v-erb-b2 erythroblastic leukemia viral oncogene homolog 2, neuro/glioblastoma derived oncogene homolog (avian) (ERBB2) - coding DNA reference sequence

(used for variant description)

(last modified July 19, 2016)


This file was created to facilitate the description of sequence variants on transcript NM_001005862.1 in the ERBB2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_007503.1, covering ERBB2 transcript NM_001005862.1.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5040
                     gttcccggatttttgtgggcgcctgccccgcccctcgtcc       c.-481

 .         .         .         .         .         .                g.5100
 ccctgctgtgtccatatatcgaggcgatagggttaagggaaggcggacgcctgatgggtt       c.-421

 .         .         .         .         | 02         .             g.5577
 aatgagcaaactgaagtgttttccatgatcttttttgag | tcgcaattgaagtaccacctc    c.-361

 .         .         .         .         .         .                g.5637
 ccgagggtgattgcttccccatgcggggtagaacctttgctgtcctgttcaccactctac       c.-301

 .         .         .    | 03    .         .         .             g.10157
 ctccagcacagaatttggcttatg | cctactcaatgtgaagatgatgaggatgaaaacctt    c.-241

 .         .         .         | 04         .         .             g.11879
 tgtgatgatccacttccacttaatgaatg | gtggcaaagcaaagctatattcaagaccaca    c.-181

 .         .         .         .         .         .                g.11939
 tgcaaagctactccctgagcaaagagtcacagataaaacgggggcaccagtagaatggcc       c.-121

 .         .         .         .         .         .                g.11999
 aggacaaacgcagtgcagcacagagactcagaccctggcagccatgcctgcgcaggcagt       c.-61

 .         .         .         .         .   | 05     .             g.23867
 gatgagagtgacatgtactgttgtggacatgcacaaaagtgag | tgtgcaccggcacagac    c.-1

          .         .         .         .         .         .       g.23927
 ATGAAGCTGCGGCTCCCTGCCAGTCCCGAGACCCACCTGGACATGCTCCGCCACCTCTAC       c.60
 M  K  L  R  L  P  A  S  P  E  T  H  L  D  M  L  R  H  L  Y         p.20

          .         .         .         .         .         .       g.23987
 CAGGGCTGCCAGGTGGTGCAGGGAAACCTGGAACTCACCTACCTGCCCACCAATGCCAGC       c.120
 Q  G  C  Q  V  V  Q  G  N  L  E  L  T  Y  L  P  T  N  A  S         p.40

          .      | 06  .         .         .         .         .    g.25226
 CTGTCCTTCCTGCAG | GATATCCAGGAGGTGCAGGGCTACGTGCTCATCGCTCACAACCAA    c.180
 L  S  F  L  Q   | D  I  Q  E  V  Q  G  Y  V  L  I  A  H  N  Q      p.60

          .         .         .         .         .         .       g.25286
 GTGAGGCAGGTCCCACTGCAGAGGCTGCGGATTGTGCGAGGCACCCAGCTCTTTGAGGAC       c.240
 V  R  Q  V  P  L  Q  R  L  R  I  V  R  G  T  Q  L  F  E  D         p.80

          .         .         .         .         .         .       g.25346
 AACTATGCCCTGGCCGTGCTAGACAATGGAGACCCGCTGAACAATACCACCCCTGTCACA       c.300
 N  Y  A  L  A  V  L  D  N  G  D  P  L  N  N  T  T  P  V  T         p.100

          .         .         .         .          | 07        .    g.26189
 GGGGCCTCCCCAGGAGGCCTGCGGGAGCTGCAGCTTCGAAGCCTCACAG | AGATCTTGAAA    c.360
 G  A  S  P  G  G  L  R  E  L  Q  L  R  S  L  T  E |   I  L  K      p.120

