Global Variome shared LOVD
PDE6B (phosphodiesterase 6B, cGMP-specific, rod, beta)
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Unique variants in the PDE6B gene
This database is one of the
"Eye disease"
gene variant databases.
The variants shown are described using the NM_000283.3 transcript reference sequence.
Legend
Please note that a short description of a certain column can be displayed when you move your mouse cursor over the column's header and hold it still. Below, a more detailed description is shown per column.
Effect
: The variant's effect on the function of the gene/protein, displayed in the format 'R/C'. R is the value reported by the source (publication, submitter) and this classification may vary between records. C is the value concluded by the curator. Note that in some database the curator uses Summary records to give details on the classification of the variant.Values used: '+' indicating the variant affects function, '+?' probably affects function, '-' does not affect function, '-?' probably does not affect function, '?' effect unknown, '.' effect was not classified.
Reported
: The number of times this variant has been reported in the database.
Exon
: number of exon/intron containing variant; 2 = exon 2, 12i = intron 12, 2i_7i = from intron 2 to intron 7, 8i_9 = intron 8/exon 9 boundary, _1 = 5' to exon 1, 18_ = 3' of exon 18, _1_18_ = encompassing the entire 18-exon gene
DNA change (cDNA)
: description of variant at DNA level, based on a coding DNA reference sequence (following HGVS recommendations); e.g. c.123C>T, c.123_145del, c.123_126dup. For deletions/duplications extending beyond the reference transcript resp. {0}/{2} is used to replace del/dup. Extent of the deletion/duplication should be specified using the genomic description (g.). "-" indicates the variant described on genomic level does not affect the coding DNA reference sequence.
RNA change
: description of variant at RNA level (following HGVS recommendations).
r.123c>u
r.? = unknown
r.(?) = RNA not analysed but probably transcribed copy of DNA variant
r.spl? = RNA not analysed but variant probably affects splicing
r.(spl?) = RNA not analysed but variant may affect splicing
r.0? = change expected to abolish transcription
Protein
: description of variant at protein level (following HGVS recommendations).
p.(Arg345Pro) = change predicted from DNA (RNA not analysed)
p.Arg345Pro = change derived from RNA analysis
p.? = unknown effect
p.0? = probably no protein produced
Classification method
: The method used for the clinical classification of this variant.
All options:
ACMG
ACGS
EAHAD-CFDB
ENIGMA
IARC
InSiGHT
kConFab
other
Clinical classification
: Clinical classification of variant, preferably based on standardised criteria (e.g. ACMG), directed on the clinical consequences as published/submitted, indicated using an enriched system including inheritance: e.g. pathogenic, pathogenic (dominant), pathogenic (recessive), pathogenic (!), pathogenic (maternal), pathogenic (paternal). Standard inheritance is covered by dominant/recessive, imprinting by maternal/paternal. A '!' warns for exceptional circumstances to be explained in the 'Remarks' field (low penetrance, variants pathogenic in heterozygous state only, hypomorphic/hypermorphic variants, protective variants, etc.). Non-disease consequences (e.g. drug metabolism (pharmacogenetics), risk factor, blood group, tasting bitter) are indicated using additions to the benign classification; benign (dominant), benign (recessive), benign (!), etc. The value 'association' is used for variants associated with a phenotype and 'NA' for variants from in vitro/in silico records. NOTE: classification may differ from the opinion of the curator as given in a variant SUMMARY-record or the 'Functional effect concluded'). NOTE: pathogenic/likely pathogenic should go together with "variant (probably) affects function" In ClassFunctional.
All options:
pathogenic
pathogenic (dominant)
pathogenic (recessive)
pathogenic (!)
pathogenic (maternal)
pathogenic (paternal)
likely pathogenic
likely pathogenic (dominant)
likely pathogenic (recessive)
likely pathogenic (!)
likely pathogenic (maternal)
likely pathogenic (paternal)
VUS
VUS (!)
likely benign
likely benign (dominant)
likely benign (recessive)
likely benign (!)
likely benign (maternal)
likely benign (paternal)
benign
benign (dominant)
benign (recessive)
benign (!)
benign (maternal)
benign (paternal)
conflicting
association
NA
DNA change (genomic) (hg19)
: HGVS description of variant at DNA level, based on the genomic (chromosomal) DNA reference sequence; e.g. g.12345678C>T, g.12345679del, g.12345678_12345890dup
DNA change (hg38)
: HGVS description of variant at DNA level, based on the hg38 genomic (chromosomal) eference sequence; e.g. g.12345678C>T, g.12345679del, g.12345678_12345890dup
Published as
: listed only when different from "DNA change"; variant as reported originally (e.g. 521delT). Variants seen in animal models, tested in vitro, predicted from RNA analysis, etc. are described between brackets like c.(456C>G)
ISCN
: description of the variant according to ISCN nomenclature
DB-ID
: database ID of variant, grouping multiple observations of the same variant together, starting with the HGNC gene symbol, followed by an underscore (_) and a six digit number (e.g. DMD_012345). _000000 is used for variants where DNA was not analysed (change predicted from RNA analysis), variants seen in animal models or variants not seen in humans but functionally tested in vitro
Variant remarks
: remarks regarding variant described, e.g. germline mosaicism in mother, 345 kb deletion, muscle RNA analysed, not in 200 control chromosomes tested, on founder haplotype, etc.
Reference
: publication describing the variant submitted, incl. links to OMIM, PubMed or other source, e.g. "den Dunnen ASHG2003 P2346"
ClinVar ID
: ID of variant in ClinVar database
dbSNP ID
: the dbSNP ID
Origin
: Origin of variant/record: Germline = in all cells, De novo = in all cells, but not in either parent, Germline/De novo (untested) = in all cells, parents not tested (use only when De novo is likely, e.g. isolated/sporadic cases with dominant disease), Somatic = present in a subset of cells, but not in either parent, Uniparental disomy = from parental disomy (maternal or paternal), CLASSIFICATION record = submitter only sharing variant classification (note another report may share Individual data), SUMMARY record = master summary record from curator (may link to another database), In vitro (cloned) = data resulting from in vitro functional assays, animal model = data from animal model, Artefact = false positive variant call, DUPLICATE record = variant already described on another chromosome (e.g. unbalanced translocation, duplicating transposition, 2nd fusion transcript, etc.)
