ER degradation enhancer, mannosidase alpha-like 3 (EDEM3) - coding DNA reference sequence

(used for variant description)

(last modified June 28, 2021)


This file was created to facilitate the description of sequence variants on transcript NM_025191.3 in the EDEM3 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000001.10, covering EDEM3 transcript NM_025191.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                         .         .                g.5021
                                        gttggggaggcggtttcctag       c.-241

 .         .         .         .         .         .                g.5081
 actacgacaccggaaagctgggggaggcgctccgggatactgagggcggagggcggtggc       c.-181

 .         .         .         .         .         .                g.5141
 agcgctggcgctggggaccggcttggtggcttcgggaaacagtttggcgccggcggccgt       c.-121

 .         .         .         .         .         .                g.5201
 ccgtgttactccgcatcccgccccgtctcggcacggctagcagccccctggccaccagcg       c.-61

 .         .         .         .         .         .                g.5261
 tccagcaatgtgtctcaccggccgggcgtagcagctgcgcgtgcgcggaaccgcggggcc       c.-1

          .         .         .         .         .         .       g.5321
 ATGAGCGAAGCCGGCGGCCGGGGCTGTGGGTCCCCGGTTCCCCAGCGAGCGCGATGGAGA       c.60
 M  S  E  A  G  G  R  G  C  G  S  P  V  P  Q  R  A  R  W  R         p.20

          .         .         .         .         .         .       g.5381
 CTAGTGGCGGCGACGGCCGCGTTCTGCCTGGTGTCGGCCACCTCCGTGTGGACGGCGGGG       c.120
 L  V  A  A  T  A  A  F  C  L  V  S  A  T  S  V  W  T  A  G         p.40

          .         .         .         | 02         .         .    g.10337
 GCCGAGCCCATGAGTAGGGAGGAGAAACAGAAGCTTGG | GAATCAAGTACTGGAAATGTTT    c.180
 A  E  P  M  S  R  E  E  K  Q  K  L  G  |  N  Q  V  L  E  M  F      p.60

          .         .     | 03   .         .         .         .    g.22232
 GATCATGCTTATGGTAACTATATG | GAACATGCTTACCCTGCTGATGAACTCATGCCTTTA    c.240
 D  H  A  Y  G  N  Y  M   | E  H  A  Y  P  A  D  E  L  M  P  L      p.80

          .         .         .         .         .         .       g.22292
 ACCTGTAGAGGTCGAGTTAGAGGCCAAGAGCCAAGTCGCGGTGACGTTGATGATGCCTTG       c.300
 T  C  R  G  R  V  R  G  Q  E  P  S  R  G  D  V  D  D  A  L         p.100

       | 04  .         .         .         .      | 05  .         . g.25279
 GGAAA | ATTTTCTCTGACACTGATTGATTCTTTGGACACTCTTGTG | GTTTTAAATAAAACT c.360
 G  K  |  F  S  L  T  L  I  D  S  L  D  T  L  V   | V  L  N  K  T   p.120

          .         .         .         .         .         .       g.25339
 AAAGAATTTGAAGATGCAGTGAGAAAAGTTTTAAGAGATGTTAATTTAGATAACGATGTA       c.420
 K  E  F  E  D  A  V  R  K  V  L  R  D  V  N  L  D  N  D  V         p.140

          .         .         .         | 06         .         .    g.26939
 GTCGTATCAGTCTTTGAAACAAACATCAGAGTTCTTGG | GGGTCTTTTGGGTGGGCACTCC    c.480
 V  V  S  V  F  E  T  N  I  R  V  L  G  |  G  L  L  G  G  H  S      p.160

          .         .         .         .         .         .       g.26999
 CTGGCAATCATGCTGAAAGAAAAAGGTGAATATATGCAGTGGTACAATGATGAACTTCTC       c.540
 L  A  I  M  L  K  E  K  G  E  Y  M  Q  W  Y  N  D  E  L  L         p.180

          .         .         .         .         .         .       g.27059
 CAAATGGCAAAGCAGTTAGGTTACAAACTTTTACCGGCTTTCAACACTACCAGTGGCCTT       c.600
 Q  M  A  K  Q  L  G  Y  K  L  L  P  A  F  N  T  T  S  G  L         p.200

