polycystic kidney disease 1 like 1 (PKD1L1) - coding DNA reference sequence

(used for variant description)

(last modified March 13, 2023)


This file was created to facilitate the description of sequence variants on transcript NM_138295.3 in the PKD1L1 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000007.13, covering PKD1L1 transcript NM_138295.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                               .         .         .                g.5034
                           tgactgtcatacttgtgaccagcttgcacaggac       c.-1

          .         .         .         .     | 02   .         .    g.9979
 ATGGCCGAGGAGGCAGCCCAGAACATTTCTGATGACCAGGAAAG | GTGTCTCCAGGCTGCC    c.60
 M  A  E  E  A  A  Q  N  I  S  D  D  Q  E  R  |  C  L  Q  A  A      p.20

          .         .         .         .         .         .       g.10039
 TGCTGCCTTTCCTTTGGTGGTGAGCTGTCTGTGAGCACTGACAAGAGCTGGGGTCTTCAT       c.120
 C  C  L  S  F  G  G  E  L  S  V  S  T  D  K  S  W  G  L  H         p.40

          .         .         .         . | 03       .         .    g.13177
 CTGTGCAGCTGTAGCCCTCCTGGAGGTGGATTGTGGGTCG | AGGTCTATGCTAATCATGTG    c.180
 L  C  S  C  S  P  P  G  G  G  L  W  V  E |   V  Y  A  N  H  V      p.60

          .         .         .         .         .         .       g.13237
 CTTCTTATGAGTGATGGGAAGTGTGGCTGTCCTTGGTGTGCTCTGAATGGAAAGGCAGAA       c.240
 L  L  M  S  D  G  K  C  G  C  P  W  C  A  L  N  G  K  A  E         p.80

          .         .         .         .      | 04  .         .    g.16531
 GACCGGGAATCACAGAGCCCATCCTCATCAGCTTCCAGGCAGAAG | AACATTTGGAAAACA    c.300
 D  R  E  S  Q  S  P  S  S  S  A  S  R  Q  K   | N  I  W  K  T      p.100

          .         .         .         .         .         .       g.16591
 ACTAGTGAAGCAGCGTTAAGTGTTGTTAATGAAAAAACACAGGCTGTTGTTAATGAAAAA       c.360
 T  S  E  A  A  L  S  V  V  N  E  K  T  Q  A  V  V  N  E  K         p.120

          .         .         .         | 05         .         .    g.21440
 ACACAGGCGCCTCTGGATTGTGATAACAGTGCTGATAG | AATTCCCCACAAACCTTTCATT    c.420
 T  Q  A  P  L  D  C  D  N  S  A  D  R  |  I  P  H  K  P  F  I      p.140

          .         .         .         .         .         .       g.21500
 ATAATCGCAAGGGCCTGGAGCAGTGGTGGCCCCAGGTTCCATCACAGGCGGCTGTGTGCT       c.480
 I  I  A  R  A  W  S  S  G  G  P  R  F  H  H  R  R  L  C  A         p.160

          .         .         .          | 06        .         .    g.22174
 ACTGGGACCGCAGACAGCACATTCTCTGCTCTTCTCCAG | CTCCAGGGCACCACTTCTGCA    c.540
 T  G  T  A  D  S  T  F  S  A  L  L  Q   | L  Q  G  T  T  S  A      p.180

          .         .         .         .         .         .       g.22234
 GCAGCTCCCTGCAGCCTGAAGATGGAGGCTTCCTGCTGTGTCCTGAGACTGCTGTGCTGT       c.600
 A  A  P  C  S  L  K  M  E  A  S  C  C  V  L  R  L  L  C  C         p.200

          .         .         .         .         .         .       g.22294
 GCGGAGGATGTGGCCACGGGGCTGCTTCCTGGGACTGTCACGATGGAGACCCCCACCAAG       c.660
 A  E  D  V  A  T  G  L  L  P  G  T  V  T  M  E  T  P  T  K         p.220

          .         .         .         .         .         .       g.22354
 GTGGCCAGACCCACTCAGACCAGCTCCCAGCGAGTGCCCCTGTGGCCGATTTCACATTTT       c.720
 V  A  R  P  T  Q  T  S  S  Q  R  V  P  L  W  P  I  S  H  F         p.240

          .        | 07.         .         .         .         .    g.23991
 CCCACTTCTCCCAGAAG | CTCCCACGGCCTTCCGCCTGGCATTCCTCGCACCCCCAGCTTC    c.780
 P  T  S  P  R  S  |  S  H  G  L  P  P  G  I  P  R  T  P  S  F      p.260

          .         .         .         .         .         .       g.24051
 ACGGCATCGCAGTCTGGTTCTGAGATCCTCTATCCCCCTACTCAGCATCCTCCTGTGGCC       c.840
 T  A  S  Q  S  G  S  E  I  L  Y  P  P  T  Q  H  P  P  V  A         p.280

          .         .         .         .         .         .       g.24111
 ATCCTAGCTCGAAATTCTGATAACTTCATGAACCCTGTTCTTAATTGCTCCCTGGAAGTG       c.900
 I  L  A  R  N  S  D  N  F  M  N  P  V  L  N  C  S  L  E  V         p.300

          .         .         .         .         .         .       g.24171
 GAAGCTCGGGCACCTCCAAATCTGGGATTCCGTGTTCATATGGCTTCTGGAGAGGCTCTC       c.960
 E  A  R  A  P  P  N  L  G  F  R  V  H  M  A  S  G  E  A  L         p.320

          .         .         .         .         .         .       g.24231
 TGTCTGATGATGGATTTCGGGGACAGTTCTGGGGTTGAAATGAGGCTACACAACATGTCT       c.1020
 C  L  M  M  D  F  G  D  S  S  G  V  E  M  R  L  H  N  M  S         p.340

