transmembrane protease, serine 6 (TMPRSS6) - coding DNA reference sequence

(used for variant description)

(last modified November 26, 2020)


This file was created to facilitate the description of sequence variants on transcript NM_153609.2 in the TMPRSS6 gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NG_012856.2, covering TMPRSS6 transcript NM_153609.2.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
           .         .         .         .         .                g.5054
       cttgagccagacccagtccagctctggtgcctgccctctggtgcgagctgacct       c.-61

 .         .         .         .         .         .                g.5114
 gagatgcacttccctcctctgtgagctgtctcggcacccacttgcagtcactgccgcctg       c.-1

          .         .       | 02 .         .         .         .    g.5269
 ATGTTGTTACTCTTCCACTCCAAAAG | GATGCCCGTGGCCGAGGCCCCCCAGGTGGCTGGC    c.60
 M  L  L  L  F  H  S  K  R  |  M  P  V  A  E  A  P  Q  V  A  G      p.20

          .         .         .         .         .         .       g.5329
 GGGCAGGGGGACGGAGGTGATGGCGAGGAAGCGGAGCCGGAGGGGATGTTCAAGGCCTGT       c.120
 G  Q  G  D  G  G  D  G  E  E  A  E  P  E  G  M  F  K  A  C         p.40

          .         .         .         .         .         .       g.5389
 GAGGACTCCAAGAGAAAAGCCCGGGGCTACCTCCGCCTGGTGCCCCTGTTTGTGCTGCTG       c.180
 E  D  S  K  R  K  A  R  G  Y  L  R  L  V  P  L  F  V  L  L         p.60

          .         .         .         .          | 03        .    g.10115
 GCCCTGCTCGTGCTGGCTTCGGCGGGGGTGCTACTCTGGTATTTCCTAG | GGTACAAGGCG    c.240
 A  L  L  V  L  A  S  A  G  V  L  L  W  Y  F  L  G |   Y  K  A      p.80

          .         .         .         .         .         .       g.10175
 GAGGTGATGGTCAGCCAGGTGTACTCAGGCAGTCTGCGTGTACTCAATCGCCACTTCTCC       c.300
 E  V  M  V  S  Q  V  Y  S  G  S  L  R  V  L  N  R  H  F  S         p.100

          .         .         .         .         .         .       g.10235
 CAGGATCTTACCCGCCGGGAATCTAGTGCCTTCCGCAGTGAAACCGCCAAAGCCCAGAAG       c.360
 Q  D  L  T  R  R  E  S  S  A  F  R  S  E  T  A  K  A  Q  K         p.120

     | 04    .         .         .         .         .         .    g.11995
 ATG | CTCAAGGAGCTCATCACCAGCACCCGCCTGGGAACTTACTACAACTCCAGCTCCGTC    c.420
 M   | L  K  E  L  I  T  S  T  R  L  G  T  Y  Y  N  S  S  S  V      p.140

          .  | 05      .         .         .         .         .    g.12612
 TATTCCTTTGG | GGAGGGACCCCTCACCTGCTTCTTCTGGTTCATTCTCCAAATCCCCGAG    c.480
 Y  S  F  G  |  E  G  P  L  T  C  F  F  W  F  I  L  Q  I  P  E      p.160

          .         .         .         .         .         .       g.12672
 CACCGCCGGCTGATGCTGAGCCCCGAGGTGGTGCAGGCACTGCTGGTGGAGGAGCTGCTG       c.540
 H  R  R  L  M  L  S  P  E  V  V  Q  A  L  L  V  E  E  L  L         p.180

          .         .         .         .         .         .       g.12732
 TCCACAGTCAACAGCTCGGCTGCCGTCCCCTACAGGGCCGAGTACGAAGTGGACCCCGAG       c.600
 S  T  V  N  S  S  A  A  V  P  Y  R  A  E  Y  E  V  D  P  E         p.200

