contactin 4 (CNTN4) - coding DNA reference sequence

(used for variant description)

(last modified November 4, 2025)


This file was created to facilitate the description of sequence variants on transcript NM_175607.2 in the CNTN4 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000003.11, covering CNTN4 transcript NM_175607.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                               .         .         .                g.5039
                      gttcgacgccaggattggctgcaagtagggagctttcgc       c.-301

 .         .         .         .         .         .                g.5099
 cgccgccccgggcccctcggactgtgccggcgccgcacccgaggctctcgccagcccggc       c.-241

 .         .    | 02    .         .         .         .             g.6738
 gccccggtgctgag | tgggtgaaaaagaacagtgtgtcatgaagacaggcacctggaggtg    c.-181

 .         .         .         .      | 03  .         .             g.245336
 atttgggtggcattcatgagaaaattcacgttaccc | gaatcattgacatagagtaactcc    c.-121

 .         .         .         .  | 04      .         .             g.477578
 acagcatgtgtcttcaagagcttccctaaaag | attaaaggttatacaaaacttaaaagaa    c.-61

 .         .         .         .         .         .                g.477638
 gcagcaattctattcgcttgttattggacttgaaactccctttgacctcggaaactgaag       c.-1

          .         .         .         .         .      | 05  .    g.642354
 ATGAGGTTGCCATGGGAACTGCTGGTACTGCAATCATTCATTTTGTGCCTTGCAG | ATGAT    c.60
 M  R  L  P  W  E  L  L  V  L  Q  S  F  I  L  C  L  A  D |   D      p.20

          .         .         .         .         .         .       g.642414
 TCCACACTGCATGGCCCGATTTTTATTCAAGAACCAAGTCCTGTAATGTTCCCTTTGGAT       c.120
 S  T  L  H  G  P  I  F  I  Q  E  P  S  P  V  M  F  P  L  D         p.40

          .         .         .         .         .         .       g.642474
 TCTGAGGAGAAAAAAGTGAAGCTCAATTGTGAAGTTAAAGGAAATCCAAAACCTCATATC       c.180
 S  E  E  K  K  V  K  L  N  C  E  V  K  G  N  P  K  P  H  I         p.60

    | 06     .         .         .         .         .         .    g.651714
 AG | GTGGAAGTTAAATGGAACAGATGTTGACACTGGTATGGATTTCCGCTACAGTGTTGTT    c.240
 R  |  W  K  L  N  G  T  D  V  D  T  G  M  D  F  R  Y  S  V  V      p.80

          .         .         .         .         .         .       g.651774
 GAAGGGAGCTTGTTGATCAATAACCCCAATAAAACCCAAGATGCTGGAACGTACCAGTGC       c.300
 E  G  S  L  L  I  N  N  P  N  K  T  Q  D  A  G  T  Y  Q  C         p.100

          .         .         .         .         .         | 07    g.725622
 ACAGCGACAAACTCGTTTGGAACAATTGTTAGCAGAGAAGCAAAGCTTCAGTTTGCTT | AT    c.360
 T  A  T  N  S  F  G  T  I  V  S  R  E  A  K  L  Q  F  A  Y |       p.120

          .         .         .         .         .         .       g.725682
 CTTGACAACTTTAAAACAAGAACAAGAAGCACTGTGTCTGTCCGTCGAGGTCAAGGAATG       c.420
 L  D  N  F  K  T  R  T  R  S  T  V  S  V  R  R  G  Q  G  M         p.140

          .         .         .     | 08   .         .         .    g.772912
 GTGCTACTGTGTGGCCCGCCACCCCATTCTGGAG | AGCTGAGTTATGCCTGGATCTTCAAT    c.480
 V  L  L  C  G  P  P  P  H  S  G  E |   L  S  Y  A  W  I  F  N      p.160

          .         .         .         .         .         .       g.772972
 GAATACCCTTCCTATCAGGATAATCGCCGCTTTGTTTCTCAAGAGACTGGGAATCTGTAT       c.540
 E  Y  P  S  Y  Q  D  N  R  R  F  V  S  Q  E  T  G  N  L  Y         p.180

          .         .         .         .         .         .       g.773032
 ATTGCCAAAGTAGAAAAATCAGATGTTGGGAATTATACCTGTGTGGTTACCAATACCGTG       c.600
 I  A  K  V  E  K  S  D  V  G  N  Y  T  C  V  V  T  N  T  V         p.200