          .         .         .         . | 08       .         .    g.37895
 GAGGCAATGGCGGTGACTGCCTACCACCAGTACTCAAAAG | GTATTTTTTTTCATCTTTTA    c.1080
 E  A  M  A  V  T  A  Y  H  Q  Y  S  K  G |   I  F  F  H  L  L      p.360

          .         .         .         .         .         .       g.37955
 CATTTTCAGTTGGATATGTCCACCTACAAAGAAGCAGAGACACAAAATACAACTTTAAAT       c.1140
 H  F  Q  L  D  M  S  T  Y  K  E  A  E  T  Q  N  T  T  L  N         p.380

          .         .         .         .         .         .       g.38015
 GTTTACTTGTGCCAAAGTGAAAACAGCTGCCTGGAAGACTCAGACCCCAGTAACCTTGGA       c.1200
 V  Y  L  C  Q  S  E  N  S  C  L  E  D  S  D  P  S  N  L  G         p.400

          .         .         | 09         .         .         .    g.45256
 TATGAGCTTATTTCTGCCTTTGTCACCA | AAGGAGTCTATATGCTCAAGGCTGTTATTTAT    c.1260
 Y  E  L  I  S  A  F  V  T  K |   G  V  Y  M  L  K  A  V  I  Y      p.420

          .         .         .         .         .         .       g.45316
 AACGAGTTTCATGGAACCGAAGTGGAGCTTGGGCCTTATTATGTGGAGATTGGCCATGAG       c.1320
 N  E  F  H  G  T  E  V  E  L  G  P  Y  Y  V  E  I  G  H  E         p.440

          .         .         .         .         .         .       g.45376
 GCCGTGTCTGCGTTCATGAACTCCAGCAGTGTCCATGAAGATGAAGTGCTTGTCTTTGCT       c.1380
 A  V  S  A  F  M  N  S  S  S  V  H  E  D  E  V  L  V  F  A         p.460

          .         .   | 10     .         .         .         .    g.47550
 GACTCCCAAGTGAATCAGAAAA | GCACTGTGGTTATACATCACTTTCCATCTATTCCTTCA    c.1440
 D  S  Q  V  N  Q  K  S |   T  V  V  I  H  H  F  P  S  I  P  S      p.480

          .         .         .         .         .         .       g.47610
 TATAACGTGTCCTTTATTTCTCAGACTCAAGTGGGTGACAGCCAGGCTTGGCACAGCATG       c.1500
 Y  N  V  S  F  I  S  Q  T  Q  V  G  D  S  Q  A  W  H  S  M         p.500

          .         .   | 11     .         .         .         .    g.48187
 ACTGTCTGGTATAAGATGCAAT | CCGTCTCTGTCTACACAAATGGAACTGTGTTTGCCACA    c.1560
 T  V  W  Y  K  M  Q  S |   V  S  V  Y  T  N  G  T  V  F  A  T      p.520

          .         .         .         .         .         .       g.48247
 GACACAGACATTACATTTACAGCTGTTACCAAGGAAACAATACCCCTGGAATTTGAGTGG       c.1620
 D  T  D  I  T  F  T  A  V  T  K  E  T  I  P  L  E  F  E  W         p.540

          .         .         .         .         .         .       g.48307
 TATTTTGGAGAGGATCCACCAGTGAGGACAACTTCAAGAAGCATTAAAAAAAGACTCAGC       c.1680
 Y  F  G  E  D  P  P  V  R  T  T  S  R  S  I  K  K  R  L  S         p.560

          .  | 12      .         .         .         .         .    g.48906
 ATCCCCCAATG | GTATCGTGTGATGGTTAAGGCTTCCAACAGGATGAGCAGTGTGGTCTCT    c.1740
 I  P  Q  W  |  Y  R  V  M  V  K  A  S  N  R  M  S  S  V  V  S      p.580

          .         .         .         .         .         .       g.48966
 GAGCCCCATGTCATCAGGGTGCAGAAGAAAATTGTGGCCAATCGGCTCACGTCCCCCTCC       c.1800
 E  P  H  V  I  R  V  Q  K  K  I  V  A  N  R  L  T  S  P  S         p.600

          .         .         .         .         .         .       g.49026
 TCAGCTCTGGTAAATGCCAGTGTGGCCTTTGAGTGCTGGATCAACTTCGGCACAGATGTT       c.1860
 S  A  L  V  N  A  S  V  A  F  E  C  W  I  N  F  G  T  D  V         p.620

          .         .         .         .         .         .       g.49086
 GCCTACCTGTGGGACTTTGGGGATGGCACCGTCAGCCTGGGGAGCAGCTCCAGCAGCCAT       c.1920
 A  Y  L  W  D  F  G  D  G  T  V  S  L  G  S  S  S  S  S  H         p.640

          .  | 13      .         .         .         .         .    g.51012
 GTCTACAGTAG | GGAAGGAGAATTTACAGTGGAGGTCCTTGCCTTCAATAATGTCAGTGCC    c.1980
 V  Y  S  R  |  E  G  E  F  T  V  E  V  L  A  F  N  N  V  S  A      p.660

          .         .         .         .         .         .       g.51072
 TCCACTCTAAGACAGCAACTTTTCATCGTGTGCGAGCCCTGCCAGCCACCCCTGGTGAAG       c.2040
 S  T  L  R  Q  Q  L  F  I  V  C  E  P  C  Q  P  P  L  V  K         p.680

          .         .     | 14   .         .         .         .    g.55316
 AACATGGGGCCTGGGAAAGTCCAG | ATATGGAGGTCTCAGCCTGTGAGGCTGGGAGTGACG    c.2100
 N  M  G  P  G  K  V  Q   | I  W  R  S  Q  P  V  R  L  G  V  T      p.700

          .         .         .         .         .         .       g.55376
 TTTGAAGCTGCAGTCTTCTGTGATATTTCCCAAGGTCTTTCTTACACCTGGAACTTGATG       c.2160
 F  E  A  A  V  F  C  D  I  S  Q  G  L  S  Y  T  W  N  L  M         p.720

