centrosomal protein 120kDa (CEP120) - coding DNA reference sequence

(used for variant description)

(last modified February 12, 2016)


This file was created to facilitate the description of sequence variants on transcript NM_153223.3 in the CEP120 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000005.9, covering CEP120 transcript NM_153223.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
           .         .         .         .         .                g.5056
     tttacagcagtagtgcgcttgcgcagctggtcccacaccaagtcgcccgcctctcc       c.-61

 .         .         .        | 02.         .         .             g.5594
 tcgtccggctagcagagggcgctgtgag | ccgccttcgcccccggaccgctcaccgcaacc    c.-1

          .         .         .         .          | 03        .    g.10088
 ATGGTCTCCAAATCCGACCAATTGCTCATCGTCGTGTCCATCCTAGAAG | GTCGGCATTTC    c.60
 M  V  S  K  S  D  Q  L  L  I  V  V  S  I  L  E  G |   R  H  F      p.20

          .         .         .         .         .         .       g.10148
 CCCAAACGTCCAAAGCATATGCTTGTAGTGGAAGCAAAGTTTGATGGAGAACAGTTGGCT       c.120
 P  K  R  P  K  H  M  L  V  V  E  A  K  F  D  G  E  Q  L  A         p.40

          .         .         .         .         .         .       g.10208
 ACTGATCCTGTGGACCACACTGACCAGCCAGAATTTGCTACTGAGTTAGCTTGGGAAATT       c.180
 T  D  P  V  D  H  T  D  Q  P  E  F  A  T  E  L  A  W  E  I         p.60

          .         .       | 04 .         .         .         .    g.12502
 GACAGGAAAGCGCTTCATCAGCACAG | GCTACAGCGTACTCCTATCAAACTCCAATGTTTT    c.240
 D  R  K  A  L  H  Q  H  R  |  L  Q  R  T  P  I  K  L  Q  C  F      p.80

          .         .         .         .         .         .       g.12562
 GCCTTGGATCCTGTAACTTCAGCCAAGGAAACCATAGGTTACATCGTTCTGGATTTAAGA       c.300
 A  L  D  P  V  T  S  A  K  E  T  I  G  Y  I  V  L  D  L  R         p.100

          .         .  | 05      .         .         .         .    g.16091
 ACCGCTCAAGAAACAAAGCAG | GCACCAAAATGGTACCAGTTGCTGAGTAATAAATACACC    c.360
 T  A  Q  E  T  K  Q   | A  P  K  W  Y  Q  L  L  S  N  K  Y  T      p.120

          .         .         .         .         .         .       g.16151
 AAATTCAAGTCTGAGATACAGATAAGTATTGCTTTGGAAACCGATACAAAGCCACCAGTG       c.420
 K  F  K  S  E  I  Q  I  S  I  A  L  E  T  D  T  K  P  P  V         p.140

          .         .         .         .    | 06    .         .    g.29325
 GATAGCTTTAAAGCAAAGGGGGCTCCCCCTCGAGATGGAAAAG | TACCTGCCATCCTGGCT    c.480
 D  S  F  K  A  K  G  A  P  P  R  D  G  K  V |   P  A  I  L  A      p.160

          .         .         .         .         .         .       g.29385
 GGACTTGACCCCAGGGACATTGTGGCTGTGCTGAATGAAGAGGGAGGCTACCATCAGATT       c.540
 G  L  D  P  R  D  I  V  A  V  L  N  E  E  G  G  Y  H  Q  I         p.180

          .         .         .         .         .         .       g.29445
 GGACCAGCAGAATACTGTACTGACTCCTTTATTATGTCAGTGACCATAGCATTTGCTACC       c.600
 G  P  A  E  Y  C  T  D  S  F  I  M  S  V  T  I  A  F  A  T         p.200

          .   | 07     .         .         .         .         .    g.35143
 CAGTTGGAACAG | TTAATTCCATGTACCATGAAACTTCCAGAAAGACAGCCTGAGTTTTTC    c.660
 Q  L  E  Q   | L  I  P  C  T  M  K  L  P  E  R  Q  P  E  F  F      p.220

