Unique variants in the ALDH7A1 gene

Information The variants shown are described using the NM_001182.4 transcript reference sequence.

189 entries on 2 pages. Showing entries 1 - 100.
Legend   How to query   « First ‹ Prev     1 2     Next › Last »

Effect     

Reported     

Exon     

AscendingDNA change (cDNA)     

RNA change     

Protein     

Classification method     

Clinical classification     

DNA change (genomic) (hg19)     

DNA change (hg38)     

Published as     

ISCN     

DB-ID     

Variant remarks     

Reference     

ClinVar ID     

dbSNP ID     

Origin     

Segregation     

Frequency     

Re-site     

VIP     

Methylation     

Owner     
+?/. 1 - c.(695+1_696-1)_(1200+1_1201-1 r.(?) p.(?) - likely pathogenic g.? g.? ALDH7A1(NM_001182.4):c.1279G>C(p.E427Q)/CDS8-13 deletion - RAD50_000000 - PubMed: Sun 2018 - - Germline/De novo (untested) ? 190 - - - LOVD
./. 1 - c.-19786395_*2052133dup - - - pathogenic g.123828524_145717285dup - - - SIL1_000024 mosaicism, copy number 3 in 0.38 cells PubMed: DDDS 2015, Journal: DDDS 2015 - - Somatic - - - - - Johan den Dunnen
-/. 2 - c.-60G>A r.(?) p.(=) - benign g.125930950C>T g.126595258C>T ALDH7A1(NM_001202404.1):c.-60G>A, ALDH7A1(NM_001202404.2):c.-60G>A - ALDH7A1_000048 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_AMC
-?/. 1 - c.-34G>C r.(?) p.(=) - likely benign g.125930924C>G g.126595232C>G ALDH7A1(NM_001202404.2):c.-34G>C - ALDH7A1_000047 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-/. 1 - c.39A>G r.(?) p.(Ala13=) - benign g.125930852T>C g.126595160T>C ALDH7A1(NM_001182.5):c.39A>G (p.A13=) - ALDH7A1_000172 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_AMC
-?/. 1 - c.73C>T r.(?) p.(Pro25Ser) - likely benign g.125930818G>A g.126595126G>A - - ALDH7A1_000050 - PubMed: Saeed 2018 - - Germline - - - - - Johan den Dunnen
+/. 1 - c.119C>G r.(?) p.(Ala40Gly) - pathogenic (recessive) g.125930772G>C g.126595080G>C - - ALDH7A1_000158 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.187G>T r.(?) p.(Gly63*) - pathogenic (recessive) g.125930704C>A g.126595012C>A - - ALDH7A1_000157 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.191del r.(?) p.(Glu64Glyfs*14) - pathogenic (recessive) g.125930700del g.126595008del c.191delA - ALDH7A1_000156 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.192+2dup r.spl? p.? - pathogenic (recessive) g.125930697dup g.126595005dup c.192+2dupT - ALDH7A1_000155 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.192+2T>G r.spl p.? - pathogenic (recessive) g.125930697A>C g.126595005A>C - - ALDH7A1_000154 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
?/. 1 - c.192+6C>T r.(=) p.(=) - VUS g.125930693G>A - ALDH7A1(NM_001182.4):c.192+6C>T - ALDH7A1_000046 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
-/. 1 - c.193-711A>G r.(=) p.(=) - benign g.125929807T>C g.126594115T>C ALDH7A1(NM_001182.5):c.193-711A>G - ALDH7A1_000045 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
-/. 1 - c.193-98A>G r.(=) p.(=) - benign g.125929194T>C g.126593502T>C ALDH7A1(NM_001182.5):c.193-98A>G - ALDH7A1_000171 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
?/. 2 - c.193-15T>C r.spl p.(=) - VUS g.125929111A>G g.126593419A>G [c.193-9T>C] [c.193-15T>C] - ALDH7A1_000153 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
?/. 1 1i c.193-12T>G r.spl p.? - VUS g.125929108A>C g.126593416A>C - - ALDH7A1_000184 - PubMed: Ganapathy 2019 - rs770632526 Germline - - - - - Johan den Dunnen