          .         .         .         .         .         .       g.55436
 GACTCTGAAGGGCTCCCTGTCTCCCTCCCTGCTGCTGTGGACACTCACAGACAGACCCTC       c.2220
 D  S  E  G  L  P  V  S  L  P  A  A  V  D  T  H  R  Q  T  L         p.740

          .         .         .         .         .  | 15      .    g.59424
 ATCCTCCCGAGCCACACCTTGGAGTATGGGAACTACACTGCCCTTGCCAAG | GTTCAGATT    c.2280
 I  L  P  S  H  T  L  E  Y  G  N  Y  T  A  L  A  K   | V  Q  I      p.760

          .         .         .         .         .         .       g.59484
 GAAGGCAGTGTGGTGTACAGCAACTACTGTGTGGGCCTGGAGGTGCGAGCCCAGGCCCCT       c.2340
 E  G  S  V  V  Y  S  N  Y  C  V  G  L  E  V  R  A  Q  A  P         p.780

          .         .         .         .         .         .       g.59544
 GTCAGTGTGATCTCCGAGGGCACACACCTATTCTTCTCCAGGACCACCTCATCCCCCATT       c.2400
 V  S  V  I  S  E  G  T  H  L  F  F  S  R  T  T  S  S  P  I         p.800

          .         .         .         .         .    | 16    .    g.62717
 GTCCTCAGAGGGACCCAGTCCTTCGACCCTGACGACCCTGGGGCGACTCTCAG | GTATCAC    c.2460
 V  L  R  G  T  Q  S  F  D  P  D  D  P  G  A  T  L  R  |  Y  H      p.820

          .         .         .         .         .         .       g.62777
 TGGGAATGCGCCACCGCTGGCTCCCCAGCACATCCCTGCTTCGACTCCTCCACTGCACAC       c.2520
 W  E  C  A  T  A  G  S  P  A  H  P  C  F  D  S  S  T  A  H         p.840

          .         .         .         .         .         .       g.62837
 CAACTGGATGCCGCGGCTCCCACTGTTTCCTTTGAGGCACAATGGCTCAGTGACAGCTAT       c.2580
 Q  L  D  A  A  A  P  T  V  S  F  E  A  Q  W  L  S  D  S  Y         p.860

          .         .         .         .         .         .       g.62897
 GATCAGTTCCTTGTGATGCTGAGGGTCTCCAGTGGTGGCCGGAACTCTTCTGAGACCCGG       c.2640
 D  Q  F  L  V  M  L  R  V  S  S  G  G  R  N  S  S  E  T  R         p.880

          .         .         .      | 17  .         .         .    g.65348
 GTGTTCCTGTCCCCCTACCCTGACTCGGCGTTCAG | ATTCGTCCACATCTCCTGGGTCAGC    c.2700
 V  F  L  S  P  Y  P  D  S  A  F  R  |  F  V  H  I  S  W  V  S      p.900

          .         .         .         .         .         .       g.65408
 TTTAAAGACACCTTCGTCAACTGGAATGACGAACTCTCTCTTCAAGCTATGTGTGAGGAC       c.2760
 F  K  D  T  F  V  N  W  N  D  E  L  S  L  Q  A  M  C  E  D         p.920

          .         .         .         .         .         .       g.65468
 TGCAGTGAAATACCGAATCTGTCTTATTCCTGGGATCTCTTTTTAGTCAATGCAACAGAA       c.2820
 C  S  E  I  P  N  L  S  Y  S  W  D  L  F  L  V  N  A  T  E         p.940

          .       | 18 .         .         .         .         .    g.67463
 AAGAATAGGATAGAAG | TTCCCTTCTGCAGAGTAGTGGGGCTGCTTGGCTCGCTGGGACTC    c.2880
 K  N  R  I  E  V |   P  F  C  R  V  V  G  L  L  G  S  L  G  L      p.960

          .         .         .         .         .         .       g.67523
 GGTGCCATTTCAGAGTCATCACAGTTAAACCTGCTGCCCACTGAGCCTGGCACTGCAGAT       c.2940
 G  A  I  S  E  S  S  Q  L  N  L  L  P  T  E  P  G  T  A  D         p.980

          .         .         .         .         .         .       g.67583
 CCTGATGCAACGACCACACCATTCTCACGGGAACCTTCACCCGTGACCCTTGGCCAACCT       c.3000
 P  D  A  T  T  T  P  F  S  R  E  P  S  P  V  T  L  G  Q  P         p.1000

          .         .         .         .         .         .       g.67643
 GCCACTTCAGCTCCAAGGGGAACCCCCACAGAGCCCATGACTGGAGTCTACTGGATTCCT       c.3060
 A  T  S  A  P  R  G  T  P  T  E  P  M  T  G  V  Y  W  I  P         p.1020

          .         .         .         .         .         .       g.67703
 CCTGCGGGGGACTCTGCAGTCCTGGGGGAGGCTCCAGAGGAAGGTTCACTAGACCTAGAG       c.3120
 P  A  G  D  S  A  V  L  G  E  A  P  E  E  G  S  L  D  L  E         p.1040

          .         .         .         .         .         .       g.67763
 CCAGGGCCACAGAGCAAGGGATCCCTGATGACTGGCCGCTCTGAGAGAAGTCAGCCCACC       c.3180
 P  G  P  Q  S  K  G  S  L  M  T  G  R  S  E  R  S  Q  P  T         p.1060

          .         .      | 19  .         .         .         .    g.68851
 CACAGCCCTGACCCTCACCTCTCTG | ATTTTGAAGCCTATTACAGTGACATTCAAGAAGCA    c.3240
 H  S  P  D  P  H  L  S  D |   F  E  A  Y  Y  S  D  I  Q  E  A      p.1080

          .         .      | 20  .         .         .         .    g.71423
 ATACCATCGGGAGGAAGACAGCCAG | CTAAGGACACCAGCTTTCCAGGATCAGGACCTAGC    c.3300
 I  P  S  G  G  R  Q  P  A |   K  D  T  S  F  P  G  S  G  P  S      p.1100

