Usher syndrome 1C (autosomal recessive, severe) (USH1C) - coding DNA reference sequence

(used for variant description)

(last modified April 26, 2021)


This file was created to facilitate the description of sequence variants on transcript NM_153676.3 in the USH1C gene based on a coding DNA reference sequence following the HGVS recommendations.

The sequence was taken from NC_000011.9, covering USH1C transcript NM_153676.3.


Please note that introns are available by clicking on the exon numbers above the sequence.
 (upstream sequence)
                     .         .         .         .                g.5049
            agctccgagggcggctggcccggtcgcggtcgcggctctttccagctcc       c.-61

 .         .         .         .         .         .                g.5109
 tggcagccgggcacccgaaggaacgggtcgtgcaacgacgcagctggacctggcccagcc       c.-1

          .         .         .       | 02 .         .         .    g.16118
 ATGGACCGAAAAGTGGCCCGAGAATTCCGGCATAAG | GTGGATTTTCTGATTGAAAATGAT    c.60
 M  D  R  K  V  A  R  E  F  R  H  K   | V  D  F  L  I  E  N  D      p.20

          .         .         .         .     | 03   .         .    g.17890
 GCAGAGAAGGACTATCTCTATGATGTGCTGCGAATGTACCACCA | GACCATGGACGTGGCC    c.120
 A  E  K  D  Y  L  Y  D  V  L  R  M  Y  H  Q  |  T  M  D  V  A      p.40

          .         .         .         .         .         .       g.17950
 GTGCTCGTGGGAGACCTGAAGCTGGTCATCAATGAACCCAGCCGTCTGCCTCTGTTTGAT       c.180
 V  L  V  G  D  L  K  L  V  I  N  E  P  S  R  L  P  L  F  D         p.60

          .         .         .         .         .         .       g.18010
 GCCATTCGGCCGCTGATCCCACTGAAGCACCAGGTGGAATATGATCAGCTGACCCCCCGG       c.240
 A  I  R  P  L  I  P  L  K  H  Q  V  E  Y  D  Q  L  T  P  R         p.80

          | 04         .         .         .         .         .    g.18176
 CGCTCCAG | GAAGCTGAAGGAGGTGCGTCTGGACCGTCTGCACCCCGAAGGCCTCGGCCTG    c.300
 R  S  R  |  K  L  K  E  V  R  L  D  R  L  H  P  E  G  L  G  L      p.100

          .         .         .         .         .         .       g.18236
 AGTGTGCGTGGTGGCCTGGAGTTTGGCTGTGGGCTCTTCATCTCCCACCTCATCAAAGGC       c.360
 S  V  R  G  G  L  E  F  G  C  G  L  F  I  S  H  L  I  K  G         p.120

          .         .        | 05.         .         .         .    g.22118
 GGTCAGGCAGACAGCGTCGGGCTCCAG | GTAGGGGACGAGATCGTCCGGATCAATGGATAT    c.420
 G  Q  A  D  S  V  G  L  Q   | V  G  D  E  I  V  R  I  N  G  Y      p.140

          .         .         .         .         .         .       g.22178
 TCCATCTCCTCCTGTACCCATGAGGAGGTCATCAACCTCATTCGAACCAAGAAAACTGTG       c.480
 S  I  S  S  C  T  H  E  E  V  I  N  L  I  R  T  K  K  T  V         p.160

          .       | 06 .         .         .  | 07      .         . g.22625
 TCCATCAAAGTGAGAC | ACATCGGCCTGATCCCCGTGAAAAG | CTCTCCTGATGAGCCCCTC c.540
 S  I  K  V  R  H |   I  G  L  I  P  V  K  S  |  S  P  D  E  P  L   p.180

          .         .         .          | 08        .         .    g.22996
 ACTTGGCAGTATGTGGATCAGTTTGTGTCGGAATCTGGG | GGCGTGCGAGGCAGCCTGGGC    c.600
 T  W  Q  Y  V  D  Q  F  V  S  E  S  G   | G  V  R  G  S  L  G      p.200

          .         .         .         .         .         .       g.23056
 TCCCCTGGAAATCGGGAAAACAAGGAGAAGAAGGTCTTCATCAGCCTGGTAGGCTCCCGA       c.660
 S  P  G  N  R  E  N  K  E  K  K  V  F  I  S  L  V  G  S  R         p.220