          .         .         .         .         .         .       g.26249
 GGAGGGGTCTTGATCCAGCGGAACCCCCAGCTCTGCTACCAGGACACGATTTTGTGGAAG       c.420
 G  G  V  L  I  Q  R  N  P  Q  L  C  Y  Q  D  T  I  L  W  K         p.140

          .         .         .         .         .         .       g.26309
 GACATCTTCCACAAGAACAACCAGCTGGCTCTCACACTGATAGACACCAACCGCTCTCGG       c.480
 D  I  F  H  K  N  N  Q  L  A  L  T  L  I  D  T  N  R  S  R         p.160

      | 08   .         .         .         .         .         .    g.26729
 GCCT | GCCACCCCTGTTCTCCGATGTGTAAGGGCTCCCGCTGCTGGGGAGAGAGTTCTGAG    c.540
 A  C |   H  P  C  S  P  M  C  K  G  S  R  C  W  G  E  S  S  E      p.180

          .    | 09    .         .         .         .         .    g.26993
 GATTGTCAGAGCC | TGACGCGCACTGTCTGTGCCGGTGGCTGTGCCCGCTGCAAGGGGCCA    c.600
 D  C  Q  S  L |   T  R  T  V  C  A  G  G  C  A  R  C  K  G  P      p.200

          .         .         .         .         .         .       g.27053
 CTGCCCACTGACTGCTGCCATGAGCAGTGTGCTGCCGGCTGCACGGGCCCCAAGCACTCT       c.660
 L  P  T  D  C  C  H  E  Q  C  A  A  G  C  T  G  P  K  H  S         p.220

           | 10        .         .         .         .         .    g.27251
 GACTGCCTG | GCCTGCCTCCACTTCAACCACAGTGGCATCTGTGAGCTGCACTGCCCAGCC    c.720
 D  C  L   | A  C  L  H  F  N  H  S  G  I  C  E  L  H  C  P  A      p.240

          .         .         .         .         .         .       g.27311
 CTGGTCACCTACAACACAGACACGTTTGAGTCCATGCCCAATCCCGAGGGCCGGTATACA       c.780
 L  V  T  Y  N  T  D  T  F  E  S  M  P  N  P  E  G  R  Y  T         p.260

          .         .         .  | 11      .         .         .    g.28817
 TTCGGCGCCAGCTGTGTGACTGCCTGTCCCT | ACAACTACCTTTCTACGGACGTGGGATCC    c.840
 F  G  A  S  C  V  T  A  C  P  Y |   N  Y  L  S  T  D  V  G  S      p.280

          .         .         .         .         .         .       g.28877
 TGCACCCTCGTCTGCCCCCTGCACAACCAAGAGGTGACAGCAGAGGATGGAACACAGCGG       c.900
 C  T  L  V  C  P  L  H  N  Q  E  V  T  A  E  D  G  T  Q  R         p.300

          .         .         .  | 12      .         .         .    g.29211
 TGTGAGAAGTGCAGCAAGCCCTGTGCCCGAG | TGTGCTATGGTCTGGGCATGGAGCACTTG    c.960
 C  E  K  C  S  K  P  C  A  R  V |   C  Y  G  L  G  M  E  H  L      p.320

          .         .         .         .         .         .       g.29271
 CGAGAGGTGAGGGCAGTTACCAGTGCCAATATCCAGGAGTTTGCTGGCTGCAAGAAGATC       c.1020
 R  E  V  R  A  V  T  S  A  N  I  Q  E  F  A  G  C  K  K  I         p.340

          .         .         .         | 13         .         .    g.32168
 TTTGGGAGCCTGGCATTTCTGCCGGAGAGCTTTGATGG | GGACCCAGCCTCCAACACTGCC    c.1080
 F  G  S  L  A  F  L  P  E  S  F  D  G  |  D  P  A  S  N  T  A      p.360

          .         .         .         .         .   | 14     .    g.32314
 CCGCTCCAGCCAGAGCAGCTCCAAGTGTTTGAGACTCTGGAAGAGATCACAG | GTTACCTA    c.1140
 P  L  Q  P  E  Q  L  Q  V  F  E  T  L  E  E  I  T  G |   Y  L      p.380

