Legend
Please note that a short description of a certain column can be displayed when you move your mouse cursor over the column's header and hold it still. Below, a more detailed description is shown per column.
Effect: The variant's effect on the function of the gene/protein, displayed in the format 'R/C'. R is the value reported by the source (publication, submitter) and this classification may vary between records. C is the value concluded by the curator. Note that in some database the curator uses Summary records to give details on the classification of the variant.Values used: '+' indicating the variant affects function, '+?' probably affects function, '-' does not affect function, '-?' probably does not affect function, '?' effect unknown, '.' effect was not classified.
Reported: The number of times this variant has been reported in the database.
Exon: number of exon/intron containing variant; 2 = exon 2, 12i = intron 12, 2i_7i = from intron 2 to intron 7, 8i_9 = intron 8/exon 9 boundary, _1 = 5' to exon 1, 18_ = 3' of exon 18, _1_18_ = encompassing the entire 18-exon gene
DNA change (cDNA): description of variant at DNA level, based on a coding DNA reference sequence (following HGVS recommendations); e.g. c.123C>T, c.123_145del, c.123_126dup. For deletions/duplications extending beyond the reference transcript resp. {0}/{2} is used to replace del/dup. Extent of the deletion/duplication should be specified using the genomic description (g.). "-" indicates the variant described on genomic level does not affect the coding DNA reference sequence.
RNA change: description of variant at RNA level (following HGVS recommendations).
- r.123c>u
- r.? = unknown
- r.(?) = RNA not analysed but probably transcribed copy of DNA variant
- r.spl? = RNA not analysed but variant probably affects splicing
- r.(spl?) = RNA not analysed but variant may affect splicing
- r.0? = change expected to abolish transcription
Protein: description of variant at protein level (following HGVS recommendations).
- p.(Arg345Pro) = change predicted from DNA (RNA not analysed)
- p.Arg345Pro = change derived from RNA analysis
- p.? = unknown effect
- p.0? = probably no protein produced
Classification method: The method used for the clinical classification of this variant.
All options:
- ACMG
- ACGS
- EAHAD-CFDB
- ENIGMA
- IARC
- InSiGHT
- kConFab
- other
Clinical classification: Clinical classification of variant, preferably based on standardised criteria (e.g. ACMG), directed on the clinical consequences as published/submitted, indicated using an enriched system including inheritance: e.g. pathogenic, pathogenic (dominant), pathogenic (recessive), pathogenic (!), pathogenic (maternal), pathogenic (paternal). Standard inheritance is covered by dominant/recessive, imprinting by maternal/paternal. A '!' warns for exceptional circumstances to be explained in the 'Remarks' field (low penetrance, variants pathogenic in heterozygous state only, hypomorphic/hypermorphic variants, protective variants, etc.). Non-disease consequences (e.g. drug metabolism (pharmacogenetics), risk factor, blood group, tasting bitter) are indicated using additions to the benign classification; benign (dominant), benign (recessive), benign (!), etc. The value 'association' is used for variants associated with a phenotype and 'NA' for variants from in vitro/in silico records. NOTE: classification may differ from the opinion of the curator as given in a variant SUMMARY-record or the 'Functional effect concluded'). NOTE: pathogenic/likely pathogenic should go together with "variant (probably) affects function" In ClassFunctional.
All options:
- pathogenic
- pathogenic (dominant)
- pathogenic (recessive)
- pathogenic (!)
- pathogenic (maternal)
- pathogenic (paternal)
- likely pathogenic
- likely pathogenic (dominant)
- likely pathogenic (recessive)
- likely pathogenic (!)
- likely pathogenic (maternal)
- likely pathogenic (paternal)
- VUS
- VUS (!)
- likely benign
- likely benign (dominant)
- likely benign (recessive)
- likely benign (!)
- likely benign (maternal)
- likely benign (paternal)
- benign
- benign (dominant)
- benign (recessive)
- benign (!)
- benign (maternal)
- benign (paternal)
- conflicting
- association
- NA
DNA change (genomic) (hg19): HGVS description of variant at DNA level, based on the genomic (chromosomal) DNA reference sequence; e.g. g.12345678C>T, g.12345679del, g.12345678_12345890dup
DNA change (hg38): HGVS description of variant at DNA level, based on the hg38 genomic (chromosomal) eference sequence; e.g. g.12345678C>T, g.12345679del, g.12345678_12345890dup
Published as: listed only when different from "DNA change"; variant as reported originally (e.g. 521delT). Variants seen in animal models, tested in vitro, predicted from RNA analysis, etc. are described between brackets like c.(456C>G)
ISCN: description of the variant according to ISCN nomenclature
DB-ID: database ID of variant, grouping multiple observations of the same variant together, starting with the HGNC gene symbol, followed by an underscore (_) and a six digit number (e.g. DMD_012345). _000000 is used for variants where DNA was not analysed (change predicted from RNA analysis), variants seen in animal models or variants not seen in humans but functionally tested in vitro
Variant remarks: remarks regarding variant described, e.g. germline mosaicism in mother, 345 kb deletion, muscle RNA analysed, not in 200 control chromosomes tested, on founder haplotype, etc.
Reference: publication describing the variant submitted, incl. links to OMIM, PubMed or other source, e.g. "den Dunnen ASHG2003 P2346"
ClinVar ID: ID of variant in ClinVar database
dbSNP ID: the dbSNP ID
Origin: Origin of variant/record: Germline = in all cells, De novo = in all cells, but not in either parent, Germline/De novo (untested) = in all cells, parents not tested (use only when De novo is likely, e.g. isolated/sporadic cases with dominant disease), Somatic = present in a subset of cells, but not in either parent, Uniparental disomy = from parental disomy (maternal or paternal), CLASSIFICATION record = submitter only sharing variant classification (note another report may share Individual data), SUMMARY record = master summary record from curator (may link to another database), In vitro (cloned) = data resulting from in vitro functional assays, animal model = data from animal model, Artefact = false positive variant call, DUPLICATE record = variant already described on another chromosome (e.g. unbalanced translocation, duplicating transposition, 2nd fusion transcript, etc.)
All options:
- Germline
- De novo
- Germline/De novo (untested)
- Somatic
- Uniparental disomy
- Uniparental disomy, maternal allele
- Uniparental disomy, paternal allele
- CLASSIFICATION record
- SUMMARY record
- In vitro (cloned)
- In silico
- animal model
- Artefact
- DUPLICATE record
- Unknown
- Not applicable
Segregation: Indicates whether the variant segregates with the phenotype (yes), does not segregate with the phenotype (no) or segregation is unknown (?)
All options:
- ? = unknown
- yes = segregates with phenotype
- no = does not segregate with phenotype
- - = not applicable
Frequency: frequency in which the variant was found; e.g 5/760 chromosomes (in 5 of 760 chromosomes tested), 1/33 patients (in 1 of 33 patients analysed in study), 0.05 controls (in 5% of control cases tested)
Re-site: restriction enzyme recognition site created (+) or destroyed (-); e.g. BglII+;BamHI-
VIP: variant VIP-status was requested for matchmaking - need collaboration(s) to crack the case - please contact the submitter/curator.
NOTE: to get VIP status ask the curator.
Methylation: result of methylation test; GOM (gain of methylation), LOM (loss of methylation), 30% (30% methylated). NOTE: when several tests were done mention the method as well (e.g. MS-PCR 75%)