          .     | 09   .         .         .         .         .    g.24927
 GGCCTTGGCTGCAG | CATTTCCAGCGGCCCCATCCAGAAGCCTGGCATCTTTATCAGCCAT    c.720
 G  L  G  C  S  |  I  S  S  G  P  I  Q  K  P  G  I  F  I  S  H      p.240

          .         .         .          | 10        .         .    g.25959
 GTGAAACCTGGCTCCCTGTCTGCTGAGGTGGGATTGGAG | ATAGGGGACCAGATTGTCGAA    c.780
 V  K  P  G  S  L  S  A  E  V  G  L  E   | I  G  D  Q  I  V  E      p.260

          .         .         .          | 11        .         .    g.26170
 GTCAATGGCGTCGACTTCTCTAACCTGGATCACAAGGAG | GCTGTAAATGTGCTGAAGAGT    c.840
 V  N  G  V  D  F  S  N  L  D  H  K  E   | A  V  N  V  L  K  S      p.280

          .         .         .       | 12 .         .         .    g.26514
 AGCCGCAGCCTGACCATCTCCATTGTAGCTGCAGCT | GGCCGGGAGCTGTTCATGACAGAC    c.900
 S  R  S  L  T  I  S  I  V  A  A  A   | G  R  E  L  F  M  T  D      p.300

          .         .         .         .         .         .       g.26574
 CGGGAGCGGCTGGCAGAGGCGCGGCAGCGTGAGCTGCAGCGGCAGGAGCTTCTCATGCAG       c.960
 R  E  R  L  A  E  A  R  Q  R  E  L  Q  R  Q  E  L  L  M  Q         p.320

          .         .         .         .         .          | 13    g.28006
 AAGCGGCTGGCGATGGAGTCCAACAAGATCCTCCAGGAGCAGCAGGAGATGGAGCGGCA | A    c.1020
 K  R  L  A  M  E  S  N  K  I  L  Q  E  Q  Q  E  M  E  R  Q  |      p.340

          .         .         .         .         .         .       g.28066
 AGGAGAAAAGAAATTGCCCAGAAGGCAGCAGAGGAAAATGAGAGATACCGGAAGGAGATG       c.1080
 R  R  K  E  I  A  Q  K  A  A  E  E  N  E  R  Y  R  K  E  M         p.360

       | 14  .         .         .         .         .         .    g.28477
 GAACA | GATTGTAGAGGAGGAAGAGAAGTTTAAGAAGCAATGGGAAGAAGACTGGGGCTCA    c.1140
 E  Q  |  I  V  E  E  E  E  K  F  K  K  Q  W  E  E  D  W  G  S      p.380

          .         .         .         .         .         .       g.28537
 AAGGAACAGCTACTCTTGCCTAAAACCATCACTGCTGAGGTACACCCAGTACCCCTTCGC       c.1200
 K  E  Q  L  L  L  P  K  T  I  T  A  E  V  H  P  V  P  L  R         p.400

          . | 15       .         .         .         .         .    g.33176
 AAGCCAAAGT | CTTTTGGATGGTTTTATCGTTACGATGGCAAATTCCCAACCATCCGGAAG    c.1260
 K  P  K  S |   F  G  W  F  Y  R  Y  D  G  K  F  P  T  I  R  K      p.420

  | 16       .         .         .         .         .         .    g.37422
  | AAAGGAAAAGATAAGAAGAAAGCCAAGTATGGCAGCCTGCAGGACTTGAGAAAGAATAAG    c.1320
  | K  G  K  D  K  K  K  A  K  Y  G  S  L  Q  D  L  R  K  N  K      p.440

          .         .         .         .         .         .       g.37482
 AAAGAACTGGAGTTTGAGCAAAAGCTTTACAAAGAGAAAGAGGAAATGCTGGAGAAGGAA       c.1380
 K  E  L  E  F  E  Q  K  L  Y  K  E  K  E  E  M  L  E  K  E         p.460

          .         .         .    | 17    .         .         .    g.38922
 AAGCAGCTAAAGATCAACCGGCTGGCCCAGGAG | GTGTCTGAGACAGAGCGGGAAGACCTT    c.1440
 K  Q  L  K  I  N  R  L  A  Q  E   | V  S  E  T  E  R  E  D  L      p.480

