potassium voltage-gated channel, shaker-related subfamily, member 1 (episodic ataxia with myokymia) (KCNA1) - coding DNA reference sequence

(used for variant description)

(last modified January 26, 2018)


This file was created to facilitate the description of sequence variants on transcript NM_000217.2 in the KCNA1 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_011815.1, covering KCNA1 transcript NM_000217.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                         .         .                g.5025
                                    aaatggaccgagcggacccgccgcc       c.-1081

 .         .         .         .         .         .                g.5085
 gcacgcaccctgctccactccaagctcctaagggctcctggcgcgccgcgtagccttggc       c.-1021

 .         .         .         .         .         .                g.5145
 gaggtccgcgctggggtgcggagagcgaagggaactggagagccatgtagatccaggctc       c.-961

 .         .         .         .         .         .                g.5205
 tcgcccgcccgcctccttcgggatcgaatcaagggctcccatagtgttaggagggggcga       c.-901

 .         .         .         .         .         .                g.5265
 gagtgctgtttatcgtcatttgcctcggagcttcgagagagggtggtattttgcttttcc       c.-841

 .         .         .         .         .         .                g.5325
 gccccgcatcctccggaactccctgcaccggagagaggacggcgtctccaggttgctggc       c.-781

 .         .         .         .         .         .                g.5385
 aaccggtgagaatgggggtagggaaggaacattttcgccgtagctgctccgtaaagcgat       c.-721

 .         .         .         .         .         .                g.5445
 tgtccaactgagaggggcgtcggacgagtggaccagggcggcgagtttgcccggcgcgtc       c.-661

 .         .         .         .         .         .                g.5505
 tcggatgctgctgcggcggccgccgcggctcccgccagggcactgcaaagacgacctgcc       c.-601

 .         .         .         .         .         .                g.5565
 gcattcccactcgggctctccgctgactcagcaccgcccctgcgccaagccagccggcca       c.-541

 . | 02       .         .         .         .         .             g.5992
 g | cgtgcatcgatcgccctggtgggagcttagaaggcggcaggcgaagaggggtaggaggg    c.-481

 .         .         .         .         .         .                g.6052
 gggagagccgaggagaagcagagagggtggcaggcgtggggatctgccgagccggcactg       c.-421

 .         .         .         .         .         .                g.6112
 caccgggtcctaggaaggctctcggaggggaggggaggccagggcgacccccgaagcaat       c.-361

 .         .         .         .         .         .                g.6172
 ggcccagtccgctagaacggcactgcgttaaggcacctgggatcaggaagaaatatctaa       c.-301

 .         .         .         .         .         .                g.6232
 acaacaacaacagaaaaccaacaaacccccaaacccaaacccaaccctctgcaaaaagct       c.-241

 .         .         .         .         .         .                g.6292
 gcacccggcccgcaggcgagggggattccaaactgagtgaaaggcagggtggaggggaag       c.-181

 .         .         .         .         .         .                g.6352
 gcagcgagaggcaaagtcgcagatctcccgacctgctcgtgttgaagcacctccccctgg       c.-121

 .         .         .         .         .         .                g.6412
 gcgtgagggagacgcgcgctccggtgggggggccgcttgggtcccccccacccctggtcc       c.-61

 .         .         .         .         .         .                g.6472
 ctggctgcttcccaccccgggctctctcctggcctcccacccccgcgcccggcttccacc       c.-1

          .         .         .         .         .         .       g.6532
 ATGACGGTGATGTCTGGGGAGAACGTGGACGAGGCTTCGGCCGCCCCGGGCCACCCCCAG       c.60
 M  T  V  M  S  G  E  N  V  D  E  A  S  A  A  P  G  H  P  Q         p.20

          .         .         .         .         .         .       g.6592
 GATGGCAGCTACCCCCGGCAGGCCGACCACGACGACCACGAGTGCTGCGAGCGCGTGGTG       c.120
 D  G  S  Y  P  R  Q  A  D  H  D  D  H  E  C  C  E  R  V  V         p.40

          .         .         .         .         .         .       g.6652
 ATCAACATCTCCGGGCTGCGCTTCGAGACGCAGCTCAAGACCCTGGCGCAGTTCCCCAAC       c.180
 I  N  I  S  G  L  R  F  E  T  Q  L  K  T  L  A  Q  F  P  N         p.60

