glucosaminyl (N-acetyl) transferase 2, I-branching enzyme (I blood group) (GCNT2) - coding DNA reference sequence

(used for variant description)

(last modified October 13, 2013)


This file was created to facilitate the description of sequence variants on transcript NM_145649.4 in the GCNT2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_007469.2, covering GCNT2 transcript NM_145649.4.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                   .                g.5011
                                                  aaactgcgttt       c.-541

 .         .         .         .         .         .                g.5071
 accttaaacaggcttactgtgttcactgctggacgcctctgggcaatcttaccctcctgg       c.-481

 .         .  | 02      .         .         .         .             g.11187
 gaactgagagag | acaatgctaggagccagaaacatgaggaatacatgagctcggcgccaa    c.-421

 .         .         .         .         .         .                g.11247
 tggaacatgctttcacaccgggtgcagctaaccaccacatcatacaaaactcgtcgctga       c.-361

 .         .         .         .         .         .                g.11307
 cgttttagatgtataatctgattggcatggactcacagaggagggagtaagggaagagta       c.-301

 .         .         | 03         .         .         .             g.12337
 agaagatttcaaaggagag | acacaggttgcaggttagcaggagaacaggcaagccaaatg    c.-241

 .         .         .         .         .         .                g.12397
 caaaggagccacttcagaaatgtgtcacagaaaagtgaaaatgcaacctagtggtaagtg       c.-181

 .         .         .         .         .         .                g.12457
 aagaggggaagaagaaagaaaaaggaccagaaccgtgaactgaagggacagggaacagcc       c.-121

 .         .         .         .         .         .                g.12517
 agacgagagcttcagccatcacgaggatgatttcggaacctggagaaaatgtaagttaaa       c.-61

 .         .         .         .         .         .                g.12577
 tatatctacactctgatcctatctcaagagagagatattttactcatttcctggttgtga       c.-1

          .         .         .         .         .         .       g.12637
 ATGATGGGCTCTTGGAAGCACTGTCTTTTTAGCGCGTCTCTTATCTCTGCCCTGATTTTT       c.60
 M  M  G  S  W  K  H  C  L  F  S  A  S  L  I  S  A  L  I  F         p.20

          .         .         .         .         .         .       g.12697
 GTATTTGTTTACAATACTGAGTTATGGGAGAATAAACGTTTTCTGAGGGCAGCTCTGTCC       c.120
 V  F  V  Y  N  T  E  L  W  E  N  K  R  F  L  R  A  A  L  S         p.40

          .         .         .         .         .         .       g.12757
 AATGCTTCACTGTTAGCAGAAGCCTGTCATCAGATTTTTGAGGGGAAAGTTTTTTACCCA       c.180
 N  A  S  L  L  A  E  A  C  H  Q  I  F  E  G  K  V  F  Y  P         p.60

          .         .         .         .         .         .       g.12817
 ACAGAAAATGCATTGAAAACTACCCTTGATGAAGCTACCTGCTATGAGTACATGGTTCGA       c.240
 T  E  N  A  L  K  T  T  L  D  E  A  T  C  Y  E  Y  M  V  R         p.80

          .         .         .         .         .         .       g.12877
 AGCCACTATGTAACAGAAACACTCTCTGAAGAAGAGGCTGGGTTCCCTTTAGCTTACACA       c.300
 S  H  Y  V  T  E  T  L  S  E  E  E  A  G  F  P  L  A  Y  T         p.100

          .         .         .         .         .         .       g.12937
 GTGACCATCCACAAAGACTTCGGCACTTTTGAGAGGCTCTTCAGGGCGATTTATATGCCC       c.360
 V  T  I  H  K  D  F  G  T  F  E  R  L  F  R  A  I  Y  M  P         p.120

          .         .         .         .         .         .       g.12997
 CAAAATGTCTACTGTGTGCACCTGGATCAGAAGGCGACGGATGCCTTTAAAGGTGCAGTG       c.420
 Q  N  V  Y  C  V  H  L  D  Q  K  A  T  D  A  F  K  G  A  V         p.140

