NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa (NDUFA10) - coding DNA reference sequence

(used for variant description)

(last modified January 31, 2025)


This file was created to facilitate the description of sequence variants on transcript NM_004544.3 in the NDUFA10 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000002.11, covering NDUFA10 transcript NM_004544.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5041
                    gcaccccggccgtgacgtcacggcagcgcgccggccgcgag       c.-61

 .         .         .         .         .         .                g.5101
 agagggccccgtcgcgaccgcgtccccttgggtccttgatcctgagctgaccgggtagcc       c.-1

          .         .         .         .         .         .       g.5161
 ATGGCCTTGCGGCTCCTGAAGCTGGCAGCGACGTCCGCGTCCGCCCGGGTCGTGGCGGCG       c.60
 M  A  L  R  L  L  K  L  A  A  T  S  A  S  A  R  V  V  A  A         p.20

          .      | 02  .         .         .         .         .    g.8107
 GGCGCCCAGCGCGTG | AGAGGAATTCATAGCAGTGTGCAGTGCAAACTGCGCTATGGAATG    c.120
 G  A  Q  R  V   | R  G  I  H  S  S  V  Q  C  K  L  R  Y  G  M      p.40

          .         .         .         .         .         .       g.8167
 TGGCATTTCCTACTTGGGGATAAAGCAAGCAAAAGACTGACAGAACGCAGCAGAGTGATA       c.180
 W  H  F  L  L  G  D  K  A  S  K  R  L  T  E  R  S  R  V  I         p.60

          .         .         .         .         .         .       g.8227
 ACTGTAGATGGCAATATATGTACTGGAAAAGGCAAACTTGCAAAAGAAATAGCAGAGAAA       c.240
 T  V  D  G  N  I  C  T  G  K  G  K  L  A  K  E  I  A  E  K         p.80

      | 03   .         .         .         .         .         .    g.9046
 CTAG | GCTTCAAGCACTTTCCTGAAGCGGGGATTCATTATCCAGACAGTACCACAGGAGAT    c.300
 L  G |   F  K  H  F  P  E  A  G  I  H  Y  P  D  S  T  T  G  D      p.100

          .         .         .         .         .         .       g.9106
 GGGAAGCCCCTCGCCACCGACTATAATGGCAACTGTAGTTTGGAGAAATTTTACGATGAT       c.360
 G  K  P  L  A  T  D  Y  N  G  N  C  S  L  E  K  F  Y  D  D         p.120

          .         .         .         .         .         .       g.9166
 CCGAGAAGCAATGATGGCAACAGTTACCGCCTGCAGTCCTGGTTGTACAGCAGTCGCCTG       c.420
 P  R  S  N  D  G  N  S  Y  R  L  Q  S  W  L  Y  S  S  R  L         p.140

          .         .         .         . | 04       .         .    g.11783
 CTGCAGTACTCAGATGCCTTGGAGCACTTGCTGACCACAG | GACAAGGTGTTGTGTTGGAG    c.480
 L  Q  Y  S  D  A  L  E  H  L  L  T  T  G |   Q  G  V  V  L  E      p.160

          .         .         .         .         .         .       g.11843
 CGCTCCATCTTCAGTGACTTTGTGTTCCTGGAGGCGATGTACAACCAGGGATTCATCCGA       c.540
 R  S  I  F  S  D  F  V  F  L  E  A  M  Y  N  Q  G  F  I  R         p.180

         | 05.         .         .         .         .         .    g.15595
 AAGCAGT | GTGTGGACCACTACAACGAGGTGAAGAGCGTCACCATCTGCGATTACCTGCCC    c.600
 K  Q  C |   V  D  H  Y  N  E  V  K  S  V  T  I  C  D  Y  L  P      p.200

          .         .         .         .         .         .       g.15655
 CCCCACCTGGTGATTTACATCGATGTGCCCGTTCCAGAGGTCCAGAGGCGGATTCAGAAG       c.660
 P  H  L  V  I  Y  I  D  V  P  V  P  E  V  Q  R  R  I  Q  K         p.220

           | 06        .         .         .         .         .    g.18757
 AAAGGAGAT | CCACATGAAATGAAGATCACCTCTGCCTATCTACAGGACATTGAGAATGCC    c.720
 K  G  D   | P  H  E  M  K  I  T  S  A  Y  L  Q  D  I  E  N  A      p.240

