potassium voltage-gated channel, KQT-like subfamily, member 1 (KCNQ1) - coding DNA reference sequence

(used for variant description)

(last modified June 6, 2014)


This file was created to facilitate the description of sequence variants on transcript NM_000218.2 in the KCNQ1 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000011.9, covering KCNQ1 transcript NM_000218.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5048
             gcggcggggctggcagcagtggctgcccgcactgcgcccgggcgctcg       c.-61

 .         .         .         .         .         .                g.5108
 ccttcgctgcagctcccggtgccgccgctcgggccggccccccggcaggccctcctcgtt       c.-1

          .         .         .         .         .         .       g.5168
 ATGGCCGCGGCCTCCTCCCCGCCCAGGGCCGAGAGGAAGCGCTGGGGTTGGGGCCGCCTG       c.60
 M  A  A  A  S  S  P  P  R  A  E  R  K  R  W  G  W  G  R  L         p.20

          .         .         .         .         .         .       g.5228
 CCAGGCGCCCGGCGGGGCAGCGCGGGCCTGGCCAAGAAGTGCCCCTTCTCGCTGGAGCTG       c.120
 P  G  A  R  R  G  S  A  G  L  A  K  K  C  P  F  S  L  E  L         p.40

          .         .         .         .         .         .       g.5288
 GCGGAGGGCGGCCCGGCGGGCGGCGCGCTCTACGCGCCCATCGCGCCCGGCGCCCCAGGT       c.180
 A  E  G  G  P  A  G  G  A  L  Y  A  P  I  A  P  G  A  P  G         p.60

          .         .         .         .         .         .       g.5348
 CCCGCGCCCCCTGCGTCCCCGGCCGCGCCCGCCGCGCCCCCAGTTGCCTCCGACCTTGGC       c.240
 P  A  P  P  A  S  P  A  A  P  A  A  P  P  V  A  S  D  L  G         p.80

          .         .         .         .         .         .       g.5408
 CCGCGGCCGCCGGTGAGCCTAGACCCGCGCGTCTCCATCTACAGCACGCGCCGCCCGGTG       c.300
 P  R  P  P  V  S  L  D  P  R  V  S  I  Y  S  T  R  R  P  V         p.100

          .         .         .         .         .         .       g.5468
 TTGGCGCGCACCCACGTCCAGGGCCGCGTCTACAACTTCCTCGAGCGTCCCACCGGCTGG       c.360
 L  A  R  T  H  V  Q  G  R  V  Y  N  F  L  E  R  P  T  G  W         p.120

          .         .       | 02 .         .         .         .    g.87971
 AAATGCTTCGTTTACCACTTCGCCGT | CTTCCTCATCGTCCTGGTCTGCCTCATCTTCAGC    c.420
 K  C  F  V  Y  H  F  A  V  |  F  L  I  V  L  V  C  L  I  F  S      p.140

          .         .         .         .         .        | 03.    g.130640
 GTGCTGTCCACCATCGAGCAGTATGCCGCCCTGGCCACGGGGACTCTCTTCTGGATG | GAG    c.480
 V  L  S  T  I  E  Q  Y  A  A  L  A  T  G  T  L  F  W  M   | E      p.160

          .         .         .         .         .         .       g.130700
 ATCGTGCTGGTGGTGTTCTTCGGGACGGAGTACGTGGTCCGCCTCTGGTCCGCCGGCTGC       c.540
 I  V  L  V  V  F  F  G  T  E  Y  V  V  R  L  W  S  A  G  C         p.180

          .         .         .         .         .         .       g.130760
 CGCAGCAAGTACGTGGGCCTCTGGGGGCGGCTGCGCTTTGCCCGGAAGCCCATTTCCATC       c.600
 R  S  K  Y  V  G  L  W  G  R  L  R  F  A  R  K  P  I  S  I         p.200

      | 04   .         .         .         .         .         .    g.131390
 ATCG | ACCTCATCGTGGTCGTGGCCTCCATGGTGGTCCTCTGCGTGGGCTCCAAGGGGCAG    c.660
 I  D |   L  I  V  V  V  A  S  M  V  V  L  C  V  G  S  K  G  Q      p.220

          .         .    | 05    .         .         .         .    g.132059
 GTGTTTGCCACGTCGGCCATCAG | GGGCATCCGCTTCCTGCAGATCCTGAGGATGCTACAC    c.720
 V  F  A  T  S  A  I  R  |  G  I  R  F  L  Q  I  L  R  M  L  H      p.240

          .         .         .         .         .         .       g.132119
 GTCGACCGCCAGGGAGGCACCTGGAGGCTCCTGGGCTCCGTGGTCTTCATCCACCGCCAG       c.780
 V  D  R  Q  G  G  T  W  R  L  L  G  S  V  V  F  I  H  R  Q         p.260

  | 06       .         .         .         .         .         .    g.132915
  | GAGCTGATAACCACCCTGTACATCGGCTTCCTGGGCCTCATCTTCTCCTCGTACTTTGTG    c.840
  | E  L  I  T  T  L  Y  I  G  F  L  G  L  I  F  S  S  Y  F  V      p.280