          .         .         .         .         .         .       g.38982
 GAAGAATCGGAAAAGATTCAATATTGGGTGGAGAGGCTCTGTCAAACGCGCCTCGAGCAG       c.1500
 E  E  S  E  K  I  Q  Y  W  V  E  R  L  C  Q  T  R  L  E  Q         p.500

          .         .         . | 18       .         .         .    g.39608
 ATTTCCTCTGCTGATAATGAGATTTCAGAG | ATGACCACAGGGCCCCCGCCTCCCCCGCCT    c.1560
 I  S  S  A  D  N  E  I  S  E   | M  T  T  G  P  P  P  P  P  P      p.520

          .         .         .         .         .         .       g.39668
 TCTGTGTCTCCCCTGGCCCCACCCTTGAGACGCTTCGCAGGCGGACTGCACCTGCACACC       c.1620
 S  V  S  P  L  A  P  P  L  R  R  F  A  G  G  L  H  L  H  T         p.540

          .         .         .         .         .         .       g.39728
 ACTGACCTGGACGACATCCCTTTGGACATGTTCTACTATCCCCCCAAGACTCCCTCTGCC       c.1680
 T  D  L  D  D  I  P  L  D  M  F  Y  Y  P  P  K  T  P  S  A         p.560

          .         .         .         .         .         .       g.39788
 TTGCCTGTGATGCCCCACCCTCCACCCTCCAACCCACCCCACAAGGTCCCGGCGCCCCCT       c.1740
 L  P  V  M  P  H  P  P  P  S  N  P  P  H  K  V  P  A  P  P         p.580

          .         .         .         .         .         .       g.39848
 GTCCTTCCCTTATCTGGCCATGTGAGCGCCTCATCCTCTCCATGGGTGCAGCGCACTCCA       c.1800
 V  L  P  L  S  G  H  V  S  A  S  S  S  P  W  V  Q  R  T  P         p.600

          .         .         .         .         .         .       g.39908
 CCCCCCATTCCCATCCCTCCCCCGCCATCCGTTCCCACCCAAGACCTCACTCCCACCCGC       c.1860
 P  P  I  P  I  P  P  P  P  S  V  P  T  Q  D  L  T  P  T  R         p.620

          .         .         .         .         .         .       g.39968
 CCACTGCCCTCGGCGCTGGAAGAAGCACTGAGCAACCATCCCTTCCGCACTGGGGACACA       c.1920
 P  L  P  S  A  L  E  E  A  L  S  N  H  P  F  R  T  G  D  T         p.640

          .         .         .         .         .         .       g.40028
 GGCAATCCAGTGGAGGACTGGGAGGCAAAGAACCACAGTGGGAAGCCCACTAACTCCCCT       c.1980
 G  N  P  V  E  D  W  E  A  K  N  H  S  G  K  P  T  N  S  P         p.660

          .         .         .    | 19    .         .         .    g.43494
 GTCCCTGAACAGAGCTTCCCACCCACCCCAAAG | ACATTTTGCCCAAGCCCACAGCCTCCA    c.2040
 V  P  E  Q  S  F  P  P  T  P  K   | T  F  C  P  S  P  Q  P  P      p.680

          .         .         .         .         .         .       g.43554
 CGAGGCCCTGGCGTGTCCACCATCTCCAAACCTGTCATGGTCCACCAGGAGCCCAATTTC       c.2100
 R  G  P  G  V  S  T  I  S  K  P  V  M  V  H  Q  E  P  N  F         p.700

          .         .         .    | 20    .         .         .    g.44746
 ATCTACAGGCCAGCTGTGAAATCTGAAGTTCTG | CCACAGGAGATGTTGAAGAGGATGGTG    c.2160
 I  Y  R  P  A  V  K  S  E  V  L   | P  Q  E  M  L  K  R  M  V      p.720

          .         .     | 21   .         .         .         .    g.47472
 GTTTATCAGACAGCATTCAGACAA | GATTTCCGGAAATATGAGGAAGGCTTTGACCCCTAC    c.2220
 V  Y  Q  T  A  F  R  Q   | D  F  R  K  Y  E  E  G  F  D  P  Y      p.740

        | 22 .         .         .         .         .         .    g.47935
 TCTATG | TTCACCCCAGAGCAGATCATGGGGAAGGATGTCCGGCTCCTACGCATCAAGAAG    c.2280
 S  M   | F  T  P  E  Q  I  M  G  K  D  V  R  L  L  R  I  K  K      p.760

  | 23       .         .         .         .         .         .    g.48326
  | GAGGGATCCTTAGACCTGGCCCTGGAAGGCGGTGTGGACTCCCCCATTGGGAAGGTGGTC    c.2340
  | E  G  S  L  D  L  A  L  E  G  G  V  D  S  P  I  G  K  V  V      p.780

