spastic paraplegia 7 (pure and complicated autosomal recessive) (SPG7) - coding DNA reference sequence

(used for variant description)

(last modified June 12, 2016)


This file was created to facilitate the description of sequence variants on transcript NM_003119.2 in the SPG7 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_008082.1, covering SPG7 transcript NM_003119.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                                         .         .                g.5021
                                        aggcgcggctttcaggccaac       c.-1

          .         .         .         .         .         .       g.5081
 ATGGCCGTGCTGCTGCTGCTGCTCCGTGCCCTCCGCCGGGGTCCAGGCCCGGGTCCTCGG       c.60
 M  A  V  L  L  L  L  L  R  A  L  R  R  G  P  G  P  G  P  R         p.20

          .         .         .         .         .         .       g.5141
 CCGCTGTGGGGCCCAGGCCCGGCCTGGAGTCCAGGGTTCCCCGCCAGGCCCGGGAGGGGG       c.120
 P  L  W  G  P  G  P  A  W  S  P  G  F  P  A  R  P  G  R  G         p.40

          .         .         .         .         .         .       g.5201
 CGGCCGTACATGGCCAGCAGGCCTCCGGGGGACCTCGCCGAGGCTGGAGGCCGAGCTCTG       c.180
 R  P  Y  M  A  S  R  P  P  G  D  L  A  E  A  G  G  R  A  L         p.60

     | 02    .         .         .         .         .         .    g.7150
 CAG | AGCTTACAATTGAGACTGCTAACCCCTACCTTTGAAGGGATCAACGGATTGTTGTTG    c.240
 Q   | S  L  Q  L  R  L  L  T  P  T  F  E  G  I  N  G  L  L  L      p.80

          .         .         .         .       | 03 .         .    g.9565
 AAACAACATTTAGTTCAGAATCCAGTCAGACTCTGGCAACTTTTAG | GTGGTACTTTCTAT    c.300
 K  Q  H  L  V  Q  N  P  V  R  L  W  Q  L  L  G |   G  T  F  Y      p.100

          .         .         .         .         .         .       g.9625
 TTTAACACCTCAAGGTTGAAGCAGAAGAATAAGGAGAAGGATAAGTCGAAGGGGAAGGCG       c.360
 F  N  T  S  R  L  K  Q  K  N  K  E  K  D  K  S  K  G  K  A         p.120

          .       | 04 .         .         .         .         .    g.20653
 CCTGAAGAGGACGAAG | AGGAGAGGAGACGCCGTGAGCGGGACGACCAGATGTACCGAGAG    c.420
 P  E  E  D  E  E |   E  R  R  R  R  E  R  D  D  Q  M  Y  R  E      p.140

          .         .         .         .         .         .       g.20713
 CGGCTGCGCACCTTGCTGGTCATCGCGGTTGTCATGAGCCTCCTGAATGCTCTCAGCACC       c.480
 R  L  R  T  L  L  V  I  A  V  V  M  S  L  L  N  A  L  S  T         p.160

          .         .         .         .         .         .       g.20773
 AGCGGAGGCAGCATTTCCTGGAACGACTTTGTCCACGAGATGCTGGCCAAGGGCGAGGTG       c.540
 S  G  G  S  I  S  W  N  D  F  V  H  E  M  L  A  K  G  E  V         p.180

          .         .         .         .         .         .       g.20833
 CAGCGCGTCCAGGTGGTGCCTGAGAGCGACGTGGTGGAAGTCTACCTGCACCCTGGAGCC       c.600
 Q  R  V  Q  V  V  P  E  S  D  V  V  E  V  Y  L  H  P  G  A         p.200

          .         | 05         .         .         .         .    g.22974
 GTGGTGTTTGGGCGGCCT | CGGCTAGCCTTGATGTACCGAATGCAGGTTGCAAATATTGAC    c.660
 V  V  F  G  R  P   | R  L  A  L  M  Y  R  M  Q  V  A  N  I  D      p.220

          .         .         .         .         .         .       g.23034
 AAGTTTGAAGAGAAGCTTCGAGCAGCTGAAGATGAGCTGAATATCGAGGCCAAGGACAGG       c.720
 K  F  E  E  K  L  R  A  A  E  D  E  L  N  I  E  A  K  D  R         p.240

          .         .         .         | 06         .         .    g.26102
 ATCCCAGTTTCCTACAAGCGAACAGGATTCTTTGGAAA | TGCCCTGTACTCTGTGGGGATG    c.780
 I  P  V  S  Y  K  R  T  G  F  F  G  N  |  A  L  Y  S  V  G  M      p.260

          .         .         .         .         .         .       g.26162
 ACGGCAGTGGGCCTGGCCATCCTGTGGTATGTTTTCCGTCTGGCCGGGATGACTGGAAGG       c.840
 T  A  V  G  L  A  I  L  W  Y  V  F  R  L  A  G  M  T  G  R         p.280

          .         .  | 07      .         .         .         .    g.27325
 GAAGGTGGATTCAGTGCTTTT | AATCAGCTTAAAATGGCTCGTTTCACCATTGTGGATGGG    c.900
 E  G  G  F  S  A  F   | N  Q  L  K  M  A  R  F  T  I  V  D  G      p.300

