peroxisomal biogenesis factor 13 (PEX13) - coding DNA reference sequence

(used for variant description)

(last modified September 6, 2020)


This file was created to facilitate the description of sequence variants on transcript NM_002618.3 in the PEX13 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_008665.1, covering PEX13 transcript NM_002618.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                         .         .                g.5023
                                      gttgtgtcttacgctccaggtgc       c.-61

 .         .         .         .         .         .                g.5083
 tggtctacgcgggcctggacagtcaggggtaggagcgggagccgagaggaggcggaggag       c.-1

          .         .         .         .         .         .       g.5143
 ATGGCGTCCCAGCCGCCACCTCCCCCCAAACCCTGGGAGACCCGCCGAATTCCGGGAGCC       c.60
 M  A  S  Q  P  P  P  P  P  K  P  W  E  T  R  R  I  P  G  A         p.20

          .         .         .   | 02     .         .         .    g.18770
 GGACCGGGACCAGGACCGGGCCCCACTTTCCA | ATCTGCTGATTTGGGTCCTACTTTAATG    c.120
 G  P  G  P  G  P  G  P  T  F  Q  |  S  A  D  L  G  P  T  L  M      p.40

          .         .         .         .         .         .       g.18830
 ACAAGACCTGGACAACCAGCACTTACCAGAGTGCCCCCACCTATTCTTCCAAGGCCATCA       c.180
 T  R  P  G  Q  P  A  L  T  R  V  P  P  P  I  L  P  R  P  S         p.60

          .         .         .         .         .         .       g.18890
 CAGCAGACAGGAAGTAGCAGTGTGAACACTTTTAGACCTGCTTACAGTTCATTTTCTTCT       c.240
 Q  Q  T  G  S  S  S  V  N  T  F  R  P  A  Y  S  S  F  S  S         p.80

          .         .         .         .         .         .       g.18950
 GGATATGGTGCCTATGGAAATTCATTTTATGGAGGCTATAGTCCTTATAGTTATGGATAT       c.300
 G  Y  G  A  Y  G  N  S  F  Y  G  G  Y  S  P  Y  S  Y  G  Y         p.100

          .         .         .         .         .         .       g.19010
 AATGGGCTGGGCTACAACCGCCTCCGTGTAGATGATCTTCCACCCAGTAGATTTGTTCAG       c.360
 N  G  L  G  Y  N  R  L  R  V  D  D  L  P  P  S  R  F  V  Q         p.120

          .         .         .         .         .         .       g.19070
 CAAGCTGAAGAAAGCAGCAGGGGTGCATTTCAGTCCATTGAAAGTATTGTGCATGCATTT       c.420
 Q  A  E  E  S  S  R  G  A  F  Q  S  I  E  S  I  V  H  A  F         p.140

          .         .         .         .         .         .       g.19130
 GCCTCTGTCAGTATGATGATGGATGCTACCTTTTCAGCTGTCTATAACAGTTTCAGGGCT       c.480
 A  S  V  S  M  M  M  D  A  T  F  S  A  V  Y  N  S  F  R  A         p.160

          .         .         .         .         .         .       g.19190
 GTATTGGATGTAGCAAATCACTTTTCCCGATTGAAAATACACTTTACAAAAGTGTTTTCA       c.540
 V  L  D  V  A  N  H  F  S  R  L  K  I  H  F  T  K  V  F  S         p.180

          .         .         .         .         .         .       g.19250
 GCTTTTGCATTGGTTAGGACTATACGGTATCTTTACAGACGGCTACAGCGGATGTTAGGT       c.600
 A  F  A  L  V  R  T  I  R  Y  L  Y  R  R  L  Q  R  M  L  G         p.200

          .         .         .         .         .         .       g.19310
 TTAAGAAGAGGCTCTGAGAATGAAGACCTCTGGGCAGAGAGTGAAGGAACTGTGGCATGC       c.660
 L  R  R  G  S  E  N  E  D  L  W  A  E  S  E  G  T  V  A  C         p.220

