serine hydroxymethyltransferase 2 (mitochondrial) (SHMT2) - coding DNA reference sequence

(used for variant description)

(last modified November 1, 2020)


This file was created to facilitate the description of sequence variants on transcript NM_005412.5 in the SHMT2 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_029163.1, covering SHMT2 transcript NM_005412.5.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                         .         .                g.5026
                                   ataaagaaaaaagcggtgagtgggcg       c.-181

 .         .         .         .         .         .                g.5086
 aactacaattcccaaaaggccacaaaggggccaccactacgcatgcgtagatccctcccg       c.-121

 .         .         .         .         .         .                g.5146
 ttagctttggcgcctcagcgagctcttctcgcgcatgcgttctccgaacggtcttcttcc       c.-61

 .         .         .         .         .         .                g.5206
 gacagcttgctgccctagaccagagttggtggctggacctcctgcgacttccgagttgcg       c.-1

          .         .         .    | 02    .         .         .    g.6257
 ATGCTGTACTTCTCTTTGTTTTGGGCGGCTCGG | CCTCTGCAGAGATGTGGGCAGCTGGTC    c.60
 M  L  Y  F  S  L  F  W  A  A  R   | P  L  Q  R  C  G  Q  L  V      p.20

          .         .         .         .         .         .       g.6317
 AGGATGGCCATTCGGGCTCAGCACAGCAACGCAGCCCAGACTCAGACTGGGGAAGCAAAC       c.120
 R  M  A  I  R  A  Q  H  S  N  A  A  Q  T  Q  T  G  E  A  N         p.40

          .         .         .         .         .         .       g.6377
 AGGGGCTGGACAGGCCAGGAGAGCCTGTCGGACAGTGATCCTGAGATGTGGGAGTTGCTG       c.180
 R  G  W  T  G  Q  E  S  L  S  D  S  D  P  E  M  W  E  L  L         p.60

          .         .         .         .         .  | 03      .    g.6917
 CAGAGGGAGAAGGACAGGCAGTGTCGTGGCCTGGAGCTCATTGCCTCAGAG | AACTTCTGC    c.240
 Q  R  E  K  D  R  Q  C  R  G  L  E  L  I  A  S  E   | N  F  C      p.80

          .         .         .         .         .         .       g.6977
 AGCCGAGCTGCGCTGGAGGCCCTGGGGTCCTGTCTGAACAACAAGTACTCGGAGGGTTAT       c.300
 S  R  A  A  L  E  A  L  G  S  C  L  N  N  K  Y  S  E  G  Y         p.100

          .  | 04      .         .         .         .         .    g.7189
 CCTGGCAAGAG | ATACTATGGGGGAGCAGAGGTGGTGGATGAAATTGAGCTGCTGTGCCAG    c.360
 P  G  K  R  |  Y  Y  G  G  A  E  V  V  D  E  I  E  L  L  C  Q      p.120

          .         .         .         .         .         .       g.7249
 CGCCGGGCCTTGGAAGCCTTTGACCTGGATCCTGCACAGTGGGGAGTCAATGTCCAGCCC       c.420
 R  R  A  L  E  A  F  D  L  D  P  A  Q  W  G  V  N  V  Q  P         p.140

          .         .         .         .         .         .       g.7309
 TACTCCGGGTCCCCAGCCAACCTGGCCGTCTACACAGCCCTTCTGCAACCTCACGACCGG       c.480
 Y  S  G  S  P  A  N  L  A  V  Y  T  A  L  L  Q  P  H  D  R         p.160

          .         .         .   | 05     .         .         .    g.7666
 ATCATGGGGCTGGACCTGCCCGATGGGGGCCA | TCTCACCCACGGCTACATGTCTGACGTC    c.540
 I  M  G  L  D  L  P  D  G  G  H  |  L  T  H  G  Y  M  S  D  V      p.180

          .         .         .         .         .     | 06   .    g.7886
 AAGCGGATATCAGCCACGTCCATCTTCTTCGAGTCTATGCCCTATAAGCTCAAC | CCCAAA    c.600
 K  R  I  S  A  T  S  I  F  F  E  S  M  P  Y  K  L  N   | P  K      p.200

          .         .         .         .         .         .       g.7946
 ACTGGCCTCATTGACTACAACCAGCTGGCACTGACTGCTCGACTTTTCCGGCCACGGCTC       c.660
 T  G  L  I  D  Y  N  Q  L  A  L  T  A  R  L  F  R  P  R  L         p.220

          .         .         .         .         .        | 07.    g.8134
 ATCATAGCTGGCACCAGCGCCTATGCTCGCCTCATTGACTACGCCCGCATGAGAGAG | GTG    c.720
 I  I  A  G  T  S  A  Y  A  R  L  I  D  Y  A  R  M  R  E   | V      p.240

          .         .         .         .         .         .       g.8194
 TGTGATGAAGTCAAAGCACACCTGCTGGCAGACATGGCCCACATCAGTGGCCTGGTGGCT       c.780
 C  D  E  V  K  A  H  L  L  A  D  M  A  H  I  S  G  L  V  A         p.260

          .         .         .         .         .         .       g.8254
 GCCAAGGTGATTCCCTCGCCTTTCAAGCACGCGGACATCGTCACCACCACTACTCACAAG       c.840
 A  K  V  I  P  S  P  F  K  H  A  D  I  V  T  T  T  T  H  K         p.280

