Unique variants in the NOBOX gene

Information The variants shown are described using the NM_001080413.3 transcript reference sequence.

76 entries on 1 page. Showing entries 1 - 76.
Legend   How to query  

Effect     

Reported     

Exon     

AscendingDNA change (cDNA)     

RNA change     

Protein     

Classification method     

Clinical classification     

DNA change (genomic) (hg19)     

DNA change (hg38)     

Published as     

ISCN     

DB-ID     

Variant remarks     

Reference     

ClinVar ID     

dbSNP ID     

Origin     

Segregation     

Frequency     

Re-site     

VIP     

Methylation     

Owner     
-/. 2 1 c.42T>C r.(?) p.(Gly14=) - benign g.144107279A>G g.144410186A>G - - NOBOX_000076 22/174 cases (heterozygous), 27/96 heterozygous cases PubMed: Bouilly 2011, PubMed: Qin 2007 - rs1208179 Germline - - - - - Johan den Dunnen
-?/. 2 1 c.66T>C r.(?) p.(Asp22=) - likely benign g.144107255A>G g.144410162A>G - - NOBOX_000075 not in 278 controls, 1/96 heterozygous cases, not in 724 control chromosomes, 3/174 cases PubMed: Bouilly 2011, PubMed: Qin 2007 - - Germline - - - - - Johan den Dunnen
?/. 1 - c.67G>A r.(?) p.(Gly23Ser) - VUS g.144107254C>T - - - NOBOX_000010 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Nijmegen
-?/. 1 - c.68G>A r.(?) p.(Gly23Asp) - likely benign g.144107253C>T g.144410160C>T - - NOBOX_000023 - PubMed: Li 2017 - rs563911669 Germline - - - - - Johan den Dunnen
+?/. 1 - c.79C>T r.(?) p.(Gln27*) - likely pathogenic g.144107242G>A - NOBOX(NM_001080413.3):c.79C>T (p.(Gln27*)) - NOBOX_000015 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
?/. 1 2 c.92C>T r.(?) p.(Pro31Leu) - VUS g.144101767G>A g.144404674G>A - - NOBOX_000074 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
-?/., ?/. 6 10, 2 c.131G>T r.(?) p.(Arg44Leu) - likely benign, VUS g.144101728C>A g.144404635C>A - - NOBOX_000073 no effect on transactivation KIT-L/GDF9 reporter, 1 more item PubMed: Bouilly 2015, PubMed: Eskenazi 2021, PubMed: Jordan 2024 - rs115206969 Germline, Germline/De novo (untested) - 14/810 cases POF - - - Johan den Dunnen
-?/. 1 2 c.138C>A r.(?) p.(Tyr46Ter) - likely benign g.144101721G>T g.144404628G>T - - NOBOX_000072 not overrepresented in POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
-?/. 1 2 c.166_168del r.(?) p.(Phe56del) - likely benign g.144101695_144101697del g.144404602_144404604del - - NOBOX_000071 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
?/. 1 - c.222T>A r.(?) p.(Asp74Glu) - VUS g.144099032A>T - NOBOX(NM_001080413.3):c.222T>A (p.(Asp74Glu)) - NOBOX_000017 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
?/. 1 - c.259C>A r.(259c>a) p.(Pro87Thr) - VUS g.144098995G>T g.144401902G>T - - NOBOX_000013 - - - - Germline ? 0,0000289 - - - Asma Sassi
-/. 3 3 c.262C>T r.(?) p.(Leu88=) - benign g.144098992G>A g.144401899G>A NOBOX(NM_001080413.3):c.262C>T (p.L88=) - NOBOX_000005 41/96 homozygous cases, 55/174 cases (homozygous), VKGL data sharing initiative Nederland PubMed: Bouilly 2011, PubMed: Qin 2007 - rs727714 CLASSIFICATION record, Germline - - - - - Johan den Dunnen, VKGL-NL_Groningen
-?/. 1 3 c.265G>T r.(?) p.(Val89Leu) - likely benign g.144098989C>A g.144401896C>A - - NOBOX_000070 - PubMed: Jordan 2024 - - Germline - 3/810 cases POF - - - Johan den Dunnen
