potassium voltage-gated channel, subfamily H (eag-related), member 2 (KCNH2) - coding DNA reference sequence

(used for variant description)

(last modified June 6, 2014)


This file was created to facilitate the description of sequence variants on transcript NM_000238.3 in the KCNH2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000007.13, covering KCNH2 transcript NM_000238.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5041
                    ccgcggccgggccgagccgcaggcgctgcccgagccgcggg       c.-361

 .         .         .         .         .         .                g.5101
 cgctggagcggctgtcggcgcggtggcaggcgggagccaggagtccggggctcgggcggg       c.-301

 .         .         .         .         .         .                g.5161
 cggagcgcagcgcggggacgcggcggagcgggccccgcggctcggcgggggccggcagac       c.-241

 .         .         .         .         .         .                g.5221
 aggtgtgccggcggcgggcggctcgcgctcaggcggctccaggccgggcccggggtccgg       c.-181

 .         .         .         .         .         .                g.5281
 agcggggagccgggagccgagcgaggacccggcgcccgcagtccagtcttggccgcgccc       c.-121

 .         .         .         .         .         .                g.5341
 gtgctcggcttggccgcggggtgcggggaccacggcccggccgggccacccgaagcctag       c.-61

 .         .         .         .         .         .                g.5401
 tgctgggccgggccgggccggggtgggtgggggcccgcccggcccgcccatgggctcagg       c.-1

          .         .         .         .         .         .       g.5461
 ATGCCGGTGCGGAGGGGCCACGTCGCGCCGCAGAACACCTTCCTGGACACCATCATCCGC       c.60
 M  P  V  R  R  G  H  V  A  P  Q  N  T  F  L  D  T  I  I  R         p.20

          .       | 02 .         .         .         .         .    g.8417
 AAGTTTGAGGGCCAGA | GCCGTAAGTTCATCATCGCCAACGCTCGGGTGGAGAACTGCGCC    c.120
 K  F  E  G  Q  S |   R  K  F  I  I  A  N  A  R  V  E  N  C  A      p.40

          .         .         .         .         .         .       g.8477
 GTCATCTACTGCAACGACGGCTTCTGCGAGCTGTGCGGCTACTCGCGGGCCGAGGTGATG       c.180
 V  I  Y  C  N  D  G  F  C  E  L  C  G  Y  S  R  A  E  V  M         p.60

          .         .         .         .         .         .       g.8537
 CAGCGACCCTGCACCTGCGACTTCCTGCACGGGCCGCGCACGCAGCGCCGCGCTGCCGCG       c.240
 Q  R  P  C  T  C  D  F  L  H  G  P  R  T  Q  R  R  A  A  A         p.80

          .         .         .         .         .         .       g.8597
 CAGATCGCGCAGGCACTGCTGGGCGCCGAGGAGCGCAAAGTGGAAATCGCCTTCTACCGG       c.300
 Q  I  A  Q  A  L  L  G  A  E  E  R  K  V  E  I  A  F  Y  R         p.100

         | 03.         .         .         .         .         .    g.23631
 AAAGATG | GGAGCTGCTTCCTATGTCTGGTGGATGTGGTGCCCGTGAAGAACGAGGATGGG    c.360
 K  D  G |   S  C  F  L  C  L  V  D  V  V  P  V  K  N  E  D  G      p.120

          .         .         .         .         .         .       g.23691
 GCTGTCATCATGTTCATCCTCAATTTCGAGGTGGTGATGGAGAAGGACATGGTGGGGTCC       c.420
 A  V  I  M  F  I  L  N  F  E  V  V  M  E  K  D  M  V  G  S         p.140

          .         .         .         .         .   | 04     .    g.24820
 CCGGCTCATGACACCAACCACCGGGGCCCCCCCACCAGCTGGCTGGCCCCAG | GCCGCGCC    c.480
 P  A  H  D  T  N  H  R  G  P  P  T  S  W  L  A  P  G |   R  A      p.160

          .         .         .         .         .         .       g.24880
 AAGACCTTCCGCCTGAAGCTGCCCGCGCTGCTGGCGCTGACGGCCCGGGAGTCGTCGGTG       c.540
 K  T  F  R  L  K  L  P  A  L  L  A  L  T  A  R  E  S  S  V         p.180

