UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 4 (B3GNT4) - coding DNA reference sequence

(used for variant description)

(last modified October 5, 2019)


This file was created to facilitate the description of sequence variants on transcript NM_030765.2 in the B3GNT4 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000012.11, covering B3GNT4 transcript NM_030765.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                               .         .         .                g.5038
                       attcccacctcctccagaagccccgcccactcccgagc       c.-181

 .         .         .         .         .         .                g.5098
 cccgagagctccgcgcacctgggcgccatccgccctggctccgctgcacgagctccacgc       c.-121

 .         .         .   | 02     .         .         .             g.5878
 ccgtaccccggcgtcacgctcag | cccgcggtgctcgcacacctgagactcatctcgcttc    c.-61

 .         .         .         .         .         .                g.5938
 gaccccgccgccgccgccgcccggcatcctgagcacggagacagtctccagctgccgttc       c.-1

          .         .         .         .         .         .       g.5998
 ATGCTTCCTCCCCAGCCTTCCGCAGCCCACCAGGGAAGGGGCGGTAGGAGTGGCCTTTTA       c.60
 M  L  P  P  Q  P  S  A  A  H  Q  G  R  G  G  R  S  G  L  L         p.20

        | 03 .         .         .         .         .         .    g.7691
 CCAAAG | GGACCGGCGATGCTCTGCAGGCTGTGCTGGCTGGTCTCGTACAGCTTGGCTGTG    c.120
 P  K   | G  P  A  M  L  C  R  L  C  W  L  V  S  Y  S  L  A  V      p.40

          .         .         .         .         .         .       g.7751
 CTGTTGCTCGGCTGCCTGCTCTTCCTGAGGAAGGCGGCCAAGCCCGCAGGAGACCCCACG       c.180
 L  L  L  G  C  L  L  F  L  R  K  A  A  K  P  A  G  D  P  T         p.60

          .         .         .         .         .         .       g.7811
 GCCCACCAGCCTTTCTGGGCTCCCCCAACACCCCGTCACAGCCGGTGTCCACCCAACCAC       c.240
 A  H  Q  P  F  W  A  P  P  T  P  R  H  S  R  C  P  P  N  H         p.80

          .         .         .         .         .         .       g.7871
 ACAGTGTCTAGCGCCTCTCTGTCCCTGCCTAGCCGTCACCGTCTCTTCTTGACCTATCGT       c.300
 T  V  S  S  A  S  L  S  L  P  S  R  H  R  L  F  L  T  Y  R         p.100

          .         .         .         .         .         .       g.7931
 CACTGCCGAAATTTCTCTATCTTGCTGGAGCCTTCAGGCTGTTCCAAGGATACCTTCTTG       c.360
 H  C  R  N  F  S  I  L  L  E  P  S  G  C  S  K  D  T  F  L         p.120

          .         .         .         .         .         .       g.7991
 CTCCTGGCCATCAAGTCACAGCCTGGTCACGTGGAGCGACGTGCGGCTATCCGCAGCACG       c.420
 L  L  A  I  K  S  Q  P  G  H  V  E  R  R  A  A  I  R  S  T         p.140

          .         .         .         .         .         .       g.8051
 TGGGGCAGGGTGGGGGGATGGGCTAGGGGCCGGCAGCTGAAGCTGGTGTTCCTCCTAGGG       c.480
 W  G  R  V  G  G  W  A  R  G  R  Q  L  K  L  V  F  L  L  G         p.160

          .         .         .         .         .         .       g.8111
 GTGGCAGGATCCGCTCCCCCAGCCCAGCTGCTGGCCTATGAGAGTAGGGAGTTTGATGAC       c.540
 V  A  G  S  A  P  P  A  Q  L  L  A  Y  E  S  R  E  F  D  D         p.180

          .         .         .         .         .         .       g.8171
 ATCCTCCAGTGGGACTTCACTGAGGACTTCTTCAACCTGACGCTCAAGGAGCTGCACCTG       c.600
 I  L  Q  W  D  F  T  E  D  F  F  N  L  T  L  K  E  L  H  L         p.200

          .         .         .         .         .         .       g.8231
 CAGCGCTGGGTGGTGGCTGCCTGCCCCCAGGCCCATTTCATGCTAAAGGGAGATGACGAT       c.660
 Q  R  W  V  V  A  A  C  P  Q  A  H  F  M  L  K  G  D  D  D         p.220

          .         .         .         .         .         .       g.8291
 GTCTTTGTCCACGTCCCCAACGTGTTAGAGTTCCTGGATGGCTGGGACCCAGCCCAGGAC       c.720
 V  F  V  H  V  P  N  V  L  E  F  L  D  G  W  D  P  A  Q  D         p.240

          .         .         .         .         .         .       g.8351
 CTCCTGGTGGGAGATGTCATCCGCCAAGCCCTGCCCAACAGGAACACTAAGGTCAAATAC       c.780
 L  L  V  G  D  V  I  R  Q  A  L  P  N  R  N  T  K  V  K  Y         p.260

          .         .         .         .         .         .       g.8411
 TTCATCCCACCCTCAATGTACAGGGCCACCCACTACCCACCCTATGCTGGTGGGGGAGGA       c.840
 F  I  P  P  S  M  Y  R  A  T  H  Y  P  P  Y  A  G  G  G  G         p.280

          .         .         .         .         .         .       g.8471
 TATGTCATGTCCAGAGCCACAGTGCGGCGCCTCCAGGCTATCATGGAAGATGCTGAACTC       c.900
 Y  V  M  S  R  A  T  V  R  R  L  Q  A  I  M  E  D  A  E  L         p.300

          .         .         .         .         .         .       g.8531
 TTCCCCATTGATGATGTCTTTGTGGGTATGTGCCTGAGGCGGCTGGGGCTGAGCCCTATG       c.960
 F  P  I  D  D  V  F  V  G  M  C  L  R  R  L  G  L  S  P  M         p.320

          .         .         .         .         .         .       g.8591
 CACCATGCTGGCTTCAAGACATTTGGAATCCGGCGGCCCCTGGACCCCTTAGACCCCTGC       c.1020
 H  H  A  G  F  K  T  F  G  I  R  R  P  L  D  P  L  D  P  C         p.340

          .         .         .         .         .         .       g.8651
 CTGTATAGGGGGCTCCTGCTGGTTCACCGCCTCAGCCCCCTCGAGATGTGGACCATGTGG       c.1080
 L  Y  R  G  L  L  L  V  H  R  L  S  P  L  E  M  W  T  M  W         p.360

          .         .         .         .         .                 g.8708
 GCACTGGTGACAGATGAGGGGCTCAAGTGTGCAGCTGGCCCCATACCCCAGCGCTGA          c.1137
 A  L  V  T  D  E  G  L  K  C  A  A  G  P  I  P  Q  R  X            p.378

          .         .         .         .         .         .       g.8768
 agggtgggttgggcaacagcctgagagtggactcagtgttgattctctatcgtgatgcga       c.*60

          .         .         .         .         .         .       g.8828
 aattgatgcctgctgctctacagaaaatgccaacttggttttttaactcctctcaccctg       c.*120

          .         .                                               g.8857
 ttagctctgattaaaaacactgcaaccca                                      c.*149

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 4 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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