nitric oxide synthase 3 (endothelial cell) (NOS3) - coding DNA reference sequence

(used for variant description)

(last modified November 1, 2019)


This file was created to facilitate the description of sequence variants on transcript NM_000603.4 in the NOS3 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_011992.1, covering NOS3 transcript NM_000603.4.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
           .         .         .         .         .                g.5056
     actgaaactaggggcaaggagacgaagagaacatgaaagttaaactttaagatgaa       c.-241

 .         .         .         .         .         .                g.5116
 gaacaaagctgaacatactgatgcattggatctttggagaggatctcagaactcattgta       c.-181

 .         .         .         .         .         .                g.5176
 cttaatttacaggctaaaaccttagaagaggaatttattatatcctacacaagactccag       c.-121

 .         .         .         .         .         .                g.5236
 ggaagcacatggccttggactgaaggctggcatctggaagctgtcagccaccagcacctt       c.-61

 .         | 02         .         .         .         .             g.7748
 ctgcagcag | gaaaaggccagggctctgctggagcaggcagcagagtggacgcacagtaac    c.-1

          .         .         .         .         .         .       g.7808
 ATGGGCAACTTGAAGAGCGTGGCCCAGGAGCCTGGGCCACCCTGCGGCCTGGGGCTGGGG       c.60
 M  G  N  L  K  S  V  A  Q  E  P  G  P  P  C  G  L  G  L  G         p.20

          .         .         .         .         .         .       g.7868
 CTGGGCCTTGGGCTGTGCGGCAAGCAGGGCCCAGCCACCCCGGCCCCTGAGCCCAGCCGG       c.120
 L  G  L  G  L  C  G  K  Q  G  P  A  T  P  A  P  E  P  S  R         p.40

          .         .         .         | 03         .         .    g.9169
 GCCCCAGCATCCCTACTCCCACCAGCGCCAGAACACAG | CCCCCCGAGCTCCCCGCTAACC    c.180
 A  P  A  S  L  L  P  P  A  P  E  H  S  |  P  P  S  S  P  L  T      p.60

          .         .         .         .         .         .       g.9229
 CAGCCCCCAGAGGGGCCCAAGTTCCCTCGTGTGAAGAACTGGGAGGTGGGGAGCATCACC       c.240
 Q  P  P  E  G  P  K  F  P  R  V  K  N  W  E  V  G  S  I  T         p.80

          .         .         . | 04       .         .         .    g.10378
 TATGACACCCTCAGCGCCCAGGCGCAGCAG | GATGGGCCCTGCACCCCAAGACGCTGCCTG    c.300
 Y  D  T  L  S  A  Q  A  Q  Q   | D  G  P  C  T  P  R  R  C  L      p.100

          .         .         .         .         .         .       g.10438
 GGCTCCCTGGTATTTCCACGGAAACTACAGGGCCGGCCCTCCCCCGGCCCCCCGGCCCCT       c.360
 G  S  L  V  F  P  R  K  L  Q  G  R  P  S  P  G  P  P  A  P         p.120

          .         .         .         .         .          | 05    g.10708
 GAGCAGCTGCTGAGTCAGGCCCGGGACTTCATCAACCAGTACTACAGCTCCATTAAGAG | G    c.420
 E  Q  L  L  S  Q  A  R  D  F  I  N  Q  Y  Y  S  S  I  K  R  |      p.140

          .         .         .         .         .         .       g.10768
 AGCGGCTCCCAGGCCCACGAACAGCGGCTTCAAGAGGTGGAAGCCGAGGTGGCAGCCACA       c.480
 S  G  S  Q  A  H  E  Q  R  L  Q  E  V  E  A  E  V  A  A  T         p.160

          .         .         .         .         .         .       g.10828
 GGCACCTACCAGCTTAGGGAGAGCGAGCTGGTGTTCGGGGCTAAGCAGGCCTGGCGCAAC       c.540
 G  T  Y  Q  L  R  E  S  E  L  V  F  G  A  K  Q  A  W  R  N         p.180

          .         .         .         .   | 06     .         .    g.12319
 GCTCCCCGCTGCGTGGGCCGGATCCAGTGGGGGAAGCTGCAG | GTGTTCGATGCCCGGGAC    c.600
 A  P  R  C  V  G  R  I  Q  W  G  K  L  Q   | V  F  D  A  R  D      p.200

