ATPase family, AAA domain containing 3A (ATAD3A) - coding DNA reference sequence

(used for variant description)

(last modified August 15, 2018)


This file was created to facilitate the description of sequence variants on transcript NM_018188.3 in the ATAD3A gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_053035.1, covering ATAD3A transcript NM_018188.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                                    g.5006
                                                       gtgtgt       c.-121

 .         .         .         .         .         .                g.5066
 gtggcgcctgcgcagtggcggtgaccaccggctcgcggcgcgtggaggctgctcccagcc       c.-61

 .         .         .         .         .         .                g.5126
 gcgcgcgagtcagactcgggtgggggtcccggcggcggtagcggcggcggcggtgcgagc       c.-1

          .         .         .         .         .         .       g.5186
 ATGTCGTGGCTCTTCGGCATTAACAAGGGCCCCAAGGGTGAAGGCGCGGGGCCGCCGCCG       c.60
 M  S  W  L  F  G  I  N  K  G  P  K  G  E  G  A  G  P  P  P         p.20

          .         .         .         .         .         .       g.5246
 CCTTTGCCGCCCGCGCAGCCCGGGGCCGAGGGCGGCGGGGACCGCGGGTTGGGAGACCGG       c.120
 P  L  P  P  A  Q  P  G  A  E  G  G  G  D  R  G  L  G  D  R         p.40

          .         .         .         .         .         .       g.5306
 CCGGCGCCCAAGGACAAATGGAGCAACTTCGACCCCACCGGCCTGGAGCGCGCCGCCAAG       c.180
 P  A  P  K  D  K  W  S  N  F  D  P  T  G  L  E  R  A  A  K         p.60

          .         .      | 02  .         .         .         .    g.8904
 GCGGCGCGCGAGCTGGAGCACTCGC | GTTATGCCAAGGACGCCCTGAATCTGGCACAGATG    c.240
 A  A  R  E  L  E  H  S  R |   Y  A  K  D  A  L  N  L  A  Q  M      p.80

          .         .         .         .   | 03     .         .    g.10042
 CAGGAGCAGACGCTGCAGTTGGAGCAACAGTCCAAGCTCAAA | ATGCGGCTGGAAGCCCTG    c.300
 Q  E  Q  T  L  Q  L  E  Q  Q  S  K  L  K   | M  R  L  E  A  L      p.100

          .         .         .         .         .         .       g.10102
 AGCCTGCTGCACACACTAGTCTGGGCATGGAGTCTCTGCCGTGCCGGAGCCGTGCAGACA       c.360
 S  L  L  H  T  L  V  W  A  W  S  L  C  R  A  G  A  V  Q  T         p.120

          .         .         .         .         .         .       g.10162
 CAGGAGCGGCTGTCAGGCAGTGCCAGCCCTGAGCAAGTGCCAGCTGGTGAGTGCTGTGCT       c.420
 Q  E  R  L  S  G  S  A  S  P  E  Q  V  P  A  G  E  C  C  A         p.140

          .         .         .         .         .         .       g.10222
 CTGCAGGAGTATGAGGCCGCCGTGGAGCAGCTCAAGAGCGAGCAGATCCGGGCGCAGGCT       c.480
 L  Q  E  Y  E  A  A  V  E  Q  L  K  S  E  Q  I  R  A  Q  A         p.160

          .         .         .         .         | 04         .    g.10585
 GAGGAGAGGAGGAAGACCCTGAGCGAGGAGACCCGGCAGCACCAGGCC | AGGGCCCAGTAT    c.540
 E  E  R  R  K  T  L  S  E  E  T  R  Q  H  Q  A   | R  A  Q  Y      p.180

          .         .         .         .         | 05         .    g.11790
 CAAGACAAGCTGGCCCGGCAGCGCTACGAGGACCAACTGAAGCAGCAG | CAACTTCTCAAT    c.600
 Q  D  K  L  A  R  Q  R  Y  E  D  Q  L  K  Q  Q   | Q  L  L  N      p.200

          .         .         .         .         .         | 06    g.13000
 GAGGAGAATTTACGGAAGCAGGAGGAGTCCGTGCAGAAGCAGGAAGCCATGCGGCGAG | CC    c.660
 E  E  N  L  R  K  Q  E  E  S  V  Q  K  Q  E  A  M  R  R  A |       p.220