          .         .         .         .         .         .       g.24940
 CGGTCGGGCGGCGCGGGCGGCGCGGGCGCCCCGGGGGCCGTGGTGGTGGACGTGGACCTG       c.600
 R  S  G  G  A  G  G  A  G  A  P  G  A  V  V  V  D  V  D  L         p.200

          .         .         .         .         .         .       g.25000
 ACGCCCGCGGCACCCAGCAGCGAGTCGCTGGCCCTGGACGAAGTGACAGCCATGGACAAC       c.660
 T  P  A  A  P  S  S  E  S  L  A  L  D  E  V  T  A  M  D  N         p.220

          .         .         .         .         .         .       g.25060
 CACGTGGCAGGGCTCGGGCCCGCGGAGGAGCGGCGTGCGCTGGTGGGTCCCGGCTCTCCG       c.720
 H  V  A  G  L  G  P  A  E  E  R  R  A  L  V  G  P  G  S  P         p.240

          .         .         .         .         .         .       g.25120
 CCCCGCAGCGCGCCCGGCCAGCTCCCATCGCCCCGGGCGCACAGCCTCAACCCCGACGCC       c.780
 P  R  S  A  P  G  Q  L  P  S  P  R  A  H  S  L  N  P  D  A         p.260

          .         .         .         .         .         .       g.25180
 TCGGGCTCCAGCTGCAGCCTGGCCCGGACGCGCTCCCGAGAAAGCTGCGCCAGCGTGCGC       c.840
 S  G  S  S  C  S  L  A  R  T  R  S  R  E  S  C  A  S  V  R         p.280

          .         .         .         .         .         .       g.25240
 CGCGCCTCGTCGGCCGACGACATCGAGGCCATGCGCGCCGGGGTGCTGCCCCCGCCACCG       c.900
 R  A  S  S  A  D  D  I  E  A  M  R  A  G  V  L  P  P  P  P         p.300

          .       | 05 .         .         .         .         .    g.25856
 CGCCACGCCAGCACCG | GGGCCATGCACCCACTGCGCAGCGGCTTGCTCAACTCCACCTCG    c.960
 R  H  A  S  T  G |   A  M  H  P  L  R  S  G  L  L  N  S  T  S      p.320

          .         .         .         .         .         .       g.25916
 GACTCCGACCTCGTGCGCTACCGCACCATTAGCAAGATTCCCCAAATCACCCTCAACTTT       c.1020
 D  S  D  L  V  R  Y  R  T  I  S  K  I  P  Q  I  T  L  N  F         p.340

          .         .         .         .         .         .       g.25976
 GTGGACCTCAAGGGCGACCCCTTCTTGGCTTCGCCCACCAGTGACCGTGAGATCATAGCA       c.1080
 V  D  L  K  G  D  P  F  L  A  S  P  T  S  D  R  E  I  I  A         p.360

          .         .         .         .         | 06         .    g.30473
 CCTAAGATAAAGGAGCGAACCCACAATGTCACTGAGAAGGTCACCCAG | GTCCTGTCCCTG    c.1140
 P  K  I  K  E  R  T  H  N  V  T  E  K  V  T  Q   | V  L  S  L      p.380

          .         .         .         .         .         .       g.30533
 GGCGCCGACGTGCTGCCTGAGTACAAGCTGCAGGCACCGCGCATCCACCGCTGGACCATC       c.1200
 G  A  D  V  L  P  E  Y  K  L  Q  A  P  R  I  H  R  W  T  I         p.400

          .         .         .         .         .         .       g.30593
 CTGCATTACAGCCCCTTCAAGGCCGTGTGGGACTGGCTCATCCTGCTGCTGGTCATCTAC       c.1260
 L  H  Y  S  P  F  K  A  V  W  D  W  L  I  L  L  L  V  I  Y         p.420

          .         .         .         .         .         .       g.30653
 ACGGCTGTCTTCACACCCTACTCGGCTGCCTTCCTGCTGAAGGAGACGGAAGAAGGCCCG       c.1320
 T  A  V  F  T  P  Y  S  A  A  F  L  L  K  E  T  E  E  G  P         p.440

