Unique variants in the CLN5 gene

An NCL gene variant database
Information The variants shown are described using the NM_006493.2 transcript reference sequence.

59 entries on 1 page. Showing entries 1 - 59.
Legend   How to query  

Effect     

Reported     

Exon     

AscendingDNA change (cDNA)     

RNA change     

Protein     

Classification method     

Clinical classification     

DNA change (genomic) (hg19)     

DNA change (hg38)     

Published as     

ISCN     

DB-ID     

Variant remarks     

Reference     

ClinVar ID     

dbSNP ID     

Origin     

Segregation     

Frequency     

Re-site     

VIP     

Methylation     

Owner     
+/., -?/., ?/. 4 - c.2T>C r.(?) p.(Met1?) - likely benign, pathogenic (recessive), VUS g.77566088T>C g.76991953T>C CLN5(NM_006493.2):c.2T>C (p.M1?), CLN5(NM_006493.4):c.-146T>C - CLN5_000025 VKGL data sharing initiative Nederland PubMed: Rots 2023 - - CLASSIFICATION record, Germline - - - - - Johan den Dunnen, VKGL-NL_Rotterdam, VKGL-NL_Groningen, VKGL-NL_VUmc
-/. 4 - c.4C>T r.(?) p.(Arg2Cys) - benign g.77566090C>T g.76991955C>T CLN5(NM_006493.2):c.4C>T (p.R2C), CLN5(NM_006493.4):c.-144C>T - CLN5_000019 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_Utrecht, VKGL-NL_Nijmegen, VKGL-NL_VUmc
?/. 1 - c.7C>T r.(?) p.(Arg3Trp) - VUS g.77566093C>T g.76991958C>T CLN5(NM_006493.4):c.-141C>T - CLN5_000001 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
-?/. 1 - c.22G>C r.(?) p.(Gly8Arg) - likely benign g.77566108G>C g.76991973G>C CLN5(NM_006493.2):c.22G>C (p.G8R) - CLN5_000002 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
+/. 1 - c.47_59del r.(?) p.(Gln16ProfsTer30) - pathogenic g.77566133_77566145del - CLN5(NM_006493.2):c.47_59delAGGGGCAAGGCGC (p.Q16Pfs*30) - CLN5_000045 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-?/. 2 - c.49G>C r.(?) p.(Gly17Arg) - likely benign g.77566135G>C g.76992000G>C CLN5(NM_006493.2):c.49G>C (p.G17R), CLN5(NM_006493.4):c.-99G>C - CLN5_000003 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_VUmc
-/., -?/., ?/. 5 - c.61C>T r.(?) p.(Pro21Ser) - benign, likely benign, VUS g.77566147C>T g.76992012C>T CLN5(NM_006493.2):c.61C>T (p.P21S, p.(Pro21Ser)), CLN5(NM_006493.4):c.-87C>T - CLN5_000020 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden, VKGL-NL_Rotterdam, VKGL-NL_Utrecht, VKGL-NL_Nijmegen, VKGL-NL_VUmc
-?/. 1 - c.65G>T r.(?) p.(Arg22Leu) - likely benign g.77566151G>T g.76992016G>T CLN5(NM_006493.4):c.-83G>T - CLN5_000004 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
-/. 2 - c.72A>G r.(?) p.(Gly24=) - benign g.77566158A>G g.76992023A>G CLN5(NM_006493.2):c.72A>G (p.G24=), CLN5(NM_006493.4):c.-76A>G - CLN5_000005 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_VUmc
-?/. 1 - c.74T>C r.(?) p.(Leu25Pro) - likely benign g.77566160T>C - CLN5(NM_006493.2):c.74T>C (p.L25P) - CLN5_000054 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-?/. 1 - c.117G>T r.(?) p.(Ser39=) - likely benign g.77566203G>T g.76992068G>T CLN5(NM_006493.4):c.-31G>T - CLN5_000006 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
-/., -?/. 2 - c.152C>T r.(?) p.(Ala51Val) - benign, likely benign g.77566238C>T g.76992103C>T CLN5(NM_006493.2):c.152C>T (p.A51V), CLN5(NM_006493.4):c.5C>T (p.A2V) - CLN5_000026 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_VUmc
