phosphorylase kinase, gamma 2 (testis) (PHKG2) - coding DNA reference sequence

(used for variant description)

(last modified January 21, 2017)


This file was created to facilitate the description of sequence variants on transcript NM_000294.2 in the PHKG2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_016616.1, covering PHKG2 transcript NM_000294.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                               .         .         .                g.5030
                               aattgggcggccggtttccaattggaaggg       c.-181

 .         .         .         .         .         .                g.5090
 cttctgagcctcagtcttcgggcggcgctgaccattggcgggcaggatggaggcggagcc       c.-121

 .         .         .         .         .         .                g.5150
 ttgggttgtcgcccgccgccgggggttaaggtgagcgactgcaggcaaacccggcgacag       c.-61

 .         .         .         .         .  | 02      .             g.5522
 cgcagctcgcgtcgaccctggctcctctgcctgccccctcag | gcccccgcctccttcagg    c.-1

          .         .         .         .         .         .       g.5582
 ATGACGCTGGACGTGGGGCCGGAGGATGAGCTGCCCGACTGGGCCGCCGCCAAAGAGTTT       c.60
 M  T  L  D  V  G  P  E  D  E  L  P  D  W  A  A  A  K  E  F         p.20

          .         .         .      | 03  .         .         .    g.7832
 TACCAGAAGTACGACCCTAAGGACGTCATCGGCAG | AGGAGTGAGCTCTGTGGTCCGCCGT    c.120
 Y  Q  K  Y  D  P  K  D  V  I  G  R  |  G  V  S  S  V  V  R  R      p.40

          .         .         .         .         .         .       g.7892
 TGTGTTCATCGAGCTACTGGCCACGAGTTTGCGGTGAAGATTATGGAAGTGACAGCTGAG       c.180
 C  V  H  R  A  T  G  H  E  F  A  V  K  I  M  E  V  T  A  E         p.60

          .         .         .         .         .         .       g.7952
 CGGCTGAGTCCTGAGCAGCTGGAGGAGGTGCGGGAAGCCACACGGCGAGAGACACACATC       c.240
 R  L  S  P  E  Q  L  E  E  V  R  E  A  T  R  R  E  T  H  I         p.80

          .         .         .  | 04      .         .         .    g.8279
 CTTCGCCAGGTCGCCGGCCACCCCCACATCA | TCACCCTCATCGATTCCTACGAGTCTTCT    c.300
 L  R  Q  V  A  G  H  P  H  I  I |   T  L  I  D  S  Y  E  S  S      p.100

          .         .       | 05 .         .         .         .    g.9967
 AGCTTCATGTTCCTGGTGTTTGACCT | GATGCGGAAGGGAGAGCTGTTTGACTATCTCACA    c.360
 S  F  M  F  L  V  F  D  L  |  M  R  K  G  E  L  F  D  Y  L  T      p.120

          .         .         .   | 06     .         .         .    g.10123
 GAGAAGGTGGCCCTCTCTGAAAAGGAAACCAG | GTCCATCATGCGGTCTCTGCTGGAAGCA    c.420
 E  K  V  A  L  S  E  K  E  T  R  |  S  I  M  R  S  L  L  E  A      p.140

          .         .         .         .         .         .       g.10183
 GTGAGCTTTCTCCATGCCAACAACATTGTGCATCGAGATCTGAAGCCCGAGAATATTCTC       c.480
 V  S  F  L  H  A  N  N  I  V  H  R  D  L  K  P  E  N  I  L         p.160

          .         .         .         .         .         .       g.10243
 CTAGATGACAATATGCAGATCCGACTTTCAGATTTCGGGTTCTCCTGCCACTTGGAACCT       c.540
 L  D  D  N  M  Q  I  R  L  S  D  F  G  F  S  C  H  L  E  P         p.180

          .       | 07 .         .         .         .         .    g.12927
 GGCGAGAAGCTTCGAG | AGTTGTGTGGGACCCCAGGGTATCTAGCGCCAGAGATCCTTAAA    c.600
 G  E  K  L  R  E |   L  C  G  T  P  G  Y  L  A  P  E  I  L  K      p.200

          .         .         .         .        | 08.         .    g.13081
 TGCTCCATGGATGAAACCCACCCAGGCTATGGCAAGGAGGTCGACCT | CTGGGCCTGTGGG    c.660
 C  S  M  D  E  T  H  P  G  Y  G  K  E  V  D  L  |  W  A  C  G      p.220