          .         .         .         .         .         .       g.32374
 TACATCTCAGCATGGCCGGACAGCCTGCCTGACCTCAGCGTCTTCCAGAACCTGCAAGTA       c.1200
 Y  I  S  A  W  P  D  S  L  P  D  L  S  V  F  Q  N  L  Q  V         p.400

          .         .    | 15    .         .         .         .    g.32637
 ATCCGGGGACGAATTCTGCACAA | TGGCGCCTACTCGCTGACCCTGCAAGGGCTGGGCATC    c.1260
 I  R  G  R  I  L  H  N  |  G  A  Y  S  L  T  L  Q  G  L  G  I      p.420

          .         .         .         .         .         .       g.32697
 AGCTGGCTGGGGCTGCGCTCACTGAGGGAACTGGGCAGTGGACTGGCCCTCATCCACCAT       c.1320
 S  W  L  G  L  R  S  L  R  E  L  G  S  G  L  A  L  I  H  H         p.440

          .         .         .         .         .         .       g.32757
 AACACCCACCTCTGCTTCGTGCACACGGTGCCCTGGGACCAGCTCTTTCGGAACCCGCAC       c.1380
 N  T  H  L  C  F  V  H  T  V  P  W  D  Q  L  F  R  N  P  H         p.460

          .         .         .         .    | 16    .         .    g.33178
 CAAGCTCTGCTCCACACTGCCAACCGGCCAGAGGACGAGTGTG | TGGGCGAGGGCCTGGCC    c.1440
 Q  A  L  L  H  T  A  N  R  P  E  D  E  C  V |   G  E  G  L  A      p.480

          .         .         .         .         .         .       g.33238
 TGCCACCAGCTGTGCGCCCGAGGGCACTGCTGGGGTCCAGGGCCCACCCAGTGTGTCAAC       c.1500
 C  H  Q  L  C  A  R  G  H  C  W  G  P  G  P  T  Q  C  V  N         p.500

          .         .         .         .         .       | 17 .    g.33379
 TGCAGCCAGTTCCTTCGGGGCCAGGAGTGCGTGGAGGAATGCCGAGTACTGCAGGG | GCTC    c.1560
 C  S  Q  F  L  R  G  Q  E  C  V  E  E  C  R  V  L  Q  G  |  L      p.520

          .         .         .         .         .         .       g.33439
 CCCAGGGAGTATGTGAATGCCAGGCACTGTTTGCCGTGCCACCCTGAGTGTCAGCCCCAG       c.1620
 P  R  E  Y  V  N  A  R  H  C  L  P  C  H  P  E  C  Q  P  Q         p.540

          .         .        | 18.         .         .         .    g.34213
 AATGGCTCAGTGACCTGTTTTGGACCG | GAGGCTGACCAGTGTGTGGCCTGTGCCCACTAT    c.1680
 N  G  S  V  T  C  F  G  P   | E  A  D  Q  C  V  A  C  A  H  Y      p.560

          .         .         .         .         .         .       g.34273
 AAGGACCCTCCCTTCTGCGTGGCCCGCTGCCCCAGCGGTGTGAAACCTGACCTCTCCTAC       c.1740
 K  D  P  P  F  C  V  A  R  C  P  S  G  V  K  P  D  L  S  Y         p.580

          .         .         .         .         .         .       g.34333
 ATGCCCATCTGGAAGTTTCCAGATGAGGAGGGCGCATGCCAGCCTTGCCCCATCAACTGC       c.1800
 M  P  I  W  K  F  P  D  E  E  G  A  C  Q  P  C  P  I  N  C         p.600

          | 19         .         .         .         .       | 20 . g.40183
 ACCCACTC | CTGTGTGGACCTGGATGACAAGGGCTGCCCCGCCGAGCAGAGAGCCAG | CCCT c.1860
 T  H  S  |  C  V  D  L  D  D  K  G  C  P  A  E  Q  R  A  S  |  P   p.620

