Legend
Please note that a short description of a certain column can be displayed when you move your mouse cursor over the column's header and hold it still. Below, a more detailed description is shown per column.
Effect : The variant's effect on the function of the gene/protein, displayed in the format 'R/C'. R is the value reported by the source (publication, submitter) and this classification may vary between records. C is the value concluded by the curator. Note that in some database the curator uses Summary records to give details on the classification of the variant.Values used: '+' indicating the variant affects function, '+?' probably affects function, '-' does not affect function, '-?' probably does not affect function, '?' effect unknown, '.' effect was not classified.
Exon : number of exon/intron containing variant; 2 = exon 2, 12i = intron 12, 2i_7i = from intron 2 to intron 7, 8i_9 = intron 8/exon 9 boundary, _1 = 5' to exon 1, 18_ = 3' of exon 18, _1_18_ = encompassing the entire 18-exon gene
DNA change (cDNA) : description of variant at DNA level, based on a coding DNA reference sequence (following HGVS recommendations); e.g. c.123C>T, c.123_145del, c.123_126dup. For deletions/duplications extending beyond the reference transcript resp. {0}/{2} is used to replace del/dup. Extent of the deletion/duplication should be specified using the genomic description (g.). "-" indicates the variant described on genomic level does not affect the coding DNA reference sequence.
RNA change : description of variant at RNA level (following HGVS recommendations).
r.123c>u
r.? = unknown
r.(?) = RNA not analysed but probably transcribed copy of DNA variant
r.spl? = RNA not analysed but variant probably affects splicing
r.(spl?) = RNA not analysed but variant may affect splicing
r.0? = change expected to abolish transcription
Protein : description of variant at protein level (following HGVS recommendations).
p.(Arg345Pro) = change predicted from DNA (RNA not analysed)
p.Arg345Pro = change derived from RNA analysis
p.? = unknown effect
p.0? = probably no protein produced
Allele : On which allele is the variant located? Does not necessarily imply inheritance! 'Paternal' (confirmed or inferred), 'Maternal' (confirmed or inferred), 'Parent #1' or #2 for compound heterozygosity without having screened the parents, 'Unknown' for heterozygosity without having screened the parents, 'Both' for homozygozity.
Classification method : The method used for the clinical classification of this variant.
All options:
ACMG
ACGS
EAHAD-CFDB
ENIGMA
IARC
InSiGHT
kConFab
other
Clinical classification : Clinical classification of variant, preferably based on standardised criteria (e.g. ACMG), directed on the clinical consequences as published/submitted, indicated using an enriched system including inheritance: e.g. pathogenic, pathogenic (dominant), pathogenic (recessive), pathogenic (!), pathogenic (maternal), pathogenic (paternal). Standard inheritance is covered by dominant/recessive, imprinting by maternal/paternal. A '!' warns for exceptional circumstances to be explained in the 'Remarks' field (low penetrance, variants pathogenic in heterozygous state only, hypomorphic/hypermorphic variants, protective variants, etc.). Non-disease consequences (e.g. drug metabolism (pharmacogenetics), risk factor, blood group, tasting bitter) are indicated using additions to the benign classification; benign (dominant), benign (recessive), benign (!), etc. The value 'association' is used for variants associated with a phenotype and 'NA' for variants from in vitro/in silico records. NOTE: classification may differ from the opinion of the curator as given in a variant SUMMARY-record or the 'Functional effect concluded'). NOTE: pathogenic/likely pathogenic should go together with "variant (probably) affects function" In ClassFunctional.
All options:
pathogenic
pathogenic (dominant)
pathogenic (recessive)
pathogenic (!)
pathogenic (maternal)
pathogenic (paternal)
likely pathogenic
likely pathogenic (dominant)
likely pathogenic (recessive)
likely pathogenic (!)
likely pathogenic (maternal)
likely pathogenic (paternal)
VUS
VUS (!)
likely benign
likely benign (dominant)
likely benign (recessive)
likely benign (!)
likely benign (maternal)
likely benign (paternal)
benign
benign (dominant)
benign (recessive)
benign (!)