          .         .         .         . | 24       .         .    g.51165
 GTTTCTGCTGTGTATGAGCGGGGAGCTGCTGAGCGGCATG | GTGGCATTGTGAAAGGGGAC    c.2400
 V  S  A  V  Y  E  R  G  A  A  E  R  H  G |   G  I  V  K  G  D      p.800

          .         .         .         .         .         .       g.51225
 GAGATCATGGCAATCAACGGCAAGATTGTGACAGACTACACCCTGGCTGAGGCTGAGGCT       c.2460
 E  I  M  A  I  N  G  K  I  V  T  D  Y  T  L  A  E  A  E  A         p.820

          .         .         . | 25       .         .         .    g.52633
 GCCCTGCAGAAGGCCTGGAATCAGGGCGGG | GACTGGATCGACCTTGTGGTTGCCGTCTGC    c.2520
 A  L  Q  K  A  W  N  Q  G  G   | D  W  I  D  L  V  V  A  V  C      p.840

          .         .       | 26 .         .         .         .    g.53773
 CCCCCAAAGGAGTATGACGATGAGCT | AGCTTCTCTTCCCTCCTCCGTAGCTGAAAGCCCC    c.2580
 P  P  K  E  Y  D  D  E  L  |  A  S  L  P  S  S  V  A  E  S  P      p.860

          .         .         .         .         .         .       g.53833
 CAACCGGTCCGAAAGCTCCTTGAAGACCGTGCTGCCGTGCACAGACACGGGTTCCTCCTG       c.2640
 Q  P  V  R  K  L  L  E  D  R  A  A  V  H  R  H  G  F  L  L         p.880

          .      | 27  .         .         .         .         .    g.55085
 CAGCTGGAGCCCACG | GACCTTCTTCTGAAGTCCAAAAGGGGAAACCAAATTCACCGTTAG    c.2700
 Q  L  E  P  T   | D  L  L  L  K  S  K  R  G  N  Q  I  H  R  X      p.899

          .         .         .         .         .         .       g.55145
 gaaacagtgagctccggccccacctcgtgaacacaaagcctcggatcagccttgagagag       c.*60

          .         .         .         .         .         .       g.55205
 gccacactacacacaccagatggcatccttgggacctgaatctatcacccaggaatctca       c.*120

          .         .         .         .         .         .       g.55265
 aactccctttggccctgaaccagggccagataaggaacagctcgggccactcttctgaag       c.*180

          .         .         .         .         .         .       g.55325
 gccaacgtggaggaaagggagcagccagccatttgggagaagatctcaaggatccagact       c.*240

          .         .         .         .         .         .       g.55385
 ctcattcctttcctctggcccagtgaatttggtctctcccagctctgggggactccttcc       c.*300

          .         .         .         .         .         .       g.55445
 ttgaaccctaataagaccccactggagtctctctctctccatccctctcctctgccctct       c.*360

          .         .         .         .         .         .       g.55505
 gctctaattgctgccaggattgtcactccaaaccttactctgagctcattaataaaatag       c.*420

          .                                                         g.55522
 atttattttccagctta                                                  c.*437

 (downstream sequence)
Legend:
Nucleotide numbering (following the rules of the HGVS for a 'Coding DNA Reference Sequence') is indicated at the right of the sequence, counting the A of the ATG translation initiating Methionine as 1. Every 10th nucleotide is indicated by a "." above the sequence. The Usher syndrome 1C (autosomal recessive, severe) protein sequence is shown below the coding DNA sequence, with numbering indicated at the right starting with 1 for the translation initiating Methionine. Every 10th amino acid is shown in bold. The position of introns is indicated by a vertical line, splitting the two exons. The start of the first exon (transcription initiation site) is indicated by a '\', the end of the last exon (poly-A addition site) by a '/'. The exon number is indicated above the first nucleotide(s) of the exon. To aid the description of frame shift variants, all stop codons in the +1 frame are shown in bold while all stop codons in the +2 frame are underlined.

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