phosphoglucomutase 3 (PGM3) - coding DNA reference sequence

(used for variant description)

(last modified February 28, 2023)


This file was created to facilitate the description of sequence variants on transcript NM_015599.2 in the PGM3 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000006.11, covering PGM3 transcript NM_015599.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
           .         .         .         .         .                g.5700
    gagccggaagccacgcagggccacgtctgcggttctgaggactgggtttgggtgcag       c.-61

 .         .         .         .         .         .        | 02    g.7924
 acgttgttgcttgggcgcttctccgctgcgtgtaggtgaagggggcttcctgaccgag | ac    c.-1

          .         .         .         .         .         .       g.7984
 ATGGATTTAGGTGCTATTACAAAATACTCAGCATTACACGCCAAGCCCAATGGACTGATC       c.60
 M  D  L  G  A  I  T  K  Y  S  A  L  H  A  K  P  N  G  L  I         p.20

          .         .         .         .         .         .       g.8044
 CTTCAATACGGGACTGCTGGATTTCGAACGAAGGCAGAACATCTTGATCATGTCATGTTT       c.120
 L  Q  Y  G  T  A  G  F  R  T  K  A  E  H  L  D  H  V  M  F         p.40

          .         .         .         .         .         .       g.8104
 CGCATGGGATTATTAGCTGTCCTGAGGTCAAAACAGACAAAATCCACTATAGGAGTCATG       c.180
 R  M  G  L  L  A  V  L  R  S  K  Q  T  K  S  T  I  G  V  M         p.60

          .         .     | 03   .         .         .         .    g.10174
 GTAACAGCGTCCCACAATCCTGAG | GAAGACAATGGTGTAAAATTGGTTGATCCTTTGGGT    c.240
 V  T  A  S  H  N  P  E   | E  D  N  G  V  K  L  V  D  P  L  G      p.80

          .         .         .         .         .         .       g.10234
 GAAATGTTGGCACCATCCTGGGAGGAACATGCCACCTGTTTAGCAAATGCTGAGGAACAA       c.300
 E  M  L  A  P  S  W  E  E  H  A  T  C  L  A  N  A  E  E  Q         p.100

          .         .         .         .         .         .       g.10294
 GATATGCAGAGAGTGCTTATTGACATCAGCGAGAAAGAAGCTGTGAATCTGCAACAAGAT       c.360
 D  M  Q  R  V  L  I  D  I  S  E  K  E  A  V  N  L  Q  Q  D         p.120

          .         .          | 04        .         .         .    g.11892
 GCCTTTGTAGTTATTGGTAGAGATACCAG | GCCCAGCAGTGAGAAACTTTCACAATCTGTA    c.420
 A  F  V  V  I  G  R  D  T  R  |  P  S  S  E  K  L  S  Q  S  V      p.140

          .         .         .        | 05.         .         .    g.15981
 ATAGATGGTGTGACTGTTCTAGGAGGTCAATTCCATG | ATTATGGCTTGTTAACAACACCC    c.480
 I  D  G  V  T  V  L  G  G  Q  F  H  D |   Y  G  L  L  T  T  P      p.160

          .         .         .         .         .         .       g.16041
 CAGCTGCACTACATGGTGTATTGTCGAAACACGGGTGGCCGATATGGAAAGGCAACTATA       c.540
 Q  L  H  Y  M  V  Y  C  R  N  T  G  G  R  Y  G  K  A  T  I         p.180

          .         .         .         .         .  | 06      .    g.17014
 GAAGGTTACTACCAGAAACTCTCTAAGGCTTTTGTGGAACTCACCAAACAG | GCTTCTTGC    c.600
 E  G  Y  Y  Q  K  L  S  K  A  F  V  E  L  T  K  Q   | A  S  C      p.200

          .         .         .         .         .         .       g.17074
 AGTGGAGATGAATACAGATCACTTAAGGTTGACTGTGCAAATGGCATAGGGGCCCTGAAG       c.660
 S  G  D  E  Y  R  S  L  K  V  D  C  A  N  G  I  G  A  L  K         p.220

