NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa (NDUFV1) - coding DNA reference sequence

(used for variant description)

(last modified February 2, 2014)


This file was created to facilitate the description of sequence variants on transcript NM_007103.3 in the NDUFV1 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000011.9, covering NDUFV1 transcript NM_007103.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                               .         .         .                g.5033
                            gaagttgaaggggcgcagcgataccggtgcgcg       c.-121

 .         .         .         .         .         .                g.5093
 gcgctggcgtcgggcgcgtgacgtctttcctgcgcgccacctagcgtctctatcgcgcca       c.-61

 .         .         .         .         .         .                g.5153
 gttcctcagcctcagtgctatgaaggtgacagcgtgaggtgacccatctggcccgccgcg       c.-1

          .         .         .         .         .         .       g.5213
 ATGCTGGCAACACGGCGGCTGCTCGGCTGGTCGCTTCCCGCGCGGGTATCTGTGCGTTTC       c.60
 M  L  A  T  R  R  L  L  G  W  S  L  P  A  R  V  S  V  R  F         p.20

          .   | 02     .         .         .         .         .    g.6592
 AGCGGCGACACG | ACAGCACCCAAGAAAACCTCATTTGGCTCGCTGAAGGATGAAGACCGG    c.120
 S  G  D  T   | T  A  P  K  K  T  S  F  G  S  L  K  D  E  D  R      p.40

          .         .         .      | 03  .         .         .    g.6725
 ATTTTCACCAACCTGTACGGCCGCCATGACTGGAG | GCTGAAAGGTTCCCTGAGTCGAGGT    c.180
 I  F  T  N  L  Y  G  R  H  D  W  R  |  L  K  G  S  L  S  R  G      p.60

          .         .         .         .         .         .       g.6785
 GACTGGTACAAGACAAAGGAGATCCTGCTGAAGGGGCCCGACTGGATCCTGGGCGAGATC       c.240
 D  W  Y  K  T  K  E  I  L  L  K  G  P  D  W  I  L  G  E  I         p.80

          .         .         .         .         .         .       g.6845
 AAGACATCGGGTTTGAGGGGCCGTGGAGGCGCTGGCTTCCCCACTGGCCTCAAGTGGAGC       c.300
 K  T  S  G  L  R  G  R  G  G  A  G  F  P  T  G  L  K  W  S         p.100

          .         .       | 04 .         .         .         .    g.7634
 TTCATGAATAAGCCCTCAGATGGCAG | GCCCAAGTATCTGGTGGTGAACGCAGACGAGGGG    c.360
 F  M  N  K  P  S  D  G  R  |  P  K  Y  L  V  V  N  A  D  E  G      p.120

          .         .         .         .         .         .       g.7694
 GAGCCGGGCACCTGCAAGGACCGGGAGATCTTACGCCATGATCCTCACAAGCTGCTGGAA       c.420
 E  P  G  T  C  K  D  R  E  I  L  R  H  D  P  H  K  L  L  E         p.140

          .         .         .         .         .         .       g.7754
 GGCTGCCTGGTGGGGGGCCGGGCCATGGGCGCCCGCGCTGCCTATATCTACATCCGAGGG       c.480
 G  C  L  V  G  G  R  A  M  G  A  R  A  A  Y  I  Y  I  R  G         p.160

          .         .         . | 05       .         .         .    g.8559
 GAATTCTACAATGAGGCCTCCAATCTGCAG | GTGGCCATCCGAGAGGCCTATGAGGCAGGT    c.540
 E  F  Y  N  E  A  S  N  L  Q   | V  A  I  R  E  A  Y  E  A  G      p.180

          .         .         .         .         .         .       g.8619
 CTGATTGGCAAGAATGCTTGTGGCTCTGGCTATGATTTTGACGTGTTTGTGGTGCGCGGG       c.600
 L  I  G  K  N  A  C  G  S  G  Y  D  F  D  V  F  V  V  R  G         p.200

          .         .         .         .         .         .       g.8679
 GCTGGGGCCTACATCTGTGGAGAGGAGACAGCGCTCATCGAGTCCATTGAGGGCAAGCAG       c.660
 A  G  A  Y  I  C  G  E  E  T  A  L  I  E  S  I  E  G  K  Q         p.220