 Effect
|

 Reported
|

 Exon
|

 DNA change (cDNA)
|

 RNA change
|

 Protein
|

 Classification method
|

 Clinical classification
|

 DNA change (genomic) (hg19)
|

 DNA change (hg38)
|

 Published as
|

 ISCN
|

 DB-ID
|
 Variant remarks
|

 Reference
|

 ClinVar ID
|

 dbSNP ID
|

 Origin
|

 Segregation
|

 Frequency
|

 Re-site
|

 VIP
|

 Methylation
|

 Owner
|
?/. |
1 |
- |
c.41A>G |
r.(?) |
p.(Asn14Ser) |
- |
VUS |
g.10828959A>G |
g.10718283A>G |
- |
- |
QTRT1_000003 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
-?/. |
1 |
- |
c.102C>A |
r.(?) |
p.(=) |
- |
likely benign |
g.10829020C>A |
- |
DNM2(NM_001005360.2):c.102C>A (p.I34=) |
- |
QTRT1_000004 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht |
-/., ?/. |
3 |
- |
c.190G>A |
r.(?) |
p.(Val64Ile) |
- |
benign, VUS |
g.10870442G>A |
g.10759766G>A |
DNM2(NM_001005360.3):c.190G>A (p.V64I) |
- |
DNM2_000062 |
VKGL data sharing initiative Nederland |
PubMed: Punetha 2016 |
- |
- |
CLASSIFICATION record, Germline/De novo (untested) |
- |
1/94 cases |
- |
- |
- |
Johan den Dunnen, VKGL-NL_AMC |
-/. |
3 |
- |
c.235+6A>G |
r.(=) |
p.(=) |
- |
benign |
g.10870493A>G |
g.10759817A>G |
DNM2(NM_001005360.2):c.235+6A>G, DNM2(NM_001005360.3):c.235+6A>G |
- |
DNM2_000035 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht, VKGL-NL_Nijmegen, VKGL-NL_AMC |
-/., ?/. |
4 |
2i |
c.235+12C>A |
r.(=) |
p.(=) |
- |
benign, VUS |
g.10870499C>A |
g.10759823C>A |
DNM2(NM_001005360.2):c.235+12C>A, DNM2(NM_001005360.3):c.235+12C>A |
- |
DNM2_000026 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Andreas Laner, VKGL-NL_Utrecht, VKGL-NL_Nijmegen, VKGL-NL_AMC |
-/. |
1 |
2i |
c.236-29C>G |
r.(=) |
p.(=) |
- |
benign |
g.10883126C>G |
g.10772450C>G |
- |
- |
DNM2_000027 |
- |
- |
- |
rs3826803 |
Germline |
- |
- |
- |
- |
- |
Andreas Laner |
-?/. |
1 |
- |
c.236-8C>G |
r.(=) |
p.(=) |
- |
likely benign |
g.10883147C>G |
g.10772471C>G |
- |
- |
DNM2_000053 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
-?/. |
2 |
- |
c.238C>T |
r.(?) |
p.(His80Tyr) |
- |
likely benign |
g.10883157C>T |
g.10772481C>T |
DNM2(NM_001005360.2):c.238C>T (p.H80Y), DNM2(NM_001005360.3):c.238C>T (p.H80Y) |
- |
DNM2_000036 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht, VKGL-NL_AMC |
?/. |
1 |
- |
c.269A>G |
r.(?) |
p.(Lys90Arg) |
- |
VUS |
g.10883188A>G |
- |
DNM2(NM_001005360.3):c.269A>G (p.K90R) |
- |
DNM2_000087 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
?/. |
1 |
- |
c.292C>T |
r.(?) |
p.(Arg98Trp) |
- |
VUS |
g.10883211C>T |
g.10772535C>T |
- |
- |
DNM2_000070 |
1 heterozygous, no homozygous; Clinindb (India) |
PubMed: Narang 2020, Journal: Narang 2020 |
- |
rs200408053 |
Germline |
- |
1/2795 individuals |
- |
- |
- |
Mohammed Faruq |
-?/. |
1 |
- |
c.480C>T |
r.(?) |
p.(Ile160=) |
- |
likely benign |
g.10886473C>T |
- |
DNM2(NM_001005360.2):c.480C>T (p.I160=) |
- |
DNM2_000089 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht |
-/. |
1 |
- |
c.519T>C |
r.(?) |
p.(Ala173=) |
- |
benign |
g.10886512T>C |
g.10775836T>C |
- |
- |
DNM2_000054 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
-?/. |
1 |
- |
c.555C>T |
r.(?) |
p.(Asp185=) |
- |
likely benign |
g.10886548C>T |
- |
DNM2(NM_001005360.2):c.555C>T (p.D185=) |
- |
DNM2_000090 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht |
+/. |
1 |
- |
c.596G>A |
r.(?) |
p.(Arg199Gln) |
- |
pathogenic |
g.10887800G>A |
g.10777124G>A |
- |
- |
DNM2_000055 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
?/. |
1 |
- |
c.637G>T |
r.(?) |
p.(Gly213Cys) |
- |
VUS |