          .         .         .         .         .         .       g.17134
 CTAAGGGAAATGGAACACTACTTCTCACAGGGCCTGTCAGTTCAGCTGTTTAATGATGGG       c.720
 L  R  E  M  E  H  Y  F  S  Q  G  L  S  V  Q  L  F  N  D  G         p.240

          .         .         .         .         .         .       g.17194
 TCCAAGGGCAAACTCAATCATTTATGTGGAGCTGACTTTGTGAAAAGTCATCAGAAACCT       c.780
 S  K  G  K  L  N  H  L  C  G  A  D  F  V  K  S  H  Q  K  P         p.260

         | 07.         .         .         .         .         .    g.19022
 CCACAGG | GAATGGAAATTAAGTCCAATGAAAGATGCTGTTCTTTTGATGGAGATGCAGAC    c.840
 P  Q  G |   M  E  I  K  S  N  E  R  C  C  S  F  D  G  D  A  D      p.280

          .         .         .         .         .         .       g.19082
 AGAATTGTTTATTACTACCATGATGCAGATGGCCACTTTCATCTCATAGATGGAGACAAG       c.900
 R  I  V  Y  Y  Y  H  D  A  D  G  H  F  H  L  I  D  G  D  K         p.300

          .         .         .         .      | 08  .         .    g.20195
 ATAGCAACGTTAATTAGCAGTTTCCTTAAAGAGCTCCTGGTGGAG | ATTGGAGAAAGTTTG    c.960
 I  A  T  L  I  S  S  F  L  K  E  L  L  V  E   | I  G  E  S  L      p.320

          .         .         .         .         .         .       g.20255
 AATATTGGTGTTGTACAAACTGCATATGCAAATGGAAGTTCAACACGGTATCTTGAAGAA       c.1020
 N  I  G  V  V  Q  T  A  Y  A  N  G  S  S  T  R  Y  L  E  E         p.340

           | 09        .         .         .         .         .    g.22927
 GTTATGAAG | GTACCTGTCTATTGCACTAAGACTGGTGTAAAACATTTGCACCACAAGGCT    c.1080
 V  M  K   | V  P  V  Y  C  T  K  T  G  V  K  H  L  H  H  K  A      p.360

          .         .         .         .         | 10         .    g.24461
 CAAGAGTTTGACATTGGAGTTTATTTTGAAGCAAATGGGCATGGCACT | GCACTGTTTAGT    c.1140
 Q  E  F  D  I  G  V  Y  F  E  A  N  G  H  G  T   | A  L  F  S      p.380

          .         .         .         .         .         .       g.24521
 ACAGCTGTTGAAATGAAGATAAAACAATCAGCAGAACAACTGGAAGATAAGAAAAGAAAA       c.1200
 T  A  V  E  M  K  I  K  Q  S  A  E  Q  L  E  D  K  K  R  K         p.400

          .         .         .         .   | 11     .         .    g.26895
 GCTGCTAAGATGCTTGAAAACATTATTGACTTGTTTAACCAG | GCAGCTGGTGATGCTATT    c.1260
 A  A  K  M  L  E  N  I  I  D  L  F  N  Q   | A  A  G  D  A  I      p.420

          .         .         .         .         .         .       g.26955
 TCTGACATGCTGGTGATTGAAGCAATCTTGGCTCTGAAGGGCTTGACTGTACAACAGTGG       c.1320
 S  D  M  L  V  I  E  A  I  L  A  L  K  G  L  T  V  Q  Q  W         p.440

          .         .         .         .      | 12  .         .    g.28473
 GATGCTCTCTATACAGATCTTCCAAACAGACAACTTAAAGTTCAG | GTTGCAGACAGGAGA    c.1380
 D  A  L  Y  T  D  L  P  N  R  Q  L  K  V  Q   | V  A  D  R  R      p.460

          .         .         .         .         .         .       g.28533
 GTTATTAGCACTACCGATGCTGAAAGACAAGCAGTTACACCCCCAGGATTACAGGAGGCA       c.1440
 V  I  S  T  T  D  A  E  R  Q  A  V  T  P  P  G  L  Q  E  A         p.480

          .         .         .         .         .         .       g.28593
 ATCAATGACCTGGTGAAGAAGTACAAGCTTTCTCGAGCTTTTGTCCGGCCCTCTGGTACA       c.1500
 I  N  D  L  V  K  K  Y  K  L  S  R  A  F  V  R  P  S  G  T         p.500