benign (maternal)
benign (paternal)
conflicting
association
NA
DNA change (genomic) (hg19) : HGVS description of variant at DNA level, based on the genomic (chromosomal) DNA reference sequence; e.g. g.12345678C>T, g.12345679del, g.12345678_12345890dup
DNA change (hg38) : HGVS description of variant at DNA level, based on the hg38 genomic (chromosomal) eference sequence; e.g. g.12345678C>T, g.12345679del, g.12345678_12345890dup
Published as : listed only when different from "DNA change"; variant as reported originally (e.g. 521delT). Variants seen in animal models, tested in vitro, predicted from RNA analysis, etc. are described between brackets like c.(456C>G)
ISCN : description of the variant according to ISCN nomenclature
DB-ID : database ID of variant, grouping multiple observations of the same variant together, starting with the HGNC gene symbol, followed by an underscore (_) and a six digit number (e.g. DMD_012345). _000000 is used for variants where DNA was not analysed (change predicted from RNA analysis), variants seen in animal models or variants not seen in humans but functionally tested in vitro
Variant remarks : remarks regarding variant described, e.g. germline mosaicism in mother, 345 kb deletion, muscle RNA analysed, not in 200 control chromosomes tested, on founder haplotype, etc.
Reference : publication describing the variant submitted, incl. links to OMIM, PubMed or other source, e.g. "den Dunnen ASHG2003 P2346"
ClinVar ID : ID of variant in ClinVar database
dbSNP ID : the dbSNP ID
Origin : Origin of variant/record: Germline = in all cells, De novo = in all cells, but not in either parent, Germline/De novo (untested) = in all cells, parents not tested (use only when De novo is likely, e.g. isolated/sporadic cases with dominant disease), Somatic = present in a subset of cells, but not in either parent, Uniparental disomy = from parental disomy (maternal or paternal), CLASSIFICATION record = submitter only sharing variant classification (note another report may share Individual data), SUMMARY record = master summary record from curator (may link to another database), In vitro (cloned) = data resulting from in vitro functional assays, animal model = data from animal model, Artefact = false positive variant call, DUPLICATE record = variant already described on another chromosome (e.g. unbalanced translocation, duplicating transposition, 2nd fusion transcript, etc.)
All options:
Germline
De novo
Germline/De novo (untested)
Somatic
Uniparental disomy
Uniparental disomy, maternal allele
Uniparental disomy, paternal allele
CLASSIFICATION record
SUMMARY record
In vitro (cloned)
In silico
animal model
Artefact
DUPLICATE record
Unknown
Not applicable
Segregation : Indicates whether the variant segregates with the phenotype (yes), does not segregate with the phenotype (no) or segregation is unknown (?)
All options:
? = unknown
yes = segregates with phenotype
no = does not segregate with phenotype
- = not applicable
Frequency : frequency in which the variant was found; e.g 5/760 chromosomes (in 5 of 760 chromosomes tested), 1/33 patients (in 1 of 33 patients analysed in study), 0.05 controls (in 5% of control cases tested)
Re-site : restriction enzyme recognition site created (+) or destroyed (-); e.g. BglII+;BamHI-
VIP : variant VIP-status was requested for matchmaking - need collaboration(s) to crack the case - please contact the submitter/curator.
NOTE: to get VIP status ask the curator.
Methylation : result of methylation test; GOM (gain of methylation), LOM (loss of methylation), 30% (30% methylated). NOTE: when several tests were done mention the method as well (e.g. MS-PCR 75%)
Effect
Exon
DNA change (cDNA)
RNA change
Protein
Classification method
Clinical classification
DNA change (genomic) (hg19)
DNA change (hg38)
Published as
ISCN
DB-ID
Variant remarks
Reference
ClinVar ID
dbSNP ID
Origin
Segregation
Frequency
Re-site
VIP
Methylation
Owner
?/.
-
c.-36437G>T
r.(?)
p.(=)
-
VUS
g.209025634C>A
-
CRYGA(NM_014617.4):c.419G>T (p.R140L)
-
C2orf80_000001
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_VUmc
?/.
-
c.-21419T>C
r.(?)
p.(=)
-
VUS
g.209010616A>G
g.208145892A>G
CRYGB(NM_005210.3):c.134T>C (p.(Ile45Thr))
-
CRYGB_000008
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
?/.