g.10887841G>T |
g.10777165G>T |
- |
- |
DNM2_000049 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
-?/. |
1 |
- |
c.643G>A |
r.(?) |
p.(Asp215Asn) |
- |
likely benign |
g.10887847G>A |
- |
DNM2(NM_001005360.3):c.643G>A (p.D215N) |
- |
DNM2_000102 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-?/. |
1 |
- |
c.666C>T |
r.(?) |
p.(Asn222=) |
- |
likely benign |
g.10887870C>T |
g.10777194C>T |
DNM2(NM_001005360.3):c.666C>T (p.N222=) |
- |
DNM2_000056 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-?/. |
1 |
- |
c.688+7C>T |
r.(=) |
p.(=) |
- |
likely benign |
g.10887899C>T |
g.10777223C>T |
DNM2(NM_001005360.3):c.688+7C>T |
- |
DNM2_000063 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
+?/. |
1 |
- |
c.745C>T |
r.(?) |
p.(Arg249Cys) |
- |
likely pathogenic |
g.10893692C>T |
g.10783016C>T |
- |
- |
DNM2_000076 |
combination of variants not reported |
PubMed: Topf 2020 |
- |
- |
Germline |
- |
1/1001 cases |
- |
- |
- |
Johan den Dunnen |
?/. |
1 |
- |
c.784C>T |
r.(?) |
p.(His262Tyr) |
- |
VUS |
g.10893731C>T |
- |
DNM2(NM_001005361.3):c.784C>T (p.(His262Tyr)) |
- |
DNM2_000103 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Leiden |
-?/. |
1 |
- |
c.788C>T |
r.(?) |
p.(Pro263Leu) |
- |
likely benign |
g.10893735C>T |
g.10783059C>T |
- |
- |
DNM2_000071 |
1 heterozygous, no homozygous; Clinindb (India) |
PubMed: Narang 2020, Journal: Narang 2020 |
- |
rs3745674 |
Germline |
- |
1/2795 individuals |
- |
- |
- |
Mohammed Faruq |
+/. |
1 |
- |
c.851A>G |
r.(?) |
p.(Gln284Arg) |
- |
pathogenic |
g.10897241A>G |
g.10786565A>G |
- |
- |
DNM2_000086 |
- |
PubMed: Thomas 2022 |
- |
- |
Germline/De novo (untested) |
- |
- |
- |
- |
- |
Johan den Dunnen |
?/. |
1 |
- |
c.853C>G |
r.(?) |
p.(Leu285Val) |
- |
VUS |
g.10897243C>G |
g.10786567C>G |
- |
- |
DNM2_000069 |
- |
PubMed: Punetha 2016 |
- |
- |
Germline/De novo (untested) |
- |
1/94 cases |
- |
- |
- |
Johan den Dunnen |
+?/. |
1 |
- |
c.869G>A |
r.(?) |
p.(Arg290Gln) |
ACMG |
likely pathogenic (dominant) |
g.10897259G>A |
g.10786583G>A |
- |
- |
DNM2_000084 |
ACMG PS3, PM2 |
PubMed: Natera-de Benito 2021 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |
-?/. |
1 |
- |
c.881C>T |
r.(?) |
p.(Pro294Leu) |
ACMG |
likely pathogenic (dominant) |
g.10897271C>T |
- |
- |
- |
DNM2_000082 |
- |
- |
- |
- |
De novo |
- |
- |
- |
- |
- |
Mariko Okubo |
+?/. |
1 |
- |
c.890G>A |
r.(?) |
p.(Arg297His) |
- |
VUS |
g.10897280G>A |
g.10786604G>A |
- |
- |
DNM2_000085 |
ACMG: PM2-PP2-PP3 |
PubMed: Ferese 2021 |
SCV000762731.1 |
rs763894364 |
Germline/De novo (untested) |
- |
- |
- |
- |
- |
Yvet den Hartog |
-?/. |
1 |
- |
c.992+11C>T |
r.(=) |
p.(=) |
- |
likely benign |
g.10897393C>T |
g.10786717C>T |
DNM2(NM_001005360.3):c.992+11C>T |
- |
DNM2_000037 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
?/. |
1 |
- |
c.1052T>C |
r.(?) |
p.(Val351Ala) |
- |
VUS |
g.10904455T>C |
- |
DNM2(NM_001005360.3):c.1052T>C (p.V351A) |
- |
DNM2_000091 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
+/. |
2 |
8 |
c.1072G>A |
r.(?) |
p.(Gly358Arg) |
- |
pathogenic |
g.10904475G>A |
g.10793799G>A |
- |
- |
DNM2_000017 |
not in 384 control chromosomes, VKGL data sharing initiative Nederland |
PubMed: Gallardo 2008, PubMed: Claeys 2009, OMIM:var0012 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, VKGL-NL_Nijmegen |
-/. |
3 |
8 |
c.1077C>T |
r.(=), r.(?) |
p.(=), p.(Gly359=) |
- |
benign |
g.10904480C>T |
g.10793804C>T |
DNM2(NM_001005360.3):c.1077C>T (p.G359=) |
- |
DNM2_000028 |
VKGL data sharing initiative Nederland |