+/., +?/., ?/. 19 3 c.271G>T r.(?) p.(Gly91Trp) - likely pathogenic (dominant), pathogenic, VUS g.144098983C>A g.144401890C>A - - NOBOX_000069 total loss transactivation KIT-L/GDF9 reporter, 2 more items PubMed: Bouilly 2011, PubMed: Bouilly 2015, PubMed: Eskenazi 2021, PubMed: Jordan 2024 - rs77587352 De novo, Germline, Germline/De novo (untested) - 32/810 cases POF - - - Johan den Dunnen
?/. 1 - c.280_292+1del r.spl? p.? - VUS g.144098963_144098976del g.144401870_144401883del NOBOX(NM_001080413.3):c.280_292+1delGAACTCACAAGGGG - NOBOX_000004 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
-/. 1 3i c.292+39C>T r.(?) p.(=) - benign g.144098923G>A g.144401830G>A - - NOBOX_000068 3/174 cases (homozygous) PubMed: Bouilly 2011 - - Germline - - - - - Johan den Dunnen
-/. 1 3i c.292+65A>G r.(?) p.(=) - benign g.144098897A>C g.144401804A>C - - NOBOX_000067 58/174 cases (homozygous) PubMed: Bouilly 2011 - rs727713 Germline - - - - - Johan den Dunnen
-?/. 1 3i c.293-71G>A r.(?) p.(=) - likely benign g.144098761C>T g.144401668C>T - - NOBOX_000066 not in 724 control chromosomes, 2/178 cases PubMed: Bouilly 2011 - - Germline - - - - - Johan den Dunnen
-?/. 1 3i c.293-23C>T r.(?) p.(=) - likely benign g.144098713G>A g.144401620G>A - - NOBOX_000065 1 homozygote in 362 controls, no heterozygous controls, 1/178 cases PubMed: Bouilly 2011 - - Germline - - - - - Johan den Dunnen
+/., -?/. 2 3 c.331G>A r.(?) p.(Gly111Arg) - likely benign, pathogenic g.144098652C>T g.144401559C>T NOBOX(NM_001080413.3):c.331G>A (p.G111R) - NOBOX_000008 total loss transactivation KIT-L/GDF9 reporter, VKGL data sharing initiative Nederland PubMed: Bouilly 2015 - - CLASSIFICATION record, Germline/De novo (untested) - - - - - Johan den Dunnen, VKGL-NL_Rotterdam
+/., +?/., -?/., ?/. 16 4 c.349C>T r.(?) p.(Arg117Trp) - likely benign, likely pathogenic (dominant), pathogenic, VUS g.144098634G>A g.144401541G>A - - NOBOX_000064 no significant overrepresentation African POI cohort, total loss transactivation KIT-L/GDF9 reporter, 1 more item PubMed: Bouilly 2011, PubMed: Bouilly 2015, PubMed: Eskenazi 2021, PubMed: Jordan 2024 - rs7800847 Germline, Germline/De novo (untested) yes 36/810 cases POF - - - Johan den Dunnen
-?/. 1 - c.350G>A r.(?) p.(Arg117Gln) - likely benign g.144098633C>T g.144401540C>T - - NOBOX_000024 - PubMed: Li 2017 - rs528754192 Germline - - - - - Johan den Dunnen
-?/. 1 4 c.362C>T r.(?) p.(Pro121Leu) - likely benign g.144098621G>A g.144401528G>A - - NOBOX_000063 - PubMed: Jordan 2024 - - Germline - 4/810 cases POF - - - Johan den Dunnen
?/. 4 4 c.454G>A r.(?) p.(Gly152Arg) - VUS g.144098529C>T g.144401436C>T - - NOBOX_000062 1 more item PubMed: Eskenazi 2021, PubMed: Jordan 2024 - rs201806397 Germline - 12/810 cases POF - - - Johan den Dunnen
-?/. 1 4 c.480G>A r.(?) p.(Pro160=) - likely benign g.144098503C>T g.144401410C>T - - NOBOX_000061 not in 724 control chromosomes, 1/178 cases (homozygous) PubMed: Bouilly 2011 - - Germline - - - - - Johan den Dunnen
?/. 1 4 c.487C>G r.(?) p.(Arg163Gly) - VUS g.144098496G>C g.144401403G>C - - NOBOX_000060 significant overrepresentation African POI cohort PubMed: Jordan 2024 - - Germline - 3/810 cases POF - - - Johan den Dunnen
?/. 2 4 c.487C>T r.(?) p.(Arg163Cys) - VUS g.144098496G>A g.144401403G>A - - NOBOX_000059 significant overrepresentation African POI cohort PubMed: Jordan 2024 - - Germline - 2/810 cases POF - - - Johan den Dunnen