          .         .         .         .         .         .       g.13060
 ACCGTGGAGCGGGAGATGGAGCTGCGGCACAAGAATGAGATGCTGCGAGTGGAGGCCGAG       c.720
 T  V  E  R  E  M  E  L  R  H  K  N  E  M  L  R  V  E  A  E         p.240

          .         .         .         .         .         .       g.13120
 GCCCGGGCGCGCGCCAAGGCCGAGCGGGAGAATGCAGACATCATCCGCGAGCAGATCCGC       c.780
 A  R  A  R  A  K  A  E  R  E  N  A  D  I  I  R  E  Q  I  R         p.260

          .         .         .         .     | 07   .         .    g.13421
 CTGAAGGCGGCCGAGCACCGTCAGACCGTCTTGGAGTCCATCAG | GACGGCTGGCACCTTG    c.840
 L  K  A  A  E  H  R  Q  T  V  L  E  S  I  R  |  T  A  G  T  L      p.280

          .         .         .         .         .     | 08   .    g.15607
 TTTGGGGAAGGATTCCGTGCCTTTGTGACAGACTGGGACAAAGTGACAGCCACG | GTGGCT    c.900
 F  G  E  G  F  R  A  F  V  T  D  W  D  K  V  T  A  T   | V  A      p.300

          .         .         .         .         .         .       g.15667
 GGGCTGACGCTGCTGGCTGTTGGGGTCTACTCAGCCAAGAATGCCACGCTTGTCGCCGGC       c.960
 G  L  T  L  L  A  V  G  V  Y  S  A  K  N  A  T  L  V  A  G         p.320

          .         .         .         .         .         .       g.15727
 CGCTTCATCGAGGCTCGGCTGGGGAAGCCGTCCCTAGTGAGGGAGACGTCCCGCATCACG       c.1020
 R  F  I  E  A  R  L  G  K  P  S  L  V  R  E  T  S  R  I  T         p.340

          .         .         . | 09       .         .         .    g.16398
 GTGCTTGAGGCGCTGCGGCACCCCATCCAG | GTCAGCCGGCGGCTCCTCAGTCGACCCCAG    c.1080
 V  L  E  A  L  R  H  P  I  Q   | V  S  R  R  L  L  S  R  P  Q      p.360

          .         .        | 10.         .         .         .    g.16729
 GACGCGCTGGAGGGTGTTGTGCTCAGT | CCCAGCCTGGAAGCACGGGTGCGCGACATCGCC    c.1140
 D  A  L  E  G  V  V  L  S   | P  S  L  E  A  R  V  R  D  I  A      p.380

          .         .         .         .         .         .       g.16789
 ATAGCAACAAGGAACACCAAGAAGAACCGCAGCCTGTACAGGAACATCCTGATGTACGGG       c.1200
 I  A  T  R  N  T  K  K  N  R  S  L  Y  R  N  I  L  M  Y  G         p.400

          .         .         .    | 11    .         .         .    g.17157
 CCACCAGGCACCGGGAAGACGCTGTTTGCCAAG | AAACTCGCCCTGCACTCAGGCATGGAC    c.1260
 P  P  G  T  G  K  T  L  F  A  K   | K  L  A  L  H  S  G  M  D      p.420

          .         .         .         .         .         .       g.17217
 TACGCCATCATGACAGGCGGGGACGTGGCCCCCATGGGGCGGGAAGGCGTGACCGCCATG       c.1320
 Y  A  I  M  T  G  G  D  V  A  P  M  G  R  E  G  V  T  A  M         p.440

          .         .         .         | 12         .         .    g.18119
 CACAAGCTCTTTGACTGGGCCAATACCAGCCGGCGCGG | CCTCCTGCTCTTTGTGGATGAA    c.1380
 H  K  L  F  D  W  A  N  T  S  R  R  G  |  L  L  L  F  V  D  E      p.460

          .         .         . | 13       .         .         .    g.19348
 GCGGACGCCTTCCTTCGGAAGCGAGCCACC | GAGAAGATAAGCGAGGACCTCAGGGCCACA    c.1440
 A  D  A  F  L  R  K  R  A  T   | E  K  I  S  E  D  L  R  A  T      p.480

