Obg-like ATPase 1 (OLA1) - coding DNA reference sequence

(used for variant description)

(last modified April 4, 2026)


This file was created to facilitate the description of sequence variants on transcript NM_013341.3 in the OLA1 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000002.11, covering OLA1 transcript NM_013341.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                                    g.5006
                                                       ggtctg       c.-181

 .         .         .         .         .         .                g.5066
 cgcgcaggtgccgctcggcgcccggcccgcccgttccgccgctgtcgccgccgtcgtgcg       c.-121

 .         .         .         .         .         .                g.5126
 tgccgctcggcggaggggacgggcctgcgttctctcctccttcctccccgcctccagctg       c.-61

 .         .         .         .         .         .                g.5186
 ccggcaggacctttctctcgctgccgctgggaccccgtgtcatcgcccaggccgagcacg       c.-1

  | 02       .         .         .         .         .         .    g.6882
  | ATGCCCCCTAAAAAGGGAGGTGATGGAATTAAACCACCCCCAATCATTGGAAGATTTGGA    c.60
  | M  P  P  K  K  G  G  D  G  I  K  P  P  P  I  I  G  R  F  G      p.20

          .         .         .         .  | 03      .         .    g.24205
 ACCTCACTGAAAATTGGTATTGTTGGATTGCCAAATGTTGG | GAAATCTACTTTCTTCAAT    c.120
 T  S  L  K  I  G  I  V  G  L  P  N  V  G  |  K  S  T  F  F  N      p.40

          .         .         .         .         .         .       g.24265
 GTGTTAACCAATAGTCAGGCTTCAGCAGAAAACTTCCCGTTCTGCACTATTGATCCTAAT       c.180
 V  L  T  N  S  Q  A  S  A  E  N  F  P  F  C  T  I  D  P  N         p.60

          .         .         .         .         .         .       g.24325
 GAGAGCAGAGTACCTGTGCCAGATGAAAGGTTTGACTTTCTTTGTCAATACCACAAACCA       c.240
 E  S  R  V  P  V  P  D  E  R  F  D  F  L  C  Q  Y  H  K  P         p.80

       | 04  .         .         .         .         .         .    g.30532
 GCAAG | CAAAATTCCTGCCTTTCTAAATGTGGTGGATATTGCTGGCCTTGTGAAAGGAGCT    c.300
 A  S  |  K  I  P  A  F  L  N  V  V  D  I  A  G  L  V  K  G  A      p.100

          .         .         .         .         .         .       g.30592
 CACAATGGGCAGGGCCTGGGGAATGCTTTTTTATCTCATATTAGTGCCTGTGATGGCATC       c.360
 H  N  G  Q  G  L  G  N  A  F  L  S  H  I  S  A  C  D  G  I         p.120

          .    | 05    .         .         .         .         .    g.111684
 TTTCATCTAACAC | GTGCTTTTGAAGATGATGATATCACGCACGTTGAAGGAAGTGTAGAT    c.420
 F  H  L  T  R |   A  F  E  D  D  D  I  T  H  V  E  G  S  V  D      p.140

          .         .         .         .         .         .       g.111744
 CCTATTCGAGATATAGAAATAATACATGAAGAGCTTCAGCTTAAAGATGAGGAAATGATT       c.480
 P  I  R  D  I  E  I  I  H  E  E  L  Q  L  K  D  E  E  M  I         p.160

          .         .         .         .         .         .       g.111804
 GGGCCCATTATAGATAAACTAGAAAAGGTGGCTGTGAGAGGAGGAGATAAAAAACTAAAA       c.540
 G  P  I  I  D  K  L  E  K  V  A  V  R  G  G  D  K  K  L  K         p.180

           | 06        .         .         .         .         .    g.130013
 CCTGAATAT | GATATAATGTGCAAAGTAAAATCCTGGGTTATAGATCAAAAGAAACCTGTT    c.600
 P  E  Y   | D  I  M  C  K  V  K  S  W  V  I  D  Q  K  K  P  V      p.200

          .         .         . | 07       .         .         .    g.130390
 CGCTTCTATCATGATTGGAATGACAAAGAG | ATTGAAGTGTTGAATAAACACTTATTTTTG    c.660
 R  F  Y  H  D  W  N  D  K  E   | I  E  V  L  N  K  H  L  F  L      p.220

          .         .         .         .         .         .       g.130450
 ACTTCAAAACCAATGGTCTACTTGGTTAATCTTTCTGAAAAAGACTACATTAGAAAGAAA       c.720
 T  S  K  P  M  V  Y  L  V  N  L  S  E  K  D  Y  I  R  K  K         p.240

          | 08         .         .         .         .         .    g.171625
 AACAAATG | GTTGATAAAAATTAAAGAGTGGGTGGACAAGTATGACCCAGGTGCTTTGGTC    c.780
 N  K  W  |  L  I  K  I  K  E  W  V  D  K  Y  D  P  G  A  L  V      p.260