          .         .         .         .         .         .       g.13057
 AAACAGTTACTCAGCTGCTTCCCAAATGCTTTTCTGGCTTCCAAGAAGGAGTCGGTTGTC       c.480
 K  Q  L  L  S  C  F  P  N  A  F  L  A  S  K  K  E  S  V  V         p.160

          .         .         .         .         .         .       g.13117
 TATGGGGGGATCTCCAGGCTCCAGGCTGACCTGAACTGCCTGGAAGACCTTGTGGCCTCT       c.540
 Y  G  G  I  S  R  L  Q  A  D  L  N  C  L  E  D  L  V  A  S         p.180

          .         .         .         .         .         .       g.13177
 GAAGTTCCCTGGAAGTATGTCATCAACACCTGCGGGCAAGACTTTCCCCTGAAAACCAAC       c.600
 E  V  P  W  K  Y  V  I  N  T  C  G  Q  D  F  P  L  K  T  N         p.200

          .         .         .         .         .         .       g.13237
 AGGGAAATAGTTCAGTATCTGAAGGGATTTAAAGGGAAAAATATCACCCCCGGAGTGCTG       c.660
 R  E  I  V  Q  Y  L  K  G  F  K  G  K  N  I  T  P  G  V  L         p.220

          .         .         .         .         .         .       g.13297
 CCTCCTGACCACGCTGTTGGACGGACTAAATACGTCCACCAAGAACTGTTAAACCACAAA       c.720
 P  P  D  H  A  V  G  R  T  K  Y  V  H  Q  E  L  L  N  H  K         p.240

          .         .         .         .         .         .       g.13357
 AATTCCTACGTGATTAAAACAACAAAATTAAAAACTCCTCCTCCTCATGACATGGTGATT       c.780
 N  S  Y  V  I  K  T  T  K  L  K  T  P  P  P  H  D  M  V  I         p.260

          .         .         .         .         .         .       g.13417
 TACTTTGGCACGGCCTACGTGGCTCTCACAAGGGACTTTGCTAACTTCGTCCTCCAAGAC       c.840
 Y  F  G  T  A  Y  V  A  L  T  R  D  F  A  N  F  V  L  Q  D         p.280

          .         .         .         .         .         .       g.13477
 CAGCTCGCACTTGACTTACTCTCCTGGTCCAAGGACACCTACAGCCCCGACGAACATTTC       c.900
 Q  L  A  L  D  L  L  S  W  S  K  D  T  Y  S  P  D  E  H  F         p.300

          .         .      | 04  .         .         .         .    g.105051
 TGGGTGACACTCAACAGGATTCCCG | GTGTTCCTGGCTCTATGCCAAATGCATCCTGGACT    c.960
 W  V  T  L  N  R  I  P  G |   V  P  G  S  M  P  N  A  S  W  T      p.320

          .         .         .         .         .         | 05    g.110084
 GGAAACCTCAGAGCTATAAAGTGGAGTGACATGGAAGACAGACACGGAGGCTGCCACG | GC    c.1020
 G  N  L  R  A  I  K  W  S  D  M  E  D  R  H  G  G  C  H  G |       p.340

          .         .         .         .         .         .       g.110144
 CACTATGTACATGGTATTTGTATCTATGGAAACGGAGACTTAAAGTGGCTGGTTAATTCA       c.1080
 H  Y  V  H  G  I  C  I  Y  G  N  G  D  L  K  W  L  V  N  S         p.360

          .         .         .         .         .         .       g.110204
 CCAAGCCTGTTTGCTAACAAGTTTGAGCTTAATACCTACCCCCTTACTGTGGAATGCCTA       c.1140
 P  S  L  F  A  N  K  F  E  L  N  T  Y  P  L  T  V  E  C  L         p.380