          .         .         .         .         .   | 09     .    g.789287
 ACAAACCACAAGGTCCTGGGGCCACCTACACCACTAATATTGAGAAATGATG | GAGTGATG    c.660
 T  N  H  K  V  L  G  P  P  T  P  L  I  L  R  N  D  G |   V  M      p.220

          .         .         .         .         .         .       g.789347
 GGTGAATATGAGCCCAAAATAGAAGTGCAGTTCCCAGAAACAGTTCCGACTGCAAAAGGA       c.720
 G  E  Y  E  P  K  I  E  V  Q  F  P  E  T  V  P  T  A  K  G         p.240

          .         .         .      | 10  .         .         .    g.793199
 GCAACGGTGAAGCTGGAATGCTTTGCTTTAGGAAA | TCCAGTACCAACTATTATCTGGCGA    c.780
 A  T  V  K  L  E  C  F  A  L  G  N  |  P  V  P  T  I  I  W  R      p.260

          .         .         .         .         .         .       g.793259
 AGAGCTGATGGAAAGCCAATAGCAAGGAAAGCCAGAAGACACAAGTCAAATGGAATTCTT       c.840
 R  A  D  G  K  P  I  A  R  K  A  R  R  H  K  S  N  G  I  L         p.280

          .         .         .         .         .         .       g.793319
 GAGATCCCTAATTTTCAGCAGGAGGATGCTGGTTTATATGAATGTGTAGCTGAAAATTCC       c.900
 E  I  P  N  F  Q  Q  E  D  A  G  L  Y  E  C  V  A  E  N  S         p.300

          .         .         .         . | 11       .         .    g.806839
 AGAGGGAAAAATGTAGCAAGGGGACAGCTAACTTTCTATG | CTCAACCTAATTGGATTCAA    c.960
 R  G  K  N  V  A  R  G  Q  L  T  F  Y  A |   Q  P  N  W  I  Q      p.320

          .         .         .         .         .         .       g.806899
 AAAATAAATGATATTCACGTGGCCATGGAAGAAAATGTCTTTTGGGAATGTAAAGCAAAT       c.1020
 K  I  N  D  I  H  V  A  M  E  E  N  V  F  W  E  C  K  A  N         p.340

          .         .         .         .         .        | 12.    g.809013
 GGAAGGCCTAAGCCTACATACAAGTGGCTAAAAAATGGCGAACCTCTGCTAACTCGG | GAT    c.1080
 G  R  P  K  P  T  Y  K  W  L  K  N  G  E  P  L  L  T  R   | D      p.360

          .         .         .         .         .         .       g.809073
 AGAATTCAAATTGAGCAAGGAACACTCAACATAACAATAGTGAACCTCTCAGATGCTGGC       c.1140
 R  I  Q  I  E  Q  G  T  L  N  I  T  I  V  N  L  S  D  A  G         p.380

          .         .         .         .         .         .       g.809133
 ATGTATCAGTGTTTGGCAGAGAATAAACATGGAGTTATCTTTTCCAACGCAGAGCTTAGT       c.1200
 M  Y  Q  C  L  A  E  N  K  H  G  V  I  F  S  N  A  E  L  S         p.400

         | 13.         .         .         .         .         .    g.831816
 GTTATAG | CTGTAGGTCCAGATTTTTCAAGAACACTCTTGAAAAGAGTAACTCTTGTCAAA    c.1260
 V  I  A |   V  G  P  D  F  S  R  T  L  L  K  R  V  T  L  V  K      p.420

          .         .         .         .         .         .       g.831876
 GTGGGAGGTGAAGTTGTCATTGAGTGTAAGCCAAAAGCGTCTCCAAAACCTGTTTACACC       c.1320
 V  G  G  E  V  V  I  E  C  K  P  K  A  S  P  K  P  V  Y  T         p.440

          .         .         .         | 14         .         .    g.894501
 TGGAAGAAAGGAAGGGATATATTAAAAGAAAATGAAAG | AATTACCATTTCTGAAGATGGA    c.1380
 W  K  K  G  R  D  I  L  K  E  N  E  R  |  I  T  I  S  E  D  G      p.460

          .         .         .         .         .         .       g.894561
 AACCTCAGAATCATCAACGTTACTAAATCAGACGCTGGGAGTTATACCTGTATAGCCACT       c.1440
 N  L  R  I  I  N  V  T  K  S  D  A  G  S  Y  T  C  I  A  T         p.480

