glucokinase (hexokinase 4) (GCK) - coding DNA reference sequence

(used for variant description)

(last modified February 21, 2019)


This file was created to facilitate the description of sequence variants on transcript NM_000162.3 in the GCK gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_008847.1, covering GCK transcript NM_000162.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
           .         .         .         .         .                g.5050
           gagcaggaaatgccgagcggcgcctgagccccagggaagcaggctaggat       c.-421

 .         .         .         .         .         .                g.5110
 gtgagagacacagtcacctgcagcctaattactcaaaagctgtccccaggtcacagaagg       c.-361

 .         .         .         .         .         .                g.5170
 gagaggacatttcccactgaatctgtctgaaggacactaagccccacagctcaacacaac       c.-301

 .         .         .         .         .         .                g.5230
 caggagagaaagcgctgaggacgccacccaagcgcccagcaatggccctgcctggagaac       c.-241

 .         .         .         .         .         .                g.5290
 atccaggctcagtgaggaagggtccagaagggaatgcttgccgactcgttggagaacaat       c.-181

 .         .         .         .         .         .                g.5350
 gaaaaggaggaaactgtgactgaacctcaaaccccaaaccagcccgaggagaaccacatt       c.-121

 .         .         .         .         .         .                g.5410
 ctcccagggacccagggcgggccgtgacccctgcggcggagaagccttggatatttccac       c.-61

 .         .         .         .         .         .                g.5470
 ttcagaagcctactggggaaggctgaggggtcccagctccccacgctggctgctgtgcag       c.-1

          .         .         .         .      | 02  .         .    g.40975
 ATGCTGGACGACAGAGCCAGGATGGAGGCCGCCAAGAAGGAGAAG | GTAGAGCAGATCCTG    c.60
 M  L  D  D  R  A  R  M  E  A  A  K  K  E  K   | V  E  Q  I  L      p.20

          .         .         .         .         .         .       g.41035
 GCAGAGTTCCAGCTGCAGGAGGAGGACCTGAAGAAGGTGATGAGACGGATGCAGAAGGAG       c.120
 A  E  F  Q  L  Q  E  E  D  L  K  K  V  M  R  R  M  Q  K  E         p.40

          .         .         .         .         .         .       g.41095
 ATGGACCGCGGCCTGAGGCTGGAGACCCATGAAGAGGCCAGTGTGAAGATGCTGCCCACC       c.180
 M  D  R  G  L  R  L  E  T  H  E  E  A  S  V  K  M  L  P  T         p.60

          .         .         | 03         .         .         .    g.42030
 TACGTGCGCTCCACCCCAGAAGGCTCAG | AAGTCGGGGACTTCCTCTCCCTGGACCTGGGT    c.240
 Y  V  R  S  T  P  E  G  S  E |   V  G  D  F  L  S  L  D  L  G      p.80

          .         .         .         .         .         .       g.42090
 GGCACTAACTTCAGGGTGATGCTGGTGAAGGTGGGAGAAGGTGAGGAGGGGCAGTGGAGC       c.300
 G  T  N  F  R  V  M  L  V  K  V  G  E  G  E  E  G  Q  W  S         p.100

          .         .         .         .         .         .       g.42150
 GTGAAGACCAAACACCAGATGTACTCCATCCCCGAGGACGCCATGACCGGCACTGCTGAG       c.360
 V  K  T  K  H  Q  M  Y  S  I  P  E  D  A  M  T  G  T  A  E         p.120

     | 04    .         .         .         .         .         .    g.43405
 ATG | CTCTTCGACTACATCTCTGAGTGCATCTCCGACTTCCTGGACAAGCATCAGATGAAA    c.420
 M   | L  F  D  Y  I  S  E  C  I  S  D  F  L  D  K  H  Q  M  K      p.140

          .         .         .         .         .         .       g.43465
 CACAAGAAGCTGCCCCTGGGCTTCACCTTCTCCTTTCCTGTGAGGCACGAAGACATCGAT       c.480
 H  K  K  L  P  L  G  F  T  F  S  F  P  V  R  H  E  D  I  D         p.160

     | 05    .         .         .         .         .         .    g.44416
 AAG | GGCATCCTTCTCAACTGGACCAAGGGCTTCAAGGCCTCAGGAGCAGAAGGGAACAAT    c.540
 K   | G  I  L  L  N  W  T  K  G  F  K  A  S  G  A  E  G  N  N      p.180

          .         .         .          | 06        .         .    g.44585
 GTCGTGGGGCTTCTGCGAGACGCTATCAAACGGAGAGGG | GACTTTGAAATGGATGTGGTG    c.600
 V  V  G  L  L  R  D  A  I  K  R  R  G   | D  F  E  M  D  V  V      p.200

          .         .         .         .         .         .       g.44645
 GCAATGGTGAATGACACGGTGGCCACGATGATCTCCTGCTACTACGAAGACCATCAGTGC       c.660
 A  M  V  N  D  T  V  A  T  M  I  S  C  Y  Y  E  D  H  Q  C         p.220

          .          | 07        .         .         .         .    g.46631
 GAGGTCGGCATGATCGTGG | GCACGGGCTGCAATGCCTGCTACATGGAGGAGATGCAGAAT    c.720
 E  V  G  M  I  V  G |   T  G  C  N  A  C  Y  M  E  E  M  Q  N      p.240

          .         .         .         .         .         .       g.46691
 GTGGAGCTGGTGGAGGGGGACGAGGGCCGCATGTGCGTCAATACCGAGTGGGGCGCCTTC       c.780
 V  E  L  V  E  G  D  E  G  R  M  C  V  N  T  E  W  G  A  F         p.260