          .         .         .         .         .         .       g.35203
 TTTTACTACTCTTTACTGGGAAATGATGTTACAAATGAACCCTTCAATGATTTAATCAAC       c.720
 F  Y  Y  S  L  L  G  N  D  V  T  N  E  P  F  N  D  L  I  N         p.240

          .         .         .         .         .         .       g.35263
 CCAAACTTTGAGCCAGAGAGAGCATCAGTTCGCATCCGTAGCAGTGTAGAAATTCTTCGT       c.780
 P  N  F  E  P  E  R  A  S  V  R  I  R  S  S  V  E  I  L  R         p.260

          .         .         . | 08       .         .         .    g.37285
 GTTTACCTGGCTCTTCAGTCTAAACTGCAG | ATTCACCTCTGCTGTGGAGACCAGTCACTT    c.840
 V  Y  L  A  L  Q  S  K  L  Q   | I  H  L  C  C  G  D  Q  S  L      p.280

          .         .         .         .         .         .       g.37345
 GGAAGTACAGAAATACCTTTAACTGGATTACTTAAAAAGGGCAGTACAGAAATCAACCAG       c.900
 G  S  T  E  I  P  L  T  G  L  L  K  K  G  S  T  E  I  N  Q         p.300

          .         .         .         .         .         .       g.37405
 CACCCAGTCACAGTCGAAGGTGCTTTTACCCTTGACCCTCCAAACAGAGCCAAACAGAAG       c.960
 H  P  V  T  V  E  G  A  F  T  L  D  P  P  N  R  A  K  Q  K         p.320

          .         .         .         .         .         .       g.37465
 CTTGCACCTATTCCTGTGGAGCTAGCCCCAACTGTGGGAGTGTCTGTGGCTCTGCAGAGA       c.1020
 L  A  P  I  P  V  E  L  A  P  T  V  G  V  S  V  A  L  Q  R         p.340

          .         | 09         .         .         .         .    g.38494
 GAAGGCATAGACTCCCAG | TCTTTAATTGAATTAAAGACCCAGAATGAACATGAGCCAGAG    c.1080
 E  G  I  D  S  Q   | S  L  I  E  L  K  T  Q  N  E  H  E  P  E      p.360

          .         .         .         .         .         .       g.38554
 CATTCAAAGAAGAAAGTTTTAACCCCCATAAAGGAGAAGACACTTACTGGGCCAAAATCA       c.1140
 H  S  K  K  K  V  L  T  P  I  K  E  K  T  L  T  G  P  K  S         p.380

          .         .         .         .         .         .       g.38614
 CCAACAGTGTCCCCTGTTCCATCTCACAACCAGTCACCTCCAACAAAAGATGATGCAACA       c.1200
 P  T  V  S  P  V  P  S  H  N  Q  S  P  P  T  K  D  D  A  T         p.400

          .         .         .         .         .      | 10  .    g.39991
 GAAAGTGAAGTGGAAAGTTTACAGTATGATAAGGACACCAAACCAAATCCAAAAG | CCAGT    c.1260
 E  S  E  V  E  S  L  Q  Y  D  K  D  T  K  P  N  P  K  A |   S      p.420

          .         .         .         .         .         .       g.40051
 TCTTCTGTACCTGCTTCACTGGCCCAGCTAGTGACTACATCCAATGCTTCAGAAGTAGCT       c.1320
 S  S  V  P  A  S  L  A  Q  L  V  T  T  S  N  A  S  E  V  A         p.440

          .         .         .         .         .         .       g.40111
 TCAGGACAGAAGATTGCTGTACCAGCAACATCACATCATTTTTGCTTTTCAATAGACTTA       c.1380
 S  G  Q  K  I  A  V  P  A  T  S  H  H  F  C  F  S  I  D  L         p.460

          .         .         .         .         . | 11       .    g.41935
 AGGAGTATACATGCCTTGGAGATTGGTTTTCCAATCAACTGTATATTAAG | GTACTCATAT    c.1440
 R  S  I  H  A  L  E  I  G  F  P  I  N  C  I  L  R  |  Y  S  Y      p.480