          .         .         .         .       | 15 .         .    g.932250
 AACCATTTTGGAACTGCTAGCAGTACTGGAAACTTGGTAGTGAAAG | ATCCAACAAGGGTA    c.1500
 N  H  F  G  T  A  S  S  T  G  N  L  V  V  K  D |   P  T  R  V      p.500

          .         .         .         .         .         .       g.932310
 ATGGTACCCCCTTCCAGTATGGATGTCACTGTTGGAGAGAGTATTGTTTTACCGTGCCAG       c.1560
 M  V  P  P  S  S  M  D  V  T  V  G  E  S  I  V  L  P  C  Q         p.520

          .         .         .         .         .         .       g.932370
 GTAACGCATGATCACTCGCTAGACATCGTGTTTACTTGGTCATTTAATGGACACCTGATA       c.1620
 V  T  H  D  H  S  L  D  I  V  F  T  W  S  F  N  G  H  L  I         p.540

          .         .         .         .   | 16     .         .    g.937007
 GACTTTGACAGAGATGGGGACCACTTTGAAAGAGTTGGAGGG | CAGGATTCAGCTGGTGAT    c.1680
 D  F  D  R  D  G  D  H  F  E  R  V  G  G   | Q  D  S  A  G  D      p.560

          .         .         .         .         .         .       g.937067
 TTGATGATCCGAAACATCCAACTGAAGCATGCTGGGAAATATGTCTGCATGGTCCAAACA       c.1740
 L  M  I  R  N  I  Q  L  K  H  A  G  K  Y  V  C  M  V  Q  T         p.580

          .         .         .         .    | 17    .         .    g.940783
 AGTGTGGACAGGCTATCTGCTGCTGCAGACCTGATTGTAAGAG | GTCCTCCAGGTCCCCCA    c.1800
 S  V  D  R  L  S  A  A  A  D  L  I  V  R  G |   P  P  G  P  P      p.600

          .         .         .         .         .         .       g.940843
 GAGGCTGTGACAATAGACGAAATCACAGATACCACTGCTCAGCTCTCCTGGAGACCCGGG       c.1860
 E  A  V  T  I  D  E  I  T  D  T  T  A  Q  L  S  W  R  P  G         p.620

          .         .         .         .         .         .       g.940903
 CCTGACAACCACAGCCCCATCACCATGTATGTCATTCAAGCCAGGACTCCATTCTCCGTG       c.1920
 P  D  N  H  S  P  I  T  M  Y  V  I  Q  A  R  T  P  F  S  V         p.640

          .         .   | 18     .         .         .         .    g.943351
 GGCTGGCAAGCAGTCAGTACAG | TCCCAGAACTCATTGATGGGAAGACATTCACAGCGACC    c.1980
 G  W  Q  A  V  S  T  V |   P  E  L  I  D  G  K  T  F  T  A  T      p.660

          .         .         .         .         .         .       g.943411
 GTGGTGGGTTTGAACCCTTGGGTTGAATATGAATTCCGCACAGTTGCAGCCAACGTGATT       c.2040
 V  V  G  L  N  P  W  V  E  Y  E  F  R  T  V  A  A  N  V  I         p.680

          .         .         .         .         .   | 19     .    g.945075
 GGGATTGGGGAGCCCAGCCGCCCCTCAGAGAAACGGAGAACAGAAGAAGCTC | TCCCCGAA    c.2100
 G  I  G  E  P  S  R  P  S  E  K  R  R  T  E  E  A  L |   P  E      p.700

          .         .         .         .         .         .       g.945135
 GTCACACCAGCGAATGTCAGTGGTGGCGGAGGCAGCAAATCTGAACTGGTTATAACCTGG       c.2160
 V  T  P  A  N  V  S  G  G  G  G  S  K  S  E  L  V  I  T  W         p.720

     | 20    .         .         .         .         .         .    g.946228
 GAG | ACGGTCCCTGAGGAATTACAGAATGGTCGAGGCTTTGGTTATGTGGTGGCCTTCCGG    c.2220
 E   | T  V  P  E  E  L  Q  N  G  R  G  F  G  Y  V  V  A  F  R      p.740

          .         .         .         .         .         .       g.946288
 CCCTACGGTAAAATGATCTGGATGCTGACAGTGCTGGCCTCAGCTGATGCCTCTAGATAC       c.2280
 P  Y  G  K  M  I  W  M  L  T  V  L  A  S  A  D  A  S  R  Y         p.760