          .       | 06 .         .         .         .         | 07 g.18873
 GGCCTAGTGATCCTGG | AAGCCAGTGTGAAAGACATAGCTGCATTGAATTCCACGCTGG | GT c.660
 G  L  V  I  L  E |   A  S  V  K  D  I  A  A  L  N  S  T  L  G |    p.220

          .         .         .         .         .         .       g.18933
 TGTTACCGCTACAGCTACGTGGGCCAGGGCCAGGTCCTCCGGCTGAAGGGGCCTGACCAC       c.720
 C  Y  R  Y  S  Y  V  G  Q  G  Q  V  L  R  L  K  G  P  D  H         p.240

          .         .         .         .         .         .       g.18993
 CTGGCCTCCAGCTGCCTGTGGCACCTGCAGGGCCCCAAGGACCTCATGCTCAAACTCCGG       c.780
 L  A  S  S  C  L  W  H  L  Q  G  P  K  D  L  M  L  K  L  R         p.260

          .         .         .         .         .         .       g.19053
 CTGGAGTGGACGCTGGCAGAGTGCCGGGACCGACTGGCCATGTATGACGTGGCCGGGCCC       c.840
 L  E  W  T  L  A  E  C  R  D  R  L  A  M  Y  D  V  A  G  P         p.280

          .         .    | 08    .         .         .         .    g.22271
 CTGGAGAAGAGGCTCATCACCTC | GGTGTACGGCTGCAGCCGCCAGGAGCCCGTGGTGGAG    c.900
 L  E  K  R  L  I  T  S  |  V  Y  G  C  S  R  Q  E  P  V  V  E      p.300

          .         .         .         .         .         .       g.22331
 GTTCTGGCGTCGGGGGCCATCATGGCGGTCGTCTGGAAGAAGGGCCTGCACAGCTACTAC       c.960
 V  L  A  S  G  A  I  M  A  V  V  W  K  K  G  L  H  S  Y  Y         p.320

          .         .         .         . | 09       .         .    g.23834
 GACCCCTTCGTGCTCTCCGTGCAGCCGGTGGTCTTCCAGG | CCTGTGAAGTGAACCTGACG    c.1020
 D  P  F  V  L  S  V  Q  P  V  V  F  Q  A |   C  E  V  N  L  T      p.340

          .         .         .         .         .         .       g.23894
 CTGGACAACAGGCTCGACTCCCAGGGCGTCCTCAGCACCCCGTACTTCCCCAGCTACTAC       c.1080
 L  D  N  R  L  D  S  Q  G  V  L  S  T  P  Y  F  P  S  Y  Y         p.360

          .         .         .    | 10    .         .         .    g.24276
 TCGCCCCAAACCCACTGCTCCTGGCACCTCACG | GTGCCCTCTCTGGACTACGGCTTGGCC    c.1140
 S  P  Q  T  H  C  S  W  H  L  T   | V  P  S  L  D  Y  G  L  A      p.380

          .         .         .         .         .         .       g.24336
 CTCTGGTTTGATGCCTATGCACTGAGGAGGCAGAAGTATGATTTGCCGTGCACCCAGGGC       c.1200
 L  W  F  D  A  Y  A  L  R  R  Q  K  Y  D  L  P  C  T  Q  G         p.400

          .         .    | 11    .         .         .         .    g.33410
 CAGTGGACGATCCAGAACAGGAG | GCTGTGTGGCTTGCGCATCCTGCAGCCCTACGCCGAG    c.1260
 Q  W  T  I  Q  N  R  R  |  L  C  G  L  R  I  L  Q  P  Y  A  E      p.420

          .         .         .         .         .         .       g.33470
 AGGATCCCCGTGGTGGCCACGGCCGGGATCACCATCAACTTCACCTCCCAGATCTCCCTC       c.1320
 R  I  P  V  V  A  T  A  G  I  T  I  N  F  T  S  Q  I  S  L         p.440