          .         .         .         . | 06       .         .    g.9163
 GGCAAGCCCCGCCTGAAGCCCCCCTTCCCCGCAGACGTGG | GAGTGTTTGGCTGCCCCACA    c.720
 G  K  P  R  L  K  P  P  F  P  A  D  V  G |   V  F  G  C  P  T      p.240

          .         .         .         .         .         .       g.9223
 ACTGTGGCCAACGTGGAGACAGTGGCAGTGTCCCCCACAATCTGCCGCCGTGGAGGTACC       c.780
 T  V  A  N  V  E  T  V  A  V  S  P  T  I  C  R  R  G  G  T         p.260

          .         .         .         .         .         .       g.9283
 TGGTTTGCTGGCTTTGGCAGAGAACGCAACTCAGGCACCAAACTATTCAACATCTCTGGC       c.840
 W  F  A  G  F  G  R  E  R  N  S  G  T  K  L  F  N  I  S  G         p.280

          .         .         .         .         .         .       g.9343
 CATGTCAACCACCCTTGCACTGTGGAGGAGGAGATGTCTGTGCCCTTGAAAGAACTGATT       c.900
 H  V  N  H  P  C  T  V  E  E  E  M  S  V  P  L  K  E  L  I         p.300

          .    | 07    .         .         .         .         .    g.9598
 GAGAAGCATGCTG | GGGGTGTCACGGGCGGCTGGGACAACCTCCTTGCTGTGATCCCTGGC    c.960
 E  K  H  A  G |   G  V  T  G  G  W  D  N  L  L  A  V  I  P  G      p.320

          .         .         .         .         .         .       g.9658
 GGCTCGTCTACCCCACTGATCCCCAAGTCTGTGTGTGAGACGGTGCTGATGGACTTCGAT       c.1020
 G  S  S  T  P  L  I  P  K  S  V  C  E  T  V  L  M  D  F  D         p.340

          .         .         .         .         .         .       g.9718
 GCGCTGGTGCAGGCACAGACAGGCCTGGGCACAGCTGCGGTGATCGTCATGGACCGCTCG       c.1080
 A  L  V  Q  A  Q  T  G  L  G  T  A  A  V  I  V  M  D  R  S         p.360

  | 08       .         .         .         .         .         .    g.10105
  | ACGGACATCGTGAAAGCCATCGCCCGCCTCATTGAGTTCTATAAGCACGAGAGCTGTGGC    c.1140
  | T  D  I  V  K  A  I  A  R  L  I  E  F  Y  K  H  E  S  C  G      p.380

          .         .   | 09     .         .         .         .    g.10306
 CAGTGTACCCCATGCCGTGAGG | GTGTGGACTGGATGAACAAGGTGATGGCACGTTTCGTG    c.1200
 Q  C  T  P  C  R  E  G |   V  D  W  M  N  K  V  M  A  R  F  V      p.400

          .         .         .         .         .         .       g.10366
 AGGGGGGATGCCCGGCCGGCCGAGATCGACTCCCTGTGGGAGATCAGCAAGCAGATAGAA       c.1260
 R  G  D  A  R  P  A  E  I  D  S  L  W  E  I  S  K  Q  I  E         p.420

          .         .         .         .         | 10         .    g.10532
 GGCCATACGATTTGTGCTCTGGGTGACGGGGCCGCCTGGCCTGTGCAG | GGTCTGATCCGC    c.1320
 G  H  T  I  C  A  L  G  D  G  A  A  W  P  V  Q   | G  L  I  R      p.440

          .         .         .         .         .         .       g.10592
 CACTTTCGGCCGGAGCTCGAGGAGCGGATGCAGCGGTTTGCCCAGCAGCATCAGGCCCGG       c.1380
 H  F  R  P  E  L  E  E  R  M  Q  R  F  A  Q  Q  H  Q  A  R         p.460

          .                                                         g.10607
 CAGGCTGCCTCTTAG                                                    c.1395
 Q  A  A  S  X                                                      p.464

          .         .         .         .         .         .       g.10667
 cccaccaccctggcctgctgtcctgcgtctatccatgtggaatgctggacaataaagcga       c.*60

          .         .                                               g.10690
 gtgctgcccaccctccagctgcc                                            c.*83

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

Powered by LOVD v.3.0 Build 09
©2004-2014 Leiden University Medical Center