          .   | 07     .         .         .         .         .    g.33566
 CCTTATCCAAGA | ATTAATTTAAAGTTTGGCATCAGAAAACCAGAAGCTCGGACAGGAACT    c.660
 P  Y  P  R   | I  N  L  K  F  G  I  R  K  P  E  A  R  T  G  T      p.220

          .         .         .         .         .         .       g.33626
 GAGACAGATACCTGTACAGCTTGTGCAGGTACCTTGATCCTTGAATTTGCTGCTTTAAGT       c.720
 E  T  D  T  C  T  A  C  A  G  T  L  I  L  E  F  A  A  L  S         p.240

          .         .        | 08.         .         .         .    g.36084
 CGATTCACAGGAGCAACAATATTTGAG | GAATATGCCAGAAAAGCTCTTGATTTTCTCTGG    c.780
 R  F  T  G  A  T  I  F  E   | E  Y  A  R  K  A  L  D  F  L  W      p.260

          .         .         .         .         .         .       g.36144
 GAAAAAAGACAGCGAAGTAGTAATTTAGTGGGCGTGACTATAAATATTCATACTGGAGAT       c.840
 E  K  R  Q  R  S  S  N  L  V  G  V  T  I  N  I  H  T  G  D         p.280

          .    | 09    .         .         .         .         .    g.38568
 TGGGTACGAAAAG | ATAGTGGAGTTGGAGCAGGGATTGATTCATATTATGAATATCTGTTG    c.900
 W  V  R  K  D |   S  G  V  G  A  G  I  D  S  Y  Y  E  Y  L  L      p.300

          .         .         .         .         .  | 10      .    g.40348
 AAAGCCTATGTCTTGCTTGGAGATGACAGTTTTCTGGAAAGATTTAACACA | CACTATGAT    c.960
 K  A  Y  V  L  L  G  D  D  S  F  L  E  R  F  N  T   | H  Y  D      p.320

          .         .         .         .         .         .       g.40408
 GCCATAATGAGGTATATTAGCCAGCCACCTCTTCTACTTGATGTGCATATCCACAAACCA       c.1020
 A  I  M  R  Y  I  S  Q  P  P  L  L  L  D  V  H  I  H  K  P         p.340

          .         .         .         .         .        | 11.    g.40665
 ATGCTGAATGCTCGGACTTGGATGGATGCTTTGCTTGCCTTCTTCCCAGGCTTGCAG | GTG    c.1080
 M  L  N  A  R  T  W  M  D  A  L  L  A  F  F  P  G  L  Q   | V      p.360

          .         .         .         .         .         .       g.40725
 TTAAAGGGGGATATTAGACCTGCTATTGAAACTCATGAAATGTTATATCAGGTGATTAAA       c.1140
 L  K  G  D  I  R  P  A  I  E  T  H  E  M  L  Y  Q  V  I  K         p.380

          .         .  | 12      .         .         .         .    g.42323
 AAACACAATTTTCTACCAGAG | GCATTTACCACAGATTTCAGAGTACACTGGGCTCAACAT    c.1200
 K  H  N  F  L  P  E   | A  F  T  T  D  F  R  V  H  W  A  Q  H      p.400

          .         .         .         .      | 13  .         .    g.42910
 CCTTTAAGGCCAGAATTTGCAGAAAGTACCTACTTCTTATATAAA | GCTACAGGAGATCCT    c.1260
 P  L  R  P  E  F  A  E  S  T  Y  F  L  Y  K   | A  T  G  D  P      p.420

          .         .         .         .         .         .       g.42970
 TACTACCTTGAAGTAGGGAAGACACTTATTGAAAATTTAAATAAATATGCTAGAGTGCCT       c.1320
 Y  Y  L  E  V  G  K  T  L  I  E  N  L  N  K  Y  A  R  V  P         p.440

          .         .         .         .         . | 14       .    g.47319
 TGCGGATTTGCTGCCATGAAGGATGTTCGTACTGGAAGTCATGAGGACAG | AATGGATTCT    c.1380
 C  G  F  A  A  M  K  D  V  R  T  G  S  H  E  D  R  |  M  D  S      p.460

