         .         .         .         .       g.200672
 TCTTTGGAACAGGAAGCAGCCAACGAGAGACAGCAGCTGGTGGAGACACACATGGCCAGA       c.1380
 S  L  E  Q  E  A  A  N  E  R  Q  Q  L  V  E  T  H  M  A  R         p.460

          .         .         .         .         .         .       g.200732
 GTGGAAGCCATGCTCAATGACCGCCGCCGCCTGGCCCTGGAGAACTACATCACCGCTCTG       c.1440
 V  E  A  M  L  N  D  R  R  R  L  A  L  E  N  Y  I  T  A  L         p.480

          .         | 12         .         .         .         .    g.220105
 CAGGCTGTTCCTCCTCGG | CCTCGTCACGTGTTCAATATGCTAAAGAAGTATGTCCGCGCA    c.1500
 Q  A  V  P  P  R   | P  R  H  V  F  N  M  L  K  K  Y  V  R  A      p.500

          .         .         .         .         .         .       g.220165
 GAACAGAAGGACAGACAGCACACCCTAAAGCATTTCGAGCATGTGCGCATGGTGGATCCC       c.1560
 E  Q  K  D  R  Q  H  T  L  K  H  F  E  H  V  R  M  V  D  P         p.520

          .         .        | 13.         .         .         .    g.221162
 AAGAAAGCCGCTCAGATCCGGTCCCAG | GTTATGACACACCTCCGTGTGATTTATGAGCGC    c.1620
 K  K  A  A  Q  I  R  S  Q   | V  M  T  H  L  R  V  I  Y  E  R      p.540

          .         .         .         .         .         .       g.221222
 ATGAATCAGTCTCTCTCCCTGCTCTACAACGTGCCTGCAGTGGCCGAGGAGATTCAGGAT       c.1680
 M  N  Q  S  L  S  L  L  Y  N  V  P  A  V  A  E  E  I  Q  D         p.560

         | 14.         .         .         .         .         .    g.263911
 GAAGTTG | ATGAGCTGCTTCAGAAAGAGCAAAACTATTCAGATGACGTCTTGGCCAACATG    c.1740
 E  V  D |   E  L  L  Q  K  E  Q  N  Y  S  D  D  V  L  A  N  M      p.580

          .         .         .         .         .         .       g.263971
 ATTAGTGAACCAAGGATCAGTTACGGAAACGATGCTCTCATGCCATCTTTGACCGAAACG       c.1800
 I  S  E  P  R  I  S  Y  G  N  D  A  L  M  P  S  L  T  E  T         p.600

          .         .         .         .         .         .       g.264031
 AAAACCACCGTGGAGCTCCTTCCCGTGAATGGAGAGTTCAGCCTGGACGATCTCCAGCCG       c.1860
 K  T  T  V  E  L  L  P  V  N  G  E  F  S  L  D  D  L  Q  P         p.620

          .         .         .         .          | 15        .    g.270754
 TGGCATTCTTTTGGGGCTGACTCTGTGCCAGCCAACACAGAAAACGAAG | TTGAGCCTGTT    c.1920
 W  H  S  F  G  A  D  S  V  P  A  N  T  E  N  E  V |   E  P  V      p.640

          .         .         .         .    | 16    .         .    g.278164
 GATGCCCGCCCTGCTGCCGACCGAGGACTGACCACTCGACCAG | GTTCTGGGTTGACAAAT    c.1980
 D  A  R  P  A  A  D  R  G  L  T  T  R  P  G |   S  G  L  T  N      p.660

          .         .         .         .         .         .       g.278224
 ATCAAGACGGAGGAGATCTCTGAAGTGAAGATGGATGCAGAATTCCGACATGACTCAGGA       c.2040
 I  K  T  E  E  I  S  E  V  K  M  D  A  E  F  R  H  D  S  G         p.680

          .         .     | 17   .         .         .         .    g.283988
 TATGAAGTTCATCATCAAAAATTG | GTGTTCTTTGCAGAAGATGTGGGTTCAAACAAAGGT    c.2100
 Y  E  V  H  H  Q  K  L   | V  F  F  A  E  D  V  G  S  N  K  G      p.700