          .         .         .         .          | 12        .    g.33956
 ACCGGGCCCGGTGTGCGGGTGCACTATGGCTTGTACAACCAGTCGGACC | CCTGCCCTGGA    c.1380
 T  G  P  G  V  R  V  H  Y  G  L  Y  N  Q  S  D  P |   C  P  G      p.460

          .         .         .         .         .         .       g.34016
 GAGTTCCTCTGTTCTGTGAATGGACTCTGTGTCCCTGCCTGTGATGGGGTCAAGGACTGC       c.1440
 E  F  L  C  S  V  N  G  L  C  V  P  A  C  D  G  V  K  D  C         p.480

          .         .         | 13         .         .         .    g.35040
 CCCAACGGCCTGGATGAGAGAAACTGCG | TTTGCAGAGCCACATTCCAGTGCAAAGAGGAC    c.1500
 P  N  G  L  D  E  R  N  C  V |   C  R  A  T  F  Q  C  K  E  D      p.500

          .         .         .         .         .         .       g.35100
 AGCACATGCATCTCACTGCCCAAGGTCTGTGATGGGCAGCCTGATTGTCTCAACGGCAGC       c.1560
 S  T  C  I  S  L  P  K  V  C  D  G  Q  P  D  C  L  N  G  S         p.520

          .         .   | 14     .         .         .         .    g.37659
 GACGAAGAGCAGTGCCAGGAAG | GGGTGCCATGTGGGACATTCACCTTCCAGTGTGAGGAC    c.1620
 D  E  E  Q  C  Q  E  G |   V  P  C  G  T  F  T  F  Q  C  E  D      p.540

          .         .         .         .         .         .       g.37719
 CGGAGCTGCGTGAAGAAGCCCAACCCGCAGTGTGATGGGCGGCCCGACTGCAGGGACGGC       c.1680
 R  S  C  V  K  K  P  N  P  Q  C  D  G  R  P  D  C  R  D  G         p.560

          .          | 15        .         .         .         .    g.38042
 TCGGATGAGGAGCACTGTG | ACTGTGGCCTCCAGGGCCCCTCCAGCCGCATTGTTGGTGGA    c.1740
 S  D  E  E  H  C  D |   C  G  L  Q  G  P  S  S  R  I  V  G  G      p.580

          .         .         .         .         .         .       g.38102
 GCTGTGTCCTCCGAGGGTGAGTGGCCATGGCAGGCCAGCCTCCAGGTTCGGGGTCGACAC       c.1800
 A  V  S  S  E  G  E  W  P  W  Q  A  S  L  Q  V  R  G  R  H         p.600

          .         .         .         .         .         .       g.38162
 ATCTGTGGGGGGGCCCTCATCGCTGACCGCTGGGTGATAACAGCTGCCCACTGCTTCCAG       c.1860
 I  C  G  G  A  L  I  A  D  R  W  V  I  T  A  A  H  C  F  Q         p.620

          | 16         .         .         .         .         .    g.39361
 GAGGACAG | CATGGCCTCCACGGTGCTGTGGACCGTGTTCCTGGGCAAGGTGTGGCAGAAC    c.1920
 E  D  S  |  M  A  S  T  V  L  W  T  V  F  L  G  K  V  W  Q  N      p.640

          .         .         .         .         .         .       g.39421
 TCGCGCTGGCCTGGAGAGGTGTCCTTCAAGGTGAGCCGCCTGCTCCTGCACCCGTACCAC       c.1980
 S  R  W  P  G  E  V  S  F  K  V  S  R  L  L  L  H  P  Y  H         p.660

          .         .         .         .         .         .       g.39481
 GAAGAGGACAGCCATGACTACGACGTGGCGCTGCTGCAGCTCGACCACCCGGTGGTGCGC       c.2040
 E  E  D  S  H  D  Y  D  V  A  L  L  Q  L  D  H  P  V  V  R         p.680