          .         .         .         .         .         .       g.47379
 TTCTTCTTGGCTGAAATGTTTAAATATCTTTACCTGTTATTTGCTGATAAAGAAGACATT       c.1440
 F  F  L  A  E  M  F  K  Y  L  Y  L  L  F  A  D  K  E  D  I         p.480

          .         .         .         .         .         .       g.47439
 ATTTTTGACATAGAAGATTACATCTTTACAACAGAAGCTCATCTGTTACCTCTTTGGCTC       c.1500
 I  F  D  I  E  D  Y  I  F  T  T  E  A  H  L  L  P  L  W  L         p.500

          .         .         .       | 15 .         .         .    g.48054
 TCTACTACAAATCAAAGCATCTCTAAAAAGAACACA | ACCTCGGAATATACAGAACTGGAT    c.1560
 S  T  T  N  Q  S  I  S  K  K  N  T   | T  S  E  Y  T  E  L  D      p.520

          .         .         .         .         .         .       g.48114
 GACAGTAACTTCGATTGGACTTGTCCAAATACTCAGATCCTCTTTCCTAATGACCCATTG       c.1620
 D  S  N  F  D  W  T  C  P  N  T  Q  I  L  F  P  N  D  P  L         p.540

          .         .         .         .         .         .       g.48174
 TATGCTCAAAGTATTCGTGAGCCCTTGAAAAATGTGGTGGATAAGAGCTGTCCTAGAGGC       c.1680
 Y  A  Q  S  I  R  E  P  L  K  N  V  V  D  K  S  C  P  R  G         p.560

          .  | 16      .         .         .         .         .    g.49409
 ATCATCAGAGT | AGAGGAGAGTTTCAGGAGTGGAGCTAAACCCCCTCTGAGAGCCAGAGAT    c.1740
 I  I  R  V  |  E  E  S  F  R  S  G  A  K  P  P  L  R  A  R  D      p.580

          .         .         .         .         .         .       g.49469
 TTCATGGCCACTAACCCTGAGCATTTAGAAATCCTGAAGAAGATGGGGGTGAGTTTGATT       c.1800
 F  M  A  T  N  P  E  H  L  E  I  L  K  K  M  G  V  S  L  I         p.600

          .         .         .         .      | 17  .         .    g.51578
 CACCTCAAAGATGGGAGAGTCCAGTTGGTCCAACATGCAATCCAA | GCTGCTAGTTCAATC    c.1860
 H  L  K  D  G  R  V  Q  L  V  Q  H  A  I  Q   | A  A  S  S  I      p.620

          .         .         .         .         .         .       g.51638
 GACGCTGAAGATGGGTTGAGGTTCATGCAGGAGATGATTGAATTGTCAAGTCAGCAACAA       c.1920
 D  A  E  D  G  L  R  F  M  Q  E  M  I  E  L  S  S  Q  Q  Q         p.640

          .         .         .         .         .         .       g.51698
 AAAGAACAGCAGCTGCCTCCACGAGCTGTACAAATTGTTTCCCACCCATTTTTTGGCAGG       c.1980
 K  E  Q  Q  L  P  P  R  A  V  Q  I  V  S  H  P  F  F  G  R         p.660

          .         .         .         .         .        | 18.    g.53102
 GTAGTATTGACTGCTGGACCAGCTCAGTTTGGGCTGGATCTGTCTAAACATAAAGAG | ACA    c.2040
 V  V  L  T  A  G  P  A  Q  F  G  L  D  L  S  K  H  K  E   | T      p.680

          .         .         .         .         .         .       g.53162
 AGAGGATTTGTTGCAAGCAGTAAACCATCCAATGGTTGTTCAGAGCTTACTAACCCAGAG       c.2100
 R  G  F  V  A  S  S  K  P  S  N  G  C  S  E  L  T  N  P  E         p.700

          .         .         .         .         .         .       g.53222
 GCAGTGATGGGAAAAATCGCACTGATACAAAGAGGACAGTGCATGTTTGCAGAAAAGGCA       c.2160
 A  V  M  G  K  I  A  L  I  Q  R  G  Q  C  M  F  A  E  K  A         p.720

          .         .         .         .    | 19    .         .    g.56928
 CGCAACATCCAGAATGCTGGAGCCATTGGTGGCATTGTTATTG | ATGACAATGAGGGGAGC    c.2220
 R  N  I  Q  N  A  G  A  I  G  G  I  V  I  D |   D  N  E  G  S      p.740

