glycerol-3-phosphate dehydrogenase 2 (mitochondrial) (GPD2) - coding DNA reference sequence

(used for variant description)

(last modified May 23, 2018)


This file was created to facilitate the description of sequence variants on transcript NM_000408.4 in the GPD2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_016606.1, covering GPD2 transcript NM_000408.4.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                   .                g.5949
                                               ccccgcgcgcctcg       c.-121

 .         .         .         .         .         .                g.6009
 ctgggagcacccgggccgaggctctgattctggggggaggccgactccaccctggctgga       c.-61

 .         .         .         .         .         .  | 02          g.45653
 ggaactgggtgctcctgcccgctggcccctcgcgcgtgaggatctatctcag | gctaagaa    c.-1

          .         .         .         .         .         .       g.45713
 ATGGCATTTCAAAAGGCAGTGAAAGGGACGATTCTTGTTGGAGGAGGTGCTCTTGCAACT       c.60
 M  A  F  Q  K  A  V  K  G  T  I  L  V  G  G  G  A  L  A  T         p.20

          .         .         .         .   | 03     .         .    g.65609
 GTTTTAGGACTTTCTCAGTTTGCTCATTACAGAAGGAAACAA | ATGAACCTGGCCTATGTT    c.120
 V  L  G  L  S  Q  F  A  H  Y  R  R  K  Q   | M  N  L  A  Y  V      p.40

          .         .         .         .         .         .       g.65669
 AAAGCAGCAGACTGCATTTCAGAACCAGTTAACAGGGAGCCTCCTTCCAGAGAAGCTCAG       c.180
 K  A  A  D  C  I  S  E  P  V  N  R  E  P  P  S  R  E  A  Q         p.60

          .         .         .         .         .         .       g.65729
 CTACTGACTTTGCAAAACACATCTGAATTTGATATCCTTGTTATTGGAGGAGGAGCAACA       c.240
 L  L  T  L  Q  N  T  S  E  F  D  I  L  V  I  G  G  G  A  T         p.80

          .         .         .     | 04   .         .         .    g.80369
 GGAAGTGGCTGTGCGCTAGATGCTGTCACCAGAG | GACTAAAAACAGCCCTTGTAGAAAGA    c.300
 G  S  G  C  A  L  D  A  V  T  R  G |   L  K  T  A  L  V  E  R      p.100

          .         .         .         .         .         .       g.80429
 GATGATTTCTCATCAGGGACCAGCAGCAGAAGCACTAAATTGATCCATGGTGGTGTGAGA       c.360
 D  D  F  S  S  G  T  S  S  R  S  T  K  L  I  H  G  G  V  R         p.120

          .         .         .          | 05        .         .    g.81788
 TATCTGCAGAAGGCCATCATGAAGTTGGATATTGAGCAG | TATAGGATGGTAAAAGAAGCC    c.420
 Y  L  Q  K  A  I  M  K  L  D  I  E  Q   | Y  R  M  V  K  E  A      p.140

          .         .         .         .         .         .       g.81848
 CTTCATGAGCGTGCCAACCTGCTAGAAATTGCTCCCCATTTATCAGCTCCATTGCCTATA       c.480
 L  H  E  R  A  N  L  L  E  I  A  P  H  L  S  A  P  L  P  I         p.160

          .        | 06.         .         .         .         .    g.82923
 ATGCTTCCAGTTTACAA | GTGGTGGCAGTTACCTTACTACTGGGTAGGAATCAAGCTGTAT    c.540
 M  L  P  V  Y  K  |  W  W  Q  L  P  Y  Y  W  V  G  I  K  L  Y      p.180

          .         .         .         .         .         .       g.82983
 GATTTGGTTGCAGGAAGCAATTGCCTAAAAAGCAGTTATGTCCTCAGCAAATCAAGAGCC       c.600
 D  L  V  A  G  S  N  C  L  K  S  S  Y  V  L  S  K  S  R  A         p.200

          .         .         .         .         .         .       g.83043
 CTTGAACATTTCCCAATGCTCCAGAAGGACAAACTGGTAGGAGCAATTGTCTACTATGAC       c.660
 L  E  H  F  P  M  L  Q  K  D  K  L  V  G  A  I  V  Y  Y  D         p.220

   | 07      .         .         .         .         .         .    g.119214
 G | GACAACATAACGATGCACGGATGAACCTTGCCATTGCTCTGACTGCTGCCAGGTATGGG    c.720
 G |   Q  H  N  D  A  R  M  N  L  A  I  A  L  T  A  A  R  Y  G      p.240