          .         .         .         .         .         .       g.946348
 GTGTTCAGGAATGAGAGCGTGCACCCCTTCTCTCCCTTTGAGGTTAAAGTAGGTGTCTTC       c.2340
 V  F  R  N  E  S  V  H  P  F  S  P  F  E  V  K  V  G  V  F         p.780

          .         .         .         .         .         | 21    g.948446
 AACAACAAAGGAGAAGGCCCTTTCAGTCCCACCACGGTGGTGTATTCTGCAGAAGAAG | AA    c.2400
 N  N  K  G  E  G  P  F  S  P  T  T  V  V  Y  S  A  E  E  E |       p.800

          .         .         .         .         .         .       g.948506
 CCCACCAAACCACCAGCCAGTATCTTTGCCAGAAGTCTTTCTGCCACAGATATTGAAGTT       c.2460
 P  T  K  P  P  A  S  I  F  A  R  S  L  S  A  T  D  I  E  V         p.820

          .         .         .         .         .  | 22      .    g.949120
 TTCTGGGCCTCCCCACTGGAGAAGAATAGAGGACGAATACAAGGTTATGAG | GTTAAATAT    c.2520
 F  W  A  S  P  L  E  K  N  R  G  R  I  Q  G  Y  E   | V  K  Y      p.840

          .         .         .         .         .         .       g.949180
 TGGAGACATGAAGACAAAGAAGAAAATGCTAGAAAAATACGAACAGTTGGAAATCAGACA       c.2580
 W  R  H  E  D  K  E  E  N  A  R  K  I  R  T  V  G  N  Q  T         p.860

          .         .         .         .         .         .       g.949240
 TCAACAAAAATCACGAACTTAAAAGGCAGTGTGCTGTATCACTTAGCTGTCAAGGCATAT       c.2640
 S  T  K  I  T  N  L  K  G  S  V  L  Y  H  L  A  V  K  A  Y         p.880

          .         .         .         .         .         | 23    g.949728
 AATTCTGCTGGGACAGGCCCCTCTAGTGCAACAGTCAATGTGACAACCCGAAAGCCAC | CA    c.2700
 N  S  A  G  T  G  P  S  S  A  T  V  N  V  T  T  R  K  P  P |       p.900

          .         .         .         .         .         .       g.949788
 CCAAGTCAACCCCCCGGAAACATCATATGGAATTCATCAGACTCCAAAATTATCCTGAAT       c.2760
 P  S  Q  P  P  G  N  I  I  W  N  S  S  D  S  K  I  I  L  N         p.920

          .         .         .         .         .  | 24      .    g.959950
 TGGGATCAAGTGAAGGCCCTGGATAATGAGTCGGAAGTAAAAGGATACAAA | GTCTTGTAC    c.2820
 W  D  Q  V  K  A  L  D  N  E  S  E  V  K  G  Y  K   | V  L  Y      p.940

          .         .         .         .         .         .       g.960010
 AGATGGAACAGACAAAGCAGCACATCTGTCATTGAAACAAATAAAACATCGGTGGAGCTT       c.2880
 R  W  N  R  Q  S  S  T  S  V  I  E  T  N  K  T  S  V  E  L         p.960

          .         .         .         .         .         .       g.960070
 TCTTTGCCTTTCGATGAAGATTATATAATAGAAATTAAGCCATTCAGCGACGGAGGAGAT       c.2940
 S  L  P  F  D  E  D  Y  I  I  E  I  K  P  F  S  D  G  G  D         p.980

          .         .         .         . | 25       .         .    g.962274
 GGCAGCAGCAGTGAACAAATTCGAATTCCAAAGATATCAA | ATGCCTACGCGAGAGGATCT    c.3000
 G  S  S  S  E  Q  I  R  I  P  K  I  S  N |   A  Y  A  R  G  S      p.1000

          .         .         .         .         .         .       g.962334
 GGGGCTTCCACTTCGAATGCATGTACGCTGTCAGCCATCAGTACAATAATGATTTCCCTC       c.3060
 G  A  S  T  S  N  A  C  T  L  S  A  I  S  T  I  M  I  S  L         p.1020

          .         .                                               g.962355
 ACAGCTAGGTCCAGTTTATGA                                              c.3081
 T  A  R  S  S  L  X                                                p.1026

          .         .         .         .         .         .       g.962415
 caaaagttatctgaaggacttgctgtttataatataagcaacatttagctagttgttttg       c.*60

          .         .         .         .         .         .       g.962475
 aagacacccagtactaagtaatattgttgttcaagtacatcttattactggaataaaaat       c.*120