          .         .         .         .         .         .       g.56988
 AGCAGTGATACTGCCCCTCTGTTCCAGATGGCAGGTGATGGAAAGGATACAGATGACATC       c.2280
 S  S  D  T  A  P  L  F  Q  M  A  G  D  G  K  D  T  D  D  I         p.760

          .         .         .         .         .         .       g.57048
 AAGATCCCCATGCTGTTCTTATTCAGCAAAGAAGGAAGTATCATACTGGATGCCATCCGG       c.2340
 K  I  P  M  L  F  L  F  S  K  E  G  S  I  I  L  D  A  I  R         p.780

          .         .         .         .          | 20        .    g.65446
 GAATATGAGGAGGTAGAAGTGCTCCTCTCTGATAAAGCAAAAGATCGAG | ATCCTGAAATG    c.2400
 E  Y  E  E  V  E  V  L  L  S  D  K  A  K  D  R  D |   P  E  M      p.800

          .         .         .         .         .         .       g.65506
 GAAAATGAAGAACAACCATCCTCTGAAAATGATTCTCAGAATCAGAGTGGTGAACAGATT       c.2460
 E  N  E  E  Q  P  S  S  E  N  D  S  Q  N  Q  S  G  E  Q  I         p.820

          .         .         .         .         .         .       g.65566
 TCATCAAGTTCTCAGGAGGTTGATTTGGTTGATCAAGAGTCTTCTGAGGAAAATTCTCTA       c.2520
 S  S  S  S  Q  E  V  D  L  V  D  Q  E  S  S  E  E  N  S  L         p.840

          .         .         .         .         .         .       g.65626
 AATTCTCACCCAGAATCATTATCTCTAGCAGATATGGACAATGCTGCAAGCATTTCCCCT       c.2580
 N  S  H  P  E  S  L  S  L  A  D  M  D  N  A  A  S  I  S  P         p.860

          .         .         .         .         .         .       g.65686
 TCTGAACAGACTTCTAATCCCACAGAAAACCATGAGACTACAAATCTTAATGGTGAATGT       c.2640
 S  E  Q  T  S  N  P  T  E  N  H  E  T  T  N  L  N  G  E  C         p.880

          .         .         .         .         .         .       g.65746
 ACAGATTTAGATAACCAGCTTCAAGAACAATCAGAAACTGAGGAAGATTCCAATCCTAAT       c.2700
 T  D  L  D  N  Q  L  Q  E  Q  S  E  T  E  E  D  S  N  P  N         p.900

          .         .         .         .         .         .       g.65806
 GTTAGCTGGGGTAAAAAGGTCCAGCCTATAGACTCCATATTAGCAGACTGGAATGAAGAT       c.2760
 V  S  W  G  K  K  V  Q  P  I  D  S  I  L  A  D  W  N  E  D         p.920

          .         .         .                                     g.65845
 ATAGAAGCATTTGAAATGATGGAGAAGGATGAGCTATGA                            c.2799
 I  E  A  F  E  M  M  E  K  D  E  L  X                              p.932

          .         .         .         .         .         .       g.65905
 cttgctaaacaatctgttggtaggtatttaaaaagaaaaggtaaactgtgtgtggttaat       c.*60

          .         .         .         .         .         .       g.65965
 agacatcctaatactaagcaggctttctaatgggaggctttaagtatggtgatgaacaac       c.*120

          .         .         .         .         .         .       g.66025
 cacgttctgactggcgtagttatcgtaggaatctggagcatgctgtgttagaattgacct       c.*180

          .         .         .         .         .         .       g.66085
 tgtttaaaactgtcccatcaaaaatggaaatccacagttcccccttcaaatgcagcactg       c.*240

          .         .         .         .         .         .       g.66145
 caccaccctgcaacacctcaggccagggaaagattactgagcattcctgcgaaccagatt       c.*300

          .         .         .         .         .         .       g.66205
 tctgttgtctctggatagacaagaaacaaaattcatttagtagtggagtggggaatagga       c.*360

          .         .         .         .         .         .       g.66265
 gtttggatagccttctaattaaaggaagctcgcctttcttggttttgggggttagaggct       c.*420