          .         .         .         .         .         .       g.119274
 GCTGCCACAGCCAATTACATGGAGGTAGTGAGCTTGCTCAAGAAGACAGACCCCCAGACA       c.780
 A  A  T  A  N  Y  M  E  V  V  S  L  L  K  K  T  D  P  Q  T         p.260

          .         .         .         .       | 08 .         .    g.120163
 GGGAAAGTGCGTGTGAGCGGCGCACGGTGCAAGGATGTCCTCACAG | GGCAGGAATTTGAC    c.840
 G  K  V  R  V  S  G  A  R  C  K  D  V  L  T  G |   Q  E  F  D      p.280

          .         .         .         .         .         .       g.120223
 GTGAGAGCCAAATGTGTTATCAATGCCACGGGACCTTTCACGGACTCTGTGCGCAAAATG       c.900
 V  R  A  K  C  V  I  N  A  T  G  P  F  T  D  S  V  R  K  M         p.300

          .         .         .         .         .         .       g.120283
 GATGATAAAGACGCAGCAGCTATCTGCCAGCCAAGTGCTGGTGTCCATATTGTGATGCCT       c.960
 D  D  K  D  A  A  A  I  C  Q  P  S  A  G  V  H  I  V  M  P         p.320

          .  | 09      .         .         .         .         .    g.126985
 GGTTATTACAG | CCCAGAGAGCATGGGACTTCTTGACCCAGCGACCAGTGATGGGCGAGTT    c.1020
 G  Y  Y  S  |  P  E  S  M  G  L  L  D  P  A  T  S  D  G  R  V      p.340

          .         .         .         .         .         .       g.127045
 ATTTTCTTCTTACCCTGGCAAAAGATGACGATCGCTGGCACTACTGATACTCCAACTGAT       c.1080
 I  F  F  L  P  W  Q  K  M  T  I  A  G  T  T  D  T  P  T  D         p.360

          .         .         .         .         .         .       g.127105
 GTTACACACCATCCAATTCCTTCAGAAGAAGATATCAACTTCATTTTGAATGAAGTGCGT       c.1140
 V  T  H  H  P  I  P  S  E  E  D  I  N  F  I  L  N  E  V  R         p.380

          .         .      | 10  .         .         .         .    g.138407
 AATTACCTGAGTTGTGATGTTGAAG | TGAGAAGAGGGGATGTCCTGGCAGCATGGAGTGGA    c.1200
 N  Y  L  S  C  D  V  E  V |   R  R  G  D  V  L  A  A  W  S  G      p.400

          .         .         .         .         .         .       g.138467
 ATCCGTCCTCTTGTTACAGACCCCAAATCTGCAGATACTCAGTCTATCTCCCGAAATCAT       c.1260
 I  R  P  L  V  T  D  P  K  S  A  D  T  Q  S  I  S  R  N  H         p.420

          .         .         .         . | 11       .         .    g.138930
 GTTGTTGATATCAGTGAGAGTGGCCTTATTACTATAGCAG | GTGGAAAGTGGACAACTTAT    c.1320
 V  V  D  I  S  E  S  G  L  I  T  I  A  G |   G  K  W  T  T  Y      p.440

          .         .         .         .         .         .       g.138990
 CGGTCTATGGCAGAAGATACCATAAATGCTGCTGTCAAAACTCATAATTTAAAAGCAGGA       c.1380
 R  S  M  A  E  D  T  I  N  A  A  V  K  T  H  N  L  K  A  G         p.460

          .         .         .         .         .         .       g.139050
 CCAAGTAGAACAGTTGGGCTTTTCCTTCAAGGGGGTAAAGATTGGAGCCCCACACTCTAC       c.1440
 P  S  R  T  V  G  L  F  L  Q  G  G  K  D  W  S  P  T  L  Y         p.480

          .         .         .       | 12 .         .         .    g.139658
 ATTAGGCTTGTGCAGGATTATGGACTTGAAAGCGAG | GTGGCACAGCATCTTGCCGCCACC    c.1500
 I  R  L  V  Q  D  Y  G  L  E  S  E   | V  A  Q  H  L  A  A  T      p.500