          .         .         .          | 13        .         .    g.29634
 GAAGATGTCGTCCGAGTATATGCAGAAGCAGACTCACAA | GAAAGTGCAGATCACCTTGCA    c.1560
 E  D  V  V  R  V  Y  A  E  A  D  S  Q   | E  S  A  D  H  L  A      p.520

          .         .         .         .         .         .       g.29694
 CATGAAGTGAGCTTGGCAGTATTTCAGCTGGCTGGAGGAATTGGAGAAAGGCCCCAACCA       c.1620
 H  E  V  S  L  A  V  F  Q  L  A  G  G  I  G  E  R  P  Q  P         p.540

                                                                    g.29703
 GGTTTCTGA                                                          c.1629
 G  F  X                                                            p.542

          .         .         .         .         .         .       g.29763
 agataattttcatattcctgagaaactggactttttacaagtctttacaaaactgtcaat       c.*60

          .         .         .         .         .         .       g.29823
 aataatggcagtactaagagatttataatcataatgtttacaatgcagcctactggattg       c.*120

          .         .         .         .         .         .       g.29883
 tctctagatctgtttttcttaaacactaacagaataattctttataaataggtaagcctt       c.*180

          .         .         .         .         .         .       g.29943
 acacttgttaaagaaatttacctctaatttcagtctcactaatgtaaaatactgggactt       c.*240

          .         .         .         .         .         .       g.30003
 aagtatacaattcagtcactaactgtacagttttatgtggggaacaattcatgcaggcta       c.*300

          .         .         .         .         .         .       g.30063
 ctggaaaattaaatcttattaccaactccttgtgatatctttgccatcaccatcacatga       c.*360

          .         .         .         .         .         .       g.30123
 gcaagatgatgttttgcagcattccccattgctgatacaaatggagagggcagagaagac       c.*420

          .         .         .         .         .         .       g.30183
 tttatacaaccagtttttccattgcagagtcttaagaaagattattagatgacttaccta       c.*480

          .         .         .         .         .         .       g.30243
 tatgactaatgccatcaggaactcagaggtatgaatagggggttgtccatccctcttcca       c.*540

          .         .         .         .         .         .       g.30303
 tactgaggtggagatgctcatgcaatacttttaaggatgcatggtccagccttcagttat       c.*600

          .         .         .         .         .         .       g.30363
 tcttcactgctcttggtgaaggtatgtgggagaaaaactaattataatacgtttcccagc       c.*660

          .         .         .         .         .         .       g.30423
 ctctgatggagaaggaacaccattctgataccagaacatggttaataaggaaaagagaaa       c.*720

          .         .         .         .         .         .       g.30483
 aatccccaaccaatcttaattgaaccaagtctgaaaccaatggaaaaaaaaaatgggtag       c.*780

          .         .         .         .         .         .       g.30543
 tgtatattttgcaggtttaagacaactcaggacaataaaaacaatggactttacatgtgt       c.*840

          .         .         .         .         .         .       g.30603
 atatatatagctctcttaggcaccataatcagtatgagccaacaatatttaaacttgatt       c.*900

          .         .         .         .         .         .       g.30663
 caggccacattcagacatttgctcttatatacaaatatttaaattaaatacaatctgaaa       c.*960

          .         .         .         .         .         .       g.30723
 tgtgttctgttacatacaaaaaaggaaaaactatacaacgcagagcagtgtgtgtgtttt       c.*1020

          .         .         .         .         .         .       g.30783
 aaataattacatttacatgtaagctaaatggaaccagcaatggtgctcaagtttttatca       c.*1080

          .         .         .         .         .         .       g.30843
 tcccttccagaaaatctttttctaccatctcttctattttttgcctggctttgctggaac       c.*1140

          .         .         .         .         .         .       g.30903
 atggtttgtggttctccagtttcatgtccttattagggaaggcatttgagtagaggatag       c.*1200

          .         .         .         .         .         .       g.30963
 gactccctgagtgtcctccacatcggcttgtgactttgctgttgaagacttgactgagca       c.*1260