          .         .         .         .         .         .       g.71483
 TTGAGTGCCGAGGAGAGCCCTGGAGATGGGGATAACCTGGTGGACCCCTCCCTGTCTGCA       c.3360
 L  S  A  E  E  S  P  G  D  G  D  N  L  V  D  P  S  L  S  A         p.1120

          .         .         .         .         .         .       g.71543
 GGCAGAGCCGAGCCTGTCCTCATGATTGACTGGCCCAAGGCCCTGCTGGGTCGAGCAGTT       c.3420
 G  R  A  E  P  V  L  M  I  D  W  P  K  A  L  L  G  R  A  V         p.1140

          .         .   | 21     .         .         .         .    g.72706
 TTCCAAGGCTATTCATCCTCAG | GTATTACAGAACAGACAGTGACAATCAAGCCATACTCT    c.3480
 F  Q  G  Y  S  S  S  G |   I  T  E  Q  T  V  T  I  K  P  Y  S      p.1160

          .         .         .         . | 22       .         .    g.75862
 CTGAGCAGTGGAGAGACGTACGTCCTGCAAGTGTCTGTGG | CTTCGAAGCATGGCTTACTG    c.3540
 L  S  S  G  E  T  Y  V  L  Q  V  S  V  A |   S  K  H  G  L  L      p.1180

          .         .         .         .         .         .       g.75922
 GGTAAAGCTCAGCTGTACTTGACAGTCAACCCGGCTCCTCGGGACATGGCCTGTCAGGTG       c.3600
 G  K  A  Q  L  Y  L  T  V  N  P  A  P  R  D  M  A  C  Q  V         p.1200

          .         .         .         .         .         .       g.75982
 CAGCCCCACCATGGTCTGGAAGCACACACCGTCTTCAGTGTCTTCTGCATGTCTGGAAAA       c.3660
 Q  P  H  H  G  L  E  A  H  T  V  F  S  V  F  C  M  S  G  K         p.1220

     | 23    .         .         .         .         .         .    g.77313
 CCG | GACTTCCATTATGAATTTAGTTACCAGATAGGAAACACCTCCAAACACACTTTGTAC    c.3720
 P   | D  F  H  Y  E  F  S  Y  Q  I  G  N  T  S  K  H  T  L  Y      p.1240

          .         .         .         .         .         .       g.77373
 CATGGGAGAGACACCCAGTATTATTTTGTGTTGCCAGCTGGTGAGCACTTGGACAATTAC       c.3780
 H  G  R  D  T  Q  Y  Y  F  V  L  P  A  G  E  H  L  D  N  Y         p.1260

      | 24   .         .         .         .         .         .    g.79519
 AAAG | TCATGGTTTCCACTGAAATCACAGATGGCAAAGGCTCCAAGGTCCAGCCGTGCACT    c.3840
 K  V |   M  V  S  T  E  I  T  D  G  K  G  S  K  V  Q  P  C  T      p.1280

          .         .         .         .         .       | 25 .    g.86863
 GTGGTGGTGACTGTGCTGCCCCGCTACCATGGAAATGACTGTCTGGGCGAGGACCT | GTAT    c.3900
 V  V  V  T  V  L  P  R  Y  H  G  N  D  C  L  G  E  D  L  |  Y      p.1300

          .         .         .         .         .         .       g.86923
 AATTCCAGCCTGAAAAACCTTTCTACCCTCCAGCTGATGGGGAGTTACACAGAAATCAGG       c.3960
 N  S  S  L  K  N  L  S  T  L  Q  L  M  G  S  Y  T  E  I  R         p.1320

          .         .         .         .         .         .       g.86983
 AACTACATCACTGTGATCACCAGAATCCTGAGTCGTTTGTCTAAGGAGGACAAAACTGCC       c.4020
 N  Y  I  T  V  I  T  R  I  L  S  R  L  S  K  E  D  K  T  A         p.1340

          .         .         .         .         .         .       g.87043
 TCCTGCAACCAATGGTCACGAATACAGGATGCATTAATTTCTTCAGTATGCAGATTGGCT       c.4080
 S  C  N  Q  W  S  R  I  Q  D  A  L  I  S  S  V  C  R  L  A         p.1360

          .   | 26     .         .         .         .         .    g.88249
 TTTGTAGATCAG | GAAGAAATGATTGGTTCTGTTCTTATGTTGAGGGACCTCGTGAGCTTC    c.4140
 F  V  D  Q   | E  E  M  I  G  S  V  L  M  L  R  D  L  V  S  F      p.1380

           | 27        .         .         .         .         .    g.94639
 TCTAATAAG | CTAGGCTTTATGAGTGCGGTTCTCATCCTCAAGTACACCCGGGCACTCCTT    c.4200
 S  N  K   | L  G  F  M  S  A  V  L  I  L  K  Y  T  R  A  L  L      p.1400

          .         .         .         .         .         .       g.94699
 GCTCAAGGCCAGTTCTCGGGGCCATTTGTGATTGACAAAGGAGTGAGGCTTGAGCTCATC       c.4260
 A  Q  G  Q  F  S  G  P  F  V  I  D  K  G  V  R  L  E  L  I         p.1420

          .         .         .         .         .         .       g.94759
 GGTCTCATATCCAGAGTCTGGGAAGTCTCTGAGCAAGAAAACTCGAAGGAGGAAGTCTAT       c.4320
 G  L  I  S  R  V  W  E  V  S  E  Q  E  N  S  K  E  E  V  Y         p.1440

          .         .         .         .   | 28     .         .    g.95659
 CGACATGAAGAAGGAATTACAGTCATCTCAGATTTATTGTTG | GGTTGTCTCTCTTTGAAC    c.4380
 R  H  E  E  G  I  T  V  I  S  D  L  L  L   | G  C  L  S  L  N      p.1460

