beaded filament structural protein 2, phakinin (BFSP2) - coding DNA reference sequence

(used for variant description)

(last modified November 11, 2023)


This file was created to facilitate the description of sequence variants on transcript NM_003571.2 in the BFSP2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000003.11, covering BFSP2 transcript NM_003571.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                   .                g.5018
                                           agacagcagacaaagcag       c.-121

 .         .         .         .         .         .                g.5078
 ccccagggataggggagattccagagaggcccgtgaccaggccacagggatgctggggct       c.-61

 .         .         .         .         .         .                g.5138
 gtaaaccaaaagccactggactctgtaaacccactgggcaccacagaggcagaaggggtg       c.-1

          .         .         .         .         .         .       g.5198
 ATGAGTGAGAGGCGAGTGGTAGTGGACTTGCCCACCAGTGCCAGCTCCAGCATGCCCCTC       c.60
 M  S  E  R  R  V  V  V  D  L  P  T  S  A  S  S  S  M  P  L         p.20

          .         .         .         .         .         .       g.5258
 CAGAGGCGCAGGGCGTCCTTCAGGGGGCCACGGTCATCATCCTCCCTGGAGAGCCCCCCA       c.120
 Q  R  R  R  A  S  F  R  G  P  R  S  S  S  S  L  E  S  P  P         p.40

          .         .         .         .         .         .       g.5318
 GCCTCCAGGACCAATGCCATGAGTGGCCTTGTCCGAGCACCCGGGGTCTATGTAGGAACA       c.180
 A  S  R  T  N  A  M  S  G  L  V  R  A  P  G  V  Y  V  G  T         p.60

          .         .         .         .         .         .       g.5378
 GCACCCAGTGGGTGCATAGGTGGCTTGGGTGCCCGTGTGACCCGCCGGGCCCTCGGCATC       c.240
 A  P  S  G  C  I  G  G  L  G  A  R  V  T  R  R  A  L  G  I         p.80

          .         .         .         .         .         .       g.5438
 AGCAGTGTCTTCCTTCAGGGCCTGCGGAGCTCAGGCCTGGCCACCGTGCCGGCTCCAGGT       c.300
 S  S  V  F  L  Q  G  L  R  S  S  G  L  A  T  V  P  A  P  G         p.100

          .         .         .         .         .         .       g.5498
 TTGGAGAGGGACCATGGTGCTGTTGAGGACCTAGGGGGCTGCCTGGTGGAATATATGGCC       c.360
 L  E  R  D  H  G  A  V  E  D  L  G  G  C  L  V  E  Y  M  A         p.120

          .         .         .         .         .         .       g.5558
 AAAGTGCACGCCCTTGAGCAAGTCAGTCAGGAGCTGGAAACACAACTGCGGATGCACCTG       c.420
 K  V  H  A  L  E  Q  V  S  Q  E  L  E  T  Q  L  R  M  H  L         p.140

          .         .         .         .         .         .       g.5618
 GAGAGCAAAGCCACACGCTCGGGAAACTGGGGTGCCCTACGGGCTTCCTGGGCCAGCAGC       c.480
 E  S  K  A  T  R  S  G  N  W  G  A  L  R  A  S  W  A  S  S         p.160

           | 02        .         .         .         .         .    g.52422
 TGCCAGCAG | GTGGGTGAGGCAGTCTTGGAAAATGCCCGGCTCATGCTGCAGACAGAAACT    c.540
 C  Q  Q   | V  G  E  A  V  L  E  N  A  R  L  M  L  Q  T  E  T      p.180

          .         .         .   | 03     .         .         .    g.53571
 ATCCAGGCCGGAGCAGATGACTTTAAAGAGAG | ATATGAAAATGAGCAGCCATTTCGAAAG    c.600
 I  Q  A  G  A  D  D  F  K  E  R  |  Y  E  N  E  Q  P  F  R  K      p.200

          .         .         .         .         .         .       g.53631
 GCGGCAGAAGAGGAAATTAACTCTCTGTATAAAGTCATTGATGAGGCTAATTTGACTAAA       c.660
 A  A  E  E  E  I  N  S  L  Y  K  V  I  D  E  A  N  L  T  K         p.220