          .         .         .         .         .         .       g.6712
 ACGCTGCTGGGCAACCCTAAGAAACGCATGCGCTACTTCGACCCCCTGAGGAACGAGTAC       c.240
 T  L  L  G  N  P  K  K  R  M  R  Y  F  D  P  L  R  N  E  Y         p.80

          .         .         .         .         .         .       g.6772
 TTCTTCGACCGCAACCGGCCCAGCTTCGACGCCATCCTCTACTACTACCAGTCCGGCGGC       c.300
 F  F  D  R  N  R  P  S  F  D  A  I  L  Y  Y  Y  Q  S  G  G         p.100

          .         .         .         .         .         .       g.6832
 CGCCTGCGGAGGCCGGTCAACGTGCCCCTGGACATGTTCTCCGAGGAGATCAAGTTTTAC       c.360
 R  L  R  R  P  V  N  V  P  L  D  M  F  S  E  E  I  K  F  Y         p.120

          .         .         .         .         .         .       g.6892
 GAGTTGGGCGAGGAGGCCATGGAGAAGTTCCGGGAGGACGAGGGCTTCATCAAGGAGGAG       c.420
 E  L  G  E  E  A  M  E  K  F  R  E  D  E  G  F  I  K  E  E         p.140

          .         .         .         .         .         .       g.6952
 GAGCGCCCTCTGCCCGAGAAGGAGTACCAGCGCCAGGTGTGGCTGCTCTTCGAGTACCCC       c.480
 E  R  P  L  P  E  K  E  Y  Q  R  Q  V  W  L  L  F  E  Y  P         p.160

          .         .         .         .         .         .       g.7012
 GAGAGCTCGGGGCCCGCCAGGGTCATCGCCATCGTCTCCGTCATGGTCATCCTCATCTCC       c.540
 E  S  S  G  P  A  R  V  I  A  I  V  S  V  M  V  I  L  I  S         p.180

          .         .         .         .         .         .       g.7072
 ATCGTCATCTTTTGCCTGGAGACGCTCCCCGAGCTGAAGGATGACAAGGACTTCACGGGC       c.600
 I  V  I  F  C  L  E  T  L  P  E  L  K  D  D  K  D  F  T  G         p.200

          .         .         .         .         .         .       g.7132
 ACCGTCCACCGCATCGACAACACCACGGTCATCTACAATTCCAACATCTTCACAGACCCC       c.660
 T  V  H  R  I  D  N  T  T  V  I  Y  N  S  N  I  F  T  D  P         p.220

          .         .         .         .         .         .       g.7192
 TTCTTCATCGTGGAAACGCTGTGTATCATCTGGTTCTCCTTCGAGCTGGTGGTGCGCTTC       c.720
 F  F  I  V  E  T  L  C  I  I  W  F  S  F  E  L  V  V  R  F         p.240

          .         .         .         .         .         .       g.7252
 TTCGCCTGCCCCAGCAAGACGGACTTCTTCAAAAACATCATGAACTTCATAGACATTGTG       c.780
 F  A  C  P  S  K  T  D  F  F  K  N  I  M  N  F  I  D  I  V         p.260

          .         .         .         .         .         .       g.7312
 GCCATCATTCCTTATTTCATCACGCTGGGCACCGAGATAGCTGAGCAGGAAGGAAACCAG       c.840
 A  I  I  P  Y  F  I  T  L  G  T  E  I  A  E  Q  E  G  N  Q         p.280

          .         .         .         .         .         .       g.7372
 AAGGGCGAGCAGGCCACCTCCCTGGCCATCCTCAGGGTCATCCGCTTGGTAAGGGTTTTT       c.900
 K  G  E  Q  A  T  S  L  A  I  L  R  V  I  R  L  V  R  V  F         p.300

          .         .         .         .         .         .       g.7432
 AGAATCTTCAAGCTCTCCCGCCACTCTAAGGGCCTCCAGATCCTGGGCCAGACCCTCAAA       c.960
 R  I  F  K  L  S  R  H  S  K  G  L  Q  I  L  G  Q  T  L  K         p.320

          .         .         .         .         .         .       g.7492
 GCTAGTATGAGAGAGCTAGGGCTGCTCATCTTTTTCCTCTTCATCGGGGTCATCCTGTTT       c.1020
 A  S  M  R  E  L  G  L  L  I  F  F  L  F  I  G  V  I  L  F         p.340