          .         .         .         .  | 14      .         .    g.20571
 CTGAACGCCTTCCTGTACCGCACGGGCCAGCACAGCAACAA | GTTCATGCTGGTCCTGGCC    c.1500
 L  N  A  F  L  Y  R  T  G  Q  H  S  N  K  |  F  M  L  V  L  A      p.500

          .         .         .         .         .         .       g.20631
 AGCAACCAACCAGAGCAGTTCGACTGGGCCATCAATGACCGCATCAATGAGATGGTCCAC       c.1560
 S  N  Q  P  E  Q  F  D  W  A  I  N  D  R  I  N  E  M  V  H         p.520

          .         .         .         .         .         .       g.20691
 TTCGACCTGCCAGGGCAGGAGGAACGGGAGCGCCTGGTGAGAATGTATTTTGACAAGTAT       c.1620
 F  D  L  P  G  Q  E  E  R  E  R  L  V  R  M  Y  F  D  K  Y         p.540

          .         .          | 15        .         .         .    g.22111
 GTTCTTAAGCCGGCCACAGAAGGAAAGCA | GCGCCTGAAGCTGGCCCAGTTTGACTACGGG    c.1680
 V  L  K  P  A  T  E  G  K  Q  |  R  L  K  L  A  Q  F  D  Y  G      p.560

          .         .         .         .         .         .       g.22171
 AGGAAGTGCTCGGAGGTCGCTCGGCTGACGGAGGGCATGTCGGGCCGGGAGATCGCTCAG       c.1740
 R  K  C  S  E  V  A  R  L  T  E  G  M  S  G  R  E  I  A  Q         p.580

          .         | 16         .         .         .         .    g.26825
 CTGGCCGTGTCCTGGCAG | GCCACGGCGTATGCCTCCGAGGACGGGGTCCTGACCGAGGCC    c.1800
 L  A  V  S  W  Q   | A  T  A  Y  A  S  E  D  G  V  L  T  E  A      p.600

          .         .         .         .         .         .       g.26885
 ATGATGGACACCCGCGTGCAAGATGCTGTCCAGCAGCACCAGCAGAAGATGTGCTGGCTG       c.1860
 M  M  D  T  R  V  Q  D  A  V  Q  Q  H  Q  Q  K  M  C  W  L         p.620

          .         .         .         .                           g.26930
 AAGGCGGAAGGGCCTGGGCGTGGGGACGAGCCCTCCCCATCCTGA                      c.1905
 K  A  E  G  P  G  R  G  D  E  P  S  P  S  X                        p.634

          .         .         .         .         .         .       g.26990
 gtccacagggagatccacagctcacggagcctggccgcggacccctcccacccctgcctt       c.*60

          .         .         .         .         .         .       g.27050
 gccggcccctgcacatttaggatatgctcctgggtggggactgggctgtgcccagggcct       c.*120

          .         .         .         .         .         .       g.27110
 ctgtcccccaggatgtcttgtggtgcgggtcggccgttctgccccccagggcaccccctg       c.*180

          .         .         .         .         .         .       g.27170
 ttgtaggcactggctagggaggggcaggcctccttcctgcccctcgagacactcttggga       c.*240

          .         .         .         .         .         .       g.27230
 gatgcattttccgtctggctcacagggggagggtgaggctttgcaccccagcccctgccc       c.*300

          .         .         .         .         .         .       g.27290
 aggccactgtgagggtgggtgctggctgagcccccggggcagcaggagccaggcaggtga       c.*360

          .         .         .         .         .         .       g.27350
 tgtctttgttctcggctcccacagcagagccaggtgagggggcgcctgccagggccagac       c.*420

          .         .         .         .         .         .       g.27410
 ccaggtggggcagcctgaaccctgcttccccctgtggccggcatgccccgatctttcaca       c.*480

          .         .         .         .         .         .       g.27470
 cactggtgaccctgagagaggagggaggagggaacctggcgggggtgtctgaggccgcac       c.*540

          .         .         .         .         .         .       g.27530
 tgtcagctggccggtccaagcctgtggctggagctggggtctgtttacctaataaagtcc       c.*600

          .                                                         g.27545
 cacaggtgcctcatt                                                    c.*615

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The ATPase family, AAA domain containing 3A protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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