          .         .         .         .         .         .       g.139718
 TATGGTGATAAGGCCTTTGAGGTGGCCAAAATGGCAAGTGTGACTGGCAAAAGGTGGCCT       c.1560
 Y  G  D  K  A  F  E  V  A  K  M  A  S  V  T  G  K  R  W  P         p.520

          .         .         .         .         | 13         .    g.140693
 ATTGTTGGAGTACGTCTTGTGTCAGAATTTCCATATATTGAAGCAGAG | GTGAAATATGGG    c.1620
 I  V  G  V  R  L  V  S  E  F  P  Y  I  E  A  E   | V  K  Y  G      p.540

          .         .         .         .         .         .       g.140753
 ATTAAGGAGTATGCCTGCACTGCTGTGGATATGATTTCACGTCGTACTCGCCTGGCCTTT       c.1680
 I  K  E  Y  A  C  T  A  V  D  M  I  S  R  R  T  R  L  A  F         p.560

          .         .         .         .         .         .       g.140813
 CTAAATGTCCAGGCAGCAGAGGAAGCCCTACCCAGGATTGTTGAACTGATGGGCAGGGAA       c.1740
 L  N  V  Q  A  A  E  E  A  L  P  R  I  V  E  L  M  G  R  E         p.580

          .         .        | 14.         .         .         .    g.148469
 CTGAATTGGGATGATTATAAGAAGCAG | GAACAACTTGAAACAGCCAGGAAGTTTCTATAT    c.1800
 L  N  W  D  D  Y  K  K  Q   | E  Q  L  E  T  A  R  K  F  L  Y      p.600

          .         .         .         .         .         .       g.148529
 TATGAAATGGGCTATAAATCTCGATCAGAACAGTTAACAGATCGCTCTGAAATTAGCCTA       c.1860
 Y  E  M  G  Y  K  S  R  S  E  Q  L  T  D  R  S  E  I  S  L         p.620

          .         . | 15       .         .         .         .    g.148673
 CTGCCTTCAGACATTGACAG | GTATAAGAAGAGATTTCATAAGTTTGATGCAGACCAGAAA    c.1920
 L  P  S  D  I  D  R  |  Y  K  K  R  F  H  K  F  D  A  D  Q  K      p.640

          .         .         .          | 16        .         .    g.149258
 GGCTTTATTACCATTGTTGATGTTCAGCGTGTATTAGAG | AGTATCAATGTCCAAATGGAT    c.1980
 G  F  I  T  I  V  D  V  Q  R  V  L  E   | S  I  N  V  Q  M  D      p.660

          .         .         .         .         .         .       g.149318
 GAAAATACACTCCATGAAATTCTAAATGAAGTTGATTTGAATAAAAATGGACAGGTTGAA       c.2040
 E  N  T  L  H  E  I  L  N  E  V  D  L  N  K  N  G  Q  V  E         p.680

          .         | 17         .         .         .         .    g.152382
 CTCAATGAATTTTTGCAG | CTGATGAGTGCTATTCAAAAAGGAAGGGTATCTGGAAGCCGG    c.2100
 L  N  E  F  L  Q   | L  M  S  A  I  Q  K  G  R  V  S  G  S  R      p.700

          .         .         .         .         .         .       g.152442
 CTTGCTATACTAATGAAAACTGCAGAAGAGAACCTCGACAGAAGAGTTCCAATTCCAGTG       c.2160
 L  A  I  L  M  K  T  A  E  E  N  L  D  R  R  V  P  I  P  V         p.720

          .         .                                               g.152466
 GACCGTAGTTGTGGAGGATTGTGA                                           c.2184
 D  R  S  C  G  G  L  X                                             p.727

          .         .         .         .         .         .       g.152526
 gtctgggcagtaaatccacagccaacaaacatagaaacgacaaatcaccatgtaacaacc       c.*60

          .         .         .         .         .         .       g.152586
 agagatgactgaaaccactctgaaataatgaatgtggatagctgccttttttaacactag       c.*120

          .         .         .         .         .         .       g.152646
 aaaacattccaaaactttaaggtgttggtgtatttgccagctttatttgctgtactttat       c.*180

          .         .         .         .         .         .       g.152706
 ttgtatttgccattcagtctagcttttaagtatatttttttctttttctcattttcaatg       c.*240

