Variant #0000001545 (NC_000004.11:g.178354367C>A, NC_000004.11(NM_000027.3):c.940+1G>T (AGA))
| Chromosome |
4 |
| Allele |
Both (homozygous) |
| Affects function (as reported) |
Affects function |
| Affects function (by curator) |
Affects function |
| Classification method |
- |
| Clinical classification |
pathogenic |
| DNA change (genomic) (Relative to hg19 / GRCh37) |
g.178354367C>A |
| DNA change (hg38) |
g.177433213C>A |
| Published as |
GT-to-TT transversion at the splice donor site of intron 8 |
| ISCN |
- |
| DB-ID |
AGA_000027 |
| Variant remarks |
1 African-American AGU patient (hom); Mutation almost completely eliminate splicing at the exon 8/intron 8 border and causes exon 8 skipping. |
| Reference |
PubMed: Fisher et al. 1991 |
| ClinVar ID |
- |
| dbSNP ID |
- |
| Origin |
SUMMARY record |
| Segregation |
yes |
| Frequency |
- |
| Re-site |
- |
| VIP |
- |
| Methylation |
- |
| Average frequency (gnomAD v.2.1.1) |
1.0E-5 View details |
| Owner |
Anne Polvi |
| Database submission license |
Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International |
| Created by |
Anne Polvi |
| Date created |
2012-08-30 15:15:23 +02:00 (CEST) |
| Date last edited |
2019-02-27 20:53:40 +01:00 (CET) |

Variant on transcripts
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