          .         .         .         .         .         .       g.13141
 GTGATCTTGTTCACACTCCTGGCTGGCTCGCCACCCTTCTGGCACCGGCGGCAGATCCTG       c.720
 V  I  L  F  T  L  L  A  G  S  P  P  F  W  H  R  R  Q  I  L         p.240

          .         .         .         .         .         .       g.13201
 ATGTTACGCATGATCATGGAGGGCCAGTACCAGTTCAGTTCCCCCGAGTGGGATGACCGT       c.780
 M  L  R  M  I  M  E  G  Q  Y  Q  F  S  S  P  E  W  D  D  R         p.260

          .         .  | 09      .         .         .         .    g.13330
 TCCAGCACTGTCAAAGACCTG | ATCTCCAGGCTGCTGCAGGTGGATCCTGAGGCACGCCTG    c.840
 S  S  T  V  K  D  L   | I  S  R  L  L  Q  V  D  P  E  A  R  L      p.280

          .         .         .         .         .         .       g.13390
 ACAGCTGAGCAGGCCCTACAGCACCCCTTCTTTGAGCGTTGTGAAGGCAGCCAACCCTGG       c.900
 T  A  E  Q  A  L  Q  H  P  F  F  E  R  C  E  G  S  Q  P  W         p.300

          .         .        | 10.         .         .         .    g.13538
 AACCTCACCCCCCGCCAGCGGTTCCGG | GTGGCAGTGTGGACAGTGCTGGCTGCTGGACGA    c.960
 N  L  T  P  R  Q  R  F  R   | V  A  V  W  T  V  L  A  A  G  R      p.320

          .         .         .         .         .         .       g.13598
 GTGGCCCTAAGCACCCATCGTGTACGGCCACTGACCAAGAATGCACTGTTGAGGGACCCT       c.1020
 V  A  L  S  T  H  R  V  R  P  L  T  K  N  A  L  L  R  D  P         p.340

          .         .         .         .         .         .       g.13658
 TATGCGCTGCGGTCAGTGCGGCACCTCATCGACAACTGTGCCTTCCGGCTCTACGGGCAC       c.1080
 Y  A  L  R  S  V  R  H  L  I  D  N  C  A  F  R  L  Y  G  H         p.360

          .         .         .         .         .         .       g.13718
 TGGGTAAAGAAAGGGGAGCAGCAGAACCGGGCGGCTCTCTTTCAGCACCGGCCCCCTGGG       c.1140
 W  V  K  K  G  E  Q  Q  N  R  A  A  L  F  Q  H  R  P  P  G         p.380

          .         .         .         .         .         .       g.13778
 CCTTTTCCCATCATGGGCCCTGAAGAGGAGGGAGACTCTGCTGCTATAACTGAGGATGAG       c.1200
 P  F  P  I  M  G  P  E  E  E  G  D  S  A  A  I  T  E  D  E         p.400

          .         .                                               g.13799
 GCCGTGCTTGTGCTGGGCTAG                                              c.1221
 A  V  L  V  L  G  X                                                p.406

          .         .         .         .         .         .       g.13859
 gacctcaaccccagggattcccaggaagcagaactctccagaagaagggttttgatcatt       c.*60

          .         .         .         .         .         .       g.13919
 ccagctcctctgggctctggcctcaggcccactaatgatcctgctaccctcttgaagacc       c.*120

          .         .         .         .         .         .       g.13979
 agcccggtacctctctccccactggccaggactctgagatcagagctggggtggaaggga       c.*180

          .         .         .         .         .         .       g.14039
 gccattctgaacgccacgcctggcccggtcagtgctgcatgcactgcatatgaaataaaa       c.*240

          .         .         .         .         .         .       g.14099
 tctgctacacgccagggagaacaggtgtcctgtgtctgtctggcttgggcaggaaagccc       c.*300

          .         .         .         .         .         .       g.14159
 agaaggtgctcagcagggtgcagggatggtgccattctggcccagacctttattggggaa       c.*360

          .         .         .         .         .         .       g.14219
 aatgttgggggtcacttggtcttgctcttgcctttacccggaggtagctggaagggccgc       c.*420

          .         .         .         .         .         .       g.14279
 tctagtgcagtcaacttgctgctgagcctttcctcgctggccttgagccgctcctccacc       c.*480

          .         .         .         .         .         .       g.14339
 agcccctggagctgctccagctctttgttcacttgggtcttgatgtaggctcggaggacg       c.*540

          .         .         .         .         .         .       g.14399
 tggatgtggcctgcaggggcagggaagaaggggcagggtgaggagagatgctgtctggca       c.*600

          .         .         .         .         .         .       g.14459
 atggggggatggtccctagttgggcaaacagtccccaaatttcccctggtggggatatag       c.*660