?/. 1 - c.178G>T r.(?) p.(Ala60Ser) - VUS g.77566264G>T - CLN5(NM_006493.2):c.178G>T (p.A60S) - CLN5_000046 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-?/. 1 - c.200_205dup r.(?) p.(Gly67_Ala68dup) - likely benign g.77566286_77566291dup g.76992151_76992156dup CLN5(NM_006493.4):c.53_58dupGCGCGG (p.G18_A19dup) - CLN5_000027 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
?/. 1 - c.208C>T r.(?) p.(Arg70Trp) - VUS g.77566294C>T - CLN5(NM_006493.2):c.208C>T (p.R70W) - CLN5_000028 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-?/. 3 - c.223T>C r.(?) p.(Trp75Arg) - likely benign g.77566309T>C g.76992174T>C CLN5(NM_006493.2):c.223T>C (p.W75R), CLN5(NM_006493.4):c.76T>C (p.W26R) - CLN5_000008 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_Groningen, VKGL-NL_VUmc
-/. 2 - c.234C>G r.(?) p.(Ala78=) - benign g.77566320C>G g.76992185C>G CLN5(NM_006493.2):c.234C>G (p.A78=), CLN5(NM_006493.4):c.87C>G (p.A29=) - CLN5_000029 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht, VKGL-NL_VUmc
+?/. 2 1 c.270G>A r.(?) p.(Trp90*) ACMG likely pathogenic g.77566356G>A - - - CLN5_000044 - - - - Germline - - - - - Corina-Marcela Rus
-?/. 1 - c.275G>A r.(?) p.(Arg92Gln) - likely benign g.77566361G>A g.76992226G>A CLN5(NM_006493.2):c.275G>A (p.R92Q) - CLN5_000038 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
+?/. 1 - c.320+5G>A r.[320_321ins[gugaa;320+6_320+581],160_320del] p.[Arg108*,Val54Alafs*3] - pathogenic (recessive) g.77566411G>A g.76992276G>A - - CLN5_000057 cryptic splice donor; RNA analysis suggests alternative transcription initiation PubMed: Bournazos 2022 - - Germline - - - - - Johan den Dunnen
-/. 1 - c.320+8C>T r.(=) p.(=) - benign g.77566414C>T g.76992279C>T CLN5(NM_001366624.2):c.173+8C>T - CLN5_000009 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
-/. 4 - c.320+18C>T r.(=) p.(=) - benign g.77566424C>T g.76992289C>T CLN5(NM_006493.2):c.320+18C>T, CLN5(NM_006493.4):c.173+18C>T - CLN5_000010 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_Utrecht, VKGL-NL_Nijmegen, VKGL-NL_VUmc
-?/. 1 - c.321-168A>G r.(=) p.(=) - likely benign g.77569030A>G g.76994895A>G CLN5(NM_006493.2):c.321-168A>G - CLN5_000011 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
?/. 1 - c.335G>A r.(?) p.(Arg112His) - VUS g.77569212G>A g.76995077G>A - - CLN5_000035 2 heterozygous, no homozygous; Clinindb (India) PubMed: Narang 2020, Journal: Narang 2020 - rs104894386 Germline - 2/2790 individuals - - - Mohammed Faruq
?/. 1 - c.335G>C r.(?) p.(Arg112Pro) - VUS g.77569212G>C g.76995077G>C - - CLN5_000060 - PubMed: Fernandez-Marmiesse 2014 - - Germline - - - - - Johan den Dunnen
+?/. 1 2 c.363del r.(?) p.(Lys122Serfs*41) ACMG likely pathogenic g.77569240del - - - CLN5_000021 - - - - Germline - - - - - Corina-Marcela Rus
+?/. 1 2 c.439C>T r.(?) p.(Gln147*) ACMG likely pathogenic g.77569316C>T - - - CLN5_000043 - - - - Germline - - - - - Corina-Marcela Rus
?/. 1 - c.470A>C r.(?) p.(Asp157Ala) - VUS g.77569347A>C g.76995212A>C CLN5 c.470A>C p.Asp157Ala - CLN5_000056 heterozygous; single variant in a recessive gene PubMed: Craiu 2015 - - Germline yes - - - - LOVD
-/., -?/. 4 - c.528T>G r.(=), r.(?) p.(=), p.(Thr176=) - benign, likely benign g.77570078T>G g.76995943T>G CLN5(NM_001366624.2):c.381T>G (p.T127=), CLN5(NM_006493.2):c.528T>G (p.T176=) - CLN5_000012 101 heterozygous; Clinindb (India), 3 homozygous; Clinindb (India), 1 more item PubMed: Narang 2020, Journal: Narang 2020 - rs34481987 CLASSIFICATION record, Germline - 101/2793 individuals, 3/2793 individuals - - - VKGL-NL_Utrecht, VKGL-NL_VUmc, Mohammed Faruq