-
c.-21374G>A
r.(?)
p.(=)
-
VUS
g.209010571C>T
g.208145847C>T
CRYGB(NM_005210.3):c.179G>A (p.R60H)
-
CRYGB_000021
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
?/.
-
c.-21372G>A
r.(?)
p.(=)
-
VUS
g.209010569C>T
g.208145845C>T
CRYGB(NM_005210.3):c.181G>A (p.G61R)
-
CRYGB_000020
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
-/.
-
c.-21361T>C
r.(?)
p.(=)
-
benign
g.209010558A>G
g.208145834A>G
-
-
CRYGB_000002
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
-?/.
-
c.-21333G>A
r.(?)
p.(=)
-
likely benign
g.209010530C>T
g.208145806C>T
CRYGB(NM_005210.3):c.220G>A (p.D74N)
-
CRYGB_000019
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
-?/.
-
c.-21322C>T
r.(?)
p.(=)
-
likely benign
g.209010519G>A
-
CRYGB(NM_005210.3):c.231C>T (p.R77=)
-
CRYGB_000024
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
-?/.
-
c.-21301G>A
r.(?)
p.(=)
-
likely benign
g.209010498C>T
g.208145774C>T
-
-
CRYGB_000018
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
-?/.
-
c.-18369C>T
r.(?)
p.(=)
-
likely benign
g.209007566G>A
g.208142842G>A
CRYGB(NM_005210.3):c.324C>T (p.D108=)
-
CRYGB_000007
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
?/.
-
c.-18295T>G
r.(?)
p.(=)
-
VUS
g.209007492A>C
-
CRYGB(NM_005210.3):c.398T>G (p.I133S)
-
CRYGB_000027
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
-?/.
-
c.-18166G>A
r.(?)
p.(=)
-
likely benign
g.209007363C>T
-
CRYGB(NM_005210.3):c.527G>A (p.*176=)
-
CRYGB_000022
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+?/.
-
c.-5319A>G
r.(?)
p.(=)
-
likely pathogenic
g.208994516T>C
g.208129792T>C
CRYGC(NM_020989.3):c.1A>G (p.M1?)
-
CRYGC_000020
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+?/.
-
c.-5159_-5157del
r.(?)
p.(=)
-
likely pathogenic
g.208994354_208994356del
g.208129630_208129632del
CRYGC(NM_020989.3):c.61_63delACT (p.T21del), CRYGC(NM_020989.4):c.61_63del (p.(Thr21del))
-
CRYGB_000017
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+?/.
-
c.-5159_-5157del
r.(?)
p.(=)
-
likely pathogenic
g.208994354_208994356del
-
CRYGC(NM_020989.3):c.61_63delACT (p.T21del), CRYGC(NM_020989.4):c.61_63del (p.(Thr21del))
-
CRYGB_000017
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
+?/.
-
c.-5159_-5157del
r.(?)
p.(=)
-
likely pathogenic
g.208994354_208994356del
-
CRYGC(NM_020989.3):c.61_63delACT (p.T21del), CRYGC(NM_020989.4):c.61_63del (p.(Thr21del))
-
CRYGB_000017
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
-?/.
-
c.-5125G>A
r.(?)
p.(=)
-
likely benign
g.208994322C>T
-
CRYGC(NM_020989.4):c.95G>A (p.(Arg32His))
-
CRYGB_000037
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
-/.
-
c.-5100C>T
r.(?)
p.(=)
-
benign
g.208994297G>A
g.208129573G>A
CRYGC(NM_020989.3):c.120C>T (p.S40=)
-
CRYGC_000019
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
?/.
-
c.-5083A>G
r.(?)
p.(=)
-
VUS
g.208994280T>C
-
CRYGC(NM_020989.4):c.137A>G (p.Y46C)
-
CRYGB_000029
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_VUmc
-?/.
-
c.-5068A>G
r.(?)
p.(=)
-
likely benign
g.208994265T>C
g.208129541T>C
CRYGC(NM_020989.3):c.152A>G (p.(Tyr51Cys))
-
CRYGC_000018
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
+/.