          .         .         .         .         .         .       g.27385
 AAGATGGGGAAAGGAGTCAGCTTCAAAGACGTGGCAGGAATGCACGAAGCCAAACTGGAA       c.960
 K  M  G  K  G  V  S  F  K  D  V  A  G  M  H  E  A  K  L  E         p.320

          .         .        | 08.         .         .         .    g.28540
 GTCCGCGAGTTTGTGGATTATCTGAAG | AGCCCAGAACGCTTCCTCCAGCTTGGCGCCAAG    c.1020
 V  R  E  F  V  D  Y  L  K   | S  P  E  R  F  L  Q  L  G  A  K      p.340

          .         .         .         .         .         .       g.28600
 GTCCCAAAGGGCGCACTGCTGCTCGGCCCCCCCGGCTGTGGGAAGACGCTGCTGGCCAAG       c.1080
 V  P  K  G  A  L  L  L  G  P  P  G  C  G  K  T  L  L  A  K         p.360

          .         .         .         .         .         .       g.28660
 GCGGTGGCCACGGAGGCTCAGGTGCCCTTCCTGGCGATGGCCGGCCCAGAGTTCGTGGAG       c.1140
 A  V  A  T  E  A  Q  V  P  F  L  A  M  A  G  P  E  F  V  E         p.380

          . | 09       .         .         .         .         .    g.29116
 GTCATTGGAG | GCCTCGGCGCTGCCCGTGTGCGGAGCCTCTTTAAGGAAGCCCGAGCCCGG    c.1200
 V  I  G  G |   L  G  A  A  R  V  R  S  L  F  K  E  A  R  A  R      p.400

          .         .         .         .         .         .       g.29176
 GCCCCCTGCATCGTCTACATCGATGAGATCGACGCGGTGGGCAAGAAGCGCTCCACCACC       c.1260
 A  P  C  I  V  Y  I  D  E  I  D  A  V  G  K  K  R  S  T  T         p.420

          .         .         .         .         .         .       g.29236
 ATGTCCGGCTTCTCCAACACGGAGGAGGAGCAGACGCTCAACCAGCTTCTGGTAGAAATG       c.1320
 M  S  G  F  S  N  T  E  E  E  Q  T  L  N  Q  L  L  V  E  M         p.440

      | 10   .         .         .         .         .         .    g.41307
 GATG | GAATGGGTACCACAGACCATGTCATCGTCCTGGCGTCCACGAACCGAGCTGACATT    c.1380
 D  G |   M  G  T  T  D  H  V  I  V  L  A  S  T  N  R  A  D  I      p.460

          .         .         .         .         .         .       g.41367
 TTGGACGGTGCTCTGATGAGGCCAGGCCGACTGGACCGGCACGTCTTCATTGATCTCCCC       c.1440
 L  D  G  A  L  M  R  P  G  R  L  D  R  H  V  F  I  D  L  P         p.480

           | 11        .         .         .         .         .    g.43312
 ACGCTGCAG | GAGAGGCGGGAGATTTTTGAGCAGCACCTGAAGAGCCTGAAGCTGACCCAG    c.1500
 T  L  Q   | E  R  R  E  I  F  E  Q  H  L  K  S  L  K  L  T  Q      p.500

          .         .         .         .         .   | 12     .    g.44614
 TCCAGCACCTTTTACTCCCAGCGTCTGGCAGAGCTGACACCAGGATTCAGTG | GGGCTGAC    c.1560
 S  S  T  F  Y  S  Q  R  L  A  E  L  T  P  G  F  S  G |   A  D      p.520

          .         .         .         .         .         .       g.44674
 ATCGCCAACATCTGCAATGAGGCTGCGCTGCACGCGGCGCGGGAGGGACACACTTCCGTG       c.1620
 I  A  N  I  C  N  E  A  A  L  H  A  A  R  E  G  H  T  S  V         p.540

          .         .         .         .    | 13    .         .    g.47114
 CACACTCTCAACTTCGAGTACGCCGTGGAGCGCGTCCTCGCAG | GGACTGCCAAAAAGAGC    c.1680
 H  T  L  N  F  E  Y  A  V  E  R  V  L  A  G |   T  A  K  K  S      p.560

          .         .         .         .         .         .       g.47174
 AAGATCCTGTCCAAGGAAGAACAGAAAGTGGTTGCGTTTCATGAGTCGGGCCACGCCTTG       c.1740
 K  I  L  S  K  E  E  Q  K  V  V  A  F  H  E  S  G  H  A  L         p.580

          .         .         .          | 14        .         .    g.49603
 GTGGGCTGGATGCTGGAGCACACGGAGGCCGTGATGAAG | GTCTCCATAACCCCTCGGACA    c.1800
 V  G  W  M  L  E  H  T  E  A  V  M  K   | V  S  I  T  P  R  T      p.600