All options:
Germline
De novo
Germline/De novo (untested)
Somatic
Uniparental disomy
Uniparental disomy, maternal allele
Uniparental disomy, paternal allele
CLASSIFICATION record
SUMMARY record
In vitro (cloned)
In silico
animal model
Artefact
DUPLICATE record
Unknown
Not applicable
Segregation
: Indicates whether the variant segregates with the phenotype (yes), does not segregate with the phenotype (no) or segregation is unknown (?)
All options:
? = unknown
yes = segregates with phenotype
no = does not segregate with phenotype
- = not applicable
Frequency
: frequency in which the variant was found; e.g 5/760 chromosomes (in 5 of 760 chromosomes tested), 1/33 patients (in 1 of 33 patients analysed in study), 0.05 controls (in 5% of control cases tested)
Re-site
: restriction enzyme recognition site created (+) or destroyed (-); e.g. BglII+;BamHI-
VIP
: variant VIP-status was requested for matchmaking - need collaboration(s) to crack the case - please contact the submitter/curator. NOTE: to get VIP status ask the curator.
Methylation
: result of methylation test; GOM (gain of methylation), LOM (loss of methylation), 30% (30% methylated). NOTE: when several tests were done mention the method as well (e.g. MS-PCR 75%)
How to query this table
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Operator
Column type
Example
Matches
Text
Arg
all entries containing 'Arg'
space
Text
Arg Ser
all entries containing 'Arg' and 'Ser'
|
Text
Arg|Ser
all entries containing 'Arg' or 'Ser'
!
Text
!fs
all entries not containing 'fs'
^
Text
^p.(Arg
all entries beginning with 'p.(Arg'
$
Text
Ser)$
all entries ending with 'Ser)'
=""
Text
=""
all entries with this field empty
=""
Text
="p.0"
all entries exactly matching 'p.0'
!=""
Text
!=""
all entries with this field not empty
!=""
Text
!="p.0"
all entries not exactly matching 'p.0?'
combination
Text
*|Ter !fs
all entries containing '*' or 'Ter' but not containing 'fs'
Date
2020
all entries matching the year 2020
|
Date
2020-03|2020-04
all entries matching March or April, 2020
!
Date
!2020-03
all entries not matching March, 2020
<
Date
<2020
all entries before the year 2020
<=
Date
<=2020-06
all entries in or before June, 2020
>
Date
>2020-06
all entries after June, 2020
>=
Date
>=2020-06-15
all entries on or after June 15th, 2020
combination
Date
2019|2020 <2020-03
all entries in 2019 or 2020, and before March, 2020
Numeric
23
all entries exactly matching 23
|
Numeric
23|24
all entries exactly matching 23 or 24
!
Numeric
!23
all entries not exactly matching 23
<
Numeric
<23
all entries lower than 23
<=
Numeric
<=23
all entries lower than, or equal to, 23
>
Numeric
>23
all entries higher than 23
>=
Numeric
>=23
all entries higher than, or equal to, 23
combination
Numeric
>=20 <30 !23
all entries with values from 20 to 29, but not equal to 23
Some more advanced examples:
Example
Matches
Asian
all entries containing 'Asian', 'asian', including 'Caucasian', 'caucasian', etc.
Asian !Caucasian
all entries containing 'Asian' but not containing 'Caucasian'
Asian|African !Caucasian
all entries containing 'Asian' or 'African', but not containing 'Caucasian'
"South Asian"
all entries containing 'South Asian', but not containing 'South East Asian'
To sort on a certain column, click on the column header or on the arrows. If that column is already selected to sort on, the sort order will be swapped. The column currently sorted on has a darker blue background color than the other columns. The up and down arrows next to the column name indicate the current sorting direction. When sorting on any field other than the default, LOVD will sort secondarily on the default sort column.
355 entries on 4 pages. Showing entries 1 - 100.
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Effect
Reported
Exon
DNA change (cDNA)
RNA change
Protein
Classification method
Clinical classification
DNA change (genomic) (hg19)
DNA change (hg38)
Published as
ISCN
DB-ID
Variant remarks
Reference
ClinVar ID
dbSNP ID
Origin
Segregation
Frequency
Re-site
VIP
Methylation
Owner
+/.
1
-

c.1923_1971delinsTCTGGGTA
r.(?)
p.(Asn643GlyfsTer29)
-
pathogenic (recessive)
g.657561_657609delinsTCTGGGTA
g.663772_663820delinsTCTGGGTA
-
-
PDE6B_000206
-
PubMed: Van Huet 2015
-
-
Germline
-
-
-
-
-
LOVD
./.
1
-
c.-547864_*2711741del
r.0?
p.0?
-
pathogenic
g.71552_3375637del
-
-
-
IDUA_000000
decreased gene dosage
PubMed: DDDS 2015
,
Journal: DDDS 2015
-
-
De novo
-
-
-
-
-
Johan den Dunnen
+?/.
1
_1_22_
c.-53_*785{0}
r.0?
p.0?
-
likely pathogenic
g.(?_619411)_(663901_?)del
-
c.(?_-1)_(*1_?)del
-
PDE6B_000287
-
PubMed: Ellingsford 2018
-
-
Germline
-
-
-
-
-
LOVD
+/., ?/.
5
-
c.?
r.(?), r.?, r.spl
p.(?), p.?
ACMG
pathogenic, pathogenic (recessive), VUS
g.619019_664928del, g.?
-
c.2194-1, E55X, NM_001145292:703delC (L235Wfs*33), PDE6B chr4:619019_664928del, Q298X
-
TRAPPC11_000000
whole gene deletion, unsolved
PubMed: Shanks 2013
,
PubMed: Zampaglione 2020
,
PubMed: Zhang 2016
-
-
Germline, Unknown
?
-
-
-
-
LOVD
+/., +?/.