          .         .         .         .         .         .       g.46751
 GGGGACTCCGGCGAGCTGGACGAGTTCCTGCTGGAGTATGACCGCCTGGTGGACGAGAGC       c.840
 G  D  S  G  E  L  D  E  F  L  L  E  Y  D  R  L  V  D  E  S         p.280

          .         .    | 08    .         .         .         .    g.47842
 TCTGCAAACCCCGGTCAGCAGCT | GTATGAGAAGCTCATAGGTGGCAAGTACATGGGCGAG    c.900
 S  A  N  P  G  Q  Q  L  |  Y  E  K  L  I  G  G  K  Y  M  G  E      p.300

          .         .         .         .         .         .       g.47902
 CTGGTGCGGCTTGTGCTGCTCAGGCTCGTGGACGAAAACCTGCTCTTCCACGGGGAGGCC       c.960
 L  V  R  L  V  L  L  R  L  V  D  E  N  L  L  F  H  G  E  A         p.320

          .         .         .         .         .          | 09    g.48694
 TCCGAGCAGCTGCGCACACGCGGAGCCTTCGAGACGCGCTTCGTGTCGCAGGTGGAGAG | C    c.1020
 S  E  Q  L  R  T  R  G  A  F  E  T  R  F  V  S  Q  V  E  S  |      p.340

          .         .         .         .         .         .       g.48754
 GACACGGGCGACCGCAAGCAGATCTACAACATCCTGAGCACGCTGGGGCTGCGACCCTCG       c.1080
 D  T  G  D  R  K  Q  I  Y  N  I  L  S  T  L  G  L  R  P  S         p.360

          .         .         .         .         .         .       g.48814
 ACCACCGACTGCGACATCGTGCGCCGCGCCTGCGAGAGCGTGTCTACGCGCGCTGCGCAC       c.1140
 T  T  D  C  D  I  V  R  R  A  C  E  S  V  S  T  R  A  A  H         p.380

          .         .         .         .         .         .       g.48874
 ATGTGCTCGGCGGGGCTGGCGGGCGTCATCAACCGCATGCGCGAGAGCCGCAGCGAGGAC       c.1200
 M  C  S  A  G  L  A  G  V  I  N  R  M  R  E  S  R  S  E  D         p.400

          .         .         .         .         .    | 10    .    g.49150
 GTAATGCGCATCACTGTGGGCGTGGATGGCTCCGTGTACAAGCTGCACCCCAG | CTTCAAG    c.1260
 V  M  R  I  T  V  G  V  D  G  S  V  Y  K  L  H  P  S  |  F  K      p.420

          .         .         .         .         .         .       g.49210
 GAGCGGTTCCATGCCAGCGTGCGCAGGCTGACGCCCAGCTGCGAGATCACCTTCATCGAG       c.1320
 E  R  F  H  A  S  V  R  R  L  T  P  S  C  E  I  T  F  I  E         p.440

          .         .         .         .         .         .       g.49270
 TCGGAGGAGGGCAGTGGCCGGGGCGCGGCCCTGGTCTCGGCGGTGGCCTGTAAGAAGGCC       c.1380
 S  E  E  G  S  G  R  G  A  A  L  V  S  A  V  A  C  K  K  A         p.460

          .                                                         g.49288
 TGTATGCTGGGCCAGTGA                                                 c.1398
 C  M  L  G  Q  X                                                   p.465

          .         .         .         .         .         .       g.49348
 gagcagtggccgcaagcgcagggaggatgccacagccccacagcacccaggctccatggg       c.*60

          .         .         .         .         .         .       g.49408
 gaagtgctccccacacgtgctcgcagcctggcggggcaggaggcctggccttgtcaggac       c.*120

          .         .         .         .         .         .       g.49468
 ccaggccgcctgccataccgctggggaacagagcgggcctcttccctcagtttttcggtg       c.*180

          .         .         .         .         .         .       g.49528
 ggacagccccagggccctaacgggggtgcggcaggagcaggaacagagactctggaagcc       c.*240

          .         .         .         .         .         .       g.49588
 ccccacctttctcgctggaatcaatttcccagaagggagttgctcactcaggactttgat       c.*300

          .         .         .         .         .         .       g.49648
 gcatttccacactgtcagagctgttggcctcgcctgggcccaggctctgggaaggggtgc       c.*360

          .         .         .         .         .         .       g.49708
 cctctggatcctgctgtggcctcacttccctgggaactcatcctgtgtggggaggcagct       c.*420

          .         .         .         .         .         .       g.49768
 ccaacagcttgaccagacctagacctgggccaaaagggcagccaggggctgctcatcacc       c.*480

          .         .         .         .         .         .       g.49828
 cagtcctggccattttcttgcctgaggctcaagaggcccagggagcaatgggagggggct       c.*540

          .         .         .         .         .         .       g.49888
 ccatggaggaggtgtcccaagctttgaatacccccagagaccttttctctcccataccat       c.*600

          .         .         .         .         .         .       g.49948
 cactgagtggcttgtgattctgggatggaccctcgcagcaggtgcaagagacagagcccc       c.*660

          .         .         .         .         .         .       g.50008
 caagcctctgccccaaggggcccacaaaggggagaagggccagccctacatcttcagctc       c.*720

          .         .         .         .         .         .       g.50068
 ccatagcgctggctcaggaagaaaccccaagcagcattcagcacaccccaagggacaacc       c.*780

          .         .         .         .         .         .       g.50128
 ccatcatatgacatgccaccctctccatgcccaacctaagattgtgtgggttttttaatt       c.*840

          .         .                                               g.50153
 aaaaatgttaaaagttttaaacatg                                          c.*865

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Glucokinase (hexokinase 4) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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