          .         .         .         .         .         .       g.66325
 cttttgggaagatgcatccgagtattgtggcattctgattatgctgccttcacaaaacac       c.*480

          .         .         .         .         .         .       g.66385
 tctaagtgacctaagtggttatgaagcaaatgcatttatggtgaaaacagtctttgctca       c.*540

          .         .         .         .         .         .       g.66445
 ttgctttctcttgtttcatttagtgacaaatgatcaagatgacttgattttttttccttc       c.*600

          .         .         .         .         .         .       g.66505
 ttaacaatgtcttttttatttaaaccaaaggtgaagccagtgtactttctcagtgagttc       c.*660

          .         .         .         .         .         .       g.66565
 tctgcataaagactaatcagtgggaccaggtaaaaaggtcatataatacattgtggagat       c.*720

          .         .         .         .         .         .       g.66625
 tgcttacttaatacttctgaaaaatggagtaagggagaaactgtaatgttgcaatatgaa       c.*780

          .         .         .         .         .         .       g.66685
 cctcccattgggccttccatagggaaagctgtgactactctgaaatggaacctagcatta       c.*840

          .         .         .         .         .         .       g.66745
 tatccttgtagggtagattataaatcatttccagttcatttctcttagaggtgattacct       c.*900

          .         .         .         .         .         .       g.66805
 ctagccatcagccttactccatcccatgtttggtatgcaatttgagccacaaggctcgta       c.*960

          .         .         .         .         .         .       g.66865
 tcgccaacagctatatacattttgttccatttttctgtcttacagagccatgatagaact       c.*1020

          .         .         .         .         .         .       g.66925
 gtggttagtgagttaaaattcctggagtaactactgtttttctcctttgaaacttaggtt       c.*1080

          .         .         .         .         .         .       g.66985
 tctaaagttgcacctaaggaatctgtcacattttctgttgaatcatggtttttgtttttg       c.*1140

          .         .         .         .         .         .       g.67045
 tttttaacagatattccttctgatacggacttgaaaattagtgtatggtgacctgtgttt       c.*1200

          .         .         .         .         .         .       g.67105
 aaaaaaaaaagtacaatacaactacatatagctatatagcttaatgagacttccaccccc       c.*1260

          .         .         .         .         .         .       g.67165
 cccctttttttttttggtttgttgttgttgtagtagtctggtgctggccacatttaagtc       c.*1320

          .         .         .         .         .         .       g.67225
 ttaaaaatttttaaattttgttgttgatgtttgtagacagccctgttgttgaaatcatgg       c.*1380

          .         .         .         .         .         .       g.67285
 ctttattcattttatttattttttaaacttgcctgaatttgttctaaaggaatatttaag       c.*1440

          .         .         .         .         .         .       g.67345
 agacataattttcttctctttaccataacattacacaaaactttttcctaaaacacggtt       c.*1500

          .         .         .         .         .         .       g.67405
 gtgaggtactgatgaggtgtaagtggagctgttaaaaacagcagtgctgtattgcagtta       c.*1560

          .         .         .         .         .         .       g.67465
 tgtatattcgtgtacagtatgtttagatcccaggtaaacatattcttttctgagaggata       c.*1620

          .         .         .         .         .         .       g.67525
 aatacctgcattcagatattccaggtaaatataattgagtcagggagtagtaaatctgat       c.*1680

          .         .         .         .         .         .       g.67585
 ggagaattcactttggggaggggaaaaagaatagtatgcaagacccttattggcttttaa       c.*1740

          .         .         .         .         .         .       g.67645
 ttatacctgaaaccaaaatggatatttttagtctctctgcatgtgagatttggtgtaaca       c.*1800

          .         .         .         .         .         .       g.67705
 agatagaactataatatatacagtatatggaaggatagatatagtgctttgttcatttta       c.*1860

          .         .         .         .         .         .       g.67765
 attgcaaagctgccaaaatagttgaagcttaattacttgacttgccttgatttataggac       c.*1920

          .         .         .         .         .         .       g.67825
 tggggcttggagaaaatgagcagatgttcctctaagacatcgattacagaagccttatat       c.*1980

          .         .         .         .         .         .       g.67885
 acatggatttgattttgtatttgtagctgaaagtcactgttgtctaaaactaacttttct       c.*2040