2
-
c.1A>G
r.(?), r.?
p.(Met1?), p.?
-
likely pathogenic, pathogenic (recessive)
g.619416A>G
g.625627A>G
4:619416A>G ENST00000496514.1:c.1A>G (Met1?), PDE6B c.1A>G, p.Met1?
-
PDE6B_000179
homozygous
PubMed: Carss 2017
,
PubMed: Turro 2020
-
-
Germline, Germline/De novo (untested)
?
-
-
-
-
LOVD
+?/.
1
-
c.2T>C
r.(?)
p.(Met1?)
-
likely pathogenic
g.619417T>C
g.625628T>C
-
-
PDE6B_000190
-
PubMed: Stone 2017
-
-
Germline
-
-
-
-
-
LOVD
+?/.
3
1
c.3dup
r.(?)
p.(Met1?), p.(Ser2Glufs*4)
ACMG
likely pathogenic, likely pathogenic (recessive)
g.619418dup
g.625629dup
c.3dup, p.Ser2Glufs*4, c.3dupG, NM_000283.3:c.3dup, NP_000274.2:p.(Met1?), NC_000004.11:g.619418dup
-
PDE6B_000255
heterozygous
PubMed: Gao 2019
,
PubMed: Liu-2020
,
PubMed: Wang 2018
-
-
Germline
?
-
-
-
-
LOVD
+/., +?/.
2
1
c.3G>T
r.(?)
p.(M1?), p.(Met1?)
-
likely pathogenic, pathogenic
g.619418G>T
g.625629G>T
-
-
PDE6B_000011
1 more item
PubMed: Costa 2017
,
PubMed: Neveling 2012
-
-
Germline
-
-
-
-
-
Kornelia Neveling
-?/.
1
-
c.23C>T
r.(?)
p.(Ala8Val)
-
likely benign
g.619438C>T
g.625649C>T
PDE6B(NM_000283.3):c.23C>T (p.A8V)
-
PDE6B_000117
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
-/.
1
-
c.26G>A
r.(?)
p.(Arg9Gln)
-
benign
g.619441G>A
g.625652G>A
PDE6B(NM_000283.4):c.26G>A (p.R9Q)
-
PDE6B_000118
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_AMC
?/.
1
-
c.44A>C
r.(?)
p.(Asn15Thr)
-
VUS
g.619459A>C
g.625670A>C
c.44A>C, p.Asn15Thr
-
PDE6B_000281
heterozygous
PubMed: Zampaglione 2020
-
-
Unknown
?
-
-
-
-
LOVD
+/.
1
1
c.54del
r.(?)
p.(Phe18Leufs*10)
-
pathogenic (recessive)
g.619469del
-
c.51delT:p.D17fs
-
PDE6B_000309
-
PubMed: Numa-2020
-
-
Germline
-
-
-
-
-
LOVD
+/.
1
-
c.120_121insGAGGA
r.(?)
p.(Pro41GlufsTer111)
-
pathogenic
g.619535_619536insGAGGA
g.625746_625747insGAGGA
PDE6B(NM_000283.3):c.120_121insGAGGA (p.P41Efs*111)
-
PDE6B_000119
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+?/.
1
-
c.121_125delins(15)
r.(?)
p.?
-
likely pathogenic
g.619536_619540delinsN[15]
g.625747_625751delinsN[15]
-
-
PDE6B_000242
-
PubMed: Coppieters 2014
-
-
Germline
-
-
-
-
-
LOVD
+/.
1
-
c.122C>G
r.(?)
p.(Pro41Arg)
-
pathogenic
g.619537C>G
g.625748C>G
PDE6B(NM_000283.3):c.122C>G (p.P41R)
-
PDE6B_000026
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+/.
1
-
c.125_126insTGCGA
r.(?)
p.(Asp43AlafsTer109)
-
pathogenic
g.619540_619541insTGCGA
g.625751_625752insTGCGA
PDE6B(NM_000283.3):c.125_126insTGCGA (p.D43Afs*109)
-
PDE6B_000120
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+/.
1
1
c.132C>A
r.(?)
p.(Cys44*)
ACMG
pathogenic
g.619547C>A
g.625758C>A
PDE6B c.132C>A, p.(Cys44*)
-
PDE6B_000323
1 more item
PubMed: Khateb 2019
-
-
Germline
yes
-
-
-
-
LOVD
-/.
1
-
c.132C>G
r.(?)
p.(Cys44Trp)
-
benign
g.619547C>G
g.625758C>G
PDE6B(NM_000283.4):c.132C>G (p.C44W)
-
PDE6B_000028
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_AMC
-/.
1
-
c.133G>A
r.(?)
p.(Asp45Asn)
-
benign
g.619548G>A
g.625759G>A
-
-
PDE6B_000074
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs138423108
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
-/., -?/., ?/.
4
-
c.145G>T
r.(?)
p.(Asp49Tyr)
-
benign, likely benign, VUS
g.619560G>T
g.625771G>T
-
-
PDE6B_000075
6 heterozygous, no homozygous;
Clinindb (India)
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
,
PubMed: Narang 2020
,
Journal: Narang 2020
,
1 more item
-
rs79826315
Germline
-
3/1204 cases with retinitis pigmentosa, 47/1204 cases with retinitis pigmentosa, 6/2795 individuals
-
-
-
Yoshito Koyanagi
,
Mohammed Faruq
+/.
1
-
c.167_171delGCACG
r.(?)
p.(Thr57Alafs*107)
ACMG
pathogenic
g.619584_619588del
g.625795_625799del
PDE6B NM_000283: g.210_214delGCACG, c.167_171delGCACG, p.T57Afs107
-
PDE6B_000235
-
PubMed: Xu 2020
-
-
Germline
yes
-
-
-
-
LOVD
+?/.
1
-
c.169_173del
r.(?)
p.(Thr57AlafsTer107)
-
likely pathogenic
g.619584_619588del
g.625795_625799del
167_171del5bp
-
PDE6B_000235
-
-
-
-
Germline
yes
-
-
-
-
LOVD
+/., +?/., ?/.