          .         .         .         .         .         .       g.12379
 TGCAGGTCTGCACAGGAAATGTTCACCTACATCTGCAACCACATCAAGTATGCCACCAAC       c.660
 C  R  S  A  Q  E  M  F  T  Y  I  C  N  H  I  K  Y  A  T  N         p.220

          .     | 07   .         .         .         .         .    g.12529
 CGGGGCAACCTTCG | CTCGGCCATCACAGTGTTCCCGCAGCGCTGCCCTGGCCGAGGAGAC    c.720
 R  G  N  L  R  |  S  A  I  T  V  F  P  Q  R  C  P  G  R  G  D      p.240

          .         .         .         .         .         .       g.12589
 TTCCGAATCTGGAACAGCCAGCTGGTGCGCTACGCGGGCTACCGGCAGCAGGATGGCTCT       c.780
 F  R  I  W  N  S  Q  L  V  R  Y  A  G  Y  R  Q  Q  D  G  S         p.260

          .         .         .       | 08 .         .         .    g.12914
 GTGCGGGGGGACCCAGCCAACGTGGAGATCACCGAG | CTCTGCATTCAGCACGGCTGGACC    c.840
 V  R  G  D  P  A  N  V  E  I  T  E   | L  C  I  Q  H  G  W  T      p.280

          .         .         .         .         .         .       g.12974
 CCAGGAAACGGTCGCTTCGACGTGCTGCCCCTGCTGCTGCAGGCCCCAGATGATCCCCCA       c.900
 P  G  N  G  R  F  D  V  L  P  L  L  L  Q  A  P  D  D  P  P         p.300

          .         .         .         .         .       | 09 .    g.13138
 GAACTCTTCCTTCTGCCCCCCGAGCTGGTCCTTGAGGTGCCCCTGGAGCACCCCAC | GCTG    c.960
 E  L  F  L  L  P  P  E  L  V  L  E  V  P  L  E  H  P  T  |  L      p.320

          .         .         .         .         .         .       g.13198
 GAGTGGTTTGCAGCCCTGGGCCTGCGCTGGTACGCCCTCCCGGCAGTGTCCAACATGCTG       c.1020
 E  W  F  A  A  L  G  L  R  W  Y  A  L  P  A  V  S  N  M  L         p.340

          .         .         .         .         .         .       g.13258
 CTGGAAATTGGGGGCCTGGAGTTCCCCGCAGCCCCCTTCAGTGGCTGGTACATGAGCACT       c.1080
 L  E  I  G  G  L  E  F  P  A  A  P  F  S  G  W  Y  M  S  T         p.360

          .         .         .         .         .  | 10      .    g.14451
 GAGATCGGCACGAGGAACCTGTGTGACCCTCACCGCTACAACATCCTGGAG | GATGTGGCT    c.1140
 E  I  G  T  R  N  L  C  D  P  H  R  Y  N  I  L  E   | D  V  A      p.380

          .         .         .         .         .         .       g.14511
 GTCTGCATGGACCTGGATACCCGGACCACCTCGTCCCTGTGGAAAGACAAGGCAGCAGTG       c.1200
 V  C  M  D  L  D  T  R  T  T  S  S  L  W  K  D  K  A  A  V         p.400

          .         .         .    | 11    .         .         .    g.15202
 GAAATCAACGTGGCCGTGCTGCACAGTTACCAG | CTAGCCAAAGTCACCATCGTGGACCAC    c.1260
 E  I  N  V  A  V  L  H  S  Y  Q   | L  A  K  V  T  I  V  D  H      p.420

          .         .         .         .         .         .       g.15262
 CACGCCGCCACGGCCTCTTTCATGAAGCACCTGGAGAATGAGCAGAAGGCCAGGGGGGGC       c.1320
 H  A  A  T  A  S  F  M  K  H  L  E  N  E  Q  K  A  R  G  G         p.440

          .         .         .         .         .         .       g.15322
 TGCCCTGCAGACTGGGCCTGGATCGTGCCCCCCATCTCGGGCAGCCTCACTCCTGTTTTC       c.1380
 C  P  A  D  W  A  W  I  V  P  P  I  S  G  S  L  T  P  V  F         p.460

          .         .         .         .         | 12         .    g.15500
 CATCAGGAGATGGTCAACTATTTCCTGTCCCCGGCCTTCCGCTACCAG | CCAGACCCCTGG    c.1440
 H  Q  E  M  V  N  Y  F  L  S  P  A  F  R  Y  Q   | P  D  P  W      p.480