          .         .         .         .         .         .       g.152766
 cacattagttttgcatctgttttgtgacctgttagatgtgacacattctctttttgttta       c.*300

          .         .         .         .         .         .       g.152826
 ttcccttattctaaatgagttctaaaaacataatattttggcaaaaattgaaaaaagctg       c.*360

          .         .         .         .         .         .       g.152886
 gagacattttgtgacatgcatacagatagcatgtgttattaaaaagagttgcctattgaa       c.*420

          .         .         .         .         .         .       g.152946
 atgatcatgtttctggagaaattaagcttatagacagcatgtgttattaaaaagagttac       c.*480

          .         .         .         .         .         .       g.153006
 ctattgaaatgatagtgtttctggagatttctcagccccatcttcctccagcttgtctac       c.*540

          .         .         .         .         .         .       g.153066
 cttcctcatgcaaacaatattccacatttttatatctagagcatgactggctaactggag       c.*600

          .         .         .         .         .         .       g.153126
 agggaaggaaaagtttagatctggttactggagcaagtctcaaagagaaactctgaaagc       c.*660

          .         .         .         .         .         .       g.153186
 ttccagaatcacaggtataagataaggatagcattgacatttgctgggagttacagtgat       c.*720

          .         .         .         .         .         .       g.153246
 agtttcatctcagcagttcatttttttcttcagtcactgctggttttctttgactattat       c.*780

          .         .         .         .         .         .       g.153306
 agttgccaggaagatccttgctcttcttactttaaaaccagcatttaagtggcaatttgg       c.*840

          .         .         .         .         .         .       g.153366
 atgtaataggatgagaccaaatttatctaattattacagtagtaatacatttaagagtta       c.*900

          .         .         .         .         .         .       g.153426
 aaaatgtgtttttatatatccacatatgataacaaaagattcaattcccaagcctaaatt       c.*960

          .         .         .         .         .         .       g.153486
 ttgaagcatgtggtattgtcaaatctagcttaccatcttttttgggggtacttgcaacca       c.*1020

          .         .         .         .         .         .       g.153546
 tagtaaaggaagatggaatagactttagttaactttaattataattatatgttaaataag       c.*1080

          .         .         .         .         .         .       g.153606
 gcacataaccagtttccaaggtcatcatggttgcttaaagtctttccccttctgtactcc       c.*1140

          .         .         .         .         .         .       g.153666
 atggaaatattctcagtaaaccaaaaacaaaaatggaaaaataatcaccaacccccatcc       c.*1200

          .         .         .         .         .         .       g.153726
 cgacacacacacagagtccaaagcaaaagtcagtgtgtattgaatttaacaagtaatgca       c.*1260

          .         .         .         .         .         .       g.153786
 gtttgggatgcttttgctacattttggtggcattttaactagttatctgaatatttatta       c.*1320

          .         .         .         .         .         .       g.153846
 atcgtacttcctcttgtaaagttaactacttacttttttgttgttgtttttttaacatca       c.*1380

          .         .         .         .         .         .       g.153906
 ggttctgtatctaataggagatgtaacactttatttcatggcaggtttttattgcagaga       c.*1440

          .         .         .         .         .         .       g.153966
 cttgaagtcttagttttttaaactggcacataaaacactttttgctgttatttttattta       c.*1500

          .         .         .         .         .         .       g.154026
 tgtcaatactgcagagtatctttatgccttattcaagtggattctgagcctgtatgtcac       c.*1560

          .         .         .         .         .         .       g.154086
 aatgtaaacactggaggttcactcacctacgcactcacccaccacctctgaaagaaacag       c.*1620

          .         .         .         .         .         .       g.154146
 aaactgcagagaaagacagcatcttagctcattttgtttttaaatgaggttttagacgct       c.*1680

          .         .         .         .         .         .       g.154206
 tgccacttcctaagggaaatcctaaaacagagcaagtgatgctcccaggtatcactgtga       c.*1740

          .         .         .         .         .         .       g.154266
 acttttttctttcaaagtgtgaatttttacactggctttttcatttttttaaagtaattg       c.*1800

          .         .         .         .         .         .       g.154326
 aagcttgtggctttacaacttagtgttttttgctatccagataacaagtttcattgttta       c.*1860

          .         .         .         .         .         .       g.154386
 gaacccagtgacacttaataggtagataaattgtcctttaaaatatcccagatgatatac       c.*1920