3
-
c.173C>T
r.(?)
p.(Ala58Val)
ACMG
likely pathogenic, pathogenic, VUS
g.619588C>T
g.625799C>T
c.2401C-->T, c.173C-->T; p.Gln801,* p.Ala58Val
-
PDE6B_000217
ACMG PM2, BP4; no variant 2nd chromosome, confirmed with Sanger sequencing; heterozygous
PubMed: Ge 2015
,
PubMed: Patel 2019
,
PubMed: Weisschuh 2024
-
-
Germline
yes
-
-
-
-
Johan den Dunnen
+?/.
4
-
c.177_248dup
r.(?)
p.(Leu60_Leu83dup)
ACMG
likely pathogenic, pathogenic (recessive)
g.619592_619663dup
g.625803_625874dup
PDE6B, variant 1: c.177_248dup/p.L83Cfs*19, variant 2: c.1401+2T>G/p.?,
1 more item
-
PDE6B_000289
1 more item
PubMed: Kuehlewein 2021
,
PubMed: Weisschuh 2020
-
-
Germline
yes
-
-
-
-
LOVD
+/.
1
1
c.181G>T
r.(?)
p.(Glu61*)
ACMG
pathogenic
g.619596G>T
g.625807G>T
PDE6B c.181G>T, p.(Glu61*)
-
PDE6B_000324
heterozygous
PubMed: Khateb 2019
-
-
Unknown
?
-
-
-
-
LOVD
+?/.
1
-
c.207dup
r.(?)
p.(Ile70Hisfs*96)
ACMG
likely pathogenic
g.619622dup
g.625833dup
PDE6B c.207dup, p.(Ile70Hisfs*96), c.207dup, p.(Ile70Hisfs*96)
-
PDE6B_000263
homozygous
PubMed: Jespersgaar 2019
-
-
Germline
?
-
-
-
-
LOVD
+/., ?/.
3
1
c.220C>T
r.(?)
p.(Arg74Cys)
ACMG
pathogenic, VUS
g.619635C>T
g.625846C>T
NM_000283.3:c.220C>T, NP_000274.2:p.(Arg74Cys), NC_000004.11:g.619635C>T
-
PDE6B_000121
VKGL data sharing initiative Nederland
PubMed: Wang 2018
-
-
CLASSIFICATION record, Germline
?
-
-
-
-
VKGL-NL_Nijmegen
+?/.
1
-
c.221dup
r.(?)
p.(Val75Argfs*91)
ACMG
likely pathogenic
g.619636dup
g.625847dup
Variant 1: c.221dup;p.(V75Rfs*91), Variant 2: c.892C>T;p.(Q298*)
-
PDE6B_000315
-
PubMed: Kuehlewein 2021
-
-
Unknown
?
-
-
-
-
LOVD
?/.
2
-
c.221G>T
r.(?)
p.(Arg74Leu)
-
VUS
g.619636G>T
g.625847G>T
-
-
PDE6B_000076
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
,
PubMed: Wang 2014
-
-
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+?/.
1
1
c.243del
r.(?)
p.(Arg82Alafs*68)
ACMG
likely pathogenic
g.619658del
g.625869del
c.243delG, p.Arg82Alafs*68
-
PDE6B_000264
Homozygous
PubMed: Birtel 2018
-
-
Germline
?
-
-
-
-
LOVD
?/.
2
-
c.245G>A
r.(?)
p.(Arg82His)
-
VUS
g.619660G>A
g.625871G>A
PDE6B(NM_000283.3):c.245G>A (p.R82H)
-
PDE6B_000029
VKGL data sharing initiative Nederland
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs757048461
CLASSIFICATION record, Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
VKGL-NL_Rotterdam
,
Yoshito Koyanagi
?/.
1
-
c.262C>T
r.(?)
p.(Gln88Ter)
ACMG
VUS
g.619677C>T
g.625888C>T
PDE6B c.C262T, p.Q88X
-
PDE6B_000296
marked as causative, heterozygous
PubMed: Ma 2021
-
-
Unknown
?
-
-
-
-
LOVD
+?/.
1
-
c.263A>G
r.(?)
p.(Gln88Arg)
-
likely pathogenic
g.619678A>G
g.625889A>G
-
-
PDE6B_000200
-
PubMed: Bravo-Gil 2017
-
-
Germline
-
-
-
-
-
Nereida Bravo Gil
-/.
2
-
c.270C>T
r.(?)
p.(Asp90=)
-
benign
g.619685C>T
g.625896C>T
PDE6B(NM_000283.3):c.270C>T (p.D90=), PDE6B(NM_000283.4):c.270C>T (p.D90=)
-
PDE6B_000030
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
,
VKGL-NL_AMC
?/.
1
-
c.291C>A
r.(?)
p.(Tyr97*)
-
VUS
g.619706C>A
g.625917C>A
-
-
PDE6B_000212
-
PubMed: Ellingford 2016
-
-
Germline
-
-
-
-
-
LOVD
+/.
1
-
c.292C>T
r.(?)
p.(Arg98Cys)
-
pathogenic
g.619707C>T
g.625918C>T
-
-
PDE6B_000218
-
PubMed: Ge 2015
-
-
Germline
-
-
-
-
-
LOVD
+?/., ?/.
2
-
c.293G>A
r.(?)
p.(Arg98His)
ACMG
likely pathogenic, VUS
g.619708G>A
g.625919G>A
PDE6B c.293G>A, p.(Arg98His), PDE6B(NM_000283.4):c.293G>A (p.(Arg98His))
-
PDE6B_000265
single heterozygous variant (recessive), VKGL data sharing initiative Nederland
PubMed: Jespersgaar 2019
-
-
CLASSIFICATION record, Germline
?
-
-
-
-
VKGL-NL_Leiden
+/., +?/.