?/. 2 - c.193-9T>C r.spl p.(=) - VUS g.125929105A>G g.126593413A>G [c.193-9T>C] [c.193-15T>C] - ALDH7A1_000152 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+?/., ?/. 2 - c.203C>A r.(?) p.(Thr68Asn), p.Thr68Asn - NA, VUS g.125929086G>T g.126593394G>T ALDH7A1(NM_001182.4):c.203C>A (p.T68N) - ALDH7A1_000151 expression cloning in E.coli (at 37oC) shows 0.535 alpha‐AASADH activity (nmol NADH/min/mg ATQ), 1 more item PubMed: Coughlin 2019 - - CLASSIFICATION record, In vitro (cloned) - - - - - Curtis Coughlin II, VKGL-NL_Rotterdam
+/. 2 - c.241C>T r.(?) p.(Arg81*) - pathogenic (recessive) g.125929048G>A g.126593356G>A - - ALDH7A1_000150 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II, Min Peng
+/. 2 - c.246+1G>A r.spl p.? - pathogenic (recessive) g.125929042C>T g.126593350C>T - - ALDH7A1_000149 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
-?/. 1 - c.246+31G>T r.(=) p.(=) - likely benign g.125929012C>A g.126593320C>A ALDH7A1(NM_001182.5):c.246+31G>T - ALDH7A1_000036 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
-/. 1 - c.246+35_246+42dup r.(=) p.(=) - benign g.125929029_125929036dup g.126593337_126593344dup ALDH7A1(NM_001182.5):c.246+6delAinsAGTGTGTGT - ALDH7A1_000043 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-?/. 1 - c.246+37_246+42del r.(=) p.(=) - likely benign g.125929031_125929036del g.126593339_126593344del ALDH7A1(NM_001182.5):c.246+37_246+42delGTGTGT - ALDH7A1_000037 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-/. 1 - c.246+37_246+42dup r.(=) p.(=) - benign g.125929031_125929036dup g.126593339_126593344dup ALDH7A1(NM_001182.5):c.246+37_246+42dupGTGTGT - ALDH7A1_000170 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-/. 1 - c.246+39_246+42del r.(=) p.(=) - benign g.125929033_125929036del g.126593341_126593344del ALDH7A1(NM_001182.5):c.246+39_246+42delGTGT - ALDH7A1_000038 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-/. 1 - c.246+39_246+42dup r.(=) p.(=) - benign g.125929033_125929036dup g.126593341_126593344dup ALDH7A1(NM_001182.5):c.246+39_246+42dupGTGT, ALDH7A1(NM_001182.5):c.246+6delAinsAGTGT - ALDH7A1_000042 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-?/. 1 - c.246+41_246+42del r.(=) p.(=) - likely benign g.125929035_125929036del g.126593343_126593344del ALDH7A1(NM_001182.5):c.246+41_246+42delGT - ALDH7A1_000041 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-?/. 1 - c.246+41_246+42dup r.(=) p.(=) - likely benign g.125929035_125929036dup g.126593343_126593344dup ALDH7A1(NM_001182.5):c.246+41_246+42dupGT, ALDH7A1(NM_001182.5):c.246+6delAinsAGT - ALDH7A1_000044 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-?/. 1 - c.246+167T>A r.(=) p.(=) - likely benign g.125928876A>T g.126593184A>T ALDH7A1(NM_001182.5):c.246+167T>A - ALDH7A1_000035 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
+/. 1 - c.247-1G>C r.spl p.? - pathogenic (recessive) g.125928422C>G g.126592730C>G - - ALDH7A1_000148 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
-/. 2 - c.273T>C r.(?) p.(Thr91=) - benign g.125928395A>G g.126592703A>G ALDH7A1(NM_001182.5):c.273T>C (p.T91=) - ALDH7A1_000034 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht, VKGL-NL_AMC
?/. 1 - c.292G>A r.(?) p.(Ala98Thr) - VUS g.125928376C>T g.126592684C>T ALDH7A1(NM_001182.4):c.292G>A (p.(Ala98Thr)) - ALDH7A1_000169 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
