peroxisomal biogenesis factor 7 (PEX7) - coding DNA reference sequence

(used for variant description)

(last modified September 9, 2020)


This file was created to facilitate the description of sequence variants on transcript NM_000288.3 in the PEX7 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_008462.1, covering PEX7 transcript NM_000288.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5042
                   acttccgtccggtctgcctggtctctctaaccgcgccagtgt       c.-61

 .         .         .         .         .         .                g.5102
 gcctccgactcggaacggcttccgcggccggggcagcgagggccgggggcggcgggcggg       c.-1

          .         .         .         .         .         .       g.5162
 ATGAGTGCGGTGTGCGGTGGAGCGGCGCGGATGCTGCGGACGCCGGGACGCCACGGCTAC       c.60
 M  S  A  V  C  G  G  A  A  R  M  L  R  T  P  G  R  H  G  Y         p.20

          .         .         .         .         .         .       g.5222
 GCCGCCGAGTTCTCCCCGTACCTGCCGGGCCGCCTGGCCTGCGCCACCGCGCAGCACTAC       c.120
 A  A  E  F  S  P  Y  L  P  G  R  L  A  C  A  T  A  Q  H  Y         p.40

          . | 02       .         .         .         .         .    g.7700
 GGCATCGCGG | GCTGTGGAACCCTACTAATATTGGATCCAGATGAAGCTGGGCTAAGGCTT    c.180
 G  I  A  G |   C  G  T  L  L  I  L  D  P  D  E  A  G  L  R  L      p.60

          | 03         .         .         .         .         .    g.8807
 TTTAGAAG | CTTTGACTGGAATGATGGTTTGTTTGATGTGACTTGGAGTGAGAACAACGAA    c.240
 F  R  S  |  F  D  W  N  D  G  L  F  D  V  T  W  S  E  N  N  E      p.80

          .         .         .         .         .         .       g.8867
 CATGTCCTCATCACCTGTAGTGGCGATGGCTCGCTGCAGCTCTGGGACACTGCCAAAGCT       c.300
 H  V  L  I  T  C  S  G  D  G  S  L  Q  L  W  D  T  A  K  A         p.100

          .         .         .          | 04        .         .    g.28072
 GCAGGGCCACTGCAAGTCTATAAAGAACACGCTCAGGAG | GTGTATAGTGTTGATTGGAGC    c.360
 A  G  P  L  Q  V  Y  K  E  H  A  Q  E   | V  Y  S  V  D  W  S      p.120

          .         .         .         .         .        | 05.    g.28512
 CAAACCAGAGGTGAACAGCTTGTGGTGTCTGGCTCATGGGATCAAACTGTCAAATTG | TGG    c.420
 Q  T  R  G  E  Q  L  V  V  S  G  S  W  D  Q  T  V  K  L   | W      p.140

          .         .         .         .         .         .       g.28572
 GATCCAACTGTTGGAAAGTCTCTGTGCACCTTTAGAGGCCATGAAAGTATTATTTATAGC       c.480
 D  P  T  V  G  K  S  L  C  T  F  R  G  H  E  S  I  I  Y  S         p.160

          .         .         .         .       | 06 .         .    g.49077
 ACAATCTGGTCTCCCCACATCCCTGGTTGTTTTGCTTCAGCCTCAG | GTGATCAGACTCTG    c.540
 T  I  W  S  P  H  I  P  G  C  F  A  S  A  S  G |   D  Q  T  L      p.180

          .         .         .         .         .         .       g.49137
 AGAATATGGGATGTGAAGGCAGCAGGAGTAAGAATCGTGATTCCTGCACATCAGGCAGAA       c.600
 R  I  W  D  V  K  A  A  G  V  R  I  V  I  P  A  H  Q  A  E         p.200

          .         .         .    | 07    .         .         .    g.52353
 ATCTTGAGTTGTGACTGGTGTAAATACAATGAG | AATTTGCTGGTGACCGGGGCGGTTGAC    c.660
 I  L  S  C  D  W  C  K  Y  N  E   | N  L  L  V  T  G  A  V  D      p.220

          .         .         .         .         .         .       g.52413
 TGTAGTTTGAGAGGCTGGGACTTAAGGAATGTACGACAACCAGTGTTTGAACTTCTTGGT       c.720
 C  S  L  R  G  W  D  L  R  N  V  R  Q  P  V  F  E  L  L  G         p.240

          .         .        | 08.         .         .         .    g.54667
 CATACCTATGCTATTAGGAGGGTGAAA | TTTTCACCATTTCATGCTTCTGTGCTGGCCTCT    c.780
 H  T  Y  A  I  R  R  V  K   | F  S  P  F  H  A  S  V  L  A  S      p.260

          .         .    | 09    .         .         .         .    g.80615
 TGCTCGTATGATTTTACTGTAAG | ATTCTGGAACTTTTCAAAGCCTGACTCTCTTCTTGAA    c.840
 C  S  Y  D  F  T  V  R  |  F  W  N  F  S  K  P  D  S  L  L  E      p.280

          .         .         .         .         .         .       g.80675
 ACAGTGGAGCATCATACAGAGTTTACTTGTGGTTTAGACTTCAGTCTTCAGAGCCCCACT       c.900
 T  V  E  H  H  T  E  F  T  C  G  L  D  F  S  L  Q  S  P  T         p.300

     | 10    .         .         .         .         .         .    g.95951
 CAG | GTGGCTGACTGTTCTTGGGATGAAACAATAAAGATCTATGACCCTGCTTGTCTTACT    c.960
 Q   | V  A  D  C  S  W  D  E  T  I  K  I  Y  D  P  A  C  L  T      p.320

          .                                                         g.95963
 ATTCCTGCTTGA                                                       c.972
 I  P  A  X                                                         p.323

          .         .         .         .         .         .       g.96023
 gatacactactttggtcagaaacagaggatgttggctgaagaactgcctaacagcaaata       c.*60

          .         .         .         .         .         .       g.96083
 aattaactatggaaaacatagacattatgcttttatatgctattcagatttcaaatcttt       c.*120

          .         .         .         .         .         .       g.96143
 ccaatttaccctggaatcagttttgagggagctgataaagactttagctgactcgttaag       c.*180

          .         .         .         .         .         .       g.96203
 cctgatacataagccatatttaaaattctaagaaataattaatgttatgatatatcttgt       c.*240

          .         .         .         .         .         .       g.96263
 agtatctattaaaatgtctctgggtcataaaatggattaaaatatgggagatcagtaggt       c.*300

          .         .         .         .         .         .       g.96323
 tatacttatatagatagtgatatatttcatttttaatttgtcatttttgatgtaaaatat       c.*360

          .         .         .         .                           g.96371
 aatcactgctgtgataaataaactatctattgatcatttatcatttta                   c.*408

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Peroxisomal biogenesis factor 7 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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