          .         .         .         .         .         .       g.19370
 CTTGGTGCTGAGGACCGAGCAGCTACCTCAGCAAAATCTTGGCCAATATTCTTGTTCTTT       c.720
 L  G  A  E  D  R  A  A  T  S  A  K  S  W  P  I  F  L  F  F         p.240

          .         .         .         .         .         .       g.19430
 GCTGTTATCCTTGGTGGTCCTTACCTCATTTGGAAACTATTGTCTACTCACAGTGATGAA       c.780
 A  V  I  L  G  G  P  Y  L  I  W  K  L  L  S  T  H  S  D  E         p.260

         | 03.         .         .         .         .         .    g.33102
 GTAACAG | ACAGCATCAACTGGGCAAGTGGTGAGGATGACCATGTAGTTGCCAGAGCAGAA    c.840
 V  T  D |   S  I  N  W  A  S  G  E  D  D  H  V  V  A  R  A  E      p.280

          .         .         .         .         .         .       g.33162
 TATGATTTTGCTGCCGTATCTGAAGAAGAAATTTCTTTCCGGGCTGGTGATATGCTGAAC       c.900
 Y  D  F  A  A  V  S  E  E  E  I  S  F  R  A  G  D  M  L  N         p.300

          .    | 04    .         .         .         .         .    g.35842
 TTAGCTCTCAAAG | AACAACAACCCAAAGTGCGTGGTTGGCTTCTGGCTAGCCTTGATGGC    c.960
 L  A  L  K  E |   Q  Q  P  K  V  R  G  W  L  L  A  S  L  D  G      p.320

          .         .         .         .         .         .       g.35902
 CAAACAACAGGACTTATACCTGCGAATTATGTCAAAATTCTTGGCAAAAGAAAAGGTAGG       c.1020
 Q  T  T  G  L  I  P  A  N  Y  V  K  I  L  G  K  R  K  G  R         p.340

          .         .         .         .         .         .       g.35962
 AAAACGGTGGAATCAAGTAAAGTTTCCAAGCAGCAACAATCTTTTACCAACCCAACACTA       c.1080
 K  T  V  E  S  S  K  V  S  K  Q  Q  Q  S  F  T  N  P  T  L         p.360

          .         .         .         .         .         .       g.36022
 ACTAAAGGAGCCACGGTTGCTGATTCTTTGGATGAACAGGAAGCTGCCTTTGAATCTGTT       c.1140
 T  K  G  A  T  V  A  D  S  L  D  E  Q  E  A  A  F  E  S  V         p.380

          .         .         .         .         .         .       g.36082
 TTTGTTGAAACTAATAAGGTTCCAGTTGCACCTGATTCCATTGGGAAAGATGGAGAAAAG       c.1200
 F  V  E  T  N  K  V  P  V  A  P  D  S  I  G  K  D  G  E  K         p.400

          .                                                         g.36094
 CAAGATCTTTGA                                                       c.1212
 Q  D  L  X                                                         p.403

          .         .         .         .         .         .       g.36154
 tatctttcatgtttgcctgcagttgaacaatactttagagtactttttaaaattatttct       c.*60

          .         .         .         .         .         .       g.36214
 cacaaagaaatgaatgtacaatccaatgaaaacatttgttattggctatttcaggtgttt       c.*120

          .         .         .         .         .         .       g.36274
 tgctgctagaaattattaaagttacacactagtatgttggtctggtgacctggttacatt       c.*180

          .         .         .         .         .         .       g.36334
 ttattatacacattattggaccataaggacatttgtttcacctagattttaagattatgg       c.*240

          .         .         .         .         .         .       g.36394
 agactgctgtcatttttatcttatttaaatctctaggtttattggaagagtaagattgat       c.*300