-
c.-5066_-5057del
r.(?)
p.(=)
-
pathogenic
g.208994256_208994265del
g.208129532_208129541del
-
-
CRYGC_000022
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
-?/.
-
c.-5056A>G
r.(?)
p.(=)
-
likely benign
g.208994253T>C
g.208129529T>C
CRYGC(NM_020989.4):c.164A>G (p.(Gln55Arg))
-
CRYGB_000016
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
-?/.
-
c.-5044G>A
r.(?)
p.(=)
-
likely benign
g.208994241C>T
g.208129517C>T
CRYGC(NM_020989.3):c.176G>A (p.(Arg59Gln))
-
CRYGB_000015
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
?/.
-
c.-5042C>T
r.(?)
p.(=)
-
VUS
g.208994239G>A
-
CRYGC(NM_020989.4):c.178C>T (p.R60*)
-
CRYGB_000028
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Groningen
+?/.
-
c.-5042C>T
r.(?)
p.(=)
-
likely pathogenic
g.208994239G>A
-
CRYGC(NM_020989.4):c.178C>T (p.R60*)
-
CRYGB_000028
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
?/.
-
c.-5000G>A
r.(?)
p.(=)
-
VUS
g.208994197C>T
-
CRYGC(NM_020989.3):c.220G>A (p.(Asp74Asn))
-
CRYGB_000034
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
?/.
-
c.-4990G>A
r.(?)
p.(=)
-
VUS
g.208994187C>T
-
-
-
CRYGB_000025
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
-?/.
-
c.-3938G>A
r.(?)
p.(=)
-
likely benign
g.208993135C>T
g.208128411C>T
CRYGC(NM_020989.3):c.317G>A (p.S106N)
-
CRYGC_000016
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
-?/.
-
c.-3921A>T
r.(?)
p.(=)
-
likely benign
g.208993118T>A
-
CRYGC(NM_020989.3):c.334A>T (p.(Ile112Phe))
-
CRYGB_000033
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
+?/.
-
c.-3870G>T
r.(?)
p.(=)
-
likely pathogenic
g.208993067C>A
-
CRYGC(NM_020989.4):c.385G>T (p.G129C)
-
CRYGC_000008
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_VUmc
-?/.
-
c.-3853C>T
r.(?)
p.(=)
-
likely benign
g.208993050G>A
-
CRYGC(NM_020989.3):c.402C>T (p.Y134=)
-
CRYGB_000026
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
?/.
-
c.-3830G>A
r.(?)
p.(=)
-
VUS
g.208993027C>T
-
CRYGC(NM_020989.3):c.425G>A (p.R142Q)
-
CRYGB_000023
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+/.
-
c.-3785G>A
r.(?)
p.(=)
-
pathogenic
g.208992982C>T
g.208128258C>T
CRYGC(NM_020989.3):c.470G>A (p.W157*)
-
CRYGC_000006
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
?/.
-
c.-3782G>A
r.(?)
p.(=)
-
VUS
g.208992979C>T
g.208128255C>T
CRYGC(NM_020989.3):c.473G>A (p.G158E)
-
CRYGC_000015
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
?/.
-
c.-3758C>G
r.(?)
p.(=)
-
VUS
g.208992955G>C
g.208128231G>C
-
-
CRYGC_000021
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
-/.
_1
c.?
r.?
p.?
-
benign
g.?
-
promoter -16_37del
-
SNRNP200_000007
not in 340 control chromosomes
PubMed: Cao 2018
-
-
Germline
-
1/34 chromosomes cases CTRCT
-
-
-
Johan den Dunnen
+?/.
-
c.7A>G
r.(?)
p.(Lys3Glu)
ACMG
likely pathogenic (dominant)
g.208989191T>C
g.208124467T>C
-
-
CRYGD_000054
ACMG PM2_suping, PP1_Strong, PP3, PP4
PubMed: Wang 2024
-
-
Germline
-
-
-
-
-
Johan den Dunnen
-?/.
-
c.9+10G>C
r.(=)
p.(=)
-
likely benign
g.208989179C>G
-
CRYGD(NM_006891.4):c.9+10G>C
-
CRYGB_000031
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
-?/.