          .         .         .         .         .         .       g.110264
 GAACTGAGGCATCGCGAAAGAACCCTCAATCAGAGTGAAACTGCGATACAACCCAGCTGG       c.1200
 E  L  R  H  R  E  R  T  L  N  Q  S  E  T  A  I  Q  P  S  W         p.400

                                                                    g.110273
 TATTTTTGA                                                          c.1209
 Y  F  X                                                            p.402

          .         .         .         .         .         .       g.110333
 gctattcatgagctactcatgactgaagggaaactgcagctgggaagaggagcctgtttt       c.*60

          .         .         .         .         .         .       g.110393
 tgtgagagacttttgccttcgtaatgttaaccgtttcaggaccacgtttatagcttcagg       c.*120

          .         .         .         .         .         .       g.110453
 acctggctacgtaattatacttaaaatatccactggacactgtgaaatacactaacagga       c.*180

          .         .         .         .         .         .       g.110513
 tggctgggtagagcaatctgggcactttggccaattttagtcttgctgtttcttgatgct       c.*240

          .         .         .         .         .         .       g.110573
 cacctctatattagtttattgttaggatcaatgataaatttaaatgacctcagatctttg       c.*300

          .         .         .         .         .         .       g.110633
 caccagatactcatcatatacaaatgttttagtaaaaaagagaattgtagataatactgt       c.*360

          .         .         .         .         .         .       g.110693
 ctaggaaaataagaattaggtttctttgaagaaggaatcttttataacaccttaacagtc       c.*420

          .         .         .         .         .         .       g.110753
 accactgtgctcaaccagacagatagtgaaacagctttctgggtaattcaccaatttcct       c.*480

          .         .         .         .         .         .       g.110813
 ttaaaacataagctacctgaatggagaatacatcttgtttctgagtttcaacactagcat       c.*540

          .         .         .         .         .         .       g.110873
 ttttggcttactcatggacaaagttctgtatatagtataaagtcattaacaagaaacagg       c.*600

          .         .         .         .         .         .       g.110933
 atatgctttaagacagaattcactgtctgttgcttcagtaaaaggacctcggggaataaa       c.*660

          .         .         .         .         .         .       g.110993
 acatttctctcttatatgccagaatgtaggctggtccctatgtcatgtcttccattaaga       c.*720

          .         .         .         .         .         .       g.111053
 acactaaaaagtccttgcaagaatggagatatgcattcaagagaggtgctatcacataga       c.*780

          .         .         .         .         .         .       g.111113
 tctagtctgaagtctggaacactttcctcttctatgacccctctctccccagtattatct       c.*840

          .         .         .         .         .         .       g.111173
 tacttgcaaaatggagaccaaattctatcctgtgaggcttttaattgcaccatagtatgc       c.*900

          .         .         .         .         .         .       g.111233
 tctgagtagctttacactgcctggtactgatagtagtggctcgatttttaagagccttca       c.*960

          .         .         .         .         .         .       g.111293
 attgtagatgaacatctctgttatttatccctcattcatccatccgttcattcattcagc       c.*1020

          .         .         .         .         .         .       g.111353
 cttcaatcaacatctcttgagtgtctattatgtacaggacatgtactgagacaaaaagga       c.*1080

          .         .         .         .         .         .       g.111413
 aacataagagctttttcactctaaaaatcttggcaataatgtcaacaccagaaagcctcc       c.*1140

          .         .         .         .         .         .       g.111473
 tctggagaatcttacagagtgattgtagtttaatacaggaacacacagggctgtgtagca       c.*1200

          .         .         .         .         .         .       g.111533
 tgataccaggcccaggagatcagtaattacaaattaagggttaaatcagagattattcaa       c.*1260

          .         .         .         .         .         .       g.111593
 cagagagggagaaaggaggagacagagggaggacctgttgtgttccagccattctggtat       c.*1320

          .         .         .         .         .         .       g.111653
 tcctttatgtatctaatttcattcaaacctcacaacagtcttgtgaggcccttatataat       c.*1380