5
1
c.293G>C
r.(?)
p.(Arg98Pro)
ACMG
likely pathogenic, pathogenic
g.619708G>C
g.625919G>C
c.293G>C, p.Arg98Pro, PDE6B c.293G>C, p.(Arg98Pro), PDE6B(NM_000283.4):c.293G>C (p.R98P)
-
PDE6B_000122
heterozygous, Homozygous, VKGL data sharing initiative Nederland
PubMed: Birtel 2018
,
PubMed: Khateb 2019
-
-
CLASSIFICATION record, Germline
?, yes
-
-
-
-
VKGL-NL_AMC
+?/., ?/.
3
-
c.298C>T
r.(?)
p.(Arg100Cys)
-
pathogenic, VUS
g.619713C>T
g.625924C>T
c.298C>T , R100C, PDE6B(NM_000283.3):c.298C>T (p.R100C)
-
PDE6B_000123
Homozygous, VKGL data sharing initiative Nederland
PubMed: Chakrabarty 2020
-
-
CLASSIFICATION record, Germline
yes
-
-
-
-
VKGL-NL_Rotterdam
+/., +?/.
12
1
c.299G>A
r.(?)
p.(Arg100His)
ACMG
likely pathogenic, pathogenic, VUS
g.619714G>A
g.625925G>A
c.299G>A, p.Arg100His, PDE6B c.299G>A, p.(Arg100His),
2 more items
-
PDE6B_000010
Homozygous, homozygous; mother - het c.1927_1969delinsG G, p.(Asn643Glyfs*29), solved, homozygous,
1 more item
PubMed: Birtel 2018
,
PubMed: Comander 2017
,
PubMed: Ge 2015
,
PubMed: Khateb 2019
,
PubMed: Riera 2017
,
4 more items
-
rs555600300
CLASSIFICATION record, Germline, Unknown
?, yes
-
-
-
-
Kornelia Neveling
,
VKGL-NL_Nijmegen
?/.
1
-
c.307G>A
r.(?)
p.(Val103Met)
-
VUS
g.619722G>A
g.625933G>A
-
-
PDE6B_000077
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs751477149
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+/., +?/., ?/.
7
1
c.313G>A
r.(?)
p.(Glu105Lys)
ACMG
likely pathogenic, likely pathogenic (recessive), pathogenic, pathogenic (recessive), VUS
g.619728G>A
g.625939G>A
c.313G>A, c.313G>A, p.Glu105Lys, PDE6B c.313G>A, p.(Glu105Lys),
1 more item
-
PDE6B_000191
heterozygous, homozygous
PubMed: Colombo-2020
,
PubMed: Costa 2017
,
PubMed: Gao 2019
,
PubMed: Jespersgaar 2019
,
PubMed: Xu 2014
,
1 more item
-
rs398123299
Germline, Unknown
?
-
-
-
-
LOVD
+?/., ?/.
2
-
c.339_353del
r.(?)
p.(Gln114_Val118del)
-
VUS
g.619754_619768del
g.625965_625979del
-
-
PDE6B_000336
-
PubMed: Ben Yosef 2023
-
-
Germline
-
-
-
-
-
Tamar Ben-Yosef
?/.
1
-
c.362A>G
r.(?)
p.(Asp121Gly)
-
VUS
g.619777A>G
g.625988A>G
PDE6B(NM_000283.4):c.362A>G (p.D121G)
-
PDE6B_000124
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_AMC
?/.
1
-
c.379G>A
r.(?)
p.(Asp127Asn)
-
VUS
g.619794G>A
g.626005G>A
-
-
PDE6B_000078
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs766141814
Germline
-
4/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+?/., ?/.
10
1
c.385G>A
r.(?)
p.(Glu129Lys)
ACMG
likely pathogenic, likely pathogenic (recessive), VUS
g.619800G>A
g.626011G>A
c.385G>A, NM_000283.3:c.385G>A, NP_000274.2:p.(Glu129Lys), NC_000004.11:g.619800G>A,
5 more items
-
PDE6B_000201
alleles in cis or trans; heterozygous, heterozygous, VKGL data sharing initiative Nederland,
1 more item
PubMed: Bravo-Gil 2017
,
PubMed: Chen 2021
,
PubMed: Chen 2021
,
PubMed: Jespersgaar 2019
,
4 more items
-
-
CLASSIFICATION record, Germline, Germline/De novo (untested), Unknown
?, yes
Taiwan Biobank: 0; GnomAD_exome_East: 0; GnomAD_All: 0.0000143
-
-
-
VKGL-NL_Nijmegen
,
Nereida Bravo Gil
+?/.
5
1
c.409G>A
r.(?)
p.(Gly137Arg)
ACMG
likely pathogenic, VUS
g.619824G>A
g.626035G>A
PDE6B c.409G>A, p.(Gly137Arg), PDE6B, variant 1: c.409G>A/p.G137R, variant 2: c.928-9_940dup/p.?,
1 more item
-
PDE6B_000192
heterozygous, solved, compound heterozygous
PubMed: Khateb 2019
,
PubMed: Kuehlewein 2021
,
PubMed: Stone 2017
,
PubMed: Weisschuh 2020
-
-
Germline, Unknown
?, yes
-
-
-
-
LOVD
+?/.
1
-
c.424G>A
r.(?)
p.(Val142Met)
-
likely pathogenic (recessive)
g.619839G>A
g.626050G>A
-
-
PDE6B_000224
-
PubMed: Xu 2014
-
-
Germline
-
1/314 case chromosomes
-
-
-
LOVD
+/.
2
1
c.428C>A
r.(?)
p.(Ala143Asp)
ACMG
pathogenic
g.619843C>A
g.626054C>A
-
-
PDE6B_000067
-
Sharon, submitted,
PubMed: Sharon 2019
-
-
Germline
-
3/2420 IRD families
-
-
-
Global Variome, with Curator vacancy
,
Dror Sharon
?/.
1
-
c.454G>C
r.(?)
p.(Glu152Gln)
-
VUS
g.619869G>C
g.626080G>C
-
-
PDE6B_000079
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
-
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+?/.
1
-
c.468+1G>A
r.spl
p.(?)
ACMG
likely pathogenic
g.619884G>A
g.626095G>A
1 more item
-
PDE6B_000307
-
PubMed: Perea-Romero 2021
-
-
Germline
yes
-
-
-
-
LOVD
+?/.