          .         .         .         .         .         .       g.36454
 gaactatagcatgcacagtttggtacagtagagatcattaatacttttaaaagttctgca       c.*360

          .         .         .         .         .         .       g.36514
 ttaattgacttggaatccttagaaatggagtggtgacatgtcagtatgagaacaggcaaa       c.*420

          .         .         .         .         .         .       g.36574
 aggtaaatttttttttttttttacaaccttaagtaatctcaataataaaattttctgatc       c.*480

          .         .         .         .         .         .       g.36634
 tgtattatatccagtgttgggtttatattttcacccacaaacaactgacactgctatctt       c.*540

          .         .         .         .         .         .       g.36694
 ttactgtatttttaaaaatttaatttgaaaaggtcacccagaagcattctgaaggaaatg       c.*600

          .         .         .         .         .         .       g.36754
 gttctagaattatagagtatgtagccctaatagttttccctcctagcaaaaagtctgaaa       c.*660

          .         .         .         .         .         .       g.36814
 tttatctttcttacaaactgttccatttcttctaaggatcccttaattatttatctcttt       c.*720

          .         .         .         .         .         .       g.36874
 aagccaggcatggtggctcacgcctgtaatcccagcactttgggaggctgaggcgggcag       c.*780

          .         .         .         .         .         .       g.36934
 atcacctgaggttgggagttcaagaccaccctgaccaacatggagaaaccccatctttac       c.*840

          .         .         .         .         .         .       g.36994
 gaaaaatacaaaattagctaggtgtggtggcacatgcctgtaatcccagctactcgggag       c.*900

          .         .         .         .         .         .       g.37054
 gctgaggcaggagaattgcttgaaccccaggaggcggaggttacgctgagccggagatct       c.*960

          .         .         .         .         .         .       g.37114
 cgccattgcacttcagcctgggcaacaaaagcgaaactccatctcaaaaaataaaattat       c.*1020

          .         .         .         .         .         .       g.37174
 ttatttctttaaaatatgactagttttcatactgggtgaatcagaagtatatgaaaggta       c.*1080

          .         .         .         .         .         .       g.37234
 tactttcttttcctacaacaaatacttgagttcttttgagtttgcacttaatgatataat       c.*1140

          .         .         .         .         .         .       g.37294
 cagttataatagtaatttttaatattttcatagattgtttgcttctaccttgtgtaattt       c.*1200

          .         .         .         .         .         .       g.37354
 tttaaattccatatttaggatgctctgtaaatattgaaaatgtgtcacattggatacatt       c.*1260

          .         .         .         .         .         .       g.37414
 tttcttttaggtttagtttttactactgagacttatttatagtcttagtgctctattgcc       c.*1320

          .         .         .         .         .         .       g.37474
 atttagaatatgataatcctcatgcctttaatctcagcactttgggaggccaaggcgggc       c.*1380

          .         .         .         .         .         .       g.37534
 ggatcacctgcggtcaggagtttgagaccagcctggccaacacggtgaaaccctgtctct       c.*1440

          .         .         .         .         .         .       g.37594
 actaaaaatacgaaaattagctgggtgcagtggcgtgcacctgtagtcccagctactcag       c.*1500

          .         .         .         .         .         .       g.37654
 gaggctgaggcaggagaatcacttgaacccgggaggcagaggttgcagggagctgagatc       c.*1560

          .         .         .         .         .         .       g.37714
 atgccactgcactccagcctaggggacagagcaagactctgtctcaaaacaaacaaacaa       c.*1620

          .         .         .         .         .         .       g.37774
 aaaataataatacgataatgctatttgacgtgttttttggtttataatgattttaaatgc       c.*1680

          .         .         .         .         .         .       g.37834
 agttaactttcagtacactgaatatttccccagaaaattggaaacttcatatacttggct       c.*1740

          .         .         .         .         .         .       g.37894
 acgaacatactacagagtaatactatcaggaatacaggtgtataagaatacatttataga       c.*1800