          .         .         .         .         .         .       g.15560
 AAGGGGAGTGCCGCCAAGGGCACCGGCATCACCAGGAAGAAGACCTTTAAAGAAGTGGCC       c.1500
 K  G  S  A  A  K  G  T  G  I  T  R  K  K  T  F  K  E  V  A         p.500

    | 13     .         .         .         .         .         .    g.15823
 AA | CGCCGTGAAGATCTCCGCCTCGCTCATGGGCACGGTGATGGCGAAGCGAGTGAAGGCG    c.1560
 N  |  A  V  K  I  S  A  S  L  M  G  T  V  M  A  K  R  V  K  A      p.520

          .         .         .         .         .         .       g.15883
 ACAATCCTGTATGGCTCCGAGACCGGCCGGGCCCAGAGCTACGCACAGCAGCTGGGGAGA       c.1620
 T  I  L  Y  G  S  E  T  G  R  A  Q  S  Y  A  Q  Q  L  G  R         p.540

          .         .        | 14.         .         .         .    g.16177
 CTCTTCCGGAAGGCTTTTGATCCCCGG | GTCCTGTGTATGGATGAGTATGACGTGGTGTCC    c.1680
 L  F  R  K  A  F  D  P  R   | V  L  C  M  D  E  Y  D  V  V  S      p.560

          .         .         .         .         .         .       g.16237
 CTCGAACACGAGACGCTGGTGCTGGTGGTAACCAGCACATTTGGGAATGGGGATCCCCCG       c.1740
 L  E  H  E  T  L  V  L  V  V  T  S  T  F  G  N  G  D  P  P         p.580

          .   | 15     .         .         .         .         .    g.20419
 GAGAATGGAGAG | AGCTTTGCAGCTGCCCTGATGGAGATGTCCGGCCCCTACAACAGCTCC    c.1800
 E  N  G  E   | S  F  A  A  A  L  M  E  M  S  G  P  Y  N  S  S      p.600

          .         . | 16       .         .         .         .    g.20873
 CCTCGGCCGGAACAGCACAA | GAGTTATAAGATCCGCTTCAACAGCATCTCCTGCTCAGAC    c.1860
 P  R  P  E  Q  H  K  |  S  Y  K  I  R  F  N  S  I  S  C  S  D      p.620

          .         .         .         .         .         .       g.20933
 CCACTGGTGTCCTCTTGGCGGCGGAAGAGGAAGGAGTCCAGTAACACAGACAGTGCAGGG       c.1920
 P  L  V  S  S  W  R  R  K  R  K  E  S  S  N  T  D  S  A  G         p.640

          .        | 17.         .         .         .         .    g.21089
 GCCCTGGGCACCCTCAG | GTTCTGTGTGTTCGGGCTCGGCTCCCGGGCATACCCCCACTTC    c.1980
 A  L  G  T  L  R  |  F  C  V  F  G  L  G  S  R  A  Y  P  H  F      p.660

          .         .         .         .         .         .       g.21149
 TGCGCCTTTGCTCGTGCCGTGGACACACGGCTGGAGGAACTGGGCGGGGAGCGGCTGCTG       c.2040
 C  A  F  A  R  A  V  D  T  R  L  E  E  L  G  G  E  R  L  L         p.680

          .         .         .         .         .         .       g.21209
 CAGCTGGGCCAGGGCGACGAGCTGTGCGGCCAGGAGGAGGCCTTCCGAGGCTGGGCCCAG       c.2100
 Q  L  G  Q  G  D  E  L  C  G  Q  E  E  A  F  R  G  W  A  Q         p.700

          .   | 18     .         .         .         .         .    g.22922
 GCTGCCTTCCAG | GCCGCCTGTGAGACCTTCTGTGTGGGAGAGGATGCCAAGGCCGCCGCC    c.2160
 A  A  F  Q   | A  A  C  E  T  F  C  V  G  E  D  A  K  A  A  A      p.720

          .         .         .         .         .         .       g.22982
 CGAGACATCTTCAGCCCCAAACGGAGCTGGAAGCGCCAGAGGTACCGGCTGAGCGCCCAG       c.2220
 R  D  I  F  S  P  K  R  S  W  K  R  Q  R  Y  R  L  S  A  Q         p.740