          .         .         .         .         .         .       g.171685
 ATTCCTTTTAGTGGGGCCTTGGAACTCAAGTTGCAAGAATTGAGTGCTGAGGAGAGACAG       c.840
 I  P  F  S  G  A  L  E  L  K  L  Q  E  L  S  A  E  E  R  Q         p.280

          .         .          | 09        .         .         .    g.172420
 AAGTATCTGGAAGCGAACATGACACAAAG | TGCTTTGCCAAAGATCATTAAGGCTGGGTTT    c.900
 K  Y  L  E  A  N  M  T  Q  S  |  A  L  P  K  I  I  K  A  G  F      p.300

          .         .         .         .         .         .       g.172480
 GCAGCACTCCAACTAGAATACTTTTTCACTGCAGGCCCAGATGAAGTGCGTGCATGGACC       c.960
 A  A  L  Q  L  E  Y  F  F  T  A  G  P  D  E  V  R  A  W  T         p.320

        | 10 .         .         .         .         .         .    g.174601
 ATCAGG | AAAGGGACTAAGGCTCCTCAGGCTGCAGGAAAGATTCACACAGATTTTGAAAAG    c.1020
 I  R   | K  G  T  K  A  P  Q  A  A  G  K  I  H  T  D  F  E  K      p.340

          .         .         .         .         .         .       g.174661
 GGATTCATTATGGCTGAAGTAATGAAATACGAAGATTTTAAAGAGGAAGGTTCTGAAAAT       c.1080
 G  F  I  M  A  E  V  M  K  Y  E  D  F  K  E  E  G  S  E  N         p.360

           | 11        .         .         .         .         .    g.178161
 GCAGTCAAG | GCTGCTGGAAAGTACAGACAACAAGGCAGAAATTATATTGTTGAAGATGGA    c.1140
 A  V  K   | A  A  G  K  Y  R  Q  Q  G  R  N  Y  I  V  E  D  G      p.380

          .         .         .         .         .                 g.178212
 GATATTATCTTCTTCAAATTTAACACACCTCAACAACCGAAGAAGAAATAA                c.1191
 D  I  I  F  F  K  F  N  T  P  Q  Q  P  K  K  K  X                  p.396

          .         .         .         .         .         .       g.178272
 aatttagttattgctcagataaacatacaacttccaaaaggcatctgatttttaaaaaat       c.*60

          .         .         .         .         .         .       g.178332
 taaaatttctgaaaaccaatgcgacaaataaagttggggagatgggaatctttgacaaac       c.*120

          .         .         .         .         .         .       g.178392
 aaattatttttatttgttttaaaattaaaatactgtgtacccccccccccccatgaaatg       c.*180

          .         .         .         .         .         .       g.178452
 caggttcactaaatgtgaacagctttgcttttcacgtgattaagaccctactccaaattg       c.*240

          .         .         .         .         .         .       g.178512
 tagaagcttttcaggaaccatattactctcatgatacttcattaatctccatcatgtatg       c.*300

          .         .         .         .         .         .       g.178572
 ccaagcctgacacatttgacagtgaggacaatgtggcttgctcctttttgaatctacaga       c.*360

          .         .         .         .         .         .       g.178632
 taatgcatgttttacagtactccagatgtctacactcaataaaacatttgacaaaaccag       c.*420

          .         .         .         .         .         .       g.178692
 ccttggtgtgtttggggatgtctgtattgactgactgtggtgtgctgaatgcgatacggc       c.*480

          .         .         .         .         .         .       g.178752
 acctggtggttgctgattacagaattttaaggcgtgtgtatgacacagtaactggcagtg       c.*540

          .         .         .         .         .         .       g.178812
 tggggcagctgcaattgtatcttaaaagtgagtctttcatgggaatcagaagaatagtat       c.*600

          .         .         .         .         .         .       g.178872
 accagggatttgtctcaaaaaagttaattaatttatagatcaacatttattgaaagatga       c.*660

          .         .         .         .         .         .       g.178932
 tagcaatgatattatgagggatatgagataggtgactgaccacaaagaagaaaattctgt       c.*720

          .         .         .         .         .         .       g.178992
 ctcaaaaattaaagaattttgtttgttattgttgttctgaccatattgaaaagaggttca       c.*780

          .         .         .         .         .         .       g.179052
 cttttaatctttcctttgaaattattaaattgtaaaaactgacccattgatgtctggtgg       c.*840

          .         .         .         .         .         .       g.179112
 gttatgttttgcttcaattcagcaatgtgtataaaagttcctacactgattttgaaatac       c.*900

          .         .         .         .         .         .       g.179172
 taagatcagactttgaaaattttaaaaattctttcattcttacttttcagatatttgaga       c.*960

          .         .         .         .         .         .       g.179232
 gcagtcgaagtggtagtatgggtaagttaagcacttcttaacattgtagcagaaaattcc       c.*1020

          .         .         .         .         .         .       g.179292
 aaaagaaagactagaacaaattggtaatttggagaccctttgccacttagccttctcttg       c.*1080