          .         .         .         .         .         .       g.41995
 CCATTCTTTGGAAGTGCAGCTCCTATTATGACTAATCCTCCTGTAGAAGTTCGGAAAAAC       c.1500
 P  F  F  G  S  A  A  P  I  M  T  N  P  P  V  E  V  R  K  N         p.500

          .         .         .         .         .         .       g.42055
 ATGGAAGTTTTTCTTCCCCAGTCTTACTGTGCATTTGATTTTGCAACTATGCCTCATCAG       c.1560
 M  E  V  F  L  P  Q  S  Y  C  A  F  D  F  A  T  M  P  H  Q         p.520

          .         . | 12       .         .         .         .    g.43499
 CTGCAAGACACCTTCTTAAG | GATTCCATTACTGGTTGAACTATGGCACAAGGATAAAATG    c.1620
 L  Q  D  T  F  L  R  |  I  P  L  L  V  E  L  W  H  K  D  K  M      p.540

          .         .         .         .         .         .       g.43559
 AGTAAAGATTTACTTCTGGGAATTGCGAGAATCCAGCTTTCTAACATCTTGTCTTCAGAA       c.1680
 S  K  D  L  L  L  G  I  A  R  I  Q  L  S  N  I  L  S  S  E         p.560

          .         .         .         .         .         .       g.43619
 AAAACTCGTTTTTTAGGTTCTAATGGTGAACAGTGTTGGCGTCAAACTTACAGTGAAAGT       c.1740
 K  T  R  F  L  G  S  N  G  E  Q  C  W  R  Q  T  Y  S  E  S         p.580

          .         .    | 13    .         .         .         .    g.45547
 GTGCCTGTTATAGCAGCACAAGG | ATCAAATAACAGGATAGCAGATCTTTCTTACACAGTG    c.1800
 V  P  V  I  A  A  Q  G  |  S  N  N  R  I  A  D  L  S  Y  T  V      p.600

          .         .         .         .         .         .       g.45607
 ACTCTAGAAGATTATGGACTAGTAAAAATGCGTGAGATTTTTATCTCTGATTCATCTCAG       c.1860
 T  L  E  D  Y  G  L  V  K  M  R  E  I  F  I  S  D  S  S  Q         p.620

  | 14       .         .         .         .         .         .    g.45763
  | GGTGTATCTGCCGTACAGCAAAAGCCGTCTTCTCTTCCTCCAGCACCTTGTCCTTCAGAG    c.1920
  | G  V  S  A  V  Q  Q  K  P  S  S  L  P  P  A  P  C  P  S  E      p.640

          .         .         .         .         .         .       g.45823
 ATCCAGACAGAGCCTCGTGAAACGTTAGAATACAAAGCAGCACTTGAGCTAGAAATGTGG       c.1980
 I  Q  T  E  P  R  E  T  L  E  Y  K  A  A  L  E  L  E  M  W         p.660

          .         .         .    | 15    .         .         .    g.46419
 AAGGAGATGCAAGAAGATATATTTGAAAATCAG | CTGAAGCAGAAAGAACTGGCTCATATG    c.2040
 K  E  M  Q  E  D  I  F  E  N  Q   | L  K  Q  K  E  L  A  H  M      p.680

          .         .         .         .         .         .       g.46479
 CAGGCTCTTGCAGAGGAATGGAAGAAAAGGGACCGAGAAAGAGAATCACTAGTAAAGAAA       c.2100
 Q  A  L  A  E  E  W  K  K  R  D  R  E  R  E  S  L  V  K  K         p.700

     | 16    .         .         .         .         .         .    g.50221
 AAG | GTGGCTGAATATACTATTCTAGAAGGAAAACTTCAAAAAACTCTAATTGACTTGGAG    c.2160
 K   | V  A  E  Y  T  I  L  E  G  K  L  Q  K  T  L  I  D  L  E      p.720

          .         .         .       | 17 .         .         .    g.51081
 AAGCGAGAGCAGCAGCTTGCTAGTGTGGAATCAGAG | CTTCAAAGAGAAAAAAAGGAACTG    c.2220
 K  R  E  Q  Q  L  A  S  V  E  S  E   | L  Q  R  E  K  K  E  L      p.740