          .         .          | 07        .         .         .    g.23063
 TATAAGAAAACCTTTCTCCCTGAGATGAG | TGAAAAATGTGAGGTTTTACAATATTCTGCA    c.780
 Y  K  K  T  F  L  P  E  M  S  |  E  K  C  E  V  L  Q  Y  S  A      p.260

          .         .     | 08   .         .         .         .    g.25143
 AGGGAAGCTCAAGATTCAAAAAAG | GTGGTAGAGGACATTGAATACCTGAAGTTCGATAAA    c.840
 R  E  A  Q  D  S  K  K   | V  V  E  D  I  E  Y  L  K  F  D  K      p.280

          .         .         .         .         . | 09       .    g.40230
 GGGCCGTGGCTCAAGCAGGACAATCGCACTTTATACCACCTGCGATTACT | GGTTCAGGAT    c.900
 G  P  W  L  K  Q  D  N  R  T  L  Y  H  L  R  L  L  |  V  Q  D      p.300

          .         .         .         .         .         .       g.40290
 AAGTTTGAGGTGCTGAATTACACAAGCATTCCTATCTTTCTCCCGGAAGTCACCATTGGA       c.960
 K  F  E  V  L  N  Y  T  S  I  P  I  F  L  P  E  V  T  I  G         p.320

          .         .         .          | 10        .         .    g.69237
 GCTCATCAGACTGACCGTGTCTTACATCAGTTCAGAGAG | CTGCCGGGCCGCAAGTACAGC    c.1020
 A  H  Q  T  D  R  V  L  H  Q  F  R  E   | L  P  G  R  K  Y  S      p.340

          .         .         .         .                           g.69285
 CCTGGGTACAACACCGAGGTGGGAGACAAGTGGATCTGGCTGAAGTGA                   c.1068
 P  G  Y  N  T  E  V  G  D  K  W  I  W  L  K  X                     p.355

          .         .         .         .         .         .       g.69345
 acgggccgccttctgctccagctgcatcacagtgatggccaagctgcatcagccgcactc       c.*60

          .         .         .         .         .         .       g.69405
 tcctggacgccatatagctttaagatcgggggagggtaaataatgcaaaaattgcacagt       c.*120

          .         .         .         .         .         .       g.69465
 ggaagaaggggtctcacaaaaagcaatccatcctgtagtataggtaatggagttggggga       c.*180

          .         .         .         .         .         .       g.69525
 agcagcttccattctggatgtttggaaccctttagctttgttttggaatggcccaccatt       c.*240

          .         .         .         .         .         .       g.69585
 ctcactggaaaacagtggtctgctgtgaaaggccagctctcggcagcccctgtggtttca       c.*300

          .         .         .         .         .         .       g.69645
 gcgctgccgctctgtgtcattcaggttgtgcacattgtttttcttctgacttccagaaat       c.*360

          .         .         .         .         .         .       g.69705
 aaaagtgtttccatgggaatttccccatcgtacgtctatgtgcgtgcgggcacgtcgaaa       c.*420

          .         .         .         .         .         .       g.69765
 ctgcacacgtgcacacacgctgctctgggccctgtttggtgtggtgtggtttaattgagg       c.*480

          .         .         .         .         .         .       g.69825
 cttacattatgctgaagagtttttctaaaggcctactgtatttattttagtaatgtgcta       c.*540

          .         .         .         .         .         .       g.69885
 cattagagtagaaaaaataagaacgtgaagaagaaatagcaaaaggagaaaattaccaca       c.*600

          .         .         .         .         .         .       g.69945
 gatttacagaacaatatgttttaagagagacgttgagaaagattcacgtggccgtcctca       c.*660

          .         .         .         .         .         .       g.70005
 gcgtctcaaactcctttgaagggagatttgagcttaggctgttgatgacataagatgcaa       c.*720