+/., ?/. 6 - c.312+1G>A r.spl, r.spl? p.? - pathogenic (recessive), VUS g.125928355C>T g.126592663C>T ALDH7A1(NM_001182.5):c.312+1G>A - ALDH7A1_000033 VKGL data sharing initiative Nederland PubMed: Coughlin 2019 - - CLASSIFICATION record, Germline - - - - - Curtis Coughlin II, VKGL-NL_Utrecht
+/. 1 3i_4i c.(312+1_313-1)_(393+1_394-1)del r.spl p.? - pathogenic (recessive) g.(125918667_125919623)_(125919705_125928355)del - - - ALDH7A1_000145 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 14 3 c.328C>T r.(?) p.(Arg110*), p.Arg110* ACMG NA, pathogenic, pathogenic (recessive) g.125919689G>A g.126583997G>A - - ALDH7A1_000006 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Coughlin 2019, PubMed: Mills 2006, PubMed: Trujillano 2017, PubMed: Tumienė 2018 - - Germline, In vitro (cloned) - - - - - Johan den Dunnen, Curtis Coughlin II, Daniel Trujillano
+/. 4 - c.332G>A r.(?) p.(Gly111Glu), p.Gly111Glu - NA, pathogenic (recessive) g.125919685C>T g.126583993C>T - - ALDH7A1_000147 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Coughlin 2019, PubMed: Coulter-Mackie 2012 - - Germline, In vitro (cloned) - - - - - Curtis Coughlin II
+/. 1 - c.346C>T r.(?) p.(Gln116Ter) - pathogenic g.125919671G>A g.126583979G>A ALDH7A1(NM_001182.5):c.346C>T (p.Q116*) - ALDH7A1_000032 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
+/., -?/. 2 - c.364C>T r.(?) p.(Arg122Trp), p.Arg122Trp - NA, pathogenic (recessive) g.125919653G>A g.126583961G>A - - ALDH7A1_000146 expression cloning in E.coli (at 37oC) shows 0.812 alpha‐AASADH activity (nmol NADH/min/mg ATQ) PubMed: Coughlin 2019 - - Germline, In vitro (cloned) - - - - - Curtis Coughlin II
-?/. 1 - c.373A>G r.(?) p.(Ile125Val) - likely benign g.125919644T>C g.126583952T>C ALDH7A1(NM_001182.5):c.373A>G (p.I125V) - ALDH7A1_000031 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-/. 1 - c.393+94del r.(=) p.(=) - benign g.125919541del g.126583849del ALDH7A1(NM_001182.5):c.393+94delT - ALDH7A1_000029 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
+/. 1 - c.394-1G>A r.spl p.? - pathogenic (recessive) g.125918667C>T g.126582975C>T - - ALDH7A1_000144 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.394-1G>C r.spl p.? - pathogenic (recessive) g.125918667C>G g.126582975C>G - - ALDH7A1_000143 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+?/. 1 - c.394G>T r.(?) p.(Val132Leu) ACMG likely pathogenic g.125918666C>A - - - ALDH7A1_000188 - - - - Unknown - - - - - Cordula Haas
?/. 1 - c.398C>G r.(?) p.(Ser133Cys) - VUS g.125918662G>C - ALDH7A1(NM_001182.4):c.398C>G (p.S133C) - ALDH7A1_000028 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
+/. 1 - c.415del r.(?) p.(Ile139Serfs*2) - pathogenic (recessive) g.125918648del g.126582956del - - ALDH7A1_000142 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
?/. 1 - c.442C>G r.(?) p.(Gln148Glu) - VUS g.125918618G>C g.126582926G>C ALDH7A1(NM_001182.4):c.442C>G (p.(Gln148Glu)) - ALDH7A1_000168 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
+/. 1 - c.442C>T r.(?) p.(Gln148*) - pathogenic (recessive) g.125918618G>A g.126582926G>A - - ALDH7A1_000141 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.445G>A r.(?) p.(Glu149Lys) - pathogenic (recessive) g.125918615C>T g.126582923C>T - - ALDH7A1_000140 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.460T>C r.(?) p.(Cys154Arg) - pathogenic (recessive) g.125918600A>G g.126582908A>G - - ALDH7A1_000139 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.467A>G r.(?) p.(Tyr156Cys) - pathogenic (recessive) g.125918593T>C g.126582901T>C - - ALDH7A1_000138 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.469G>C r.(?) p.Ala157Pro - NA g.125918591C>G g.126582899C>G - - ALDH7A1_000137 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Korasick 2017 - - In vitro (cloned) - - - - - Curtis Coughlin II