          .         .         .         .         .         .       g.179352
 tgatgatggcctgaaagctctctcggccctgagcctccctttctctcccatgtttccatt       c.*1140

          .         .         .         .         .         .       g.179412
 cctgtgagacctcccttccttgtccttgtcctctgcccttttgtgctcttctgtgatcac       c.*1200

          .         .         .         .         .         .       g.179472
 aggaccatttccatggaatgcagattcatacccagccagcctttgcctctactgtatcgc       c.*1260

          .         .         .         .         .         .       g.179532
 tttgggactttaaagatgcagaagtattagaacacacacaaacttaaaatggaaagttac       c.*1320

          .         .         .         .         .         .       g.179592
 caaatgtagcactagaggcaagaaaaggggtgattttttaaagatttggctatacttaag       c.*1380

          .         .         .         .         .         .       g.179652
 atatttaaagaggatgaggttgagtcgtgagtataatttagaagctctccagtgagtatt       c.*1440

          .         .         .         .         .         .       g.179712
 tttttagtatcaaatagtgatcttcttttgctaacataaaaatgagtaaactacagcaga       c.*1500

          .         .         .         .         .         .       g.179772
 gaaataagaataaaactaatgaagggttttttaaaagaactaaataaaacaaataaaact       c.*1560

          .         .         .         .         .         .       g.179832
 aggctacaggtatagctgaccaagtttgctgtgaaaaatccttgttatatctatttctgt       c.*1620

          .         .         .         .         .         .       g.179892
 attggagtaatgtgtagattagtggattgttagggatttcagcagtataagaaagaatca       c.*1680

          .         .         .         .         .         .       g.179952
 aatatcttgcttttgggtcttctccaaagtaaattgcatggacttcttaaagaagtttga       c.*1740

          .         .         .         .         .         .       g.180012
 aatcagtaaaaagacattaggatcatgcaattttactttgtctagcttctaatgtggtaa       c.*1800

          .         .         .         .         .         .       g.180072
 attgcacattgtgcaacagaaccattaataaaagaaaggagttagttttgaggtaactgc       c.*1860

          .         .         .         .         .         .       g.180132
 attcattaggggctgaaaataaatgttaaaaatgtttaatttggttagaagttctacaac       c.*1920

          .         .         .         .         .         .       g.180192
 attgtatgtacatatacaaaatttcattttctctgaaagtcgagaattccaagaactgtt       c.*1980

          .         .         .         .         .         .       g.180252
 acatataatcatatatatgcctatatctaaacgttttccctcctttaatattgataaagt       c.*2040

          .         .         .         .         .         .       g.180312
 taatatattttaggatgttatgtaaatatttttgcatgtatctgtagctccatcttaatc       c.*2100

          .         .         .         .         .         .       g.180372
 aaatttatggttaaaagagatttgaggccaggcgtggaggctcacacctataatcccaac       c.*2160

          .         .         .         .         .         .       g.180432
 actttgggaggccgaggtgggaggatcacttgagcacaggagtttgagaccagcctgtgc       c.*2220

          .         .         .         .         .         .       g.180492
 aacatcatgaaacatcatctctacataaaaaaatacatatatacaaaaattagctgggca       c.*2280

          .         .         .         .         .         .       g.180552
 tcatggcacacacctgtagtcccagctacttaggaggctgagatgggaggattgatcgat       c.*2340

          .         .         .         .         .         .       g.180612
 cgcttgagcctgggaggtggaggctactgtgagccatgatcatgccactgcactccagcc       c.*2400

          .         .         .         .         .         .       g.180672
 tgggcaacagagtgagaccctgtctccaaagagaaagagaaacttgagaaggcttgtgcc       c.*2460

          .         .         .         .         .         .       g.180732
 caaagcttgaagaaagattgtaatagcatttagttgtgttttatcatgttatcttcataa       c.*2520

          .         .         .         .         .         .       g.180792
 catgcattttgcatatggctcagagcagagccggatctcccaaggaagcacaaatagttt       c.*2580

          .         .         .         .         .         .       g.180852
 ttgtcgctaacttagttatgagtgaagcctctgttcacttataacttgccagtttcattg       c.*2640

          .         .         .         .         .         .       g.180912
 gtggaataagtccccttactcatgattcatcaatattcctatattaaaattccagtttga       c.*2700

          .         .         .         .         .         .       g.180972
 tgtttgtctctagttgtctgtgtataatatttccaaagctcctttgtaaaccccgtctcc       c.*2760

          .         .         .         .         .         .       g.181032
 tttcattcagagagtcagagacggtatctcctcctcctgcctcttctattgttctgatta       c.*2820

          .         .         .         .         .         .       g.181092
 gtctacttaaattcacttgatgctctttttattttacaagagacttgagaaatgtcggtt       c.*2880

          .         .         .         .         .         .       g.181152
 gttcctaatggcaaactactttagctgggaaaattcatttcaacttattttaagcttgta       c.*2940

          .         .         .                                     g.181191
 aaatacactgtggtgataaaataaaagagctgggtttga                            c.*2979

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Obg-like ATPase 1 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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