          .         .         .         .         .         .       g.95719
 CATGTTAGCACTGGGCAGATGGAGTTCCGGACCCTTCTTCATTACAACCTTCAGAGCTCT       c.4440
 H  V  S  T  G  Q  M  E  F  R  T  L  L  H  Y  N  L  Q  S  S         p.1480

          .         .         .         .         .         .       g.95779
 GTCCAGAGCCTGGGATCTGTCCAGGTGCATTTACCTGGTGACCTTGCTGGGCACAGTCCT       c.4500
 V  Q  S  L  G  S  V  Q  V  H  L  P  G  D  L  A  G  H  S  P         p.1500

          .         .         .         .         .         .       g.95839
 GCTGGGGCGGAGACACAGAGCCCATGCTACATTAGCCAGCTCATACTCTTCAAGAAGAAC       c.4560
 A  G  A  E  T  Q  S  P  C  Y  I  S  Q  L  I  L  F  K  K  N         p.1520

          .         .         . | 29       .         .         .    g.98238
 CCATATCCAGGGAGCCAAGCTCCTGGGCAG | ATTGGTGGAGTTGTGGGCCTCAACCTCTAT    c.4620
 P  Y  P  G  S  Q  A  P  G  Q   | I  G  G  V  V  G  L  N  L  Y      p.1540

          .         .         .         .         .         .       g.98298
 ACCTGCTCCAGCAGAAGACCCATCAACAGGCAATGGCTAAGGAAACCCGTGATGGTCGAG       c.4680
 T  C  S  S  R  R  P  I  N  R  Q  W  L  R  K  P  V  M  V  E         p.1560

          .         .  | 30      .         .         .         .    g.98473
 TTTGGGGAGGAGGATGGCCTG | GATAATAGGAGAAATAAAACGACATTTGTATTACTTCGG    c.4740
 F  G  E  E  D  G  L   | D  N  R  R  N  K  T  T  F  V  L  L  R      p.1580

          .         .         .         .         .         .       g.98533
 GATAAAGTGAATCTCCATCAGTTCACTGAGCTTTCCGAAAACCCCCAGGAATCTCTACAG       c.4800
 D  K  V  N  L  H  Q  F  T  E  L  S  E  N  P  Q  E  S  L  Q         p.1600

          .         .         .         .         .          | 31    g.100247
 ATAGAAATTGAATTTTCCAAACCTGTTACAAGGGCATTTCCCGTCATGTTGCTAGTAAG | A    c.4860
 I  E  I  E  F  S  K  P  V  T  R  A  F  P  V  M  L  L  V  R  |      p.1620

          .         .         .         .         .         .       g.100307
 TTCTCTGAGAAACCTACTCCCTCTGATTTTCTTGTGAAGCAGATCTACTTCTGGGATGAG       c.4920
 F  S  E  K  P  T  P  S  D  F  L  V  K  Q  I  Y  F  W  D  E         p.1640

          .         .         .         . | 32       .         .    g.106422
 TCAATTGTGCAGATTTATATACCTGCTGCTTCTCAGAAAG | ATGCCAGTGTAGGCTATTTA    c.4980
 S  I  V  Q  I  Y  I  P  A  A  S  Q  K  D |   A  S  V  G  Y  L      p.1660

          .         .         .         .         .         .       g.106482
 TCCTTATTGGATGCTGACTATGACAGAAAACCTCCAAACAGATATTTAGCTAAGGCAGTG       c.5040
 S  L  L  D  A  D  Y  D  R  K  P  P  N  R  Y  L  A  K  A  V         p.1680

          .         .         .         .         .         .       g.106542
 AACTATACAGTACATTTCCAGTGGATCCGATGCCTGTTTTGGGACAAGAGAGAGTGGAAA       c.5100
 N  Y  T  V  H  F  Q  W  I  R  C  L  F  W  D  K  R  E  W  K         p.1700

          .         .         .         .         .    | 33    .    g.108402
 TCTGAACGTTTCTCTCCACAACCAGGGACTTCTCCTGAAAAAGTGAACTGCAG | CTACCAT    c.5160
 S  E  R  F  S  P  Q  P  G  T  S  P  E  K  V  N  C  S  |  Y  H      p.1720

          .         .         .         .         .         .       g.108462
 CGCCTCGCGGCATTCGCTCTCCTAAGGAGAAAGCTGAAGGCCAGTTTTGAAGTGAGTGAC       c.5220
 R  L  A  A  F  A  L  L  R  R  K  L  K  A  S  F  E  V  S  D         p.1740

          .        | 34.         .         .         .         .    g.110347
 ATTTCCAAGCTACAGAG | CCACCCAGAAAACTTGCTTCCCAGTATTTTTATTATGGGTTCT    c.5280
 I  S  K  L  Q  S  |  H  P  E  N  L  L  P  S  I  F  I  M  G  S      p.1760

          .         .         .         .         .         .       g.110407
 GTGATTCTTTATGGATTTTTGGTCGCTAAAAGTAGACAAGTAGATCATCATGAAAAAAAG       c.5340
 V  I  L  Y  G  F  L  V  A  K  S  R  Q  V  D  H  H  E  K  K         p.1780

          .         .         .         .         .         .       g.110467
 AAAGCTGGTTACATCTTTCTGCAAGAAGCTTCCCTGCCGGGCCATCAGCTATATGCGGTC       c.5400
 K  A  G  Y  I  F  L  Q  E  A  S  L  P  G  H  Q  L  Y  A  V         p.1800

          .         .         .         .      | 35  .         .    g.112921
 GTCATTGACACTGGCTTCCGAGCTCCGGCCAGGTTGACCTCAAAG | GTGTACATTGTTTTA    c.5460
 V  I  D  T  G  F  R  A  P  A  R  L  T  S  K   | V  Y  I  V  L      p.1820

          .         .         .         .         .         .       g.112981
 TGTGGCGACAATGGACTGTCAGAAACCAAGGAGCTCTCCTGTCCAGAGAAGCCCCTGTTT       c.5520
 C  G  D  N  G  L  S  E  T  K  E  L  S  C  P  E  K  P  L  F         p.1840