+?/. 1 - c.545T>G r.(?) p.(Met182Arg) - likely pathogenic g.77570095T>G g.76995960T>G c.545T>G, p.(Met182Arg) - CLN5_000051 homozygous PubMed: Jilani 2019 - - Germline ? - - - - LOVD
+?/. 1 - c.578G>A r.(?) p.(Cys193Tyr) - likely pathogenic g.77570128G>A g.76995993G>A - - CLN5_000022 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Nijmegen
+/., +?/. 4 3 c.595C>T r.(?) p.(Arg199Ter) - likely pathogenic, pathogenic g.77570145C>T g.76996010C>T CLN5(NM_006493.2):c.595C>T (p.R199*), CLN5(NM_006493.4):c.448C>T (p.R150*) - CLN5_000030 VKGL data sharing initiative Nederland PubMed: Ganapathy 2019 - - CLASSIFICATION record, Germline - - - - - Johan den Dunnen, VKGL-NL_Rotterdam, VKGL-NL_Groningen, VKGL-NL_VUmc
-?/., ?/. 4 - c.606G>A r.(?) p.(Met202Ile) - likely benign, VUS g.77570156G>A g.76996021G>A CLN5(NM_006493.2):c.606G>A (p.M202I), CLN5(NM_006493.4):c.459G>A (p.M153I) - CLN5_000013 VKGL data sharing initiative Nederland PubMed: Fernandez-Marmiesse 2014 - - CLASSIFICATION record, Germline - - - - - Johan den Dunnen, VKGL-NL_Rotterdam, VKGL-NL_VUmc
?/. 1 - c.634G>T r.(?) p.(Ala212Ser) - VUS g.77570184G>T - CLN5(NM_006493.4):c.487G>T (p.(Ala163Ser)) - CLN5_000059 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
+?/. 1 3 c.657_661dup r.(?) p.(Asp221Valfs*12) ACMG likely pathogenic g.77570207_77570211dup - - - CLN5_000042 - - - - Germline - - - - - Corina-Marcela Rus
?/. 1 - c.691G>A r.(?) p.(Val231Ile) - VUS g.77570241G>A g.76996106G>A CLN5(NM_006493.2):c.691G>A (p.V231I) - CLN5_000031 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
+?/. 1 3i c.712+1G>A r.spl? p.? ACMG likely pathogenic g.77570263G>A - - - CLN5_000041 - - - - Germline - - - - - Corina-Marcela Rus
-?/. 1 - c.712+17T>C r.(=) p.(=) - likely benign g.77570279T>C - CLN5(NM_006493.4):c.565+17T>C - CLN5_000047 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
-/. 1 - c.712+39C>A r.(=) p.(=) - benign g.77570301C>A g.76996166C>A CLN5(NM_006493.2):c.712+39C>A - CLN5_000014 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
-?/. 1 - c.712+40A>C r.(=) p.(=) - likely benign g.77570302A>C g.76996167A>C CLN5(NM_006493.2):c.712+40A>C - CLN5_000015 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Utrecht
-/., -?/., ?/. 5 - c.726C>A r.(?) p.(Asn242Lys) - benign, likely benign, VUS g.77574606C>A g.77000471C>A CLN5(NM_006493.2):c.726C>A (p.N242K), CLN5(NM_006493.4):c.579C>A (p.N193K) - CLN5_000016 60 heterozygous, no homozygous; Clinindb (India), VKGL data sharing initiative Nederland PubMed: Fernandez-Marmiesse 2014, PubMed: Narang 2020, Journal: Narang 2020 - rs138611001 CLASSIFICATION record, Germline - 60/2795 individuals - - - Johan den Dunnen, VKGL-NL_Groningen, VKGL-NL_Utrecht, VKGL-NL_VUmc, Mohammed Faruq
+?/. 1 4 c.746_747insCA r.(?) p.(Lys249AsnfsTer16) - likely pathogenic g.77574626_77574627insCA g.77000491_77000492insCA - - CLN5_000050 - PubMed: Ganapathy 2019 - - Germline - - - - - Johan den Dunnen
-?/. 1 - c.765A>C r.(?) p.(Gly255=) - likely benign g.77574645A>C g.77000510A>C CLN5(NM_006493.2):c.765A>C (p.G255=) - CLN5_000032 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
+?/. 1 4 c.822G>A r.(?) p.(Trp274*) ACMG likely pathogenic g.77574702G>A - - - CLN5_000040 - - - - Germline - - - - - Corina-Marcela Rus