          .         .         .         .         .         .       g.40243
 CTGACGTCCATCATCTCTGCGGTGGTTGGCATTCTGCTGGTCGTGGTCTTGGGGGTGGTC       c.1920
 L  T  S  I  I  S  A  V  V  G  I  L  L  V  V  V  L  G  V  V         p.640

          .         .         .         .         .         .       g.40303
 TTTGGGATCCTCATCAAGCGACGGCAGCAGAAGATCCGGAAGTACACGATGCGGAGACTG       c.1980
 F  G  I  L  I  K  R  R  Q  Q  K  I  R  K  Y  T  M  R  R  L         p.660

          .      | 21  .         .         .         .         .    g.40443
 CTGCAGGAAACGGAG | CTGGTGGAGCCGCTGACACCTAGCGGAGCGATGCCCAACCAGGCG    c.2040
 L  Q  E  T  E   | L  V  E  P  L  T  P  S  G  A  M  P  N  Q  A      p.680

          .         .         .         .         .         .       g.40503
 CAGATGCGGATCCTGAAAGAGACGGAGCTGAGGAAGGTGAAGGTGCTTGGATCTGGCGCT       c.2100
 Q  M  R  I  L  K  E  T  E  L  R  K  V  K  V  L  G  S  G  A         p.700

          .         | 22         .         .         .         .    g.40814
 TTTGGCACAGTCTACAAG | GGCATCTGGATCCCTGATGGGGAGAATGTGAAAATTCCAGTG    c.2160
 F  G  T  V  Y  K   | G  I  W  I  P  D  G  E  N  V  K  I  P  V      p.720

          .         .         .         .         .        | 23.    g.41589
 GCCATCAAAGTGTTGAGGGAAAACACATCCCCCAAAGCCAACAAAGAAATCTTAGAC | GAA    c.2220
 A  I  K  V  L  R  E  N  T  S  P  K  A  N  K  E  I  L  D   | E      p.740

          .         .         .         .         .         .       g.41649
 GCATACGTGATGGCTGGTGTGGGCTCCCCATATGTCTCCCGCCTTCTGGGCATCTGCCTG       c.2280
 A  Y  V  M  A  G  V  G  S  P  Y  V  S  R  L  L  G  I  C  L         p.760

          .         .         .         .         .         .       g.41709
 ACATCCACGGTGCAGCTGGTGACACAGCTTATGCCCTATGGCTGCCTCTTAGACCATGTC       c.2340
 T  S  T  V  Q  L  V  T  Q  L  M  P  Y  G  C  L  L  D  H  V         p.780

          .         .         .         .         .         .       g.41769
 CGGGAAAACCGCGGACGCCTGGGCTCCCAGGACCTGCTGAACTGGTGTATGCAGATTGCC       c.2400
 R  E  N  R  G  R  L  G  S  Q  D  L  L  N  W  C  M  Q  I  A         p.800

     | 24    .         .         .         .         .         .    g.41966
 AAG | GGGATGAGCTACCTGGAGGATGTGCGGCTCGTACACAGGGACTTGGCCGCTCGGAAC    c.2460
 K   | G  M  S  Y  L  E  D  V  R  L  V  H  R  D  L  A  A  R  N      p.820

          .         .         .         .         .         .       g.42026
 GTGCTGGTCAAGAGTCCCAACCATGTCAAAATTACAGACTTCGGGCTGGCTCGGCTGCTG       c.2520
 V  L  V  K  S  P  N  H  V  K  I  T  D  F  G  L  A  R  L  L         p.840

          .         .         .          | 25        .         .    g.42208
 GACATTGACGAGACAGAGTACCATGCAGATGGGGGCAAG | GTGCCCATCAAGTGGATGGCG    c.2580
 D  I  D  E  T  E  Y  H  A  D  G  G  K   | V  P  I  K  W  M  A      p.860

