peroxisomal biogenesis factor 10 (PEX10) - coding DNA reference sequence

(used for variant description)

(last modified September 8, 2020)


This file was created to facilitate the description of sequence variants on transcript NM_153818.1 in the PEX10 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_008342.1, covering PEX10 transcript NM_153818.1.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                                                    g.5009
                                                    atcagttct       c.-61

 .         .         .         .         .         .                g.5069
 cgcccgtctgggcgtgggcgtggccggcgtggctgctcgggaccacccgaacccgcggcc       c.-1

          .         .         .         .         .         .       g.5129
 ATGGCCCCGGCCGCCGCCAGCCCCCCGGAGGTGATCCGCGCGGCGCAGAAGGACGAGTAC       c.60
 M  A  P  A  A  A  S  P  P  E  V  I  R  A  A  Q  K  D  E  Y         p.20

          .         .         .         .         .   | 02     .    g.7128
 TACCGCGGTGGGCTGCGGAGCGCGGCGGGCGGCGCCCTGCACAGCCTGGCGG | GTGCGAGG    c.120
 Y  R  G  G  L  R  S  A  A  G  G  A  L  H  S  L  A  G |   A  R      p.40

          .         .         .         .         .         .       g.7188
 AAGTGGCTGGAGTGGAGGAAGGAGGTTGAGCTGCTCTCAGATGTGGCCTACTTTGGCCTC       c.180
 K  W  L  E  W  R  K  E  V  E  L  L  S  D  V  A  Y  F  G  L         p.60

          .    | 03    .         .         .         .         .    g.8760
 ACCACACTTGCAG | GCTACCAGACCCTGGGGGAGGAGTACGTCAGCATCATCCAGGTGGAC    c.240
 T  T  L  A  G |   Y  Q  T  L  G  E  E  Y  V  S  I  I  Q  V  D      p.80

          .         .         .         .         .         .       g.8820
 CCATCGCGGATACATGTGCCCTCCTCGCTGCGCCGTGGCGTGCTGGTGACACTGCATGCC       c.300
 P  S  R  I  H  V  P  S  S  L  R  R  G  V  L  V  T  L  H  A         p.100

          .         .         .         .         .         .       g.8880
 GTCCTGCCCTACCTGCTGGACAAGGCCCTGCTCCCCCTGGAGCAGGAGCTGCAGGCTGAC       c.360
 V  L  P  Y  L  L  D  K  A  L  L  P  L  E  Q  E  L  Q  A  D         p.120

          .         .         .         .         .         .       g.8940
 CCCGACAGTGGGCGACCCTTGCAGGGGAGCCTGGGGCCAGGTGGGCGTGGCTGCTCAGGG       c.420
 P  D  S  G  R  P  L  Q  G  S  L  G  P  G  G  R  G  C  S  G         p.140

          .         .         .         .         .         .       g.9000
 GCGCGGCGCTGGATGCGTCACCACACGGCCACCCTGACTGAGCAGCAGAGGAGGGCGCTG       c.480
 A  R  R  W  M  R  H  H  T  A  T  L  T  E  Q  Q  R  R  A  L         p.160

          .         .         .         .         .         .       g.9060
 CTGCGGGCGGTCTTCGTCCTCAGACAGGGCCTCGCCTGCCTCCAGCGGCTACATGTTGCC       c.540
 L  R  A  V  F  V  L  R  Q  G  L  A  C  L  Q  R  L  H  V  A         p.180

          .         .         .         .         .         .       g.9120
 TGGTTTTACATCCACGGTGTCTTCTACCACCTGGCCAAGAGGCTCACGGGGATCACGTAC       c.600
 W  F  Y  I  H  G  V  F  Y  H  L  A  K  R  L  T  G  I  T  Y         p.200

  | 04       .         .         .         .         .         .    g.10676
  | CAGGCGCTGAGGCCAGATCCCCTCAGGGTCCTGATGAGTGTGGCGCCATCTGCCTTACAG    c.660
  | Q  A  L  R  P  D  P  L  R  V  L  M  S  V  A  P  S  A  L  Q      p.220

          .         .         .         .         .         .       g.10736
 CTCCGTGTCCGCAGCCTGCCCGGAGAGGACCTGAGGGCCCGTGTTAGCTACAGGCTGCTG       c.720
 L  R  V  R  S  L  P  G  E  D  L  R  A  R  V  S  Y  R  L  L         p.240