?/. 1 4 c.547G>T r.(?) p.(Glu183Ter) - VUS g.144098436C>A g.144401343C>A - - NOBOX_000058 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 2/810 cases POF - - - Johan den Dunnen
+/. 1 - c.569del r.(?) p.(Gly190GlufsTer3) - pathogenic g.144098416del g.144401323del 567delG - NOBOX_000022 - PubMed: Li 2017 - - Germline - - - - - Johan den Dunnen
?/. 1 4 c.628A>G r.(?) p.(Asn210Asp) - VUS g.144098355T>C g.144401262T>C - - NOBOX_000057 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
+/. 2 4 c.822del r.(?) p.(Thr275Hisfs*13), p.Thr275Hisfs*13 - NA, pathogenic g.144098161del g.144401068del NM_001080413.2:c.567delG - NOBOX_000001 1 more item PubMed: Li 2017 - - Germline, In vitro (cloned) -, ? - - - - Johan den Dunnen, Lin Li
+/. 2 4 c.826C>T r.(?) p.(Arg276*) ACMG pathogenic (recessive) g.144098157G>A g.144401064G>A - - NOBOX_000012 ACMG PVS1, PM2, PP3 PubMed: Sassi 2021 - - Germline yes - - - - Asma Sassi
+?/. 1 5 c.907C>T r.(?) p.(Arg303Ter) - likely pathogenic (dominant) g.144097343G>A g.144400250G>A - - NOBOX_000056 1 more item PubMed: Bouilly 2011 - - Germline/De novo (untested) - - - - - Johan den Dunnen
?/. 1 - c.944G>A r.(?) p.(Arg315His) - VUS g.144097306C>T - NOBOX(NM_001080413.3):c.944G>A (p.(Arg315His)) - NOBOX_000016 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
+/. 1 - c.961del r.(?) p.(Ala321ProfsTer27) - pathogenic g.144097293del g.144400200del - - NOBOX_000006 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Nijmegen
-?/. 1 5 c.963C>T r.(?) p.(Ala321=) - likely benign g.144097287G>A g.144400194G>A - - NOBOX_000055 not in 724 control chromosomes, 1/178 cases PubMed: Bouilly 2011 - - Germline - - - - - Johan den Dunnen
+?/. 4 5 c.1025G>C r.(?) p.(Ser342Thr) - likely pathogenic (dominant) g.144097225C>G g.144400132C>G - - NOBOX_000054 1 more item PubMed: Bouilly 2011 - - Germline/De novo (untested) - - - - - Johan den Dunnen
?/. 1 5 c.1031G>A r.(?) p.(Arg344His) - VUS g.144097219C>T g.144400126C>T - - NOBOX_000053 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
?/. 1 5 c.1037C>T r.(?) p.(Ala346Val) - VUS g.144097213G>A g.144400120G>A - - NOBOX_000052 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
+?/. 1 6 c.1048G>T r.(?) p.(Val350Leu) - likely pathogenic (dominant) g.144096956C>A g.144399863C>A - - NOBOX_000051 1 more item PubMed: Bouilly 2011 - - Germline/De novo (untested) - - - - - Johan den Dunnen
?/. 1 6 c.1063C>T r.(?) p.(Arg355Cys) - VUS g.144096941G>A g.144399848G>A - - NOBOX_000050 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
+/., +?/. 2 6 c.1064G>A r.(?) p.(Arg355His) - likely pathogenic (dominant), pathogenic g.144096940C>T g.144399847C>T - - NOBOX_000009 1 heterozygous, no homozygous; Clinindb (India), 1 more item PubMed: Narang 2020, Journal: Narang 2020, PubMed: Qin 2007 - rs201947677 Germline - 1/2795 individuals - - - Johan den Dunnen, Mohammed Faruq
?/. 2 6 c.1064G>C r.(?) p.(Arg355Pro) - VUS g.144096940C>G g.144399847C>G - - NOBOX_000049 - PubMed: Eskenazi 2021, PubMed: Jordan 2024 - rs201947677 Germline - 1/810 cases POF - - - Johan den Dunnen
?/. 1 6 c.1075T>C r.(?) p.(Trp359Arg) - VUS g.144096929A>G g.144399836A>G - - NOBOX_000048 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