          .         .         .         .         .         .       g.51141
 CAATCAGAACGTCAGCGGAACCTGCAAGAACTGCAGGACTCTATCCGTAGGGCCAAAGAG       c.2280
 Q  S  E  R  Q  R  N  L  Q  E  L  Q  D  S  I  R  R  A  K  E         p.760

          .         .         .         .         .         .       g.51201
 GACTGTATTCACCAAGTAGAACTAGAAAGGTTAAAAATCAAACAGCTCGAAGAGGATAAA       c.2340
 D  C  I  H  Q  V  E  L  E  R  L  K  I  K  Q  L  E  E  D  K         p.780

          .         | 18         .         .         .         .    g.55862
 CACCGCCTTCAGCAACAG | CTTAATGATGCTGAAAATAAGTATAAGATTTTGGAAAAAGAG    c.2400
 H  R  L  Q  Q  Q   | L  N  D  A  E  N  K  Y  K  I  L  E  K  E      p.800

          .         .         .         .         .         .       g.55922
 TTCCAACAGTTCAAGGACCAGCAAAACAACAAACCAGAAATCCGTCTACAGTCTGAAATA       c.2460
 F  Q  Q  F  K  D  Q  Q  N  N  K  P  E  I  R  L  Q  S  E  I         p.820

          .         .  | 19      .         .         .         .    g.64037
 AATCTTCTCACCTTGGAAAAG | GTTGAACTTGAAAGAAAGTTGGAATCTGCAACTAAGTCT    c.2520
 N  L  L  T  L  E  K   | V  E  L  E  R  K  L  E  S  A  T  K  S      p.840

          .         .         .         .         .         .       g.64097
 AAACTGCATTACAAGCAGCAGTGGGGACGAGCTTTGAAAGAACTTGCCAGACTTAAACAG       c.2580
 K  L  H  Y  K  Q  Q  W  G  R  A  L  K  E  L  A  R  L  K  Q         p.860

  | 20       .         .         .         .         .         .    g.78563
  | AGGGAGCAAGAAAGTCAAATGGCTCGTCTTAAAAAACAGCAGGAAGAATTGGAACAGATG    c.2640
  | R  E  Q  E  S  Q  M  A  R  L  K  K  Q  Q  E  E  L  E  Q  M      p.880

          .         .         .         .         .         .       g.78623
 AGACTACGTTACCTTGCCGCTGAGGAAAAAGATACAGTAAAAACCGAGCGACAAGAATTG       c.2700
 R  L  R  Y  L  A  A  E  E  K  D  T  V  K  T  E  R  Q  E  L         p.900

          .         .       | 21 .         .         .         .    g.81873
 TTGGATATAAGAAATGAATTGAACAG | GTTAAGGCAACAAGAGCAAAAACAATACCAGGAT    c.2760
 L  D  I  R  N  E  L  N  R  |  L  R  Q  Q  E  Q  K  Q  Y  Q  D      p.920

          .         .         .         .         .         .       g.81933
 TCCACAGAGATTGCAAGTGGAAAAAAGGATGGCCCCCATGGCAGTGTATTGGAAGAAGGT       c.2820
 S  T  E  I  A  S  G  K  K  D  G  P  H  G  S  V  L  E  E  G         p.940

          .         .         .         .         .         .       g.81993
 TTGGATGATTATTTGACTCGCCTGATAGAAGAAAGGGATACTTTGATGAGAACGGGTGTG       c.2880
 L  D  D  Y  L  T  R  L  I  E  E  R  D  T  L  M  R  T  G  V         p.960

          .         .         .         .         .         .       g.82053
 TATAATCACGAGGATCGAATAATAAGTGAACTCGACCGACAGATCAGAGAGATTTTGGCA       c.2940
 Y  N  H  E  D  R  I  I  S  E  L  D  R  Q  I  R  E  I  L  A         p.980

          .         .                                               g.82074
 AAAAGCAATGCCAGTAATTAA                                              c.2961
 K  S  N  A  S  N  X                                                p.986

          .         .         .         .         .         .       g.82134
 taacatttggaaaagctttatagagactctaagtctaaattttaatttctttgtaaaaac       c.*60