-
c.10-7C>G
r.(=)
p.(=)
-
likely benign
g.208989085G>C
g.208124361G>C
CRYGD(NM_006891.3):c.10-7C>G (p.(=))
-
CRYGB_000013
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Leiden
+?/.
-
c.19T>C
r.(?)
p.(Tyr7His)
-
likely pathogenic
g.208989069A>G
g.208124345A>G
-
-
CRYGD_000036
-
PubMed: Huang 2015
-
-
Germline
-
-
-
-
-
LOVD
?/.
2
c.29G>T
r.(?)
p.(Arg10Leu)
-
VUS
g.208989059C>A
g.208124335C>A
-
-
CRYGD_000051
-
PubMed: Liu 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.43C>A
r.(?)
p.(Arg15Ser)
-
pathogenic
g.208989045G>T
g.208124321G>T
-
-
CRYGD_000012
mapped by linkage; not in 206 control chromosomes
PubMed: Zhang 2009
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.43C>A
r.(?)
p.(Arg15Ser)
-
pathogenic (dominant)
g.208989045G>T
g.208124321G>T
-
-
CRYGD_000012
-
PubMed: Zhai 2017
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.43C>T
r.(?)
p.(Arg15Cys)
-
pathogenic
g.208989045G>A
g.208124321G>A
C>T
-
CRYGD_000001
mapped by linkage, not in 400 control chromosomes
PubMed: Stephan 1999 , OMIM:var0001
-
rs121909595
Germline
-
-
HaeIII-
-
-
Johan den Dunnen
+/.
2
c.43C>T
r.(?)
p.(Arg15Cys)
-
pathogenic
g.208989045G>A
g.208124321G>A
C34T (R14C)
-
CRYGD_000001
mapped by linkage; not in 200 control chromosomes
PubMed: Gu 2006
-
rs121909595
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.43C>T
r.(?)
p.(Arg15Cys)
-
pathogenic (dominant)
g.208989045G>A
g.208124321G>A
-
-
CRYGD_000001
-
PubMed: Ma 2018
-
-
Germline
yes
-
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
T51C
-
CRYGD_000007
not seggregating with disease
PubMed: Plotnikova 2007
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
Y17Y
-
CRYGD_000007
7/11 families tested
PubMed: Santana 2009
-
rs2242074
Germline
-
07/11/15
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
Y17Y
-
CRYGD_000007
-
PubMed: Santhiya 2004
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
Y17Y
-
CRYGD_000007
-
PubMed: Santana 2009
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
Y17Y
-
CRYGD_000007
variant in family
PubMed: Santana 2009
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
Y17Y
-
CRYGD_000007
-
PubMed: Santhiya 2004
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
Y17Y
-
CRYGD_000007
-
PubMed: Santhiya 2004
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
2
c.51T>C
r.(?)
p.(=)
-
benign
g.208989037A>G
g.208124313A>G
Y17Y
-
CRYGD_000007
-
PubMed: Santhiya 2004
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
-
c.51T>C
r.(?)
p.(Tyr17=)
-
benign
g.208989037A>G
g.208124313A>G
CRYGD(NM_006891.4):c.51T>C (p.Y17=), LOC100507443(NR_038437.1):n.97+5088A>G
-
CRYGD_000007
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Groningen
-/.
-
c.51T>C
r.(?)
p.(Tyr17=)
-
benign
g.208989037A>G
g.208124313A>G
CRYGD(NM_006891.4):c.51T>C (p.Y17=), LOC100507443(NR_038437.1):n.97+5088A>G
-
CRYGD_000007
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Nijmegen
-?/.
-
c.51T>C
r.(?)
p.(Tyr17=)
-
likely benign
g.208989037A>G
g.208124313A>G
-
-
CRYGD_000007
-
PubMed: Li 2019
-
rs2242074
Germline
-
-
-
-
-
Johan den Dunnen
-/.
-
c.51T>C
r.(=)
p.(Tyr17=)
-
benign
g.208989037A>G
g.208124313A>G
T51C
-
CRYGD_000007
-
PubMed: Plotnikova 2007
-
-
Germline
no
-
-
-
-
Johan den Dunnen
+?/.