          .         .         .         .         .         .       g.37954
 tattgttgaaaactttgaactgtttgataaaaattgtgatttagtattttttcttttgtc       c.*1860

          .         .         .         .         .         .       g.38014
 tttttttgaaacggagtctcactctgtcgcccaggctggagtccagtggcgcgatctcgg       c.*1920

          .         .         .         .         .         .       g.38074
 ctcactgcaagctccgcctcccgggttcacgccattctcctgcctcagcctcccgagtag       c.*1980

          .         .         .         .         .         .       g.38134
 ctgggactacaggcgcctgccaccaggcccggctaattttttttgtatttttagtagaga       c.*2040

          .         .         .         .         .         .       g.38194
 cggggtttcaccgtgttacccaggatggtctccatctcctgacctcgtgatgagcccgct       c.*2100

          .         .         .         .         .         .       g.38254
 tcggtctcccaaagtgttgggattacaggcgtgagccaccgcacccagcgatttagtatt       c.*2160

          .         .         .         .         .         .       g.38314
 tttttctaatagactatgttcaacaaataagtaattctcgaatagttcagattaaaacat       c.*2220

          .         .         .         .         .         .       g.38374
 acaggaaccaagtacatacccagcatagaagaactttactaaaggcttcttggaaagccc       c.*2280

          .         .         .         .         .         .       g.38434
 ttttttgaaacgacagtatcgtaagtaacatatcatttataatagaaatcttgacccagt       c.*2340

          .         .         .         .         .         .       g.38494
 gcagaaaaataaatatagtaaaatttatttatctttggccagttttccaacacccaggta       c.*2400

          .         .         .         .         .         .       g.38554
 ttagccttgaagttgaagagataaggtttcttgtatattatttttcatttgtgttctaca       c.*2460

          .         .         .         .         .         .       g.38614
 attaaaggttctgctttgatttgtcagataatttatagaaattttgttctcaaaacaaat       c.*2520

          .         .         .         .         .         .       g.38674
 gtttgataaaacagattattaaatttggggttgagatgtctaaattgaatgctagaagta       c.*2580

          .         .         .         .         .         .       g.38734
 aagtagaagtgaccactattaaagatgtatagggagaagagtacagcacaaagtgataaa       c.*2640

          .         .         .         .         .         .       g.38794
 atagtgacacttttgtaggggtgtttattgtttggttaagtctgctaaattacggtatgc       c.*2700

          .         .         .         .         .         .       g.38854
 attatctggtgactatttgtgcctgaaaattcgttttgtattaaaattctggagaaggaa       c.*2760

          .         .         .         .         .         .       g.38914
 ttcaggactagaataaagagaaattttgtaaccttttttatcatgacagttttagaataa       c.*2820

          .         .         .         .         .         .       g.38974
 tttttttagctgagattaaatgttcaaggctccaatattatttttaggaacttatttaag       c.*2880

          .         .         .         .         .         .       g.39034
 gagtgctactttacagaaattactaacacaccaaaacattattaattaaataaaatataa       c.*2940

          .         .         .         .         .         .       g.39094
 gtttacaataataaaacatgtttcttttaatttttctgattatattttatgagttcagaa       c.*3000

          .         .         .         .         .         .       g.39154
 aggaaatggtaaaagaactatacattttcatgttttaacattttatgtacgtacttgatt       c.*3060

          .         .         .         .         .         .       g.39214
 ctgtctgtgtcataattacacatttacttgaacacagctatcctttatcttgtgctttct       c.*3120

          .         .         .         .         .         .       g.39274
 ttaatagaaaaatgaacagaaactgaatgcagttaaatttttatttttagtaggttgtga       c.*3180

          .         .         .         .                           g.39314
 agttacttttactggagaaataaaaatatgttaaacttga                           c.*3220

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Peroxisomal biogenesis factor 13 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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