          .         .         .         .         .         .       g.82194
 ctcaaaagtgaggaaaatggatgttttaaaatggtattttcaattttttataagcaaaat       c.*120

          .         .         .         .         .         .       g.82254
 tttgtatgttattgtatagtatttatttgatcttatttactttatgctacctctcccaca       c.*180

          .         .         .         .         .         .       g.82314
 ctggttttatttgtaatttgcatttatatactcattttaaatgacttttcagtgtttttc       c.*240

          .         .         .         .         .         .       g.82374
 atagtttataatctgatggctaactaactttcaaaacagcttttaactaagtttgttgta       c.*300

          .         .         .         .         .         .       g.82434
 ggagaaatgactgcggtaatttccagttctataatgtttcatgttgagccaaaagagtat       c.*360

          .         .         .         .         .         .       g.82494
 atcttgcactttaaaaacgctgcgtcctattccatttgaatgtaaattcttaaaagttga       c.*420

          .         .         .         .         .         .       g.82554
 gaccaattgtaaccagtttaactcattttagatgacctttttttcttataatatttgcaa       c.*480

          .         .         .         .         .         .       g.82614
 gtgacaagtttgaaaacaaagcaagatcagtgcagagaagccacatgacatgttgggtga       c.*540

          .         .         .         .         .         .       g.82674
 cagattggtcatttatttaaataaagttaatacagattaaatttgtttcaagagctattg       c.*600

          .         .         .         .         .         .       g.82734
 aattttcaaattttcagtgtatttataacttttaagaacatgaagtattagcttaatata       c.*660

          .         .         .         .         .         .       g.82794
 gttttctctgttggtttcttcctcaagtttgcattgttttcttttgttaaaattagagat       c.*720

          .         .         .         .         .         .       g.82854
 ttctttttattttccagttatagtaatactagctgtcagcttaaaccctctgtaatagaa       c.*780

          .         .         .         .         .         .       g.82914
 catggaaacagacacataaagacattagctgaaaaaatagagtgaaaatcaactattttt       c.*840

          .         .         .         .         .         .       g.82974
 tactcccgctaatttcaatcaatcgttttcaaaagcgcacgagattcactcattggattt       c.*900

          .         .         .         .         .         .       g.83034
 atgcagtgccctgtctgtataaaaactcttaagagttcctttatatcatattcttcagag       c.*960

          .         .         .         .         .         .       g.83094
 ccaacatttgtcctcaaagcaacgtttcccacctccttttactgagtactgaaaaagttt       c.*1020

          .         .         .         .         .         .       g.83154
 tagcaaagtcacagattaggttgaatttcaaaatatatgtactttaaaaagttctgattt       c.*1080

          .         .         .         .         .         .       g.83214
 ccaaatataataaagttaaaattaagtatatactttaggaagttaccaataacttccatc       c.*1140

          .         .         .         .         .         .       g.83274
 aaagcagagtaggatatatggtaacattaattttcggtcatttcaaatgaggtatatttc       c.*1200

          .         .         .         .         .         .       g.83334
 ttattagggaaattaaagtccctatatttattatatattttttccttattaacagagtat       c.*1260

          .         .         .         .         .         .       g.83394
 taatctagtaaaaaataacccagcagtaaataataaagaaattactgaatgagaggataa       c.*1320

          .         .         .         .         .         .       g.83454
 tgaatctgaatcatagcaggaatttgcaatattaattatggttagctatttttctctcat       c.*1380

          .         .         .         .         .         .       g.83514
 tgatttttgtgccacttgaatggaacagaagcaagccttatgttttggaaggtctgcggt       c.*1440

          .         .         .         .         .         .       g.83574
 aaaatgctgtgactgtttactttcaattgcattgtgtgttgcctgtgactgctttcaaac       c.*1500

          .         .         .         .         .         .       g.83634
 gctagagggggcctctgatttaaagaaataaaaaggacttttctaaaatggatgtgtagt       c.*1560

          .         .         .         .         .         .       g.83694
 ttattttgccttttgtaaagctcttttggctattgtaacttaacaaataaaatcataatt       c.*1620

          .                                                         g.83708
 gtgtgcatctctga                                                     c.*1634

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Centrosomal protein 120kDa protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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