          .         .         .   | 36     .         .         .    g.113839
 GAAAGGAATTCCAGACACACCTTTATCCTGAG | CGCTCCTGCCCAACTGGGCCTGCTGAGG    c.5580
 E  R  N  S  R  H  T  F  I  L  S  |  A  P  A  Q  L  G  L  L  R      p.1860

          .         .         .         .         .         .       g.113899
 AAGATCCGCCTCTGGCACGACAGCCGTGGGCCTTCCCCAGGCTGGTTCATCAGCCACGTG       c.5640
 K  I  R  L  W  H  D  S  R  G  P  S  P  G  W  F  I  S  H  V         p.1880

          .         .         .         .         .         .       g.113959
 ATGGTGAAGGAGCTGCACACGGGACAGGGCTGGTTCTTCCCTGCCCAGTGCTGGCTGTCT       c.5700
 M  V  K  E  L  H  T  G  Q  G  W  F  F  P  A  Q  C  W  L  S         p.1900

          .         .         .         .         .         .       g.114019
 GCCGGCAGGCATGATGGTCGCGTGGAGCGGGAGCTCACCTGTCTGCAAGGGGGACTCGGC       c.5760
 A  G  R  H  D  G  R  V  E  R  E  L  T  C  L  Q  G  G  L  G         p.1920

           | 37        .         .         .         .         .    g.116430
 TTCCGGAAG | CTTTTCTATTGCAAGTTCACAGAGTACCTGGAGGATTTCCATGTCTGGCTG    c.5820
 F  R  K   | L  F  Y  C  K  F  T  E  Y  L  E  D  F  H  V  W  L      p.1940

          .         .         .         .         .         .       g.116490
 TCGGTGTACAGCAGGCCCTCCTCCAGCCGCTACCTGCACACGCCGCGCCTCACCGTGTCC       c.5880
 S  V  Y  S  R  P  S  S  S  R  Y  L  H  T  P  R  L  T  V  S         p.1960

          .         .         .         .         .         .       g.116550
 TTCTCCCTGCTGTGCGTCTACGCGTGTCTCACTGCCCTGGTTGCTGCTGGAGGGCAAGAG       c.5940
 F  S  L  L  C  V  Y  A  C  L  T  A  L  V  A  A  G  G  Q  E         p.1980

     | 38    .         .         .         .         .         .    g.118287
 CAG | CCCCACTTGGACGTCAGCCCCACCCTTGGATCCTTCAGGGTGGGTCTCCTGTGTACC    c.6000
 Q   | P  H  L  D  V  S  P  T  L  G  S  F  R  V  G  L  L  C  T      p.2000

          .         .         .         .         .     | 39   .    g.118440
 CTCCTGGCTTCTCCAGGGGCCCAGCTCTTGTCCCTGCTCTTCAGGCTCAGCAAG | GAAGCC    c.6060
 L  L  A  S  P  G  A  Q  L  L  S  L  L  F  R  L  S  K   | E  A      p.2020

          .         .         .         .         .         .       g.118500
 CCGGGGTCTGCCCGAGTGGAGCCACACAGCCCACTTAGAGGAGGAGCACAGACCGAGGCA       c.6120
 P  G  S  A  R  V  E  P  H  S  P  L  R  G  G  A  Q  T  E  A         p.2040

         | 40.         .         .         .         .     | 41   . g.120227
 CCCCATG | GTCCTAATTCCTGGGGAAGGATACCAGACGCACAGGAGCCACGCAAG | CAACCT c.6180
 P  H  G |   P  N  S  W  G  R  I  P  D  A  Q  E  P  R  K   | Q  P   p.2060

          .         .         .         .         .         .       g.120287
 GCATCAGCCATTCTCTCTGGGAGTGGCAGGGCCCAAAGGAAGGCGGCAAGTGACAATGGC       c.6240
 A  S  A  I  L  S  G  S  G  R  A  Q  R  K  A  A  S  D  N  G         p.2080

          .         .         .         .         .         .       g.120347
 ACAGCTTGTCCAGCCCCTAAGCTGCAGGTTCATGGGGCTGACCACAGCAGGACTTCTCTG       c.6300
 T  A  C  P  A  P  K  L  Q  V  H  G  A  D  H  S  R  T  S  L         p.2100

          .         .         .        | 42.         .         .    g.122144
 ATGGGGAAAAGCCACTGCTGCCCTCCCCACACTCAAG | CACCCAGCAGTGGTTTGGAGGGA    c.6360
 M  G  K  S  H  C  C  P  P  H  T  Q  A |   P  S  S  G  L  E  G      p.2120

          .         .         .         .         .         .       g.122204
 CTAATGCCCCAGTGGTCAAGGGCCCTTCAGCCTTGGTGGAGCTCTGCAGTGTGGGCCATT       c.6420
 L  M  P  Q  W  S  R  A  L  Q  P  W  W  S  S  A  V  W  A  I         p.2140

          .         .         .         .         .    | 43    .    g.123356
 TGTGGGACCGCTTCTTTGGCCTGCAGTTTGGGGACAGGATTTCTAGCCTACAG | GTTTGGC    c.6480
 C  G  T  A  S  L  A  C  S  L  G  T  G  F  L  A  Y  R  |  F  G      p.2160

          .         .         .         .         .         .       g.123416
 CAGGAGCAATGTGTGCAGTGGCTGCACCTGCTGTCCCTCTCCGTGGTCTGCTGTATTTTC       c.6540
 Q  E  Q  C  V  Q  W  L  H  L  L  S  L  S  V  V  C  C  I  F         p.2180

          .         | 44         .         .         .         .    g.123914
 ATCACCCAGCCACTTATG | GTATGCCTCATGGCCTTGGGTTTTGCTTGGAAAAGAAGAGCT    c.6600
 I  T  Q  P  L  M   | V  C  L  M  A  L  G  F  A  W  K  R  R  A      p.2200