1
1i
c.469-776C>G
r.?
p.?
-
likely pathogenic (recessive)
g.627690C>G
g.633901C>G
-
-
PDE6B_000214
-
PubMed: Fadaie 2021
-
-
Germline
yes
-
-
-
-
Zeinab Fadaie
?/.
1
-
c.480C>G
r.(?)
p.(Phe160Leu)
-
VUS
g.628477C>G
g.634688C>G
-
-
PDE6B_000080
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
-
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
?/.
1
-
c.482G>A
r.(?)
p.(Ser161Asn)
-
VUS
g.628479G>A
g.634690G>A
-
-
PDE6B_000243
-
PubMed: Wang 2014
-
-
Germline
-
-
-
-
-
LOVD
?/.
1
-
c.485C>T
r.(?)
p.(Ser162Leu)
-
VUS
g.628482C>T
g.634693C>T
-
-
PDE6B_000081
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs772012465
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
-/., -?/.
4
2
c.496G>A
r.(?)
p.(Glu166Lys)
-
benign, likely benign
g.628493G>A
g.634704G>A
PDE6B(NM_000283.3):c.496G>A (p.E166K)
-
PDE6B_000012
29 heterozygous, no homozygous;
Clinindb (India)
, predicted benign,
1 more item
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
,
PubMed: Narang 2020
,
Journal: Narang 2020
,
1 more item
-
rs115775983
CLASSIFICATION record, Germline
no
2/1204 cases with retinitis pigmentosa, 29/2795 individuals
-
-
-
Kornelia Neveling
,
VKGL-NL_Rotterdam
,
Yoshito Koyanagi
,
Mohammed Faruq
+?/.
1
-
c.537_540del
r.(?)
p.(Ile180*)
-
likely pathogenic
g.628534_628537del
g.634745_634748del
-
-
PDE6B_000162
-
PubMed: Holtan 2020
-
-
Germline
-
1/899 cases
-
-
-
Global Variome, with Curator vacancy
?/.
1
-
c.551A>G
r.(?)
p.(Lys184Arg)
ACMG
VUS
g.628548A>G
g.634759A>G
-
-
PDE6B_000350
ACMG PM2
PubMed: Weisschuh 2024
-
-
Germline
-
-
-
-
-
Johan den Dunnen
?/.
1
-
c.556G>A
r.(?)
p.(Val186Ile)
-
VUS
g.628553G>A
g.634764G>A
-
-
PDE6B_000082
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs779085612
Germline
-
3/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
?/.
1
-
c.582C>G
r.(?)
p.(Asn194Lys)
ACMG
VUS
g.628579C>G
g.634790C>G
-
-
PDE6B_000351
ACMG PM2
PubMed: Weisschuh 2024
-
-
Germline
-
-
-
-
-
Johan den Dunnen
-?/.
1
-
c.582C>T
r.(?)
p.(Asn194=)
-
likely benign
g.628579C>T
g.634790C>T
PDE6B(NM_000283.3):c.582C>T (p.N194=)
-
PDE6B_000031
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+/.
2
-
c.583A>T
r.(?)
p.(Lys195*), p.(Lys195Ter)
-
pathogenic
g.628580A>T
g.634791A>T
-
-
PDE6B_000049
VKGL data sharing initiative Nederland
PubMed: Haer-Wigman 2017
-
-
CLASSIFICATION record, Germline
-
-
-
-
-
VKGL-NL_Nijmegen
?/.
1
-
c.592G>A
r.(?)
p.(Gly198Ser)
-
VUS
g.628589G>A
g.634800G>A
-
-
PDE6B_000083
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs199690401
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+/.
1
-
c.610G>T
r.(?)
p.(Glu204Ter)
-
pathogenic (recessive)
g.628607G>T
g.634818G>T
-
-
PDE6B_000225
-
PubMed: Xu 2014
-
-
Germline
-
-
-
-
-
LOVD
-/., -?/.
3
2
c.615C>T
r.(=), r.(?)
p.(=), p.(Asp205=)
-
benign, likely benign
g.628612C>T
g.634823C>T
c.615C>T, PDE6B(NM_000283.3):c.615C>T (p.D205=), PDE6B(NM_000283.4):c.615C>T (p.D205=)
-
PDE6B_000032
VKGL data sharing initiative Nederland
PubMed: González-del Pozo-2011
-
-
CLASSIFICATION record, Germline
-
-
-
-
-
VKGL-NL_Rotterdam
,
VKGL-NL_AMC
+/.
1
2
c.616G>T
r.(?)
p.(Glu206*)
-
pathogenic (recessive)
g.628613G>T
-
c.616G>T
-
PDE6B_000298
-
PubMed: Colombo-2020
-
-
Germline
-
-
-
-
-
LOVD
+/.
1
2
c.621+97_*785del
r.622_2562del
p.(Val208_855del)
-
pathogenic (recessive)
g.628715_664681del
g.634926_670892del
-
-
PDE6B_000215
-
PubMed: Fadaie 2021
-
-
Germline
yes
-
-
-
-
Zeinab Fadaie
+?/.
2
2i
c.622-1G>T
r.spl
p.(?)
-
likely pathogenic
g.629668G>T
g.635879G>T
PDE6B AG to AT splice acceptor site mutation in intron 2
-
PDE6B_000316
actual variants extrapolated from literature and protein annotation
PubMed: Danciger 1995
-
-
Germline
yes
-
-
-
-
LOVD
?/.
1
3
c.622G>A
r.(?)
p.(Val208Met)
ACMG
VUS
g.629669G>A
g.635880G>A
PDE6B c.622G>A, p.(Val208Met)
-
PDE6B_000275
heterozygous
PubMed: Dan 2020
-
-
Germline/De novo (untested)
yes
-
-
-
-
LOVD
?/.
1
-
c.650C>G
r.(?)
p.(Thr217Arg)
-
VUS
g.629697C>G
g.635908C>G
-
-
PDE6B_000084
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
-
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+?/., -/., -?/., ?/.