          .         .         .         .         .         .       g.31023
 cattgaagaacggcaggagctgctccatactgcgcacggtgcagatggtgagcagcaagt       c.*1320

          .         .         .         .         .         .       g.31083
 gccctggctcccaacccaatgttctccctgagttgtcttcctctggatttttctgcagaa       c.*1380

          .         .         .         .         .         .       g.31143
 aacaaaaagtgaactggtattaatacaacagacaatgtggtatgttagaaaaattaaaaa       c.*1440

          .         .         .         .         .         .       g.31203
 tatataaactttggcaattggtcaagaaatgaatacaaatgacattaagtttctaactcc       c.*1500

          .         .         .         .         .         .       g.31263
 tgacctgatcaaaacccttggtgcttctgagaccttttactgccatttattagttttaca       c.*1560

          .         .         .         .         .         .       g.31323
 tggagcagtctaacattgtagtaatagttcccaactagaatgcgcagataagcttagtta       c.*1620

          .         .         .         .         .         .       g.31383
 acagaaatagctttgaacaggaatagagtcaaacataaaagttttatgttgtgctttgta       c.*1680

          .         .         .         .         .         .       g.31443
 tttactcaaaaagctcccaggtttctgaaccctcactactgtaaccaaggactaggtcac       c.*1740

          .         .         .         .         .         .       g.31503
 aaaattactacagaaaaaaggaacaaagtgctttatacatttcataatatatcccctttt       c.*1800

          .         .         .         .         .         .       g.31563
 attataattagttaattcccttttatctaaatggcctaaatttgccatgatggtagcagt       c.*1860

          .         .         .         .         .         .       g.31623
 gtccaaagtgaataattactgtcagtactgcatcacagagaaaggaagggatccctcagg       c.*1920

          .         .         .         .         .         .       g.31683
 agacactgctgtctccttctgggttgtgctaaacaacatagggaggaaagctggacctgg       c.*1980

          .         .         .         .         .         .       g.31743
 agtcaaaggaattgagttagtgtgctggctctgccatacttacggcacccttgggcagga       c.*2040

          .         .         .         .         .         .       g.31803
 tatacaaaggttcctcacttataaaatgggacagtctaaaactaccttttagtagagaag       c.*2100

          .         .         .         .         .         .       g.31863
 tcaaatgagaaggtatgtgaaaactctgtcaactaaatataaagactaataatttgggta       c.*2160

          .         .         .         .         .         .       g.31923
 ttaagaggctagtttgagaagccacctgaattacacaaacacagctacagacatcattct       c.*2220

          .         .         .         .         .         .       g.31983
 gtctagagaaagataagagagaacaggttggttgaacttgggcagaatcacagatacaat       c.*2280

          .         .         .         .         .         .       g.32043
 tccacactaaagaatgaaaataagcaatgaactagacagaaggaagaaatcatgaagact       c.*2340

          .         .         .         .         .         .       g.32103
 taggaagcagaattacaatctgtcatattaacaaatggagtttgccttctaagatcagat       c.*2400

          .         .         .         .         .         .       g.32163
 gttgctcagaaactttcattgtttacctaataatttaatatcactagtttcctagtgggt       c.*2460

          .         .         .         .         .         .       g.32223
 caagcagatgcaaaatccagcttattttcttctatgtgctctcaagcttattgcttattt       c.*2520

          .         .         .         .         .         .       g.32283
 taaagtaaaatcctgaaaaaggaaaatattaggttggtgcaaacgtaattgcggtttttg       c.*2580

          .         .         .         .         .         .       g.32343
 cattgttgaaatttgccgttttatattggagtacattcttaaataaatgtggttatgtta       c.*2640

          .         .         .         .         .         .       g.32403
 tacatcattttaagcatatttctcactttttttttgctaatgacttattgctgtttatat       c.*2700

          .         .         .         .         .         .       g.32463
 ttattttagactatggaaatgatgttagacaaaaatcaaatttagcgattttctgagttc       c.*2760

          .         .         .         .         .         .       g.32523
 aaaataggttataaagcagcagagacaacacacaacatcaacaatgcatttggcccagga       c.*2820

          .         .         .         .         .         .       g.32583
 actgctaatgaacatacagtgccgtgatggctcaagaagttttgcaaaggagactagagc       c.*2880