          .         .         .         .         .         .       g.49663
 AACGCCGCCCTGGGCTTTGCTCAGATGCTCCCCAGAGACCAGCACCTCTTCACCAAGGAG       c.1860
 N  A  A  L  G  F  A  Q  M  L  P  R  D  Q  H  L  F  T  K  E         p.620

          .         .         .         .         .         .       g.49723
 CAGCTGTTTGAGCGGATGTGCATGGCCCTGGGAGGACGGGCCTCGGAAGCACTGTCCTTC       c.1920
 Q  L  F  E  R  M  C  M  A  L  G  G  R  A  S  E  A  L  S  F         p.640

          .       | 15 .         .         .         .         .    g.50441
 AACGAGGTCACTTCTG | GGGCACAGGACGACCTGAGGAAGGTCACCCGCATCGCCTACTCC    c.1980
 N  E  V  T  S  G |   A  Q  D  D  L  R  K  V  T  R  I  A  Y  S      p.660

          .         .         .         .         .         .       g.50501
 ATGGTGAAGCAGTTTGGGATGGCACCTGGCATCGGGCCCATCTCCTTCCCTGAGGCGCAG       c.2040
 M  V  K  Q  F  G  M  A  P  G  I  G  P  I  S  F  P  E  A  Q         p.680

          .         .         .         .         .         .       g.50561
 GAGGGCCTCATGGGCATCGGGCGGCGCCCCTTCAGCCAAGGCCTGCAGCAGATGATGGAC       c.2100
 E  G  L  M  G  I  G  R  R  P  F  S  Q  G  L  Q  Q  M  M  D         p.700

     | 16    .         .         .         .         .         .    g.51146
 CAT | GAAGCAAGACTGCTGGTGGCCAAGGCCTACAGACACACCGAGAAGGTGCTGCAGGAC    c.2160
 H   | E  A  R  L  L  V  A  K  A  Y  R  H  T  E  K  V  L  Q  D      p.720

          .         .  | 17      .         .         .         .    g.53529
 AACCTGGACAAGTTGCAGGCG | CTGGCAAACGCCCTTCTGGAAAAGGAAGTGATAAACTAT    c.2220
 N  L  D  K  L  Q  A   | L  A  N  A  L  L  E  K  E  V  I  N  Y      p.740

          .         .         .         .         .         .       g.53589
 GAGGACATTGAGGCTCTCATTGGCCCGCCGCCCCATGGGCCGAAGAAAATGATCGCACCG       c.2280
 E  D  I  E  A  L  I  G  P  P  P  H  G  P  K  K  M  I  A  P         p.760

          .         .         .         .         .         .       g.53649
 CAGAGGTGGATCGACGCCCAGAGGGAGAAACAGGACTTGGGCGAGGAGGAGACCGAAGAG       c.2340
 Q  R  W  I  D  A  Q  R  E  K  Q  D  L  G  E  E  E  T  E  E         p.780

          .         .         .         .                           g.53697
 ACCCAGCAGCCTCCACTTGGAGGCGAAGAGCCGACTTGGCCCAAGTAG                   c.2388
 T  Q  Q  P  P  L  G  G  E  E  P  T  W  P  K  X                     p.795

          .         .         .         .         .         .       g.53757
 ttgggaggtgttggctgcacgtgcgggtggtccgggaagtgagggctcactcagccaccc       c.*60

          .         .         .         .         .         .       g.53817
 tgagttgcttttcagctgaggtttgcacttcctctcgcggccctcagtagtccctgcaca       c.*120

          .         .         .         .         .         .       g.53877
 gtgacttctgagatctgttgattgatgacccttttcatgattttaagtttctctgcagaa       c.*180

          .         .         .         .         .         .       g.53937
 actactgacggagtcctgtgtttgtgagtcgtttcccctatggggaaggttatcagtgct       c.*240

          .         .         .         .         .         .       g.53997
 tcccgagtgagcatggaacacttcgagttcccagggttatagacagtcgttcccagtgtg       c.*300

          .         .         .         .         .         .       g.54057
 gctgaggccacccagaggcagcagagcattcagactccaaacagacccctgttcatgccg       c.*360

          .         .         .         .         .         .       g.54117
 acgcttgcacgaccgccccagttcctgtggctccctcggaatgctaaggggatcggacat       c.*420

          .         .         .         .         .         .       g.54177
 gaaaggaccctgtgagccgattgtcctatctccagcggccctgtcatccagctcactcat       c.*480

          .         .         .         .         .         .       g.54237
 caatggggccagtcaggcccaggcactgggctccggaggactcaccactgccccctgctg       c.*540

          .         .         .         .         .         .       g.54297
 ccatgtggactggtgcaagttgaggacttcttgctggtctagtcacgcatgcagtgttgg       c.*600

          .         .         .         .         .         .       g.54357
 ggatgccttggtttttactgctctgagaattgttgagatactttactaataaactgtgta       c.*660

          .                                                         g.54370
 gttggaaaatcta                                                      c.*673

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Spastic paraplegia 7 (pure and complicated autosomal recessive) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

Powered by LOVD v.3.0 Build 15
©2004-2016 Leiden University Medical Center