          .         .         .         .         .         .       g.284048
 GCAATCATTGGACTCATGGTGGGCGGTGTTGTCATAGCGACAGTGATCGTCATCACCTTG       c.2160
 A  I  I  G  L  M  V  G  G  V  V  I  A  T  V  I  V  I  T  L         p.720

          .         .         .         .         .  | 18      .    g.294059
 GTGATGCTGAAGAAGAAACAGTACACATCCATTCATCATGGTGTGGTGGAG | GTTGACGCC    c.2220
 V  M  L  K  K  K  Q  Y  T  S  I  H  H  G  V  V  E   | V  D  A      p.740

          .         .         .         .         .         .       g.294119
 GCTGTCACCCCAGAGGAGCGCCACCTGTCCAAGATGCAGCAGAACGGCTACGAAAATCCA       c.2280
 A  V  T  P  E  E  R  H  L  S  K  M  Q  Q  N  G  Y  E  N  P         p.760

          .         .         .                                     g.294152
 ACCTACAAGTTCTTTGAGCAGATGCAGAACTAG                                  c.2313
 T  Y  K  F  F  E  Q  M  Q  N  X                                    p.770

          .         .         .         .         .         .       g.294212
 acccccgccacagcagcctctgaagttggacagcaaaaccattgcttcactacccatcgg       c.*60

          .         .         .         .         .         .       g.294272
 tgtccatttatagaataatgtgggaagaaacaaacccgttttatgatttactcattatcg       c.*120

          .         .         .         .         .         .       g.294332
 ccttttgacagctgtgctgtaacacaagtagatgcctgaacttgaattaatccacacatc       c.*180

          .         .         .         .         .         .       g.294392
 agtaatgtattctatctctctttacattttggtctctatactacattattaatgggtttt       c.*240

          .         .         .         .         .         .       g.294452
 gtgtactgtaaagaatttagctgtatcaaactagtgcatgaatagattctctcctgatta       c.*300

          .         .         .         .         .         .       g.294512
 tttatcacatagccccttagccagttgtatattattcttgtggtttgtgacccaattaag       c.*360

          .         .         .         .         .         .       g.294572
 tcctactttacatatgctttaagaatcgatgggggatgcttcatgtgaacgtgggagttc       c.*420

          .         .         .         .         .         .       g.294632
 agctgcttctcttgcctaagtattcctttcctgatcactatgcattttaaagttaaacat       c.*480

          .         .         .         .         .         .       g.294692
 ttttaagtatttcagatgctttagagagattttttttccatgactgcattttactgtaca       c.*540

          .         .         .         .         .         .       g.294752
 gattgctgcttctgctatatttgtgatataggaattaagaggatacacacgtttgtttct       c.*600

          .         .         .         .         .         .       g.294812
 tcgtgcctgttttatgtgcacacattaggcattgagacttcaagcttttctttttttgtc       c.*660

          .         .         .         .         .         .       g.294872
 cacgtatctttgggtctttgataaagaaaagaatccctgttcattgtaagcacttttacg       c.*720

          .         .         .         .         .         .       g.294932
 gggcgggtggggaggggtgctctgctggtcttcaattaccaagaattctccaaaacaatt       c.*780

          .         .         .         .         .         .       g.294992
 ttctgcaggatgattgtacagaatcattgcttatgacatgatcgctttctacactgtatt       c.*840

          .         .         .         .         .         .       g.295052
 acataaataaattaaataaaataaccccgggcaagacttttctttgaaggatgactacag       c.*900

          .         .         .         .         .         .       g.295112
 acattaaataatcgaagtaattttgggtggggagaagaggcagattcaattttctttaac       c.*960

          .         .         .         .         .         .       g.295172
 cagtctgaagtttcatttatgatacaaaagaagatgaaaatggaagtggcaatataaggg       c.*1020

          .         .         .         .         .         .       g.295232
 gatgaggaaggcatgcctggacaaacccttcttttaagatgtgtcttcaatttgtataaa       c.*1080

          .         .         .         .                           g.295272
 atggtgttttcatgtaaataaatacattcttggaggagca                           c.*1120

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Amyloid beta (A4) precursor protein protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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