+/. 1 - c.481T>C r.(?) p.(Ser161Pro) - pathogenic (recessive) g.125918579A>G g.126582887A>G - - ALDH7A1_000136 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.494G>A r.(?) p.(Gly165Glu) - pathogenic (recessive) g.125918566C>T g.126582874C>T - - ALDH7A1_000135 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.494G>T - p.Gln165Val - NA g.125918566C>T g.126582874C>T - - ALDH7A1_000135 1 more item PubMed: Korasick 2017 - - In vitro (cloned) - - - - - Curtis Coughlin II
+/. 1 - c.497G>T r.(?) p.Gln166Val - NA g.125918563C>A g.126582871C>A - - ALDH7A1_000134 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Korasick 2017 - - In vitro (cloned) - - - - - Curtis Coughlin II
+/. 3 - c.503_506del r.(?) p.(Ile168Serfs*10) - pathogenic (recessive) g.125918554_125918557del g.126582862_126582865del c.503_506delTCTT - ALDH7A1_000133 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 4 - c.517+5G>A r.spl? p.? - pathogenic (recessive) g.125918538C>T g.126582846C>T - - ALDH7A1_000132 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
-/., -?/. 3 - c.518-12T>G r.(=) p.(=) - benign, likely benign g.125912915A>C g.126577223A>C ALDH7A1(NM_001182.5):c.518-12T>G - ALDH7A1_000027 12 heterozygous, no homozygous; Clinindb (India), VKGL data sharing initiative Nederland PubMed: Narang 2020, Journal: Narang 2020 - rs79544459 CLASSIFICATION record, Germline - 12/2790 individuals - - - VKGL-NL_Utrecht, VKGL-NL_AMC, Mohammed Faruq
+/., +?/. 3 - c.518-1G>C r.spl p.? - likely pathogenic, pathogenic (recessive) g.125912904C>G g.126577212C>G - - ALDH7A1_000003 - PubMed: Coughlin 2019 - - Germline yes - - - - Curtis Coughlin II, Nicolai Kohlschmidt
+/. 2 5i_6i c.(517+1_518-1)_(650+1_651-1)del r.spl p.? - pathogenic (recessive) g.(125911157_125912770)_(125912904_125918542)del - - - ALDH7A1_000123 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.529G>C r.(?) p.(Ala177Pro) - pathogenic (recessive) g.125912892C>G g.126577200C>G - - ALDH7A1_000131 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 4 - c.530C>A r.(?) p.(Ala177Glu), p.Ala177Glu - NA, pathogenic (recessive) g.125912891G>T g.126577199G>T - - ALDH7A1_000130 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Coughlin 2019, PubMed: Korasick 2017 - - Germline, In vitro (cloned) - - - - - Curtis Coughlin II
?/. 1 - c.530C>T r.(?) p.(Ala177Val) - VUS g.125912891G>A g.126577199G>A ALDH7A1(NM_001182.4):c.530C>T (p.(Ala177Val)) - ALDH7A1_000167 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
+/. 1 - c.532_542del r.(?) p.(Leu178Valfs*46) - pathogenic (recessive) g.125912882_125912892del g.126577190_126577200del c.532_542del11 - ALDH7A1_000129 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
?/. 1 - c.544T>C r.(?) p.(Trp182Arg) - VUS g.125912877A>G g.126577185A>G ALDH7A1(NM_001182.4):c.544T>C (p.(Trp182Arg)) - ALDH7A1_000166 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
+/. 1 6 c.571A>G r.(?) p.(Ile191Val) - pathogenic g.125912850T>C g.126577158T>C NM_001182: c.A571G; p.I191V - ALDH7A1_000007 - PubMed: Karaca 2015 - - Germline - - - - - Johan den Dunnen