          .         .         .         .         .         .       g.962535
 gttttttgcttctttaggaatggcattatacagtacttcctcaaagcaaatctagctttg       c.*180

          .         .         .         .         .         .       g.962595
 tctgaagtttctttggaaactctgcaatgcactgaagacatctgtaatatgatgttacca       c.*240

          .         .         .         .         .         .       g.962655
 aagcagtttacatatgtccttatatgcatattttttattatatatttagtgttttataga       c.*300

          .         .         .         .         .         .       g.962715
 attttttaaagttaacatataatgtagatattaattttttcctcggctgtaaaatgctat       c.*360

          .         .         .         .         .         .       g.962775
 gggcaacacaatcatgcaattataatttgaaaatatttcctttaaagacagagtttgaaa       c.*420

          .         .         .         .         .         .       g.962835
 ctcatcttggtaaataaattgcaaattactcgtacagttttacaaggatctcatggcaga       c.*480

          .         .         .         .         .         .       g.962895
 acagcggaagacttggtccgtaactcaaggctgttgtatgcaaactactcttctagtggt       c.*540

          .         .         .         .         .         .       g.962955
 taatgcacttgacatgtacagtatgtttcccatgccgttgtgattttgacatgtacagta       c.*600

          .         .         .         .         .         .       g.963015
 tgttttcatgccgttgtgaattttgttgttcaacccaacttgagatggtttcaggaatgg       c.*660

          .         .         .         .         .         .       g.963075
 ctgcaatctcaaaagctcaatgtactgcccaagaggcaccttgtgcaatattcccatccc       c.*720

          .         .         .         .         .         .       g.963135
 tgaatttagcattgtacaggaagattttcttttcactcaactgagttagcattgtctttg       c.*780

          .         .         .         .         .         .       g.963195
 tggtagcattatcttagacattaaatttgaagtaacatatatcctgtagtaacatagacc       c.*840

          .         .         .         .         .         .       g.963255
 caaagttactatagtcaaccaagtctttcaaaggataaaagatcattttattatctttaa       c.*900

          .         .         .         .         .         .       g.963315
 ctgtatctattttgaatgtaaatttaaaaaaagtaattctctgtcaatggattcgtaatt       c.*960

          .         .         .         .         .         .       g.963375
 tctttacaaaatttcttatatataatatgtgtatctctgtaataatagagcccttctttt       c.*1020

          .         .         .         .         .         .       g.963435
 gaatcaaaattacatatggactttggaagattgctcctatttcaacaaatagttgctgca       c.*1080

          .         .         .         .         .         .       g.963495
 agaatttttaatatgactctataaaagctctttagtacaattgtatggtttcttgatgat       c.*1140

          .         .         .         .         .         .       g.963555
 tctgttttgcaataggtagcctagttgctttatatgctttaccttctaggtcttaaaatc       c.*1200

          .         .         .         .         .         .       g.963615
 acacattggaaaatgacaatatcaacaaaactgtattcttatgaaaagaactatttgtta       c.*1260

          .         .         .         .         .         .       g.963675
 caatgagaaaggttttgtgagtaaaccctactggacagtgacataaaaggcaatggaatt       c.*1320

          .         .         .         .         .         .       g.963735
 ttctataaacattttctcatgtaaacatgctgccaccttttcttctttctcagagaactc       c.*1380

          .         .         .         .         .         .       g.963795
 aaatttgctatagtttgtcatttttgcttacaaataatataacttttcaaccttctagtt       c.*1440

          .         .         .         .         .         .       g.963855
 atatttatccaataaagtcataatcgggattccatttgtgtaaaaactagggtggtaacc       c.*1500

          .         .         .         .         .         .       g.963915
 ggaaaaaaatattgtcagtatttcaagctgtgttcctttcttagtttgatatggttactt       c.*1560

          .         .         .         .         .         .       g.963975
 ctatgttgaaataaaatttaaaatcacatgcaaaaaaaaaatcagcaaaataataaaatg       c.*1620

          .         .         .         .         .         .       g.964035
 aacgaaaaaaaatgacacccagggagttcccaaccccagtgtaaatgatatttaccagtg       c.*1680

          .         .         .         .         .         .       g.964095
 atctagcatatgtaatcttttttaaaggtattgttaataaatattctgtcatttgtaaag       c.*1740

                                                                    g.964096
 a                                                                  c.*1741

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Contactin 4 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

Powered by LOVD v.3.0 Build 30b
©2004-2025 Leiden University Medical Center