          .         .         .         .         .         .       g.123974
 GACAACCACTTTTTTACTGAGTCTTTATGTGAGGCTACCAGGGATCTGGACTCTGAATTG       c.6660
 D  N  H  F  F  T  E  S  L  C  E  A  T  R  D  L  D  S  E  L         p.2220

          .         .         .         .         .         .       g.124034
 GCAGAACGTTCCTGGACTCGCCTCCCCTTCTCTTCAAGCTGCAGTATTCCTGACTGTGCA       c.6720
 A  E  R  S  W  T  R  L  P  F  S  S  S  C  S  I  P  D  C  A         p.2240

          .      | 45  .         .         .         .         .    g.126050
 GGCGAGGTTGAAAAA | GTCTTGGCTGCCCGACAACAAGCTCGCCACCTGCGCTGGGCGCAT    c.6780
 G  E  V  E  K   | V  L  A  A  R  Q  Q  A  R  H  L  R  W  A  H      p.2260

          .         .         .         .         .         .       g.126110
 CCACCATCCAAGGCCCAGCTGAGGGGCACCAGACAGAGGATGAGGAGAGAGAGTCGCACA       c.6840
 P  P  S  K  A  Q  L  R  G  T  R  Q  R  M  R  R  E  S  R  T         p.2280

          .     | 46   .         .         .         .         .    g.132333
 CGGGCTGCCCTGAG | AGACATTTCCATGGACATCCTCATGCTGCTTCTGCTTTTGTGTGTA    c.6900
 R  A  A  L  R  |  D  I  S  M  D  I  L  M  L  L  L  L  L  C  V      p.2300

          .         .         .         .         .         .       g.132393
 ATATATGGGAGATTTTCCCAAGATGAATACTCCCTCAATCAAGCTATCCGGAAAGAATTT       c.6960
 I  Y  G  R  F  S  Q  D  E  Y  S  L  N  Q  A  I  R  K  E  F         p.2320

       | 47  .         .         .         .         .         .    g.138071
 ACAAG | AAATGCCAGAAACTGCTTGGGTGGCCTGAGAAACATCGCTGACTGGTGGGACTGG    c.7020
 T  R  |  N  A  R  N  C  L  G  G  L  R  N  I  A  D  W  W  D  W      p.2340

          .         .         .         .         .         .       g.138131
 AGTCTGACCACACTTCTGGATGGCCTGTACCCGGGAGGCACCCCGTCAGCCCGTGTGCCG       c.7080
 S  L  T  T  L  L  D  G  L  Y  P  G  G  T  P  S  A  R  V  P         p.2360

           | 48        .         .         .         .         .    g.139510
 GGGGCTCAG | CCTGGAGCTCTTGGAGGAAAATGCTACCTAATAGGCAGTTCCGTAATTAGG    c.7140
 G  A  Q   | P  G  A  L  G  G  K  C  Y  L  I  G  S  S  V  I  R      p.2380

          .         .         .    | 49    .         .         .    g.140207
 CAGCTAAAAGTTTTTCCTAGGCATTTATGCAAG | CCTCCCAGGCCATTTTCAGCACTCATC    c.7200
 Q  L  K  V  F  P  R  H  L  C  K   | P  P  R  P  F  S  A  L  I      p.2400

          .         .         .         .         .         .       g.140267
 GAAGACTCTATTCCTACATGTAGTCCCGAAGTTGGAGGCCCTGAGAACCCCTACCTGATA       c.7260
 E  D  S  I  P  T  C  S  P  E  V  G  G  P  E  N  P  Y  L  I         p.2420

          .         .         .         .         .         .       g.140327
 GACCCAGAGAACCAAAACGTGACCCTGAATGGTCCTGGGGGCTGTGGGACAAGGGAGGAC       c.7320
 D  P  E  N  Q  N  V  T  L  N  G  P  G  G  C  G  T  R  E  D         p.2440

          .         .       | 50 .         .         .         .    g.141456
 TGTGTGCTCAGCCTGGGCAGAACAAG | GACTGAAGCCCACACAGCCCTGTCCCGACTCAGG    c.7380
 C  V  L  S  L  G  R  T  R  |  T  E  A  H  T  A  L  S  R  L  R      p.2460

          .         .         .         .         .         .       g.141516
 GCCAGCATGTGGATTGACCGCAGCACCAGGGCTGTGTCTGTGCACTTCACTCTCTATAAC       c.7440
 A  S  M  W  I  D  R  S  T  R  A  V  S  V  H  F  T  L  Y  N         p.2480

          .         .         .         .         .         .       g.141576
 CCTCCAACCCAACTCTTCACCAGCGTGTCCCTGAGAGTGGAGATCCTCCCTACGGGGAGT       c.7500
 P  P  T  Q  L  F  T  S  V  S  L  R  V  E  I  L  P  T  G  S         p.2500

          .         .         .         .         .         .       g.141636
 CTCGTCCCCTCATCCCTGGTGGAGTCATTCAGCATCTTCCGCAGCGACTCAGCCCTGCAG       c.7560
 L  V  P  S  S  L  V  E  S  F  S  I  F  R  S  D  S  A  L  Q         p.2520

          .         .  | 51      .         .         .         .    g.143935
 TACCACCTCATGCTTCCCCAG | CTGGTCTTCCTGGCACTCAGCCTGATCCACCTCTGTGTT    c.7620
 Y  H  L  M  L  P  Q   | L  V  F  L  A  L  S  L  I  H  L  C  V      p.2540

          .         .         .         .         .         .       g.143995
 CAACTCTACCGTATGATGGACAAGGGCGTCCTCAGCTACTGGCGAAAGCCAAGGAACTGG       c.7680
 Q  L  Y  R  M  M  D  K  G  V  L  S  Y  W  R  K  P  R  N  W         p.2560

        | 52 .         .         .         .         .         .    g.145140
 CTGGAG | CTCTCCGTGGTTGGAGTGAGCCTCACCTACTATGCAGTTTCCGGCCACCTTGTT    c.7740
 L  E   | L  S  V  V  G  V  S  L  T  Y  Y  A  V  S  G  H  L  V      p.2580