          .         .         .         .         .         .       g.30713
 CCTGCTACCGAGTGTGGCTACGCCTGCCAGCCGCTGGCTGTGGTGGACCTCATCGTGGAC       c.1380
 P  A  T  E  C  G  Y  A  C  Q  P  L  A  V  V  D  L  I  V  D         p.460

          .         .         .         .         .         .       g.30773
 ATCATGTTCATTGTGGACATCCTCATCAACTTCCGCACCACCTACGTCAATGCCAACGAG       c.1440
 I  M  F  I  V  D  I  L  I  N  F  R  T  T  Y  V  N  A  N  E         p.480

          .         .         .         .         .         .       g.30833
 GAGGTGGTCAGCCACCCCGGCCGCATCGCCGTCCACTACTTCAAGGGCTGGTTCCTCATC       c.1500
 E  V  V  S  H  P  G  R  I  A  V  H  Y  F  K  G  W  F  L  I         p.500

          .         .         .         .         .        | 07.    g.31482
 GACATGGTGGCCGCCATCCCCTTCGACCTGCTCATCTTCGGCTCTGGCTCTGAGGAG | CTG    c.1560
 D  M  V  A  A  I  P  F  D  L  L  I  F  G  S  G  S  E  E   | L      p.520

          .         .         .         .         .         .       g.31542
 ATCGGGCTGCTGAAGACTGCGCGGCTGCTGCGGCTGGTGCGCGTGGCGCGGAAGCTGGAT       c.1620
 I  G  L  L  K  T  A  R  L  L  R  L  V  R  V  A  R  K  L  D         p.540

          .         .         .         .         .         .       g.31602
 CGCTACTCAGAGTACGGCGCGGCCGTGCTGTTCTTGCTCATGTGCACCTTTGCGCTCATC       c.1680
 R  Y  S  E  Y  G  A  A  V  L  F  L  L  M  C  T  F  A  L  I         p.560

          .         .         .         .         .         .       g.31662
 GCGCACTGGCTAGCCTGCATCTGGTACGCCATCGGCAACATGGAGCAGCCACACATGGAC       c.1740
 A  H  W  L  A  C  I  W  Y  A  I  G  N  M  E  Q  P  H  M  D         p.580

          .         .         .         .         .         .       g.31722
 TCACGCATCGGCTGGCTGCACAACCTGGGCGACCAGATAGGCAAACCCTACAACAGCAGC       c.1800
 S  R  I  G  W  L  H  N  L  G  D  Q  I  G  K  P  Y  N  S  S         p.600

          .         .         .         .         .         .       g.31782
 GGCCTGGGCGGCCCCTCCATCAAGGACAAGTATGTGACGGCGCTCTACTTCACCTTCAGC       c.1860
 G  L  G  G  P  S  I  K  D  K  Y  V  T  A  L  Y  F  T  F  S         p.620

          .         .         .         .         .         .       g.31842
 AGCCTCACCAGTGTGGGCTTCGGCAACGTCTCTCCCAACACCAACTCAGAGAAGATCTTC       c.1920
 S  L  T  S  V  G  F  G  N  V  S  P  N  T  N  S  E  K  I  F         p.640

          .         .      | 08  .         .         .         .    g.32229
 TCCATCTGCGTCATGCTCATTGGCT | CCCTCATGTATGCTAGCATCTTCGGCAACGTGTCG    c.1980
 S  I  C  V  M  L  I  G  S |   L  M  Y  A  S  I  F  G  N  V  S      p.660

          .         .         .         .         .         .       g.32289
 GCCATCATCCAGCGGCTGTACTCGGGCACAGCCCGCTACCACACACAGATGCTGCGGGTG       c.2040
 A  I  I  Q  R  L  Y  S  G  T  A  R  Y  H  T  Q  M  L  R  V         p.680

          .         .         .         .         .         .       g.32349
 CGGGAGTTCATCCGCTTCCACCAGATCCCCAATCCCCTGCGCCAGCGCCTCGAGGAGTAC       c.2100
 R  E  F  I  R  F  H  Q  I  P  N  P  L  R  Q  R  L  E  E  Y         p.700

