UDP-galactose-4-epimerase (GALE) - coding DNA reference sequence

(used for variant description)

(last modified August 11, 2025)


This file was created to facilitate the description of sequence variants on transcript NM_000403.3 in the GALE gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000001.10, covering GALE transcript NM_000403.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
           .         .         .         .         .                g.5314
       tcattcattgccggcctgaggactcctagctcggccccgctccgcgctacagcc       c.-181

 .         .         .         .         .         .                g.5374
 caaagcccagcctgagacccagccgccctcgtatgcccacggcctagctccccttccctc       c.-121

 .         .         .         .         .    | 02    .             g.6384
 caacagacagactgggaaaaccgagtgggcgacggctgagcaag | gactctccagtcctca    c.-61

 .         .         .         .         .         .     | 03       g.6797
 gtcaccttggacaaagaagtgtggatcctcagattccatcttttccaactccaag | gtgcc    c.-1

          .         .         .         .         .         .       g.6857
 ATGGCAGAGAAGGTGCTGGTAACAGGTGGGGCTGGCTACATTGGCAGCCACACGGTGCTG       c.60
 M  A  E  K  V  L  V  T  G  G  A  G  Y  I  G  S  H  T  V  L         p.20

          .         .         .         .         .         .       g.6917
 GAGCTGCTGGAGGCTGGCTACTTGCCTGTGGTCATCGATAACTTCCATAATGCCTTCCGT       c.120
 E  L  L  E  A  G  Y  L  P  V  V  I  D  N  F  H  N  A  F  R         p.40

   | 04      .         .         .         .         .         .    g.7133
 G | GAGGGGGCTCCCTGCCTGAGAGCCTGCGGCGGGTCCAGGAGCTGACAGGCCGCTCTGTG    c.180
 G |   G  G  S  L  P  E  S  L  R  R  V  Q  E  L  T  G  R  S  V      p.60

          .         .         .         .         .        | 05.    g.7577
 GAGTTTGAGGAGATGGACATTTTGGACCAGGGAGCCCTACAGCGTCTCTTCAAAAAG | TAC    c.240
 E  F  E  E  M  D  I  L  D  Q  G  A  L  Q  R  L  F  K  K   | Y      p.80

          .         .         .         .         .         .       g.7637
 AGCTTTATGGCGGTCATCCACTTTGCGGGGCTCAAGGCCGTGGGCGAGTCGGTGCAGAAG       c.300
 S  F  M  A  V  I  H  F  A  G  L  K  A  V  G  E  S  V  Q  K         p.100

          .         .         .         .         .  | 06      .    g.7942
 CCTCTGGATTATTACAGAGTTAACCTGACCGGGACCATCCAGCTTCTGGAG | ATCATGAAG    c.360
 P  L  D  Y  Y  R  V  N  L  T  G  T  I  Q  L  L  E   | I  M  K      p.120

          .         .         .         .         .         .       g.8002
 GCCCACGGGGTGAAGAACCTGGTGTTCAGCAGCTCAGCCACTGTGTACGGGAACCCCCAG       c.420
 A  H  G  V  K  N  L  V  F  S  S  S  A  T  V  Y  G  N  P  Q         p.140

          .         .         .         .         .         .       g.8062
 TACCTGCCCCTTGATGAGGCCCACCCCACGGGTGGTTGTACCAACCCTTACGGCAAGTCC       c.480
 Y  L  P  L  D  E  A  H  P  T  G  G  C  T  N  P  Y  G  K  S         p.160

          .         .         .         .         | 07         .    g.8669
 AAGTTCTTCATCGAGGAAATGATCCGGGACCTGTGCCAGGCAGACAAG | ACTTGGAACGCA    c.540
 K  F  F  I  E  E  M  I  R  D  L  C  Q  A  D  K   | T  W  N  A      p.180

          .         .         .         .         .         .       g.8729
 GTGCTGCTGCGCTATTTCAACCCCACAGGTGCCCATGCCTCTGGCTGCATTGGTGAGGAT       c.600
 V  L  L  R  Y  F  N  P  T  G  A  H  A  S  G  C  I  G  E  D         p.200

          .         .         .         .   | 08     .         .    g.8880
 CCCCAGGGCATACCCAACAACCTCATGCCTTATGTCTCCCAG | GTGGCGATCGGGCGACGG    c.660
 P  Q  G  I  P  N  N  L  M  P  Y  V  S  Q   | V  A  I  G  R  R      p.220

          .         .         .         .          | 09        .    g.9033
 GAGGCCCTGAATGTCTTTGGCAATGACTATGACACAGAGGATGGCACAG | GTGTCCGGGAT    c.720
 E  A  L  N  V  F  G  N  D  Y  D  T  E  D  G  T  G |   V  R  D      p.240

          .         .         .         .         .         .       g.9093
 TACATCCATGTCGTGGATCTGGCCAAGGGCCACATTGCAGCCTTAAGGAAGCTGAAAGAA       c.780
 Y  I  H  V  V  D  L  A  K  G  H  I  A  A  L  R  K  L  K  E         p.260

          .      | 10  .         .         .         .         .    g.9263
 CAGTGTGGCTGCCGG | ATCTACAACCTGGGCACGGGCACAGGCTATTCAGTGCTGCAGATG    c.840
 Q  C  G  C  R   | I  Y  N  L  G  T  G  T  G  Y  S  V  L  Q  M      p.280

          .         .         .    | 11    .         .         .    g.9566
 GTCCAGGCTATGGAGAAGGCCTCTGGGAAGAAG | ATCCCGTACAAGGTGGTGGCACGGCGG    c.900
 V  Q  A  M  E  K  A  S  G  K  K   | I  P  Y  K  V  V  A  R  R      p.300

          .         .         .         .         .         .       g.9626
 GAAGGTGATGTGGCAGCCTGTTACGCCAACCCCAGCCTGGCCCAAGAGGAGCTGGGGTGG       c.960
 E  G  D  V  A  A  C  Y  A  N  P  S  L  A  Q  E  E  L  G  W         p.320

          .         .         | 12         .         .         .    g.9829
 ACAGCAGCCTTAGGGCTGGACAGGATGT | GTGAGGATCTCTGGCGCTGGCAGAAGCAGAAT    c.1020
 T  A  A  L  G  L  D  R  M  C |   E  D  L  W  R  W  Q  K  Q  N      p.340

          .         .                                               g.9856
 CCTTCAGGCTTTGGCACGCAAGCCTGA                                        c.1047
 P  S  G  F  G  T  Q  A  X                                          p.348

          .         .         .         .         .         .       g.9916
 ggaccctcccctaccaaggaccaggaaaagcagcagctgcctgctctccagcctctggca       c.*60

          .         .         .         .         .         .       g.9976
 ggaactcagggccctggagctgctggggccaagccaaggcctcccctacctcaaacccca       c.*120

          .         .         .         .         .         .       g.10036
 gctgggcccgcttagcccaccaggcatgaggccaagggctccactgaccaggaggccgag       c.*180

          .         .         .         .         .         .       g.10096
 gtctctaactcttatcttccacagggtccaagagttcatcaggacccccaagagtgagtg       c.*240

          .         .         .         .         .         .       g.10156
 agggggcaaggctctggcacaaaacctcctcctcccaggcactcatttatattgctctga       c.*300

          .         .         .         .         .                 g.10206
 aagagctttccaaagtatttaaaaataaaaacaagttttcttacactggg                 c.*350

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The UDP-galactose-4-epimerase protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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