          .         .         .         .         .         .       g.32643
 cttgaagatgaggagtgcagtggccagtcatcggaaattgataatgaccaattgagaaca       c.*2940

          .         .         .         .         .         .       g.32703
 tcatcgaagctgatcctcttacaactataagagagctgcccaagaactcaatgttgacca       c.*3000

          .         .         .         .         .         .       g.32763
 ttttatggtcgttcggcatttgaagcaaattgaaaaggtgaaaaagctcaataaatgggt       c.*3060

          .         .         .         .         .         .       g.32823
 gcctcatgagctgagtgaaaaataaaaaaattcgttgttttgaagtgtcattttctctat       c.*3120

          .         .         .         .         .         .       g.32883
 tctatgcaacaataatgaatcatttctctatcggattgtgatgtgtgccaaaaggtggat       c.*3180

          .         .         .         .         .         .       g.32943
 tttatacgacaactggcgatgaccagctcagtggctggactgaaagaagctccaaagcac       c.*3240

          .         .         .         .         .         .       g.33003
 ttcccaaagccaaacttgctccaaaaaatggtcatggtcattgtttggtggtttgctgcc       c.*3300

          .         .         .         .         .         .       g.33063
 agtctgatccactacagctttctgaatccaggtgaaaccattacatctgataagtatgct       c.*3360

          .         .         .         .         .         .       g.33123
 cagcaaatcaatgagatgcaccaaaaactgcaatgcctgcagccggcattggccaccaga       c.*3420

          .         .         .         .         .         .       g.33183
 aagggcccaattcttttcacgacaacactgggccgcacgttgcacaaccaacgcttcgaa       c.*3480

          .         .         .         .         .         .       g.33243
 aattgaactaattgggctatgaagttttgcctcatctgccatattcacctgacctcttgc       c.*3540

          .         .         .         .         .         .       g.33303
 caacaaactaccacttctttaggcatctcagcaacgttttgcagggaaattgcttccaca       c.*3600

          .         .         .         .         .         .       g.33363
 actagcaggacacagaaaatgctttccaagagttcgtcaaatttggaagcatggattttt       c.*3660

          .         .         .         .         .         .       g.33423
 atgctacaggagtaaacaaacttatttctcattggcaaaaatgtgttgattgtaatggtt       c.*3720

          .         .         .         .         .         .       g.33483
 cctattttaattaataaagatttgtgtgaacctagttataatgacttaaaattcatggtc       c.*3780

          .         .         .         .         .         .       g.33543
 ccaaacagcaattacttttgcaccaaactaaaaatataagttaaaatggaagagtctagg       c.*3840

          .         .         .         .         .         .       g.33603
 agcaaaccaagaaaagatcacctacttcatcatctctggtcaaaaacaaaccaaaaaact       c.*3900

          .         .         .         .         .         .       g.33663
 taacagctatcacttaagtttgcttcctagcaattatttagcttccagtctagattacag       c.*3960

          .         .         .         .         .         .       g.33723
 gatatataaaactttctttctttctttcttaactatgacactggcaccaatgagagtcct       c.*4020

          .         .         .         .         .         .       g.33783
 gtgactgactttcacatttccaccattactcaattactggtaccataccacctctaatcc       c.*4080

          .         .         .         .         .         .       g.33843
 cctaaatcaaactgcaattcaacaataaagggcgtacagagatgactttgtcctgaagga       c.*4140

          .         .         .         .         .         .       g.33903
 aaatgaatatccttgtaccctctatatagctaacttccaaatgtaagagaactatggggt       c.*4200

          .         .         .         .         .         .       g.33963
 aaccttttgtttctattcctatcaagatgagcctttaagagagggacttttattaagctc       c.*4260

          .         .         .         .         .         .       g.34023
 ttgaccaagaagaatacacttgattcagagtttctgatgctcttaatcagaactatatgt       c.*4320

          .         .         .         .                           g.34064
 attgtctcaatattaaataaagtcaaatgtttccatacaaa                          c.*4361

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Phosphoglucomutase 3 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

Powered by LOVD v.3.0 Build 29
©2004-2023 Leiden University Medical Center