- |
- |
rs112238216 |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Andreas Laner, VKGL-NL_Nijmegen, VKGL-NL_AMC |
+?/. |
1 |
- |
c.1090C>T |
r.(?) |
p.(Arg364Cys) |
- |
likely pathogenic |
g.10904493C>T |
g.10793817C>T |
DNM2(NM_001005360.3):c.1090C>T (p.R364C) |
- |
DNM2_000038 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_VUmc |
+/., +?/. |
11 |
8 |
c.1102G>A |
r.(?) |
p.(Glu368Lys) |
ACMG |
likely pathogenic, pathogenic, pathogenic (dominant) |
g.10904505G>A |
g.10793829G>A |
- |
- |
DNM2_000001 |
1 heterozygous, no homozygous; Clinindb (India), ACMG PM1, PM2, PM3, PM5, PM6, PP3, PP5, 3 more items |
PubMed: Bitoun 2005, OMIM:var0007, PubMed: Gonzalez-Quereda 2020, PubMed: Natera-de Benito 2021, 3 more items |
- |
rs121434510, rs121909092 |
CLASSIFICATION record, De novo, Germline |
- |
1/2793 individuals |
- |
- |
- |
Johan den Dunnen, Tom Winder, Sandra Cooper, VKGL-NL_Nijmegen, Mohammed Faruq, Mariko Okubo |
+/. |
2 |
8 |
c.1102G>C |
r.(?) |
p.(Glu368Gln) |
- |
pathogenic |
g.10904505G>C |
g.10793829G>C |
DNM2(NM_001005360.3):c.1102G>C (p.E368Q) |
- |
DNM2_000012 |
VKGL data sharing initiative Nederland |
PubMed: Echaniz-Laguna 2007 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, VKGL-NL_AMC |
+/. |
1 |
- |
c.1103A>T |
r.(?) |
p.(Glu368Val) |
- |
pathogenic |
g.10904506A>T |
- |
- |
- |
DNM2_000097 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
+/., +?/. |
6 |
8 |
c.1105C>T |
r.(?) |
p.(Arg369Trp) |
- |
likely pathogenic, pathogenic |
g.10904508C>T |
g.10793832C>T |
- |
- |
DNM2_000008 |
combination of variants not reported, not in 300 control chromosomes, 1 more item |
PubMed: Bitoun 2005, OMIM:var0005, PubMed: Gonzalez-Quereda 2020, PubMed: Topf 2020 |
- |
- |
CLASSIFICATION record, Germline |
- |
1/1001 cases |
AciI- |
- |
- |
Johan den Dunnen, VKGL-NL_Nijmegen |
+/., +?/. |
5 |
8 |
c.1106G>A |
r.(?) |
p.(Arg369Gln) |
ACMG |
likely pathogenic, likely pathogenic (dominant), pathogenic |
g.10904509G>A |
g.10793833G>A |
DNM2(NM_001005360.2):c.1106G>A (p.R369Q) |
- |
DNM2_000007 |
AD, segregates with disease, not in 300 control chromosomes, VKGL data sharing initiative Nederland |
PubMed: Antoniadi 2015, PubMed: Bitoun 2005, OMIM:var0004, PubMed: Gonzalez-Quereda 2020 |
- |
rs121909089 |
CLASSIFICATION record, De novo, Germline |
- |
- |
AciI- |
- |
- |
Johan den Dunnen, VKGL-NL_Utrecht, Mariko Okubo |
+?/. |
1 |
8 |
c.1115T>C |
r.(?) |
p.(Phe372Ser) |
- |
likely pathogenic |
g.10904518T>C |
g.10793842T>C |
- |
- |
DNM2_000023 |
- |
- |
- |
- |
De novo |
- |
- |
- |
- |
- |
Tom Winder |
-?/. |
1 |
- |
c.1218C>T |
r.(?) |
p.(Asp406=) |
- |
likely benign |
g.10906758C>T |
g.10796082C>T |
DNM2(NM_001005360.3):c.1218C>T (p.D406=) |
- |
DNM2_000039 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-/. |
1 |
- |
c.1335+13C>T |
r.(=) |
p.(=) |
- |
benign |
g.10906888C>T |
g.10796212C>T |
DNM2(NM_001005360.3):c.1335+13C>T |
- |
DNM2_000064 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-?/. |
2 |
- |
c.1336-1085C>T |
r.(=) |
p.(=) |
- |
likely benign |
g.10908077C>T |
g.10797401C>T |
DNM2(NM_001005361.2):c.1218C>T (p.D406=), DNM2(NM_001005361.3):c.1218C>T (p.D406=) |
- |
DNM2_000040 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht, VKGL-NL_AMC |
+?/. |
1 |
- |
c.1336-1012dup |
r.? |
p.? |
- |
likely pathogenic |
g.10908150dup |
g.10797474dup |
NM_001005361.2:c.1291dup |
- |
DNM2_000077 |
combination of variants not reported |
PubMed: Topf 2020 |
- |
- |
Germline |
- |
1/1001 cases |
- |
- |
- |
Johan den Dunnen |
+?/. |
1 |
- |
c.1373G>A |