          .         .         .         .         .         .       g.53691
 ATGGACCTGGAGAGTCAAATAGAAAGTCTGAAAGAAGAACTTGGCTCTCTATCAAGAAAC       c.720
 M  D  L  E  S  Q  I  E  S  L  K  E  E  L  G  S  L  S  R  N         p.240

           | 04        .         .         .         .         .    g.55408
 TATGAAGAG | GATGTGAAGCTGCTGCACAAACAGTTGGCAGGGTGTGAGCTGGAACAAATG    c.780
 Y  E  E   | D  V  K  L  L  H  K  Q  L  A  G  C  E  L  E  Q  M      p.260

          .         .         .         .         .         .       g.55468
 GATGCTCCCATTGGCACTGGTCTGGACGACATCCTTGAGACGATCAGAATTCAGTGGGAG       c.840
 D  A  P  I  G  T  G  L  D  D  I  L  E  T  I  R  I  Q  W  E         p.280

          .         .         .         .         .  | 05      .    g.71891
 AGAGATGTTGAAAAGAACCGGGTGGAGGCAGGAGCCCTGCTCCAAGCTAAG | CAACAGGCG    c.900
 R  D  V  E  K  N  R  V  E  A  G  A  L  L  Q  A  K   | Q  Q  A      p.300

          .         .         .         .         .         .       g.71951
 GAGGTGGCCCACATGTCCCAGACCCAGGAGGAGAAGCTGGCAGCTGCCCTCAGGGTGGAG       c.960
 E  V  A  H  M  S  Q  T  Q  E  E  K  L  A  A  A  L  R  V  E         p.320

          .         .         .         .         .         .       g.72011
 TTACACAACACTTCGTGCCAAGTCCAGAGCCTCCAGGCTGAGACAGAATCCTTACGTGCC       c.1020
 L  H  N  T  S  C  Q  V  Q  S  L  Q  A  E  T  E  S  L  R  A         p.340

     | 06    .         .         .         .         .         .    g.77456
 CTG | AAACGAGGCCTGGAGAACACCTTGCACGATGCCAAGCACTGGCATGACATGGAGCTC    c.1080
 L   | K  R  G  L  E  N  T  L  H  D  A  K  H  W  H  D  M  E  L      p.360

          .         .         .         .         .         .       g.77516
 CAGAACCTGGGCGCTGTGGTCGGCCGGCTGGAGGCGGAGCTCAGGGAAATCCGAGCGGAG       c.1140
 Q  N  L  G  A  V  V  G  R  L  E  A  E  L  R  E  I  R  A  E         p.380

          .         .         .         .         .         .       g.77576
 GCGGAGCAGCAGCAACAGGAGCGCGCGCATCTGCTGGCCCGCAAGTGCCAGCTGCAGAAG       c.1200
 A  E  Q  Q  Q  Q  E  R  A  H  L  L  A  R  K  C  Q  L  Q  K         p.400

          .         .         .         .     | 07                  g.80039
 GACGTGGCGTCCTACCACGCCCTGCTGGACAGGGAGGAGAGCGG | CTGA                c.1248
 D  V  A  S  Y  H  A  L  L  D  R  E  E  S  G  |  X                  p.415

          .         .         .         .         .         .       g.80099
 tggagaaacttcctctttttcatgaagaaaacacccttcctcaacagctgacccaagaag       c.*60

          .         .         .         .         .         .       g.80159
 ttgcttgaggagctttctcctgagctccagtccctgctggattccctggttaattcagct       c.*120

          .         .         .         .         .         .       g.80219
 tgagctgaaaagcttcctggaagtggagaggatccttctgctttaatctgagtagtctgt       c.*180

          .         .         .         .         .         .       g.80279
 agcttgagcaatctcccttgtcctccttcaaataaatgctttgtgcgcagcgtccagttt       c.*240

 

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Beaded filament structural protein 2, phakinin protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

Powered by LOVD v.3.0 Build 29
©2004-2023 Leiden University Medical Center