          .         .         .         .         .         .       g.14519
 aggtagcaatgttgtttccctttaggaaatgttagcaagcccttgtgtgagaggtagttg       c.*720

          .         .         .         .         .         .       g.14579
 ggtagggtggctatgctggactttgcagcttcaaattctgatccctactcagtagctgtg       c.*780

          .         .         .         .         .         .       g.14639
 tgaccttaggcaggttatttaacctatctgtgcctcagtttccttgtatgaaatgtggat       c.*840

          .         .         .         .         .         .       g.14699
 agtgatacctagcacataggattgagggaggattaaatgagttaatttatgtaaaatgct       c.*900

          .         .         .         .         .         .       g.14759
 tagagcagggcatgcactgcacacctattgccaagtatgtgctggctgttattgtcattg       c.*960

          .         .         .         .         .         .       g.14819
 gctttctctttttttttttttttttgagatggagtcttgctttatcccccaggctggagt       c.*1020

          .         .         .         .         .         .       g.14879
 gcagtggcagcgatctcagctcactgcaagctctgcctcccaggttcatgccattctcct       c.*1080

          .         .         .         .         .         .       g.14939
 gcctcagcctcccagtagctgggactacaggcacccgccaccacgcccggctaacttttt       c.*1140

          .         .         .         .         .         .       g.14999
 gtatttttagtagagacggggtttcacagtgttagccaggatggactcgatctcctgacc       c.*1200

          .         .         .         .         .         .       g.15059
 tcgtgatccgcctgcctcagcctcccaaagtgctgggattacagttgtgagccactgcac       c.*1260

          .         .         .         .         .         .       g.15119
 ctggcctgttctttgtttttttttaactcttaagttctgggatacgagcagaacatgcag       c.*1320

          .         .         .         .         .         .       g.15179
 gtttgctacgtaggtatacatgggccatggtggtttgctttacccatcaacccatcatat       c.*1380

          .         .         .         .         .         .       g.15239
 aggttttaagccaccgtcattggctttctaatgatcatttctctggagccacttcagctg       c.*1440

          .         .         .         .         .         .       g.15299
 tgctttttgtttgtttgtttgtttgttttgagacagagtcttgctctgttgcccaggctg       c.*1500

          .         .         .         .         .         .       g.15359
 gagtgcagtggccagatcttggctcactgcagtctccacctcctgggttcatgcagttct       c.*1560

          .         .         .         .         .         .       g.15419
 cctgcctcagcctcctgagtagctgggactacaagcgcgcaccaccatgcctggctattt       c.*1620

          .         .         .         .         .         .       g.15479
 tttgtattttagtagatagggggtttcacggtgttgcccaggctggtcgcgaactcctga       c.*1680

          .         .         .         .         .         .       g.15539
 gctcaggcaatccgcctgcctcagattgtgctgggattacaggtgtgagccaccacgcct       c.*1740

          .         .         .         .         .         .       g.15599
 ggcctgcagctgtgcttttatctgtcatcttggacttctgcataagggatcatttagaga       c.*1800

          .         .         .         .         .         .       g.15659
 aaggactctgactaaaaacaaaaagtctgaagtcctgatgtcatccaaacccttcattct       c.*1860

          .         .         .         .         .         .       g.15719
 acacctgctcagagggacagggcagcctgccctctccagatcctcacttggctctggctc       c.*1920

          .         .         .         .         .         .       g.15779
 tggtggggccactgtctctagttcctctttctgcggggtaactgcctgctcctccatctc       c.*1980

          .         .         .         .         .         .       g.15839
 cttgctttcttctttctctgcaaaccagaagcaggaagagactgtggccccaggcctggc       c.*2040

          .         .         .         .         .         .       g.15899
 ccagcccagccctgccctggcactctcccttacccgtctcactctctggccacagtttgg       c.*2100

          .         .         .         .         .         .       g.15959
 gtggctgtagccccatgtaagtcaaagacagatccagccgcacctgggaagcaaggcaga       c.*2160

          .         .         .         .         .         .       g.16019
 gggaggctgaaaggagtgcacctgtgctgaggggaggggcggttgagggtggctcctcat       c.*2220

          .         .         .         .         .         .       g.16079
 ggtccaccaccccctacctggggtgtgaagacgtatttatagagcttgaagtggcggaag       c.*2280

          .         .         .         .         .         .       g.16139
 taagtgttgaccacgtagtcttccaaggccagcagctgttcctctttgaagaggtcgatg       c.*2340