r.(?) |
p.(Arg458Gln) |
- |
likely pathogenic |
g.10909199G>A |
g.10798523G>A |
- |
- |
DNM2_000078 |
combination of variants not reported |
PubMed: Topf 2020 |
- |
- |
Germline |
- |
1/1001 cases |
- |
- |
- |
Johan den Dunnen |
?/. |
1 |
- |
c.1384A>G |
r.(?) |
p.(Thr462Ala) |
- |
VUS |
g.10909210A>G |
g.10798534A>G |
- |
- |
DNM2_000050 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
+/., +?/. |
15 |
11 |
c.1393C>T |
r.(?) |
p.(Arg465Trp) |
ACMG |
likely pathogenic, pathogenic |
g.10909219C>T |
g.10798543C>T |
DNM2(NM_001005360.2):c.1393C>T (p.(Arg465Trp), p.R465W) |
- |
DNM2_000009 |
not in 300 control chromosomes, VKGL data sharing initiative Nederland |
PubMed: Bitoun 2005, OMIM:var0006 |
- |
- |
CLASSIFICATION record, De novo, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, Tom Winder, VKGL-NL_Leiden, VKGL-NL_Utrecht, Mariko Okubo |
-/. |
1 |
- |
c.1423-12G>A |
r.(=) |
p.(=) |
- |
benign |
g.10912952G>A |
g.10802276G>A |
DNM2(NM_001005360.3):c.1423-12G>A |
- |
DNM2_000041 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
?/. |
1 |
- |
c.1456A>G |
r.(?) |
p.(Ile486Val) |
- |
VUS |
g.10912997A>G |
- |
DNM2(NM_001005360.3):c.1456A>G (p.I486V) |
- |
DNM2_000095 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
+?/. |
2 |
- |
c.1483G>A |
r.(?) |
p.(Gly495Arg) |
ACMG |
likely pathogenic (dominant) |
g.10913024G>A |
g.10802348G>A |
- |
- |
DNM2_000073 |
- |
- |
- |
- |
De novo, Germline |
yes |
- |
- |
- |
- |
Mathieu Cerino, Mariko Okubo |
?/. |
1 |
- |
c.1493A>C |
r.(?) |
p.(Asn498Thr) |
- |
VUS |
g.10913034A>C |
- |
- |
- |
DNM2_000092 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
-?/. |
1 |
- |
c.1545+14C>G |
r.(=) |
p.(=) |
- |
likely benign |
g.10916657C>G |
g.10805981C>G |
DNM2(NM_001005360.2):c.1545+14C>G |
- |
DNM2_000057 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht |
?/. |
1 |
13i |
c.1545+86C>G |
r.(=) |
p.(=) |
- |
VUS |
g.10916729C>G |
g.10806053C>G |
- |
- |
DNM2_000029 |
- |
- |
- |
- |
Germline |
- |
- |
- |
- |
- |
Andreas Laner |
+?/. |
1 |
- |
c.1559T>G |
r.(?) |
p.(Val520Gly) |
ACMG |
pathogenic (dominant) |
g.10922941T>G |
- |
- |
- |
DNM2_000080 |
- |
- |
- |
- |
De novo |
- |
- |
- |
- |
- |
Mariko Okubo |
+/., +?/. |
5 |
15 |
c.1565G>A |
r.(?) |
p.(Arg522His) |
- |
likely pathogenic (recessive), pathogenic |
g.10922947G>A |
g.10812271G>A |
DNM2(NM_001005360.3):c.1565G>A (p.R522H) |
- |
DNM2_000022 |
VKGL data sharing initiative Nederland |
PubMed: Park 2017 |
- |
- |
CLASSIFICATION record, Germline |
- |
1/209 cases |
- |
- |
- |
Johan den Dunnen, Tom Winder, Andreas Laner, VKGL-NL_Nijmegen, VKGL-NL_VUmc |
?/. |
2 |
- |
c.1609G>A |
r.(?) |
p.(Gly537Ser) |
ACMG |
VUS |
g.10922991G>A |
g.10812315G>A |
- |
- |
DNM2_000051 |
ACMG grading: PM2,PM5, VKGL data sharing initiative Nederland |
- |
- |
rs121909093 |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Andreas Laner, VKGL-NL_Nijmegen |
+/. |
2 |
15 |
c.1609G>T |
r.(?) |
p.(Gly537Cys) |
- |
pathogenic |
g.10922991G>T |
g.10812315G>T |
1597G>T, DNM2(NM_001005360.3):c.1609G>T (p.G537C) |
- |
DNM2_000010 |
not in 200 control chromosomes, VKGL data sharing initiative Nederland |
PubMed: Fabrizi 2007, OMIM:var0008 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, VKGL-NL_AMC |
?/. |
1 |
- |
c.1619A>G |
r.(?) |
p.(Glu540Gly) |
- |
VUS |
g.10923001A>G |
g.10812325A>G |
- |
- |
DNM2_000065 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
?/. |
1 |
- |
c.1663G>A |
r.(?) |
p.(Asp555Asn) |
- |
VUS |
g.10923045G>A |
- |
DNM2(NM_001005361.3):c.1663G>A (p.(Asp555Asn)) |
- |