          .         .         .         .         .         .       g.67945
 aagttatcaaaacaacctaatttcttttccaacaaggagaacttaatggcatgaaggatt       c.*2100

          .         .         .         .         .         .       g.68005
 gtgtgacacattggaaaagccagcttactgccactctcttcctttggccattagagggag       c.*2160

          .         .         .         .         .         .       g.68065
 gtgttgcctttcattgacgcttagaagcaaattgttcacttgttaagaaaagtaaatcct       c.*2220

          .         .         .         .         .         .       g.68125
 taaaaaaagaaaaggaaaaaatttaaccaatttttcttaatacccagaaggaattatact       c.*2280

          .         .         .         .         .         .       g.68185
 caatatttccctagttaagaaaagaggagataatgttcgtctaaaaaactccaacgttgt       c.*2340

          .         .         .         .         .         .       g.68245
 aattacaactctacattcatttacttacttgacatactgccacaaagtagtttttgagtt       c.*2400

          .         .         .         .         .         .       g.68305
 cattaaaaattccaaaggcattagttgttttttttttttttagtgttttgttttttagtt       c.*2460

          .         .         .         .         .         .       g.68365
 aacttttatagacattttagtaacttgctaaagattcaggggattctatgaaaccccgaa       c.*2520

          .         .         .         .         .         .       g.68425
 tttagaaacatctggtctacctcagttaaatgttgactgcttagaaatatagctgaagtg       c.*2580

          .         .         .         .         .         .       g.68485
 atcaccacagccataaaattgtttaagaaagatttatataatgtttacaaatctggaatc       c.*2640

          .         .         .         .         .         .       g.68545
 aaggattttagctgaaatcctttaagagatattagagcaagtatttaattcaggtatttt       c.*2700

          .         .         .         .         .         .       g.68605
 caagttttaaaacttaacctgtttacctactaaaaataaaatagctagtttttttctgca       c.*2760

          .         .         .         .         .         .       g.68665
 tataaaagttcattgaaatgatatgcccttatttgcaatacttttcccataaagttttaa       c.*2820

          .         .         .         .         .         .       g.68725
 gtgtgaaagaattgtaatttactagatatgtttggtatgggatattttgttaggcaagtt       c.*2880

          .         .         .         .         .         .       g.68785
 ttcttttttcttcttaaattgcaataggcttccaaaaagagtataattgtttcagaacaa       c.*2940

          .         .         .         .         .         .       g.68845
 attaactcttggcattatacgtctccctttttctttacagtattagtaaaaagaaaaatt       c.*3000

          .         .         .         .         .         .       g.68905
 gtacactttctgattttaacttcactaatgtaattactctctcaagaagcttttaaaatt       c.*3060

          .         .         .         .         .         .       g.68965
 taaattaccatcacacaaccttttttatagtaaagccaacatttgttctctcaccaaacc       c.*3120

          .         .         .         .         .         .       g.69025
 ccatgccaaattcatcatgaagaaagctcagcataagtaattcaaatactgcttataatt       c.*3180

          .         .         .         .         .         .       g.69085
 ttagaggggggtagaatttagtaaatattccagccggtcgttttatgcacaaggcttcag       c.*3240

          .         .         .         .         .         .       g.69145
 tcagaacatagaaaaaaaaaacattctgtgaatgaaatattgtatgttcagattttataa       c.*3300

          .         .         .         .         .         .       g.69205
 aagacatttttaaaagcccaatttacagccgtatattttcttatgatgtaatttatgaaa       c.*3360

          .         .         .         .         .         .       g.69265
 aagatgtctgtactaacaggtgctgtaacactactgttgttggattttattgtttggtga       c.*3420

          .         .         .         .         .         .       g.69325
 taaatgtatacaatatttctaagggaaactatgtactgtgatgtaaaagtctgggcaaaa       c.*3480

          .         .         .         .         .         .       g.69385
 tgtatataatcctgtatataattatgtatttgattataattactgattgtaaagatttaa       c.*3540

          .         .         .                                     g.69417
 taaaatatgtaaatattccagtttagttttaa                                   c.*3572

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The ER degradation enhancer, mannosidase alpha-like 3 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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