+/. 3 - c.575C>T r.(?) p.(Thr192Met) - pathogenic (recessive) g.125912846G>A g.126577154G>A - - ALDH7A1_000128 unknown variant 2nd allele PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/., +?/? 4 6 c.584A>G r.(?) p.(Asn195Ser) - likely pathogenic, pathogenic (recessive) g.125912837T>C g.126577145T>C - - ALDH7A1_000002 - PubMed: Coughlin 2019, PubMed: Della Mina et al 2014 - - Germline yes - - - - Lab Zuffardi, Curtis Coughlin II
+/. 1 - c.586T>A r.(?) p.(Phe196Ile) - pathogenic (recessive) g.125912835A>T g.126577143A>T - - ALDH7A1_000127 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 8 - c.589C>T r.(?) p.(Pro197Ser) - pathogenic, pathogenic (recessive) g.125912832G>A g.126577140G>A ALDH7A1(NM_001182.5):c.589C>T (p.P197S) - ALDH7A1_000026 unknown variant 2nd allele, VKGL data sharing initiative Nederland PubMed: Coughlin 2019 - - CLASSIFICATION record, Germline - - - - - Curtis Coughlin II, VKGL-NL_Utrecht
+/. 2 - c.596C>T r.(?) p.Ala199Val - NA g.125912825G>A g.126577133G>A - - ALDH7A1_000126 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Coulter-Mackie 2012, PubMed: Mills 2006 - - In vitro (cloned) - - - - - Curtis Coughlin II
+/. 3 - c.605G>A r.(?) p.(Gly202Asp) - pathogenic (recessive) g.125912816C>T g.126577124C>T - - ALDH7A1_000125 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.607T>G r.(?) p.Trp203Gly - NA g.125912814A>C g.126577122A>C - - ALDH7A1_000124 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Coulter-Mackie 2012 - - In vitro (cloned) - - - - - Curtis Coughlin II
-?/. 1 - c.615C>T r.(?) p.(Asn205=) - likely benign g.125912806G>A - ALDH7A1(NM_001182.5):c.615C>T (p.N205=) - ALDH7A1_000182 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
?/. 1 - c.622G>A r.(?) p.(Ala208Thr) - VUS g.125912799C>T - ALDH7A1(NM_001182.5):c.622G>A (p.(Ala208Thr)) - ALDH7A1_000190 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
?/. 1 - c.632G>A r.(?) p.(Cys211Tyr) - VUS g.125912789C>T - - - ALDH7A1_000179 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Nijmegen
?/. 1 - c.632G>T r.(?) p.(Cys211Phe) - VUS g.125912789C>A g.126577097C>A ALDH7A1(NM_001182.4):c.632G>T (p.C211F) - ALDH7A1_000025 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
+/. 3 - c.651-3_651-1del r.spl p.? - pathogenic (recessive) g.125911157_125911159del g.126575465_126575467del c.651-3_651-1delAAG - ALDH7A1_000122 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 3 6i_7i c.(650+1_651-1)_(695+1_696-1)del r.spl p.? - pathogenic (recessive) g.(125906552_125911111)-(125911157_125912770)del - - - ALDH7A1_000054 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/., +?/. 5 6 c.664A>G r.(?) p.(Thr222Ala) ACMG likely pathogenic, pathogenic (recessive) g.125911143T>C g.126575451T>C - - ALDH7A1_000052 - PubMed: Coughlin 2019, PubMed: Tumienė 2018 - - Germline - - - - - Johan den Dunnen, Curtis Coughlin II
-/. 2 - c.675C>T r.(?) p.(Leu225=) - benign g.125911132G>A g.126575440G>A ALDH7A1(NM_001182.5):c.675C>T (p.L225=) - ALDH7A1_000024 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht, VKGL-NL_AMC
-?/. 1 - c.695+10T>C r.(=) p.(=) - likely benign g.125911102A>G - ALDH7A1(NM_001182.5):c.695+10T>C - ALDH7A1_000186 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