DNM2_000104 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Leiden |
+/. |
1 |
15_15i |
c.1664_1671+1del |
r.1663_1671del |
p.[Asp555_Glu558del, Asp555Glyfs*12] |
- |
pathogenic |
g.10923046_10923054del |
g.10812370_10812378del |
1652_1659+1delATGAGGAGg |
- |
DNM2_000021 |
mapped by linkage; not in 500 control chromosomes |
PubMed: Zuchner 2005, OMIM:var0001 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |
+/. |
1 |
16 |
c.1675_1677del |
r.(?) |
p.(Lys559del) |
- |
pathogenic |
g.10930659_10930661del |
g.10819983_10819985del |
1675_1677delAAA |
- |
DNM2_000002 |
- |
PubMed: Bitoun 2008 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |
+/., +?/. |
2 |
16 |
c.1678G>A |
r.(?) |
p.(Glu560Lys) |
- |
likely pathogenic, pathogenic |
g.10930662G>A |
g.10819986G>A |
- |
- |
DNM2_000003 |
VKGL data sharing initiative Nederland |
PubMed: Bitoun 2009 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, VKGL-NL_Nijmegen |
+/., +?/. |
4 |
16 |
c.1684A>G |
r.(?) |
p.(Lys562Glu) |
- |
likely pathogenic, pathogenic |
g.10930668A>G |
g.10819992A>G |
1672A>G, DNM2(NM_001005360.3):c.1684A>G (p.K562E) |
- |
DNM2_000018 |
VKGL data sharing initiative Nederland |
PubMed: Claeys 2009, PubMed: Zuchner 2005, PubMed: Claeys 2009, OMIM:var0002 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, VKGL-NL_Nijmegen, VKGL-NL_AMC |
+/., +?/., ?/. |
3 |
16 |
c.1684_1686del |
r.(?) |
p.(Lys562del) |
- |
likely pathogenic, pathogenic, VUS |
g.10930668_10930670del |
g.10819992_10819994del |
1672_1674delAAG, DNM2(NM_001005360.3):c.1684_1686delAAG (p.K562del) |
- |
DNM2_000019 |
VKGL data sharing initiative Nederland |
PubMed: Zuchner 2005, PubMed: Claeys 2009, OMIM:var0003 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, Andreas Laner, VKGL-NL_AMC |
+/. |
2 |
16 |
c.1709T>A |
r.(?) |
p.(Leu570His) |
- |
pathogenic |
g.10930693T>A |
g.10820017T>A |
1697T>A, DNM2(NM_001005360.3):c.1709T>A (p.L570H) |
- |
DNM2_000011 |
not in 200 control chromosomes, VKGL data sharing initiative Nederland |
PubMed: Fabrizi 2007, OMIM:var0009 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, VKGL-NL_AMC |
+/. |
1 |
- |
c.1739T>C |
r.(?) |
p.(Met580Thr) |
- |
pathogenic (dominant) |
g.10930723T>C |
g.10820047T>C |
- |
- |
DNM2_000072 |
- |
PubMed: Antoniadi 2015 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |
-?/. |
1 |
- |
c.1752C>T |
r.(?) |
p.(His584=) |
- |
likely benign |
g.10930736C>T |
g.10820060C>T |
DNM2(NM_001005360.3):c.1752C>T (p.H584=) |
- |
DNM2_000058 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-/., -?/. |
2 |
- |
c.1781+17C>A |
r.(=) |
p.(=) |
- |
benign, likely benign |
g.10930782C>A |
g.10820106C>A |
DNM2(NM_001005360.2):c.1781+17C>A, DNM2(NM_001005360.3):c.1781+17C>A |
- |
DNM2_000042 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht, VKGL-NL_AMC |
-/. |
1 |
- |
c.1782-11C>T |
r.(=) |
p.(=) |
- |
benign |
g.10934453C>T |
g.10823777C>T |
DNM2(NM_001005360.3):c.1782-11C>T |
- |
DNM2_000066 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-?/. |
1 |
- |
c.1782-7C>G |
r.(=) |
p.(=) |
- |
likely benign |
g.10934457C>G |
g.10823781C>G |
DNM2(NM_001005360.2):c.1782-7C>G (p.(=)) |
- |
DNM2_000059 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Leiden |
-?/. |
1 |
- |
c.1782-4G>A |
r.spl? |
p.? |
- |
likely benign |
g.10934460G>A |
g.10823784G>A |
DNM2(NM_001005360.3):c.1782-4G>A |
- |
DNM2_000043 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
?/. |
1 |
- |
c.1844G>T |
r.(?) |
p.(Ser615Ile) |
- |
VUS |
g.10934526G>T |
g.10823850G>T |
- |
- |