          .         .         .         .         .         .       g.70065
 aagcaaaataatatactctctttattacccagaaaatcaagttgccagtcaaaactgaga       c.*780

          .         .         .         .         .         .       g.70125
 aatgagaaagaaaatcagatttctttattcatctctgttgaagcctagaaaaccaaaaca       c.*840

          .         .         .         .         .         .       g.70185
 agctggttgtggttcagcatcatggtttaggaatcaagctgtcagttgtgagtcctactg       c.*900

          .         .         .         .         .         .       g.70245
 aactgtgggttttccactgtaaagctccactgtgtccattaggaatcaggctgccagttg       c.*960

          .         .         .         .         .         .       g.70305
 tgagtcctactgaactgtgggttttccactgtaaagctccactgtgtccaatatggtagc       c.*1020

          .         .         .         .         .         .       g.70365
 tcctagccacatgtgggtattgaaatttaaatgagctaaaatgtaatagagtttaaaatt       c.*1080

          .         .         .         .         .         .       g.70425
 gggttccttggttgcactggccatagttcaggcactccacagccgcctgtgggcagtagt       c.*1140

          .         .         .         .         .         .       g.70485
 tccagtgctggtgcagaggacgatgctctgctccccgcggaagctctaccaggcctcgct       c.*1200

          .         .         .         .         .         .       g.70545
 gctgcggagcatgcgaagaagatgcacactccttccctccttgcgtccgcctgccttttt       c.*1260

          .         .         .         .         .         .       g.70605
 ccctctccccttccttccctccttctttcctcctccttccctcccttcctttcttccttc       c.*1320

          .         .         .         .         .         .       g.70665
 catctgtccttgttttcctcccttcccttcctccctgcctctttccttccctccttctct       c.*1380

          .         .         .         .         .         .       g.70725
 tccttccttccgtctgtccttgttttcctccctgcctctttccttccctccttctcttcc       c.*1440

          .         .         .         .         .         .       g.70785
 ttccttccttccgtctgtccttgttttcctcccttcccttcctccctgcctccttccttg       c.*1500

          .         .         .         .         .         .       g.70845
 ttttaagaatttgaaaataaagtttcccaggagttttgaattggagtcgagatttaagtg       c.*1560

          .         .         .         .         .         .       g.70905
 gctgaagttttgcatttcactaggaaaccaacagctttaatcatgaaatgaaagcacagc       c.*1620

          .         .         .         .         .         .       g.70965
 tgggcattgggccagtcacagagtgtcttttgctctgagcacttcacaaacccattgtgg       c.*1680

          .         .         .         .         .         .       g.71025
 aggggaggaaagaaaaagaaagccatctttaattatcttagctgttcctaatgtctttgg       c.*1740

          .         .         .         .         .         .       g.71085
 ctgcaaagagctagctgtttccttcaaccttggtggttgcacgggtagtgtcctcagcag       c.*1800

          .         .         .         .         .         .       g.71145
 tgagagggcaggtctgccctgtggtcaggattgcccttgtgaggggcagagctctccaac       c.*1860

          .         .         .         .         .         .       g.71205
 catgcagggctccgtgtcggcatggtgtggactcgggtgctctgatcatcccctgtgttt       c.*1920

          .         .         .         .         .         .       g.71265
 gcgtctgaccctgtgtggttgcattcccttgatggagtgggaagtatgtaatttgtagtg       c.*1980

          .         .         .         .         .         .       g.71325
 ctgaggacattcgtctgtttgattttctggtgttttcaatgacatgcatgttcagcagag       c.*2040

          .         .         .         .         .         .       g.71385
 aaagatgaataaacactgtccaattcttctctccacatagaagcctcaagaagaggtgag       c.*2100

          .         .         .         .         .         .       g.71445
 gagatgccccgatttccttatttcagagcagtacatgcgttcgtctcacgaaagctctta       c.*2160

          .         .         .         .         .         .       g.71505
 caactaaaacaacagcaccaacaaaccaggatcaaaataatcgtgcattttccaggattc       c.*2220