          .         .         .         .      | 09  .         .    g.32909
 TTCCAGCACGCCTGGTCCTACACCAACGGCATCGACATGAACGCG | GTGCTGAAGGGCTTC    c.2160
 F  Q  H  A  W  S  Y  T  N  G  I  D  M  N  A   | V  L  K  G  F      p.720

          .         .         .         .         .         .       g.32969
 CCTGAGTGCCTGCAGGCTGACATCTGCCTGCACCTGAACCGCTCACTGCTGCAGCACTGC       c.2220
 P  E  C  L  Q  A  D  I  C  L  H  L  N  R  S  L  L  Q  H  C         p.740

          .         .         .         .         .         .       g.33029
 AAACCCTTCCGAGGGGCCACCAAGGGCTGCCTTCGGGCCCTGGCCATGAAGTTCAAGACC       c.2280
 K  P  F  R  G  A  T  K  G  C  L  R  A  L  A  M  K  F  K  T         p.760

          .         .         .         .         .         .       g.33089
 ACACATGCACCGCCAGGGGACACACTGGTGCATGCTGGGGACCTGCTCACCGCCCTGTAC       c.2340
 T  H  A  P  P  G  D  T  L  V  H  A  G  D  L  L  T  A  L  Y         p.780

          .         .         .         .         .         | 10    g.34267
 TTCATCTCCCGGGGCTCCATCGAGATCCTGCGGGGCGACGTCGTCGTGGCCATCCTGG | GG    c.2400
 F  I  S  R  G  S  I  E  I  L  R  G  D  V  V  V  A  I  L  G |       p.800

          .         .         .         .         .         .       g.34327
 AAGAATGACATCTTTGGGGAGCCTCTGAACCTGTATGCAAGGCCTGGCAAGTCGAACGGG       c.2460
 K  N  D  I  F  G  E  P  L  N  L  Y  A  R  P  G  K  S  N  G         p.820

          .         .         .         .         .         .       g.34387
 GATGTGCGGGCCCTCACCTACTGTGACCTACACAAGATCCATCGGGACGACCTGCTGGAG       c.2520
 D  V  R  A  L  T  Y  C  D  L  H  K  I  H  R  D  D  L  L  E         p.840

          .         .         .         .         .         .       g.34447
 GTGCTGGACATGTACCCTGAGTTCTCCGACCACTTCTGGTCCAGCCTGGAGATCACCTTC       c.2580
 V  L  D  M  Y  P  E  F  S  D  H  F  W  S  S  L  E  I  T  F         p.860

          .   | 11     .         .         .         .         .    g.34819
 AACCTGCGAGAT | ACCAACATGATCCCGGGCTCCCCCGGCAGTACGGAGTTAGAGGGTGGC    c.2640
 N  L  R  D   | T  N  M  I  P  G  S  P  G  S  T  E  L  E  G  G      p.880

          .         .         .         .         .   | 12     .    g.35444
 TTCAGTCGGCAACGCAAGCGCAAGTTGTCCTTCCGCAGGCGCACGGACAAGG | ACACGGAG    c.2700
 F  S  R  Q  R  K  R  K  L  S  F  R  R  R  T  D  K  D |   T  E      p.900

          .         .         .         .         .         .       g.35504
 CAGCCAGGGGAGGTGTCGGCCTTGGGGCCGGGCCGGGCGGGGGCAGGGCCGAGTAGCCGG       c.2760
 Q  P  G  E  V  S  A  L  G  P  G  R  A  G  A  G  P  S  S  R         p.920

          .         .         .         .         .         .       g.35564
 GGCCGGCCGGGGGGGCCGTGGGGGGAGAGCCCGTCCAGTGGCCCCTCCAGCCCTGAGAGC       c.2820
 G  R  P  G  G  P  W  G  E  S  P  S  S  G  P  S  S  P  E  S         p.940

          .         .         .         .         .         .       g.35624
 AGTGAGGATGAGGGCCCAGGCCGCAGCTCCAGCCCCCTCCGCCTGGTGCCCTTCTCCAGC       c.2880
 S  E  D  E  G  P  G  R  S  S  S  P  L  R  L  V  P  F  S  S         p.960

          .         .         .         .         .         .       g.35684
 CCCAGGCCCCCCGGAGAGCCGCCGGGTGGGGAGCCCCTGATGGAGGACTGCGAGAAGAGC       c.2940
 P  R  P  P  G  E  P  P  G  G  E  P  L  M  E  D  C  E  K  S         p.980