DNM2_000060 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
+/. |
2 |
17 |
c.1852G>A |
r.(?) |
p.(Ala618Thr) |
- |
pathogenic |
g.10934534G>A |
g.10823858G>A |
- |
- |
DNM2_000013 |
VKGL data sharing initiative Nederland |
PubMed: Bitoun 2007 |
- |
- |
CLASSIFICATION record, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, VKGL-NL_Nijmegen |
+/. |
3 |
17 |
c.1853C>A |
r.(?) |
p.(Ala618Asp) |
ACMG |
pathogenic, pathogenic (dominant) |
g.10934535C>A |
g.10823859C>A |
- |
- |
DNM2_000005 |
ACMG PS2, PM1, PM2, PM5, PP2, PP3, PP5 |
PubMed: Marinakis 2021, PubMed: Melberg 2010 |
- |
rs1555715869 |
De novo, Germline |
- |
- |
- |
- |
- |
Johan den Dunnen, Tom Winder, Jan Traeger-Synodinos |
+/. |
1 |
17 |
c.1856C>G |
r.(?) |
p.(Ser619Trp) |
- |
pathogenic |
g.10934538C>G |
g.10823862C>G |
- |
- |
DNM2_000015 |
- |
PubMed: Bitoun 2007, OMIM:var0011 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |
+/., +?/. |
6 |
17 |
c.1856C>T |
r.(?) |
p.(Ser619Leu) |
ACMG |
likely pathogenic, pathogenic |
g.10934538C>T |
g.10823862C>T |
DNM2(NM_001005360.3):c.1856C>T (p.S619L) |
- |
DNM2_000014 |
1 heterozygous, no homozygous; Clinindb (India), VKGL data sharing initiative Nederland |
PubMed: Bitoun 2007, OMIM:var0010, PubMed: Narang 2020, Journal: Narang 2020 |
- |
rs121909095 |
CLASSIFICATION record, De novo, Germline |
- |
1/2795 individuals |
- |
- |
- |
Johan den Dunnen, VKGL-NL_VUmc, Mohammed Faruq, Mariko Okubo |
+/. |
1 |
17 |
c.1862T>C |
r.(?) |
p.(Leu621Pro) |
- |
pathogenic |
g.10934544T>C |
g.10823868T>C |
- |
- |
DNM2_000006 |
- |
PubMed: Jungbluth 2010 |
- |
- |
Germline |
- |
- |
AvaI+ |
- |
- |
Johan den Dunnen |
+?/. |
2 |
- |
c.1871G>T |
r.(?) |
p.(Gly624Val) |
ACMG |
likely pathogenic (dominant) |
g.10934553G>T |
- |
- |
- |
DNM2_000081 |
- |
- |
- |
- |
De novo |
- |
- |
- |
- |
- |
Mariko Okubo |
+/. |
1 |
17 |
c.1873_1875del |
r.(?) |
p.(Val625del) |
- |
pathogenic |
g.10934555_10934557del |
g.10823879_10823881del |
1873_1875delGTC |
- |
DNM2_000016 |
- |
PubMed: Bitoun 2007 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |
+/. |
1 |
17 |
c.1879C>T |
r.(?) |
p.(Pro627Ser) |
ACMG |
pathogenic |
g.10934561C>T |
g.10823885C>T |
- |
- |
DNM2_000101 |
- |
- |
- |
- |
Germline/De novo (untested) |
? |
gnomAD no frequency |
- |
- |
- |
JA Bevilacqua |
+/. |
1 |
17 |
c.1880C>A |
r.(?) |
p.(Pro627His) |
- |
pathogenic |
g.10934562C>A |
g.10823886C>A |
- |
- |
DNM2_000025 |
- |
PubMed: O'Grady 2016 |
- |
- |
De novo |
- |
- |
- |
- |
- |
Sandra Cooper |
?/. |
1 |
17i |
c.1893+32dup |
r.(=) |
p.(=) |
- |
VUS |
g.10934607dup |
g.10823931dup |
- |
- |
DNM2_000031 |
- |
- |
- |
- |
Germline |
- |
- |
- |
- |
- |
Andreas Laner |
-/., -?/. |
3 |
- |
c.1902C>T |
r.(?) |
p.(Asn634=) |
- |
benign, likely benign |
g.10935741C>T |
g.10825065C>T |
DNM2(NM_001005360.2):c.1902C>T (p.N634=), DNM2(NM_001005360.3):c.1902C>T (p.N634=) |
- |
DNM2_000044 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht, VKGL-NL_Nijmegen, VKGL-NL_AMC |
+/. |
1 |
18 |
c.1932del |
r.(?) |
p.(Met645Trpfs*39) |
- |
pathogenic |
g.10935771del |
g.10825095del |
- |
- |
DNM2_000032 |
- |
- |
- |
- |
Germline |
- |
- |
- |
- |
- |
Andreas Laner |
?/. |
1 |
18 |
c.1940C>G |
r.(?) |
p.(Pro647Arg) |
- |
VUS |
g.10935779C>G |
g.10825103C>G |
- |
- |
DNM2_000024 |
- |
- |
- |
- |
Unknown |
- |
- |
- |
- |
- |
Olivera Casar-Borota |
+/. |
1 |
18 |
c.1948G>A |
r.(?) |
p.(Glu650Lys) |
- |
pathogenic |
g.10935787G>A |
g.10825111G>A |
- |
- |
DNM2_000004 |
- |
PubMed: Bitoun 2009 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |
-/. |
1 |