          .         .         .         .         .         .       g.71565
 catgttggacttctcagtgctttggagatcaggaaataatcatgctgttgcagcagtatg       c.*2280

          .         .         .         .         .         .       g.71625
 gttttgtgtctggattttattcatacaggcatgtgtttacaggcatgagaattctgtatt       c.*2340

          .         .         .         .         .         .       g.71685
 gaaaagaaagtccttgtttttttctaacgtatctttctgttccatcaactgttaaaacca       c.*2400

          .         .         .         .         .         .       g.71745
 aattgttaagaacattgagcttcttaggagagattacatgcagctacttaggaccacctc       c.*2460

          .         .         .         .         .         .       g.71805
 agcaaaatggagttgcctgggtagatagcagcagcagctcaccagccccacgctgccagg       c.*2520

          .         .         .         .         .         .       g.71865
 ctgctggctgctgtccaccaggcagctgtggaacctccatgttctgcctaggtgttgtgg       c.*2580

          .         .         .         .         .         .       g.71925
 caagaacagcagggaaacaggcggccgcctccaggccacaggtggacccagggaccttca       c.*2640

          .         .         .         .         .         .       g.71985
 gttacgccgcttcaattgaattcgtggtggtttctctgctacagcagaagtggaagaagc       c.*2700

          .         .         .         .         .         .       g.72045
 tcttgtcttgtttggcatttgtcccattttttggctaataattggctttgaatttctctg       c.*2760

          .         .         .         .         .         .       g.72105
 tgccctgcttaccaattatagctttctggattggctgttcttagcagtgcaaatgtcaat       c.*2820

          .         .         .         .         .         .       g.72165
 gcaaagaagcaagcaggcggctactttctgggaagaagcatagtccgtgctcacactgga       c.*2880

          .         .         .         .         .         .       g.72225
 tataaatctgcaagatttgggggtttggcaaaataggggtggagggaaagctgccatggc       c.*2940

          .         .         .         .         .         .       g.72285
 tgtcagaaattggggctttttgaagaaaagcttgtgtaggcatcagccactggctggcca       c.*3000

          .         .         .         .         .         .       g.72345
 gaattccatgaatggaagcaggtgcccgagtgatctggggctttacatgtggatataaat       c.*3060

          .         .         .         .         .         .       g.72405
 agaagccgggagcctgaggctttgctttaggaaaatcatgagccagaaaacagaggaggt       c.*3120

          .         .         .         .         .         .       g.72465
 gattgtcagtagtcacctcacgccgctagtgttttctaatactctctcgaattgtcaaag       c.*3180

          .         .         .         .         .         .       g.72525
 caaaggaccttataacagcaacacgtgtgtgactcgaagcagcgagcttcccttgggaaa       c.*3240

          .         .         .         .         .         .       g.72585
 aggagcctcttctcagcagagggtcccagcctttctgtccttccccatcggaatgccagg       c.*3300

          .         .         .         .         .         .       g.72645
 ctctgtgagtttggatgttggacattgccacctgaattccaggaggccggggagctccag       c.*3360

          .         .         .         .         .         .       g.72705
 tgatggacttgtccccaaaagagtggtgctgttctcagagccataaatgttccactgaaa       c.*3420

          .         .         .         .         .         .       g.72765
 gtgtctgtcccctggctcacgctggctgcgcttgcttgaaggaggctgatttaagggttc       c.*3480

          .         .         .         .         .         .       g.72825
 taataggaagacaaatgaaactgtcaaattttatctttaagcatgtgagtaagtttgctc       c.*3540

          .         .         .         .         .         .       g.72885
 attcgcttttactattgatgtatagttttaaaattcttaatttaaaaattattttaatag       c.*3600

          .         .         .         .         .         .       g.72945
 taaatttttcacaagtgaacactttttatctttaaattaaaattctgaagctccctagtt       c.*3660

          .         .         .         .         .         .       g.73005
 agttagatccaattgctggttacattttgggaagctctcattttagtgctatgtagtttc       c.*3720

          .         .                                               g.73031
 attgaataaacatgtttttaatgaga                                         c.*3746

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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