+/. 2 - c.696-502G>C r.spl p.(=) - pathogenic (recessive) g.125907053C>G g.126571361C>G - - ALDH7A1_000121 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.696-1G>T r.spl p.? - pathogenic (recessive) g.125906552C>A g.126570860C>A - - ALDH7A1_000120 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.773+5G>A r.spl p.? - pathogenic (recessive) g.125906469C>T g.126570777C>T - - ALDH7A1_000119 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 3 - c.774-1095_800delinsG r.spl p.? - pathogenic (recessive) g.125904022_125905143delinsC g.126568330_126569451delinsC 774-1095_716delinsG - ALDH7A1_000117 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
-/. 1 - c.774-256C>G r.(=) p.(=) - benign g.125904304G>C g.126568612G>C ALDH7A1(NM_001182.5):c.774-256C>G - ALDH7A1_000023 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
+/. 4 - c.796C>T r.(?) p.(Arg266*) - pathogenic (recessive) g.125904026G>A g.126568334G>A - - ALDH7A1_000118 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/., +?/. 2 - c.821G>A r.(?) p.(Gly274Glu), p.Gly274Glu - NA, pathogenic (recessive) g.125904001C>T g.126568309C>T - - ALDH7A1_000116 expression cloning in E.coli (at 37oC) shows 0.22 alpha‐AASADH activity (nmol NADH/min/mg ATQ) PubMed: Coughlin 2019 - - Germline, In vitro (cloned) - - - - - Curtis Coughlin II
+/. 1 - c.826A>C r.(?) p.(Thr276Pro) - pathogenic (recessive) g.125903996T>G g.126568304T>G - - ALDH7A1_000115 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 18 - c.834G>A r.spl? p.(Val278=) - pathogenic (recessive) g.125903988C>T g.126568296C>T - - ALDH7A1_000114 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
?/. 2 - c.838A>G r.(?) p.(Lys280Glu) - VUS g.125903984T>C g.126568292T>C ALDH7A1(NM_001182.4):c.838A>G (p.K280E), ALDH7A1(NM_001182.5):c.838A>G (p.K280E) - ALDH7A1_000176 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_Groningen
+/. 1 - c.841C>T r.(?) p.(Gln281*) - pathogenic (recessive) g.125903981G>A g.126568289G>A - - ALDH7A1_000113 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 2 - c.848G>A r.(?) p.(Gly283Asp), p.Gly283Asp - NA, pathogenic (recessive) g.125903974C>T g.126568282C>T - - ALDH7A1_000112 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Coughlin 2019, PubMed: Korasick 2017 - - Germline, In vitro (cloned) - - - - - Curtis Coughlin II
+/. 1 - c.871+1G>A r.spl p.? - pathogenic (recessive) g.125903950C>T g.126568258C>T - - ALDH7A1_000111 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
+/. 1 - c.871+5G>A r.spl p.? - pathogenic (recessive) g.125903946C>T g.126568254C>T - - ALDH7A1_000110 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
-/. 1 - c.872-192T>C r.(=) p.(=) - benign g.125897008A>G g.126561316A>G ALDH7A1(NM_001182.5):c.872-192T>C - ALDH7A1_000049 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
-/. 1 - c.872-5T>A r.spl? p.? - benign g.125896821A>T g.126561129A>T ALDH7A1(NM_001182.5):c.872-5T>A - ALDH7A1_000165 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
+/. 1 - c.872G>A r.(?) p.Gly291Glu - NA g.125896816C>T g.126561124C>T - - ALDH7A1_000109 expression cloning in E.coli shows no alpha‐AASADH activity PubMed: Korasick 2017 - - In vitro (cloned) - - - - - Curtis Coughlin II
+/. 1 - c.876_877dup r.(?) p.(Ser293Lysfs*22) - pathogenic (recessive) g.125896811_125896812dup g.126561119_126561120dup c.876_877dupAA - ALDH7A1_000108 - PubMed: Coughlin 2019 - - Germline - - - - - Curtis Coughlin II
Legend   How to query   « First ‹ Prev     1 2     Next › Last »


Screenscraping/webscraping (downloading large amounts of data using scripts) is strictly prohibited.
Use our APIs to retrieve data.