- |
c.1958T>G |
r.(?) |
p.(Val653Gly) |
- |
benign |
g.10935797T>G |
g.10825121T>G |
- |
- |
DNM2_000067 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
?/. |
1 |
- |
c.2014C>T |
r.(?) |
p.(Arg672Cys) |
- |
VUS |
g.10935853C>T |
- |
DNM2(NM_001005360.3):c.2014C>T (p.R672C) |
- |
DNM2_000105 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Groningen |
-/. |
1 |
18i |
c.2058+89G>A |
r.(=) |
p.(=) |
- |
benign |
g.10935986G>A |
g.10825310G>A |
- |
- |
DNM2_000033 |
- |
- |
- |
rs57561584 |
Germline |
- |
- |
- |
- |
- |
Andreas Laner |
-/. |
2 |
- |
c.2139T>C |
r.(?) |
p.(Ala713=) |
- |
benign |
g.10939792T>C |
g.10829116T>C |
DNM2(NM_001005360.3):c.2139T>C (p.A713=) |
- |
DNM2_000045 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen, VKGL-NL_AMC |
?/. |
1 |
- |
c.2144A>G |
r.(?) |
p.(Gln715Arg) |
- |
VUS |
g.10939797A>G |
- |
DNM2(NM_001005360.2):c.2144A>G (p.Q715R) |
- |
DNM2_000093 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_VUmc |
?/. |
1 |
- |
c.2153G>A |
r.(?) |
p.(Arg718Gln) |
- |
VUS |
g.10939806G>A |
- |
DNM2(NM_001005360.3):c.2153G>A (p.R718Q) |
- |
DNM2_000096 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-?/. |
1 |
- |
c.2171G>A |
r.(?) |
p.(Arg724His) |
ACMG |
likely pathogenic (dominant) |
g.10939824G>A |
- |
- |
- |
DNM2_000083 |
- |
- |
- |
- |
De novo |
- |
- |
- |
- |
- |
Mariko Okubo |
?/. |
1 |
- |
c.2179C>T |
r.(?) |
p.(His727Tyr) |
- |
VUS |
g.10939832C>T |
- |
DNM2(NM_001005360.3):c.2179C>T (p.H727Y) |
- |
DNM2_000079 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
?/. |
1 |
- |
c.2257G>A |
r.(?) |
p.(Asp753Asn) |
- |
VUS |
g.10939910G>A |
g.10829234G>A |
- |
- |
DNM2_000052 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Nijmegen |
?/. |
1 |
- |
c.2276G>A |
r.(?) |
p.(Ser759Asn) |
- |
VUS |
g.10939929G>A |
- |
DNM2(NM_001005360.3):c.2276G>A (p.S759N) |
- |
DNM2_000094 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-/. |
1 |
19i |
c.2292-85A>G |
r.(=) |
p.(=) |
- |
benign |
g.10940718A>G |
g.10830042A>G |
- |
- |
DNM2_000034 |
- |
- |
- |
rs58724234 |
Germline |
- |
- |
- |
- |
- |
Andreas Laner |
?/. |
1 |
- |
c.2306G>A |
r.(?) |
p.(Arg769His) |
- |
VUS |
g.10940817G>A |
- |
DNM2(NM_001005360.3):c.2306G>A (p.R769H) |
- |
DNM2_000100 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
-?/. |
1 |
- |
c.2393T>G |
r.(?) |
p.(Val798Gly) |
- |
likely benign |
g.10940904T>G |
g.10830228T>G |
DNM2(NM_001005360.2):c.2393T>G (p.V798G) |
- |
DNM2_000046 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht |
-/. |
1 |
- |
c.2484G>A |
r.(?) |
p.(Pro828=) |
- |
benign |
g.10940995G>A |
g.10830319G>A |
DNM2(NM_001005360.3):c.2484G>A (p.P828=) |
- |
DNM2_000068 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_AMC |
?/. |
1 |
- |
c.2516C>T |
r.(?) |
p.(Pro839Leu) |
- |
VUS |
g.10941027C>T |
g.10830351C>T |
- |
- |
DNM2_000098 |
- |
- |
- |
- |
Germline/De novo (untested) |
- |
- |
- |
- |
- |
Gemeinschaftspraxis für Humangenetik Dresden |
-?/. |
2 |
- |
c.2543+7C>G |
r.(=) |
p.(=) |
- |
likely benign |
g.10941061C>G |
g.10830385C>G |
DNM2(NM_001005360.2):c.2543+7C>G, DNM2(NM_001005360.3):c.2543+7C>G |
- |
DNM2_000047 |
VKGL data sharing initiative Nederland |
- |
- |
- |
CLASSIFICATION record |
- |
- |
- |
- |
- |
VKGL-NL_Utrecht, VKGL-NL_AMC |
+/. |
1 |
21 |
c.2576_2581del |
r.(?) |
p.(Thr859_Ile860del) |
- |
pathogenic |
g.10941686_10941691del |
g.10831010_10831015del |
2564_2569delCCATTA |
- |
DNM2_000020 |
not in 384 control chromosomes |
PubMed: Claeys 2009 |
- |
- |
Germline |
- |
- |
- |
- |
- |
Johan den Dunnen |