          .        | 08.         .         .         .         .    g.8650
 ACTCTTCGAGGGGCCAG | GTCAGGGCTCATCTTCTACCGGAAAGGGGTGAAGGCTGTGGAC    c.900
 T  L  R  G  A  R  |  S  G  L  I  F  Y  R  K  G  V  K  A  V  D      p.300

          .         .         .         .         .         .       g.8710
 CCCAAGACTGGCCGGGAGATCCCTTACACATTTGAGGACCGAATCAACTTTGCCGTGTTC       c.960
 P  K  T  G  R  E  I  P  Y  T  F  E  D  R  I  N  F  A  V  F         p.320

          .         .         .         .         .         .       g.8770
 CCATCCCTGCAGGGGGGCCCCCACAATCATGCCATTGCTGCAGTAGCTGTGGCCCTAAAG       c.1020
 P  S  L  Q  G  G  P  H  N  H  A  I  A  A  V  A  V  A  L  K         p.340

     | 09    .         .         .         .         .         .    g.9047
 CAG | GCCTGCACCCCCATGTTCCGGGAGTACTCCCTGCAGGTTCTGAAGAATGCTCGGGCC    c.1080
 Q   | A  C  T  P  M  F  R  E  Y  S  L  Q  V  L  K  N  A  R  A      p.360

          .         .         .         .    | 10    .         .    g.9193
 ATGGCAGATGCCCTGCTAGAGCGAGGCTACTCACTGGTATCAG | GTGGTACTGACAACCAC    c.1140
 M  A  D  A  L  L  E  R  G  Y  S  L  V  S  G |   G  T  D  N  H      p.380

          .         .         .         .         .         .       g.9253
 CTGGTGCTGGTGGACCTGCGGCCCAAGGGCCTGGATGGAGCTCGGGCTGAGCGGGTGCTA       c.1200
 L  V  L  V  D  L  R  P  K  G  L  D  G  A  R  A  E  R  V  L         p.400

          .         .         .         .         .         .       g.9313
 GAGCTTGTATCCATCACTGCCAACAAGAACACCTGTCCTGGAGACCGAAGTGCCATCACA       c.1260
 E  L  V  S  I  T  A  N  K  N  T  C  P  G  D  R  S  A  I  T         p.420

          .          | 11        .         .         .         .    g.9471
 CCGGGCGGCCTGCGGCTTG | GGGCCCCAGCCTTAACTTCTCGACAGTTCCGTGAGGATGAC    c.1320
 P  G  G  L  R  L  G |   A  P  A  L  T  S  R  Q  F  R  E  D  D      p.440

          .         .         .         .         .         .       g.9531
 TTCCGGAGAGTTGTGGACTTTATAGATGAAGGGGTCAACATTGGCTTAGAGGTGAAGAGC       c.1380
 F  R  R  V  V  D  F  I  D  E  G  V  N  I  G  L  E  V  K  S         p.460

         | 12.         .         .         .         .         .    g.9714
 AAGACTG | CCAAGCTCCAGGATTTCAAATCCTTCCTGCTTAAGGACTCAGAAACAAGTCAG    c.1440
 K  T  A |   K  L  Q  D  F  K  S  F  L  L  K  D  S  E  T  S  Q      p.480

          .         .         .         .         .         .       g.9774
 CGTCTGGCCAACCTCAGGCAACGGGTGGAGCAGTTTGCCAGGGCCTTCCCCATGCCTGGT       c.1500
 R  L  A  N  L  R  Q  R  V  E  Q  F  A  R  A  F  P  M  P  G         p.500

          .                                                         g.9789
 TTTGATGAGCATTGA                                                    c.1515
 F  D  E  H  X                                                      p.504

          .         .         .         .         .         .       g.9849
 aggcacctgggaaatgaggcccacagactcaaagttactctccttccccctacctgggcc       c.*60

          .         .         .         .         .         .       g.9909
 agtgaaatagaaagcctttctattttttggtgcgggagggaagacctctcacttagggca       c.*120

          .         .         .         .         .         .       g.9969
 agagccaggtatagtctcccttcccagaatttgtaactgagaagatcttttctttttcct       c.*180

          .         .         .         .         .         .       g.10029
 ttttttggtaacaagacttagaaggagggcccaggcactttctgtttgaacccctgtcat       c.*240

          .         .         .         .         .         .       g.10089
 gatcacagtgtcagagacgcgtcctctttcttggggaagttgaggagtgcccttcagagc       c.*300

          .         .         .         .         .         .       g.10149
 cagtagcaggcaggggtgggtaggcaccctccttcctgtttttatctaataaaatgctaa       c.*360

          .         .         .         .         .         .       g.10209
 cctgccctgagtttccattactgtgggtggggttcccctgggccaaacagtgatttgtct       c.*420

          .         .         .         .         .         .       g.10269
 ccctcaatgtgtacaccgctccgctcccaccaccgctaccacaaggacccccggggctgc       c.*480

          .         .         .         .         .         .       g.10329
 agcctcctctttctgtctctgatcagagccgacaccagacgtgattagcaggcgcagcaa       c.*540

          .         .         .                                     g.10363
 attcaatttgttaaatgaaattgtattttgccca                                 c.*574

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Serine hydroxymethyltransferase 2 (mitochondrial) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

Powered by LOVD v.3.0 Build 25
©2004-2020 Leiden University Medical Center