?/. 1 - c.830C>T r.(?) p.(Ser277Phe) - VUS g.77574710C>T g.77000575C>T CLN5(NM_006493.4):c.683C>T (p.S228F) - CLN5_000039 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
+/. 2 - c.835G>A r.(?) p.(Asp279Asn) - pathogenic, pathogenic (recessive) g.77574715G>A g.77000580G>A - - CLN5_000036 1 heterozygous, no homozygous; Clinindb (India) PubMed: Fernandez-Marmiesse 2014, PubMed: Narang 2020, Journal: Narang 2020 - rs28940280 Germline - 1/2795 individuals - - - Johan den Dunnen, Mohammed Faruq
-?/. 1 - c.871T>C r.(?) p.(Leu291=) - likely benign g.77574751T>C - CLN5(NM_006493.2):c.871T>C (p.L291=) - CLN5_000055 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
+?/. 1 - c.1068_1069del r.(?) p.(Leu358Alafs*4) - likely pathogenic g.77574951_77574952del g.77000816_77000817del 1 more item - CLN5_000052 heterozygous PubMed: Surl 2020 - - Germline yes - - - - LOVD
-?/. 1 - c.1072T>C r.(?) p.(Leu358=) - likely benign g.77574952T>C g.77000817T>C CLN5(NM_006493.4):c.925T>C (p.L309=) - CLN5_000034 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
+?/. 1 - c.1100_1103del r.(?) p.(Lys368Serfs*15) - likely pathogenic g.77574983_77574986del g.77000848_77000851del 1 more item - CLN5_000053 heterozygous PubMed: Surl 2020 - - Germline yes - - - - LOVD
-/. 5 - c.1103A>G r.(?) p.(Lys368Arg) - benign g.77574983A>G g.77000848A>G CLN5(NM_006493.2):c.1103A>G (p.K368R), CLN5(NM_006493.4):c.956A>G (p.K319R) - CLN5_000023 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam, VKGL-NL_Groningen, VKGL-NL_Utrecht, VKGL-NL_Nijmegen, VKGL-NL_VUmc
+/. 1 - c.1137G>A r.(?) p.(Trp379Ter) ACMG pathogenic (recessive) g.77575017G>A g.77000882G>A - - CLN5_000058 ACMG PM2, PVS1_STRONG, PP5_STRONG; no variant 2nd chromosome PubMed: Weisschuh 2024 - - Germline - - - - - Johan den Dunnen
?/. 1 - c.1149G>T r.(?) p.(Met383Ile) - VUS g.77575029G>T g.77000894G>T CLN5(NM_006493.2):c.1149G>T (p.M383I) - CLN5_000017 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
?/. 1 - c.1166A>C r.(?) p.(Lys389Thr) - VUS g.77575046A>C g.77000911A>C CLN5(NM_006493.2):c.1166A>C (p.K389T) - CLN5_000024 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-?/. 1 - c.1173A>G r.(?) p.(Thr391=) - likely benign g.77575053A>G - CLN5(NM_006493.2):c.1173A>G (p.T391=) - CLN5_000048 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-?/. 1 - c.1185C>T r.(?) p.(Ile395=) - likely benign g.77575065C>T g.77000930C>T CLN5(NM_006493.2):c.1185C>T (p.I395=) - CLN5_000033 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-?/. 1 - c.1188T>C r.(?) p.(Pro396=) - likely benign g.77575068T>C g.77000933T>C CLN5(NM_006493.4):c.1041T>C (p.P347=) - CLN5_000018 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_VUmc
?/. 2 - c.1192C>T r.(?) p.(Pro398Ser) - VUS g.77575072C>T g.77000937C>T CLN5(NM_006493.2):c.1192C>T (p.(Pro349Ser)) - CLN5_000037 1 heterozygous, no homozygous; Clinindb (India), VKGL data sharing initiative Nederland PubMed: Narang 2020, Journal: Narang 2020 - rs41287036 CLASSIFICATION record, Germline - 1/2794 individuals - - - VKGL-NL_Leiden, Mohammed Faruq
?/. 1 - c.1195_1198dup r.(?) p.(Arg400Asnfs*131) - VUS g.77575075_77575078dup - CLN5(NM_006493.2):c.1195_1198dupATCA (p.R400Nfs*131) - CLN5_000049 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
Legend   How to query  


Screenscraping/webscraping (downloading large amounts of data using scripts) is strictly prohibited.
Use our APIs to retrieve data.