-
c.51T>G
r.(?)
p.(Tyr17Ter)
-
VUS
g.208989037A>C
g.208124313A>C
-
-
CRYGD_000046
hypotesized nonsense mediated mRNA decay preventing protein production
PubMed: Reis 2013
-
-
Germline
no
-
-
-
-
Johan den Dunnen
-?/.
-
c.63C>T
r.(?)
p.(Ser21=)
-
likely benign
g.208989025G>A
g.208124301G>A
CRYGD(NM_006891.3):c.63C>T (p.S21=)
-
CRYGD_000033
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic
g.208989018G>T
g.208124294G>T
P23T
-
CRYGD_000002
-
PubMed: Santhiya 2002 , OMIM:var0004
-
rs28931605
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic
g.208989018G>T
g.208124294G>T
305C>A (P23T)
-
CRYGD_000002
mapped by linkage; not in 200 control chromosomes
PubMed: Nandrot 2003 , OMIM:var0004
-
rs28931605
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic
g.208989018G>T
g.208124294G>T
C>A (P23T)
-
CRYGD_000002
linked by mapping (LOD score 3.81); not in 340 control chromosomes
PubMed: Mackay 2004
-
rs28931605
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.Pro24Thr
-
NA
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
expression cloning, less soluble in HLE B-3 cells
PubMed: Mackay 2004
-
rs28931605
In vitro (cloned)
-
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.Pro24Thr
-
pathogenic
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
mapped by linkage; not in 206 control chromosomes
PubMed: Zhang 2009
-
rs28931605
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic
g.208989018G>T
g.208124294G>T
305C>A (P23T)
-
CRYGD_000002
mapped by linkage (LOD score 3.72); not in 200 control chromosomes
PubMed: Burdon 2004
-
rs28931605
Germline
-
-
-
-
-
Johan den Dunnen
+?/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
likely pathogenic
g.208989018G>T
g.208124294G>T
P23T
-
CRYGD_000002
-
PubMed: Khan 2009
-
-
Germline
yes
-
-
-
-
Jamie Zeegers
+?/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
likely pathogenic
g.208989018G>T
g.208124294G>T
P23T
-
CRYGD_000002
-
PubMed: Khan 2009
-
-
Germline
yes
-
-
-
-
Jamie Zeegers
+?/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
likely pathogenic
g.208989018G>T
g.208124294G>T
P23T
-
CRYGD_000002
-
PubMed: Khan 2009
-
-
Germline
yes
-
-
-
-
Jamie Zeegers
+?/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
likely pathogenic
g.208989018G>T
g.208124294G>T
P23T
-
CRYGD_000002
-
PubMed: Khan 2009
-
-
Germline/De novo (untested)
-
-
-
-
-
Jamie Zeegers
+?/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
likely pathogenic
g.208989018G>T
g.208124294G>T
c.70C-->A; p.Pro24Thr
-
CRYGD_000002
no Sanger sequencing; heterozygous
PubMed: Patel 2019
-
-
Germline
?
-
-
-
-
LOVD
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Zhai 2017
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Jackson 2020
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+?/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
ACMG
likely pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
ACMG PM1, PM2, PP1, PP2, PP5
PubMed: Zhuang 2019
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Li 2018
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Fan 2020
-
-
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Fan 2020
-
-
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Ma 2016
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Taylan Sekeroglu 2020
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+?/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
likely pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
ACMG PS3, PS4mod, PM2
PubMed: Kessel 2021
VCV000016940.3
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Wang 2023
-
-
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
-
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
2
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Liu 2023
rs28931605
rs28931605
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Cai 2021
-
-
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
-
PubMed: Cai 2021
-
-
Germline
yes
-
-
-
-
Johan den Dunnen
+/.
-
c.70C>A
r.(?)
p.(Pro24Thr)
-
pathogenic (dominant)
g.208989018G>T
g.208124294G>T
-
-
CRYGD_000002
segregates with cataract (4/4 affected)
PubMed: Li 2020
-
-
Germline
yes
-
-
-
-
Johan den Dunnen