          .         .         .         .         .         .       g.39541
 TCGGCCGCCGTGCGCCCCGTCTGCCTGCCCGCGCGCTCCCACTTCTTCGAGCCCGGCCTG       c.2100
 S  A  A  V  R  P  V  C  L  P  A  R  S  H  F  F  E  P  G  L         p.700

          .         .         .         . | 17       .         .    g.41711
 CACTGCTGGATTACGGGCTGGGGCGCCTTGCGCGAGGGCG | GCCCCATCAGCAACGCTCTG    c.2160
 H  C  W  I  T  G  W  G  A  L  R  E  G  G |   P  I  S  N  A  L      p.720

          .         .         .         .         .         .       g.41771
 CAGAAAGTGGATGTGCAGTTGATCCCACAGGACCTGTGCAGCGAGGTCTATCGCTACCAG       c.2220
 Q  K  V  D  V  Q  L  I  P  Q  D  L  C  S  E  V  Y  R  Y  Q         p.740

          .         .         .         .         .        | 18.    g.42418
 GTGACGCCACGCATGCTGTGTGCCGGCTACCGCAAGGGCAAGAAGGATGCCTGTCAG | GGT    c.2280
 V  T  P  R  M  L  C  A  G  Y  R  K  G  K  K  D  A  C  Q   | G      p.760

          .         .         .         .         .         .       g.42478
 GACTCAGGTGGTCCGCTGGTGTGCAAGGCACTCAGTGGCCGCTGGTTCCTGGCGGGGCTG       c.2340
 D  S  G  G  P  L  V  C  K  A  L  S  G  R  W  F  L  A  G  L         p.780

          .         .         .         .         .         .       g.42538
 GTCAGCTGGGGCCTGGGCTGTGGCCGGCCTAACTACTTCGGCGTCTACACCCGCATCACA       c.2400
 V  S  W  G  L  G  C  G  R  P  N  Y  F  G  V  Y  T  R  I  T         p.800

          .         .         .                                     g.42574
 GGTGTGATCAGCTGGATCCAGCAAGTGGTGACCTGA                               c.2436
 G  V  I  S  W  I  Q  Q  V  V  T  X                                 p.811

          .         .         .         .         .         .       g.42634
 ggaactgcccccctgcaaagcagggcccacctcctggactcagagagcccagggcaactg       c.*60

          .         .         .         .         .         .       g.42694
 ccaagcagggggacaagtattctggcggggggtgggggagagagcaggccctgtggtggc       c.*120

          .         .         .         .         .         .       g.42754
 aggaggtggcatcttgtctcgtccctgatgtctgctccagtgatggcaggaggatggaga       c.*180

          .         .         .         .         .         .       g.42814
 agtgccagcagctgggggtcaagacgtcccctgaggacccaggcccacacccagcccttc       c.*240

          .         .         .         .         .         .       g.42874
 tgcctcccaattctctctcctccgtccccttcctccactgctgcctaatgcaaggcagtg       c.*300

          .         .         .         .         .         .       g.42934
 gctcagcagcaagaatgctggttctacatcccgaggagtgtctgaggtgcgccccactct       c.*360

          .         .         .         .         .         .       g.42994
 gtacagaggctgtttgggcagccttgcctccagagagcagattccagcttcggaagcccc       c.*420

          .         .         .         .         .         .       g.43054
 tggtctaacttgggatctgggaatggaaggtgctcccatcggaggggaccctcagagccc       c.*480

          .         .         .         .         .         .       g.43114
 tggagactgccaggtgggcctgctgccactgtaagccaaaaggtggggaagtcctgactc       c.*540

          .         .         .         .         .         .       g.43174
 cagggtccttgccccacccctgcctgccacctgggccctcacagcccagaccctcactgg       c.*600

          .         .         .         .                           g.43215
 gaggtgagctcagctgccctttggaataaagctgcctgatc                          c.*641

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Transmembrane protease, serine 6 protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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