          .         .      | 19  .         .         .         .    g.23168
 GCCGAGGGCCTGCAGTTGCTGCCAG | GTCTGATCCACGTGCACAGGCGGAAGATGTTCCAG    c.2280
 A  E  G  L  Q  L  L  P  G |   L  I  H  V  H  R  R  K  M  F  Q      p.760

          .         .         .         .     | 20   .         .    g.23358
 GCTACAATCCGCTCAGTGGAAAACCTGCAAAGCAGCAAGTCCAC | GAGGGCCACCATCCTG    c.2340
 A  T  I  R  S  V  E  N  L  Q  S  S  K  S  T  |  R  A  T  I  L      p.780

          .         .         .         .         .         .       g.23418
 GTGCGCCTGGACACCGGAGGCCAGGAGGGGCTGCAGTACCAGCCGGGGGACCACATAGGT       c.2400
 V  R  L  D  T  G  G  Q  E  G  L  Q  Y  Q  P  G  D  H  I  G         p.800

          .         .         .         .         .         .       g.23478
 GTCTGCCCGCCCAACCGGCCCGGCCTTGTGGAGGCGCTGCTGAGCCGCGTGGAGGACCCG       c.2460
 V  C  P  P  N  R  P  G  L  V  E  A  L  L  S  R  V  E  D  P         p.820

          .         .         .         .         .   | 21     .    g.24067
 CCGGCGCCCACTGAGCCCGTGGCAGTAGAGCAGCTGGAGAAGGGCAGCCCTG | GTGGCCCT    c.2520
 P  A  P  T  E  P  V  A  V  E  Q  L  E  K  G  S  P  G |   G  P      p.840

          .         .         .         .         .         .       g.24127
 CCCCCCGGCTGGGTGCGGGACCCCCGGCTGCCCCCGTGCACGCTGCGCCAGGCTCTCACC       c.2580
 P  P  G  W  V  R  D  P  R  L  P  P  C  T  L  R  Q  A  L  T         p.860

          .         .         .         .         .         .       g.24187
 TTCTTCCTGGACATCACCTCCCCACCCAGCCCTCAGCTCTTGCGGCTGCTCAGCACCTTG       c.2640
 F  F  L  D  I  T  S  P  P  S  P  Q  L  L  R  L  L  S  T  L         p.880

          .         .         .         .      | 22  .         .    g.24556
 GCAGAAGAGCCCAGGGAACAGCAGGAGCTGGAGGCCCTCAGCCAG | GATCCCCGACGCTAC    c.2700
 A  E  E  P  R  E  Q  Q  E  L  E  A  L  S  Q   | D  P  R  R  Y      p.900

          .         .         .         .         .         .       g.24616
 GAGGAGTGGAAGTGGTTCCGCTGCCCCACGCTGCTGGAGGTGCTGGAGCAGTTCCCGTCG       c.2760
 E  E  W  K  W  F  R  C  P  T  L  L  E  V  L  E  Q  F  P  S         p.920

          .         .         .         .         .         .       g.24676
 GTGGCGCTGCCTGCCCCACTGCTCCTCACCCAGCTGCCTCTGCTCCAGCCCCGGTACTAC       c.2820
 V  A  L  P  A  P  L  L  L  T  Q  L  P  L  L  Q  P  R  Y  Y         p.940

          .         .         .         .         .         .       g.24736
 TCAGTCAGCTCGGCACCCAGCACCCACCCAGGAGAGATCCACCTCACTGTAGCTGTGCTG       c.2880
 S  V  S  S  A  P  S  T  H  P  G  E  I  H  L  T  V  A  V  L         p.960

          .       | 23 .         .         .         .         .    g.24887
 GCATACAGGACTCAGG | ATGGGCTGGGCCCCCTGCACTATGGAGTCTGCTCCACGTGGCTA    c.2940
 A  Y  R  T  Q  D |   G  L  G  P  L  H  Y  G  V  C  S  T  W  L      p.980

          .         .         .         .     | 24   .         .    g.26311
 AGCCAGCTCAAGCCCGGAGACCCTGTGCCCTGCTTCATCCGGGG | GGCTCCCTCCTTCCGG    c.3000
 S  Q  L  K  P  G  D  P  V  P  C  F  I  R  G  |  A  P  S  F  R      p.1000

          .         .         .         .         .         .       g.26371
 CTGCCACCCGATCCCAGCTTGCCCTGCATCCTGGTGGGTCCAGGCACTGGCATTGCCCCC       c.3060
 L  P  P  D  P  S  L  P  C  I  L  V  G  P  G  T  G  I  A  P         p.1020