          .         .         .         .         .      | 26  .    g.42572
 CTGGAGTCCATTCTCCGCCGGCGGTTCACCCACCAGAGTGATGTGTGGAGTTATG | GTGTG    c.2640
 L  E  S  I  L  R  R  R  F  T  H  Q  S  D  V  W  S  Y  G |   V      p.880

          .         .         .         .         .         .       g.42632
 ACTGTGTGGGAGCTGATGACTTTTGGGGCCAAACCTTACGATGGGATCCCAGCCCGGGAG       c.2700
 T  V  W  E  L  M  T  F  G  A  K  P  Y  D  G  I  P  A  R  E         p.900

          .         .         .         .         .         .       g.42692
 ATCCCTGACCTGCTGGAAAAGGGGGAGCGGCTGCCCCAGCCCCCCATCTGCACCATTGAT       c.2760
 I  P  D  L  L  E  K  G  E  R  L  P  Q  P  P  I  C  T  I  D         p.920

          .         .   | 27     .         .         .         .    g.43460
 GTCTACATGATCATGGTCAAAT | GTTGGATGATTGACTCTGAATGTCGGCCAAGATTCCGG    c.2820
 V  Y  M  I  M  V  K  C |   W  M  I  D  S  E  C  R  P  R  F  R      p.940

          .         .         .         .         .         .       g.43520
 GAGTTGGTGTCTGAATTCTCCCGCATGGCCAGGGACCCCCAGCGCTTTGTGGTCATCCAG       c.2880
 E  L  V  S  E  F  S  R  M  A  R  D  P  Q  R  F  V  V  I  Q         p.960

  | 28       .         .         .         .         .         .    g.43735
  | AATGAGGACTTGGGCCCAGCCAGTCCCTTGGACAGCACCTTCTACCGCTCACTGCTGGAG    c.2940
  | N  E  D  L  G  P  A  S  P  L  D  S  T  F  Y  R  S  L  L  E      p.980

          .         .         .         .         .         .       g.43795
 GACGATGACATGGGGGACCTGGTGGATGCTGAGGAGTATCTGGTACCCCAGCAGGGCTTC       c.3000
 D  D  D  M  G  D  L  V  D  A  E  E  Y  L  V  P  Q  Q  G  F         p.1000

          .         .         .         .         .         .       g.43855
 TTCTGTCCAGACCCTGCCCCGGGCGCTGGGGGCATGGTCCACCACAGGCACCGCAGCTCA       c.3060
 F  C  P  D  P  A  P  G  A  G  G  M  V  H  H  R  H  R  S  S         p.1020

           | 29        .         .         .         .         .    g.44206
 TCTACCAGG | AGTGGCGGTGGGGACCTGACACTAGGGCTGGAGCCCTCTGAAGAGGAGGCC    c.3120
 S  T  R   | S  G  G  G  D  L  T  L  G  L  E  P  S  E  E  E  A      p.1040

          .         .         .         .         .         .       g.44266
 CCCAGGTCTCCACTGGCACCCTCCGAAGGGGCTGGCTCCGATGTATTTGATGGTGACCTG       c.3180
 P  R  S  P  L  A  P  S  E  G  A  G  S  D  V  F  D  G  D  L         p.1060

          .         .         .         .         .         .       g.44326
 GGAATGGGGGCAGCCAAGGGGCTGCAAAGCCTCCCCACACATGACCCCAGCCCTCTACAG       c.3240
 G  M  G  A  A  K  G  L  Q  S  L  P  T  H  D  P  S  P  L  Q         p.1080

          .         .         .         .         .         .       g.44386
 CGGTACAGTGAGGACCCCACAGTACCCCTGCCCTCTGAGACTGATGGCTACGTTGCCCCC       c.3300
 R  Y  S  E  D  P  T  V  P  L  P  S  E  T  D  G  Y  V  A  P         p.1100