8
3
c.655T>C
r.(?)
p.(Tyr219His)
-
benign, likely benign, likely pathogenic, VUS
g.629702T>C
g.635913T>C
c.655T>C, PDE6B(NM_000283.3):c.655T>C (p.Y219H)
-
PDE6B_000013
predicted benign, predicted benign; not segregating with disease in other families,
1 more item
PubMed: Booij-2011
,
PubMed: Holtan 2020
,
PubMed: Neveling 2012
,
PubMed: Tiwari 2016
-
-
CLASSIFICATION record, Germline
no, yes
2/899 cases
-
-
-
Global Variome, with Curator vacancy
,
Kornelia Neveling
,
VKGL-NL_Rotterdam
+/.
1
3
c.669T>A
r.(?)
p.(Tyr223*)
-
pathogenic
g.629716T>A
-
c.669T>A
-
PDE6B_000259
-
PubMed: Eisenberger-2013
-
-
Germline
-
-
-
-
-
LOVD
?/.
1
-
c.683T>A
r,(?)
p.(Leu228His)
-
VUS
g.629730T>A
g.635941T>A
PDE6B Leu228His
-
PDE6B_000317
coding DNA extrapolated from protein annotation; mutation non-causative of ADRP
PubMed: Gao 1996
-
-
Germline
yes
-
-
-
-
LOVD
+?/.
1
3
c.698C>T
r.(?)
p.(Thr233Met)
ACMG
likely pathogenic
g.629745C>T
g.635956C>T
NM_000283.3:c.698C>T, NP_000274.2:p.(Thr233Met), NC_000004.11:g.629745C>T
-
PDE6B_000256
-
PubMed: Wang 2018
-
-
Germline
?
-
-
-
-
LOVD
+/.
1
3
c.699G>A
r.(=)
p.(=)
-
pathogenic
g.629746G>A
-
-
-
PDE6B_000239
-
PubMed: Jin 2008
-
-
Unknown
-
-
-
-
-
LOVD
+?/.
1
-
c.700C>T
r.(?)
p.(Arg234Cys)
-
likely pathogenic (recessive)
g.629747C>T
g.635958C>T
-
-
PDE6B_000226
-
PubMed: Xu 2014
-
-
Germline
-
1/314 case chromosomes
-
-
-
LOVD
+?/.
1
3
c.703C>T
r.(?)
p.(Arg235Cys)
-
likely pathogenic
g.629750C>T
-
c.703C>T
-
PDE6B_000260
-
PubMed: Eisenberger-2013
-
-
Germline
-
-
-
-
-
LOVD
+?/., ?/.
2
3
c.704G>A
r.(?)
p.(Arg235His)
-
likely pathogenic, VUS
g.629751G>A
-
c.704G>A
-
PDE6B_000261
VKGL data sharing initiative Nederland
PubMed: Eisenberger-2013
-
-
CLASSIFICATION record, Germline
-
-
-
-
-
VKGL-NL_Nijmegen
+?/.
1
-
c.704G>C
r.(?)
p.(Arg235Pro)
ACMG
likely pathogenic
g.629751G>C
g.635962G>C
c.G704C
-
PDE6B_000211
-
PubMed: Zhang 2016
-
-
Germline
-
-
-
-
-
LOVD
-?/., ?/.
2
-
c.711+10C>T
r.(=), r.spl?
p.(=), p.?
-
likely benign, VUS
g.629768C>T
g.635979C>T
PDE6B(NM_000283.3):c.711+10C>T
-
PDE6B_000033
VKGL data sharing initiative Nederland
PubMed: Wang 2014
-
rs201100689
CLASSIFICATION record, Germline
-
-
-
-
-
VKGL-NL_Rotterdam
+?/.
1
4
c.723G>A
r.(?)
p.(Trp241*)
-
likely pathogenic (recessive)
g.647652G>A
-
c.723G>A
-
PDE6B_000299
-
PubMed: Liu-2020
-
-
Germline
-
-
-
-
-
LOVD
+/., +?/., ?/.
5
-
c.739T>A
r.(?)
p.(Phe247Ile)
ACMG
likely pathogenic, likely pathogenic (recessive), pathogenic (recessive), VUS
g.647668T>A
g.653879T>A
4:647668T>A ENST00000496514.1:c.739T>A (Phe247Ile), c.739T>A, p.Phe247Ile,
1 more item
-
PDE6B_000180
ACMG PM2, PP5_STRONG, PS4_MODERATE, heterozygous, homozygous
PubMed: Carss 2017
,
PubMed: Turro 2020
,
PubMed: Weisschuh 2024
,
PubMed: Zampaglione 2020
349362
-
Germline, Germline/De novo (untested), Unknown
?
-
-
-
-
Johan den Dunnen
+?/.
1
-
c.754G>A
r.(?)
p.(Asp252Asn)
-
likely pathogenic
g.647683G>A
g.653894G>A
-
-
PDE6B_000202
-
PubMed: Bravo-Gil 2017
-
-
Germline
-
-
-
-
-
Nereida Bravo Gil
+?/.
1
-
c.756del
r.(?)
p.(Asp252Glufs*29)
-
likely pathogenic
g.647685del
g.653896del
PDE6B c.756delC, p.D252EfsX29
-
PDE6B_000282
compound heterozygous
PubMed: Jauregui 2020
-
-
Unknown
?
-
-
-
-
LOVD
+?/., ?/.
2
4
c.760G>A
r.(?)
p.(Glu254Lys)
ACMG
likely pathogenic (recessive), VUS
g.647689G>A
g.653900G>A
c.760G>A, PDE6B:NM_000283 c.G760A, p.E254K
-
PDE6B_000277
heterozygous, individual unsolved, causality of variants unknown
PubMed: Colombo-2020
,
PubMed: Rodriguez-Munoz 2020
-
rs146204075
Germline
?, yes
-
-
-
-
LOVD
+/., +?/., ?/.