          .         .         .         .       | 25 .         .    g.27189
 TTCCGGGGATTCTGGCAGGAGCGGCTGCATGACATTGAGAGCAAAG | GGCTGCAGCCCACT    c.3120
 F  R  G  F  W  Q  E  R  L  H  D  I  E  S  K  G |   L  Q  P  T      p.1040

          .         .         .         .         .         .       g.27249
 CCCATGACTTTGGTGTTCGGCTGCCGATGCTCCCAACTTGACCATCTCTACCGCGACGAG       c.3180
 P  M  T  L  V  F  G  C  R  C  S  Q  L  D  H  L  Y  R  D  E         p.1060

          .         .         .         .         .         .       g.27309
 GTGCAGAACGCCCAGCAGCGCGGGGTGTTTGGCCGAGTCCTCACCGCCTTCTCCCGGGAA       c.3240
 V  Q  N  A  Q  Q  R  G  V  F  G  R  V  L  T  A  F  S  R  E         p.1080

          .      | 26  .         .         .         .         .    g.27713
 CCTGACAACCCCAAG | ACCTACGTGCAGGACATCCTGAGGACGGAGCTGGCTGCGGAGGTG    c.3300
 P  D  N  P  K   | T  Y  V  Q  D  I  L  R  T  E  L  A  A  E  V      p.1100

          .         .         .         .         .         .       g.27773
 CACCGCGTGCTGTGCCTCGAGCGGGGCCACATGTTTGTCTGCGGCGATGTTACCATGGCA       c.3360
 H  R  V  L  C  L  E  R  G  H  M  F  V  C  G  D  V  T  M  A         p.1120

          .         .         .         .         .         .       g.27833
 ACCAACGTCCTGCAGACCGTGCAGCGCATCCTGGCGACGGAGGGCGACATGGAGCTGGAC       c.3420
 T  N  V  L  Q  T  V  Q  R  I  L  A  T  E  G  D  M  E  L  D         p.1140

          .         .         . | 27       .         .         .    g.27982
 GAGGCCGGCGACGTCATCGGCGTGCTGCGG | GATCAGCAACGCTACCACGAAGACATTTTC    c.3480
 E  A  G  D  V  I  G  V  L  R   | D  Q  Q  R  Y  H  E  D  I  F      p.1160

          .         .         .         .         .         .       g.28042
 GGGCTCACGCTGCGCACCCAGGAGGTGACAAGCCGCATACGCACCCAGAGCTTTTCCTTG       c.3540
 G  L  T  L  R  T  Q  E  V  T  S  R  I  R  T  Q  S  F  S  L         p.1180

          .         .         .         .         .         .       g.28102
 CAGGAGCGTCAGTTGCGGGGCGCAGTGCCCTGGGCGTTCGACCCTCCCGGCTCAGACACC       c.3600
 Q  E  R  Q  L  R  G  A  V  P  W  A  F  D  P  P  G  S  D  T         p.1200

          .                                                         g.28114
 AACAGCCCCTGA                                                       c.3612
 N  S  P  X                                                         p.1203

          .         .         .         .         .         .       g.28174
 gagccgcctggctttcccttccagttccgggagagcggctgcccgactcaggtccgcccg       c.*60

          .         .         .         .         .         .       g.28234
 accaggatcagccccgctcctcccctcttgaggtggtgccttctcacatctgtccagagg       c.*120

          .         .         .         .         .         .       g.28294
 ctgcaaggattcagcattattcctccaggaaggagcaaaacgcctcttttccctctctag       c.*180

          .         .         .         .         .         .       g.28354
 gcctgttgcctcgggcctgggtccgccttaatctggaaggcccctcccagcagcggtacc       c.*240

          .         .         .         .         .         .       g.28414
 ccagggcctactgccacccgcttcctgtttcttagtcgaatgttagattcctcttgcctc       c.*300

          .         .         .         .         .         .       g.28474
 tctcaggagtatcttacctgtaaagtctaatctctaaatcaagtatttattattgaagat       c.*360

          .         .         .         .         .         .       g.28534
 ttaccataagggactgtgccagatgttaggagaactactaaagtgcctaccccagctcat       c.*420

          .                                                         g.28544
 gtggattaca                                                         c.*430

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Nitric oxide synthase 3 (endothelial cell) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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