          .         .         .         .         .         .       g.7552
 TCTAGTGCAGTGTACTTTGCCGAGGCGGAAGAAGCTGAGTCGCACTTCTCCAGTATCCCC       c.1080
 S  S  A  V  Y  F  A  E  A  E  E  A  E  S  H  F  S  S  I  P         p.360

          .         .         .         .         .         .       g.7612
 GATGCTTTCTGGTGGGCGGTGGTGTCCATGACCACTGTAGGATACGGTGACATGTACCCT       c.1140
 D  A  F  W  W  A  V  V  S  M  T  T  V  G  Y  G  D  M  Y  P         p.380

          .         .         .         .         .         .       g.7672
 GTGACAATTGGAGGCAAGATCGTGGGCTCCTTGTGTGCCATCGCTGGTGTGCTAACAATT       c.1200
 V  T  I  G  G  K  I  V  G  S  L  C  A  I  A  G  V  L  T  I         p.400

          .         .         .         .         .         .       g.7732
 GCCCTGCCCGTACCTGTCATTGTGTCCAATTTCAACTATTTCTACCACCGAGAAACTGAG       c.1260
 A  L  P  V  P  V  I  V  S  N  F  N  Y  F  Y  H  R  E  T  E         p.420

          .         .         .         .         .         .       g.7792
 GGGGAAGAGCAGGCTCAGTTGCTCCACGTCAGTTCCCCTAACTTAGCCTCTGACAGTGAC       c.1320
 G  E  E  Q  A  Q  L  L  H  V  S  S  P  N  L  A  S  D  S  D         p.440

          .         .         .         .         .         .       g.7852
 CTCAGTCGCCGCAGTTCCTCTACTATGAGCAAGTCTGAGTACATGGAGATCGAAGAGGAT       c.1380
 L  S  R  R  S  S  S  T  M  S  K  S  E  Y  M  E  I  E  E  D         p.460

          .         .         .         .         .         .       g.7912
 ATGAATAATAGCATAGCCCATTATAGACAGGTCAATATCAGAACTGCCAATTGCACCACT       c.1440
 M  N  N  S  I  A  H  Y  R  Q  V  N  I  R  T  A  N  C  T  T         p.480

          .         .         .         .                           g.7960
 GCTAACCAAAACTGCGTTAATAAGAGCAAGCTACTGACCGATGTTTAA                   c.1488
 A  N  Q  N  C  V  N  K  S  K  L  L  T  D  V  X                     p.495

          .         .         .         .         .         .       g.8020
 aaaacaaaggcaagcaaacaaaaaagccccacttagcagctcaaaagacttaaaaaacaa       c.*60

          .         .         .         .         .         .       g.8080
 aacagaaaacctagtgactcatgtcacgctttgtagatactttactaagtagacttggaa       c.*120

          .         .         .         .         .         .       g.8140
 tgctctatttaactgtcaatgcgttgttgcattgaggattttgggggtggtgaaccagaa       c.*180

          .         .         .         .         .         .       g.8200
 gctttcaagatccatgacaaaataaactattttccttttattaaaaaatgggaaaagaga       c.*240

          .         .         .         .         .         .       g.8260
 gagtattttctaaaactggcttaaaaagattcagtccacgaactagtctaggtaaaataa       c.*300

          .         .         .         .         .         .       g.8320
 taatcatatgcttccccaaactgaaacatttttaatgctttggtttctttaactttttta       c.*360

          .         .         .         .         .         .       g.8380
 aaaactcagaacaagatgatcacttagaaatatgaaattgaaattcgcatgggactccag       c.*420

          .         .         .         .         .         .       g.8440
 taaaacatctttgcaaactgcgtagcacattgaagacagtgcatcagatgtattatatgt       c.*480

          .         .         .         .         .         .       g.8500
 aacatgatagaccagccaaaatggacaatgaatagatatttttatttcgatcaactgaac       c.*540

          .         .         .         .         .         .       g.8560
 tgcatattacaaggtgaaaaaagaaaactccgattacttaagactggttcacaaagcacc       c.*600

          .         .         .         .         .         .       g.8620
 ttataaattggatactggtcctgatctgtagggatttccccctgggcccattctctttct       c.*660