3
4
c.772C>A
r.(?)
p.(His258Asn)
-
likely pathogenic, pathogenic (dominant), VUS
g.647701C>A
g.653912C>A
-
-
PDE6B_000116
-
PubMed: Gal 1994
,
PubMed: Stone 2017
,
PubMed: Zeitz-2009
-
rs121918582
Germline
yes
-
-
-
-
Johan den Dunnen
+?/.
1
5
c.782_784del
r.(?)
p.(Phe261del)
-
likely pathogenic
g.647711_647713del
g.653922_653924del
c.782_784del, p.(Phe261del)
-
PDE6B_000273
Homozygous
PubMed: Tayebi 2019
-
-
Germline
yes
-
-
-
-
LOVD
?/.
1
-
c.785A>G
r.(?)
p.(Tyr262Cys)
-
VUS
g.647714A>G
g.653925A>G
-
-
PDE6B_000085
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
-
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+?/.
1
-
c.786C>A
r.(?)
p.(Tyr262Ter)
-
likely pathogenic (recessive)
g.647715C>A
g.653926C>A
-
-
PDE6B_000227
-
PubMed: Xu 2014
-
-
Germline
-
1/314 case chromosomes
-
-
-
LOVD
+/., +?/.
2
-
c.786C>G
r.(?)
p.(Tyr262*)
-
likely pathogenic, pathogenic
g.647715C>G
g.653926C>G
c.786C>G
-
PDE6B_000086
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
,
PubMed: Panneman 2023
-
-
Germline, Unknown
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
,
Daan Panneman
?/.
1
-
c.787A>G
r.(?)
p.(Thr263Ala)
-
VUS
g.647716A>G
g.653927A>G
PDE6B(NM_000283.4):c.787A>G (p.T263A)
-
PDE6B_000125
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_AMC
?/.
1
-
c.793C>G
r.(?)
p.(Arg265Gly)
ACMG
VUS
g.647722C>G
g.653933C>G
PDE6B:NM_000283 c.C793G, p.R265G
-
PDE6B_000278
heterozygous, individual unsolved, causality of variants unknown
PubMed: Rodriguez-Munoz 2020
-
-
Germline
?
-
-
-
-
LOVD
+/., ?/.
7
4
c.794G>A
r.(?)
p.(Arg265Gln)
ACMG
pathogenic, VUS
g.647723G>A
g.653934G>A
PDE6B(NM_000283.3):c.794G>A (p.R265Q), PDE6B(NM_000283.4):c.794G>A (p.R265Q),
1 more item
-
PDE6B_000034
heterozygous, individual solved, variant non-causal, VKGL data sharing initiative Nederland
PubMed: Bernardis 2016
,
PubMed: Rodriguez-Munoz 2020
,
PubMed: Tiwari 2016
-
-
CLASSIFICATION record, Germline
?
-
-
-
-
VKGL-NL_Rotterdam
,
VKGL-NL_Groningen
,
VKGL-NL_Nijmegen
,
VKGL-NL_AMC
+/.
2
4
c.797_798insGGTACTT
r.(?)
p.(Tyr267Valfs* 24)
ACMG
pathogenic
g.647726_647727insGGTACTT
g.653937_653938insGGTACTT
PDE6B c.797_798insGGTACTT, p.(Tyr267Valfs* 24)
-
PDE6B_000325
heterozygous
PubMed: Khateb 2019
-
-
Germline
yes
-
-
-
-
LOVD
+?/.
2
4
c.801C>A
r.(?)
p.(Tyr267*)
-
likely pathogenic
g.647730C>A
g.653941C>A
c.801C>A
-
PDE6B_000014
predicted to affect function, but insufficient evidence for definite conclusion
PubMed: Neveling 2012
,
PubMed: Panneman 2023
-
-
Germline, Unknown
no
-
-
-
-
Kornelia Neveling
,
Daan Panneman
-?/.
1
-
c.804C>T
r.(?)
p.(Leu268=)
-
likely benign
g.647733C>T
g.653944C>T
PDE6B(NM_000283.3):c.804C>T (p.L268=)
-
PDE6B_000126
VKGL data sharing initiative Nederland
-
-
-
CLASSIFICATION record
-
-
-
-
-
VKGL-NL_Rotterdam
+/., +?/., ?/.
7
4
c.810C>A
r.(?)
p.(Cys270*), p.(Cys270Ter)
-
likely pathogenic, pathogenic, pathogenic (recessive), VUS
g.647739C>A
g.653950C>A
c.810C>A, PDE6B Cys270X, PDE6B Ex.4 c.810C>A p.(Cys270*), Ex.4 c.810C>A p.(Cys270*)
-
PDE6B_000050
homozygous, nucleotide extrapolated from protein annotation, VKGL data sharing initiative Nederland
PubMed: Abu-Safieh-2013
,
PubMed: Avila Fernandez 2010
,
PubMed: Jacobson 2007
,
PubMed: Tiwari 2016
,
1 more item
-
-
CLASSIFICATION record, Germline, Unknown
?, yes
-
-
-
-
VKGL-NL_Nijmegen
+/., +?/.
3
-
c.811G>A
r.(?)
p.(Glu271Lys)
-
likely pathogenic, pathogenic, pathogenic (recessive)
g.647740G>A
g.653951G>A
c.[811G>A];[c.1879_1893del], [p.(E271K), p.(R627_E631del)]
-
PDE6B_000087
heterozygous
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
,
PubMed: Palmowski 2019
,
PubMed: Tiwari 2016
-
rs374156343
Germline
yes
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
?/.
1
-
c.815G>A
r.(?)
p.(Arg272Gln)
-
VUS
g.647744G>A
g.653955G>A
-
-
PDE6B_000088
-
PubMed: Koyanagi 2019
,
Journal: Koyanagi 2019
-
rs760089278
Germline
-
1/1204 cases with retinitis pigmentosa
-
-
-
Yoshito Koyanagi
+?/.
1
-
c.830T>C
r.(?)
p.(Leu277Pro)
-
likely pathogenic (recessive)
g.647759T>C
g.653970T>C
-
-
PDE6B_000181
-
PubMed: Taylor 2017
-
-
Germline
-
-
-
-
-
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