+?/. 1 - c.1078C>T r.(?) p.(Arg360Ter) - likely pathogenic g.144096926G>A g.144399833G>A - - NOBOX_000021 - PubMed: Jolly 2019 - - Germline - - - - - Johan den Dunnen
-?/., ?/. 4 6 c.1079G>A r.(?) p.(Arg360Gln) - likely benign, VUS g.144096925C>T g.144399832C>T NOBOX(NM_001080413.3):c.1079G>A (p.R360Q) - NOBOX_000014 4/278 controls, 1/96 heterozygous cases, significant overrepresentation European POI cohort, 1 more item PubMed: Jordan 2024, PubMed: Qin 2007 - - CLASSIFICATION record, Germline - 5/810 cases POF - - - Johan den Dunnen, VKGL-NL_Groningen
+/. 1 6 c.1112A>C r.(?) p.(Lys371Thr) - pathogenic g.144096892T>G g.144399799T>G - - NOBOX_000047 total loss transactivation KIT-L/GDF9 reporter PubMed: Bouilly 2015 - rs1893066575 Germline/De novo (untested) - - - - - Johan den Dunnen
-/. 3 6i c.1154+11T>C r.(=), r.(?) p.(=) - benign g.144096839A>G g.144399746A>G NOBOX(NM_001080413.3):c.1154+11T>C - NOBOX_000003 41/96 homozygous cases, 56/174 cases (homozygous), VKGL data sharing initiative Nederland PubMed: Bouilly 2011, PubMed: Qin 2007 - rs757388 CLASSIFICATION record, Germline - - - - - Johan den Dunnen, VKGL-NL_Groningen
-/. 1 6i c.1155-22G>A r.(?) p.(=) - benign g.144096597A>T g.144399504A>T - - NOBOX_000046 41/96 homozygous cases PubMed: Qin 2007 - rs11769847 Germline - - - - - Johan den Dunnen
?/. 1 7i c.1240+2T>G r.spl p.? - VUS g.144096488A>C g.144399395A>C - - NOBOX_000045 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
-/. 1 7i c.1240+34G>A r.(?) p.(=) - benign g.144096456C>T g.144399363C>T - - NOBOX_000044 33/174 cases (homozygous) PubMed: Bouilly 2011 - rs11769787 Germline - - - - - Johan den Dunnen
-/. 1 8 c.1308G>A r.(?) p.(Arg436=) - benign g.144096204C>T g.144399111C>T 1306G>A (synonymous) - NOBOX_000043 52/362 heterozygous controls, 1/178 cases PubMed: Bouilly 2011 - - Germline - - - - - Johan den Dunnen
?/. 1 8 c.1330A>T r.(?) p.(Ser444Cys) - VUS g.144096182T>A g.144399089T>A - - NOBOX_000042 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 2/810 cases POF - - - Johan den Dunnen
-/. 1 8 c.1350G>A r.(?) p.(Arg450=) - benign g.144096162C>T g.144399069C>T - - NOBOX_000041 17/362 heterozygous controls, 1/178 cases PubMed: Bouilly 2011 - - Germline - - - - - Johan den Dunnen
-?/., ?/. 7 8 c.1354G>A r.(?) p.(Asp452Asn) - likely benign, VUS g.144096158C>T g.144399065C>T - - NOBOX_000040 29/278 controls, 1/96 heterozygous cases, 1 more item PubMed: Eskenazi 2021, PubMed: Jordan 2024, PubMed: Qin 2007 - rs112190116 Germline - 26/810 cases POF - - - Johan den Dunnen
+/. 2 8 c.1421del r.(?) p.(Gly474Alafs*76) ACMG pathogenic (recessive) g.144096091del, g.144096092del g.144398999del 1421delG - NOBOX_000011 ACMG PVS1, PM2, PP3 PubMed: Sassi 2021 - - Germline yes - - - - Asma Sassi
-/. 2 8 c.1444G>A r.(?) p.(Gly482Ser) - benign g.144096068C>T g.144398975C>T - - NOBOX_000039 1/96 homozygous cases, 27/96 heterozygous cases, 8/174 cases (homozygous) PubMed: Bouilly 2011, PubMed: Qin 2007 - rs2525702 Germline - - - - - Johan den Dunnen
?/. 1 8 c.1466C>T r.(?) p.(Thr489Ile) - VUS g.144096046G>A g.144398953G>A - - NOBOX_000038 significant overrepresentation African POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
?/. 1 - c.1469+5G>A r.spl? p.? - VUS g.144096038C>T - NOBOX(NM_001080413.3):c.1469+5G>A - NOBOX_000018 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Groningen