          .         .         .         .         .         .       g.8680
 aatccagattattctctaagaaaaagttaactgaattaaattaattgattcttctgcagt       c.*720

          .         .         .         .         .         .       g.8740
 gccgctaaatggtctcaactgcagatgagccaaatacaggtcttttctcaccaggcctgc       c.*780

          .         .         .         .         .         .       g.8800
 actccgacccctggctttcagaactggatgtaaaaccttagcctccttattgcaagagag       c.*840

          .         .         .         .         .         .       g.8860
 cacaaatgaagttaaatgtaagcatgtttgaatctgatacaatttattttataatcgcat       c.*900

          .         .         .         .         .         .       g.8920
 gctgagaagttaacccagacaataggggataagcttaagttgaaatcgattcttctaaaa       c.*960

          .         .         .         .         .         .       g.8980
 atagatcctttttcatttgcattcaccaaaagtgcactcctccatttattaactatttta       c.*1020

          .         .         .         .         .         .       g.9040
 ttagtaaataaagtactgtatttaagtgcatatgttagtcagatgggaacaataactttt       c.*1080

          .         .         .         .         .         .       g.9100
 tggagctcaaagcatgttctcttattcagcattatggcctatttgactaagatgtacctt       c.*1140

          .         .         .         .         .         .       g.9160
 gaattaattaatgcatgatttcagtaataaaaattttaaaagtaataaaaattacaagtc       c.*1200

          .         .         .         .         .         .       g.9220
 tgtggggtgaaaggcccaatagaaattatggggggtgggggtgggggcactcagtcaatt       c.*1260

          .         .         .         .         .         .       g.9280
 ttcctgcctttgctcagggaaataccaggtttttgtgcaggtataggcggagagaggacc       c.*1320

          .         .         .         .         .         .       g.9340
 aatatgcccatcccttaaagggaagccatgtgaaaaactcaataagtcatcaaagtacat       c.*1380

          .         .         .         .         .         .       g.9400
 atagcaacacctaagaacaagtattctttctagctgaagacaaacacaagcaacacaaac       c.*1440

          .         .         .         .         .         .       g.9460
 aagcaaacaaacaaacaaacaaaaaggtgcaatactgcatgttttttggtgcattcttag       c.*1500

          .         .         .         .         .         .       g.9520
 gatgtaaatgaaaatgtttctctattatatgcatccgaagcagagctgatttttttttct       c.*1560

          .         .         .         .         .         .       g.9580
 ttgcagtcattctttgaagtctgtagagacttcagccctccccttgaggctccctgaaga       c.*1620

          .         .         .         .         .         .       g.9640
 aactaaaccaattgatttaatagttgcttagtgcctttatcctgtacccacagtgaactg       c.*1680

          .         .         .         .         .         .       g.9700
 tagaaagtgcctccttaacacagctgagaagttaggtagcaaaagtggggaagggttggg       c.*1740

          .         .         .         .         .         .       g.9760
 gcacagaccttttgctttttctttttccattctcgctctctcatttcaccactgtgagaa       c.*1800

          .         .         .         .         .         .       g.9820
 gaccacaccaccctaaaccctggagaggagagacccaggagggtgctgtctctctggcca       c.*1860

          .         .         .         .         .         .       g.9880
 tctactagcattggtccctttgacagcctgacgctggatgtgaactgagacccatctttg       c.*1920

          .         .         .         .         .         .       g.9940
 aactggacatgaactgtgaacttgttttttcctctctccaccaaagccaagataaacttt       c.*1980

          .         .         .         .         .         .       g.10000
 ttgggaatttgtttcctatcgagggccactttggacacacaaggcttcctcaggtccagt       c.*2040

          .         .         .         .         .         .       g.10060
 gtagtgctcctggcacctttccttatttttttctctgtcggtaacagcactttgcaaatc       c.*2100

          .         .         .         .         .         .       g.10120
 tctctgacggtccagtcttttcaggcattgttgtggatgtgggaacactcagttcataat       c.*2160

          .         .         .         .         .         .       g.10180
 aacctttcctaggccttccctcctggtctacccctttcagatatttcctgatgcccctat       c.*2220