          .         .         .         .         .         .       g.145200
 ACTCTTGCTGGAGATGTCACTAACCAGTTTCACAGAGGACTTTGCCGAGCATTTATGGAC       c.7800
 T  L  A  G  D  V  T  N  Q  F  H  R  G  L  C  R  A  F  M  D         p.2600

          .         .        | 53.         .         .         .    g.150162
 CTCACCCTTATGGCATCATGGAATCAG | AGGGCTCGATGGCTCCGGGGAATCCTCTTATTC    c.7860
 L  T  L  M  A  S  W  N  Q   | R  A  R  W  L  R  G  I  L  L  F      p.2620

          .         .         .         .         .         .       g.150222
 CTCTTCACATTAAAATGCGTCTATCTTCCTGGCATTCAAAACACAATGGCATCCTGCTCC       c.7920
 L  F  T  L  K  C  V  Y  L  P  G  I  Q  N  T  M  A  S  C  S         p.2640

          .         .         .         .   | 54     .         .    g.152612
 TCCATGATGCGCCACTCACTCCCCAGCATCTTTGTAGCAGGG | CTGGTGGGGGCACTGATG    c.7980
 S  M  M  R  H  S  L  P  S  I  F  V  A  G   | L  V  G  A  L  M      p.2660

          .         .         .         .         .         .       g.152672
 CTGGCCGCCCTCTCCCACCTGCACCGATTTCTGCTCTCTATGTGGGTTCTACCACCTGGC       c.8040
 L  A  A  L  S  H  L  H  R  F  L  L  S  M  W  V  L  P  P  G         p.2680

          .         .         .         .         .         .       g.152732
 ACCTTCACAGACGCCTTCCCCGGGCTGCTGTTTCATTTTCCCAGAAGAAGCCAAAAAGAC       c.8100
 T  F  T  D  A  F  P  G  L  L  F  H  F  P  R  R  S  Q  K  D         p.2700

          .         .         .         .         .         .       g.152792
 TGCCTCCTTGGCCTTTCCAAGTCTGACCAGCGGGCCATGGCTTGTTACTTTGGGATCCTT       c.8160
 C  L  L  G  L  S  K  S  D  Q  R  A  M  A  C  Y  F  G  I  L         p.2720

          .         .         .    | 55    .         .         .    g.157350
 TTAATAGTCTCTGCCACACTGTGTTTTGGAATG | CTGAGAGGTTTTCTCATGACTTTACCC    c.8220
 L  I  V  S  A  T  L  C  F  G  M   | L  R  G  F  L  M  T  L  P      p.2740

          .         .         .         .         .         .       g.157410
 CAAAAAAGAAAATCTTTTCAAAGTAAATCTTTTGTGAGACTTAAAGATGTCACTGCTTAT       c.8280
 Q  K  R  K  S  F  Q  S  K  S  F  V  R  L  K  D  V  T  A  Y         p.2760

          .         .         .         .         .         .       g.157470
 ATGTGGGAAAAGGTCCTCACCTTTCTGAGACTGGAAACACCAAAGTTGGAAGAGGCTGAG       c.8340
 M  W  E  K  V  L  T  F  L  R  L  E  T  P  K  L  E  E  A  E         p.2780

          .      | 56  .         .         .         .         .    g.160721
 ATGGTTGAGAATCAC | AATTACTACTTGGATGAATTTGCAAATCTGTTAGACGAACTTCTG    c.8400
 M  V  E  N  H   | N  Y  Y  L  D  E  F  A  N  L  L  D  E  L  L      p.2800

          .         .         .         .         .         .       g.160781
 ATGAAGATTAATGGTTTGTCCGACAGCCTACAACTCCCCCTTCTGGAAAAAACATCCAAC       c.8460
 M  K  I  N  G  L  S  D  S  L  Q  L  P  L  L  E  K  T  S  N         p.2820

          .         .         .         .         .         .       g.160841
 AACACAGGGGAGGCAAGGACAGAAGAGAGTCCCTTAGTGGACATTTCTAGTTACCAAGCT       c.8520
 N  T  G  E  A  R  T  E  E  S  P  L  V  D  I  S  S  Y  Q  A         p.2840

        | 57 .         .         .                                  g.178361
 GCTGAG | CCAGCAGACATCAAGGACTTCTGA                                  c.8550
 A  E   | P  A  D  I  K  D  F  X                                    p.2849

          .         .         .         .         .         .       g.178421
 ggagcctggtaccttgcataggcactatggaccctgttttgcttaacccacccaacagcc       c.*60

          .         .         .         .         .         .       g.178481
 aattttagcagacatcctagttttgcaggtgagaagagctgaggtacgaagaagttttgt       c.*120

          .         .         .         .         .         .       g.178541
 taatttttccagttcacgtaacaagtaaatgggaaaccaggatgaaaatcaaggtttatc       c.*180

          .         .         .         .         .         .       g.178601
 tgtcatcagactgttactcataatcaccattcggagagttcagatgtgggacaagattct       c.*240

          .         .         .         .         .         .       g.178661
 aactccagccttctcccaaatggttaatttgccagttgccctagagttacatattgtctt       c.*300

          .         .         .         .         .         .       g.178721
 atttgtttgttttactgaatctgtctgagtattaaaagccttgtatcttgtgaaatttct       c.*360

          .         .         .         .         .         .       g.178781
 ttcaggtctcataaaagcgatgaaagagaccaggataacattctaatatttaaataagat       c.*420

          .         .         .         .         .         .       g.178841
 ttttgaagtaaaatccttattttgtaaatttaacaattgaatcttgctagattaataacg       c.*480

          .                                                         g.178852
 catctttcctg                                                        c.*491

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Polycystic kidney disease 1 like 1 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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