          .         .         .         .         .         .       g.132975
 TACCTGGCTGAGAAGGACGCGGTGAACGAGTCAGGCCGCGTGGAGTTCGGCAGCTACGCA       c.900
 Y  L  A  E  K  D  A  V  N  E  S  G  R  V  E  F  G  S  Y  A         p.300

          .         .  | 07      .         .         .         .    g.143483
 GATGCGCTGTGGTGGGGGGTG | GTCACAGTCACCACCATCGGCTATGGGGACAAGGTGCCC    c.960
 D  A  L  W  W  G  V   | V  T  V  T  T  I  G  Y  G  D  K  V  P      p.320

          .         .         .         .         .         .       g.143543
 CAGACGTGGGTCGGGAAGACCATCGCCTCCTGCTTCTCTGTCTTTGCCATCTCCTTCTTT       c.1020
 Q  T  W  V  G  K  T  I  A  S  C  F  S  V  F  A  I  S  F  F         p.340

          .   | 08     .         .         .         .         .    g.145269
 GCGCTCCCAGCG | GGGATTCTTGGCTCGGGGTTTGCCCTGAAGGTGCAGCAGAAGCAGAGG    c.1080
 A  L  P  A   | G  I  L  G  S  G  F  A  L  K  V  Q  Q  K  Q  R      p.360

          .         .         .         .         | 09         .    g.147591
 CAGAAGCACTTCAACCGGCAGATCCCGGCGGCAGCCTCACTCATTCAG | ACCGCATGGAGG    c.1140
 Q  K  H  F  N  R  Q  I  P  A  A  A  S  L  I  Q   | T  A  W  R      p.380

          .         .         .         .         .         .       g.147651
 TGCTATGCTGCCGAGAACCCCGACTCCTCCACCTGGAAGATCTACATCCGGAAGGCCCCC       c.1200
 C  Y  A  A  E  N  P  D  S  S  T  W  K  I  Y  I  R  K  A  P         p.400

          .         .         .         .         .  | 10      .    g.148731
 CGGAGCCACACTCTGCTGTCACCCAGCCCCAAACCCAAGAAGTCTGTGGTG | GTAAAGAAA    c.1260
 R  S  H  T  L  L  S  P  S  P  K  P  K  K  S  V  V   | V  K  K      p.420

          .         .         .         .         .         .       g.148791
 AAAAAGTTCAAGCTGGACAAAGACAATGGGGTGACTCCTGGAGAGAAGATGCTCACAGTC       c.1320
 K  K  F  K  L  D  K  D  N  G  V  T  P  G  E  K  M  L  T  V         p.440

          .         .         .         .         .         .       g.148851
 CCCCATATCACGTGCGACCCCCCAGAAGAGCGGCGGCTGGACCACTTCTCTGTCGACGGC       c.1380
 P  H  I  T  C  D  P  P  E  E  R  R  L  D  H  F  S  V  D  G         p.460

          .    | 11    .         .         .         .         .    g.222017
 TATGACAGTTCTG | TAAGGAAGAGCCCAACACTGCTGGAAGTGAGCATGCCCCATTTCATG    c.1440
 Y  D  S  S  V |   R  K  S  P  T  L  L  E  V  S  M  P  H  F  M      p.480

          .         .         .         .         .         .       g.222077
 AGAACCAACAGCTTCGCCGAGGACCTGGACCTGGAAGGGGAGACTCTGCTGACACCCATC       c.1500
 R  T  N  S  F  A  E  D  L  D  L  E  G  E  T  L  L  T  P  I         p.500

          .     | 12   .         .         .         .         .    g.328899
 ACCCACATCTCACA | GCTGCGGGAACACCATCGGGCCACCATTAAGGTCATTCGACGCATG    c.1560
 T  H  I  S  Q  |  L  R  E  H  H  R  A  T  I  K  V  I  R  R  M      p.520

          .         .         . | 13       .         .         .    g.335999
 CAGTACTTTGTGGCCAAGAAGAAATTCCAG | CAAGCGCGGAAGCCTTACGATGTGCGGGAC    c.1620
 Q  Y  F  V  A  K  K  K  F  Q   | Q  A  R  K  P  Y  D  V  R  D      p.540

          .         .         .         .         .         .       g.336059
 GTCATTGAGCAGTACTCGCAGGGCCACCTCAACCTCATGGTGCGCATCAAGGAGCTGCAG       c.1680
 V  I  E  Q  Y  S  Q  G  H  L  N  L  M  V  R  I  K  E  L  Q         p.560

       | 14  .         .         .         .         .   | 15     . g.337993
 AGGAG | GCTGGACCAGTCCATTGGGAAGCCCTCACTGTTCATCTCCGTCTCAG | AAAAGAGC c.1740
 R  R  |  L  D  Q  S  I  G  K  P  S  L  F  I  S  V  S  E |   K  S   p.580