          .         .         .         .         .         .       g.10240
 gatcttcccacctggcagtcacttcacaggttgaacatctaacttctgctgcccccccgt       c.*2280

          .         .         .         .         .         .       g.10300
 tacccagcccagagaatggtggggaccctgttcctggctgaaagagagccacggaacaca       c.*2340

          .         .         .         .         .         .       g.10360
 ggcctctggagctcggcagctgcccaccggtggagaggtactcacagcctttcaaaggac       c.*2400

          .         .         .         .         .         .       g.10420
 cctgaggtggggaatcttcattctgcacttagcatgtggctgcctgttacctgacattct       c.*2460

          .         .         .         .         .         .       g.10480
 ggcccagcttcttctgaaaatctgtcctgcttctcccacccctttcccccatcctgtcct       c.*2520

          .         .         .         .         .         .       g.10540
 agaactagcagtgaggcaatcaccctagaaactcgagttacacccattctggctaactcg       c.*2580

          .         .         .         .         .         .       g.10600
 attaaaagaaagaacatggatatcttattttcctatgtgacttttgtgaatctgtgagat       c.*2640

          .         .         .         .         .         .       g.10660
 gaacacaacacacatcgtggaagatgaggggccaagaactgcgcagcatccgactacagg       c.*2700

          .         .         .         .         .         .       g.10720
 gcattaaaccctcccatgtgatgtctccttctcgtctgaaccttaactcattctggcgat       c.*2760

          .         .         .         .         .         .       g.10780
 tcctttcctacttgcttaaaaatccccaattaggaaaaaaatgccaacctcctcccaggc       c.*2820

          .         .         .         .         .         .       g.10840
 ttggggttatcttgatctttcatttcaacgttgaggtctagtgcacacagaacttgaaac       c.*2880

          .         .         .         .         .         .       g.10900
 accgcactctgtcaacagcaataatccactcagtactgtgggatggatgggttaatggat       c.*2940

          .         .         .         .         .         .       g.10960
 gagaaaacggcaccaagactgactttgggtatttggtatatttaccgtggttacactctg       c.*3000

          .         .         .         .         .         .       g.11020
 gactggttgattcttctgcatgtgatatagaaaaaagtgctgcatgcggtgaacctgtca       c.*3060

          .         .         .         .         .         .       g.11080
 gtctgggactgggggtgagttgttgttatgagtttggggtggtgtgaggaaagtgaatgc       c.*3120

          .         .         .         .         .         .       g.11140
 tgcttagctcatctgtagctcattgcaatgaattcagtaagaatggagtacagggattat       c.*3180

          .         .         .         .         .         .       g.11200
 ctgtgtagcataggcatgcaatgtttgaccaagctcttaccctcgcactgtaatgtgttg       c.*3240

          .         .         .         .         .         .       g.11260
 aaatgtctttgtagacctgaaggtgcacttaacaaaactgcctattaagggatgactatt       c.*3300

          .         .         .         .         .         .       g.11320
 ttttggtttacttattcatatttattttagcagcctttttaccttttcttccccttccta       c.*3360

          .         .         .         .         .         .       g.11380
 ggcatggagctgtaacagctcatgtcctgactatgtgttttctccagaaggagaagactt       c.*3420

          .         .         .         .         .         .       g.11440
 ctgatgtgctgatagctataattcctctcttccagtctattggggccctagttcaatagg       c.*3480

          .         .         .         .         .         .       g.11500
 gtggcaatagaagagttggtcacaccagggctgttagccatcccagaatctctgaagtgg       c.*3540

          .         .         .         .         .         .       g.11560
 ttaactcacctgaagtgatctgaatcagagagaccaaagacattcatttcctctgtcctc       c.*3600

          .         .         .         .         .         .       g.11620
 agatttctagaagacaaattctagccaggaaaactttctgtttttgcatctcccttttcc       c.*3660

          .         .         .         .         .         .       g.11680
 catttgtgcccaactccccttgcactccctggagacttgagttctgattttcagttatat       c.*3720

          .         .         .         .         .         .       g.11740
 cagctcattgggagtgtgttcgtgggtgagccttgcagaatcagataaaccaatagcaag       c.*3780

          .         .         .         .         .         .       g.11800
 tccttctccaggattctggccagtgggcagtcatttccctgaaatgaattgtagggcagg       c.*3840