          .         .   | 30     .         .         .         .    g.44587
 CTGACCTGCAGCCCCCAGCCTG | AATATGTGAACCAGCCAGATGTTCGGCCCCAGCCCCCT    c.3360
 L  T  C  S  P  Q  P  E |   Y  V  N  Q  P  D  V  R  P  Q  P  P      p.1120

          .         .         .         .         .         .       g.44647
 TCGCCCCGAGAGGGCCCTCTGCCTGCTGCCCGACCTGCTGGTGCCACTCTGGAAAGGCCC       c.3420
 S  P  R  E  G  P  L  P  A  A  R  P  A  G  A  T  L  E  R  P         p.1140

          .         .         .         .         .         .       g.44707
 AAGACTCTCTCCCCAGGGAAGAATGGGGTCGTCAAAGACGTTTTTGCCTTTGGGGGTGCC       c.3480
 K  T  L  S  P  G  K  N  G  V  V  K  D  V  F  A  F  G  G  A         p.1160

          .         .         .         .         .         .       g.44767
 GTGGAGAACCCCGAGTACTTGACACCCCAGGGAGGAGCTGCCCCTCAGCCCCACCCTCCT       c.3540
 V  E  N  P  E  Y  L  T  P  Q  G  G  A  A  P  Q  P  H  P  P         p.1180

          .         .         .         .         .         .       g.44827
 CCTGCCTTCAGCCCAGCCTTCGACAACCTCTATTACTGGGACCAGGACCCACCAGAGCGG       c.3600
 P  A  F  S  P  A  F  D  N  L  Y  Y  W  D  Q  D  P  P  E  R         p.1200

          .         .         .         .         .         .       g.44887
 GGGGCTCCACCCAGCACCTTCAAAGGGACACCTACGGCAGAGAACCCAGAGTACCTGGGT       c.3660
 G  A  P  P  S  T  F  K  G  T  P  T  A  E  N  P  E  Y  L  G         p.1220

          .                                                         g.44905
 CTGGACGTGCCAGTGTGA                                                 c.3678
 L  D  V  P  V  X                                                   p.1225

          .         .         .         .         .         .       g.44965
 accagaaggccaagtccgcagaagccctgatgtgtcctcagggagcagggaaggcctgac       c.*60

          .         .         .         .         .         .       g.45025
 ttctgctggcatcaagaggtgggagggccctccgaccacttccaggggaacctgccatgc       c.*120

          .         .         .         .         .         .       g.45085
 caggaacctgtcctaaggaaccttccttcctgcttgagttcccagatggctggaaggggt       c.*180

          .         .         .         .         .         .       g.45145
 ccagcctcgttggaagaggaacagcactggggagtctttgtggattctgaggccctgccc       c.*240

          .         .         .         .         .         .       g.45205
 aatgagactctagggtccagtggatgccacagcccagcttggccctttccttccagatcc       c.*300

          .         .         .         .         .         .       g.45265
 tgggtactgaaagccttagggaagctggcctgagaggggaagcggccctaagggagtgtc       c.*360

          .         .         .         .         .         .       g.45325
 taagaacaaaagcgacccattcagagactgtccctgaaacctagtactgccccccatgag       c.*420

          .         .         .         .         .         .       g.45385
 gaaggaacagcaatggtgtcagtatccaggctttgtacagagtgcttttctgtttagttt       c.*480

          .         .         .         .         .         .       g.45445
 ttactttttttgttttgtttttttaaagatgaaataaagacccagggggagaatgggtgt       c.*540

          .         .         .         .         .         .       g.45505
 tgtatggggaggcaagtgtggggggtccttctccacacccactttgtccatttgcaaata       c.*600

          .                                                         g.45523
 tattttggaaaacagcta                                                 c.*618

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The V-erb-b2 erythroblastic leukemia viral oncogene homolog 2, neuro/glioblastoma derived oncogene homolog (avian) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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