3-hydroxymethyl-3-methylglutaryl-CoA lyase (HMGCL) - coding DNA reference sequence

(used for variant description)

(last modified March 16, 2022)


This file was created to facilitate the description of sequence variants on transcript NM_000191.2 in the HMGCL gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000001.10, covering HMGCL transcript NM_000191.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5044
                 cacgcggggcccagctggactgccgcgggggattctgggccaag       c.-1

          .         .         .         .         .         .       g.5104
 ATGGCAGCAATGAGGAAGGCGCTTCCGCGGCGACTGGTGGGCTTGGCGTCCCTCCGGGCT       c.60
 M  A  A  M  R  K  A  L  P  R  R  L  V  G  L  A  S  L  R  A         p.20

  | 02       .         .         .         .         .         .    g.9926
  | GTCAGCACCTCATCTATGGGCACTTTACCAAAGCGGGTGAAAATTGTGGAAGTTGGTCCC    c.120
  | V  S  T  S  S  M  G  T  L  P  K  R  V  K  I  V  E  V  G  P      p.40

          .         .     | 03   .         .         .         .    g.12912
 CGAGATGGACTACAAAATGAAAAG | AATATCGTATCTACTCCAGTGAAAATCAAGCTGATA    c.180
 R  D  G  L  Q  N  E  K   | N  I  V  S  T  P  V  K  I  K  L  I      p.60

          .         .         .         .         .         .       g.12972
 GACATGCTTTCTGAAGCAGGACTCTCTGTTATAGAAACCACCAGCTTTGTGTCTCCTAAG       c.240
 D  M  L  S  E  A  G  L  S  V  I  E  T  T  S  F  V  S  P  K         p.80

          .   | 04     .         .         .         .         .    g.13737
 TGGGTTCCCCAG | ATGGGTGACCACACTGAAGTCTTGAAGGGCATTCAGAAGTTTCCTGGC    c.300
 W  V  P  Q   | M  G  D  H  T  E  V  L  K  G  I  Q  K  F  P  G      p.100

          .         .         .         .         | 05         .    g.16133
 ATCAACTACCCAGTCCTGACCCCAAATTTGAAAGGCTTCGAGGCAGCG | GTTGCTGCTGGA    c.360
 I  N  Y  P  V  L  T  P  N  L  K  G  F  E  A  A   | V  A  A  G      p.120

          .         .         .         .         .         .       g.16193
 GCCAAGGAAGTAGTCATCTTTGGAGCTGCCTCAGAGCTCTTCACCAAGAAGAACATCAAT       c.420
 A  K  E  V  V  I  F  G  A  A  S  E  L  F  T  K  K  N  I  N         p.140

          .         .         .         .         .         .       g.16253
 TGTTCCATAGAGGAGAGTTTTCAGAGGTTTGACGCAATCCTGAAGGCAGCGCAGTCAGCC       c.480
 C  S  I  E  E  S  F  Q  R  F  D  A  I  L  K  A  A  Q  S  A         p.160

          .        | 06.         .         .         .         .    g.19703
 AATATTTCTGTGCGGGG | GTACGTCTCCTGTGCTCTTGGCTGCCCTTATGAAGGGAAGATC    c.540
 N  I  S  V  R  G  |  Y  V  S  C  A  L  G  C  P  Y  E  G  K  I      p.180

          .         .  | 07      .         .         .         .    g.22175
 TCCCCAGCTAAAGTAGCTGAG | GTCACCAAGAAGTTCTACTCAATGGGCTGCTACGAGATC    c.600
 S  P  A  K  V  A  E   | V  T  K  K  F  Y  S  M  G  C  Y  E  I      p.200

          .         .         .         .         .         .       g.22235
 TCCCTGGGGGACACCATTGGTGTGGGCACCCCAGGGATCATGAAAGACATGCTATCTGCT       c.660
 S  L  G  D  T  I  G  V  G  T  P  G  I  M  K  D  M  L  S  A         p.220

          .         .         .         .         .         .       g.22295
 GTCATGCAGGAAGTGCCTCTGGCTGCCCTGGCTGTCCACTGCCATGACACCTATGGTCAA       c.720
 V  M  Q  E  V  P  L  A  A  L  A  V  H  C  H  D  T  Y  G  Q         p.240

          .         .         . | 08       .         .         .    g.25964
 GCCCTGGCCAACACCTTGATGGCCCTGCAG | ATGGGAGTGAGTGTCGTGGACTCTTCTGTG    c.780
 A  L  A  N  T  L  M  A  L  Q   | M  G  V  S  V  V  D  S  S  V      p.260

          .         .         .         .         .         .       g.26024
 GCAGGACTTGGAGGCTGTCCCTACGCACAGGGGGCATCAGGAAACTTGGCCACAGAAGAC       c.840
 A  G  L  G  G  C  P  Y  A  Q  G  A  S  G  N  L  A  T  E  D         p.280

          .         .         .       | 09 .         .         .    g.27919
 CTGGTCTACATGCTAGAGGGCTTGGGCATTCACACG | GGTGTGAATCTCCAGAAGCTTCTG    c.900
 L  V  Y  M  L  E  G  L  G  I  H  T   | G  V  N  L  Q  K  L  L      p.300

          .         .         .         .         .         .       g.27979
 GAAGCTGGAAACTTTATCTGTCAAGCCCTGAACAGAAAAACTAGCTCCAAAGTGGCTCAG       c.960
 E  A  G  N  F  I  C  Q  A  L  N  R  K  T  S  S  K  V  A  Q         p.320

          .                                                         g.27997
 GCTACCTGTAAACTCTGA                                                 c.978
 A  T  C  K  L  X                                                   p.325

          .         .         .         .         .         .       g.28057
 gccccttgcccacctgaagccctggggatgatgtggaaataggggcacacacagatgatt       c.*60

          .         .         .         .         .         .       g.28117
 catggatggggacatggaaatgagaataggttaaatggtgcaggtacctcatagccagct       c.*120

          .         .         .         .         .         .       g.28177
 ctacacagaggtctctcctggcagaaagcaggcgaagggcaggaggagctgcttggcaga       c.*180

          .         .         .         .         .         .       g.28237
 aggacctcctgcccagacctgaggagtgagaggctttgagggctgaagtctccctttgtt       c.*240

          .         .         .         .         .         .       g.28297
 acggaccctggcccaggagttgaatgcctgaggacgtgtgggaaccccgttccctactta       c.*300

          .         .         .         .         .         .       g.28357
 gcatgatccttgagtctcctctctggatggaatccgcgagctggccacctggccaccctc       c.*360

          .         .         .         .         .         .       g.28417
 tacacggctccaccctgccatggccgtggggcccttgctctctgacttctcaggacacag       c.*420

          .         .         .         .         .         .       g.28477
 gtcatggaggttcttcccaagctggcagaggccatttgtggaaagtggagagctacgtgg       c.*480

          .         .         .         .         .         .       g.28537
 tggccgtctgccaactccagcatctctggaaaatctccacgctgaatgtgatttttgaaa       c.*540

          .         .         .         .                           g.28583
 acagcttatgtaattaaaggttgaatggcacatcataattccagca                     c.*586

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The 3-hydroxymethyl-3-methylglutaryl-CoA lyase protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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