          .         .         .         .         .         .       g.11860
 tttagattccactatggtggacgtgaagcacaggtggtgtcacaatcttgatttgcttga       c.*3900

          .         .         .         .         .         .       g.11920
 gaattaaaaaaatacatgtaaatggtaaatgaggaatacatttttttaaagtagaaattt       c.*3960

          .         .         .         .         .         .       g.11980
 ggtttagcctataaaaggccttcttcacattgtgtatagttacacgtttttcaaattagg       c.*4020

          .         .         .         .         .         .       g.12040
 taccatctaaaagtcaataaaaatagtttcctagccctctcatttaatataggagacctc       c.*4080

          .         .         .         .         .         .       g.12100
 aaaacacatgctttttaacaattttacattttaattcttagtttggtagattggattgaa       c.*4140

          .         .         .         .         .         .       g.12160
 agaaaggagaaagaacattagcagaaggcactttcccattttcttccaggaatgacttat       c.*4200

          .         .         .         .         .         .       g.12220
 tcctggggtggtgagaattggtgggtggtaaccatccatagtataaaattgttagaaaga       c.*4260

          .         .         .         .         .         .       g.12280
 atataaactgccaaacaagcatgttatcttcaggcttttccaagcaagaatgaagtcttt       c.*4320

          .         .         .         .         .         .       g.12340
 tgatgtttatgttcattttaagaagacaaacaaactaaaattttaagaccagacacaacc       c.*4380

          .         .         .         .         .         .       g.12400
 caagttgaattgtgatctcaggaggtgaactctcattcaccatgtggcatattactacct       c.*4440

          .         .         .         .         .         .       g.12460
 gtatttatatcatggaatttcagggtatatgtgaacatgtctagtatgactcaggtaaac       c.*4500

          .         .         .         .         .         .       g.12520
 ctttaaagaatgtatgttacttaccatttttgtaaagaagcaaacaggagctgaattgtt       c.*4560

          .         .         .         .         .         .       g.12580
 aaccaaaactgttccattaccttgggtcactgtgcaaactaattcagggtacagatataa       c.*4620

          .         .         .         .         .         .       g.12640
 agtttagaagccttgggattaaatgccagcctctttgctcaggcaaaatgaccctgggct       c.*4680

          .         .         .         .         .         .       g.12700
 ttcttgggaagtccagcatgtatgtaaggggtgaggccctgctgacctcagggcttttcg       c.*4740

          .         .         .         .         .         .       g.12760
 ctttaaggagattaaccctagtcacagtgattttcatttaggagctaactaggagtttac       c.*4800

          .         .         .         .         .         .       g.12820
 tctttatgacgtgaaacttcaaagagtatagaaaacttttgtaccacaatcaaagaagaa       c.*4860

          .         .         .         .         .         .       g.12880
 gaaatggtgtatggaaagaaaacaaaacaaaacaagaaatctcttgtaaaatattccagg       c.*4920

          .         .         .         .         .         .       g.12940
 tcaaagttgtctcctctccaaaccttgcagaagcacctttcttctcttcagcgcactgtt       c.*4980

          .         .         .         .         .         .       g.13000
 ttgggactgtttatgcagcagatgtaagtagacaacatggactccatgtgacatgcctct       c.*5040

          .         .         .         .         .         .       g.13060
 aatagtaaagataaagtattactgaggttaaaaataaaaattgagtagtattaatttaaa       c.*5100

          .         .         .         .         .         .       g.13120
 gtgcaccatcaggacaacaaaccatttaagctgaaaaaacgctattttatttcttgagtt       c.*5160

          .         .         .         .         .         .       g.13180
 tgccagttgcttccaccttgagttaaggacgtgtctcatcttcacctactgcgcattctc       c.*5220

          .         .         .         .         .         .       g.13240
 ccttctctaactgtgtaatatgtcaggtcaaggacattgaatgttatgaattgagaacct       c.*5280

          .         .         .         .         .         .       g.13300
 aattgatgcgcatagttttcatctatgcaattttacttgcttctgtcactttacgatctg       c.*5340

          .         .         .         .         .                 g.13350
 ttcatatttggcatcaattaaagatactttttaaggatcttatcaaggaa                 c.*5390

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Potassium voltage-gated channel, shaker-related subfamily, member 1 (episodic ataxia with myokymia) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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