          .         .         .         .         .         .       g.10796
 GGGGTCATCTCACTGCTGCACCTGGTGCTGTCCATGGGGCTGCAGCTGTACGGTTTCAGG       c.780
 G  V  I  S  L  L  H  L  V  L  S  M  G  L  Q  L  Y  G  F  R         p.260

          .         .         .         .         .       | 05 .    g.10956
 CAGCGGCAGCGAGCCAGGAAGGAGTGGAGGCTGCACCGCGGCCTGTCTCACCGCAG | GGCC    c.840
 Q  R  Q  R  A  R  K  E  W  R  L  H  R  G  L  S  H  R  R  |  A      p.280

          .         .         .         .         .         .       g.11016
 TCCTTGGAGGAGAGAGCCGTTTCCAGAAACCCCCTGTGCACCCTGTGCCTGGAGGAGCGC       c.900
 S  L  E  E  R  A  V  S  R  N  P  L  C  T  L  C  L  E  E  R         p.300

          .         .         .         .         .         .       g.11076
 AGGCACCCAACAGCCACGCCCTGCGGCCACCTGTTCTGCTGGGAGTGCATCACCGCGTGG       c.960
 R  H  P  T  A  T  P  C  G  H  L  F  C  W  E  C  I  T  A  W         p.320

          .   | 06     .         .         .         .         .    g.11785
 TGCAGCAGCAAG | GCGGAGTGTCCCCTCTGCCGGGAGAAGTTCCCTCCCCAGAAGCTCATC    c.1020
 C  S  S  K   | A  E  C  P  L  C  R  E  K  F  P  P  Q  K  L  I      p.340

          .         .                                               g.11806
 TACCTTCGGCACTACCGCTGA                                              c.1041
 Y  L  R  H  Y  R  X                                                p.346

          .         .         .         .         .         .       g.11866
 gccggcgcccgggtgggcctggacacagatgacctctacgggagtctgaacgccaagatt       c.*60

          .         .         .         .         .         .       g.11926
 tagtctcaggattaaccttgcttgcacagaagttagaacactctcagttttttgtcatgt       c.*120

          .         .         .         .         .         .       g.11986
 aagatactaacctagccaccctgggagagaacagaaagctgtccctggctgcgctttctc       c.*180

          .         .         .         .         .         .       g.12046
 agccctgggaggggcgcctgaacccagaacatttccctaaccccaacctggtaggactca       c.*240

          .         .         .         .         .         .       g.12106
 gccacttcttcaggaatttcacttatttggacgggattttaggtttccctcccttcccca       c.*300

          .         .         .         .         .         .       g.12166
 aaccatacagttgagaagtaattcagaagtaggccagaagacactttattcgtttatatt       c.*360

          .         .         .         .         .         .       g.12226
 gtgagaaaacagccccatcaggcttgtgttaaggcaatggactgaatgagtgcgtgctgg       c.*420

          .         .         .         .         .         .       g.12286
 gtggggtggggcacggaggctggcgggttgcttcagccagtgcagtgagaacagcagccc       c.*480

          .         .         .         .         .         .       g.12346
 cacggccccatgggaggcggcgctgctctccccgagggcggctgggcagagcacatcccc       c.*540

          .         .         .         .         .         .       g.12406
 caggacttgatgaccacacggggcagagagaaaccaaccaaggccagcacctccgtcgga       c.*600

          .         .         .         .         .         .       g.12466
 agcatttggcacacacaccttcaatacacgtcaaggtcgcttccagttttagaaaacaga       c.*660

          .         .         .         .         .         .       g.12526
 aatctgcatctcagcctgagacgcacagagaggtctcttcctgacccagacgcactcacg       c.*720

          .         .         .         .         .         .       g.12586
 agccaggtcctgggggtatgggggctgccaggggcgcccgagccctctcctggggggcct       c.*780

          .         .         .         .         .         .       g.12646
 gctgggcaggcgacctgctgacccacggtcactgctgtgttcagcccctcagctcggccc       c.*840

          .         .         .         .         .         .       g.12706
 cagcctatttcccgcctccatttgatgtttccaggttttcaaaactgcatttaacctgcg       c.*900

          .         .         .         .         .         .       g.12766
 ccagagagttcaccgtaggcatctttaataaactaactccagcaaaatgtgggtacgtta       c.*960

                                                                    g.12770
 ctaa                                                               c.*964

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Peroxisomal biogenesis factor 10 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

Powered by LOVD v.3.0 Build 24
©2004-2020 Leiden University Medical Center