-/. 1 8i c.1470-51G>T r.(?) p.(=) - benign g.144095730C>A g.144398637C>A - - NOBOX_000037 39/96 homozygous cases PubMed: Qin 2007 - rs11979528 Germline - - - - - Johan den Dunnen
?/. 1 9 c.1484C>T r.(?) p.(Pro495Leu) - VUS g.144095665G>A g.144398572G>A - - NOBOX_000036 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
+/. 1 9 c.1489del r.(?) p.(Cys497ValfsTer53) - pathogenic (recessive) g.144095660del g.144398567del 1489delT - NOBOX_000020 - - - - Germline yes - - - - Johan den Dunnen
-/. 2 9 c.1549T>C r.(?) p.(Phe517Leu) - benign g.144095600A>G g.144398507A>G NOBOX(NM_001080413.3):c.1549T>C (p.F517L) - NOBOX_000002 26/96 homozygous cases, VKGL data sharing initiative Nederland PubMed: Qin 2007 - rs2699503 CLASSIFICATION record, Germline - - - - - Johan den Dunnen, VKGL-NL_Groningen
-?/. 1 9 c.1649C>T r.(?) p.(Thr550Met) - likely benign g.144095500G>A g.144398407G>A - - NOBOX_000035 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
-?/. 1 - c.1650G>A r.(?) p.(Thr550=) - likely benign g.144095499C>T g.144398406C>T NOBOX(NM_001080413.3):c.1650G>A (p.T550=) - NOBOX_000007 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Rotterdam
?/. 1 9 c.1674_1675del r.(?) p.(Phe559TyrfsTer39) - VUS g.144095480_144095481del g.144398387_144398388del - - NOBOX_000034 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
?/. 1 9 c.1678del r.(?) p.(Met560CysfsTer24) - VUS g.144095471del g.144398378del - - NOBOX_000033 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
-?/. 1 9 c.1709C>T r.(?) p.(Ser570Leu) - likely benign g.144095440G>A g.144398347G>A - - NOBOX_000032 - PubMed: Jordan 2024 - - Germline - 2/810 cases POF - - - Johan den Dunnen
-?/. 1 9 c.1735T>A r.(?) p.(Ser579Thr) - likely benign g.144095414A>T g.144398321A>T - - NOBOX_000031 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
?/. 1 10 c.1788G>C r.(?) p.(Trp596Cys) - VUS g.144094621C>G g.144397528C>G - - NOBOX_000030 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
?/. 1 10 c.1795C>T r.(?) p.(Pro599Ser) - VUS g.144094614G>A g.144397521G>A - - NOBOX_000029 significant overrepresentation European POI cohort PubMed: Jordan 2024 - - Germline - 3/810 cases POF - - - Johan den Dunnen
-?/. 1 10 c.1826C>T r.(?) p.(Pro609Leu) - likely benign g.144094583G>A g.144397490G>A - - NOBOX_000028 - PubMed: Jordan 2024 - - Germline - 3/810 cases POF - - - Johan den Dunnen
-?/. 1 10 c.1849C>T r.(?) p.(His617Tyr) - likely benign g.144094560G>A g.144397467G>A - - NOBOX_000027 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
-?/., ?/. 3 10, 2 c.1856C>T r.(?) p.(Pro619Leu) - likely benign, VUS g.144094553G>A g.144397460G>A - - NOBOX_000026 significant decrease (0.30) transactivation KIT-L/GDF9 reporter PubMed: Bouilly 2015, PubMed: Jordan 2024 - rs1466227301 Germline, Germline/De novo (untested) - 3/810 cases POF - - - Johan den Dunnen
?/. 1 10 c.1859G>C r.(?) p.(Gly620Ala) - VUS g.144094550C>G g.144397457C>G - - NOBOX_000025 - PubMed: Jordan 2024 - - Germline - 1/810 cases POF - - - Johan den Dunnen
-?/. 1 - c.1991A>G r.(?) p.(Lys664Arg) - likely benign g.144094418T>C - NOBOX(NM_001080413.3):c.1991A>G (p.(Lys664Arg)) - NOBOX_000019 VKGL data sharing initiative Nederland - - - CLASSIFICATION record - - - - - VKGL-NL_Leiden
Legend   How to query  


Screenscraping/webscraping (interacting with LOVD using scripts to download data) is strictly prohibited.
Use our APIs to retrieve data.