          .         .         .         .         .     | 16   .    g.407782
 AAGGATCGCGGCAGCAACACGATCGGCGCCCGCCTGAACCGAGTAGAAGACAAG | GTGACG    c.1800
 K  D  R  G  S  N  T  I  G  A  R  L  N  R  V  E  D  K   | V  T      p.600

          .         .         .         .         .         .       g.407842
 CAGCTGGACCAGAGGCTGGCACTCATCACCGACATGCTTCACCAGCTGCTCTCCTTGCAC       c.1860
 Q  L  D  Q  R  L  A  L  I  T  D  M  L  H  Q  L  L  S  L  H         p.620

          .         .         .         .         .         .       g.407902
 GGTGGCAGCACCCCCGGCAGCGGCGGCCCCCCCAGAGAGGGCGGGGCCCACATCACCCAG       c.1920
 G  G  S  T  P  G  S  G  G  P  P  R  E  G  G  A  H  I  T  Q         p.640

          .         .         .         .         .         .       g.407962
 CCCTGCGGCAGTGGCGGCTCCGTCGACCCTGAGCTCTTCCTGCCCAGCAACACCCTGCCC       c.1980
 P  C  G  S  G  G  S  V  D  P  E  L  F  L  P  S  N  T  L  P         p.660

          .         .         .         .         .                 g.408013
 ACCTACGAGCAGCTGACCGTGCCCAGGAGGGGCCCCGATGAGGGGTCCTGA                c.2031
 T  Y  E  Q  L  T  V  P  R  R  G  P  D  E  G  S  X                  p.676

          .         .         .         .         .         .       g.408073
 ggaggggatggggctgggggatgggcctgagtgagaggggaggccaagagtggccccacc       c.*60

          .         .         .         .         .         .       g.408133
 tggccctctctgaaggaggccacctcctaaaaggcccagagagaagagccccactctcag       c.*120

          .         .         .         .         .         .       g.408193
 aggccccaataccccatggaccatgctgtctggcacagcctgcacttgggggctcagcaa       c.*180

          .         .         .         .         .         .       g.408253
 ggccacctcttcctggccggtgtgggggccccgtctcaggtctgagttgttaccccaagc       c.*240

          .         .         .         .         .         .       g.408313
 gccctggcccccacatggtgatgttgacatcactggcatggtggttgggacccagtggca       c.*300

          .         .         .         .         .         .       g.408373
 gggcacagggcctggcccatgtatggccaggaagtagcacaggctgagtgcaggcccacc       c.*360

          .         .         .         .         .         .       g.408433
 ctgcttggcccagggggcttcctgaggggagacagagcaacccctggaccccagcctcaa       c.*420

          .         .         .         .         .         .       g.408493
 atccaggaccctgccaggcacaggcagggcaggaccagcccacgctgactacagggccgc       c.*480

          .         .         .         .         .         .       g.408553
 cggcaataaaagcccaggagcccatttggagggcctgggcctggctccctcactctcagg       c.*540

          .         .         .         .         .         .       g.408613
 aaatgctgacccatgggcaggagactgtggagactgctcctgagcccccagcttccagca       c.*600

          .         .         .         .         .         .       g.408673
 ggagggacagtctcaccatttccccagggcacgtggttgagtggggggaacgcccacttc       c.*660

          .         .         .         .         .         .       g.408733
 cctgggttagactgccagctcttcctagctggagaggagccctgcctctccgcccctgag       c.*720

          .         .         .         .         .         .       g.408793
 cccactgtgcgtggggctcccgcctccaacccctcgcccagtcccagcagccagccaaac       c.*780

          .         .         .         .         .         .       g.408853
 acacagaaggggactgccacctccccttgccagctgctgagccgcagagaagtgacggtt       c.*840

          .         .         .         .         .         .       g.408913
 cctacacaggacaggggttccttctgggcattacatcgcatagaaatcaataatttgtgg       c.*900

          .         .         .         .         .         .       g.408973
 tgatttggatctgtgttttaatgagtttcacagtgtgattttgattattaattgtgcaag       c.*960

          .         .         .         .         .         .       g.409033
 cttttcctaataaacgtggagaatcacaggctgggctgggcactgctctcaccttggttc       c.*1020

          .         .         .         .         .         .       g.409093
 ctggggcatccatggggtctctcacagacaggacccctgcagttcccctggaagcagtgc       c.*1080

          .         .                                               g.409120
 ccaggtggctgtggaataggaacgcta                                        c.*1107

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Potassium voltage-gated channel, KQT-like subfamily, member 1 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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