          .         .      | 13  .         .         .         .    g.35835
 AGCGACACTTGCAACCCCCTGTCAG | GCGCCTTCTCAGGAGTGTCCAACATTTTCAGCTTC    c.3000
 S  D  T  C  N  P  L  S  G |   A  F  S  G  V  S  N  I  F  S  F      p.1000

          .         .         .         .         .         .       g.35895
 TGGGGGGACAGTCGGGGCCGCCAGTACCAGGAGCTCCCTCGATGCCCCGCCCCCACCCCC       c.3060
 W  G  D  S  R  G  R  Q  Y  Q  E  L  P  R  C  P  A  P  T  P         p.1020

          .         .         .         .         .         .       g.35955
 AGCCTCCTCAACATCCCCCTCTCCAGCCCGGGTCGGCGGCCCCGGGGCGACGTGGAGAGC       c.3120
 S  L  L  N  I  P  L  S  S  P  G  R  R  P  R  G  D  V  E  S         p.1040

          .         .         .   | 14     .         .         .    g.36288
 AGGCTGGATGCCCTCCAGCGCCAGCTCAACAG | GCTGGAGACCCGGCTGAGTGCAGACATG    c.3180
 R  L  D  A  L  Q  R  Q  L  N  R  |  L  E  T  R  L  S  A  D  M      p.1060

          .         .         .         .         .         .       g.36348
 GCCACTGTCCTGCAGCTGCTACAGAGGCAGATGACGCTGGTCCCGCCCGCCTACAGTGCT       c.3240
 A  T  V  L  Q  L  L  Q  R  Q  M  T  L  V  P  P  A  Y  S  A         p.1080

          .         .         .         .         .         .       g.36408
 GTGACCACCCCGGGGCCTGGCCCCACTTCCACATCCCCGCTGTTGCCCGTCAGCCCCCTC       c.3300
 V  T  T  P  G  P  G  P  T  S  T  S  P  L  L  P  V  S  P  L         p.1100

          .         .         . | 15       .         .         .    g.37830
 CCCACCCTCACCTTGGACTCGCTTTCTCAG | GTTTCCCAGTTCATGGCGTGTGAGGAGCTG    c.3360
 P  T  L  T  L  D  S  L  S  Q   | V  S  Q  F  M  A  C  E  E  L      p.1120

          .         .         .         .         .         .       g.37890
 CCCCCGGGGGCCCCAGAGCTTCCCCAAGAAGGCCCCACACGACGCCTCTCCCTACCGGGC       c.3420
 P  P  G  A  P  E  L  P  Q  E  G  P  T  R  R  L  S  L  P  G         p.1140

          .         .         .         .         .         .       g.37950
 CAGCTGGGGGCCCTCACCTCCCAGCCCCTGCACAGACACGGCTCGGACCCGGGCAGTTAG       c.3480
 Q  L  G  A  L  T  S  Q  P  L  H  R  H  G  S  D  P  G  S  X         p.1159

          .         .         .         .         .         .       g.38010
 tggggctgcccagtgtggacacgtggctcacccagggatcaaggcgctgctgggccgctc       c.*60

          .         .         .         .         .         .       g.38070
 cccttggaggccctgctcaggaggccctgaccgtggaaggggagaggaactcgaaagcac       c.*120

          .         .         .         .         .         .       g.38130
 agctcctcccccagcccttgggaccatcttctcctgcagtcccctgggccccagtgagag       c.*180

          .         .         .         .         .         .       g.38190
 gggcaggggcagggccggcagtaggtggggcctgtggtccccccactgccctgagggcat       c.*240

          .         .         .         .         .         .       g.38250
 tagctggtctaactgcccggaggcacccggccctgggccttaggcacctcaaggactttt       c.*300

          .         .         .         .         .         .       g.38310
 ctgctatttactgctcttattgttaaggataataattaaggatcatatgaataattaatg       c.*360

          .         .         .         .                           g.38359
 aagatgctgatgactatgaataataaataattatcctgaggagactcca                  c.*409

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Potassium voltage-gated channel, subfamily H (eag-related), member 2 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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