          .         .         .         .         .         .       g.111713
 tactcccattttgcagatgaagtaactgaggcttagaaaggttaatagcaccggggaaca       c.*1440

          .         .         .         .         .         .       g.111773
 atttctctgggtgagaattgggactctgttgctggtcttctcagttcatttcctgaggtg       c.*1500

          .         .         .         .         .         .       g.111833
 gatttactgagagaaggtgaaataaagccatatttagtataccagagaaggtagatttta       c.*1560

          .         .         .         .         .         .       g.111893
 agaatggtctcagtgttaatactgagaaaaagtcctgtcagttcagaaaaaatgtgaagt       c.*1620

          .         .         .         .         .         .       g.111953
 ctactttagtattcctgtaatactaaaccgttgagtttctaaatatttatttattctaac       c.*1680

          .         .         .         .         .         .       g.112013
 aaaaagcaattactacaaatggatgacacatttaatgaacacaattttattttttttctg       c.*1740

          .         .         .         .         .         .       g.112073
 taactgtgcttgttgaatgtcaatcatatttaaagggaatgactttgaagtaaaaccttt       c.*1800

          .         .         .         .         .         .       g.112133
 tttcttgctactgaaaaaaatggagttgttttgggtggtaaagtgttaaggaatagggac       c.*1860

          .         .         .         .         .         .       g.112193
 agctggtcacacaaggaactcttgaaggccacatgtgaaaacctgtcacttgcacagagg       c.*1920

          .         .         .         .         .         .       g.112253
 ccagtcccactaaggtgaccagagtgggctccaagcacaaactgccattggctatagatg       c.*1980

          .         .         .         .         .         .       g.112313
 ggactgtgtccccccaaaattcatgtgttggagccttaaccctcaatgtgatggtatttg       c.*2040

          .         .         .         .         .         .       g.112373
 agatggggcctttggtaagggaagtttagatgaggtcacgagggtaggaccctcatgatg       c.*2100

          .         .         .         .         .         .       g.112433
 ggatgagtccccttacaagacctctggcttgggccgggcgtggtggctcacacctgtaat       c.*2160

          .         .         .         .         .         .       g.112493
 cccaacactttgggaggccaaggcaggtagatcacttgatgccaggagttccagaccagg       c.*2220

          .         .         .         .         .         .       g.112553
 ctggccgacatggtgaaaccccatctctactaaaaaatataaaaattagccgggctttgt       c.*2280

          .         .         .         .         .         .       g.112613
 ggcatgtgcctgtaatcccagctatttggcaggctgaggcatgagaatcgcttgaaccca       c.*2340

          .         .         .         .         .         .       g.112673
 ggaggtggaggttacagtgagctgagagtgccccactgcactccagcctgggtgacagag       c.*2400

          .         .         .         .         .         .       g.112733
 cgagactttgtcccaaaacaaaataggtgaggggatagcgaatgcactcagggtcagcag       c.*2460

          .         .         .         .         .         .       g.112793
 tggagtttaaaaattgtctcttttcaacttatttaaatgacagcacctgagaagaggaac       c.*2520

          .         .         .         .         .         .       g.112853
 cgttttacactggatgtttctcatgtagaacaagaaatctttctggaattgatgtttaca       c.*2580

          .         .         .         .         .         .       g.112913
 tgtctgttgttggtcatctctcctgtgtcttaaatactttaatgttggaagagcatagtg       c.*2640

          .         .         .         .         .         .       g.112973
 tttgggctagtgggtttctgacagcccatgggaatgccctgaaactactgtatctgatgt       c.*2700

          .         .         .         .         .         .       g.113033
 ttgttttcgatgaggttccatgttttgttttcttgggaataaattaatatattgttttcc       c.*2760

                                                                    g.113034
 a                                                                  c.*2761

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Glucosaminyl (N-acetyl) transferase 2, I-branching enzyme (I blood group) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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