          .         .         .         .         .         .       g.16199
 ctgaaaggaggccgctgtggtggtgactcggaattagaaccctgactaccttccggagcc       c.*2400

          .         .         .         .         .         .       g.16259
 ctggctttgcctccaaaagcccagcaacaggagcaaggagagcccactggggtcttcaca       c.*2460

          .         .         .         .         .         .       g.16319
 agaagataagggtgatgaatgtgagagagactgggtgagaccttgtctggggatgggtaa       c.*2520

          .         .         .         .         .         .       g.16379
 agtttccagaatgttccaggggaactgaccctgactccatggcaaaaaaggacactggtg       c.*2580

          .         .         .         .         .         .       g.16439
 aagtagcggtagcactcctccacgttgcccaagggggttgctggtagggaaagcaagatg       c.*2640

          .         .         .         .         .         .       g.16499
 cagcagtgaggccctctctggtatccattcattcacttcactcaacagctgtttatgacc       c.*2700

          .         .         .         .         .         .       g.16559
 atgagcttcagaagcagacagatctgggtttcagcactggcttgtttccttaactcatgt       c.*2760

          .         .         .         .         .         .       g.16619
 aacaaatactgaatacccactatatgcccactgtatggttttcggcactgaacaagacag       c.*2820

          .         .         .         .         .         .       g.16679
 acaaggtcctgcccttacgaagcttatattctaggggaataaaccaagaaatagatcatt       c.*2880

          .         .         .         .         .         .       g.16739
 tcagctattaaacattctgaagcaagagctattaaacattctaaagcaggtgttattgtg       c.*2940

          .         .         .         .         .         .       g.16799
 cactatgcatatatttgcatatattatttctcagaacagtcctgtaaaatgtgtgctgta       c.*3000

          .         .         .         .         .         .       g.16859
 tccttaatttctagataaggaagcagtggattggaaagctgatggcttgtgtatgatgat       c.*3060

          .         .         .         .         .         .       g.16919
 gctactaataatgacatattccaggcagaaatcccctgcttctgcttcccatggtcactt       c.*3120

          .         .         .         .         .         .       g.16979
 gtgccaggcccggttcctcttctccctggggctcaaacctggtagctgccccctctcacc       c.*3180

          .         .         .         .         .         .       g.17039
 aatacaagccttgtgaagatcctggagcagggcacaagccgctgacgtctgctccagtga       c.*3240

          .         .         .         .         .         .       g.17099
 gaagccctgctggcggcagaaaatgagcgcgtggcagaagaggtccagggtgatggcgtc       c.*3300

          .         .         .         .         .         .       g.17159
 cctcaggctctgctcaggacaccctagctccagcagctcagccagcacccttgggaggga       c.*3360

          .         .         .         .         .         .       g.17219
 gagaggagtgagtgacaactgggcctcctttcatcaccctacacccaccacatgctttgg       c.*3420

          .         .         .         .         .         .       g.17279
 agtcagccattcctcatgttttcccaacctgacccctcagcctttgccaagagctcttcc       c.*3480

          .         .         .         .         .         .       g.17339
 cacgcccccctcagtccctactccctcatctcagcattggtggtcttctccagctggtgc       c.*3540

          .         .         .         .         .         .       g.17399
 atggaatggacgtccaggtacttcctgttatagtaaaagaaaaagagtattggtggccgt       c.*3600

          .         .         .         .         .         .       g.17459
 tacctatcatgacaaggctgtgacagctagtgcgtgagactgggagttggccaccggcgt       c.*3660

          .         .         .         .         .         .       g.17519
 gaagctgggctcttttgccagcttgctgtgtgactatgcaaatcgttaactctctgggcc       c.*3720

          .         .         .         .         .         .       g.17579
 taaatgaactcttatgagcctctccatttctaaagcctagggttaggaatcttgaattct       c.*3780

          .         .         .         .         .         .       g.17639
 tttttctgctctgccactaccttgtatgaccttggtcaagtactccctgtggccctcagt       c.*3840

          .         .         .         .         .         .       g.17699
 gtccccctctgtacaatactccttagcggccatgagactccatttacattctgtctttgg       c.*3900

          .         .         .         .         .         .       g.17759
 ctctttttttctcacactgcctcctctttggactggagaggctggaaagccaacttccag       c.*3960

          .         .         .         .         .         .       g.17819
 tcacctggagtaattgcatctccaggcctcagtctcatctgtaaaatggggatgccctgg       c.*4020

          .         .         .         .         .                 g.17871
 ccacagacaggactgttggggagacaataaagaacgcaaatattcagtgtaa               c.*4072

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Phosphorylase kinase, gamma 2 (testis) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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