          .         .         .         .         .         .       g.154446
 acaatatggtacatttgtgctctctctctctgtttttctctctttctctttctagttaga       c.*1980

          .         .         .         .         .         .       g.154506
 tcaagataacgatgacttgtaccctccctgattctgttacagtagggcccgggcagatct       c.*2040

          .         .         .         .         .         .       g.154566
 gtgtttgttaaacaggccttgtttgtgcatgctttgctatgaatgaagttcctttaagga       c.*2100

          .         .         .         .         .         .       g.154626
 caaagaaaagcacacttttcttcttttgagcatatctgcttttactttaaatctgctaat       c.*2160

          .         .         .         .         .         .       g.154686
 ttctaaaatgtagagtccttcaccaatcccagagactcaatttggaaatgaactgatttc       c.*2220

          .         .         .         .         .         .       g.154746
 aagccgttactgtgaataaagcaccccagcattttgtataagctcttaattaaacctgta       c.*2280

          .         .         .         .         .         .       g.154806
 cagcttctttacctgatttaagaaagggagacaagcaataggggggaataagcttcttca       c.*2340

          .         .         .         .         .         .       g.154866
 aaattcattccaagcacaaaagaaattttttccctttgcatataaacttgacatcagttg       c.*2400

          .         .         .         .         .         .       g.154926
 attctgttggggtcggggtgggtatgcagggattgccttttattatcaagtgatttattt       c.*2460

          .         .         .         .         .         .       g.154986
 caagagcctttgaggggattcaggtgaaggaacccccatctgtgctggagagttggatac       c.*2520

          .         .         .         .         .         .       g.155046
 tcctttaaatagcccccaccacagtcataacaataatgataatgctggattatttgttaa       c.*2580

          .         .         .         .         .         .       g.155106
 gccaaggttgtctgcctcatatccatcatgctgtttgcaatattcttgctttcaatcaat       c.*2640

          .         .         .         .         .         .       g.155166
 ttatactgagtgtaactttaggatttctgctattaaatgcatgctctctatcctgcttca       c.*2700

          .         .         .         .         .         .       g.155226
 gtttctggctttgctttgtctgtttcaaaatatgtagcttcctcttttgtacaacaaaaa       c.*2760

          .         .         .         .         .         .       g.155286
 actcattctcacttttactaaatatactgtaggagtcatcattgatgttatttttctctt       c.*2820

          .         .         .         .         .         .       g.155346
 atgtatctgtaaagatttttggcatatgaatgtaatattaaagtcaatgatgctataact       c.*2880

          .         .         .         .         .         .       g.155406
 tgcgatgtttgcatcatgtcaacctttttgaaggagtgaaaaagccctactatgttttta       c.*2940

          .         .         .         .         .         .       g.155466
 aatagcaagtgtaagctcagtgctagagtggatatacacaccgcatgttttcatatgtgg       c.*3000

          .         .         .         .         .         .       g.155526
 cacttttatgtatcatgttgggttattgttctagactggactgttaaatactatgtttga       c.*3060

          .         .         .         .         .         .       g.155586
 ggctgggttgtcatttttataactgtcttggtgttttatggccattatttattacttttg       c.*3120

          .         .         .         .         .         .       g.155646
 atacacagaatgagctgcatgcatttatagagcaataagaggatgtatttaatgtgcctt       c.*3180

          .         .         .         .         .         .       g.155706
 gtttttaactgaataagaactggaagcatgaatcaataaaactgattaaaatggtctatt       c.*3240

          .         .         .         .         .         .       g.155766
 tgctagcattttgatgttacttgcagtcagataactttgattactgttgaagtttaaaaa       c.*3300

          .         .         .         .         .         .       g.155826
 aagtttgaaaatatttttacaaactgtgtttttgatgacacaaaagtgaaatatctacag       c.*3360

          .         .         .         .         .         .       g.155886
 agatagatgtaattttataagactgccagaattatttgtattaatttgttgctgtagcct       c.*3420

          .         .         .         .         .         .       g.155946
 ttagggcatgacttctgtatttgtgcaatcctattctacaattacattcatcctattaca       c.*3480

                                                                    g.155951
 actca                                                              c.*3485

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Glycerol-3-phosphate dehydrogenase 2 (mitochondrial) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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